BEST OF ASCO LUNG CANCER 2012 David R. Gandara, MD University of California Davis Comprehensive Cancer Center Disclosures • Research Grants: Abbott, BMS/ImClone, Genentech, GSK, Lilly, Merck, Novartis • Consultant: Abbott Molecular, AstraZeneca, Biodesix, Boehringer-Ingelheim, BMS/ImClone, Caris, Celgene, GlaxoSmithKline, Genentech, Lilly, Merck, Novartis, Pfizer, Response Genetics, Sanofi-Aventis BEST OF ASCO LUNG CANCER 2012 Abstracts for Discussion: – Small Cell Lung Cancer (SCLC): • Limited & Extensive Stage – Non Small Cell Lung Cancer(NSCLC): • Genomics: The “Big Bang” effect • Advanced Stage NSCLC – Targeted Therapies: “Coming of Age” » ALK » ROS1 » MEK – Emerging Role of Immunotherapy SCLC Abstracts for Discussion • #7004: Concurrent TRT-Chemotherapy: 1st Cycle vs 3rd Cycle. Phase III (Park et al) • #7003: Amrubicin-Cisplatin vs Irinotecan-Cisplatin in E-SCLC. Phase III JCOG 0509 (Kotani et al) • #7005: Weekly Topotecan +/- AVE0005 (Aflibercept) in 2nd line therapy of E-SCLC. Randomized Phase II S0802 (Allen et al) #7004 Limited Stage: Timing of Chemo-Radiation #7003 Extensive Stage 1st Line Chemotherapy: Amrubicin #7005 Extensive Stage 2nd Line Therapy: AVE0005 Demographic, Biologic, Clinical & Therapeutic Differences between SCLC & NSCLC Feature SCLC NSCLC Incidence Decreasing Increasing Association with Smoking Universal Highly Variable Growth Kinetics ~Rapid Variable Biologic Diversity (Histologic & Molecular) ~Homogeneous Distinct Subtypes Early Metastases Universal Variable Sensitivity to DNA-damaging chemotherapy (1st line) High Variable Sensitivity to Radiotherapy High Variable Advances in Therapy ~15 years Few Advances Dramatic Advances #7004: 1st versus 3rd Cycle TRT + Cisplatin-Etoposide in L-SCLC (Park et al) 1st Cycle arm E P (n=111) LD-SCLC Treatmentnaïve E P E P E P TRT EP: Etoposide 100mg/m2 D1-3 R 1:1 PCI for patients with PR or CR Cisplatin 70mg/m2 D1, q3 w TRT: 52.5 Gy/25 fxs (2.1 Gy/fx, once daily) N=219 3rd Cycle Delayed arm E P E P (n=108) E P E P TRT Primary end point: Complete response rate (WHO criteria) Secondary end point: ORR, OS, PFS, and toxicity (NCI-CTC ver. 2.0) Enrollment between 2003 and 2010 (7 years) Median Follow Up is 59.4 months (about 5 years) Efficacy Comparisons: 1st (initial) vs 3rd (delayed) cycle TRT Favors Cycle 1 but not significantly different Perspective on this Abstract: Therapy of Limited Stage SCLC • Platinum/Etoposide (PE) + 1st cycle concurrent thoracic radiotherapy (TRT) has been standard of care in the U.S. for ~20 years • Regimens adding new systemic agents or substituting agents have generally failed to show sufficient promise to replace PE • Advance: Twice day hyperfractionated RT + PE was proven superior to once daily standard fraction RT (Turrisi et al: NEJM, 1999), but has not been widely adopted in practice • A great deal of attention has already been paid to optimizing the timing of TRT in L-SCLC. Why Revisit It Now? • In reality, 1st cycle concurrent TRT is not feasible in a substantial subset of patients with L-SCLC • Radiation volume considerations (V20 or other parameters) • Delays in radiation