PEDS EXAM 2 STUDY GUIDE Development Erikson stages: o TRUST vs MISTRUST (birth to 1 year old) Infant. No concept of danger. Falls. Inhalation of foreign objects-everything goes in the mouth. They cry to relay their needs- you can’t spoil them. o AUTONOMY vs SHAME AND DOUBT (1 to 3 years old): Toddler. “Negativism”persistent negative responses to questions. “Ritualization” provides sense of comfort. Need to maintain sameness. REGRESSION. Not aware of dangers o INITIATIVE vs GUILT (3 to 6 years old): Preschooler. Feelings of guilt, anxiety, and fear may result from thoughts that differ from expected behaviors. Believe in the power of words and are very literal. “magical thinkers”-egocentric. Animism- they think inanimate objects are alive. o INDUSTRY vs INFERIORITY (6 to 12 years old): School age. Like to have a sense of accomplishment, carry tasks through to completion. Children learn to compete and cooperate with others, and they learn the rules! Form groups (same sex groups) Feelings of inferiority is developed if too much is expected of them or if they believe that they cannot measure up to the standards set. o IDENTITY vs ROLE CONFUSION (12 to 18 years old): Adolescent. They struggle to fit the roles they have played and those they hope to play with the current roles adopted by peers and therefore may result in a role confusion. Peer pressure and approval! Need for independence and freedom, risk takers. Types of play and which age groups utilize each type most often: o Parallel: Toddler. Children play independently but among other children. (side by side no interaction) o Associative: Preschooler. Children play together and are engaged in similar or even identical activity, but there is no organization, division of labor, leadership assignment, or mutual goals. Children borrow and lend play materials. Each child acts according to his or her own wishes, there is no group goal. o Cooperative: School age. There’s RULES. Like to play with SAME SEX. Organized and children play in a group with other children. They discuss and plan activities for the purposes of accomplish an end. Play helps them grow intellectually, socially, sensor motor and to be creative! It puts them in control and allows them to relay their needs/feelings/frustration. Don’t orient them to reality. Playing make believe helps them communicate with others. Communication o Infants: listening to their cry, talk in low quiet voice. Empower parents to help o Preschooler: let them touch, feel it, and smell things. Ask specific questions. (yes/no). Use words they will recognize. (tell time with things they understand-after lunch/nap) They’re egocentric and “magical thinkers” and believe in animism. o School age: explanation and reason for everything, simple terms, can’t get them to communicate, involve them in play! o Teenagers: Let them express their feeling. Ask open ended questions and be honest with them Assessment order of infant and toddler: do heart and lung first if they’re quiet. Don’t take them away from parent. Belly reader for babies. Pick up baby if they’re crying! Choking hazards in preschoolers: prevent it by teaching parents common things they choke on. Preop teaching for preschool and school age: let them touch, feel, smell, hear it How do you help a young child understand the concept of time or what time it is? Associate it with things they know. After lunch/nap Who is most concerned with body image? Teenagers Relationship of teenagers to risky behaviors- think it’ll never happen to them and engage in risky behaviors Best way to get a toddler to eat in a hospital: bring their utensils from home (paw patrol plate), give them their fav foods, stick with their rituals The type of injuries is most associated with what factor: developmental age of the child Atraumatic care: therapeutic care that eliminates or minimizes psychologic or physical distress by children or their families. Goal is FIRST DO NO HARM! Transitional object- demonstrate on animal first. Activities of a 6-month-old: o hold objects o rolls around o starting to teeth o Separation anxiety starts o Can hold their head up on their own- don’t need support Regression in a toddler: Peeing the bed, wanting a bottle, baby talk, holding bowel movement PERFUSION General congenital heart disease (CHD): Assessment: H&P exam- positive prenatal hx (maternal chronic health conditions, DM & Lupus both have increased incidence of children with CHD), maternal med use- some are teratogenic, maternal exposure to infection-rubella, family hx of heart defect (parent, sibling) Inspection: Failure to thrive or poor weight gain!! Presence of heart murmur is often 1st indicator of heart defect!!! (listen to heart for 1 minute) Pre-op lab findings in cyanotic heart: Polycythemia (chronic low O2, there’s an increase in RBC, trying to get more oxygen. Blood becomes more viscous and increases risk for clotting!) Clubbing (later sign) How does CHD affect play: children need to play and be around other kids! Will usually limit themselves/self-regulate Early signs of impending heart failure: o Tachypnea o Tachycardia o