A CPMC Regional CME Event INFECTIOUS DISEASE UPDATE - Microbiome and Emerging Infections Saturday October 19, 2013 HPV UPDATE: HEAD AND NECK CARCINOMA Gerald Kangelaris, MD San Francisco Otolaryngology • No Financial Disclosures HPV IN THE MEDIA HPV IN THE MEDIA HPV IN THE MEDIA CONCERNED PATIENTS GOALS • • • • Describe HPV associated head & neck cancer Understand at-risk population Appreciate disease presentation Describe basics of treatment and outcomes • Improve ability to counsel patients! OUTLINE – HPV IN HEAD & NECK CARCINOMA • • • • • • Virology Epidemiology Carcinogenesis Presentation Treatment & Outcomes Future Directions VIROLOGY • HPV - dsDNA virus - 100+ strains isolated - 15 strains high risk • Types 16 & 18 • Genitals • Anus • Oropharynx http://hpvvirusinwomen.com/images/hpv_virus_in_women3.jpg VIROLOGY http://faculty.ksu.edu.sa/dralghamdi/Pictures%20Library/طبقات%20الجلد%20skin%20layers.jpg VIROLOGY http://upload.wikimedia.org/wikipedia/commons/b/b4/Normal_Epidermis_and_Dermis_with_Intradermal_Nevus_10x.JPG http://www.lab.anhb.uwa.edu.au/mb140/corepages/Lymphoid2/images/tns02he.jpg VIROLOGY • Head & Neck Sites - Palatine tonsil - Tongue base http://www.region3sweetadelines.org/documents/AIM%202011/pharynx.jpg EPIDEMIOLOGY D’Souza G, Kreimer A, et al. Case-Control Study of Human Papillomavirus and Oropharyngeal Cancer. N Eng J Med 2007, 356:1944-56. EPIDEMIOLOGY • Head and Neck Cancers - Overall decreasing - Oropharynx increasing • OP Cancer Epidemic - OP HPV (-) • 2.0 1.0 per 100,000 - OP HPV (+) • 0.8 2.6 per 100,000 Chaturvedi AK, Engels EA, et al. Human Papillomavirus and Rising Oropharyngeal Cancer Incidence in the United States. J Clin Onc 2011. 29(32):4294-4301. EPIDEMIOLOGY • Typical Head & Neck Cancer Patient http://quittea.com/wp-content/uploads/2012/06/Old-Guy-Smoking-Cigar.jpg http://i.telegraph.co.uk/multimedia/archive/01589/Lorna-Gobey_1589754c.jpg EPIDEMIOLOGY • HPV Oropharynx Cancer Patient http://maennling.com/wp/wp-content/uploads/2012/11/DSC_6796.jpg http://ak9.picdn.net/shutterstock/videos/4194004/preview/stock-footage-smart-caucasian-middle-aged-man-looking-to-the-camera-in-the-park-close-up-portrait.jpg EPIDEMIOLOGY HPV (+) OPSCC as Sexually Transmitted Disease • Presence of HPV in Oral Samples Increases With… • • • • • • Being sexually active Early age sexual activity Increasing # oral sex partners Increasing # vaginal & anal sex partners Male No difference if hetero- or homosexual/bisexual Gillison ML, Broutian T, et al. Prevalence of Oral HPV Infection in the United States, 2009-2010. J Am Med Assoc 2012. 307(7):693-703. EPIDEMIOLOGY HPV (+) OPSCC as Sexually Transmitted Disease • Presence of HPV in Oral Samples… Gillison ML, Broutian T, et al. Prevalence of Oral HPV Infection in the United States, 2009-2010. J Am Med Assoc 2012. 307(7):693-703. EPIDEMIOLOGY HPV (+) OPSCC as Sexually Transmitted Disease • HPV (+) vs. HPV (-) OPSCC - Lifetime # Oral Sex Partners • 0 partners OR 1.0 • 1-5 partners OR 3.8 • 6+ partners OR 8.6 - Lifetime # Vaginal Sex Partners • 0-5 partners OR 1.0 • 6-25 partners OR 2.7 • 26+ partners OR 4.2 D’Souza G, Kreimer A, et al. Case-Control Study of Human Papillomavirus and Oropharyngeal Cancer. N Eng J Med 2007, 356:1944-56. EPIDEMIOLOGY HPV (+) OPSCC HPV (-) OPSCC Younger (<50 years) Older (>60 years) Never / Mild Smoker Heavy Smoker Mild / Mod Alcohol Heavy Alcohol High Sexual Exposure Low Sexual Exposure Higher Socioeconomic Status Lower Socioeconomic Status Increasing Incidence Decreasing Incidence CARCINOGENESIS • HPV DNA - Two capsid proteins, L1 and L2 - Six non-structural proteins • Two viral oncoproteins E6 and E7 • E6 and E7 