Tetanus Method of: Ramesh K. Khurana, MD, FAAN James P. Richardson, MD, MPH Tetanus, one of the oldest and most preventable afflictions of humankind, results from infection by the anaerobic gram-positive organism Clostridium tetani. Tetanospasmin, the neurotoxin produced by the organism, blocks spinal and brainstem inhibitory pathways, leading to localized or generalized muscle spasms. It often presents itself as the increased tone of the masseter muscles, or trismus— hence the former name lockjaw. Etiology The causative organism of tetanus, C. tetani, exists as spores that are resistant to boiling for 20 minutes and to disinfectants, and, hence, it is nearly ubiquitous. Spores have been found in animal and human feces, as well as soil, dust, human dwellings, and hospitals. Vegetative cells, however, are susceptible to heat, antiseptics, and several antibiotics. Epidemiology Tetanus is a rare disease in the United States, with an annual incidence of approximately 0.02 per 100,000 people. Less than 50 cases are reported to the Centers for Disease Control and Prevention (CDC) each year. However, many cases of tetanus probably go unreported. In recent cases reported to the CDC, 55% of the patients were 20 to 59 years old; 36% were 60 years old and older. There is a slightly higher incidence of tetanus in men, older adults, recent immigrants, and parenteral drug users. Serologic surveys document lower levels of protective antibody levels in older adults, women, Hispanic Americans, and those with lower incomes and educational levels. Untreated, tetanus is usually fatal. Even with treatment, the overall case-fatality rate is greater than 10%, increasing with age to 40% in those older than 60 years in the most recent report from the CDC. It is well worth noting, however, that in the United States since 1989, no deaths have occurred in individuals with current tetanus immunization. The disease is much more common worldwide because of lower levels of immunization. The World Health Organization (WHO) estimates that in the year 2000, 309,000 people died of tetanus, including 200,000 neonates. Pathogenesis Tetanus spores gain entrance to the body through skin injuries. These injuries are often so minor that they do not result in any medical attention (e.g., a prick from a thorn bush or a minor puncture wound). Because C. tetani is an obligate anaerobe, the spores will grow only in areas of low oxygen tension, such as occurs with pressure sores, puncture wounds, or gangrene. Reports of tetanus following abortion, animal bites and stings, splinters, and body piercing are documented. The portal of entry in the newborn is usually through the contaminated umbilical stump. Growing or vegetative C. tetani organisms produce tetanospasmin, one of the most potent neurotoxins known, which reaches the nervous system via two routes: blood-borne delivery to peripheral nerves and retrograde intraneuronal transport. The toxin exerts its effects on the peripheral nerves, neuromuscular junction, muscle, spinal cord, brainstem, and possibly the hypothalamus. Tetanospasmin is recognized by high-affinity receptors located on the surface of the peripheral nerve endings, is internalized and retrogradely transported to the neurons in the spinal cord and brainstem. The toxin then migrates transsynaptically to presynaptic terminals and blocks the release of the inhibitory neurotransmitters gamma-aminobutyric acid (GABA) and glycine. Loss of inhibition affects the alpha motor neurons and preganglionic sympathetic neurons, producing muscle spasms and autonomic hyperactivity, respectively. Recovery involves synthesis of new presynaptic components and their transport to the distal axons. Clinical Presentation The incubation period of tetanus is usually from 3 days to 3 weeks, but tetanus can occur several months after an injury. Cases with shorter incubation periods and rapid generalization of spasms tend to be the most severe. There are three clinical forms of tetanus based on the site of toxin action and the age of the patient: generalized, localized, and neonatal. Generalized disease is the most common of the forms ( Box 1 ). Typical presenting complaints include trismus, neck rigidity, stiffness, dysphagia, restlessness, and reflex spasms. Tetanus patients may display risus sardonicus (a characteristic grimace manifested as raised eyebrows and a wrinkled forehead with the corners of the mouth pulled up). Muscle rigidity usually starts with the jaw and facial muscles and then spreads to the trunk (opisthotonos) and extensor muscles of the limbs. Hands and feet are relatively spared. Spasms may occur spontaneously or may be provoked by external stimuli such as noise, touch, lights, and parenteral injections. Tetanic spasms differ from grand mal seizures in that patients with tetanic spasms remain conscious. These spasms affect agonist and antagonist muscle groups together and are extremely painful. Violent paroxysms of generalized spasms may result in fractures, muscle rupture and rhabdomyolysis, and laryngospasm and apnea, both of which preclude ventilation and feeding. BOX 1 Presentation of Tetanus Generalized Disease Trismus Risus sardonicus Dysphagia Opisthotonos Isolated cranial nerve palsies Rigidity