16870 W. Bernardo Drive, Suite 390 San Diego, CA 92127 Phone: 858-618-1400 Facsimile: 858-618-1441 www.aegisthera.com “Increasing transmucosal absorption and improving protein therapeutic viability with alkylsaccharides” BIOCOM – February 13, 2013 Edward T. Maggio, PhD CEO, Aegis Therapeutics © 2013 Aegis © 2013 Aegis Therapeutics, Therapeutics LLCLLC Aegis’ Company Background Located in San Diego We out-license advanced intranasal & transmucosal delivery and stabilization technologies for therapeutic proteins, peptides, and small molecule drugs (Aegis’ Intravail® & ProTek® technologies) Patented technology from the UAB medical school exclusive license; additional patents recently issued and pending worldwide Multiple product-specific licenses issued to date: ~30 research licenses for ~34 API’s; 8 full commercialization licenses with more conversions in negotiations © 2013 Aegis Therapeutics LLC 2 Intravail®/ProTek® Technologies - Based on Alkylsaccharides (sugar + alkyl chain - various linkages) Typical oligosaccharides: maltose maltotriose maltotetraose sucrose trehalose O sucrose trehalulose COCH2 H3C turanose (CH2) nn O maltulose leucrose OH palatinose isomaltose OH maltitol OH CH2OH CH2OH O O OH OH OH HOCH2 O OH CH2OH OH Typical alkyl chain lengths: 10-18 carbons © 2013 Aegis Therapeutics LLC CH3 (CH2) nn O OH O O OH Typical linkages: glycosidic thioglycosidic amide linkage ureide ester 3 Multiple Modes of Transmucosal Delivery for Macromolecular Drugs Nasal Metered spray pumps Oral (gastrointestinal) Gelcaps Tablets Oral cavity (buccal, sublingual) Flash dissolve Edible films © 2013 Aegis Therapeutics LLC 4 5 Intravail® Opens Tight Junctions Paracellular Absorption Demonstrated by Reduction in TEER* (Normal Human Tracheal/Bronchial Epithelial Cell Derived Mucociliary Tissue) Intravail® Excipients % TEER Decrease 120 100 80 Non-Intravail® Alkylsaccharides 60 40 20 0 PB S Ty pe A, 0. Ty 1% pe A, 0. Ty 2% pe B, 0. Ty 1% pe B, 0. 2% Ty pe C, 0. Ty 1% pe C, No 0. n2% In tr. X ,0 No .1 n% In tr. X, No 0. n2% In tr. Y, No 0. n1% In tr. Y, 0. 2% 0.1% 0.2% 0.1% 0.2% 0.1% 0.2% 0.1% 0.2% 0.1% 0.2% PBS C14M C12M C12S C8G C7G *Adapted from: Chen,S.-C., Eiting,K.T.,Li, A.A.W., Lamharzi, N. and Quay, S.C. (2005), 45th American Society for Cell Biology Meeting, December 10-14, 2005, San Francisco (late abstract) Peptide Drug Permeation Enhancement By Select Classes of Lipids Key: M≡Maltoside, S ≡ Sucrose ester, G ≡ Glucoside © 2013 Aegis Therapeutics LLC *1h. exposure 6 Intravail® Induces Transcytosis in Nasal Epithelium (Transmission Electron Microscopy) Without Intravail® Enhancer With Intravail®-TDM Enhancer v cc gc n n (cc) ciliated cell (n) Nucleus (gc) goblet cell (v) vesicle © 2013 Aegis Therapeutics LLC gc cc Rat Nasal Epithelium Magnification 3500X Intravail® Enhances Nasal Epithelium Absorption of FITC-Insulin (Fluorescence Light Microscopy) Without Intravail® Enhancer With Intravail®-TDM Enhancer Rat Nasal Epithelium Magnification 40X © 2013 Aegis Therapeutics LLC 7 Reversible Effect of Intravail®-TDM Enhancer on Nasal Mucosa Rat Model Data Somatropin 350 300 0 minutes 60 minutes 120 minutes 250 200 150 100 50 0 0 40 80 Time (minutes) © 