Physical therapy Orthotics Control of spasticity Orthopedic surgery Approaches : Remove Noxious Stimuli Rehabilitation Therapy Oral Medications Neurolysis Orthopedic Options Neurosurgical Procedures Selective dorsal rhizotomy Intrathecal baclofen Botulinum-A toxin Modified Ashworth Scale: 0 = no increase in muscle tone 1 = slight increase in muscle tone (catch or min resistance at end range) 1 + = slight increase in muscle resistance throughout the range. 2 = moderate increase in muscle tone throughout ROM, PROM is easy 3 = marked increase in muscle tone throughout ROM, PROM is difficult 4 = marked increase in muscle tone, affected part is rigid Positioning Avoid prolong sitting(less hip & hamstring flexion ) Prone lying at night (less hip flexion ) Abduction wedge at night & in wheelchair (less hip adduction) AFO splint Standing frame Molded thoracolumbar orthosis for early scoliosis or kyphosis Total contact support incorporated into a contoured seating system PHYSIOTHERAPY PHYSICAL AGENTS Aim: a. Analgesia b. Ms. Relaxation c. Collagen extensibility Modalities: 1) Ice 20mins. 2) Heat: Superficial : Dry: I.R. Moist: hot packs Deep : S.W. U.S ELECTRIC CURRENTS Aim: Ms. strengthening (galvanic & faradic) . Analgesia ( TENS, IF) EXERCISES For spasticity : Passive ROM Stretch (short ms.) Strengthening (weak ms., antagonist), resistive > 3/5 For hypotonia : Strengthening ( weak ms) Balance For athetosis : Training to control simple joint motion SERIAL CASTING Indications: focal contracture (especially elbows, Method: knees, ankles ). Limb is stretched then casted in a lengthened position ( can be combined with blocks ) Changed every few days or weeks to gradually stretch contracted structures. Neurolysis Botox Injections Phenol Injections Dorsal Rhizotomy NEUROSURGERY - Ideal patient: young child (3-8 yrs.) w/ spastic diplegia ambulatory w/ spastic gait. - Method: - Surgical cutting of posterior (sensory) root to decrease sensory input to spinal cord reducing muscle tone (but decreases sensation) - Must be followed by PT & OT - Cutting anterior root produces atrophy Baclofen is a GABA agonist that binds to B receptor to inhibit ca++ influx into presynaptic terminals to inhibit the release of excitatory neuotransmitters. Baclofen is lipophilic and doesn't cross the BBB. Intrathecal Baclofen can be used for the long term control of severe spasticity without significant central side effects at a dose less than 100 times the oral dose. Benefits: ITB reduces tone, spasms and pain resulting in improved function ADL's, Mobility, care giver burden, speech,sleep, bladder control, etc. ITB will allow reduction in mind altering spasticity medications, which will improve cognition. Symptoms: Fever Pruritus Rebound Spasticity Tachycardia Hyper/Hypotension Seizure Altered Mental Status Rebound Spasticity Myoclonus Symptoms Decreased tone Lethargy Unresponsive Respiratory Depression Hypothermia Hypotension Bradycardia Treatment Reduce rate of ITB Hold oral Baclofen Monitor Vital Signs Monitor O2 Provide airway support Stretching Positioning Seating Cryotherapy Biofeedback Inhibitive Casting Pool Therapy Orthotics Electrical Stimulation Neuro-developmental therapy Sensory integration therapy Patterning Conductive education Pressure point stimulation Practice specific, relevant and functional skills • Facilitation of normal movement patterns • Work for better active participation • Improve/maintain range of movement • Improve/maintain muscle strength and control • Improve/maintain postural alignment • Parent participation and education Patients should be assessed individually and treated age appropriately. APPROPRIATE MANAGEMENT • Importance of early referral and intervention • Anticipate progression/effects of condition POSTURAL MANAGEMENT PROGRAMME • 24 hours • Variation in environment, activity and intervention • Positively impacting on posture and function • Enhanced communication and participation • Transitioning through stages of life Positioner Wedge Standing frame Wheelchair (seating system) Immature skeletal and neuromuscular system Biomechanical alignment Considerations should be given to: Assistive device for play, feeding, relaxing and independence Stretching positions Sleeping positions Equipments varieties: 1. Wedges: Abductor W : prevent adduction deformities 2. Trumble form wedges & trumbles. 3. Large inflatable ball set 4.Crawlers: -platforms on wheels or wedges on wheels -A canavas sling under child” abdomen & supports on casters, straps to hold thighs in flexion. 