Motor Speech Disorders Apraxia of speech and dysarthria First The SLP does not fix or improve anyone People fix themselves (or not) Requires Willingness Ability Establishing these is as or more critical than all the other diagnostic stuff we are usually taught For example Hypernasality can be caused by weakness of soft palate Strain-strangle dysphonia can be caused by hypertonicity Apraxic articulatory breakdown can be caused by dyscoordination Patient one So what do you hear? Strain-strangle dysphonia Whitaker on CD Slow rate Hypernasality Consonant imprecision Trend toward equal and even stress Medical diagnosis Progressive supranuclear palsy (PSP) Speech first abnormality in 35% of cases Typical dysarthria Hypokinetic Ataxic Spastic Note her hands appear normal as is her gait Often mistaken for Parkinson’s disease This lady has spastic Tight dysphonia Slowness Hypernasality not so severe Often called pseudobulbar Treatment The best treatment we have is skill treatment To increase differentiation of voiced and voiceless To improve rate To normalize stress Program will be featured at appropriate time Example Reported gradual onset Speech difficulty Which she called difficulty pronouncing words And once she called it stuttering Denied any cognitive or linguistic difficulties and mostly she is right No postural, gait or upper extremity deficits Patient two So what do you hear? What does she have? What would you do? Hear Slow Effortful Syllabification Mild articulatory errors Trend toward equal and even stress Dx Primary progressive apraxia of speech Tx Skill training at sentence level Neuroprotection Evolution Decline can occur over many years Nearly inevitably pts become mute Condition evolves into Dementia PNFA Corticobasal degeneration Progressive supranuclear palsy Amyotrophic lateral sclerosis Leading to what some call progressive anarthria Example What do you hear? What do you think the disease might be What would you do Dyscoordination What do you hear? What do you think the condition might be What would you do about it One type What do you hear? What might the medical condition be What do we do? Treatment: other pathophysiology Some like depression and apathy usually require Meds Psychiatry/psychology like poor attention can be managed behaviorally Functional components Lips Jaw Tongue tip and back Soft palate Larynx For example Weakness in respiratory muscles Leads to inadequate loudness and often short phrases The treatment is respiratory muscle strengthening Who knows how to do that? Followed by skill training So, question for you Which of the treatments you use (or have heard about)results in making patient stronger Which increase background of effort Which increase skill For example If a patient’s speech abnormality is not related to weakness then it is a waste of time to use strengthening treatments Also a waste if weakness is present but not severe enough to influence speech (which is most of the time by the way) Regardless of technique or type of deficit Motor speech therapy must be cognitive motor therapy to be maximally effective MUST start here Lansford et al (2011). A cognitive-perceptual approach to conceptualizing speech intelligibility and remediation practice in hypokinetic dysarthria. Parkinsons Disease, doi 10:4061/2011/150962 Six parts the way we do it-THIS IS HOW ALL TREATMENT STARTS Why important ? Anyone here not heard a patient or family member say “He talks really good when he remembers” ? Or, “He talks really good in therapy but not at home”? Learning what to do is usually relatively easy Remembering to do it is godawful hard Thus We ought to spend more time in therapy helping a patient remember Rather than-as we do now-teaching them what to do 1. Flip the switch Flipping the switch means engaging volitional- purposive control Tx follows a rough shape Teach, flip the switch Emphasis on planning every utterance prior to production-extremely challenging Many pts hate this and acceptance requires counseling And promise that with luck they will not have to do it for all time We tell them what we call it and they can use that or some other name But pt MUST agree to flip Otherwise they are at mercy of phonetics and spontaneous recovery Procedure continued We try to be creative in helping pt identify a cue to prompt the planning (flipping) Such as a slight shift in posture Or quick inhalation Or gesture Then practice, practice, practice On patient generated responses as opposed to imitation whenever possible 2. Listen and evaluate flipping the switch and response adequacy Must attend to evidence switch was flipped and Pt must come to be best judge of speech adequacy- loudness, rate, precision, etc Pt and cl agree on a scale of adequacy Three points which pts usually immediately turn into 5 (1.5 2.5) Anchors : 1= the speech they came to you with and 3=the best possible speech We drag out one of these 1 2 3 4 Old speech 5 Best possible Best possible Next Get as complete a view of what pt requires to assign the higher scores May have to negotiate this if pt only accepts normal If at all possible elicit a functional response from pt First warning them that they will be responsible for assigning a scale score Then the pt followed by the clinician evaluate the response Differences