Indications for Plasma Exchange
Indication
Code
Collagen
Vascular
1
2
3
4
Polymyositis
Polyarteritis nodosa
Scleroderma
Vasculitis
710.4
447.6
710.1
447.6
Dermatology
1
2
Pemphigus
Dermatomyositis
694.4
710.3
Hematology
1
2
3
4
5
6
7
8
9
10
11
12
13
Crisis CAPS
cGVHD
Cold Agglutinin Disease
Cryobulinemia
Cutaneous T Cell Lymphona
HELLP
Red Cell Alloimunization in Pregnancy
Hyperviscosity
Pure Red Cell Aplasia
Thrombocytosis
TTP
aHUS
Anti Factor 8 Antibodies
284.9
Metabolic
1
2
3
Hyperlipidemia
Hypertriglyceridemia
Pruritis (Liver Disease)
272.0
272.4
000.0
Neurology
1
2
3
4
5
6
7
8
9
10
11
12
13
14
ADEM
CIDP
Anti MAG Neuropathy
Eaton Lambert
Guillan Barre
MS Variant
Myasthenia Gravis
NMO
POEMS
Paraneoplastic Syndrome
Anti GAD Antibody(incl Stiff Person Syndrome)
Anti NMDA Antibody
Sydenham Chorea
Transverse Myelitis
1
2
3
Sickle Cell
Malaria
Babesiosis
Red Blood Cell
283.0
273.2
357.8
000.0
773.0
284.0
289.9
446.6
283.1
999.8
357.8
358.1
357.0
358.0
340.0
203.3
000.0
292.9
357.0
282.6
1
Renal
Transplant
1
2
3
4
5
6
7
8
9
ANCA Pulmonary Hemmorhage
ANCA Renal Limited
Anti GBM Pulmonary Hemmorhage
Anti GBM Renal Limited
FSGS Native Kidney
FSGS Transplanted Kidney
Henoch-Schoenlein Purpura
MPGN
RPGN (not ANCA)
287.0
1
2
3
4
5
6
7
996.83
996.82
996.84
10
Cardiac Acute Humoral Rejection
Liver ABO Incompatible transplant
Lung Acute Humoral rejection
Lung Transplant Desensitization
Pancreas Acute Humoral Rejection
Renal Acute Humoral Rejection
Renal Live Donor Desensitization ABO
Incompatible
Renal Live donor Desensitization HLA
Incompatible
Renal Live Donor Desensitization ABO/HLA
Incompatible
Renal Deceased Donor Desensitization
1
2
3
4
Autologous
Allogeneic
ABO Incompatible
DLI
8
9
Stem Cell
446.2
583.9
996.8
583.4
996.8
996.85
Simple Descriptors of Diseases
Indication
Collagen
Vascular
1
2
3
4
Polymyositis
Polyarteritis
nodosa
Scleroderma
Vasculitis
Description
Evidence of inflammation of blood vessels in the skin or other organs of patients who do
not have Systernic Lupus Erythematosuor P or C ANCA vasculitis or Wegeners
Granulomatosus (Granulomatosus Angitis) or microscopic polyangitis or Churg Strauss
Vasculitis. ICD Code 447.6
N.B. 2) Lupus (SLE)-Diagnosis of lupus or have ANA positivity with a elevated double
stranded DNA antibody and evidence of kidney involvement ICD Code 710.0
Dermatology
1
2
Pemphigus
Dermato-myositis
Hematology
1
Crisis CAPS
2
2
3
4
5
6
7
8
9
10
11
12
13
Metabolic
1
2
3
Neurology
1
2
3
4
5
6
7
8
9
10
11
12
13
14
Red Blood Cell
1
2
3
cGVHD
Cold Agglutinin
Disease
Cryo-bulinemia
Cutaneous T Cell
Lymphona
HELLP
Red Cell
Alloimuniz-ation
in Pregnancy
Hyper-viscosity
Pure Red Cell
Aplasia
Thrombo-cytosis
TTP
aHUS
Anti Factor 8
Antibodies
Hyperlipi-demia
Hypertriglyceridemia
Pruritis (Liver
Disease)
ADEM
CIDP
Anti MAG
Neuropathy
Eaton Lambert
Guillan Barre
MS Variant
Myasthenia
Gravis
NMO
POEMS
Paraneoplastic
Syndrome
Anti GAD
Antibody
(including Stiff
Person
Syndrome)
Anti NMDA
Antibody
Sydenham
Chorea
Transverse
Myelitis
Sickle Cell
Malaria
Babesiosis
3
Renal
1
ANCA Pulmonary
Hemmorhage
2
ANCA Renal
Limited
Anti GBM
Pulmonary
Hemmorhage
Anti GBM Renal
Limited
FSGS Native
Kidney
FSGS
Transplanted
Kidney
HenochSchoenlein
Purpura
3
4
5
6
7
Transplant
8
9
MPGN
RPGN (not
ANCA)
1
Cardiac Acute
Humoral
Rejection
Liver ABO
Incompatible
transplant
Lung Acute
Humoral rejection
Lung Transplant
Desensitiz-ation
Pancreas Acute
Humoral
Rejection
Renal Acute
Humoral
Rejection
Renal Live Donor
Desensitiz-ation
ABO
Incompatible
Renal Live donor
Desensiti-zation
HLA Incompatible
Renal Live Donor
Desensiti-zation
ABO/HLA
Incompatible
Renal Deceased
Donor Desensitization
2
3
4
5
6
7
8
9
10
Hypersenitivity Angilitis- Patients who have either C or P ANCA vasculitis or Wegeners or
granulomatous vasculitis or microscopic polyangilitis or Strauss vasculitis who often have
pulmonary hemorrhage kidney involvement plus or minus skin involvement and nerve
involvement ICD code 287.0
Goodpasture Syndrome- Patients who suffer from pulmonary hemorrhage and renal
failure and either have anti-glomerular basement membrane, antibodies on serology or
linear immunoe-Fluorescence on kidney biopsy. ICD code 446.2
Anti GBM Pulmomary Hemorrhage
FSGS Native Kidney
Focal Segmental Glomeruloscerosis–Patients in the immediate post renal transplant
period who develop a nephritic syndrome and on biopsy are known to have focal
glomerulscerosis. ICD Code 583.9
A systemic Vasculitis –Mostly seen in children in which they have joint pain, skin rash –
which is distal and symmetrical, renal and gut involvement
ICD code 996.8
Transplant rejection heart ICD code 996.83
Transplant rejection liver ICD code 996.82
Transplant rejection lung ICD code 996.84
Lung Transplant Desensitization
Pancreas Acute Humoral Rejection
Transplant rejection kidney ICD code 996.8
Pre-Transplant category- this is for preparation for patients who are pre-sensitized or
ABO incompatible and receive plasma exchange both pre and post live related renal
transportation. ICDcode 996.8
Renal Live Donor Desensitization HLA Incompatible
Renal Live Donor Desensitization ABO/HLA Incompatible
Renal Deceased Donor Desensitization
4
Stem Cell
1
2
3
4
Autologous
Allogeneic
ABO
Incompatible
DLI
5