or stiffness in an extremity Neck stiffness Restlessness Tetanic seizures Poor sucking (newborns) Localized Disease Rigidity or stiffness in an extremity Cephalic Disease Single or multiple cranial nerve palsies Autonomic dysfunction usually complicates severe cases, occurring some days after spasms. This dysfunction may be one of overactivity or underactivity of the sympathetic and parasympathetic nervous systems. Sympathetic disturbances may manifest as labile or sustained hypertension, tachycardia, dysrhythmia, peripheral vasoconstriction, profuse sweating, glycosuria, and elevated plasma and urinary catecholamines. Parasympathetic manifestations include profuse salivation, increased bronchial secretions, gastric stasis, and ileus. Hypotension, bradycardia, and cardiac arrest may occur. Two less common types of tetanus are localized tetanus and cephalic tetanus. Localized tetanus is characterized by painful spasms of muscles near the site of injury. This disorder is usually self-limiting and lasts less than 2 weeks, but progression to generalized disease can occur if untreated. Cephalic tetanus is a frequently severe form of localized tetanus. The bacillus enters through minor head trauma or chronic otitis media. Cephalic tetanus may present as single or multiple, often unilateral, cranial nerve palsies before the development of trismus, dysphagia, dysarthria, head tilt, and possible generalization. Neonatal tetanus presents as an inability to suck and irritability 3 to 10 days after birth. It is usually a generalized form characterized by muscle rigidity, opisthotonos, apnea, and cyanosis. Diagnosis Tetanus is a clinical diagnosis; there is no specific confirmatory laboratory test. A history of a predisposing injury in an inadequately immunized host is helpful. As noted earlier, however, a history of injury is not always present. A well-documented history of primary immunization and a booster immunization within the last 10 years makes the diagnosis of tetanus less likely. The diagnosis is based on the observation of characteristic clinical features. Apte and colleagues, in administering a spatula test to diagnose tetanus, observed that 94% of 359 patients with tetanus involuntarily bit the spatula because of the reflex spasm of masseter muscles, instead of gagging and expelling it. Absence of sensory deficits and a clear sensorium supports the diagnosis of tetanus. Laboratory tests such as complete blood counts and routine blood chemistry tests are not helpful. Creatine kinase may be elevated. Cultures are positive in only 32% to 50% of patients, and, in any event, treatment cannot wait for their completion. Tetanus antitoxin antibody levels are not usually available quickly and are not reliable after the administration of human tetanus immune globulin (HTIG). Electromyography of the involved muscles, or the masseter muscle, shows continuous motor unit discharge. Laboratory tests can, however, be useful in excluding other conditions. For example, a urine screen may be positive in cases of strychnine poisoning. CURRENT DIAGNOSIS ▪ The diagnosis is clinical; laboratory tests are not helpful, except in eliminating other diagnoses. ▪ A history of adequate tetanus immunization makes the diagnosis much less likely. ▪ Involuntary biting of a spatula because of masseter muscle spasm is highly suggestive. ▪ Generalized disease is the most common form of tetanus and may present as trismus, neck rigidity, stiffness, dysphagia, restlessness, reflex spasms, and risus sardonicus. Established generalized tetanus is easily recognized, whereas the diagnosis of cephalic tetanus can pose some difficulty. Cranial nerve involvement is common and may confuse the physician. Trismus may result from intraoral disease or an acute dystonic reaction to phenothiazines or metoclopramide (Reglan). Muscular stiffness can also be a manifestation of strychnine poisoning, meningitis, hepatic encephalopathy, rabies, hypocalcemic tetani, stiff-man syndrome, and conversion reaction. A delay in the diagnosis of tetanus has occurred in patients presenting with dysphagia. Rigid abdominal muscles may simulate an acute abdomen. Treatment Whenever possible, patients with suspected tetanus should be transferred to a facility that has experience with this disease. Patients should be kept in a quiet and dark environment to minimize sensory stimulation. Treatment has the following goals: • Neutralization of the circulating toxin that has not yet entered the nervous system • Elimination of the source of the toxin by careful surgical débridement and by antibiotic administration to inhibit growth of the bacilli • Prevention of respiratory and metabolic complications • Prevention of muscle spasms • Management of cardiovascular complications caused by autonomic instability Tetanus antitoxin should be given to prevent further fixation of the toxin to the central nervous system, although it will not reduce manifestations already present. Between 3000 and 6000 units of HTIG (or Hyper-Tet) should be given intramuscularly as soon as possible and definitely before manipulating the wound. Some authorities recommend giving some of the HTIG near the site of the wound. Tetanus does not confer immunity. Therefore, active