planning in some settings/countries • Need for systemic therapy on an urgent basis in some cases Meta-Analysis of TRT Timing: Overall Survival 2-3 Year OS 5 Year OS Meta-Analysis Favors Early TRT Pijls-Johannasma et al: Cancer Treat Rev, 2007 Two Ongoing Phase III Trials in L-SCLC: Testing Radiation Dose Schedules Amended to allow Cycle 1 or Cycle 2 TRT Testing Cycle 2 TRT in both arms • Both are focused on TRT Dose Schedule • Neither is investigating timing of TRT Summary: #7004 Timing of TRT • The results add to literature concluding that early TRT is important (but not necessarily cycle 1) in optimizing efficacy of Chemo-Radiation in L-SCLC • Cycle 1 TRT leads to an increase in some toxicities • Other ongoing Phase III trials are investigating alternative TRT dose schedules but not timing or radiation volume issues • New systemic agents for inclusion into chemoradiation regimens for L-SCLC are needed #7003: JCOG 0509 (Kotani et al) ED-SCLC 20-70 yrs PS 0-1 IP Stratification ● PS ● institution ● sex Sample size n= 282 (n= 141 per Arm) R A N D O M I Z E Irinotecan 60 mg/m2 D1,8,15 Cisplatin 60 mg/m2 D1 Q4 weeks x 4 cycles PCI if CR (2.5Gy/10 Fx) Amrubicin* 40 mg/m2 D1-3 Cisplatin 60 mg/m2 D1 Q3 weeks x 4 cycles AP • • • • Primary Endpoint= OS IP dose schedule was identical to J9511 & SWOG 0124 Amrubicin dose amended to 35 mg/m2 due to FN Trial was closed early by the DSMC Efficacy Comparisons: AP versus IP (JCOG0509) Phase III Investigation of “Newer” Chemotherapeutic Agents in E-SCLC Response Rate in Phase II: 1st line/2nd line Results (1st line in combination with Platinum) Paclitaxel ~35%/~25% Negative Phase III trial (Niell et al) Gemcitabine ~25%/14% Phase II: not promising (Hesketh et al) Topotecan ?/~18% “Positive” Phase III: but not adopted (Heigener et al) Irinotecan ~35%/~25% Conflicting results of Phase III trials (Noda; Lara; Hanna) ? Negative Phase III trial (Socinski et al) ~40% Negative Phase III trial as 2nd line- single agent ( Jotte et al) Agent Pemetrexed Amrubicin from Gandara et al: NCI Early Drug Development Symposium, April 2012 Comparative Efficacy of JCOG 9511 versus SWOG 0124 S0124 did not confirm results of J9511 Efficacy of Irinotecan greater in Japanese patients Toxicity was also greater in Japanese patients Population-related Pharmacogenomics may have influenced results Lara et al: JCO, 2009 Summary: #7003: AP vs IP in 1st Line Therapy of E-SCLC • Another promising drug in SCLC has failed to pass the Phase III test • Approaches exploiting the initial high sensitivity of SCLC to 1st line DNA-damaging chemotherapy are worth pursuing (ECOG 2511: PARPi ABT888) • Demonstrating new agent activity in the 2nd line setting in platinum-refractory disease may be a logical prerequisite for testing in the 1st line setting #7005: Topotecan +/- AVE0005 (Aflibercept) in 2nd Line Therapy of E-SCLC (S0802- Allen et al) Eligibility Criteria Small cell lung cancer Extensive or limited stage 1 prior platinum-based chemotherapy regimen ECOG PS 0-1 Adequate organ function No “anti-angiogenic” risk factors S T R A T I F Y Platinum Sensitive Response to 1st