IDIOPATHIC PULMONARY FIBROSIS: A NEW ERA Saturday, October 10, 2015 School of Nursing Auditorium School of Nursing University of Kansas Medical Center Kansas City, Kansas Sponsored by the Pulmonary Disease Department and University of Kansas Medical Center Continuing Education & Professional Development COURSE DIRECTOR: Mark Hamblin, MD, FCCP, Assistant Professor, University of Kansas Pulmonary Critical Care Division. Dr. Hamblin is Director of The KU Interstitial Lung Disease Center, which is one of 21 of the Pulmonary Fibrosis Foundation's National Care Network Centers, as well as The Director for The Rare Lung Disease Clinic that is part of the International Rare Lung Disease Consortium. Dr. Hamblin's research has focused on Idiopathic Pulmonary Fibrosis and educating residents on the detection and progression of this disease. OVERVIEW: There will be 5 speakers presenting at the conference. All are specialists in pulmonary fibrosis at either the University of Kansas Medical Center or Washington University, which are both designated Pulmonary Fibrosis Foundation Centers of Excellence. The speakers will develop the content based on evidence from the existing pulmonary fibrosis literature. The content will be reviewed by the directors of the pulmonary fibrosis centers prior to presentation to ensure the evidence based nature of the content. The course content will be built around a strategy to highlight our evolution of the understanding of pulmonary fibrosis. The initial lecture will focus on our current understanding of the natural history of pulmonary fibrosis in terms of symptom onset, progression, and change over time. It will highlight existing knowledge of environmental and genetic factors that play a role in disease development. It will also discuss co-morbid conditions that contribute to progression of the disease. It will conclude with an initial presentation of therapeutic options. The second lecture will provide a more in depth look at drug therapy focusing on nuances of the medications that might influence treatment decisions for an individual patient. The third lecture will focus on diagnostic nuances that could lead to an incorrect diagnosis and treatment algorithm. This lecture will highlight pitfalls in imaging acquisition, deficiencies in the lab evaluation, as well as the rational use of lung biopsy in the diagnostic process. The final didactic lecture will focus on autoimmune variants of the disease with a focus this year on the anti-synthetase syndrome, which is an often under-recognized phenomenon. The afternoon session will encompass small group discussion of various case presentations that exemplify real world challenges in the diagnosis and treatment of pulmonary fibrosis. Specific educational points that will be highlighted includes optimal work-up for chronic cough, the role of HRCT, and the importance of appropriate techniques to elicit diagnostic information that could impact treatment decisions. There will be a focus on drug therapy and management of adverse effects. Attendees will also be encouraged to submit their own challenging cases for review and discussion. There will be a concurrent afternoon session that will focus on patients and care givers. This will include lectures in a more informal interactive format that will focus on the natural history of the disease, and co-morbid conditions. There will also be a discussion of oxygen, and options for patients. It will conclude with a discussion of current and future therapeutic options. TARGET AUDIENCE: This symposium is designed for pulmonologists, lung radiologists, internal medicine and family physicians as well as nurse practitioners, nurses and other health professionals. OBJECTIVES: At the completion of this symposium participants should be able to: 1. Know how to order an HRCT for the most complete diagnostic information. 2. Describe the criteria for HRCT classification of definite, possible, inconsistent UIP patterns. 3. Explain the disease states that could be encompassed by the inconsistent UIP pattern and differences in treatment strategy. 4. List the indications for drug therapy for IPF. 5. Examine the contraindications to individual therapies for individual patients. 6. Cite the important co-morbid conditions that should be addressed in the work-up of IPF. 7. Describe the diagnostic work-up for the Anti-synthetase syndrome. 8. Identify key lab abnormalities that will affect treatment decisions for the Anti-synthetase syndrome. 