increased activity in high-risk HPV strains http://img.medscape.com/fullsize/migrated/585/223/erm585223.fig2.jpg CARCINOGENESIS • E6 - Degradation of tumor suppressor p53 - Prevents apoptosis • E7 - Loss of retinoblastoma (Rb) tumor suppressor - Accumulates p16 - Pushes cells from G1 S phase PRESENTATION • Palatine or Lingual Tonsil Location http://www.nidcr.nih.gov/NR/rdonlyres/04B2E6CA-B032-47C0-BC09-D995D6655AA6/18010/OralCancerFig14High.jpg PRESENTATION • Symptoms - Painful oral lesion Dysphagia or odynophagia Bleeding Asymmetry Trismus Otalgia Hypoesthesia • Asymptomatic! PRESENTATION http://www.ghorayeb.com/files/carcinoma_of_tonsil.jpg PRESENTATION http://www.ghorayeb.com/files/Tongue_Sq_Cell_Ca_700_x_500.jpg PRESENTATION • Differential Diagnosis - Infectious - Benign lesions - Neoplastic - Inflammatory PRESENTATION http://quebal.icebergcms.com.au/images/product/image/enl_who_circumvallate_papillae.jpg PRESENTATION http://www.capedental.com/cdmain/wp-content/uploads/2011/05/IMG_3641.jpg PRESENTATION • High Rates Nodal Metastases • Often Tumor Undetectable at Primary Site http://www.aafp.org/afp/2002/0901/afp20020901p831-f3.jpg http://1.bp.blogspot.com/-wotdvG47uXI/T3DkTZOhIZI/AAAAAAAAKPQ/ujuwutpvCyo/s1600/CysticNodesHPV.JPG PRESENTATION • Consider HPV(+) OPSCC - Neck mass persisting for 4+ weeks, unresponsive to medical therapy • • • Upper jugular chain Firm, discrete, mobile, nontender May be asymptomatic & non-visible at primary site! - Persistent OP sore throat 4+ weeks, unresponsive to medical therapy • Tonsillar asymmetry, otalgia - Advanced disease • Dysphagia, pharyngeal bleeding, trismus, voice changes PRESENTATION • Workup - FNA neck mass • US guidance may improve yield in cystic masses - Imaging • Contrast enhanced CT / MRI neck • CXR - OHNS evaluation • Fiberoptic nasopharyngoscopy • Exam under anesthesia, biopsies TREATMENT & OUTCOME • Treatment Options - Concurrent chemoradiation - Surgery with adjuvant radiation, +/- chemotherapy TREATMENT & OUTCOME • Improved survival in HPV (+) OPSCC tumors Ang KK, Harris J, et al. Human Papillomavirus and Survival of Patients with Oropharyngeal Cancer.N Eng J Med 2010. 363(1):24-35. TREATMENT & OUTCOME • Improved survival in HPV (+) OPSCC tumors - 53% better overall survival - 74% better disease specific survival - Improvements in progression free survival, disease free survival O’Rorke MA, Ellison MV, et al. Human Papillomavirus Related Head and Neck Cancer Survival: A Systematic Review and Meta-Analysis. Oral Oncology 2012. 48:1191-1201. TREATMENT & OUTCOME • Mechanisms for Improved Outcomes - Lack of field cancerization - Increased sensitivity to radiation therapy • Degraded wild-type p53, not mutations - Immune response FUTURE DIRECTIONS • De-intensification strategies - Lower dose of radiation therapy - Targeted chemotherapeutics - Surgery with de-escalation of adjuvant treatment http://www.healthspablog.org/wp-content/uploads/2010/11/radiotherapy-6D.jpg http://oralcancernews.org/wp/wp-content/uploads/2011/09/robotic_surgery03.jpg FUTURE DIRECTIONS • Vaccination http://www.pulsetoday.co.uk/Pictures/web/d/v/a/Cervarix_vaccine_pack_hpv_cervical.jpg http://www.thedailysheeple.com/wp-content/uploads/2012/10/GARDASIL111308.jpg FUTURE DIRECTIONS • Vaccination http://www.skepticalraptor.com/blog/wp-content/uploads/2012/10/gardasil-ad1.jpg http://1.bp.blogspot.com/-ejglTzhvHAg/T6CydnVyaxI/AAAAAAAAAOs/pGVsBwnF3Pw/s1600/new%2Bdoc_1.jpg FUTURE DIRECTIONS • Vaccination http://1.bp.blogspot.com/-0DPj7SzNye0/TzW3wpLXojI/AAAAAAAAB_I/DkBrrVtXdfA/s400/gardasil4-1.jpg http://gaia-health.com/gaia-blog/wp-content/uploads/2012/11/Say-No-to-Cervarix-and-Gardasil.jpg