Biology of Hair and Nails Trichinosis Molecular and Cellular Pathology Dr Tim Scott-Taylor Health and Human Sciences Topics Topics covered; the nature of hair follicles structure of keratin normal patterns of hair growth causes of hair lost Tutorial; review of skin structure and function light microscopy Learning Objectives to know the nature of skin follicles and hair growth to know the function of hair in animals and humans to know the structure of hair fibres to understand the causes and treatment of hair loss Hair Longitudinal filamentous growth from the skin Composed of keratin Found mainly in mammals; definition of phylum Wool, fur, pelage Function: insulation protection protective coloration ornamentation / communication sensory (vibrissae) Skin and Keratin Keratinized stratified squamous epithelium is found only in the skin Keratin accumulation within maturing cells effectively waterproofs the cells, blocking diffusion of nutrients and wastes. The cells subsequently die. Hair is specialised adaptation of epithelial production of keratin Keratocytes • keratocytes are cells that make keratins • >40 highly insoluble proteins forming a network in the cytoplasm of keratocytes. • transform from undifferentiated basal cells to cornified skin cells. • four continuous layers basal spinous recognizable granular histologically cornified In the course of approximately 13 days columnar basal cells mature through a polygonal spinous cell, a diamond-shaped granular cell to a flat cornified cell that covers 25 basal cells. Parts of Hair Hair follicle; involution of epidermis Root; implanted in skin Shaft or scapus; projecting from surface hair Bulb; root enlargment, soft, white Papilla; dermal, blood and nerves Sebaceous glands; open into follicle Arrector muscle; attached to epidermis Nails Longitudinal section through nail and its nail groove Claws, Nails, Hooves and Spurs Keratin structures found in all mammals except cetaceans (whales). Derived from reptile claws. Consist of dorsal unguis = nail plate ventral subunguis = sole plate a) claws - unguis is curved and encloses the subunguis retractable in some carnivores. b) hooves - Unguis completely surrounds subunguis. cloven hooves in even-toed ungulates (Artiodactyls) c) spurs - in male monotremes a hollow keratin spur on hind legs poison gland associated with it. d) nails - only in primates. Flat unguis + subunguis greater precise manipulation of food or tools. Some Horns and antlers rhino horn - mass of keratin threads produced by epidermis bovid horn - bony core, horny sheath, no shedding pronghorn - bony core, horny sheath shed annually Hair is a Defining Feature Comparison Reptiles - Mammals Reptiles Mammals scales hair few epidermal glands many epidermal glands no mammary glands mammary glands 3-chambered heart 4-chambered heart ectothermy endothermy little cerebral development much cerebral development indeterminate growth determinate growth egg laying live birth Hair is characteristic of the phylla Temperature regulation was a fundamental development in mammalian evolution Animal Hair Fur, coat, pelage, wool: furry insulating covering Special adaptations; Spines; porcupine Bristles; lion’s mane UV transporter; polar bear dolphins, whales; Size and hair; aquatic adaptation (otters and seals) mass 1/ follicle per cm2 eg elephant, rhinoceros heat loss Types of Animal Hair Vibrissae; elongated + stiffened associaed with many nerve fibers mainly tactile receptors facial and carpal especially in carnivores primates rodentia Types of Animal Hair Underhair; main function is insulation. a) wool long soft and curly angora b) fur fine relatively short hair definitive growth c) velli down or fuzz with velvety appearance Types of Animal Hair Guard hair; a) awns b) spines long, straight and pointed overhairs present on most mammals stiff intermediate sized hair, protects down enlarged, stiff guard hairs with finite growth evolved parallel hedgehogs ~6 times in mammals spiny anteaters tenrecs barbs porcupines poisonous montremes c) bristles long firm hair eg. horse and lion manes# hair serves to insulate, to conceal, to signal, to protect, and to sense the immediate surroundings. Insulation serves to conserve heat, but can protect against excessive heat eg camel Tenrec •Tenrec ecaudatus (tailless tenrec) •The common tenrec occurs on Madagascar and on the Comoro Islands, between Madagascar and Africa. • Pelage is not dense and is a combination of hairs and blunt spines. Spiny Anteaters Echidnas, genus Tachyglossus, subclass Holotheria. monotreme found only in Australia and New Guinea. lays a single egg that is kept in her pouch for seven to ten days until spines begin to harden • Pelage a mixture of spines and quills Hair on Humans Filamentous growth from the skin Mainly in mammals; genus definition Function head: protective, ornamental eyelashes: protect eyes from dust eyebrows: shield eyes axillae; wicking of sweat scalp axillae terminal pubes chest hair beard Naked ape palms everywhere soles bare else covered penis in vellus hair labia fingers mucus membranes Naked Ape Great apes have sparse and bare areas but none extensive Why is man different???? 