activity intolerance (especially with feeds) o sweating especially of head o weight gain-weigh every day! o Call doc! o Higher risk for URI bc of fluid accumulation in lungs! CHF and cardiac defects: HF is a complication common to all severe cardiac defects! Feeding an infant with CHF: o more frequent feeds o feed at 1st sign of hunger o increase formula density o GAVAGE feeds- limit nipple feeds to no longer than 30 mins Discharge teaching for parents after cardiac surgery: Instruct parent to notify physician iftemperature above 37.7 (100 F), new/frequent coughing, turning blue or bluer than normal, difficulty feeding! Report if they can’t pee Where to check BP for a child with CHD: ALL 4 extremities Cardiac catherization: use femoral vein- right side of the heart. Femoral artery- left side of heart Pre op: Teaching parents and age appropriate for child Accurate height and weight Assess for history of allergies (esp dye/shellfish) in parents -DOESN’T CANCEL TEST! History of infection (esp fever or diaper rash in femoral access!)- WILL CANCEL TEST! Baseline vitals and pulses- Mark the pedal pulses prior and establishes a baseline Baseline labs for renal functions NPO status Pre med- sedation or antibiotic Post op: Monitor pulses- esp distal to site, note extremity color and temp Monitor vitals (dysrhythmias are most common complication) Assess dressing- bleeding or hematoma ***if bleeding occurs- apply direct continuous pressure about 1 inch ABOVE insertion site to localize pressure over the vessel puncture. For child- CALL right away if they have bleeding! Observe for signs of infection- swelling, drainage, bleeding, fever. Notify physician if this happens! Tell child to keep their leg still !!! Weighing the child with CHD: weigh every day at the same time with same clothing Timing of digoxin dosing: teach how to draw it up (small amounts), give at same time every day, if child vomits -call prescriber! Dose depends on WEIGHT! Signs of digoxin toxicity: seeing halos, nausea and vomiting. FOR INFANT: VOMITING can indicate toxicity!! Call doc if they vomit, don’t repeat dose! A fall in the serum potassium level enhances the effects of digitalis, increasing the risk of digoxin toxicity. Increased serum potassium levels diminish digoxin's effect. Therefore, serum potassium levels must be carefully monitored Goals of management: can’t reverse damage if already done. improve cardiac function (DIGOXIN- check pulse for a minute before giving. Digoxin slows the HR! HOLD IF HF is LESS than 60!) remove accumulated fluid and sodium: give diuretics- lasix, fluid restriction and low sodium intake decrease cardiac demand: limit physical activity Improve tissue oxygenation & decrease oxygen consumption Predisposition of CHD: mother exposure to rubella in first 7 weeks of pregnancy family hx of heart defects maternal hx of diabetes and lupus Parental overprotection: Avoid smother love! Children need to play, parents need to understand this. Giving inconsistent discipline (spoiling them) Tetralogy of Fallot (TOF): Pathophysiological changes notes in TOF: An overriding aorta is a congenital heart defect where the aorta is positioned directly over a ventricular septal defect, instead of over the left ventricle. The result is that the aorta receives some blood from the right ventricle, which reduces the amount of o2 in the blood o has FOUR defects: o o o o Ventricular Septal Defect (VSD) Pulmonary stenosis (PS) overriding aorta right ventricular hypertrophy They’re severely cyanotic from birth! Has right to left shunting! (the right side has increased pressure!) dec pulmonary pressure Positioning for TOF to relieve dyspnea: SQUAT (knee-chest position) decreases blood flow to lower extremities and allows more to upper body (think about them being cyanotic-very blue!) teach parent to put infant in knee chest position Problems associated with TOF: TET SPELLS- occur with crying or feeding (they become hyper cyanotic/veryyy blue!) They’re more at-risk neurological complications (CVA, stroke, brain abscesses and developmental delay) COA: (Coarctation of the Aorta) Taking blood pressures and checking pulses in a patient with COA: Take BP in all 4 extremities! Will have high blood pressure & bounding pulses in arms/upper extremities Low blood pressure in lower extremities. Weak femoral pulses & cool lower extremities ASD/VSD: Pulmonary blood flow with VSD: increased pulmonary blood flow. Left to right shunt! Post cardiac catherization care- same as above Kawasaki Disease (KD): Acute- happens all of a sudden. Lasts a long time! No diagnostics Discharge teaching for KD: importance of follow up care, defer any live immunizations for 11 months after IgG administration, no varicella vaccine. They will be on ASA therapy! Signs and symptoms of KD: strawberry tongue fever (doesn’t come down or respond to anything, no Tylenol/antibiotics!) CONJUNCTIVA will be red but NO discharge/exudate Soles of hands and feet are red and skin is peeling lips red irritability Cardiac complication of KD: long term complications of KD include the development of coronary artery aneurysms disrupting blood flow. Treatment: High dose IgG (effective in reducing coronary artery aneurysm)---repeat if fever persists Aspirin for its antiplatelet effect (risk for reyes syndrome!). initially given for antiinflammatory effect Don’t want them to get any live vaccine (NO varicella!) Hemophilia: LIFELONG disease. They miss one clotting factor (factor 8) and bleed and bleed. Its hereditary, will not grow out of it! X linked RECESSIVE TRAIT- males are affected, females may be carriers Hemophilia treatment and nursing interventions: o prevent bleeding- close supervision & safe environment for toddlers o Symptoms may not occur until 6 months of age: WHY?