are resolved Repeat Continue resolving differences A bit of slop in the scale is unavoidable Scaling rate Here is an example done by students-their first time Thus there are multiple ways to improve what they did We will discuss those Go to the audio: ataxia liver transplant 1 & 2. Flip and judge We use these with all patients At some time-usually as early as possible-in the therapy These are among the critical conceptual or cognitive parts of treatment They take time but it is time well spent in our opinion Then there are at least four more cognitive manipulations in much of our treatment 3. Preparing patient to judge effort This is the effort the pt feels is being invested in talking therapeutically Cl and pt work out a 3, 5 or 7 point scale of effort Pts reject treatments even ones that improve intelligibility and naturalness if they perceive them as requiring too much effort (5,6,7) Can write effort reduction goal Effort continued We try to move folks at least two effort points We have a rough notion that effort that stays in range of 5-7 is harmful to carry over Effort in the 1-3 range is better Effort seems to be mostly concentration for our folks We score effort only once per session usually We have them score themselves outside clinic as well 4. Speak therapeutically Patients must be willing to speak therapeutically For us a major component of that is “keeping speech in a box” That means doing all the planning and evaluating And avoiding long utterances without control Don’t tell me the whole story tell me one thing The issue The best treatment for speaking is not speaking The best treatment for speaking is speaking therapeutically One critical component It seems important as well that there be a balance in expectations early on in tx A balance between what the pt wants from therapy What the clinician thinks is possible If there is a gap then that gap must be resolved Or treatment is likely to fail Pt wants Cl expect TO AVOID FAILURE Need to work toward Cl expect Pt wants or Cl expect Pt wants 5. Remember your brain is plastic We speak about “getting your brain to substitute for the damaged nervous system part(s)” Example of ataxia secondary to cerebellar damage In other words we use plasticity language How worded depends, of course, on ability and understanding of each patient So what is this? Bit of treatment Status post MVA without LOC Post So what do you conclude? One session of tx Three weeks or so later she sounded as you hear 6. Adding cognitive-linguistic load We begin with as much cognitive-linguistic load as person can manage And then add as much as we can as fast as we can Imitation is of limited usefulness although it may be important for a few repetitions early in treatment Means Manipulating complexity of answers required by Q Having pt select what to practice Means introducing competition into the session Have person do an entirely different activity and then switch back to the Q-A LOAD Requiring longer responses And series of responses for example in the telling of a story And requiring pt to evaluate several answers at one time rather than evaluating after each And bringing in other communication partners And making it a group activity And trying to duplicate this arrangement in the pt’s environment Admittedly This is a lot And we may not require all of this and in fact don’t in the beginning May introduce rules as treatment moves along HOWEVER if a patient is not finally able to do all these things improvement will be Limited and Contingent mostly on environmental cueing Putting it all together This is a program of my design using bits and pieces of numerous “individual” programs A program that can be made to work with the most severe to the mildest, regardless of speech diagnosis And the clinician can enter the program anywhere depending Begins (cause has to begin somewhere) with an emphasis on articulatory competence In any motor speech disorder characterized by articulatory errors including omissions, distortions, substitutions and distorted substitutions All the dysarthrias and apraxia of speech But expands to treat all of speech Putting it all together And can easily be shaped to work on all aspects of prosody Including rate and abnormal pitch and stress Again without regard for speech diagnosis And respiratory mechanism, larynx and palate That has independent functional speech as its goal It is a false assumption that hard work under tightly controlled clinical conditions produces treatments that generalize Generalization steps MUST be built in Heart is Sound Production Therapy SPT was originally developed for AoS using minimal pairs Data are strongest in apraxia “individuals with apraxia of speech can be expected to make improvements in speech production a a result of treatment, even when apraxia of speech is chronic” Wambaugh et al (2006a). Treatment guidelines….JMS-LP, 14, xv-xxxiii See also: Wambaugh et al (2006b). Treatment guidelines for acquired apraxia of speech. JMS-LP, 14, xxxv-Lxvii Unfortunately no data for PPAoS SPT Five step program, from less to more cueing Depends on minimal contrast pairs in words For example, p vs b (voicing)-where they started One sound is (usually) the target-usually voiceless Fifteen treatment sessions: and we and they