1). Adaptation; cool forest to hot savana bipedal locomotion upright stance but other cursorial apes, eg gorilla, chimpanzee, no loss ape pelage shields from UV, wind, radiant heat 2). Eco-parasites; fitness cost high cohabitation, communal living but other gregarious apes, eg chimpanzee, no loss 3). Aquatic ape; 5-7 e6 yr BC, Danakil region Ethiopia extended period wading lifestyle hair loss and subcut. fat more efficient theory not account for eccrine gland, density same as gorilla an chimp but developed for sweat production Neoteny paedomorphism slowing of certain aspects of physiological development retention by adults of juvenile physical characteristics dogs share many physical features of immature wolves Louis Bolk 1926: "man is a primate fetus that has become sexually mature" advocated by; Desmond Morris: The Naked Ape Stephen Jay Gould: chimp bone brain 4 fold increase in hominid brain size over past 3e6 years loss of body hair a side effect Types of Hair Languno: Vellus: Terminal: fine hair covers nearly entire embryo poorly pigmented, short, peach fuzz growing most areas fully developed, longer, coarser thicker and darker Although vellus hair continues to develop and accounts for 6% to 25% of scalp hair, it is less noticeable because of its light pigmentation Middle ear hair Depth vellus follicles situated high in the dermis large terminal follicles rooted deep in the subcutaneous fat Dermis Variable Skin The density of hair and the numbers of associated eccrine glands varies with different situations in the body Hair Growth Hair elongates from the dermal papilla Length And Growth Rate Length of hair and growth rate per day vary for each site on the body hairs on the head Eyebrows beards and whiskers armpit hairs pubic hairs 70cm / 0.35mm 3cm / 0.15mm 28cm / 0.4mm 8cm / 0.3mm 10cm / 0.2mm Normal Hair Growth anagen 1000 days Anagen = growth phase 2.5 – 3 years Catgen = short Telogen = resting 100 days catgen Telogen 100 days Cyclical pattern asynchronous Growth Cycle • 100 to 150,000 follicles on the scalp • ~95% of them are in an active growth phase called Anagen • ~5% completed their growth phase • Telogen hairs typically remain in the scalp for about three months before they are shed. • shampooing, combing or brushing typically releases hair at a rate of about 50 to 80 per day. Functions of Human Hair head hair for insulation and protection; trauma UV eyelashes blink to prevent entry into eye eyebrows, like awnings, protect the eyes from sunlight and sweat that might be hazardous body hair for insulation; goose bumps traps air residual? axilla; wicking of sweat long hair; marker of health? secondary selection Inner Ear Hair Hairs in the ampullae of the semi-circular canals are responsible for balance Otoliths, crystals of calcium carbonate, floating in gelatinous medium of the saccule brush against the stereocilia of the inner ear. This movement generates stereotypic awareness Hair Colour Two types of melanin account for all possible hair colors: Eumelanin: colors hair brown to black Pheomelanin: an iron-rich pigment colours hair yellow-blonde to red Both made from amino acid tyrosine, by tyrosinase. Increased tyrosinase activity results in darker hair color Melanocytes in the hair bulb contain subcellular organelles melanosomes; synthesize and store melanin. Melanocytes deliver the melanosomes to keratinocytes, where they are incorporated into the growing hair shaft Long Hair anthropologists speculate functional significance of long head hair may be adornment byproduct of secondary natural selection once other somatic hair had been lost or Fisherian runaway sexual selection; lustrous hair is a visible marker for a health waist length hair = ~1 m or 39 inches long ~80 months, 7 years, to grow long period of nutrition stability hygiene explain why long hair attractive both sexes Shape Affects Curls straight hair is round curly hair is flattened Hair Structure medulla = central core of cuboidal cells cortex = highly packed cells cuticular scale = outer layer Follicle The hair follicle consists of two coats—an outer or dermic, and an inner or epidermic. The outer or dermic coat is formed mainly of fibrous tissue; it is continuous with the dermis, is highly vascular, and supplied by numerous minute nervous filaments. Dermal coat consists of three layers The most internal is a hyaline basement membrane, well-marked only in the larger hair follicles, it is limited to the deeper part of the follicle Outside this is a compact layer of fibers and spindle-shaped cells arranged circularly around the follicle; this layer extends from the bottom of the follicle as high as the entrance of the ducts of the sebaceous glands. Externally is a thick layer of connective tissue, arranged in longitudinal