VU University Medical Center 8th Science Exchange Day Friday 7 March 2014 Abstract book Meike de Wit, PhD Photograph: Mark van den Brink Vaste Commissie voor de Wetenschapsbeoefening (VCW) Abstracts VU University Medical Center Science Exchange Day Friday 7 March 2014 9:00 – 15.30 VUmc Amstelzaal, Foyer & Waver Vaste Commissie voor de Wetenschapsbeoefening (VCW) VU University Medical Center Science Exchange Day 2014 3 4 Index Page 6 Preface Page 7 Programme VU University Medical Center Science Exchange Day Page 8 Members of the Vaste Commissie voor de Wetenschapsbeoefening (VCW) Abstracts Page 11 Animal Models Page 24 Biomarkers: Clinical Page 36 Biomarkers: Experimental and Methods Page 52 Biomedical Engineering Page 66 Clinical and Epidemiological Surveys Page 91 Clinical Intervention Page 107 Clinical – Surveys on Volunteers Page 108 Diagnostic Studies – Patients Page 135 Literature Surveys Page 138 Preclinical Disease Models Page 163 Quality of Care – Safety – Auditing Page 172 Grants Desk VU/VU University Medical Center Index Page 173 Presenting author, title of abstract, subjectgroup, research institute VU University Medical Center Science Exchange Day 2014 5 Preface Welcome to the 8th edition of the VU University Medical Center Science Exchange Day. As before, the goal of this day is to stimulate communication between researchers across the borders of departments and the different research institutes. Hopefully this will result in exchange of ideas and new collaborations to further strengthen our research! Each institute has delegated an oral presenter of one of their most exciting recent research achievements. This year, based on evaluation results of previous years, we have included workshops for young researchers in the program, and shortened the plenary presentations. The central highlight of the day remains the poster session, as here the informal contacts between researchers blossom. This year we are proud to have received 161 abstracts showing exciting results from the research performed at CCA, EMGO+, ICaR-VU, MOVE and NCA, as well as our partner VU University institutes AIMMS and Laserlab. The corresponding posters cover a wide range of topics and are on display in the Foyer of VU University Medical Center. They have been ordered by similarity in research approach rather than by disease or discipline, to enable maximal interaction. The categories are: - Animal models - Biomarkers: Clinical - Biomarkers: Experimental and Methods - Biomedical Engineering - Clinical & Epidemiological Surveys - Clinical Intervention - Clinical – surveys on volunteers - Diagnostic Studies – Patients - Literature Surveys - Preclinical Disease Models - Quality of Care – Safety - Auditing The VCW has rated all abstracts based on their scientific quality but also on their appeal to researchers from across the different institutes, as interdisciplinary communication is one of the major goals of this day. The best rated abstract will receive an award, and additional awards will be granted to the best short oral presentation and to the best poster on display. We gratefully acknowledge the Dean for making these awards available. The VU University Medical Center can take great pride in the fact that this year it ranked number 1 in the citation analysis of the Dutch University Medical Centers (CWTS analysis, MNCS-score). This proof of excellence is the result of the combined efforts of the community of researchers within the VUmc. This abstract book, as documentation of the development in the research programmes of the VUmc research institutes remains available on the VCW website. On behalf of all VCW members, Prof. A.J.G. Horrevoets, PhD Chair Vaste Commissie voor de Wetenschapsbeoefening 6 Programme VU University Medical Center Science Exchange Day Friday 7 March 2014; 9.00 – 15.30 Amstel Lecture theatre & Foyer of VU University Medical Center 09.00 – 09.30 Registration 09.30 – 10.00 Introduction session I: 1. Outstanding: Make your grant application stand out! Dr. L. Klomp, Director Grants Desk 2. Shining: Pimp your Curriculum Vitae but don’t overdo! Prof. dr. G.A.M.S. van Dongen, department of Nuclear Medicine & PET Research 3.Swift: Speeding up your publication Prof. dr. P.J.F. Snijders, department of Pathology 4. Compelling: Powering your presentation Prof. dr. M. Boers, department of Epidemiology & Biostatistics 5. Impressive: Grab media attention E. Krab & drs. C. Arps, Communications department 6.Virtuous: Moral excellence in research