ISSN 1174-44170 New Zealand Deafness Notification Data January – December 2005 Report prepared by Greville Consulting for National Audiology Centre Auckland District Health Board March 2007 PO Box 26 506, Epsom, Auckland 1344, New Zealand Phone: 0800 87 11 00; +64 27 281 3072; greville@ihug.co.nz ; www.grevilleconsulting.co.nz 2 NZ Deafness Notification Data CONTENTS Summary ................................................................................................................................ 3 Introduction ......................................................................................................................... 4 Notification and Reporting Criteria ........................................................................... 5 Age of identification .......................................................................................................... 7 Degree of Hearing Loss ................................................................................................... 10 Other Disabilities ..............................................................................................................11 Cause of Hearing Loss ...................................................................................................... 12 Confirmation of Hearing loss .......................................................................................... 13 Risk Factors ........................................................................................................................ 16 Ethnicity .............................................................................................................................. 17 Location ............................................................................................................................... 21 Unilateral Hearing Loss .................................................................................................. 26 REFERENCES ......................................................................................................................... 27 March 2007 Greville Consulting 3 NZ Deafness Notification Data Summary This report presents deafness notification data differently from past years. Efforts have been made to remove duplicate entries from the database, and to ensure that numbers quoted refer only to children meeting the notification criteria. The average age of identification of a moderate or greater degree of hearing loss for children notified during 2005 was 33 months – 10 months on average after hearing loss was first suspected. The average age of confirmation is considerably better than in 2004 when it was 45 months. Analysis of the degree of hearing loss showed that the improvement was due to improved identification of children with moderate hearing loss. However, the internationally recommended age of identification of a hearing loss is three months, with intervention commencing by six months (Joint Committee on Infant Hearing, 2000). Only 10% of children with bilateral prelingual hearing loss had hearing loss severe or profound in degree. Most children (82%) had no handicaps apart from hearing loss. 58% of children had no risk factors. However, a family history of hearing loss was present in 32% of notifications. Children with risk factors present were identified earlier on average for children with mild and moderate hearing loss. Parents were most likely to suspect hearing loss (41%) followed by Vision and Hearing Technicians (19%). Maori children continue to be over-represented in the data. They made up 43% of 2005 notifications with Census data (2001) showing this group making up 23% of the population. The proportion of Maori children is highest amongst those with mild hearing loss. Maori children also tended to be identified later than European and Asian children, although Pacific Island children were the last to be identified. The area with the highest prevalence of prelingual hearing loss notifications is Northland, followed by Bay of Plenty and East Coast. These are areas with particularly high proportions of Maori children with prelingual hearing loss. The average age of identification varies widely across regions. March 2007 Greville Consulting 4 NZ Deafness Notification Data Introduction When a child is confirmed with a hearing loss, the person confirming the loss, usually an audiologist, notifies the national deafness database. New Zealand’s national policy is to use the high-risk register for infants born with risk factors for permanent hearing loss. These risk factors are: 1. 