Reproductive System Disorders Pathophysiology Male Reproductive System • Anatomy – Gonads = Testes – Ductile system = epididymis, vas deferens, ejaculatory duct, urethra – Supportive glands = seminal vesicles, prostate, bulbourethral (Cowper’s) – External genitals = scrotum, penis • Testes – tunica vaginalis = parietal peritoneum that remains surrounding testis after its descent – tunica albuginea = tough connective tissue membrane that surrounds testis and enters the gland to form septa – seminiferous tubules = where sperm are developed; approx. 100 yards in in testis; contain Sertoli cells; between tubules are inter-stitial spaces that contain Leydig cells • Testes (cont) – Physiology • Spermatogenesis – mature sperm formed by process of Meiosis » Key = getting mature gamete with ½ number of chromosomes » mature sperm = head (nucleus & acrosome), neck (mitochondria), and tail » takes 60 days +/- to make a sperm – primary spermatocyte, secondary spermatocyte, spermatids, sperm • Testosterone Production – 2 key functions » masculinization » anabolism • Male Ductal System – Epididymis – storage tank for sperm – sperm get final maturation – Vas Deferens – becomes Ejaculatory Duct after it joins seminiferous tubule duct – Urethra • Accessory Glands – Seminal Vesicles – contributes 60% of semen » rich in fructose ; provides energy for the sperm – Prostate – contributes 30% of semen ; provides nutrients for the sperm; antibiotic secretion – Bulbourethral Glands (Cowper’s) – contribute 5-10% of semen ; provides lubrication & sterilization • External Genitalia – Penis – 3 columns of erectile tissue » corpora cavernosa (2) & corpora spongiosum (1) – glans covered by foreskin (prepuce) – Scrotum – skin-covered (has hair follicles) pouch suspended from groin • Hormones and male reproductive function Female Reproductive System • Anatomy – gonads = ovaries – ductal system = fallopian tubes, uterus, vagina – accessory glands = Bartholin's, breasts – external genitalia = clitoris, labia majora & minora, perineum • Ovaries – contain gametes (oocytes) surrounded by some cells (follicular cells) – these called Primary Follicles » each ovary has appox. 1 million at birth – life cycle of oocyte after puberty: primary oocyte, secondary oocyte, ovum – functions • gamete production • hormone production – Estrogen = causes feminization ; from granulosa cells – Progesterone = prepares for pregnancy ; from corpus luteum • Female Ductal System – Fallopian Tubes • distal end = fimbria • Outer 1/3 = fertilization – Uterus • composed of fundus, body, & cervix • has myometrium & endometrium] – Vagina • Accessory Glands – Bartholin’s (greater vestibular) • exocrine gland • provides lubrication – Breasts • composed of glands & ducts surrounded by fat tissue • External Genitalia – clitoris, labia majora & minora (no hair follicles), vestibule, perineum • The Menstrual Cycle – begins after menarche ; ends with menopause – 4 basic parts: – Menses – Proliferative Phase = first half of cycle » deals with maturation of follicle & development of more granulosa cells thus producing more estrogen – Ovulation = usually at midcycle – Secretory Phase = second half of cycle » deals with conversion of ruptured follicle to corpus luteum » corpus luteum produces progesterone • hormonal control • hypothalamus--------GnRH (gonadotropin releasing hormone) • anterior pituitary---- FSH (follicle stimulating hormone) LH (luteinizing hormone) • Ovary --------------- Estrogen Progesterone Male reproductive tract disorders overall outline • Disorders of testes & scrotum • Disorders of prostate • Disorders of the penis Disorders of the Testes & Scrotum • Cryptorchidism – undescended testis – By age one, 80% are in scrotum – incidence: 3% of term babies; 20% of premies – increases the incidence of carcinoma (Seminoma) – treat early-------the longer you wait, the greater the chance of decreased sperm & testosterone production • Remember: – Tunica Albuginea = thick connective tissue that covers testes & divides substance of testes into lobules – Tunica Vaginalis = peritoneum that