-----Mobility leads to injuries from falls and accidents (need safe environment for toddlers) o dental procedures in controlled situation (soft toothbrush -wet it first) o wear ID bracelet o shave only with electric razor o avoid IM injections o avoid ASA/Ibuprofen- give acetaminophen for mild pain o superficial bleed- apply pressure for at least 15 mins, ice to constrict. RICE! o Replace clotting factors (via IV) on a regular basis o transfusions done at HOME! o ****Bleeding in the neck, mouth, or thorax is serious because the airway can become obstructed o Hemoarthritis---immobilize, elevate and ice—RICE (rest, ice, compression, elevate) during bleeding episodes. No physical therapy in initial phase; only AFTER! ROM exercises AFTER bleeding stops to prevent contractures, Sports activity and hemophilia: NON-CONTACT SPORTS! (chess, golf, bowling, swimming, fishing) Use of VIII in hemophilia- hemophilia A affects the most people. They have a deficiency of factor VIII. Need to replace it via IV. Treatment of bleed: will start transfusing at HOME!!! HIV is not a concern as much anymore bc the blood is tested better CELLULAR REGULATION: Leukemia: Leukemia is an unrestricted proliferation of IMMATURE WBCs in the blood-forming tissues of the body! Acute Lymphoblastic leukemia (ALL)- aka stem or blast cell. Most curable. Clinical manifestations of leukemia: WBC will be low---not functioning! These abnormal cells compete for metabolic elements and causes gradual weakening of bone & possible fractures. Watch for anemia (low RBC), infection(low WBC), and bleeding (low platelets). Treatment: o chemotherapy o HSCT (hematopoietic stem cell transplantation) for ALL (acute lymphoblastic leukemia). Transplant given when child is in remission Side effects and complications: o anemia from decreased RBCs o infection from neutropenia o bleeding from decreased platelet production o can infiltrate other organs too. Spleen, liver, & lymph glands become infiltrated and enlarged- eventually become fibrotic. CNS becomes infiltrated- IICP Nursing management: Prepare child and family. Multiple painful tests/procedures (explanation/therapeutic play, sedation) Relieve pain Prevention of complications of myelosuppression- infection, hemorrhage, anemia Manage problems of drug toxicityo N/V- antiemetic, steroids- given BEFORE chemo. Prevents s/s o anorexia- may need TPN o mucosal ulceration – bland diet, soft tooth brushes o neuropathy o hemorrhagic cystitis- fluids o ALOPECIA!!! Handle chemo with care Blood transfusions: may be necessary- could have a reaction to blood transfusion!! STOP blood transfusion and stay with pt if they have a reaction. Don’t force saline after stopping infusion! SCD (sickle cell disease) Genetic transmission of SCD: GENETICS (both parents need to have the trait) Symptoms of vaso-occlusive crisis: severe pain! Treatment of a vaso-occlusive crisis: hydration, pain med: narcotics such as morphine are given around the clock! HEAT to sight! Home management/education: first thing is to hydrate them (oral & IV therapy) Prevent infection- hand hygiene Give penicillin as order for infection Oxygen- sickled cells don’t carry oxygen good enough Analgesia for severe pain from vasoocclusion (give MORPHINE! Usually given around the clock!) Blood replacements to treat anemia & to reduce the viscosity of the sickled blood Antibiotics to treat any existing infection Explanation of the disease & its consequences Seek early intervention for problems such as fever IMMUNITY Primary immunizations are started at BIRTH!- hep B General side effects of vaccinations Within 24-48 hours: local tenderness, erythema, and swelling, and induration at the injection site Low fever, drowsiness, fretfulness, eating less, prolonged or unusual cry Low grade fever means they are developing an immune response Should see PCP if symptoms severe Contraindications: severe febrile illness, LIVE VIRUS is not administer to anyone with an altered immune system. Avoid MMR if allergic to neomycin, streptomycin or eggs HIB vaccine- provides protection against BACTERIAL MENINGITIS, epiglottis, bacterial pneumonia, septic arthritis, and sepsis Schedule for Hepatitis B: starts at birth. Given to newborn. Injecting IM vastus lateralis. Don’t forget EMLA/LMX cream (its an anesthetic cream) There’s 3 doses for this Varicella- LIVE VACCINE! recommended for 12-15 months. Don’t get with aspirin!! Can cause Reyes syndrome! Don’t give to cancer/chemo