2013 Aegis Therapeutics LLC 120 Serum Somatropin (ng/mL) Plasma Calcitonin (pg/mL) Calcitonin 50 40 30 20 10 0 0 20 40 60 80 100120 Time (minutes) 8 Intravail® Provides Intranasal Bioavailability Comparable to Injection OB-3 ~1kDa B/A=363% Diazepam 0.28kDa B/A=96% © 2013 Aegis Therapeutics LLC 9 Relatively Tight CV’s Upon Nasal Administration Insulin Courtesy of Drs. E. Meezan and D. Pillion, Univ. Alabama, School of Medicine, Birmingham © 2013 Aegis Therapeutics LLC 10 Intravail® Speeds Onset of Action 11 Cuts Tmax in half vs. s.c. injection Tmax (Average Minutes) 70 60 50 40 30 20 10 0.060% 0.125% 0.250% 0.500% Intravail™ DoseConcentration Intravail®-TDM Calcitonin Insulin © 2013 Aegis Therapeutics LLC Leptin SubQ Somatropin (HGH) 3-Way Human Crossover Study — Increases Calcitonin Bioavailability >5-fold Intravail® Mean Plasma Drug Concentration vs. S.C. Injection in 10 Healthy Females 60 Average Intravail® bioavailability ~37% 50 Concentration Plasma Calcitonin ng/mL No Intravail® control ~ 6.6% 40 30 20 10 Time (hrs) Injection © 2013 Aegis Therapeutics LLC Nasal-No Intravail Nasal + Intravail 4 3.75 3.5 3.25 3 2.75 2.5 2.25 2 1.75 1.5 1.25 1 0.75 0.5 0.25 0 0 12 2-Way Human Crossover - Intravail® Speeds Sumatriptan Bioavailability by ~20X Meanblood ± S.D.levels Plasma Profilesat for2Intravail® Nasal Spray Equivalent achieved to 3 min. Sumatriptan vs. 60 min. for current spray (Tmax reduced from 60 min. down to 8 min.) 70 60 Concentration (ng/ml) 50 40 Control Reference Test Article A Formulation Drug, No Intravail® 30 Drug + Intravail® 20 10 0 0 1 2 3 4 5 6 7 8 9 10 11 12 13 14 15 16 17 18 19 20 21 22 23 24 Time (hr) post-dose US Pat. 8,268,791 © 2013 Aegis Therapeutics LLC 13 Intravail® Nasal Diazepam Provides Superior PK Compared to Diastat® Rectal Gel Intravail® Nasal Diazepam (Licensed by Neurelis Therapeutics, San Diego, CA) Bioavailability 96% vs. i.v. injection (vs. Diastat ~90%) Tmax 1.5 hr (same as Diastat rectal gel) Cmax 272 ng/mL (Diastat rectal gel ~262ng/mL) Greater convenience/patient acceptance Source: Neurelis Therapeutics, Phase I Study © 2013 Aegis Therapeutics LLC 14 Multiple Modes of Transmucosal Delivery for Macromolecular Drugs Nasal Metered spray pumps Oral (gastrointestinal) Gelcaps Tablets Oral cavity (buccal, sublingual) Flash dissolve Edible films © 2013 Aegis Therapeutics LLC 15 Oral Octreotide with Intravail® Provides 4-fold higher Bioavailability vs. S.C. Injection Uptake of 30ug Octreotide in PBS s.c. 16 Oral Uptake of 30ug Octreotide in Intravail® 7 60 A B 6 311.63 50 5 Octreotide acetate (ng/ml) Octreotide acetate (ng/ml) AUC (ng/ml/min) 4 3 AUC (ng/ml/min) 1254.08 AUC1 AUC2 353.03 901.04 40 30 20 2 1 2 10 1 1 0 0 0 10 20 30 40 50 60 70 80 90 100 110 120 Ti m e ( m i nut e s) Regulatory Peptides 167 (2011) 233–238 © 2013 Aegis Therapeutics LLC 130 140 150 160 170 180 190 0 10 20 30 40 50 60 70 80 90 100 110 120 130 140 150 160 170 180 190 Time (minutes) Oral Delivery of [D-leu-4]OB3 Anti-Obesity Peptide in Rodents (~1kDa MW) Serum Peptide Conc. (ng/mL) 10000 With Intravail® 8000 552,710 ng*min/mL ~56% oral bioavailability 6000 4000 2000 No Intravail® 137,585 ng*min/mL 0 0 20 40 60 Time (min.) Lee