Line Chemotherapy and Progression > 90 days (ES) or 180 days (LS) Platinum Refractory Progression ≤ 90 days (ES) or < 180 days (LS) after 1st Line Chemotherapy R A N D O M I Z E R A N D O M I Z E Topotecan IV 4 mg/m2 Days 1, 8, and 15 AVE0005 IV 6 mg/kg on Day 1 Topotecan IV 4 mg/m2 Days 1, 8, and 15 Topotecan IV 4 mg/m2 Days 1, 8, and 15 AVE0005 IV 6 mg/kg on Day 1 Topotecan IV 4 mg/m2 Days 1, 8, and 15 * Topotecan is omitted on Day 15 for all patients starting on Cycle 5. #7005: Efficacy of Topotecan +/- AVE0005 Perspective on this Abstract: 2nd Line Therapy of Extensive SCLC • In 2nd line therapy, a number of chemotherapeutic agents are active in “platinum-sensitive” patients, but the “platinum-refractory” subset fares poorly • Example: Topotecan is primarily active only in “platinumsensitive” patients • Identifying agents active in the “platinum-refractory” subset is therefore a high priority in clinical research in SCLC • Additional studies evaluating novel targeted agents in SCLC are needed Investigation of “Targeted Therapies” in Extensive SCLC Selected Agents Target(s) Results Imatinib (Johnson et al) KIT, SCF Inactive Bec2/BCG (Giaccone) GD3 ganglioside Bortezomib (PS-341) (Lara et al) Proteasome Sorafenib (Gitliz et al) VEGFR Vandetanib (ZD6474) (Arnold et al) EGFR/VEGFR ABT263 & Obatoclax (Rudin et al; Langer et al) Bcl-2 Negative Phase III trial Insufficient activity Insufficient activity PR: PlatSens: 5% PlatRef: 2% HR 1.43 vs Placebo for OS Insufficient activity PE + GDC0449 orofIMC-A12: Hedgehog or occur without Pending Completion • Biologic Activity some Targeted Agents may RECIST response E1508 (Belani/Rudin) • Manifest as improved DCR IGF-1R (CR/PR + SD), PFS/OS or Biomarker/Imaging effects • “Four Dimensional Model”PARP ABT888 + PE vs PE: E2511 Pending Activation (Owonikoko/Belani) Measuring Effects of “Novel Therapeutic Agents”: A Four Dimensional Model Classic Tumor Response (RECIST) Disease Control (CR + PR + SD) or Timed DCR Survival Endpoints (OS, PFS) Biologic Effects on Tumor (Biomarkers, Functional imaging) adapted from Gandara et al, Clin Lung Cancer, 2007 Biologic Activity without RECIST Response Phase II Study of Aflibercept in Refractory NSCLC Number of patients 98 Treatment Aflibercept 4 mg/kg q 2 wks Primary Objective (RECIST) Best response vs baseline 69.4% pts ≥ 3 lines ORR 2 % 95% CI [0.2 – 7.2%] 20 Best % Tumor Shrinkage Prior treatment 40 0 -20 -40 Patients Leighl et al: J Thorac Oncol , 2010 SHARP Trial: Sorafenib vs Placebo in Hepatocellular Cancer Llovet et al: NEJM 2008 Summary: #7005: Topotecan +/-VE0005 • The S0802 trial met the primary endpoint of improved 3month PFS • RECIST response was low & there was no impact on OS • These data remain hypothesis-generating & require confirmation (Predictive Biomarker development is essential) • How to best combine VE0005 & Chemotherapy remains unclear Advances in Sequencing Technologies and Human Genomics (kilobases/day/machine) Sequencing Technology Massively parallel sequencing Capillary sequencing Gel-based Systems & Lung Cancer (year) Automated slab gel (50) Manual slab gel (10) I 