recognize the challenges here Wambaugh et al (1998) Effects of treatment for sound errors in apraxia of speech. JSLHR, 41, 725-743 Components Modeling Repetition Minimal pair contrasts Integral stimulation Articulatory placement cueing Feedback To prepare for it Clinician needs to understand the articulatory errors in each patient’s speech Lets listen to two patients with different speech diagnoses So here is patient for us to treat Listen to connected speech very severe and later All you need to hear to be able to begin fashioning treatment What would you work on? He tries to say “Madison” And another Can be adapted for a variety of other neuropathologies Starting with those having increased tone usually called spasticity A cardinal feature of such patients is that they have difficulty turning the larynx off Same as in apraxia Thus voice for voiceless substitutions and common The contrast then is between voiced and voiceless sounds To demonstrate will start with a severe, obvious case Which adds to the relevance of discussing program basics first Errors Total distortion Voicing is pervasive Plosion is also Sound production treatment (SPT) The Pittsburgh group has structured a number of traditional steps into a useful partial approach Stimulus selection is key to making it broadly useful Fricative vs plosive voice vs voiceless Program has been subjected to experimental scrutiny in a series of single case studies with replication The first minimal pair they treated was /p/ and /b/ But clinicians can use anything they want Step one: modeling imitation Clinician produces both in pair and pt says both If error, then each one of pair presented and produced separately If both correct, repeat and on to next pair Provide knowledge of results (good, okay, etc) Already seeing need for change, right? If not correct, step is repeated If still not, go to next step Hardest step Is imitation Thus you can see this is a rigidly controlled program Allows patients no anonymity Attempts to keep error rates low The problem is that the brain learns more from errors than from correct responses Step two: modeling + Cl shows printed (known for generations that apraxic talkers especially are likely to profit from visual-in this case reading-input) versions of the target Say “this is the sound you are working on” Then repeat step one If BOTH okay go on to next pair If not, go to next step Step three: Integral stimulation If only target is wrong earlier or if both are then only target (or both) is subjected to integral stimulation Watch me, listen and say what I say Rbt Milisen from the 30s If correct try to get two to four more repetitions If correct go on to next pair If target (or other sound in my version) is incorrect go to next step Step four: modeling with juncture Cl produces the target using silent juncture after the target and before the rest of word P………….it If correct, go to next pair If not, go to next step Step five: articulatory placement Cl provides verbal description of sound and produces it in isolation To make a /p/ put lips together, build up a bit of air, then puff the air out by quickly opening lips Correct or incorrect Cl go on to next pair Or as a permutation, simplify the context Although as designed the program used words Stimuli Usually use 8 to 10 stimuli (for ex: pit-bit, par-bar, pan ban, pot-bought, etc In substitutions use sound that most frequently substitutes for the target Try to work at word or phrase level Try to use all stimuli in each session Try to get through all at least 4 to 8 times per session The data Trained and untrained items improved Generalization was limited As was maintenance or stability over time Subjects had aphasia and apraxia A PROBLEM IS OVERGENERALIZATION OF THE SOUND TREATED So if treating /p/ it began to appear for /b/ Over generalization A huge problem But worse in AoS than in any other motor speech disorder Possible answers: Treat more than one sound pair at a time Treat different manners such as fricatives and plosives Use at least quasi-random presentation of stimuli so pt has to change set Commentary This program uses all the traditional approaches It is the time honored task continuum The study itself is controlled in the traditional ways with generalization probes, baseline line and maintenance probes Value of this report Can do the treatment based on it Some of our very best data And it is a spring board for further creative treatment development Problems In addition to overgeneralization of treated stimuli Have too little generalization across time-in other words has less than satisfying maintenance of effects They have gone to work on the issue Wambaugh & Nessler (2004). Modifications of SPT…Aphasiology, 18, 407-427 Revised SPT Wambaugh & Mauszycki (2010). Sound production treatment with severe apraxia of speech. Aphasiology, 24 (6-8), 814-825 This article on treatment of one severe pt contains a revised form of the protocol in response to some issues Who by the way had a recurring utterance that was pieces of the one phrase-I want water-that had been her practice item in earlier therapy Modified protocol Used “minimal pairs” and actually multiple stimuli Set 1 w vs b, s, l Set 2 w vs m, d, f So you can see that manner, voicing and place are all manipulated