2011-2012 Academic Year
CARDIOMYOPATHY FELLOWSHIP
Goals
• To provide the necessary skills for the fellow to become an expert in the field of
inherited cardiomyopathies, which includes understanding the pathophysiology and
genetics of these conditions as well as understanding the role imaging and
hemodynamics plays in diagnosis and management.
• To provide the necessary skills for the fellow to become a clinical investigator to study
these conditions further.
Curriculum
• Fundamentals of Genetics
• AHA & ESC Classification Scheme for Cardiomyopathies
• Genetics of Inherited Cardiomyopathies
• Genetic Screening & Counseling
• Dilated Cardiomyopathies
•Pathophysiology
•Diagnosis
•Treatment
•Genetics
• Hypertrophic Cardiomyopathy
•Pathophysiology
•Diagnosis
•Treatment
•Genetics
• Athlete’s Heart
• Diagnosis
• Differences with HCM
• Arrhythmogenic Right Ventricular Cardiomyopathy
•Pathophysiology
•Diagnosis
•Treatment
•Genetics
• Restrictive Cardiomyopathies
•Pathophysiology
•Diagnosis
•Treatment
•Genetics
• Left Ventricular Noncompaction
•Pathophysiology
•Diagnosis
•Treatment
•Genetics
• Other cardiomyopathies, including but not limited to:
• Ischemic
• Viral
• Toxin-mediated
• Drug-mediated
• Inflammatory
• Familial Storage Diseases
• Deposit-mediated: Hemochromatosis, Amyloid
• Neurologic/Neuromuscular (i.e. Limb-girdle muscular dystrophy, Duchenne’s)
• Endomyocardial (i.e. hypereosinophilic heart disease, endomyocardial
fibroelastosis)
• Stress-mediated cardiomyopathies
•Imaging Modalities with Cardiomyopathies
• Echo, including stress echo
• MRI
• Nuclear, including cardiopulmonary stress testing
• CT
• Hemodynamics
•HCM & RCM particularly
Clinical Responsibilities
• Inherited Cardiomyopathy Clinic
•Heart Failure/Transplant Clinic
• Inpatient Consultation Service
• Echo lab - 2 days a week with additional exposure in the clinics
•Special focus on inherited cardiomyopathies
•Participation in the Heart Transplant Recipient Review Committee
•Participation in Genetics Conferences
•Cardiac Cath Lab •Particularly participation in invasive assessment of pts referred by the Inherited
Cardiomyopathy Service
• Participation in Cardiac MR when possible
• especially if referred from the Cardiomyopathy Service
•Participation in cardiopulmonary stress testing
•2 months at UCL •Participation in the inherited cardiomyopathy clinics
• Attendance of Cardiomyopathy Meetings
•Involvement with research projects, if available
•Observation (? Participation) in any relevant invasive procedures such as
alcohol septal ablations, myomectomies
•Research
•Participation in research protocols/project
•Investigative Medicine Courses •Introduction to Biostatistics in Clinical Investigation (dates for this course
for this past year were July 12-23 M-F 8:30-11:15)
•Principles of Clinical Research (dates last year were July 26-August 6 MF 2-4)