1975 I Human Genomics 2nd generation capillary 1st generation sequencer (103) capillary sequencer (102) I 1980 I I 1985 I I 1990 I I 1995 I Ras mutations as 1st oncogenes (1982) I 2000 I Single molecule? (109) Short-read sequencers (107) Microwell pyrosequencing (105) I 2005 I EGFR mutations (2004-2009) Human Genome Project 1000 Human (2001-2006) Genome (2007- ) Somatic mutations in lung adenocarcinoma (2008) Li, Gandara et al: JCO 2012 (in press) I 2010 I Future ALK gene rearrangement (2007-2011) The Cancer Genome Atlas (2010- ) lung adenocarcinoma genome (2008) Small cell lung cancer genome (2009) Squamous cell lung cancer genome (2012) Comprehensive Characterization of Squamous Cell NSCLC (SCCA) #7006 Ramaswamy Govindan, Peter Hammerman, Neil Hayes, Matthew Wilkerson, Steve Baylin and Matthew Meyerson On Behalf of the Lung Cancer Working Group of The Cancer Genome Atlas (TCGA) Project #7006: Characterization of Genomic Alterations in Cancer (TCGA) Structural variants • • • Translocations Fusions Inversion Copy number alterations • • • Amplifications Deletions LOH Point mutations & indels • • • • Missense Nonsense Splice site Frameshift Gene expression • • • Outlier expression Isoform usage Pathways & signatures Wild type AGTGA Mutant AGAGA • This presentation: Squamous Cell Cancer • Goal 500 • Accrued so far 300 • Analysis completed 178 reported here From Govindan et al: ASCO 20`2 #7006: NSCLC (including SCCA) has a very high rate of somatic mutations n=109 81 64 38 316 100 / Mb 10 / Mb 1 / Mb 100 17 82 28 119 20 “Smart Cancers” “Stupid Cancers” 0.1 / Mb ? ? 29 40 CarcinogenInduced Cancers Ovarian, Breast & Prostate Cancers Hematologic & Childhood Cancers 21 Courtesy: Gaddy Getz and Mike Lawrence, Broad Institute, MIT mRNA Expression Analysis of SCCA 15% 36% PI3K alterations 30 24% 25% NF1 loss New Therapeutic Targets in squamous cell lung carcinoma (SCCA) Gene Event Type Frequency CDKN2A Deletion/MutationMethylation 72% PI3KCA Mutation 16% PTEN Mutation/Deletion 15% FGFR1 Amplification 15% EGFR Amplification 9% PDGFRA Amplification/Mutation 9% CCND1 Amplification 8% DDR2 Mutation 4% BRAF Mutation 4% ERBB2 Amplification 4% FGFR2 Mutation 3% Summary: Characterization of Squamous Cell NSCLC (SCCA) • SCCA characterized by: Complex genomes with frequent and unique rearrangements • Proposed a molecular sub-classification (yet to be clinically validated) • Multiple mechanisms for alteration/inactivation of the same gene (e.g. CDKN2A) • Potentil therapeutic targets identified in 75% of patients, including FGFRs, PI3 kinase pathway, EGFR/ERBB2 and Cyclin/CDK complexes “Targeted Therapies Coming of Age” (from Li, Gandara et al: JCO 2012, in press) Adenocarcinoma NSCLC as one disease Squamous Cell Cancer FGFR1 Amp EGFRvIII Unknown Histology-based Subtyping PI3KCA EGFR DDR2 #7500: LUX-Lung 3: Phase III trial of afatinib versus pemetrexed and cisplatin as first-line treatment for EGFR mutation+ adenocarcinoma (Yang et al) Stage IIIB-IV Adenocarcinoma with EGFR mutation R A N D O M I Z A T I O N Afatinib 2:1 Pemetrexed + cisplatin ● Primary endpoint: PFS ● Secondary endpoints: ORR, DCR, OS #7500: LUX-Lung 3: Phase III trial of afatinib versus pemetrexed and cisplatin as first-line treatment for EGFR mutation+ adenocarcinoma (Yang et al) Response Afatinib Cis/Pem Overall 56% 23% E19del/L858R 69% 44% The Story of “ALK” in NSCLC 2012 2007-2012 Crizotinib FDA approval in 2011 2010 2008 2007 ALK-positive NSCLC & Impact of ALK inhibition by Crizotinib Therapy Activity of ALK inhibitor Crizotinib in patients with advanced ALKpositive NSCLC (Response Rate=61%) • • • • • Previously treated advanced NSCLC N=116 59% male 72% never-smoker 56% ≥2 prior regimens Camidge et al: ASCO 2011; Abs #2501 First-in-human Phase I trial of ALK inhibitor LDK378 in ALK+ solid tumors Ranee Mehra,1 D. Ross Camidge,2 Sunil Sharma,3 Enriqueta Felip,4 Daniel Tan,5 Johan Vansteenkiste,6 Tommaso De Pas,7 Dong-Wan Kim,8Armando Santoro,9 Geoffrey Liu,10 Meredith Goldwasser,11 David Dai,12 Anthony L. Boral,11 Alice Shaw13 • Potent activity in enzymatic and cell based assays • LDK378 treatment results in tumor regression in EML4ALK expressing xenografts Mehra R, et al. ASCO. 2012; #3007 LDK378 IC50 (μM) Crizotinib IC50 (μM) Enzymatic ALK MET 0.00015 3.2 0.003 0.008 Cell-based ALK MET 0.027 1.3 0.11 0.028 Assay LDK378 has antitumor activity in ALK+ NSCLC NSCLC Other diseases Initial dose (mg) Evaluable Patients (n) Responses (PR) < 400 8 2 (25) ≥ 400 33 22 (67) 50 – 600 6 0 • Of the 24 responding patients, 11 responses were confirmed, and 7 are awaiting confirmatory scans • Response rate was 81% (21/26) in patients with NSCLC treated at ≥ 400 mg who progressed following crizotinib Mehra R, et al. ASCO. 2012; #3007 Response to LDK378 Baseline Mehra R, et al. ASCO. 2012; #3007 After 6 weeks on LDK378 #7508: Clinical Activity of Crizotinib in Advanced Non-Small Cell Lung Cancer (NSCLC) Harboring ROS1 Rearrangement Alice T. Shaw1, D. Ross Camidge2, Jeffrey A. Engelman1, Benjamin J. Solomon3, Eunice L. Kwak1, Jeffrey W. Clark1, Ravi Salgia4, Geoffrey I. Shapiro5, Yung-Jue Bang6, Weiwei Tan7, Lesley Tye7, Keith D. Wilner7, Patricia Stephenson8, Marileila Varella-Garcia2, Kristen Bergethon1, A. John Iafrate1, and Sai-Hong I. Ou9 1Massachusetts General Hospital Cancer Center, Boston, MA, USA; 2University of Colorado Cancer Center, Aurora, CO, USA; 3Peter MacCallum Cancer Centre, East Melbourne, Australia; 4University of Chicago Cancer Center, Chicago, IL, USA; 5Dana Farber Cancer Institute, Boston, MA, USA; 6Seoul National University, Seoul, Korea; 7Pfizer Inc, La Jolla, CA, USA; 8Rho, Inc, Chapel Hill, NC; 9Chao Family Comprehensive Cancer Center, Orange, CA, USA Shaw et al: ASCO Annual Meeting 2012, June 1–5, Chicago, IL #7508: Clinical activity of crizotinib in ROS1-positive NSCLC (Shaw A et al) ● ROS1 rearrangement in ~1% of NSCLC cases ROS-1 fusion partners TPM3-ROS1 SDC4-ROS1 ● More common in younger never or light smokers with adenocarcinoma SLC34A2-ROS1 ● Multiple ROS1 fusion partners CD74-ROS1 ● Measured by “Break-Apart” FISH Assay EZR-ROS1 LRIG3-ROS1 ● No overlap with other oncogenic drivers (EGFR MT) Break-Apart FISH Assay Bergethon et al., JCO 30(8): 863-70, 2012; Takeuchi