2. 3. 4. 5. 6. 7. 8. 9. Family history of hearing loss Jaundice requiring exchange transfusion Craniofacial abnormalities Ototoxic drugs Mechanical ventilation lasting five or more days Low Apgar scores (0 to 4 one minute or 0 to 6 at five minutes) Birth weight less than 1500 grams Bacterial meningitis Infection such as rubella, herpes and toxoplasmosis and those associated with hearing loss In some areas, a tenth factor is also used: 10. Stigmata or other findings associated with a syndrome known to include sensorineural hearing loss (eg Waardenburg, Usher's syndromes, etc.) Hearing loss in infants referred for being high risk is usually confirmed using Auditory Brainstem Response (ABR) audiometry, often in conjunction with Otoacoustic Emissions and/or behavioural assessment. Behavioural techniques are the primary tools for assessing older children. The data presented here are the notification data for the year i.e. those children notified to the database in a calendar year, rather than those who are identified in this year. In the case of hearing loss the incidence of permanent prelingual hearing loss would be the number of children born with hearing loss in any one year. This is difficult to estimate because of delays in identification of hearing loss in many children, particularly those with milder degrees of hearing loss. March 2007 Greville Consulting 5 NZ Deafness Notification Data Notification and Reporting Criteria In the year 2005, 209 children were reported to the Deafness Detection Database. Of the 209 notifications, 135 met the audiometric criteria for inclusion. The notification criteria are: “Children under 18 years with congenital hearing losses or any hearing loss not remediable by medical or surgical means, and who require hearing aids and/or surgical intervention. They must have an average bilateral hearing loss (over four audiometric frequencies 500-4000Hz), greater than 26dBHL in the better ear (Northern and Downs classification 1984).” Those children who were excluded on audiometric criteria were: 23 with slight hearing losses (<26dBHL in the better ear) 51 with unilateral losses In addition, those excluded for non-audiometric reasons were: 19 with acquired hearing losses 24 who were born overseas The total number meeting all criteria and used in the following analysis was therefore 93. There was a slight decrease in the level of notifications in 2005 following higher levels experienced during the years 1998 – 2003 (see Figure 1). Note that these numbers are lower than in previous reports. The database has now been cleansed of duplicate entries, and notifications not within the referral criteria have been excluded. March 2007 Greville Consulting 6 NZ Deafness Notification Data Numbers notified each year 160 140 120 y = 20.9Ln(x) + 55 100 80 60 40 20 0 1983 1984 1985 1986 1987 1988 1989 1990 1991 1992 1993 1994 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 Figure 1: The number of children meeting referral criteria notified to the Deafness Database from 1983 to 2005 March 2007 Greville Consulting 7 NZ Deafness Notification Data Age of identification Figure 2 shows the degree of hearing loss for the 93 children notified in 2005, by birth year. The large numbers of children detected in 1999 corresponds to the years when 5 and 6 year olds were born and reflects the contribution to identification of children with predominantly mild hearing loss of the Vision and Hearing Screening Programme. The trend shown is very similar to that in previous years. Children with a severe or profound hearing loss were born no earlier than 1999. 20 18 16 14 12 Prof Sev Mod Mild 10 8 6 4 2 0 1988 1990 1991 1992 1993 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 Birth year Figure 2: Degree of hearing loss for children notified in 2005 as a function of birth year (n=93). Figure 3 below shows the average age of identification of hearing loss (for children with hearing loss at least moderate in degree) over the last 15 years. This shows an improvement of 12 months to an average age of 33 months for 2005 compared with 2004. Figure 4 details the age of confirmation by degree of hearing loss over the same period. From this graph, it is evident that the improvement in 2005 was due to earlier identification of children with moderate hearing losses, the age of confirmation of children with other categories of hearing loss having remained relatively static. March 2007 Greville Consulting 8 NZ Deafness