Prof. dr. J.C.J.M. de Haes, Ombudsman Scientific Integrity Academic Medical Center 10.10 – 10.40 Introduction session II; Similar as session I 10.40 – 11.00 A sweet break with coffee and tea 11.00 – 11.30 Welcome by prof. dr. A.J.G. Horrevoets, chairman VCW & Introduction of the programme Marjolein Glas, MSc. (AIMMS) Sandra Zwijsen, MSc. (EMGO+) Erik Valent, MSc. (IcarVU) 11.30 – 13.30 Poster presentation 12.00 – 13.00 Lunch available (only if registered before 28 February 2014) 13.30 – 14.00 Introduction this part of the programme by prof.dr. A.J.G. Horrevoets Boy Braaf, MSc. (Laserlab) Joost van Kordelaar, MSc. (MOVE) Martijn Steenwijk, MSc. (NCA) Esther Kleibeuker, MSc. (Vumc CCA) 14.05 – 14.35 The evolution of science by prof. dr. J.C. Clevers, President, Royal Netherlands Academy of Arts and Science (KNAW) 14.35 – 14.50 Prize ceremony Best abstract, Best poster, Best presentation 14.50 – 15.00 End of the programme 15.00 – 15.30 Informal reception in the Foyer Members of VCW VUmc: on behalf of: A.J.G. Horrevoets, MD, PhD (chairman) aj.horrevoets@vumc.nl ICaR-VU Molecular Cellbiology and Immunology M. Boers, MSc, MD, PhD m.boers@vumc.nl Epidemiology and Biostatistics W.M. van der Flier, PhD wm.vdflier@vumc.nl NCA Neurology / Epidemiology and Biostatistics J. Harlaar, PhD j.harlaar@vumc.nl MOVE Rehabilitation Medicine R.J.A. van Moorselaar, MD, PhD rja.vanMoorselaar@vumc.nl VUmc CCA Urology P.J.F. Snijders, PhD pjf.snijders@vumc.nl VUmc CCA Pathology F.J. Snoek, MD, PhD fj.snoek@vumc.nl EMGO+ Medical Psychology J. van der Velden, PhD j.vandervelden@vumc.nl ICaR-VU Physiology D.J Veltman, PhD dj.veltman@vumc.nl NCA Psychiatry E. Dijkstra (secretary) e.dijkstra@vumc.nl Strategie, Bestuur & Projecten 8 Abstracts 9 10 Animal models 1. Extracting gene-behavior relations in mice using Markov modeling on longitudinal automated home cage data Emmeke Aarts1, Conor Dolan2, Oliver Stiedl1,3, Bastijn Koopmans4, Maarten, Loos3,4, Grégoire Maroteaux1, August B. Smit3, Matthijs Verhage1,5, Sophie van der Sluis1,5 Department of Functional Genomics, VU University Amsterdam Department of Biological Psychology, VU University Amsterdam 3 Department of Molecular and Cellular Neurobiology, VU University Amsterdam 4 Synaptologics BV 5 Department of Clinical Genetics, VU Medical Center 1 2 Introduction Increasingly, automated home cage systems like the PhenoTyper and DualCage are used in mice to extract gene-behavior relations. The advantage of these instrumental home cages is that the animal is observed in a habituated environ-ment without enhancing unspecific stress levels due to animal handling. Also, the home cage allows for a prolonged period of systematic observation, therefore the development of behavior over time can be studied, with possible application of disease progression over time. These systems provide measurement of behavior over multiple hours, days or even weeks and provide a wealth of information. As yet, this information is often summarized (e.g., frequencies, proportions of durations of one behavioral act). However, the design allows for the study of the temporal patterns of behavior, i.e., the dynamics of behavior, and the role of genes herein. Methods We use continuous time Hidden Markov Modeling (CT-HMM) within a Bayesian framework to analyze spontaneous behavior of young (8-12 weeks) and old (50-60 weeks) C57BL/6J mice. Additionally, to enable statistical comparisons between the two age groups, the CT-HMM is extended to a multigroup model. Results Simulation studies showed that CT-HMM provides reliable and robust parameter recovery. The CT-HMM uncovered interesting behavioral pattern differences in the two age groups. Conclusions The comparison between the two age groups shows that the new information on behavioral phenotypes that is obtained with CT-HMM uncovers behavioral differences that classical behavioral tests, and classical statistical methods, cannot detect. CT-HMM, therefore, addresses an entirely new set of questions about mouse behavior, which makes it possible to shed a new light on the development and prognosis of neural disorders and diseases. VU University Medical Center Science Exchange Day 2013 11 Animal models 2. Closer look at the machinery of cilia: Focusing on the steps of IFT kinesins Şeyda Açar1, Anna Meijering1, Bram Prevo1, Dennis L.H.Kruijssen1, Felix Oswald1, Erwin J. G. Peterman1 1 Physics and Astronomy, Faculty of Sciences, VU University Amsterdam Introduction Ciliopathies, a variety of human diseases related to malfunction or not functioning of cilia focuses attention to cilia. We use Caenorhabditis elegans as our model organism to study the intraflagellar transport (IFT) in sensory cilia. IFT is used to build up and maintain cilia. IFT machinery is composed of microtubules (MTs) on which the transport is achieved by kinesin and dynein motors in a bipolar way. IFT is driven by two different kinesin-2 family motor proteins; heterotrimeric kinesin-II and OSM-3 in the anterograde direction. Our specific question here is “What makes the two kinesin-2 motors different?”