W was because that was sound that pt produced nearly inevitably More contrasts absolutely critical Also less frequent feedback-also critical It worked in the clinic testing However We have some apraxic persons (and some dysarthric) so severe that they cannot work on words and sometimes not even sounds BTW must guarantee that such patients are not more severely aphasic than apraxic Thus lets extend the program at the bottom So lets expand SPT For severe, single sound and maybe even nonverbal movements If single sounds CATE would say that it is more efficient to choose difficult, less stimulable-complxity account of therapeutic efficacy So /sh/ rather than /s/ for example Because one gets greater generalization Depends on the amount of co-existing difficulty The purer the apraxia, for example the more likely CATE is to be a good idea But move the single sound into a word ASAP And only work on one if doing more is too hard Will demonstrate a pt in a moment Oral nonverbal movements Students are taught they are critical to speaking-NO Neural circuitry controlling such movements are different from speaking Maas and colleagues predict that generalization to speech is unlikely Maas et al (2008). Principles of motor learning in treatment of motor speech disorders. AJSLP, 17, 277-298 Rules on oral non-verbal movements They should generally be a last resort tx target Those you choose should resemble real speech acts Clark (2003). Neuromuscular treatments for speech and swallowing: A tutorial. AJ S-LP, 12, 400-415 Generalization will not occur unless you structure treatment to specifically cause generalization Contrast Too much Just right sometimes Clinician needs to be even more basic To prepare a person’s body to talk So lets expand SPT Prostheses single sounds/nonverbal movements Prostheses Palatal lift Nasal insert Bite block Maxillary reconfiguration Abdominal binder Example Person with MS needing a belly binder Another Person with stroke needing laryngeal manipulation Another Person with stroke needing a palatal lift or other palatal management New device using Passey-Muir valves Here is an example Going to leave presentation so I can manipulate the samples if need be Polke Expand more Prostheses Posture SPT with multiple stimuli (words) usin Imitation For severe single Visual, written Sound and maybe even Phonetic placement Nonverbal movements Posture General Best is normal sitting Although prone is sometimes good if respiration reduced Stabilized, especially in adventitious movements Head Level Jaw up (mouth closed) Stabilized, especially in adventitious movements Example Person with multiple system atrophy (a form of parkinsonism) Needing increased background of effort Consider this pt KS DVD What is going on with her? What would you do? SIMPLE Get person is best upright posture Provide instruction and respiratory support By pressing respiratory muscles with hands Have pt say low cognitive-linguistic load utterance such as counting Experiment with varying pressures on inhalation and exhalation Have pt provide the respiratory support Expand more Prostheses Posture Compensations SPT with multiple stimuli (words) usin Imitation For severe single Visual, written Sound and maybe even Phonetic placement Nonverbal movements Compensations Sensory tricks in dystonia Amplifiers AAC Here is a dramatic example What does he remind you of? What does his compensation do? Go to GS DVD So lets expand Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements Program easy to expand Can create a kind of procedure drop down menu For now we will stay with single words as stimuli To demonstrate will assume using /p/ /b/ /s/ and /t/ And have created a list: pie, by, sigh, tie; pick bic, sick, tick; pack, back, sack, tack; poor, bore, sore, tore The menu Lay out all in written form and tell pt to choose one say it and I (clinician) will report what is heard Patient says a self-selected word from those worked on or another word with the target (no visual stimuli) and asks clinician to say it back I love these tasks Often speech is better here than in other tasks (even some “easier” ones) Or use same stimulus and multiple different responses-give me one of the words, now another, now another Or introduce competition-have pt make a gesture between each utterance Turn on recorded noise during practice More Clinician spells and has pt say what was spelled Clinician defines a word and patient says Clinician asks for a rhyming word So That’s eight additional “steps” I am sure you could add others I have no idea if these can be rank ordered for difficulty Probably doesn’t matter What’s important is They use principles of skill building They provide variety which is badly needed in speech rehab They make treatment cognitive And some give pt more autonomy Purpose of these All may enhance generalization They may slow acquisition So you have to decide what your goal is Good performance in clinic Good performance outside Techniques that give one seldom give the other Pt has AoS Isaiah DVD tx Working on words Using CATE /s/ /t/ /st/ Using visual cause it helps him as it does most with AoS unless they have too much aphasias So lets expand Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements Sentences Sentence stuff Use some of