Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) and ventricular
tachycardia in patient with concurrent right ventricular clot
Zahra Alizadeh-Sani MD, Anoushiravan Vakili-Zarch MD, Behdad Bahadorian MD, Amir Farjam
Fazelifar MD, Majid Kiavar MD, Fariba Alizadeh-Sani MS and Fahimeh Khozeimeh MS
Rajaei cardiovascular Medical & Research center, Iran University of medical sciences
Introduction
Arrhythmogenic right ventricular dysplasia is a heritable disease characterized by fibrofatty
degeneration of ventricles. Patients present with ventricular arrhythmias or heart failure
symptoms, and sudden cardiac death in some cases. There is little information about the other
complications such as clot formation or left sided valvular involvement; therefore, we present
the case of arrhythmogenic right ventricular dysplasia with concurrent ventricular clot
formation.
Case summary
This is a case of 26 years old female diagnosed with ARVC .The patient has unusual presentation
with ventricular tachycardia and non specific electrocardiogram changes for ARVC such as T
wave inversion in V1- V3.In Trans thoracic echocardiogram right ventricular apical clot was
observed. Interestingly, in CMR there were diffuse changes in right ventricle and ARVC
diagnosed. The origin of tachyarrhythmia considered right outflow tract and treated with
ablation successfully.
Conclusion
Patients with arrhythmogenic right ventricular dysplasia may have other complications other
than arrhythmia as well. Management in these setting should be individualized.