et al. Regulatory Peptides 160 (2010) 129–132 © 2013 Aegis Therapeutics LLC 80 100 120 17 Oral Delivery of Exenatide & [D-leu-4]OB3 – Synergy in Weight Loss & Glucose Control Leinung MC & Grasso P (2012) Regulatory Peptides 179(1-3):33-8. © 2013 Aegis Therapeutics LLC 18 19 AFPep Stops Growth of Human Tumor Xenografts Oral AFPep cyclic 9-mer – Blocks Hsp-70 anti-apoptotic protein – Projected oral human dose ~200 - 500μg/day; Non-toxic at 200X-1,000X effective dose Tamoxifen Sensitive Breast Cancer Tamoxifen Resistant Breast Cancer Control Control AFPep Tamox AFPep © 2013 Aegis Therapeutics LLC Intravail® Potentiates Oral Anti-estrogenic Activity of AFPep by ~ 5X Uterine Hyperplasia Pharmacodynamics Assay AFPep AFPep in Saline μg p.o. Inhibition of E-2 Stimulated Growth of Immature Mouse Uterus, % 100 10 1 0.1 41 + 4 41 + 6 33 + 4 6+4 AFPep in 0.3 % Intravail 47 + 3 40 + 5 43 + 4 28 + 8 * * Significantly different from AFPep in Saline p < 0.01 Wilcoxon analysis Data courtesy Dr. Jim Bennett et al, Albany Medical College © 2013 Aegis Therapeutics LLC 20 21 Intravail® Oral Antisense Drug Absorption in Primates Conducted by Aegis-licensee Six canulated monkeys for IJ administration Antisense oligonucleotide - MW ~ 7KDa Absorption without Intravail® - not detectable Absorption with Intravail® - up to 18% Eight-fold reduction in required excipient volume No decapitation of intestinal pili Presently optimizing the formulation © 2013 Aegis Therapeutics LLC Multiple Modes of Transmucosal Delivery for Macromolecular Drugs 22 Nasal Metered spray pumps Oral (gastrointestinal) Gelcaps Tablets Oral cavity (buccal, sublingual) Flash dissolve Edible films © 2013 Aegis Therapeutics LLC 23 Intravail® Enhancement of Buccal Absorption Ex Vivo Flux of Lidocaine Across Porcine Buccal and Palatal Mucosa Enhancement Ratio Vehicle Water (No Excipient Control) Buccal Tissue Palatal Tissue (keratinized) 1 1 Intravail® B3 Alkyl Saccharide 22.2 14.5 Non-Intravail® Alkyl Saccharide I 1.2 1 Non-Intravail® Alkyl Saccharide II 0.8 1.1 Non-Intravail® Alkyl Saccharide III 1.2 1.1 Transcutol®:Water (50:50) 2.3 10.9 Ethanol:Water (50:50) 1.3 3.5 © 2013 Aegis Therapeutics LLC Intravail® Enhancement of Desmopressin Absorption in Flash-dissolve (Buccal) Format Desmopressin (pg/mL) Desmopressin PK Following Buccal Administration in Monkeys 60 50 Monkey #1 Monkey #2 Monkey 50μg dose,#3 mean 50µg n=3Buccal animals, 40 30 20 dissol. time 3 sec. 10 73 3 64 1 54 9 45 8 36 8 27 6 18 4 93 2 0 Time (minutes) Therapeutic threshold (10 pg/mL) surpassed at 15 min. © 2013 Aegis Therapeutics LLC 24 Intravail® Flash-Dissolve Desmopressin vs. Oral Comparisons Comparable PK Parameters for Intravail®-Flash Dissolve vs. Currently Available Oral Dosage Forms 12-Fold Relative AUC Increase vs. Sublingual Liquid 23-Fold Relative AUC Increase vs. Chewable Tablets © 2013 Aegis Therapeutics LLC 25 26 Protein Aggregation and Immunogenicity Defining the Problem Current Formulation Practice Need for Alternatives Regulatory Impact Fibrils of a linear octapeptide CD4 blocker form within 10 min. of aqueous dissolution (electron micrograph). © 2013 Aegis Therapeutics LLC 27 Problems Caused by Protein Aggregation