the previous words (if tx began with words) With apologies: I got pie on my tie and so on Or if patient is mild-moderate may be able to use almost any sentences Which we do in our neuroprotective programs Can even use imitation-diagnostically- to be sure pt has the motor ability under controlled conditions to handle what you (or they) have created Expanding sentences Can use many of the permutations already discussed for words Tell me the sentence that tells me something about your tie Give me another sentence with the same key word; now give me another sentence; another Say any sentence and I’ll tell you what I heard This is actually an easier step with sentences than with single words BTW the best step here would be for the pt to create the sentences Here now can realistically work on rate and other aspects of prosody as well Say it faster Say it with stress on ________ An example Pt has an apraxia plus he did not receive any therapy for months Using CATE-specifically /j/, the hardest sound on average for persons with apraxia of speech Work on words (and risk overgeneralization) cause I use same sound for awhile Go to audio again so can manipulate as time permits Begins with single words written and my pointing to them-no imitation unless necessary Then use the hardest contrast Move around from word to sentence and back First word is “yes” So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements Sentences Here is an example This lady has multiple medical problems And a complex dysarthria with ataxic features dominating This is an early session I give her my standard set of admonitions Fricatives are difficult as is control of all aspects of prosody Thus goal will be to work on both simultaneously Ataxia liver stroke Contrastive stress drill Way to approximate communication Contrastive stress drill is a Q-A drill Could be used even with single words Idea is for cl to ask a variety of Qs about components of sentences already worked on in other ways For example Stimulus: I got pie on my tie Drill Cl: Did you get tooth paste on your tie? Pt: No, I got PIE on my tie Cl: Did you get pie on your shoe? Pt: No, I got pie on my TIE And so on Cerebellar degeneration Contrastive stress drill Goal is less on specific points of articulation More on prosody Especially on rate and rhythm Other forms of cognitive-linguistic load As evidence that many methods are totally ignorant of what we think they are good for Contrastive stress drill PACE: Promoting Aphasic Communicative Effectiveness Stimuli are put on cards and placed between cl and pt Take turns selecting one and saying it without showing to other person Scripts: Create two or more sentences to tell a more complex story I will not embarrass all of us with an example So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements Sentences GROUPS Communication Partners Groups Inserted at end in this presentation but can actually be used from the beginning Limited data but consistent with expectations Communication partners Developed for aphasia but can also work in dysarthria Hunter et al (1991). The use of strategies to increase speech intelligibility in CP. BJDC, 26, 163-174 Communication Partners Bring other people into the clinic suite The principle is that a learned response is most likely recovered in an environment that resembles the one in which it was learned No wonder families say,” He talks so much better to you than to me.” Bit more on method No need to go far here as this is the birthplace of the idea But to be clear This is not bringing others in for education in a traditional sense This is a method for making others skilled, facilitating communicators For example Partner training Hunter et al (1991). BJDC, 26, 163-174 Excellent modern version of this is by Borrie et al (2012). Perceptual learning of dysarthric speech: a review of experimental studies. JSLHR, 55, 290-305 The data based lessons Listeners can be taught to understand and this is a critical part of treatment Clinicians learn as well and that may contaminate their view of how much better the pt is So what have we done? Taken the original five-step AoS program and made it a menu Best of all perhaps is having added more functional steps And these functional steps serve to move this from a focal (articulation) therapy to a more general therapy That can be used to modify not only articulation but also prosody including rate So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements Sentences GROUPS Communication Partners Move to more functional But what about apps and DAF They are not treatments They are adjuncts They can be fit into the framework So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements DAF Amplifier Etc Sentences GROUPS Communication Partners Move to more functional Here is one ex What does it do to naturalness of speech Data on rate reduction from Yorkston et al 1990 Intelligibility systematically improved for both groups-ataxic and hypokinetic Greatest at 60% of habitual Some subjects could not tolerate or achieve the 60% Finding the right percent of habitual is worthwhile Rate manipulation can be a powerful tool for a general approach to dysarthria treatment Don’t neglect the simplest stuff Six or so studies of simple directions to encourage some form