Chapter 7 Blood and Blood-Forming Organs Diseases and Disorders Copyright Copyright © 2010 © 2010 Delmar, Delmar, Cengage Cengage Learning. Learning. ALLALL RIGHTS RIGHTS RESERVED. RESERVED. Anatomy and Physiology • Hematologic system • Major functions of blood: – Transport nutrients to cells – Aid removal of wastes • Average adult has 5 to 6 liters of circulating blood Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Blood Components Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Erythrocytes – Normal count: • 4.2 to 6.3 million – Life span: • 120 days – Form in bone marrow and do not reproduce Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Hemoglobin important in oxygen transport • Normal hemoglobin: – Male • 13.5 to 18 hemoglobin in grams (gm)/100 milliliter (ml) – Female • 12 to 16 gm/100ml Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Leukocytes protect individual from infection – Normal count: • 4,500 to 11,000 Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Platelets – Also known as thrombocytes – Important in blood clotting – Normal count: • 150,000 to 350,000 Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Blood-forming organs: – – – – Lymph nodes Bone marrow Spleen Liver • Lymph system protects against pathogens Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Anatomy and Physiology • Bone marrow – Major blood cell producer • Spleen produces lymphocytes, plasma cells, and antibodies to filter microorganisms from blood • Liver produces prothrombin and fibrinogen for blood clotting Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Animation Click Here to Play Blood Animation Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Erythrocytopenia – Decrease in RBCs leading to anemia – Symptoms: • • • • • Fatigue Headache Low RBCs Pallor Shortness of breath Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Erythrocytosis – Increased RBCs – Symptoms: • • • • • High RBCs Reddened skin tones Bloodshot eyes Increased blood volume and pressure Increased blood volume of heart Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Leukocytopenia – Decreased white blood cells – Weakens immune system • Leukocytosis – Increased white blood cells – Normal response to acute infections Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Thrombocytopenia – Decreased platelet count leading to coagulation problem – Symptoms: • Petechiae – Small hemorrhages in skin • Ecchymoses – Large areas of bruising or hemorrhage Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Thrombocytopenia – Symptoms: • Epistaxis – Nosebleeds • Bleeding in mouth, gums, and mucous membranes Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Common Signs and Symptoms • Thrombocytosis – Increase in platelets – Uncommon – Usually no serious side effects Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Diagnostic Tests • Complete blood count with differential and indices • Biopsy of blood-forming organs • Hematocrit (Hct) reflects amount of red cell mass as proportion of whole blood • Hemoglobin (Hgb) reflects blood’s oxygencarrying potential Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Diagnostic Tests • Bleeding time determines platelet disorders – E.g., hemophilia, thrombocytopenia, disseminated intravascular coagulation • Prothrombin time (PT) and partial prothrombin time (PTT) measure blood’s ability to clot Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Diagnostic Tests • Biopsy – Bone marrow – Lymph node Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Anemia – Decrease in oxygen-carrying ability of RBC – Symptoms: • Pallor • Fatigue • Shortness of breath Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Anemia – Symptoms: • • • • Tachycardia Headache Irritability Syncope Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Iron deficiency anemia – Loss of iron or inadequate intake of iron – Causes: • Blood loss • Low dietary intake – Treatment: • Increase dietary intake of iron Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Folic acid deficiency anemia – Folic acid needed for maturation of RBCs – Causes: • Poor diet • Overcooking of vegetables • Over consumption of alcohol – Treatment: • Increase folic acid intake by eating green and yellow vegetables Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Pernicious anemia – Lack of intrinsic factor leading to inadequate absorption of vitamin B12 – Treatment: • Monthly injections of vitamin B12 for life Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Hemolytic anemia – Destruction of RBCs related to antibody-antigen reaction – Disorder of immune system leading to destruction of erythrocytes – Treatment: • Exchange transfusion and/or splenectomy Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Sickle cell anemia – Hereditary – Found in African American race – Abnormal sickle shape of erythrocyte • Does not allow cell to travel smoothly through vessels – Symptomatic treatment – No cure Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Aplastic anemia – Failure of bone marrow to produce blood components – Causes: • • • • Chemotherapy Radiation Viruses Toxins Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Aplastic anemia – Treatment: • Avoid causative agent • Bone marrow transplantation • Transfusions Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Polycythemia – Too many blood cells – Symptoms: • • • • Enlarged spleen Reddened mucous membranes Bloodshot eyes Deep red color on