Developmental dysplasia of the Hip (DDH) Natural history, management and outcomes West Bank, Autumn 2009 Aetiology Genetic: polygenic syndromic sex-linked Hormonal: oestrogen ; relaxin Mechanical: breech liquor deficiency Mechanical Left : Right – 4 : 1 Breech : DDH ≥ x 10 (N.B. frank) Liquor ↓ : moulded baby - plagiocephaly - scoliosis - foot deformity - skew pelvis Genetic / mechanical Joint laxity Acetabular and femoral version Birth pathology in DDH Simple: Acetabulum normal Femoral head normal Labrum normal Capsule stretched Neonatal DDH Ligamentum teres True socket Teratological DDH Irreducible False acetabulum Defective anterior acetabulum “anteverted” Increased femoral neck anteversion False acetabulum Arthrogryposis with dislocations & delivery fracture Untreated dysplasia without dislocation in the Navajo 18 children 15 became normal 3 stayed dysplastic Pratt, Freiberger, Arnold. CORR; 1982 Which hip dysplasia pain? • Complete dislocation with no false acetabulum: NO • Complete dislocation with false acetabulum: • Subluxation: YES YES Wedge, Wasylenko. CORR, 1978 45-year old • Subluxation • False acetabulum • Severe OA ... and adult unrecognised dysplasia? Early treatment • Diagnose! • Splint • Review Ortolani test Ultra Sound ! UK Screening Committee: the problems • Poor science • Poor testers • No national training • No national audit • Litigation programme U.K. National Screening Committee (2006) • Universal U.S. not recommended • Clinical exam. • by properly trained ( at birth & 6 weeks) Refer “at risk” babies The extended role practitioner & orthopaedic team working Annie: extended role physio. Oxford experience • 1500 new screenings / year • 700 follow-up screenings / year • 95% successful splints Challenges in hip dysplasia • Subluxation • Incongruity • Early arthritis The older child Closed reduction • E.U.A. • Adductor tenotomy • Safe position in POP Open reduction • Bikini incision • Psoas tenotomy • Ligamentum teres? • Transverse ligament • Limbus? • Capsulorraphy Arthrogram • Head shape • Cover • Congruity • Articular cartilage • Labrum DDH: what influences arthritis risk? • Age at treatment • Quality of reduction • Stability • AVN Oxford DDH follow-up Results - Arthritis Opposite hips 4%: moderate/ severe OA Affected hips 40%: moderate/ severe OA Femoral operation • Shortening • Varus/valgus +/- rotation • Trochanteric transfer • Neck lengthening Femoral shortening for DDH Hey-Groves (1928) Valgus/ extension osteotomy? AVN with trochanteric overgrowth Better in adduction and flexion Neck-shaft angle after femoral osteotomy Pelvic operation Re-alignment: simple e.g. Salter complex e.g. Bernese Re-shaping: e.g. Pemberton Augmentation: e.g. shelf Chiari Salter Innominate osteotomy Salter & femoral osteotomy K. E. 21 - 12 - 1999 Staheli shelf Chiari osteotomy Outcome of Chiari osteotomy • 236 of 388 osteotomies reviewed at 25 years • 51% good; 30% fair; 18% poor • Best results: ≤ 7 years; no OA • Femoral osteotomy: no better (Windhager et al. JBJS 1991) Very late salvage Schanz osteotomy Radical salvage • • • Fusion Replacement Excision Hip arthrodesis Consider for: i. Young male ii. Unilateral iii. Infection Joint replacement Consider for: i. Severe arthritis ii. Failed “ conservative” Rx. iii. Bilateral disease Joint replacement • • • May be complex +/- femoral shortening +/- acetabular grafting Severe arthritis DDH AVN OA End-stage O.A. High, painful DDH DDH: THR does not solve all ills! Right: painless Left: severe pain THR outcomes in DDH • Charnley cemented hips: 5 of 38 loose at 11 years Bobak, Wroblewski et al 2000 • Harris uncemented hips: 20% loose at 7 years 46% loose at 12 years Jasty, Anderson, Harris, 1999