of “try to speak more carefully” have been published Yorkston (1996). JSHR, 39, 546-557 Building improved speech from basic background of effort And a bit of prosthetic bracing of respiratory system can also be good starts Transition Lets move from this discussion of skill training to methods that seem to combine elements of skill and strengthening And can form a foundation upon which the skill training can be imposed Thus may begin with the two types of therapy to be described Maximum performance training Strengthening So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements DAF Amplifier Etc Maximum performance Strengthening Sentences GROUPS Communication Partners LSVT All permutations of this program require certification In the interest of fidelity to the protocols Thus I cannot teach it As probably all of you know the emphasis is on maximum performance at least initially And it is most studied for effects Maximum performance training:our view May influence both skill (learning to use enhanced effort) and endurance The idea is simple: have pt perform quality maximum performance tasks And learn to transfer that effort to speaking An absolute minimum of 25 per day, five and preferably six days per week Steps Get pt in best posture-usually sitting upright Have pt increase background of effort-valsalva Have pt get to best size-appropriate inhalation Check or hold that inhalation so air does not escape in a rush Then start maximum duration of vowel With attention to consistent airflow, loudness and quality Repeat enough so that you get a sense of duration person can achieve with control Steps, cont Cue pt to the sound and feel of this maximum performance mode Carefully monitor for laryngeal hyperfunction, pain, dizziness, other discomfort Have pt get a timer URGE maximum, consistent performance Work as hard as you need to to transfer the same intensity and effort to speech using short sentences heavy on plosives Further steps Some of the steps or procedures listed in SPT can now be introduced If the patient can identify appropriate loudness and if effort is not 5, 6, 7 then adding to the cognitive linguistic load is next Without these steps generalization is unlikely Bonus It appears that LSVT and other maximum performance training influences more than just the larynx Even some evidence from LSVT that lingual strength improves How is that possible? Moving on More or less pure muscle strengthening But by self unlikely in majority of patients to have functional consequences So lets expand Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements DAF Amplifier Etc Maximum performance Strengthening Sentences GROUPS Communication Partners Strengthening Have some for respiration Emphasis here cause of data Although in swallowing For the tongue For the velopharynx And perhaps, depending on what you believe, for pharynx Methods for respiration are Expiratory muscle strength trainers (EMST) With main effect on respiratory muscles other than diaphragm Inspiratory muscle strength trainers (IMST) With main effect for diaphragm Warning: no data based guidelines on which to use but will describe ours after description of methods Candidacy Those with respiratory system weakness or reduced endurance Can potentially be just about anyone with a neurodegenerative disease So long as they are not profoundly weak Those with respiratory system rigidity PD, MSA are prime examples Perhaps even those with hypertonicity Potentially any of the parkinson plus syndromes such as progressive supranuclear palsy (PSP) Strengthening those with hypertonicity does not increase tone Relevance Respiration provides critical air pressure and flow for speech Reduced respiratory drive can influence all other components of the speaking mechanism Respiration is coordinated with swallowing and respiratory deficit can influence swallowing efficiency and safety Some superficially oropharyngeal abnormalities may be secondary to inadequate apneic period as but one example EMST Pt blows into a device fitted with a one-way spring-loaded, pressure release valve Amount of pressure can be controlled Increasing the pressure to open valve can increase respiratory drive Training based on 70%80% of maximum expiratory pressure (MEP) Or on clinical judgment EMST This device calibrated from approximately 5 to 140 cc of H2O So covers most of the range of normal pressures Cost 60.00 or so plus shipping Can order from www.aspireproducts.org Another view This is a good diagram of the device At left end (in this view) is the cap that can be tightened or loosened to influence pressure Training load Can measure maximum inspiratory and expiratory pressures and train at 70-80% of max Using a spirometer Or can set clinically-judge the work or effort Remember the principle of overload Muscles to strengthen must work harder than they work ordinarily Basic treatment guideline EMST set at 75% of MEP (or clinically) Nose clip and cheek/lip press-CRITICAL 25 trials per day in five groups of five I prefer more reps in two groups Five sessions per day is burdensome Five days per week I prefer 6 Five weeks and I prefer 3 months or even longer Cheek lip press Critical to maximize flow thru mouth Minimize through nose Enhance lip seal Pt can do or caregiver may have to