Notification Data Age confirmed 50 45 40 Age (months) 35 30 25 20 15 10 5 0 1991 1992 1995 1994 1993 1996 1997 1998 1999 2000 2002 2001 2003 2004 2005 Figure 3: Average age of identification for children with hearing loss at least moderate in degree over 15 years Age of confirmation of hearing loss by degree 90 80 70 Age (months) 60 Mild Mod Sev Prof 50 40 30 20 10 0 1991 1992 1993 1994 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 Figure 4: Average age of identification by degree of hearing loss over 15 years March 2007 Greville Consulting 9 NZ Deafness Notification Data Figure 5 shows the cumulative percentage identified by each year of age for the last six years. In this method of presenting the data as well, 2005 emerged as a better year compared with performance in recent years. 100% 90% 80% 70% 60% 2001 2002 2003 2004 2005 50% 40% 30% 20% 10% 0% 0 1 2 3 4 5 >5 Cumulative age at confirmation (years) Figure 5: Cumulative percentage of children with hearing loss at least moderate in the better ear notified from 2001 to 2005 in yearly age groups March 2007 Greville Consulting 10 NZ Deafness Notification Data Degree of Hearing Loss The classification for the degree of hearing loss used in this report is based on the Northern and Downs classification (1984). The degree of hearing loss is based on the better hearing ear, and is an average of the pure-tone thresholds at 500, 1000, 2000 and 4000 Hz. The divisions for the degrees of hearing loss are: Mild 26-40 dB HL Moderate 41-65 dB HL Severe 66-95 dB HL Profound 96+ dB HL Figure 6 shows the distribution of each degree of hearing loss for children notified during 2005, including the degree of hearing loss in the worse ear. Degree of Hearing loss Sev-sev 4% Prof-prof 6% Mod-sev 4% Mild-mild 34% Mod-mod 39% Mild-mod 11% Mild-sev 2% Figure 6: Distribution of degree of hearing loss (better ear - worse ear), n=93 March 2007 Greville Consulting 11 NZ Deafness Notification Data Other Disabilities Most children (82%) had no other disability apart from hearing loss. 5% of children notified had syndromes other than Downs. 4% had intellectual disability (including those with Downs syndrome), and only 1% had multiple disabilities. Other Disabilities 1% 1% 1% 1% 2% 2% 5% 5% None Syndromes Other IHC Downs Syndrome OME Multiple Heart problems Blindness 82% Figure 7: Other disabilities (apart from hearing loss) for the children notified in 2005 (n=93). March 2007 Greville Consulting 12 NZ Deafness Notification Data Cause of Hearing Loss This year the primary cause of prelingual hearing loss continues to be classed as unknown (58%). Cause of Hearing loss 1% 1% 2% 1% 2% 3% Unknown Family history Facial malformation Ototoxic drugs Other 32% 58% Multiple Congenital infection Asphyxia Figure 8: Causes of hearing loss identified for the children with prelingual hearing loss notified during 2005 (n=93). A family history of hearing loss continues to be the strongest predictor of prelingual hearing loss (32%). There appears to be a strong link between causation and ethnicity. Of the 40 Maori children notified with a hearing loss, 17 (or 43%) have a family history of prelingual hearing loss. This is significantly higher than for non-Maori children where for 13 of 52 children (25%) a family history was reported. In addition to the 93 children with prelingual hearing loss, 16 children with acquired hearing loss were notified. Ten of these had the sequelae of OME, two had meningitis, and four had unidentified acquired hearing loss. 6 of these children were born overseas. Of the 16 children born overseas with prelingual hearing loss, ten had no known risk factors, four had a family history, and two had facial malformation. March 2007 Greville Consulting 13 NZ Deafness Notification Data Confirmation of Hearing loss Figure 9 shows the mean ages of suspicion and confirmation of children with at least a moderate hearing loss over the past six years. In 2005 the average age when a hearing loss was first suspected was 23 months, with average confirmation age of 33 months. This shows it takes 10 months on average to confirm a hearing loss. This is shorter than for any year over the last 6 years – the range over this period being from 10 to 15 months. Age suspected and confirmed 50 45 40 Age (months) 35 30 Age suspected Age confirmed 25 20 15 10 5 0 2000 2001 2002 2003 2004 2005 Figure 9: Mean age (months) of suspicion and confirmation of a moderate or greater hearing loss for years 2000-2005. As usual, parents were most likely to