Loss of efficacy Altered PK Increased immunogenicity Anaphylaxis or skin sensitization Reduced shelf-life Manufacturing yield losses due to membrane or column fouling or precipitation mAb’s particularly prone to aggregation © 2013 Aegis Therapeutics LLC 28 Surfactants Counteract Protein Aggregation Surfactants prevent or reduce aggregation This results in stabilized bioactivity and reduced immunogenicity Polysorbates (i.e. PS-20 and PS-80) are the most commonly used anti-aggregation surfactants Highly effective at preventing aggregation Well-accepted excipients - long track record of use © 2013 Aegis Therapeutics LLC Composition of polysorbate 20 and polysorbate 80 (Tween 20 and Tween 80 •Mixtures of structurally-related fatty acid esters of polyoxyethylene sorbitan. •Polyoxyethylene chains vary in length with the average number of monomer moieties totaling (W+X+Y+X) approximately 20 for Tween 80. •Principal fatty acids - lauric acid and oleic acid comprising up to 60% of the total fatty acid composition with esters of fatty acids of different chain length making up the remainder of the molecules •Common impurities: polyoxyethylene, sorbitan polyoxyethylene, and isosorbide •Plus spontaneously formed oxidation products whenever O2 is present © 2013 Aegis Therapeutics LLC 29 Spontaneously Formed Oxidation products Polysorbate 20 and Polysorbate 80 Reactive Contaminant Species Site of Damage Alkyl Peroxides methionine, histidine, and tryptophan moieties Aldehydes Primary amines Epoxy Acids Accessible nucleophiles such as those found in lysine, histidine, cysteine, and tyrosine © 2013 Aegis Therapeutics LLC 30 Examples of Peroxide Assay of Random Polysorbate Samples Following re-purification peroxides are detectable within a few weeks upon air exposure Alkyl saccharide © 2013 Aegis Therapeutics LLC Ray W.J. Jr. et al. Anal. Biochem., 146(2): 307-12, 1985. 31 Problems with Polysorbates 32 Underlying chemical structures spontaneously oxidize to peroxides, epoxy-acids and aldehydes These reactive elements increase immunogenicity Non-immunologic hypersensitivity and anaphylactoid reactions have also been attributed to poylsorbates in biotherapeutics Growing immunogenicity concerns by regulatory authorities, physicians, and patients creates a need to find non-reactive alternative surfactants © 2013 Aegis Therapeutics LLC ProTek® Alkyl Saccharide Excipients Possible Alternatives to Polysorbates Prevent aggregation Reduce immunogenicity Increase shelf-life Reduce denaturation due to elevated temperatures and shear force Increase reproducibility of lyophilizates upon reconstitution Extend patent franchise of existing biotherapeutics through formulation “Compositions of Matter” © 2013 Aegis Therapeutics LLC Provided Courtesy of Aegis Therapeutics, LLC 33 ProTek® Stabilization of Insulin–pH 6.5 & pH 7.5 37°C, 150 RPM Continuous Agitation – 90 days Stabilization of Humulin-R, pH 6.5 ProTek® Type vs. Concentration © 2013 Aegis Therapeutics LLC Stabilization of Humulin-R, pH 7.5 ProTek® vs. Non-ProTek® Isomer 34 Stabilization of β-Interferons 37°C, 150 RPM Continuous Agitation ProTek® Stabiliz ation of be ta-I nte r fe r ons 100 No ProTek® Excipient