immunization with tetanus and diphtheria toxoid (Td) or diphtheria toxoid–pertussis vaccine–tetanus toxoid (DPT) or DTaP, as appropriate, also should be given, at a site contralateral from that for tetanus immune globulin (TIG) ( Table 1 ). TABLE 1 -- Routine Diphtheria and Tetanus Immunization Schedule for Persons 7 Years of Age and Older Dose Age/Interval Product Primary 1 First dose Td Primary 2 4–8 weeks after the first dose[*] Td Primary 3 6–12 months after second dose[*] Td Boosters Every 10 years after last dose Td From Immunization Practices Advisory Committee: Diphtheria, tetanus, and pertussis: Recommendations for vaccine use and other preventive measures-recommendations of the Immunization Practices Advisory Committee (ACIP). MMWR 1991;40(No. RR-10). Abbreviation: Td = tetanus and diphtheria toxoid. * Prolonging the interval does not require restarting series. CURRENT THERAPY ▪ Tetanus antitoxin[2] and/or human tetanus immune globulin (BayTet) should be given immediately, followed by débridement and appropriate antibiotic therapy (e.g., metronidazole [Flagyl]). ▪ Tetanus immunization with tetanus and diphtheria toxoid (Td) should also be given. ▪ Tetanic spasms should be controlled with benzodiazepines. ▪ Fentanyl (Sublimaze)[1] may help control autonomic cardiovascular instability (manifested as hypertension and tachycardia) by attenuating the sympathetic efferent discharge. ▪ Supportive care includes protection of the airway, management of fluids and electrolyte balance, nutrition, bowel and bladder functions, skin care, deep venous thrombosis prophylaxis, and physiotherapy. 2 Not available in the United States. 1 Not FDA approved for this indication. Débridement is important for several reasons. It removes live organisms, creates an aerobic environment unfavorable for further growth, and secures specimens for culture. Débridement should be delayed until several hours after the administration of antitoxin because tetanospasmin may be released into the bloodstream. Antibiotic therapy is essential to sterilize the wound and eradicate the bacilli in their vegetative form. The antibiotic of choice is metronidazole (Flagyl), given at a dose of 7.5 mg per kg every 6 hours up to a maximum of 500 mg. Acceptable alternatives are doxycycline (Vibramycin) and imipenem cilastatin (Primaxin).[1] Penicillin, once the drug of choice, should not be used because it acts as a competitive antagonist to GABA and promotes hyperexcitability and convulsions. Oxygenation is ensured by protecting the airway. In all but the mildest of cases, prophylactic intubation should be initiated early. Intubation will usually require sedation with a benzodiazepine (e.g., lorazepam [Ativan],[1] 2 mg intravenously) and neuromuscular blockade (e.g., vecuronium [Norcuron], 0.08 to 0.1 mg per kg). Patients in whom orotracheal intubation precipitates laryngeal spasms, require more than 10 days of intubation, or have generalized seizures should undergo elective tracheostomy. An oropharyngeal airway will allow removal of secretions and prevent biting in mild cases that do not require intubation. Control of tetanic spasms and rigidity is best achieved with the benzodiazepines. Additional benefits are that these drugs produce sedation and amnesia. Diazepam (Valium)[1] can be given at a large dose of 0.5 mg per kg to 15 mg per kg per day[3] intravenously. Alternatively, continuous infusions of lorazepam (Ativan) at a dose of 0.1 to 2.0 mg per kg per hour,[3] midazolam (Versed)[1] at a dose of 0.01 to 0.10 mg per kg per hour, or propofol (Diprivan)[1] at a dose of 3.5 to 4.5 mg/kg per hour can be given. The intrathecal administration of baclofen (Lioresal)[1] has been found useful, but it is both costly and invasive. In patients whose muscle spasms do not respond to sedation, neuromuscular blocking agents, such as vecuronium (Norcuron),[1] are often necessary. The patients will require assisted ventilation, often for several days or weeks. Because neuromuscular agents prevent skeletal muscle movements only and do not reduce pain or provide sedation, it is essential that patients be monitored very closely for adequate pain relief. Later in the course of the disease, autonomic cardiovascular instability may develop. Both morphine[1] and fentanyl (Sublimaze)[1] may control hypertension and tachycardia by attenuating the sympathetic efferent discharge. Fentanyl (Sublimaze)[1] is considered superior because it does not depress myocardium. Previously used agents phentolamine (Regitine) and metoprolol (Lopressor) for treatment of hypertension and tachycardia are no longer recommended. Hypotension induced by phentolamine may be difficult to reverse, and β-adrenergic blockers may contribute to cardiac failure and high mortality. Hypotension may require monitoring of cardiac output and intravenous fluids or pressor agents. Bradycardia may develop, requiring placement of a pacemaker. 