palms Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Red Blood Cells • Polycythemia – Treatment: • Donate blood at regular intervals to reduce blood volume Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Mononucleosis – Also known as kissing disease – Symptoms: • Fatigue • Sore throat • Swollen glands Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Mononucleosis – Diagnosis by increased monocytes in white blood cells (WBCs) – Treatment: • Rest • Analgesics • Throat gargles Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Leukemia – – – – Malignant neoplasm of blood-forming organs Abnormal production of immature leukocytes May be acute or chronic Acute forms affect children, progress rapidly, and may be fatal Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Leukemia – Chronic forms affect older adults, are often asymptomatic, and may not be fatal – Classified as: • Myelogenous – Affecting bone marrow • Lymphocytic – Affecting lymph nodes Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Leukemia – Diagnosis by bone marrow biopsy – Symptoms: • Fatigue • Headache • Sore throat Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Leukemia – Symptoms: • Dyspnea bleeding of mucous membranes of mouth and gastrointestinal (GI) system • Bone and joint pain • Enlargement of lymph nodes, liver, and spleen – Infections common Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Leukemia – Treatment: • Aggressive chemotherapy • Once in remission, bone marrow transplant to replace neoplastic tissue with normal tissue • Remission at 50 percent Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Hodgkin’s disease – Most common lymphoma – Symptoms: • Painless enlargement of lymph nodes in neck • Weight loss • Fever – Primarily affects young adults • Average age of 35 Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Hodgkin’s disease – Cause thought to be viral – Diagnosis by presence of Reed-Sternberg cell in lymphatic tissue – Treatment: • Radiation • Chemotherapy – If in remission for five years or more, complete cure possible Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Non-Hodgkin’s lymphoma (NHL) – Lymphomas lacking Reed-Sternberg cell – Symptoms: • Painless enlargement of lymph nodes of neck, axilla, and inguinal areas • Fever • Night sweats • Weight loss Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Multiple myeloma – Malignant neoplasm of plasma cells or B-lymphocytes – Increases with age • Peaks in 70s – Plasma cells multiply abnormally in bone marrow • Causes weakness • Leads to fractures and bone pain Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Multiple Myeloma Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of White Blood Cells • Multiple myeloma – Diagnosis by honeycombed bone pattern, hypercalcemia, Bence-Jones protein found in blood and urine, and bone marrow biopsy – Treatment: • Chemotherapy • Radiation • Not effective – Poor prognosis Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Hemophilia – X-linked hereditary bleeding disorder – Several types • Type A – Most common – Male children from asymptomatic mothers – Lack protein necessary for clot formation Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Hemophilia – Symptoms: • Epistaxis • Bruising • Prolonged bleeding – Diagnosis by blood test Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Hemophilia – Treatment: • • • • Prevention of injury Treat symptoms Blood transfusions Concentrated form of clotting protein – No cure Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Thrombocytopenia – Also known as thrombocytopenia purpura – Decrease in platelets leading to inability to normally clot blood – Symptoms: • Abnormal bleeding in skin, mucous membranes, and internal organs • Petechiae Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Thrombocytopenia – Symptoms: • • • • Ecchymoses GI hemorrhages Epistaxis Hematuria Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Thrombocytopenia – Diagnosis by platelet count and bleeding time – Treatment: • • • • Avoid tissue trauma to reduce bleeding Vitamin K Transfusions of platelets Splenectomy Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Disseminated intravascular coagulation (DIC) – Abnormal clotting followed by abnormal bleeding – Usually follows major trauma • E.g., complicated childbirth, surgery, tissue destruction, septicemia, snakebite, shock – Multiple clots in capillaries – Life-threatening Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • DIC – Symptoms: • • • • • Petechiae Ecchymosis Hematoma Hematuria GI bleeding Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • DIC – Symptoms: • Hematemesis • Blood in stool – Treatment: • Heparin • Platelets Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Rare diseases – Thalassemia • Primarily affects people of Mediterranean descent • Fragile, thin RBCs form defective hemoglobin Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Disorders of Platelets • Rare diseases – von Willebrand’s disease • • • • • Hereditary Congenital Deficiency in clotting factor and platelet function Also known as angiohemophilia Affects females and males Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED. Effects of Aging • Age-related changes in other systems (e.g., immune, digestive) leave older adults more susceptible to infections and nutritionally related blood disorders • Decreased iron • Poor nutrition Copyright © 2010 Delmar, Cengage Learning. ALL RIGHTS RESERVED.