remains around testes after descent – 2 layers: visceral (on testis) & parietal (around testis) • Hydrocele – most common disease of testes – it’s fluid in cavity bound by the 2 layers of tunica vaginalis – this may communicate with peritoneal cavity via congenital patency of process vaginalis – this may cause size to vary from time to time • Infertility Problems – deals with decreased production and/or quality of sperm – 2 distinct reasons – poor production in sperm development » One correctable cause = varicocele – blockage of ductile system – low count = oligospermia – zero count = azospermia • Varicocele – varicosities around the testis (usually left testis) – left spermatic vein into renal vein (10 cm higher than insertion of right spermatic vein into inferior vena cava) – usually begins at puberty – may be relieved by lying down • Torsion of the testis – Etiol: • Spontaneous • Post trauma – Timing • Usually puberty – Path: necrosis & infarction • Testicular Cancer – range from VERY aggressive to least aggressive • Germ cell tumors » Seminoma = least aggressive (most common) » Nonseminomas * embryonal carcinoma * teratomas * choriocarcinoma = most aggressive • Non- germ cell tumors » May be hormonally active (secrete androgen or estrogen) » Exp: leydig cell, Sertoli cell – tumors of young men ( age 15 - 35) – diagnosis : tumors are solid masses - no transillumination – Usually unilateral – predisposing factors: – undescended testes – inguinal hernia during childhood – prior history of mumps orchitis » Note: in mumps orchitis, 50% of cases result in testicular atrophy – Cure rate = 95% Prostate Diseases • Benign Prostatic Hypertrophy (BPH) – enlargement of the prostate common in older men – Involves central area of gland – complications include: • pyelonephritis • hydronephrosis • uremia • Cancer – primarily occurs in men over age 50 – third leading cause of cancer death – Involves periphery of gland – Usually begins as nodule on posterior surface of gland – Many are androgen dependent – If metastases, first usually to bone – diagnosis » DRE » 2 serum markers » PSA (prostatic specific antigen) » Prostatic acid phosphatase » Ultrasound Pathology of the Penis • Foreskin (prepuce) – phimosis – paraphimosis – redundant foreskin • Glans – Balantitis STD from Yeast (Candida) • Carcinoma – – – – Rare Risk factors: HPV (now have vaccination) First sign = usually leukoplakia circumcision in child prevents it • adult circumcision does not prevent it • Impotency – approx. 50% of men age 40 - 70 have, at times, some degree or complete impotency ( failure to get an erection) – sexual stimulation causes release of nitric acid from nerves in penis – an enzyme breaks down the product of nitric acid that causes the erection – this enzyme’s effect is loss of the erection – this is where Viagra works ; it prevents loss of the erection Female reproductive tract disorders overall outline • Structural abnormalities • Menstrual disorders – Endometriosis – Menopause • Infections • Tumors – Benign – Malignant • Breast • Pregnancy • STD’s Structural abnormalities • Pelvic relaxation disorders – Normal variations of uterine position • Uterine mobility is key to normalcy – Uterine prolapse – First, second, & third degrees – Cystocele – Rectocele Normal variations of uterine position – Uterine mobility is key to normalcy – midline – Anteverted & anteflexed – Retroverted & retroflexed Uterine Prolapse • def = downward displacement of uterus • etiol = fascial tissue defect • First degree • Get vaginal shortening • Second degree • Cervix at introitus • Third degree • Vagina completely everted • Uterus hanging outside vagina • Cystocele • downward displacement of bladder into vagina • Can get retention & frequent cystitis • urethra may or may not accompany it » called cysto-urethrocele » frequently get symptom of urinary stress incontinence • Rectocele • displacement of rectum into vagina • Usually asymptomatic • If very large may get constipation & inability to completely evacuate rectum • May get ulceration of vaginal wall • See picture Menstrual Disorders • Dysmenorrhea – Primary dysmenorrhea = when no obvious pathology found – ? Hormonal cause » prostaglandins » hormonal changes secondary to teenage ovulatory cycles – Secondary dysmenorrhea = when obvious pathology found as the cause • Amenorrhea – Primary Amenorrhea = never having a menstrual flow – Secondary Amenorrhea = having menstrual cycles & then they stop – causes = many !!! » Treatment directed at the underlying cause • Dysfunctional Uterine Bleeding (DUB) – abnormal menstrual flow when no obvious cause is known – frequently thought to be secondary to some type of hormonal imbalance, but specific diagnosis not necessary to have DUB – Types: » » » » » oligomenorrhea polymenorrhea menorrhagia metrorrhagia meno-metrorrhagia • Premenstrual Syndrome (PMS) – group of symptoms that occur in the woman’s secretory phase of cycle – Currently called : PMDD (premenstrual dysphoric disorder) • Def of dysphoria = excessive pain, anguish, & agitation – usually secondary to inappropriate ovulation – Key = too much estrogen & not enough progesterone in the second half of the cycle • Endometriosis – A condition when you get endometrial tissue located outside its normal position, which is the inside lining of the uterus – symptoms depend on where the ectopic tissue is located – the tissue has function, i.e. bleeds with menstruation – Sx : pain – Complications • Fibrosis • Scarring • Adhesions • Infertility • Dyspareunia • menopause – Get cessation of menses & drop in estrogens which can cause: – general symptoms » irritability » short term memory loss » Insomnia » Vasomotor instability = hot flashes & night sweats – gynecological symptoms » vaginal dryness & dyspareunia » urinary stress incontinence – Cardiovascular problems » ASHD » coronary artery disease » strokes – Osteoporosis – Dx: – High FSH; low estrogens Infections of the Female Reproductive Tract • Vaginitis – 3 types: • Yeast Vaginitis – caused by fungus from genus Candida or Monilia • Trichomonas – caused by a protozoa – may be sexually transmitted • Bacterial Vaginosis – caused by different bacterial overgrowth – used to be called non-specific vaginitis or Gardnella • Generally most cases of vaginitis are NOT sexually transmitted, but at times they ALL may be sexually transmitted !! • Pelvic Inflammatory Disease (PID) – usually acute, but may be chronic – may involve some or all of the pelvic organs – get tissue inflammatory reaction with resultant symptoms – Key symptom = pelvic pain – Pain worsens with movement & sex – frequently secondary to untreated or inadequately treated STD – Complications – Infertility (pyosalpinx) – Adhesions – Dysuria – Irregular vaginal bleeding See next slide • Note PID spread: – – – – Vaginitis Cervicitis Endometritis Oophoritis • Toxic Shock Syndrome (TSS) – vaginal infection with systemic symptoms – caused by staphlococci toxin which comes from nidus of infected tampon – prevention by proper tampon toilet – Symptoms begin immediately post menses Bartholin cyst (Bartholinitis) Etiol = pathogens that cause inflammation Duct become obstructed Get “large pimple” Tumors of the Female Reproductive Tract • Cervix – Benign • Cervical polyps – malignant • key ages: 20 - 40 • pap smear • Etiol: HPV – Vaccine available • Uterus – benign • fibroids = commonest tumor of female repo. System – leiomyomas – only in premenopause – See next slide – malignant • ? Estrogen related • Age: 50 – 70 • Dx: pmb • • Estimated that half the women get them during the reproductive years Clinically symptoms depend on size & location • Submucous = bleeding problems, infertility • Intramural = sx only if large • Subserous = pressure sx from surrounding structures • Ovary – Benign • Functional (commonest) – Follicular cyst – Corpus luteum cyst • Non-functional (benign germ cell) (e.g. Teratoma) – Malignant Solid teratoma • Factors that suppress ovulation decrease the risk • Avg age = 40 • 2 basic types – Epithelial (line ovary or follicles) – Germ cell – aggressive » Mainly in children & adolescents • See next slide re: – Late diagnoses – seeding Functional (follicular) cyst