pt! DON’T give to patient with HIV Inactivated polio virus/DTap: its okay to give to an immunocompromised pt. you can give to pt who has a sibling who’s getting chemo. Varicella zoster immune globulin (VZIG)- given to high risk children to prevent varicella! Recommended for children who are IMMUNOCOMPROMISED and are EXPOSED to the virus, who have no previous hx of varicella, and who are likely to contract the disease and have complications as a result. Therapeutic communication for patients receiving vaccinations- Need informed consents for immunizations. VIS (vaccine information sheet)- information statements that MUST BE GIVEN to parents before administration of given vaccines. Vaccines can be given if child has a slight cold- not if febrile!! Preferred immunization sites based on age- vastus lateralis or ventrogluteal muscle for infants! Deltoid after 18 months! 1 inch needle Use of acyclovir with varicella/chicken pox: for someone who HAS chicken pox/varicella. treat with acyclovir to decrease the duration of the disease! Rubella and congenital defects: mild infection in children but to the UNBORN FETUS it presents serious problems. Its teratogenic- it affects unborn fetus! If mom is exposed to rubella, fetus is at risk for defects. Isolation practices for patients with chicken pox: strict isolation with AIRBORNE PRECAUTIONS. Can go back to school once the lesions are crusted over. Vaccine information statement (VIS): information statements that MUST BE GIVEN to parents before administration of given vaccines Impact of febrile illness: LIVE VIRUS is not administered to anyone with an altered immune system or severe febrile illness. COLLABORATION Case Management: the ability to develop an appropriate plan of care based on assessment of clients and families. To coordinate needed resources and services for the clients well-being across a continuum of care. Coordinate care for multiple clients with complex issues. This usually involves clients who are at greatest risk for needing extensive coordination of health care services (e.g., clients with neurological disease, trauma victims, and clients with complex medical or psychiatric conditions). A care coordinate or manager should be appointed early in the discharge process. Individuals present at a patient care conference: Family and key health professionals! Roles of the case manager in coordinating multiple services: They collaborate with others in the planning and implementation phases to ensure appropriate care after hospitalization. STRESS & COPING Sibling reaction to ill child: May feel guilt, jealous, or resentment toward the ill child. Sibling may need play therapy too Major stressor of hospitalization in younger child: major stress from middle infancy throughout preschool years is separation anxiety How children cope with a terminal illness diagnosis: Periods of sadness and anger are normal in the child’s adjustment to a chronic illness. Allow the child to express their opinions, encourage play therapy, promote normalization (let child have as much control as possible). Tell them it’s okay to cry. Preschoolers think they caused the illness!!! How children view hospitalization: think they caused the illness and feel guilty. They think it’s a punishment!!! Communication with parents: empower and enable parents to take care of child. Ask open ended questions esp at diagnosis. Sometimes parents don’t want to tell the child about their illness---let them know that children are ill and know when they are dying. Establish a support system with grief to deal with the child’s illness. Assess they’re coping and if they have family/friend support. SATA- which shows effective coping- parent says “I know my child is dying and it hurts”, says she’s grateful for her friend that helps her, one more? -Parent seems asking same question- keep answering patiently GRIEF Children’s reaction to death: Preschoolers are magical thinkers. Believe their thoughts are sufficient to cause death; the consequence is the burden of guilt, shame, and punishment. May feel guilty and responsible for death School-age children still associate misdeeds or bad thoughts with causing death and feel intense guilt and responsibility for the event. They have a deeper understanding of death in a concrete sense. Are interested in funerals and burials, want to know what happens to the body. Test-father is dead and parents say he’s in heaven. Child sees father and says is this heaven? Adolescents have most difficulty dealing with death Children attending funerals: it depends on the child! Age group that has the most difficulty dealing with death: Adolescents Helping parents and children deal with the death: If parent needs time with the child/baby— give it to them! Grief responses by parents: They are initially at disbelief when their child is ill, injured, or hospitalized SIDS (sudden infant death syndrome) Back to sleep campaign helped raise awareness for this. Breast feeding may help prevent this Risk factors: Smoking (during pregnancy or in the environment) Co sleeping Prone sleeping Prolonged QT interval Soft bedding