. First of all their structure is different in that OSM-3 is a homodimer whereas kinesin-II is a heterodimer, having two different motor domains, KLP-11 and KLP-20. Methods We developed molecular biology tools to be able to make dimers of different motor domains, in that we can make non-native dimers (e.g. one motor Osm-3 and the other KLP-20 domain of kinesin-II), as well as the “native” dimers to study the motility of different dimeric constructs. We use in vitro motility assays in which the motility parameters (velocity and run length) of fluorescently labelled, truncated motors are measured using widefield epi-fluorescence and/or total internal reflection fluorescence (TIRF) microscopy. Results According to our preliminary results OSM-3 is a more processive (takes more number of steps once it is attached to the MTs) motor compared to kinesin-II. Kinesin-II is a slower (0.3µm/sec) whereas; OSM-3 is faster (1µm/sec). Kinesin-II is most probably made less processive by one of its motor domains, KLP-11. KLP-11 homodimers do not take steps; rather go through a cycle of attachment /detachment on the MTs in our motility assays. Conclusions Our current results suggest that using the molecular biology and microscopy tools we developed, we can dissect the processes in the stepping of kinesins towards better understanding of their motility. 12 Animal models 3. AMPK Activation Regulates Microvascular Perfusion and insulin-mediated vasoreactivity through control over endothelin-1 activity Michiel P. de Boer1, Rick I. Meijer1, Erik H. Serné1, Geerten P. van Nieuw Amerongen2, Pieter Sipkema2, Pieter Koolwijk2, Benoit Viollet3, Victor W.M. van Hinsbergh2, Yvo M. Smulders1, Etto C. Eringa2 Department of Internal Medicine, Institute for cardiovascular research, VU University Medical Center, The Netherlands 2 Laboratory for Physiology, Institute for Cardiovascular Research, VU University Medical Center, The Netherlands 3 Institut Cochin, Inserm, U1016, Cnrs, UMR8104, Univ Paris Descartes, Paris, France 1 Introduction Decreased tissue perfusion is an important risk factor for the development of insulin resistance and cardiovascular disease in the obese. Obesity-associated hypoadiponectinemia and subsequent decreased 5’AMP activated kinase (AMPK) activity have been linked to insulin resistance. It is, however, unknown whether and how AMPK controls microvascular perfusion. Our objective was to test whether AMPK, and especially its α2 subunit, controls muscle perfusion and insulin-induced vasodilation and to investigate the mechanisms involved. Methods Effects of AMPK activation on insulin-mediated vasoreactivity were studied ex-vivo, using pressure myography of isolated muscle resistance arteries (RA) of Wistar rats, AMPKα2 KO mice and their WT littermates. In vivo, effects of AMPKα2 on muscle perfusion were studied using contrast enhanced ultrasonography (CEU) during a hyperinsulinemic euglycemic clamp. Results Globular adiponectin (gAdn) and 5-aminoimidazole-4-carboxamide-1-β-d-ribofuranoside (AICAR) increased AMPK activity which inhibited insulin-induced ERK1/2 activity, resulting in vasodilation ex-vivo. In mice, genetic deletion of AMPKα2 abolished the interaction between gAdn and insulin in isolated RAs. In AMPKα2-/- mice but not in AMPKα2+/+ mice, hyperinsulinemia decreased skeletal muscle perfusion. Conclusions AMPKα2 controls muscle perfusion during hyperinsulinemia through inhibition of the ERK1/2 pathway. Our findings provide a novel mechanism linking AMPK to regulation of insulin sensitivity and organ perfusion. VU University Medical Center Science Exchange Day 2014 13 Animal models 4. MAO-A inhibition reduces basal oxygen consumption and restores isoprenaline sensitivity of hypertrophied rat papillary muscle in vitro S.J.P. Bogaards1, F.M. Vaz2, I. Schalij3, D. van Groen1, W.J. van der Laarse1 VU University Medical Center, Institute for Cardiovascular Research, 1Department