9. Discuss the nuances of lung pathology in UIP that might suggest an alternative diagnostic etiology than IPF. PLANNING COMMITTEE: Mark Hamblin, MD, FCCP, Assistant Professor, Pulmonary Disease, University of Kansas Medical Center, Kansas City, Kan. Kristin Simpson, RN, BSN, University of Kansas Medical Center, Kansas City, Kan. Marla Sutton, MS, Senior Program Manager, Office of Continuing Education and Professional Development , University of KS Medical Center, Kansas City, Kan. Terri Schmitz, BSN, RN, Senior Coordinator, University of Kansas Medical Center Area Health Education Center, University of KS Medical Center, Kansas City, Kan. ACCREDITATION: All participants are required to sign attendance rosters at the beginning of each day. A certificate of completion will be provided to all activity participants based on completion of the program evaluation, documentation of actual attendance time, meeting minimum attendance requirements specific to the activity, and payment in full. If you are not paid in full, a link to complete evaluation and get your certificate will be emailed to you upon receipt of payment. Physicians: The University of Kansas Medical Center Office of Continuing Medical Education & Professional Development is accredited by the Accreditation Council for Continuing Medical Education to provide continuing medical education for physicians. The KU Medical Center Office of Continuing Medical Education designates this live activity for a maximum of 8 AMA PRA Category 1 Credits TM. Physicians should claim only the credit commensurate with the extent of their participation in the activity. Nurses: Up to 8 contact hours will be awarded to all individuals based on documentation of actual attendance time, meeting minimum attendance requirements specific to the activity, and payment in full. ACKNOWLEDGEMENTS: This symposium is supported in part by an educational grant from Boehringer -Ingelheim. EXHIBITS: Commercial vendors are invited to exhibit at this meeting. Limited exhibit space will be available. Call Suzy Williams at 913-588-4488 or e-mail swilliams16@kumc.edu for an application or more information. FACULTY: Mark Hamblin, MD, FCCP University of Kansas Medical Center, Kansas City, KS Lucas Pitts, MD, FCCP; University of Kansas Medical Center, Kansas City, KS Tonya Russell, MD, FCCP; Barnes-Jewish Hospital/Washington University, St. Louis, MO Adrian Shifren, MD, FCCP; Barnes-Jewish Hospital/Washington, St. Louis, MO Mark L Wencel, MD, FCCP; Via Christi Clinic, University of Kansas Medical Center-Wichita, Wichita, KS AGENDA: Session I 8:00 a.m. Welcome & Introduction Mark Hamblin, MD, FCCP; University of Kansas Medical Center University 8:15 a.m. Overview of Idiopathic Pulmonary Fibrosis Tonya Russell, MD, FCCP; Barnes-Jewish Hospital/Washington University 9:15 a.m. Diagnostic Nuances – Imaging, Pathology, and Treatment Mark Hamblin, MD, FCCP; University of Kansas Medical Center 10:15 a.m. Break 10:30 a.m. Esbriet, OFEV, and the Future of Pulmonary Fibrosis Therapy Adrian Shifren, MD, FCCP; Barnes-Jewish Hospital/Washington 11:30 a.m. Autoimmune-ILD: Focus on the Anti-Synthetase Syndrome Lucas Pitts, MD, FCCP; University of Kansas Medical Center 12:30 p.m. Break for Lunch Session II Clinical Case Reviews/Multidisciplinary Group Case Review 1:15 p.m. Clinical Case Review 4:00 p.m. Expert Panel Question and Answer 4:30 p.m. Adjourn Session III Patient and Care-Giver Session 1:15 p.m. Understanding Pulmonary Fibrosis - Diagnostic Nuances and the Impact on Treatment and Survival Mark L Wencel, MD, FCCP; Via Christi Clinic, University of Kansas Medical Center-Wichita 2:15 p.m. Understanding Your Oxygen Rights Mark Hamblin, MD, FCCP; University of Kansas Medical Center 3:15 p.m. Esbriet, OFEV, and the Future of Pulmonary Fibrosis Therapy Adrian Shifren, MD, FCCP; Barnes-Jewish Hospital/Washington 4:15 p.m. Expert Panel Question and Answer 4:30 p.m. Adjourn REGISTRATION AND FEES: Payment is required at the time of registration. Only registrations accompanied with payment will be accepted. Please register in advance. Fees include course materials, continental breakfast, lunch, refreshments and continuing education credit. Physician $50.00 KU Physician $40.00 Nurse $40.00 KU Nurse $30.00 Other Health Professional $25.00 PRIVACY POLICY: KU Continuing Education does not share, sell, or rent its mailing lists. You have our assurance that any information you provide will be held in confidence by KU Continuing Education. We occasionally use mailing lists that we have leased. If you receive unwanted communication from KUCE, it is because your name appears on a list we have acquired from another source. In this case, please accept our apologies. 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