Basic Concepts of Cancer Neoplasia Disease of cell growth, division, and differentiation Benign tumors • Localized, clear margins (encapsulated), noninvasive, slow growing, well differentiated • Functional adenomas if glandular tissue Malignant neoplasms Rapid growth, no clear margins (invasive) Aneuploidy, uncontrolled cellular multiplication, lytic enzymes Decreased cell adhesion, increased motility (metastatic) Angiogenesis---abnormal vessels Classifications of malignancies Carcinoma--epithelial Sarcoma—CT or muscle Glioma--glial cells Neuroblastoma--neurons Lymphoma Leukemia Cancer is a genetic disorder, but it is rarely inherited Epigenetic modifications p53 protein—guardian of the genome – Errors in p53 show up in ~50% of all cancers – Different mutations seem to prevail in different cancers Telomerase—prevents normal shortening of telomeres at end of chromosomes – Absent in most somatic cells, present in 85% of cancers – Allows for infinite number of divisions Multi-step Model for Cause of Cancer One cell suffers multiple genetic mutations, • Proto-oncogenes induce cell proliferation and growth (normal function) – Defined by what happens when turned on • Tumor suppressor genes suppress cell growth – Defined by what happens when turned off – P53--guardian of genome, halts faulty cycle Initiation--promotion--progression theory Initiation genome is first insult or series of insults to Types of Initiation Steps Changes in proto-oncogenes oncogenes Point mutations—always dominant (ras gene, telomerase gene) Gene amplification Chromosomal rearrangement Viral insertion and activation • human papillomavirus, hepatitis B and C, Epstein Barr (?) Changes in tumor suppressor genes (p53 is #1 example) Removes controls on cell cycle Removes review/editing of DNA copying mistakes Typically recessive mutations, so need 2 hits Chemical damage to DNA Epigenetic modifications, base substitutions Aromatic hydrocarbons, aromatic amines Insecticides, asbestos Anti-neoplastic drugs Aflatoxins Nitrosamines and nitrosamides in food, water Physical damage to DNA Breaks, deletions, translocations Sunlight (ultraviolet) Radiation--therapy or diagnostic use Predisposing factors Age, sex, heredity 15-20% of all cancers are caused by infection(usually viruses) Exposure to DNA damaging compounds Precancerous lesions • Colon polyps • Metaplastic cells Promotion = Proliferation Intracellular antioxidant enzymes should repair damaged DNA Apoptosis should remove damaged cells Cancers become more malignant with each generation of transformed cells Immune surveillance by cytotoxic T cells should remove transformed cells • Tumor associated antigens presented by MHC 1 molecules • Decrease in thymus activity with age means more cancers in older individuals Progression--becoming malignant Rate of growth depends on cell cycle time and rate of angiogenesis • Epithelial cancers usually grow faster To metastasize, must separate from original cluster of cells and invade blood or lymph vessel • Must penetrate basement membrane • Metastasis is NOT inevitable once penetrate vessels • First downstream capillary bed and lymph node are most vulnerable Clinical Manifestations of Cancer Fatigue is the #1 complaint • Starts early, for unknown reasons • May last months after tumor is gone • Causes most severe decrease in quality of life Pain—may not arise until late stages • caused by compression local tissue, inflammation, or nerve injury (therapy) Cachexia Malnutrition from metabolic demands of tumor, release of cachectin (TNF) • anorexia, weight loss • weakness, anemia Additional problems 60-80% of late stage cancer patients will experience clinical depression Lack of sleep Fear Alterations in carbohydrate metabolism Tumors metabolize glucose anaerobically • Patient must convert lactate back to pyruvate for use • Higher than normal insulin suggests post receptor abnormalities • Metabolic changes persist after tumor removal TNF will increase insulin resistance in body Alterations in protein metabolism Patient loses muscle mass • Resembles situation in burn/sepsis/hyperthyroid patients • Protein metabolism shifts to support tumor • Acute phase protein response--liver makes proteins for tumor, not the body – Associated with poor prognosis Alterations in amino acid levels that persist after tumor removal Alterations in fat metabolism Decrease in fat synthesis, increase in lipolysis • Lipid mobilizing factor found in urine • Increases cAMP levels, acts like lipolytic enzymes • TNF-alpha stimulates lipolysis • High levels of Ω-3 fatty acids may have benefit Other complications Increased risk of infection due to leukopenia, therapy Anemia Bleeding disorders—thrombocytopenia, vascular invasion, therapy Malnutrition from GI dysfunction Prognosis Tumor Grading System—based on microscopic exam of cells by pathologist • • • • I II III IV Well differentiated Moderately well differentiated Poorly differentiated Undifferentiated Prognosis Staging the tumor Stages 1-4 • Depends on number of sites, involvement of lymph nodes • Automatically get Stage 3 if tumor and/or mets cross the midline or the diaphragm Prognosis TNM Classification System • Tumor 1-4 (based on size) – Tx—cannot be assessed – Tis—carcinoma in situ • Nodes 0-3 • Metastasis 0-1 Etiology of cancer—various cancers have specific progressions