of Physiology, Department of Pulmonology, Amsterdam 3 Amsterdam Medical Center, University of Amsterdam, Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Amsterdam 1 2 Introduction Mechanical efficiency (work/oxygen consumption) of RV papillary muscle of pulmonary hypertensive rats is reduced. We hypothesize that the efficiency reduction is due to monoamine oxidase A (MAO-A), which oxidizes catecholamines and produces H2O2 on the outer mitochondrial membrane. Methods Thin papillary muscles (volume 0.3-0.6 µl) were isolated from the RV of control and monocrotaline (MCT, 60 mg/kg)-induced pulmonary hypertensive male Wistar rats and mounted in an oxygen chamber equipped with a motor to determine efficiency (work loops at 5 Hz sinusoidal length changes at 37°C). Mitochondrial characteristics were determined by quantitative enzyme histochemistry and cardiolipin and phosphatydylglycerol by HPLC-MS. Results The efficiency reduction (P=0.027) and cardiomyocyte hypertrophy (P=0.001) were confirmed. Isoprenaline (1 µM) doubled power output and isometric tension in control papillary muscles. In MCT muscles oxygen consumption doubled (P=0.004) but power output did not increase. MAO-A inhibition by 2 µM clorgyline reduced basal oxygen consumption only in MCT papillary muscles (by 48 SEM 24 µM/s, P=0.045), and restored the inotropic effect of isoprenaline (P=0.017). In the RV free wall of MCT rats the ratio of maximum mitochondrial complex I/complex II activity (P=0.032) and cardiolipin content (CL72:8; P=0.023) decreased, maximum complex II, IV and V activities were similar to control, and phosphatidylglycerol (PG34:1, P=0.005) and MAO-A activity (P=0.025) were increased. Conclusions Oxidation of catecholamines in hypertrophied cardiomyocytes can prevent positive inotropy and produces a large amount of H2O2. MAO-A contributes to the efficiency reduction of hypertrophied myocardium because it consumes oxygen and because the H2O2 it produces may cause mitochondrial dysfunction. 14 Animal models 5. Improvement of an experimental rat model of rheumatoid arthritis for positron emission tomography D.M.S.H. Chandrupatla1, K. Weijers1, Y.Y. Gent1, I. de Greeuw2, M.Verlaan2, M. Mooijer2, J. van den Hoek2, D. Laan2, M.C.M Al1, A.A. Lammertsma2, C.J. van der Laken1, C.F.M Molthoff2 1 2 Department of Rheumatology and Radiology & Nuclear Medicine, VU University Medical Center, Amsterdam Introduction Activated macrophages (MØ) play a key role in the pathophysiology of rheumatoid arthritis (RA). To this end, animal models of RA may be helpful for innovative disease imaging techniques (e.g. PET) and monitoring of therapeutic interventions. Methods Wister rats were immunized twice with methylated bovine serum albumin (mBSA) in complete Freund’s adjuvant and Bordetella pertussis antigen followed by an intra-articular (i.a) mBSA injection and a variable number of boost injections of mBSA) in the right knee (the control, left knee was injected with saline). Knee sections were verified for arthritis development by specific immunostaining for macrophage involvement in synovial tissue with the macrophage markers ED1 and ED2. Imaging feasibility of the RA rat model was evaluated by [18F]FDG and (R)-[11C]PK11195 PET tracers and ex-vivo tissue biodistribution. Results Synovial inflammation in the right knee was confirmed by infiltration of ED1- and ED2-positive macrophages. Their numbers increased upon repeated i.a. boost injections along with prolonged sustainment of synovial inflammation. The control knee showed marginal macrophage infiltration and no synovial inflammation. Both PET tracers [18F]-FDG and (R)-[11C]-PK11195 demonstrated increased uptake in the arthritic knee compared to the control lateral knee in rats with only a single i.a injection. Lastly, ex-vivo tissue biodistribution 1 h after tracer injection showed 1.2-1.4 fold increased tracer uptake in RA knees compared to the control knees. Conclusions A RA rat model was successfully developed for imaging and monitoring of RA by PET tracers targeting activated MØ. VU University Medical Center Science Exchange Day 2014 15 Animal models 6. Slow BMP-2 release from a fibrin-hyaluronate hydrogel for intervertebral disc regeneration in a large animal model Suzanne E.L. Detiger1, Lindsay S. Karfeld-Sulzer2, Keren M. Kaplan3, Roel J.W. Hoogendoorn1, Barend J. van Royen1, Theo H. Smit1, Avner Yayon3, Franz E. Weber2, Marco N. Helder1 Department of Orthopaedic Surgery, VU University Medical Center and research