suspect a hearing loss in their children (see Figure 10). The second key group of people were Vision Hearing Technicians. March 2007 Greville Consulting 14 NZ Deafness Notification Data Who suspected hearing loss Ear nurse 1% Other family member 2% Teacher ENT PHN 1% 2% 2% Tech 3% Plunket 3% Speech path 1% Unknown 4% Parent 41% GP 4% Aud 4% Other 5% Paed 8% VHT 19% Figure 10: Role of person who suspected hearing loss for children notified in 2005 (n=93). In 96% of cases notified during 2005, an audiologist confirmed the hearing loss. A significant delay between suspecting and confirming a hearing loss is longer than six months. Figure 11 shows that, for the year 2005, 55% had no delay in confirming this loss. In 17% of cases, the reason for any delay was unknown. Parents emerged as the largest identified category with 9%. The presence of a conductive overlay was the next most common reason cited. March 2007 Greville Consulting 15 NZ Deafness Notification Data Cause of delay Untestable Slight HL 1% 1% Referral pathway 2% Child ill 1% ENT 1% Combination 4% Waiting list 4% Conductive overlay 5% Parents 9% None 55% Unknown 17% Figure 11: Reasons for any delay in confirming hearing losses in 2005 (n=93). March 2007 Greville Consulting 16 NZ Deafness Notification Data Risk Factors The average age of identification varies greatly with the degree of hearing loss and this can be seen below in Figure 12 and earlier in Figure 4. Not surprisingly, the less the degree of hearing loss in the better ear, the later the hearing loss tends to be confirmed. Amongst children notified during 2005 the average age for detecting a mild loss was 76 months, moderate 36 months, severe 34 months and profound 13 months. Figure 12 also shows the age of identification related to the presence of risk factors for hearing loss. These risk factors are noted in the introduction (see Page x). For all degrees of hearing loss apart from severe (with only four children represented), there was a slight average advantage for children with risk factors. Those children with mild and moderate hearing losses were identified on average 13 months earlier if they had risk factors present. In children with profound losses there was a risk advantage of 3 months. Risk factors & age of identification 90 80 70 Age (months) 60 50 No risk factors Risk factors 40 30 20 10 0 Mild Mod Sev Prof Figure 12: Age of identification for mild (26-40dBHL), moderate (41-65dBHL), severe (6695dBHL) and profound (>95dBHL) degrees of hearing loss according to risk factors. This year’s report shows, contrary to earlier years, some advantage in the use of the risk register in assisting with the detection of hearing loss in children. March 2007 Greville Consulting 17 NZ Deafness Notification Data Ethnicity Figure 13 shows the ethnicity of the children reported to the database during 2005. This graph shows that Maori children make up 43% of the notifications and European children comprised 48%. The proportion of Pacific Island children notified is lower than usual at 4%, compared to 16% last year. The 2001 Census population statistics for children (aged up to 19 years) showed percentages of European, Maori, Pacific Island and Asian and peoples to be 61%, 23%, 8% and 7% respectively. Maori children continue to be significantly over-represented in the notifications. . Ethnicity (2005 notifications) Pacific Id 4% Asian Other 1% 4% European 48% European Maori Pacific Id Asian Other Maori 43% Figure 13: Ethnic origin of children identified in 2005 with bilateral hearing loss (n=93). The ethnic makeup of the database showing children born since 1990 (when ethnicity data were first collected) is shown in Figure 14. It is clear from this that Maori children are consistently over-represented. March 2007 Greville Consulting 18 NZ Deafness Notification Data Ethnicity by year of birth 160 140 120 100 U/K Other Asian Pacific Id Maori European 80 60 40 20 0 1990 1991 1992 1993 1994 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 Figure 14: Ethnic origin of children born since 1990 with bilateral hearing loss (n=1354). Maori children notified are more likely to have mild hearing losses than any other ethnic grouping. The degree of hearing loss as a function of ethnicity is shown in Figures 15 (2005 notifications) and 16 (data since 1990). Degree of HL & ethnicity 2005 notifications 50 45 40 35 30 Other Asian Pacific Id Maori European 25 20 15 10 5 0 Mild Mod Sev Prof Figure 15: Ethnic origin of children identified in 2005 with bilateral