MA Assessment and Treatment Aynsley Brian, Brittany Garay, Caroline Johnson, Sarah Williams and Melissa Gutierrez Assessment • Periodic assessments are needed due to the different times in development that a child with a cleft can experience communication issues. • • All children with a history of a cleft or craniofacial are at risk for communication disorders Risk for communication disorders for a child with cleft of the primary palate is due to dental abnormalities. Cleft of the secondary palate puts the child at risk for the possibility of a fluctuation of hearing loss and VP dysfunction. These factors can cause problems in the areas of articulation, language, phonation and resonance at different times in development. Continuing Assessments • Perceptual and instrumental measures should be done prior to surgery to aid in improvement of speech and resonance afterwards. • A post-op assessment should be done to determine the effect of surgery on speech and possible further need for intervention. • Annual screenings with the craniofacial team is conducted until 4 years of age. • The child should receive a speechlanguage evaluation around age 3. Diagnostic Interview • Parent and family interview • If possible, obtain information prior to the interview about the child’s medical and developmental history and parent’s current concerns about speech. Possible Questions • Was your child quiet, average, or very vocal as an infant? • Does your child have any difficulty chewing, sucking, or swallowing? • Does your child snore at night? • Has your child ever had a speech evaluation or speech therapy? • What concerns you about your child’s speech? • What sounds does your child currently use? • Does your child sound nasal to you? • How does your child communicate? • Was your child born with any congenital problems? Language Screening • Observe the child and make note of their play behaviors, ability to request, follow commands, their spontaneous speech production, and repetition. • Done throughout preschool years • Done yearly at cleft palate team visits • Can be done via parent questionnaire Speech Evaluation • • • • Formal articulation Tests Templin-Darley Tests of Articulation Bzoch Error Pattern Diagnostic Articulation Test Iowa Pressure Articulation test o Designed for assessing VP function o Tests are easy to use, however only assess children at the single word level Informal Articulation Assessment • Informal assessment of the child’s articulation at the sentence level provides better information about the child’s current functioning. • Informal articulation assessment measures include syllable repetition and sentence repetition. Samples should contain many pressure sensitive consonants that are voiceless. • To assess hypernasality, the sample should contain voiced oral sounds. • To assess hyponasality, sentences should contain high frequency of nasal phonemes. Assessing in connected speech • Counting and rote speech could be used with children. Assessing the child during connected speech could be difficult, so have the child count or recite the alphabet. • Hypernasality, articulation errors and nasal emissions are more apparent in connected speech. What to evaluate? • Articulation- important to identify the type and potential cause of errors and types of compensatory errors if present. o Stimulability- is the child stimulable to correct erred sound by merely changing placement? If so, this is a good prognostic factor for correction with speech therapy. o Nasal air emission- if present, determine the intensity, if there’s a rustle due to opening, or if a grimace is accompanied. o Consistency- how consistent are the errors or emissions. What to evaluate? • Phonation o Types and severity of dysphonia • Oral motor dysfunction o Is apraxia of speech present? If so, should cause errors in valve closing for oral sounds. • Resonance o Note whether normal, hyper, hypo, denasal, cul-de-sec or mixed o Determine type and severity Low and no-tech evaluation procedures Visual Detection • Mirror test: o Mirror held under nose in order to evaluate nasal air emission • Air paddle o Piece of paper is placed under the nose during speech tasks to determine if nasal air emission is present • See scape o Nasal olive is placed in the child’s nose and is attached to a flexible tube that’s connected to a rigid vertical tube. o As the child repeats pressure-sensitive phonemes, a styrofoam stopper rises in the tube is there’s nasal emission. Tactile detection • Feeling the sides of the nose o