et al., Nat Med 18(3): 378-81, 2012 Abstract: 7508 Background on ROS1 Signaling Pathways #7508: Clinical activity of crizotinib in ROS1-positive NSCLC (Shaw A et al) (N=14) Bergethon et al., JCO 30(8): 863-70, 2012; Takeuchi et al., Nat Med 18(3): 378-81, 2012 Abstract: 7508 Chemotherapy +/- MEK inhibition (Selumetinib or AZ6244) in KRAS mutant NSCLC (Janne et al: ASCO 2012, #7503) R A N D O M I Z A T I O N Stage IIIB-IV NSCLC with KRAS mutation Docetaxel + AZD6244 Docetaxel ● Primary endpoint: PFS ● Secondary endpoints: ORR, DCR, OS Parameter Docetaxel Docetaxel/AZD6244 mPFS (mos) 2.1 5.3 Response 0% 37% OS 5.3 9.4 Chemotherapy +/- MEK inhibition (Selumetinib or AZ6244) in KRAS mutant NSCLC (Janne et al: ASCO 2012, #7503) PFS OS #7509: Clinical Activity and Safety of Anti-PD1 (BMS-936558, MDX-1106) in Advanced Non-Small-Cell Lung Cancer J.R. Brahmer,1 L. Horn,2 S.J. Antonia,3 D. Spigel,4 L. Gandhi,5 L.V. Sequist,6 J.M. Wigginton,7 D. McDonald,7 G. Kollia,7 A. Gupta,7 S. Gettinger8 Role of PD-1 in suppressing antitumor immunity (“Tumor Cell Defense”) Activation (cytokines, proliferation, migration, lysis) APC T cell B7.1 MHC-Ag CD28 TCR Signal 1 Tumor From Keir ME et al, Annu Rev Immunol 2008; Pardoll DM, Nat Rev Cancer 2012 Role of PD-1 in suppressing antitumor immunity (“Tumor Cell Defense”) Activation (cytokines, proliferation, migration, lysis) APC T cell B7.1 MHC-Ag CD28 TCR Signal 1 (-) (-) (-) PD-1 PD-L1 Tumor Inhibition Tumor of Tumor Cell Defense From Keir ME et al, Annu Rev Immunol 2008; Pardoll DM, Nat Rev Cancer 2012 Role of PD-1 in suppressing antitumor immunity (“Tumor Cell Defense”) Activation (cytokines, proliferation, migration, lysis) APC T cell B7.1 MHC-Ag CD28 TCR Signal 1 (-) (-) (-) PD-1 AntiPD-1 PD-L1 Tumor Inhibition Blocked Tumor From Keir ME et al, Annu Rev Immunol 2008; Pardoll DM, Nat Rev Cancer 2012 #7509: Clinical Activity and Safety of Anti-PD1 (BMS-936558, MDX1106) in Advanced NSCLC Clinical Activity in NSCLC Patients Pop ALL NSCLC NSCLC Dose (mg/kg) Pts n ORR n (%) Duration of Response (mo) SD 24 wk n (%) PFSR at 24 wk (%) 1-10 76 14 (18) 1.9+ to 30.8+ 5 (7) 26 1 18 1 (6) 9.2+ 1 (6) 16 3 19 6 (32) 1.9+ to 30.8+ 2 (11) 41 10 39 7 (18) 3.7 to 14.8+ 2 (5) 24 • ORR was assessed using modified RECIST v1.0 • 3 NSCLC patients had a persistent reduction in baseline target lesions in the presence of new lesions but were not classified as responders for the ORR calculation Pre/Post Anti-PD1 Treatment - 58 y/o ex smoker with squam NSCLC - 4 prior regimens for Stage IV disease Association of PD-1 Expression in Tumor and Response to Anti-PD1 Treatment Best of ASCO 2012: Lung Cancer: Gandara Summary • Incremental progress in being made in understanding the underlying biology & genomics of lung cancer • These findings are leading directly to discovery of new therapeutic targets and new therapeutic agents • The age of “personalized therapy” for lung cancer is rapidly emerging • Considerable challenges remain • In every challenge there are opportunities • We must take full advance of these opportunities to advance the care & cure of lung cancer patients