hearing loss of various degrees (n=93). March 2007 Greville Consulting 19 NZ Deafness Notification Data Degree of HL & ethnicity 1990-2005 700 600 500 Other Asian Pacific Id Maori European 400 300 200 100 0 Mild Mod Sev Prof Figure 16: Ethnic origin of children born since 1990 with bilateral hearing loss of various degrees (n=1354) Figure 17 shows the cumulative percentage of children identified in each year of age with hearing loss at least moderate in degree as a function of ethnicity in the year 2005. European children tend to be identified earlier than other ethnic groups – the 50% point for European children is around 18 months, compared with 2 years for Asian children, and just under 4 years for Maori children. There was only one Pacific Island child who was identified late, so the data for this group are distorted. For the database as a whole, the picture is a little different (see Figure 18). Overall Asian children tended to be identified earlier (the 50% point being around 18 months), followed by European (just under 2 years) & other groupings. Maori children came next (3½ years), followed by Pacific Island children of whom only 50% were identified by 5 years of age. March 2007 Greville Consulting 20 NZ Deafness Notification Data 100% 90% 80% 70% 60% European Maori Pacific Id Asian 50% 40% 30% 20% 10% 0% 1 2 3 4 5 >5 Cumulative age at confirmation (years) Figure 17: Cumulative percentage of children identified during 2005 at each age for hearing losses at least moderate in degree, by ethnicity (n=48) 100% 90% 80% 70% 60% European Maori 50% Pacific Id Asian Other 40% 30% 20% 10% 0% 1 2 3 4 5 >5 Cumulative age at confirmation (years) Figure 18: Cumulative percentage of children identified 1990-2005 at each age for hearing losses at least moderate in degree, by ethnicity (n=815) March 2007 Greville Consulting 21 NZ Deafness Notification Data Location Table 1 shows the area of residence for the children notified to the Database in 2005, as well as numbers born in the 15 years prior to the 2001 census. Table 1: Numbers of children with prelingual hearing loss notified during 2005, and from the database as a whole, those born during 1987-2001, compared to population figures (2001 census). Also shown are prevalence estimates of prelingual hearing loss at 2001. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland Notified 2005 16 68 27 2 15 0 5 11 26 3 3 0 28 2 0 2 Born 19872001 144 494 140 41 117 32 48 76 100 110 42 10 149 25 38 45 Population <15 years 35,178 269,607 77,049 24,303 42,678 12,087 24,393 34,836 50,532 91,044 26,460 6,810 86,136 11,106 32,712 22,794 Prevalence/1000 4.09 1.83 1.82 1.69 2.74 2.65 1.97 2.18 1.98 1.21 1.59 1.47 1.73 2.25 1.16 1.97 Areas with prevalence above 2/1000 are displayed in colour in the above table. The area that showed the highest prevalence was Northland. Other areas with rates above 2.5 are Bay of Plenty and East Coast. Numbers notified during 2005 with acquired hearing loss, or born outside New Zealand, or with unilateral hearing losses are shown in Table 2. The interaction of area and ethnicity on the children with prelingual hearing loss born between 1987 and 2001 (where known) is shown in Table 3. Particularly high proportions of Maori children are evident in East Coast (83%), Northland (78%), Bay of Plenty (64%), Hawkes Bay (63%) and Taranaki (61%). March 2007 Greville Consulting 22 NZ Deafness Notification Data Table 2: Numbers of children notified during 2005 not meeting the notification criteria, by geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland Bilateral loss Born overseas Acquired 1 1 10 11 3 2 1 2 Unilateral 6 14 3 1 2 2 1 2 5 10 2 2 10 Table 3: Proportion of children with prelingual hearing loss born during 1987-2001 of different ethnic groupings by geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland European 20% 34% 43% 48% 32% 17% 34% 36% 38% 58% 73% 100% 83% 79% 86% 74% Maori 78% 32% 52% 42% 64% 83% 61% 63% 53% 21% 24% 0% 8% 13% 11% 26% Pacific Id 1% 23% 2% 6% 3% 0% 2% 1% 6% 12% 3% 0% 5% 0% 3% 0% Asian 1% 8% 3% 3% 1% 0% 2% 0% 1% 8% 0% 0% 3% 8% 0% 0% Other 0% 2% 1% 0% 0% 0% 0% 0% 2% 1% 0% 0% 1% 0% 0% 0% There were also geographical differences in degree of hearing loss (see Table 4). Areas with the highest proportions of mild hearing loss were West Coast (70%), Taranaki (63%), Northland and Nelson/Marlborough (57%), Bay of Plenty (56%). March 2007 Greville Consulting 23 NZ Deafness Notification Data Areas with the highest proportions of children with severe or profound hearing