Vibration can be felt from hypernasality Auditory detection • Nose pinch (cul-de-sac) o Done by having the child produce speech with nose occluded and unconcluded. o In normal speech, no difference in quality should be heard. • Stethoscope o Drum of the stethoscope should be placed on either side of the nose. o Hypernasality can easily be heard through the stethoscope. • Straw o Place one end of the straw in the child’s nose and the other end near the examiners ear o Can hear nasal emission • Listening tube o A plastic tube that works like the straw and stethoscope o One end is placed in the nose and the other near the examiners ear to assess nasal emission Differential Diagnosis • Hypernasality and air emission can be caused by VPI, nasal fistula or articulation disorder • Important to know the cause since it can have a direct impact on treatment recommendations o If oronasal fistula is present: • Size and position can effect speech • Compare anterior vs posterior sounds to determine if it’s symptomatic • Close the fistula and compare occluded with unoccluded speech • If hypernasality or nasal air emission is present, it’s important to determine if it’s cause is structural or due to misarticulation o Is it due to a nasal rustle? o Is it phoneme specific? o Is the child stimulable? Follow-up • Recommendations: o Treatment recommendations may be surgical, prosthetic management, or speech therapy o Discuss results with primary physician o Should be based on cause, severity, and type of disorder. • Family counseling o Important outcome of the evaluation o Give handouts on useful information • Evaluation report o Must be accurate, succinct, clear and concise MA Recap • 8 year old, 1st grade student in regular classroom • DiGeorge syndrome and Pierre Robin Sequalae • Tracheomalacia o Tracheostomy tube secondary to tracheomalacia o 2 decannulations unsuccessful due to cyanotic • Complete bilateral cleft – repaired at 12 months o Sucking and feeding problems • Fed via Mickey tube until age 6 • Expressive language: apraxia, severe nasality and past use of AAC device Compensatory Errors with Pierre Robin • Misarticulations that occur as response to velopharyngeal dysfunction • Generalized backing • Velar fricative • Nasalization of oral consonants and vowels • Nasal sniff and snort • Pharyngeal plosive, fricative, affricate and nasal fricative • Glottal stop • Usually treated with speech therapy Obligatory Errors with Pierre Robin • Obligatory productions occur when articulation placement is normal but abnormal anatomy/physiology causes speech distortion • Short utterance length • Weak or omitted consonant sounds • Changed rate and speech segment durations • Nasalization of oral sound • Requires surgical or prosthetic intervention for correction Eliminating Misarticulations with Speech Therapy • Educate child on anatomy and articulator placement • Feedback o Visual: diagrams o Tactile: tongue blade, peanut butter o Auditory: contrasting nasal and non-nasal, Oral-Nasal Listener (or straw) Eliminating Misarticulations with Speech Therapy • Begin by training front sounds • Plosives: bilabials and linguavelars • Feedback: o Visual: mirror, yawn technique (to push the tongue down and the velum up) o Tactile: tongue blade o Auditory: open and close nose to contrast nasality Eliminating Misarticulations through Speech Therapy • • • • Pharyngeal plosive substitutions Start with /ng/ and transition to /k,g/ Coordination of air pressure/release Feedback: o Tactile: spoon or tongue blade to suppress tongue tip, palpating throat Eliminating Misarticulations through Speech Therapy • Pharyngeal fricatives and affricates • Feedback o Auditory: Straw (listening for airflow), alternate occluding nostrils • Linguavelars (/t,d,n/) • Feedback: o Tactile: biting tongue blade between incisors Childhood Apraxia of Speech (CAS) • Makes inconsistent sound errors • Can understand language much better than he or she can talk • Is hard to understand, especially for an unfamiliar listener • Has difficulty imitating speech • May appear to be groping when attempting to produce sounds or to coordinate the lips, tongue, and jaw for purposeful movement • Has more difficulty saying longer words or phrases than shorter ones • Speech may be affected by situational anxiety • Sounds choppy, monotonous, or stresses the wrong syllable or word Speech Therapy for CAS • The focus of intervention for CAS is on improving the planning, sequencing, and coordination of muscle movements for speech production. • Prosody