bundles, forming a more open texture and corresponding to the reticular part of the dermis; in this are contained the blood vessels and nerves. Keratins A long-chain protein of >300 residues contain a high proportion glycine H side smallest amino acids alanine methyl chains sterically-unhindered hydrogen bonding tight between the amino and carboxyl groups -helices peptide bonds on adjacent protein chains closely aligned and tightly bound fibres tertiary structure: fibres twisted in helical filaments second in stength to chitin in organic molecules Keratin Secondary Structure keratin molecules > 300 residues high proportion of smallest of amino acids; glycine H side group alanine, methyl side group. sterically-unhindered hydrogen bonding between the amino and carboxyl groups of peptide bonds on adjacent protein chains close alignment and strong binding between chains keratin molecules twist around each other to form helical intermediate filaments. Keratin Tertiary Structure keratin molecules twine around each other in a left-hand helix coil structure two helices in turn form another left rotating helical fibre, called a protofibril eight protofibrils form a circular or square structure, called a microfibril, that is the basis of the structure of hair. This structure is stretchy and flexible and can be compared to a rope containing various threads that are twined together. The Arrangement of Fibres • The a-helix coiled keratin molecules are wound together in protofibrils. • protofibrils are bound together into microfibrils • Bundles of microfibrils are stitched together to make macrofibrils • Each hair is wrapped in a cuticle made up of protein scales and contains macrofibrils embedded in matrix proteins Interchain Bonding In addition to intra- and intermolecular hydrogen bonds, keratins have large amounts of the sulfur-containing amino acid cysteine ~14% disulfide bridges confer additional strength rigid, permanent, thermally-stable crosslinking similar to sulfur bridges in vulcanized rubber disulfide bonding contributes to insolubility of keratins pungent smells of burning hair and rubber due to the sulfur compounds formed Strength Intra- and intermolecular hydrogen bonds disulfide bridges that confer additional strength and rigidity by permanent, thermally-stable crosslinking It can be made to curl ’permanently’ or set temporarily. The breakage and reseting of the interchain bonds allow hair to regain its shape. Hair can stretched about 70%. Cross-linking creates strength. Hair is equivalent in strenght to iron wire. A wound strand of 5 mm can withstand a weight of 60kg Static The close connections of chains is associated with the hair's ability to become charged with static electricity. keratin is a good insulator of heat and electricity The capacity to hold an electric charge is refered to as triboelectric Styling hair heated with steam and pulled breaks the relatively weak hydrogen bonds the a-helices The a-helices can elongate without breaking the molecules • matrix proteins form a tangled supporting mechwork linked by many disulphide bridges. These bridges are also disrupted with moist heat • new interchain hydrogen bonds and disulphide bridges are formed after styling to keep the hair in its new style Nails Growth Growth occurs from a nail bed over a keratin matrix layer Nail Keratin Nailbed The nailbed is an essentially parallel epidermal structure located directly beneath the fingernail formed with parallel lines spaced at intervals. During normal growth, the fingernail travels over the nailbed. The nail is also composed of keratin microfibrils but the molecules are arranged in flat B-pleated sheets Nails Arranged in Stacks The molecules of b-keratin in finger and toe nails are organised in sheets stacked in layers. The proteins still fall into two groups; the helical and matrix, but in nail there is less sulphur in the matrix than in the hair matrix. Hair Length Sexual selection; visible marker of health 1.25 cm / 0.5 inch per month: 39 cm = 7 years good hygiene nutrition health stabilty Dimorphism • male androgens at puberty • testosterone • vellus - terminal hair • affects androgen sensitivity growth rate weight length Hair and Culture Much variation in style and length in different times and places Egypt head hair shaved, especially children long single lock of hair growing Maasai warrior Middle ages: shaved head + wig 17 to 18th C: long hair eg Cromwell Napoleon Washington WWI: lice and fleas brought typhus, short hair adopted Body Hair attitudes towards hair on the human body also vary between different cultures and times some cultures excessive chest hair on men is a symbol of virility and masculinity, other societies display a hairless body as a sign of youthfulness ancient Egypt, people regarded a completely smooth, hairless body as the standard of beauty adopted Greeks; hairless body = youth and beauty (strigyl) Islam; many hair tenets, five traits of fitrah Western