Reality of treatment Any pt with cognitive decline may have trouble learning the steps Take deep inhalation Place device in mouth Press cheeks and lips Blow hard and quick Quit when you hear (or feel) that pressure valve has opened Distinguishing from flow around device takes practice REMARKABLY HARD FOR BOTH CLINICIAN AND PATIENT TO LEARN Especially early in clinician’s use and for patient with cognitive decline or multiple system involvement Thus Often need our whole bag of behavioral tricks We have been training MSA and PSP Nearly inevitably have to begin them with just blowing and then blowing harder Then introduce the device but at no resistance Then hold cheeks for them (or get caregiver to) And then help mold their holding of device and of their cheeks Method continued Add just the smallest amount of resistance (approx 5 cc of water pressure equivalent) And then repeat, repeat, repeat Hone them in on the sound of quick airflow that signals the valve has been broken Educate caregiver as well THE CHEEK/LIP SEAL IS CRITICAL Sometimes takes several sessions merely to learn how to use device Aim Originally designed to improve strength of respiratory mechanism With thought that stronger system would be able to support sufficiently long apneic period And better, especially louder speech And perhaps produce a respiratory system better able to support and coordinate with the other parts of swallow and speech mechanisms The literature Best article is Kim, Sapienza. (2005). JRRD, 42, 211-224 Best book is Sapienza & Troche. (2012). Respiratory Muscle Strength Training. Plural Publishing Strict schedule worked out 25 repetitions per day in 5 groups of 5 At 70%-75% of maximum expiratory pressure Home practice 5 out of every 7 days Weekly visits for 4 weeks (minimum) to reset device if strength improving Can train for longer or shorter Will likely need to combine with other txs Summary of uses So far used to treat speech and swallowing in PD, MSA, stroke, Lance-Adams, some inherited ataxic disorders, COPD, MS, Pompe, ALS, ventilator dependent (usually inhalatory) Results are tentative with all groups Strongest with PD Appears that hypophonia can be reduced-but not without accompanying skill training Intelligibility improved Airway invasion reduced Cough strengthened BUT NOT IN EVERYONE Cough in PD Pitts et al (2009) Utilizing voluntary cough to predict penetration and aspiration…Chest, 135, 1301-1308 Two findings Voluntary cough predicts penetrating and aspirating PD pts Voluntary cough competence is improved by EMST at the previously discussed frequency and duration Masked facies Data showing that computerized images of facial expression reflect improvement in masked face In mild and moderate patients with PD With caregivers and patients reporting improved communication IMST used Unpublished data by Bowers (2013) Our program: once again 75% of maximum expiratory effort 25 reps divided among at least two sessions Six days per week For 4 to 12 weeks, OR LONGER, depending on response Visit clinic once per week for adjustment and drill Contraindications Untreated cardiac abnormalities Untreated HTN Till MD approves post surgery anywhere in body RECALL: this is real exercise What is happening SLPs are hearing about this Trying it sometimes even unsuccessfully on themselves Are unsuccessful and reject the method Or try unguided with a patient, fail, and reject the method Or they try it without transfer techniques and person gets stronger but nothing else changes IMST DEVICE Order from: WWW.RESPIRONICS.COM This device is calibrated for 0 to 40 cm of H2o So good for very weak Use of IMT Notion is to get quick, smooth, deep inhalation using diaphragm Followed by long controlled exhalation These two actions roughly parallel speech breathing especially by some treated dysarthric speakers Need to inhibit exaggerated shoulder raising and other maladaptive responses Use nose plug Systematically increase resistance based on pt performance When to use IMST when diaphragm is focally or more weakened than other respiratory muscles As can happen in phrenic nerve damage Not so likely in the neurodegenerative diseases May come to point when both are used And some are beginning to argue for the primacy of IMST because of the importance of sufficient inhalation The main idea for both I and E The treatment data in PD are positive The data and protocol can be used as a guide for interventions with patients having similar control abnormalities Rigidity or Weakness or Reduced neural drive generally Recommendation EMST and IMST are not cure-alls Often will have to be joined by one or more skill treatments But are powerful new tools Including for reduced cough, a common sign in a variety of neurodegenerative diseases Because of Neurology publication going to spread into clinics rapidly Clinician training can be accomplished in one day The program Contrastive stress PACE SCRIPTS Prostheses Posture Compensations Sound nonverbal SPT Single word with refinements DAF Amplifier Etc Maximum performance Strengthening Sentences GROUPS Communication Partners Summary Treatment must be cognitive I outlined the treatment options In hopes of giving us something to do for the full range of persons from most to least severe Qs Thank you very much