CARDIAC EXAM THREE Congenital Heart Disease Acyanotic Defects I. Etiology a. Possible Causes i. Fetal exposure to drugs 1. Phenytoin 2. Lithium 3. Alcohol 4. Tobacco smoke ii. Maternal metabolic disorders 1. Diabetes mellitus 2. hypercalcemia iii. increased maternal age iv. genetic patterns v. chromosomal abnormalities 1. trisomy syndromes 13, 15, 18, 21 a. 21 is downs syndrome b. Physical Consequences i. Most dangerous and most common is CHF ii. Increased work load of the heart 1. Decreases exercise tolerance iii. Pulmonary hypertension 1. Tachypnea and recurrent respiratory infections iv. Inadequate systemic output 1. Tissue hypoxia v. Cyanotic defects vi. Growth retardation vii. Child at risk for acid base problems and dehydration c. Signs and Symptoms i. Feeding difficulties resulting in poor weight gain ii. Cyanosis intermittent or persistent 1. Clubbing of fingers and toes iii. Exercise intolerance 1. Hypotonic posture iv. Frequent respiratory infections, dyspnea, stridor v. Characteristic heart murmur vi. Infants bradycardia <120 or tachy >160 vii. Weak or muffled cries II. 1. Cries should be angry viii. General level of activity is restless or lethargic ix. Observe posture 1. Hypotonic, hyper extension of neck, dyspnea when supine x. When sitting upright tripod position, chin out tongue protruding xi. Hearing loss Types of CHD a. Atrial Septal Defect i. Size and symptoms depend on size and location of defect ii. Small and high on the septum 1. No problem iii. Large and close to entry of vena cava 1. Some mixing of blood iv. Murmur = systolic with a widely split second heart sound v. EKG = diastolic overload at R atrium vi. Treatment 1. Closed during a cardiac catheterization 2. Closed by surgery-done by school age 3. Closes by self b. Ventricular Septal Defect i. Most common cardiac defect ii. Blood flows from L ventricle to R ventricle iii. Limited damage because pulmonary vasculature is low pressure iv. Size and location related to pulmonary pressure 1. R ventricular hypertrophy 2. L atrial hypertrophy 3. As children age extensive L to R shunting no longer occurs because increase in pulmonary pressures 4. Eisenmengers Syndrome a. Sometimes R pressures becomes greater and L to R shunt may occur b. Exception to rule about mixing of blood v. Signs and symptoms depend on size and location vi. Assessment 1. Most defects are asymptomatic 2. Defects typically small a. Not much L to R shunting 3. Harsh, loud or blowing left parasternal pansystolic murmur (left of the sternal border and occurs throughout systole) may be heard with thrill 4. Medium sized or larger defecs during infancy a. May cause dyspnea, tachypnea, slow physical development, feeding difficulties and frequent pulmonary infections b. Mild cyanosis upon crying vii. Treatment 1. Closed via cardiac catheterization 2. If defect small and asymptomatic no treatment a. Will close by 1-2 years of age 3. Treat surgically a. If large need pacemaker 4. Medical management CHF 5. Risk of infective endocarditis children a. Need antibiotics before invasive procedure c. Patent ductus Arterious (PDA) i. Twice as frequent in females ii. Typically closes in the first 24 to 72 hours of life iii. If does not close, the higher pressure in the aorta can cause the blood to flow into the pulmonary artery 1. Oxygenated blood recirculates through the pulmonary system 2. Increase work on the L side of the heart and vascular pressure in the pulmonary tree, increase blood flow in the ascending aorta iv. Signs and symptoms depend on the size of ductus and amount of shunting v. Assessment 1. Classic machinery type of murmur 2. Dyspnea on exertion, easy fatigability (susceptibility to fatigue) 3. Physical under development 4. Increase infections 5. HR >150 gallop rhythm, bounding pulses and wide systemic pulse pressure 6. CHF at 6 to 12 weeks in a full term infant vi. Management 1. Medical a. Supportive fluid restriction b. Diuretics c. Digoxin i. Special considerations for neonates 2. Surgical a. Transection, ligation of the ductus (done at 6 months) i. Treat even if asymptomatic because of CHF, infective endocarditis, and calcification at the ductal site 3. Pharmacologic closure low birth rate infants a. Indomethacin (Indocin) i. Inhibits prostaglandin synthesis (cell contractility) ii. Improvement occurs in 12 to 18 hours iii. May contribute