loss were Canterbury (26%), East Coast (25%), Otago (24%), Southland (22%) and Lakes (20%). Corresponding numbers of children with each degree of hearing loss are presented in Table 5. Table 4: Proportion of children with prelingual hearing loss born during 1987-2001 with different degrees of hearing loss for each geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland Mild 57% 49% 54% 46% 56% 34% 63% 51% 52% 45% 57% 70% 29% 48% 37% 53% Moderate 31% 34% 31% 34% 37% 41% 23% 36% 33% 38% 33% 20% 46% 36% 39% 24% Severe 10% 12% 13% 12% 3% 16% 10% 12% 8% 14% 5% 0% 17% 8% 21% 13% Profound 2% 5% 2% 7% 3% 9% 4% 1% 7% 3% 5% 10% 8% 8% 3% 9% Table 5: Numbers of children with prelingual hearing loss born during 1987-2001 with different degrees of hearing loss for each geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland March 2007 Mild Moderate 82 244 76 19 66 11 30 39 52 50 24 7 43 12 14 24 44 167 43 14 43 13 11 27 33 42 14 2 68 9 15 11 Severe Profound 15 57 18 5 4 5 5 9 8 15 2 26 2 8 6 3 26 3 3 4 3 2 1 7 3 2 1 12 2 1 4 Greville Consulting 24 NZ Deafness Notification Data The average age of confirmation of hearing loss by area for each degree of hearing loss is presented in Tables 6 (those notified during 2005) and 7 (those notified 1991-2004). Particularly concerning are those with severe or profound hearing loss identified late – amongst those notified in 2005, mean age of confirmation of children with severe hearing losses was particularly poor in Auckland and Waikato. These represented only 3 children, however. Table 6: Mean age (months) of children with different degrees of prelingual hearing loss notified during 2005 for each geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland Mild 61 85 82 76 63 66 88 Mod 65 36 41 71 72 14 51 52 Sev 42 37 Prof 1 37 47 19 18 12 14 22 22 46 Table 7: Mean age (months) of children with different degrees of prelingual hearing loss notified 1991- 2004 for each geographical area. Area Northland Auckland Waikato Lakes Bay of Plenty East Coast Taranaki Hawkes Bay Manawatu Wanganui Wellington Nelson Marlborough West Coast Canterbury South Canterbury Otago Southland March 2007 Mild 58 67 72 61 67 82 71 66 75 64 54 72 54 49 95 70 Mod 53 54 41 46 54 39 27 25 59 49 30 36 42 30 59 46 Sev 25 21 20 24 45 27 12 5 26 18 3 19 15 20 18 Prof 25 18 16 7 21 17 15 3 19 11 18 3 15 34 13 11 Greville Consulting 25 NZ Deafness Notification Data The mean age of confirmation for children with hearing loss at least moderate in degree over the last 15 years is presented in Figure 19. There appears to have been an increase in the age of confirmation, compared with the baseline years of 1991-1995, in many areas of the country – specifically in northern areas (north of Bay of Plenty), in Manawatu to Wellington, and, to a lesser degree, in the four most southern regions. A further deterioration from 1996-2000 to 2001-2005 is evident in a few areas – Lakes, Manawatu/Wanganui & Wellington. An improvement over this period was observed in Northland, East Coast, Nelson/Marlborough, and Otago. Mean age of confirmation by area 60 50 40 1991-1995 1996-2000 2001-2005 30 20 10 th la nd go ta O So u so n el N at u an aw M W el lin gt on M ar lb or ou gh W es tC oa st C an te So rb ur ut y h C an te rb ur y y ga nu i W an s Ba ki ke H aw st oa ra na Ta y Ea st C of Pl en t La ke s Ba y o W ai ka t N or th la n d Au ck la nd 0 Figure 19: Mean age of confirmation (in months) for children with prelingual hearing loss at least moderate in degree by area and for each of the last 5-year periods (n=856). March 2007 Greville Consulting 26 NZ Deafness Notification Data Unilateral Hearing Loss A total of 51 children with unilateral hearing loss were notified during 2005. Of these, 28 had a mild hearing loss in the worse ear, 14 had a moderate unilateral loss, and 9 had severe unilateral hearing loss. Cause of Unilateral Losses 4% 3% 14% 1% 55% 14% Acquired Congenital infection Family history Mumps OME Other Unknown 9% Unilateral loss was more likely to be associated with acquired hearing loss (20% cf 13% for children with bilateral loss). This was also true for the database as a whole (22% cf 11% for the period 1991-2005). March 2007 Greville Consulting 27 NZ Deafness Notification Data REFERENCES Northern J.L. and Downs M.P. (1984) Hearing in Children, Third Edition, Williams and Wilkins, Baltimore Joint Committee on Infant Hearing - Year 2000 Position Statement: Principles and Guidelines for Early Detection and Intervention Programs March 2007 Greville Consulting