3 Exceeds dosage recommended by the manufacturer. Complications Supportive care is critical to the prevention of complications. It includes management of fluids and electrolyte balance, nutrition, bowel and bladder functions, skin care, and physiotherapy. Most of the complications are those that are common to immobile patients. Frequent turning of the patient will prevent pressure sores. Low-dose heparin or enoxaparin (Lovenox) should be administered to prevent deep venous thrombosis and formation of pulmonary emboli. Physical therapy should be given as soon as possible to prevent contractures. Orthopedic management may be required for fractures and dislocations resulting from tetanic seizures. Prognosis The severity of illness, age of the patient, and the facilities available are the most important factors determining prognosis. In the developing world where mechanical ventilation is unavailable, asphyxia is the most common cause of death. Those who survive the acute phase may succumb to autonomic dysfunction. With expanding facilities for intensive care, most patients eventually make a full recovery over 4 to 6 weeks, but some patients remain hypertonic; some patients remain amnestic for the event, whereas others have unpleasant memories of painful tetanic spasms, physiotherapy to the chest, and tracheal suction. Tracheal stenosis as a sequel to prolonged intubation and tracheostomy is common. It is important that recovering patients complete a primary series of immunizations because having had the disease does not confer immunity ( Table 2 ). TABLE 2 -- Guide to Tetanus Prophylaxis in Routine Wound Management History of Adsorbed Tetanus Toxoid Clean, Minor All Other (doses) Wounds Wounds[*] Td[†] TIG[†] Td[†] TIG[†] Unknown or <Three Yes No Yes Yes ≥Three[‡] No[§] No No[II] No From Immunization Practices Advisory Committee: Diphtheria, tetanus, and pertussis: Recommendations for vaccine use and other preventive measures—recommendations of the Immunization Practices Advisory Committee (ACIP). MMWR 1991;40(No. RR-10). Abbreviations: DT = pediatric diphtheria and tetanus toxoid; DTaP = diphtheria and tetanus toxoid and acellular pertussis vaccine; DTP = diphtheria and tetanus toxoid and whole-cell pertussis vaccine; Td = tetanus and diphtheria toxoid; TIG = tetanus immune globulin; TT = tetanus toxoid. * Such as, but not limited to, wounds contaminated from dirt, feces, soil, saliva; puncture wounds; avulsions; and wounds resulting from missiles, crushing, burns, or frostbite. † For children under 7 years old, DTaP, DTP, or DT if pertussis vaccine is contraindicated is preferred to TT alone. For persons 7 years of age and older, Td is preferred to TT alone. ‡ If only three doses of fluid toxoid have been received, a fourth dose of toxoid, preferably an adsorbed dose, should be given. § Yes, if more than 10 years since last dose. II Yes, if more than 5 years since last dose. (More frequent boosters are not needed and can accentuate side effects.) Prevention Prevention of tetanus through immunization is the key to the elimination of tetanus. It is useful to distinguish between primary and booster immunization. A patient 7 years old or older who has never been immunized requires two additional doses of Td beyond that given when the wound is treated (see Table 2 ). Wounded patients who have never been immunized may require HTIG (see Table 1 ). The elderly are particularly susceptible if they have never been immunized or if their immunity has lapsed. The American Academy of Pediatrics now recommends that adolescents 11 to 18 years of age receive a single dose of Tdap (tetanus toxid, reduced diphtheria toxid, acellular pertussis vaccine) for booster immunization to prevent pertussis (in addition to tetanus and diphtheria) in this population. Those adolescents who have received Td but not Tdap should receive a single dose of Tdap after a suggested interval of at least 5 years to reduce the risk of adverse reactions. Physicians should use a case-finding approach to increase tetanus immunization rates. System changes (such as clinical pathways that allow immunization without a physician's order) are the most effective means of increasing immunization rates. Reminders placed at physicians' desks or computer-generated reminders attached to charts or patients' bills have also increased immunization rates. Td should be given whenever tetanus immunization is necessary to ensure immunity to diphtheria as well as to tetanus. Td is a safe vaccine. Adverse reactions consist primarily of local edema, tenderness, and fever. Anaphylactoid reactions are rare. Most adverse reactions occur in persons with evidence of hyperimmunization. The only contraindications of Td are a history of a neurologic sequela or a severe hypersensitivity reaction following a previous dose. To reduce neonatal tetanus and protect the mother, pregnant women who are due for a booster should receive Td, preferably during the last two trimesters. HTIG should be given to pregnant women only when clearly indicated. The WHO recommends that women attending prenatal clinics in developing countries be given two doses: • During the first pregnancy • In the third trimester at least 4 weeks before delivery These should be followed by one dose in each subsequent pregnancy, up to a total of five doses. Needless to say, promoting clean delivery and hygienic cord care practices constitutes a key element in the prevention of neonatal tetanus. Copyright © 2007 Elsevier Inc. All rights reserved. - www.mdconsult.com Bookmark URL: /das/book/0/view/1444/81.html