to hyperbilirubinemia (causes jaundice), transient renal dysfunction, and hyponatremia d. Pulmonic Stenosis i. Pulmonary valve is obstructed by fusion of the cusps at their commissures 1. Increases systolic pressure and hypertrophy of the right ventricle ii. In general cyanosis iii. Loud Pulmonary systolic ejection murmur iv. Management 1. Mild to moderate do nothing 2. Severe do valvotomy to open valve e. Aortic Stenosis i. Valvular or Subaortic ii. Causes restriction of blood outflow and L hypertrophy iii. Signs and symptoms 1. Small is typically asymptomatic until physical growth requires additional CO 2. Longer fatigue, dizziness, fainting, and episodes of pulmonary edema iv. With age 1. Faint peripheral pulses and angina pain 2. Death after sudden exertion because of decreased blood flow to heart 3. Coarse systolic ejection murmur with thrill a. Radiates to neck and down L sternal border f. Coarction of the Aorta i. Localized malformation caused by a deformity of the aorta that results in a narrowing of the lumen of the vessel ii. Two types 1. Preductal a. Between subclavian artery and the ductus arterious 2. Postductal a. Distal to the ductus arterious iii. Assessment 1. BP is higher then normal in upper part of body 2. Pt may have headache, dizziness, fainting, epistasis, and later CVA 3. BP is decreased in lower areas of body a. Absence or diminished femoral pulses, legs cooler than arms and muscle cramps with exercise iv. Management 1. Surgical repair is the desired treatment, especially for infants or children with long stenosis v. Complications 1. Hypertension 2. GI problems occur N?V 3. Distention 4. Pain a. If severe may indicate small bowel obstruction Cyanotic Defects I. Tetralogy of Fallot a. Four anomalies i. Obstruction to R ventricular out flow (pulmonary stenosis) ii. Ventricular septal defect iii. Overriding aorta iv. R ventricular hypertrophy b. Assessment i. Infants are not cyanotic because of patent ductus ii. Cyanosis can be seen lips mouth finger and toes iii. Dusky body (dark in color) iv. Polycythemia v. 1 to 2 years of age clubbing vi. Knee chest position vii. Paroxysmal dyspnea attacks (blue spells) 1. Can last a few minutes to a couple of hours 2. Short episode –sleep 3. Long –unconsciousness, convulsions and death 4. Occurs with no warning a. Follow feeding, emotional upset and defecation, hypoxia, and metabolic acidosis viii. Management 1. Prevent above 2. Corrective Procedures a. Close VSD b. Pulmonary Valve open 3. Palliative a. Many names essentially create a ductus b. Therapy prostaglandin E (PGE) i. Relaxes smooth mucle of the ductus and keeps it open c. May produce systemic hypotension c. Transposition of Great Vessel i. The tricuspid valve fails to open thus no communication between R atrium and R ventricle ii. Management 1. Blood flows through ASD or patent foramen ovale to the L side of the heart 2. Prostoglandin E d. Truncus Arteriosus i. Pulmonary artery and aorta do not separate ii. 1 vessel receives blood from L and R side of heart iii. Requires large VSD for survival Nursing Care I. Assessment a. Acyanotic i. Poor weight gain, small stature ii. Respiratory diseases iii. Exercise intolerance iv. Tachycardia, tachypnea, dyspnea v. Not or mild cyanosis b. Cyanotic i. Usually at time of birth ii. Difficulty eating because of inability to breath and suck at the same time iii. Delayed physical growth because of chronic hypoxia iv. Frequent and severe respiratory infections v. Moderate to severe exercise intolerance vi. Chest pain that becomes severe with exercise vii. Hypoxic spell during periods of high demand for O2 1. Sob, cyanosis, chest pain, squats viii. Chronic hypoxia 1. Increases RBC count 2. Causes clubbing of fingers and toes \ 3. Hgb may rise 20-30 gm or more 4. Hematocrit 60-80% increase ix. Polycythemia c. Pre op i. Baseline vitals, including apical pulse, existence and quality of peripheral pulses ii. Educational needs iii. Lab values, CBC, chemistry d. Post Op i. Respiratory states, chest tubes and drainage, breath sounds ii. Vital signs, including apical and femoral pulse, arterial an venous pressures, cardiac rhythm iii. Hydration and output status 1. Weigh diapers iv. S and s of CHF v. Color of skin, mucous membranes, nail beds and ear lobes vi. Level of discomfort and anxiety vii. Surgical incisions (suture line)