5. Sitters Apparatus for supporting standing a) Prone or supine standers to encourage weight bearing & standing b) Standing frames adjusting correct alignment: -checked for height so that child does not grasp them w/ abnormal shoulder hunching , excessive elbow flexion & radial deviation of wrist. -supplied w/ strapping to correct flexed hip & knees -feet held at right angles by a board &/or foot place. c) Parallel bars d) Mirrors e) Stairs with bannisters: very in height. f) Rumps, uneven ground, various floor services for gait training. Walking aids Walkers Crutches Braces & Calipers: Knee gaiters (polyethylene knee moulds) to keep knee straight abduction parts to keep legs apart. Elbow gaiters which keep elbow straight for correct arm push & grasp of walkers. Advantages Bone density Decreased incidence of fractures Decreased incidence of hip dysplasia Increased bone growth Improved passive range of movement (maintaining neutral alignment) Influences tone Activation of anti-gravity muscles Improved lung function Improved bladder and bowel function Socialisation and interaction In physical therapy sessions, the therapist works with the child in supine and prone positions to improve head and trunk control. He supports the child in the sitting position to develop weight shifting and unilateral balance, ability to rotate the body and the ability to respond to sudden changes in position. The rehabilitation team strives for long-term functional mobility in a variety of environments so that the child will integrate into the community and social life in a healthy way. Bobath neurodevelopmental technique: This is the most commonly used therapy approach in CP worldwide. It aims to normalize muscle tone, inhibit abnormal primitive reflexes and stimulate normal movement. It uses the idea of reflex inhibitory positions to decrease spasticity and stimulation of key points of control to promote the development of advanced postural reactions. It is believed that through positioning and stimulation, a sense of normal movement will develop. An important part of treatment of the infant is teaching the mother how to position the child at home during feeding and other activities. The baby is held in the anti-spastic position to prevent formation of contractures. Sensory input to the CNS produces reflex motor output. The various neuro-facilitation techniques are based on this basic principle. All of the techniques aim to normalize muscle tone, to establish advanced postural reactions and to facilitate normal movement patterns. Vojta method of technique: Vojta established 18 points in the body for stimulation and used the positions of reflex crawling and reflex rolling. He proposed that placing the child in these positions and stimulation of the key points in the body would enhance CNS development. In this way, the child is presumed to learn normal movement patterns in place of abnormal motions. Positioning and stimulation techniques are different from NDT. Vojta stated that therapy should be applied by the primary caregiver at home at least 4 - 5 times daily and stopped after a year if there is no improvement Rood Method: Use of peripheral input of cutaneous sensory stimuli (brushing, tapping, icing, heating, pressure, ms. stretch, muscle contraction, joint approximation. or retraction) Various nerves & sensory receptors are described & classified into types ,location, effect, response, indication. Propioceptive Neuromuscular facilitation (Kabat & Knott) Use of such mechanisms as maximum resistance , quick stretch & spiral diagonal (mass) movements, sensory afferent stimuli (touch, pressure, traction,compression & visual) to facilitate normal mov . [special techniques: irradiation. stim. of reflexes,reversal(successive induction), relaxation.]. 4. Brunstrom Method ( hemiplegia): Produces motion by provoking primitive movement pattern or synergitic pattern as follows : -Reflex response used initially & later voluntary control -Control of head & trunk by stim. of TNR, tonic labrinythine R -Associated reaction : hyperextension of the thumb produces relaxation of finger flexors. Motor relearning program of Carr & Shepherd: functional training, practice, repitition, in the performance of tasks & carry over those motor skills into functional activities. 6. Forced use paradigm (= constraint - induced movements therapy CIMT): Non hemiplegic limb is restrained in a sling during 90% of waking hrs. to force the patient to use the hemiplegic limb. The minimum amount of motion in the paretic limb before being enrolled into CIMT protocol is 20 of wrist extension and 10 of extension of 2 fingers at MCP or IPJ. Conductive education: This approach, developed by professor Peto in Hungary depends on educational principles which become the core stone during treatment. A conductor is responsible to treat the child in integrated pattern in group therapy. Each task is divided into steps and learned to child one by one, using special rhythm of songs and verbal commands. Occupational therapy and play: Occupational therapy (OT) aims to improve hand and upper extremity function in the child through play and purposeful activity. There are defined systematic treatment methods for occupational therapy. Ayres sensory integration therapy aims to enhance the child’s ability to organize and integrate sensory information. In response to sensory feedback, CNS perception and execution functions may improve and the motor planning capacity of the child may increase. Bracing: Braces are devices which hold the extremities in a stable position. The goals of bracing are to increase function, prevent deformity, keep the joint in the functional position, stabilize the trunk and extremities, facilitate selective motor control and decrease spasticity. Lower extremity bracing: Orthoses are usually named according to the body parts they cover. Various kinds of ankle foot orthoses (AFOs) are the most common braces used in CP. Static