Breast disorders • Fibrocystic breasts • Was called fibrocystic “disease” • “lumpy” breasts • Fibroadenoma • Benign • In young girls (age 15-25) • nontender • Intraductile papilloma • Get nipple discharge • Mammary duct ectasia – Get lumpiness beneath areola – Seen in – Postmenopausal – Pregnancy – Lactation – Get thick nipple discharge – Pathophysiology: ducts dilate & fill with cellular debris; get inflammation • Breast cancer – – – – – 1 out of 8 women in USA Most are intraductile carcinomas 50% in upper outer quadrant Ca in situ = mammary dysplasia Risk factors: – Family history – Menstrual history – Reproductive history Pathology in Pregnancy • Morning Sickness – severe form = Hyperemesis Gravidarum • Spontaneous Abortion – 3 Types : Complete, Incomplete, Missed • Ectopic Pregnancy • Toxemia of Pregnancy = syndrome of hypertension, proteinuria, & edema • called Preeclampsia • If severe & accompanied by convulsions, called Eclampsia • Placental Problems – Placenta Praevia – Abruptio Placenta • Hydatidiform Mole = development abnormality of conception • may progress to Choriocarcinoma • Preterm Birth – 8% of all births in US – Preterm labor – Preterm PROM (premature rupture of membranes) » Responsible for half of all premie deliveries in US • Trauma during pregnancy – Complicates 1 out of 12 pregnancies in US – Watch for: » Uterine contractions » Uterine tenderness &/or irritability » Ruptured BOW » Nonreassuring FHR pattern » Vaginal bleeding • Maternal hemorrhage – Is the leading cause of maternal mortality – Hemorrhagic shock – Postpartum hemorrhage • Endometritis – Occurs in 1-3% of vaginal births – Occurs in 10-50% of cesarean sections STD’s • AIDS (Acquired Immunodeficiency Syndrome) • Def: progressive impairment of the immune system caused by the immunodeficiency virus (HIV) – Attacks helper T lymphocytes • Initial infection similar to URI • Then latency • Then AIDS – Begins with generalized adenopathy, weight loss, fatigue, nt. Sweats, and diarrhea – Get opportunistic infections: » PCP (pneumocystis carinii pneumonia) = caused by small protozoa (? fungus) that can normally be found in lung tissue of certain animals (dogs) and in humans » Toxoplasmosis = small protozoan that can infect many mammals including cats and dogs » Herpes simplex » Herpes zoster (shingles) » TB • AIDS (continued) – Get opportunistic cancers » Non-Hodgkins lymphoma » Kaposi’s sarcoma • HIV also has predilection to attack G-I cells & CNS cells – Get malabsorption, colitis, and proctitis – Dementia • Diagnosis – ELISA (enzyme-linked immunosorbent assay) – Western blot test • Treatment – AZT = reverse transcriptase inhibitors – Protease inhibitors – Fusion inhibitors • Chlamydia – Most frequent bacterial STD – Known as the “silent STD” – Transmitted via oral, anal, or genital intercourse » Oral route can lead to conjunctivitis – If symptomatic, get urethritis – Incubation = 1-3 weeks • Gonorrhea – – – – Bacterial Incubation = 1-3 weeks (usually less than 1 week) Very similar in signs & symptoms to chlamydia Antibiotic resistance • Syphilis – – – – – – Bacterial Can get primary, secondary, and tertiary forms New cases at an all time low Primary = hard, painless chancre in 2-3 weeks ------------ see pictures Secondary syphilis may appear 1-3 months later Then latency for years & then possible tertiary syphilis • Chancroid – Soft chancre (painful) with bubo(necrotizing ulceration & lymphadenopathy) in 1 week • See pictures – Bacterial – Frequent in developing tropical countries – Increasing in urban USA • Genital Herpes – Type I & type II – Short incubation of 2-7 days – See pictures • Hepatitis B & C – Transmitted in body fluids • Genital warts – Very contagious – First exposure incidence: – 40% ---to--- 90% – Viral; HPV – 120 different serotypes – A few cause dysplasia & neoplasia – Condylomata accuminatum – Benign growths – See picture – Prolonged incubation of 1-6 months – Most frequent STD – Estimated that 60% of sexually active young women in USA have it – New vaccine available Differences in clinical appearance among genital ulcers