societies; removal, bikini fashion, ‘manscaping’ Hirsutism Hormonal changes alter hair presence and thickness Vellus hairs on face of women, invisible/inconspicuous Oestrogen, antagonist of DTH Menopause; thicker and darker Diseases; Polycystic ovary syndrome Cushing's disease ovarian or adrenal gland tumors Hair Loss Whales & porpoises, and walrus use blubber for insulation. Elephants, rhinos, hippos - warm climate, favorable mass/surface ratio -> retention of heat no problem. molt = continuous or seasonal (1 or 2x /year) hair replacement seasonal fur color change: arctic fox, hares, some weasels Hair Loss genetic aging skin conditions diseases medications, eg anticancer drugs. mechanical damage skin infections. The followings are the most common Alopecia areata Telogen effluvium Alopecia androgenica = Male Pattern Hair Loss caused by range of factors; Alopecia androgenica characterized by "receding hairline" from lateral sides of the forehead follicular miniaturization, shaft width decreases becoming fragile 30% males by 50 yrs 50% by 65 years 66% of adult males largely genetically determined caused by male hormones or androgens esp DHT Male Pattern Baldness occur in varying forms in about 66% of adult males at some point characteristic (i) receding hair from lateral forehead stages; (ii) bald patch develops on vertex (iii) coalescence of patches pattern baldness is classified on the Hamilton-Norwood scale I-VIII Process of Balding In presence of DTH in genetically prone men, hair undergoes progressive thining; - the anagen growth phase is shortened so the hair is shorter when it stops growing - overseveral life cycles progressive follicular miniaturization decreases shaft width and hair becomes thinner and shorter Treatments Finasteride (marketed in the U.S. as Propecia) Minoxidil (marketed in the U.S. as Rogaine) Saw Palmetto (Serenoa repens) is an herbal DHT inhibitor easier to prevent the aging and falling out of healthy hairs than to regrow hair Alopecia Areata characterized by patchy scalp hair loss many as 1 in 1,000 people some time most common causes are medications, pregnancy, birth control pills, thyroid malfunctions, anemia, syphilis, and arthritis autoimmune response, immunological rejection, anti-follicular Often resolves spontaneously 50% of people will have recurrence Cyclosporins may have dramatic effects but are usually temporary careful review of your medical history Alopecia Universalis • complete loss of hair from all site of body • some are born with some hair but begin losing it quickly • can be inherited as an autosomal recessive trait. • traced to mutation in a gene dubbed HR in chromosome band 8p21.2. human homologue of mouse "hairless" gene • Several families known where hairlessness passed through 3 generations Telogen Effluvium characterized by sudden diffuse hair loss general thinning of the hair over a period of months most commonly experienced by those who have just given birth, or are undergoing chemotherapy Also caused infection, severe chronic illness, severe psychological stress, major surgery, hyperthyroidism, Crash Diets resulting in poor health or inadequate protein, and medications Trichotillomania characterized by incessant pulling or plucking of one's own hair tillein Greek for "to pluck, pull out children, males most commonly in adulthood and adolescence, most patients are females hair manipulations usually occur sedentary activities, reading, writing, or watching television impulse control disorder mental state characterized by tension with gratification or relief from the hair pulling once the behavior is established, it becomes habitual, regardless of the initial causative emotional problem Resolution requires psychological intervention Tinea Capitis infection characterized by bare patches of skin on the scalp fungal infection of the skin of the scalp, eyebrows and eyelashes most commonly found in children ages 10 and under, scaly non-inflamed area of skin seborrheic dermatitis person-to-person transmission. The organism remains viable on combs, brushes, couches, and sheets Since effective treatment of Tinea Capitis by griseofulvin in the 1950s incidence dropped from 14% to 1.2% Aging pigment in the hair is lost, hair becomes colourless time varies from person to person men tend to become grey at younger ages than women pale blond hair becomes white instead of grey red hair becomes a sandy color and later white gray or white appearance due to air bubbles in medula scattering light scalp hair loss or thinning with aging in both sexes half of all men are affected by male pattern baldness by the time they are 50 Death It is commonly claimed that hair and nails will continue growing for several days after death. This is a myth; the appearance of growth is actually caused by the retraction of skin as the surrounding tissue dehydrates, nails and hair become more prominent Histological Prep Crossectional View medulla cortex cuticle epidermal sheath dermal sheath