R e l. Light Scatte r, 500nm 80 Betaseron 60 No ProTek® Excipient 40 Rebif With ProTek® Excipient 20 0 0 .0 With ProTek® Excipient 5 .0 1 0 .0 1 5 .0 2 0 .0 Da y Patent Pending © 2013 Aegis Therapeutics LLC Provided Courtesy of Aegis Therapeutics, LLC 2 5 .0 3 0 .0 3 5 .0 4 0 .0 US Pat. No. 8,084,022 35 36 Some Other Examples of ProTek® Stabilization (150 RPM, 37o - 40oC) Human Growth Hormone 37 Deg. C. , Continuous Agitation @ 150 RPM PTH Type I 40 Deg. C @ 150 RPM Os tabolin C, pH 5.0, 40 deg. C 1000 No ProTek® Excipient Rel. Light Scat ter, 500 nm 100 No ProTek® Excipient 80 60 40 US Pat. No. 7,425,542 800 600 400 200 US Pat. No. 8,076,290 With ProTek® Excipient 0 20 With ProTek® Excipient -2 0 0 0 0 .0 5 .0 1 0 .0 1 5 .0 0 2 0 .0 1 2 4 5 Stabilization of Pramlintide and Calcitonin 800 No ProTek® Excipient 1 0 .0 8 .0 6 .0 Pramlintide 4 .0 2 .0 With ProTek® Excipient 0 .0 -2 .0 Calcitonin 5 .0 1 0 .0 1 5 .0 No ProTek® Excipient With ProTek® Excipient 2 0 .0 Day © 2013 Aegis Therapeutics LLC 2 5 .0 3 0 .0 3 5 .0 4 0 .0 Relat ive Light Scatt er, 500 nm 1 2 .0 -4 .0 0 .0 3 Day Day Relat ive Ligh t S cat t er ( 500n m) R e l. Light Sc atte r , 500nm 120 Monoclonal Antibody (IgG-3) 40 Deg. C @ 150 RPM I gG-3 (QE D Sample 1) pH 5.0 700 No ProTek® Excipient 600 500 400 300 US Pat. No. 8,226,949 With ProTek® Excipient 200 100 0 .0 0 0 .5 0 1 .0 0 1 .5 0 2 .0 0 Day 2 .5 0 3 .0 0 3 .5 0 4 .0 0 Intravail®/ProTek® Safety Profile Safe, odorless, tasteless, non-toxic, non-mutagenic, and nonirritating Chemically synthesized molecules - metabolize to CO2 & H2O Nonionic, non-denaturing, and pharmaceutically compatible with virtually any protein, peptide or drug Non-sensitizing and non-irritating to the rabbit eye @ 25% concentration Mild surfactants used in personal care and food products (NOEL ~ 20g/kg bw); designated as “GRAS” by FDA W.H.O. ADI ~ 15,000X the daily intake (~41 yrs of daily use) © 2013 Aegis Therapeutics LLC 37 Intravail® Summary 38 Allows non-invasive delivery of large and small molecule drugs (enhanced mucosal absorption) Unmatched intranasal bioavailability (up to ~30kD) Rapid onset of action Avoidance of gastric hydrolysis & “first pass effect” Elimination of needle stick injuries/infections Compatible with “off-the-shelf” metered nasal spray devices and oral dosage forms High oral bioavailability for certain peptides/non-peptides Greater patient convenience and compliance Low cost of GMP Intravail® excipients © 2013 Aegis Therapeutics LLC 39 ProTek® Summary Increased stability Aggregation reduction Reduced intrinsic immunogenicity No peroxide damage or peroxide induced immunogenicity Higher manufacturing yields Less stringent “cold-chain” requirements Extended patent franchise for existing biotherapeutics through formulation “Compositions of Matter” © 2013 Aegis Therapeutics LLC Provided Courtesy of Aegis Therapeutics, LLC 16870 West Bernardo Drive, Suite 390 San Diego, CA 92127 Phone: 858-618-1400 Facsimile: 858-618-1441 www.aegisthera.com Contact Information: Edward T. Maggio, Ph.D., Chief Executive Officer emaggio@aegisthera.com Ralph R. Barry, Chief Business Officer & CFO rbarry@aegisthera.com © 2013 Aegis Therapeutics LLC