braces immobilize the joint, while flexible ones use body weight to stretch the muscles of the leg and ankle. AFOs provide appropriate contact with the ground during stance and foot clearance during swing. Knee immobilizing splints and hip abduction splints are prescribed both for non-ambulatory and ambulatory children. Knee-ankle foot orthoses (KAFOs) work in children who use them. AFOs are not very useful as night splints because they do not prevent knee flexion. Orthopedic surgery is widely used in the management of children with CP to prevent or correct certain musculoskeletal problems such as muscle shortening and bone deformities. The goal of orthopedic surgery in a child with walking potential is to improve functional ambulation. For non-ambulatory children, the goal of orthopedic surgery is to facilitate sitting, improve hygiene, prevent pain and obtain plantigrade stable feet. Tenotomy Myotomy Osteotomy Fusion Tendon Transplant Tendon Lengthening Neurosurgical Procedures Neurectomy Myelotomy Rhizotomy Selective Dorsal Rhizotomy Chordotomy Implantable dural electric stimulator Intrathecal Baclofen Pump Spastic equinovarus foot: combination of: a. Achillis tendon lengthening ( equinus def. ) b. Split anterior tibial transfer: Splitting TA tendon medial half left attached to its origin lateral half tunneled into 3rd cuneiform & cuboid 2. Tight hip adductor: Adductor tenotomy or derotational osteotomy ( + surgical reduction ) 3. Scoliosis: surgical correction in ambulatory child w/ curvature > 45 & vital capacity < 35% A significant change in all the primary impairments is expected after surgery. There is a need for gentle return to function. Range of motion and strength has to be regained as early as possible after surgery. Mobilization should be started as soon as the child is comfortable and painless, usually on the second to fourth day after soft tissue procedures. Training with range of motion exercises starts and gradually progress to strengthening as healing allows. Keep in mind that a spastic muscle is also a weak muscle, so strengthen the muscles after muscle lengthening. The ultimate aim is to improve the ambulatory capacity. It usually takes approximately 3 months to regain the preoperative muscle strength after multi-level surgery. Immediate postoperative physical therapy re-introduces movement and the new alignment. The skills that the patient acquires are established in 3 - 6 months after surgery. Team: speech language specialist, OT, Dietary specialist. Items: Changes in posture & head position during feeding. Oral motor exercise for the tongue & lips to increase strength, ROM, velocity, percision. Use of thickened fluid & soft food in small bolus Use of alternative feeding routes e.g. nasogastric tube, gastrotomy or jejunostomy tubes with severe aspiration or caloric need. Team : speech -language pathologist & nurse Items : 1- oral option : electrolarynx 2 - non oral options : - simple hand writing - gestures - augmentative communication device (simple alphabet & picture board to sophosticated computer systems 3- treatment of hearing & visual problems Team: audiologist, speech therapist, OT Items: Cochlear implants (for profoundly deaf): to stimulate auditory nerve & provide awareness of sound Hearing aid : - Do not help purely central hearing loss. Used for ttt of profound sensorineural hearing loss in infancy & early childhood Training of postural reaction (large balls, rolls) Use of compensatory stimuli (auditory, tactile, vestibular, propioceptive) for:. -Training of motor function of child’s life e.g dressing, feeding, bathing, roll over, creeping, crawling (listen to sound, reach to sound, move to sound). -Training of body image movements enjoyment (hand to hand, hand to mouth, hand to body) Mother - child relationship ( kisses, touches, stroking, talking to the baby) is important. Use of vibrating toys, bells & playthings placed for his tummy legs & similar ideas. Language development: Important to talk & clearly label the body parts & to encourage the child’s language. Visual enhancement (illumination, magnification, altered contrast, glare reduction, expanders of visual field) Visual substitution: Recorded talking books, Computer w/ vebral output, Braille book. Elimination of air way secretion by manually assisted cough OR mechanical insufflator or exsufflator. Respiratory ms. aid by manual force (breathing ex) OR mechanical ventillatory assistance(hypoxia) Mouth intermittent positive pressure ventillation (IPPV) in late stages. Timed bladder emptying schedule Regulation of fluid intake. Use of diapers. Adequate cleaning of perineum Family education about transfer & dressing skill . REHAB. OF BOWEL PROBLEMS A timed toileting schedule for incontinence Use of dietary fibers, adequate fluid intake, stool softeners, supp., & enema for constipation . Team : occupational therapist Items : - provision of self help devices - training in activities of ADL - provision of creative interest - training in suitable work Team : psychiatrist + social specialist Items : - provision of recreational activities e.g.- special olympics, athletic competition - horse back riding programs (recreational & therapeutic ) - computers ( for schools & recreation