training • Imitate words and sentences of increasing length • Getting feedback from a number of senses, such as tactile and visual cues (e.g., watching him/herself in the mirror) as well as auditory feedback • Home exercise programs for maximum stimulation Speech therapy for hypernasality and nasal emission • Effective when the nasality is due to misarticulations • Exception: residual hypernasality and/or nasal emission after VPI surgery and, occasionally hypernasality secondary to dysarthria • Therapy techniques are the same for hypernasality and nasal emission. Low-tech auditory feedback tools for hypernasality/ nasal emission • Straw o Place 1 end at the entrance of the child’s nostril and the other end in his ear. • Listening Tube o Used the same way as the straw • Oral & Nasal Listener o A dual stethoscope with the end of a tube placed in the child’s nostril OR a funnel added to the end of the tube and placed in front of the child’s mouth Low-tech visual feedback tools for hypernasality/ nasal emission cont’d • Air Paddle o Paper paddle placed in front of mouth while producing pressure-sensitive phonemes with enough air pressure to force the air paddle to move • See-Scape o While producing pressure-sensitive consonants, nasal olive placed in nostril that is attached to a flexible tube which is connected to a rigid plastic vertical tube containing a Styrofoam float High-tech auditory feedback tools for hypernasality/ nasal emission • Digital Recording Equipment o Audio recordings of normal and hypernasal speech used to help discriminate and self-evaluate High-tech visual feedback tools for hypernasality/ nasal emission • Nasometer o Reads sentences, aiming to keep nasality below the clinician-set threshold. • Pressure-Flow Instrumentation o Pressure-flow is recorded to correct articulation errors that cause phoneme-specific nasal air emission. • Nasopharyngoscopy o Allows direct visualization of the velopharyngeal movements in order to develop a degree of active control over the movements for opening/closing the valve Tactile feedback for hypernasality/ nasal emission • Raise velum up/down with tongue depressor while producing vowel sounds • Lightly touch side of nose and face to feel vibration • Yawn so that the posterior tongue is depressed and the velum is elevated in order to coarticulate the yawn with vowels and anterior consonant sounds Tactile feedback for hypernasality/ nasal emission cont’d • Increase volume • Increase anterior mouth opening • Pinch nostrils in order to feel increase in oral airflow and pressure Phonation • Dysphonia, impairment of any or one of the vocal organs, is common among people with VPI or craniofacial anomalies • Characteristics of dysphonia: Hoarseness Breathiness Glottal fry Hard glottal attack Inappropriate pitch level Restricted pitch range Displophonia (a condition where two sounds of a different pitch are produce simultaneously) o Inappropriate loudness o o o o o o o Phonation • Dysphonia in patients with cleft palate most commonly due to: o Increased respiratory and muscular effort o Hyper-adduction of vocal folds while attempting to close the velopharyngeal valve • The presence of dysphonia often masks nasality, making perceptual evaluation difficult • Increased vocal effort may also increase VP function and decrease gap size for better resonance • Should also note: o Quality of breath support o Type of breathing pattern o Ability to sustain phonation MA • History of tracheomalacia (weakness/floppiness of the tracheal walls) • Underwent a tracheostomy and used a tracheostomy tube for respiration • After attempts at decannulation, MA became cyanotic and had severe stridor (tracheotomy tube was replaced). Techniques for Therapy • Biofeedback-calls attention to automatic or unconscious physiological processes to manipulate with conscious control • See-Scape• Aerodynamics-pressure-flow instrumentation o provides objective documentation of therapy progress Phonation • Pneumotachograph-real-time feedback measures: o Inspiratory volume o Maximum phonation volume • To isolate inadequate respiratory support from velopharyngeal dysfunction, the clinician may plug the nostrils for one measurement then open them for the other • Prolongation of voiceless continuants may also help discrimination between respiratory and velopharyngeal factors Therapy Techniques continued • • • • • Voice hygiene recommendations Inspiratory Muscle Training Holding breath for a certain time Phonating while pushing/pulling Pitch glides up and down