DR. MOSI DDH Coxa vara Genu valgum Genu varus Genu recarvatum Spectrum of disorders including : Acetabular dysplasia Instability (dislocation and subluxation) Teratological malarticulation – dislocation in utero , irreducible at birth , pseudoacetabulum and associted with neuro muscular conditions eg arthrogyposis Left > right Females > males at 7:1 20 % bilateral At birth dislocation is 1:1000 and dysplasia 1:100 Genetics Generalized joint laxity – dominant Shallow acetabular – polygenic Hormonal factors High levels of progesterone and relaxin in last days of pregnancy hence ligament laxity Intrauterine malposition complete breech, oligohydraminos,packaging deformities ( congenital muscular torticollis, metatarsus adductus, congenital knee dislocation Postnatal factors Initial instability leads to dysplasia Normal acetabulum but lax capsule Changes in the acetabulum and femoral head occur from the instabilty but some from primary acetabular and femoral head dysplasia Dislocation is posterolateral then superolateral Cartilagenous head of normal size but nucleus appears late Shallow anteverted socket Stretched capsule Elongated and hypertrophied ligamentum teres Superior limbus and capsule pushed into socket On weightbearing above changes worsen False socket is created Idelly diagonised at birth Barlows test Ortolanis test Galeazzis test limited abduction clicking hip asymetry in skin folds – thigh gluteal labial trendelenburg gait , waddling gait Ludolfs sign Radiographs useful at 4-6 months after head begins to ossify Helgenreiners line Shentons line Perkins line Acetabular index Center edge angle of wiberg Ce 20 -25. ai- 30 20 <20 Ultrasound Dynamic ( Hacke) and static (graf) Useful before head ossification Alpha angle : lines along bony acetabulum and ilium ( >60) Beta angle : line along labrum and ilium (<55) Use in high risk group or in positive physical findings Monitoring of treatment Confirmation after closed reduction Identification of possiblle blocks: ◦ Inverted labrum ◦ Inverted limbus ◦ Hour glass appearance CT Scan : study of choice MRI : significant role Abduction splinting Pavliks harness , Von rosens < 6months Contraindicated in teratological hip Requires normal muscle function for successful outcome ◦ Complications ◦ ◦ ◦ ◦ Avn Skin breakdown Brachial plexus injury 6 – 2yrs Failure of pavlicks harness Traction may be applied prior Under anaesthesia or gradually over about three weeks 60 flexion, 40 abduction, 20 internal rotation At 6 weeks convert to splint that prevents adduction obstacles to reduction ligamentum teres, the transverse acetabular ligament, the constricted anteromedial joint capsule , an inverted and hypertrophied labrum degree of anteromedial hip capsular constriction Shortened iliopsoas and adductors > 2YEARS or in failed closed reduction between 6 mnths and 2 years Anatomic changes such as anteversion and coxa valga Traction preop may help Hip spica for three months the splinting Older children Severe dysplasia with marked acetabular changes Reduced potential of acetabular remodeling Dega, ganz, permbenton Avascular necrosis Seen in all treatment forms Escessive forceful abduction Late surgery dx. By late appearance of ossification center Broadening of femoral neck or fragmentation Failed reduction and recurence Reduction in neck shaft angle <120 160 at birth 125 by adulthood Developemental Congenital Dysplastic Acquired Physis Metaphysis Subtrochanteric Associated with congenital short femur and proximal femoral deficiency Unilateral Subtrochanteric Ass with retroversion of femur and out toeing High propensity of progression Onset of ambulation, trendelenburg gait usually noted Defective endochondral ossification posteromedialy (physeal defect) Pathognomonic sign is a inferoposterior metaphyseal fragment Underlying bone anomaly eg rickets, fibrous dysplaia Usually bilateral Commonly due to Trauma Infection iatrogenic Results in increasing limb length discrepancy and abductor weaknes Clinical features Painless limp – waddling or trendelenburgs gait Limb length desripancy Developemental :Hilgenreiner epiphyseal angle > 60 - all progress. 45 – 60 may or may not progress. < 45 often correct spontaneously Dysplastic and acquired unpredictable Traumatic may resolve due to remodelling Halting deformity progression – investigate and treat renal osteodystrophy , rickets etc Correct proximal femoral anatomy : Poximal valgus osteotomy Trochanteric Subtrochanteric Greater trochanter epiphysodesis Greater trochanter transfer Pauwels Y-SHAPED OSTEOTOMY, Langenskiöld intertrochanteric osteotomy, BORDEN SUBTROCHANTERIC OSTEOTOMY Averages 40 at birth but decreases to about 10 -15 in adults. about 5 more in females Idiopathic or associated with other hip disorders eg sufe ddh cp dcv In toeing gait but this usually resolves Cosmesis Anterior knee pain due to patellar malalignment • Observation • Rotational osteotomy Rarely indicated ( most children have no functional deficits) Child over 10 – 12 years with internal rotation of > 80 and external rotation of <10 Intertrochanteric vs mid-diaphysis Physiologic – usually <2 years and bilateral) Pathologic – trauma , infection, rickets, dysplaisia of bone ,blounts disease, >2years Unilateral Severe Associated shortening Obesity 10m-15 Cosmesis Patellofemoral instability/ maltracking Altered gait - lateral thrust, circumduction Early walkers – genu varum Determine severity Site : Intermalleoar distance and intercondylar distance Metadiaphyseal angle Langenskiold classification of tibia vara distal femur vs proximal tibia Likelihood of progress is the cause permanent eg epiphyseal bar, achondroplasia, osteochondroma BMI >22 Full length standing Line should bisect knees Md 11, 11 - 16 tibia vara or osteochondrosis deformans of the proximal tibia Impaired ossification medial proximal tibia Hueter volkamn effect Infantile Juvenile Adolescents Observation Bracing – children less than 2 yrs with early blounts ( stage 1 and 2) Guided growth Hemiepiphysiodesis on convex side using screws, staples, tension band paltes In the past relied on growth charts Corrective osteotomy ( acute vs gradual correction using an ilizarov ) Blounts – before 4 yrs and at stage 1 or 2( surgery differs for 3&4,5&6) Children near maturity Permanent physeal issue Mechanism Laxity of posterior capsule Abnormal inclination of tibia articular surface Usually 14+/- 3.6 posterioly. Forward tilt if the anterior physis is damaged Observation – hypermobile, (10 -15 ) Bracing Prevents hyper extension Can result in stiff knee Ankle orthosis holding at 5-10 shown to prevent recarvatum in cerebral palsy Anterior wedge osteotomy Poserior closed wedge osteotomy Flexion supracondylar osteotomy of femur Gradual correction using an external fixator Epiphysiodesis : When secondary to physeal damage Reefing of the posterior capsule of the knee joint Anterior patellar block Quadriceps lengthening THANK YOU