institute MOVE, Amsterdam, The Netherlands 2 Department of Maxillofacial Surgery, University Hospital Zürich, Switzerland 3 ProCore BioMed Ltd. Ness Ziona, Israel 1 Introduction: Intervertebral disc (IVD) degeneration is an important target for regenerative strategies and starts with proteoglycan depletion from the nucleus pulposus (NP). Cellular proteoglycan production can be increased by several growth factors, including bone morphogenetic protein-2 (BMP-2). As unbound growth factors only exert their effect during short periods in vivo, covalent incorporation of BMP-2 was explored. Our objective was to assess safety and efficacy of covalently conjugated BMP-2 in a fibrin-hyaluronate hydrogel after injection into IVDs. Methods: In seven adult goats, lumbar IVDs were chemically degenerated in three months and subsequently randomised to three intervention groups: hydrogel with 200 ng/ml covalently conjugated BMP-2, hydrogel alone and no intervention (negative control). After 3 months followup, IVDs were analysed by T2-weighted MRI and colorimetric assays for glycosaminoglycan (GAG) and hydroxyproline (Hyp) content. Results: MRI signal intensity was significantly higher in IVDs treated with BMP-2 compared to hydrogel alone (p=0.02; figure 1A) and lower in hydrogel-treated than in control IVDs (p=0.003). GAG content showed the same tendency without statistical significance (figure 1B). Hydroxyproline content remained relatively constant between the groups, representing an unchanged collagen amount in the NP (figure 1C). Conclusions Fibrin-hyaluronate hydrogel with conjugated BMP-2 appeared safe and efficacious after injection into mildly degenerated goat IVDs. Our results suggest a regenerative effect of covalently conjugated BMP-2 compared to hydrogel alone, as substantiated by an increased MRI index, and the trend of increased GAG content in the NP. Possibly, increasing the dose of BMP-2 could enhance this regenerative potential in future experiments. Figure 1: MRI index in % of healthy level (A), GAG (B) and hydroxyproline content (C) in μg / mg dry weight plotted per intervention group (n = 7). Data plotted as mean and SD (*p < 0.05; **p < 0.01). 16 Animal models 7. A post docking role of the Synaptotagmin1-C2B base domain Girish H. Kedar1, Anders. S. Munch2, Jon-Ruben Van Rhijn1, Jan R.T. van Weering1, Jakob Sørensen2, Matthijs Verhage1 Secretory vesicle trafficking group, Dept. Functional Genomics, Centre for Neurogenomics and cognitive research, Neuroscience Campus Amsterdam, VU University Amsterdam and VU Medical Center, Amsterdam, The Netherlands 2 Department of Neuroscience and Pharmacology, Faculty of Health Sciences, University of Copenhagen, 2200 Copenhagen N, Denmark 1 Introduction Synaptotagmin-1 (Syt-1) is the principle Ca2+ sensor for exocytosis in neurons and neuroendocrine cells. Syt-1 is also essential for the initial large dense core vesicle (LDCV) docking process. It binds the t-SNARE protein SNAP25/Syntaxin acceptor complex, thereby establishing docking of the vesicle to the plasma membrane. Additional interactions with lipids may also contribute to this process. However, how Syt-1 regulates LDCV docking is still unresolved. To determine the molecular mechanism of Syt-1 function in docking, we overexpressed the Syt-1 R398,399Q mutant in Syt-1 null mutant chromaffin cells. This mutant interacts with SNARE proteins and lipids but was previously shown to severely reduce exocytosis in neurons probably by affecting membrane association by its base domain. Methods We carried out ultra-structural evaluation using electron microscope and physiological secretion analysis by voltage clamp method Results We show by ultra-structural evaluation that Syt1-KO chromaffin cells infected with the R398,399Q mutant show normal number of docked LDCV. Exocytosis in these cells is not restored, in contrast the sustained release component is further reduced in Syt-KO cells expressing Syt-RQ. Conclusions Hence, the R398,399 region appears to be dispensable for LDCV docking, but is important for secretion since Syt1- R398,399Q mutation severely impaired exocytosis. VU University Medical Center Science Exchange Day 2014 17 Animal models 8. Microvascular flow disturbances in a rat model of cardiopulmonary bypass are not caused by hemodilution Nick J. Koning1,2, Rob F.P. van den Akker1,2, Hans W. Niessen3, Charissa E. van den Brom1,2, Christa Boer2 Department of Anesthesiology, VU University Medical Center Department of Physiology, VU University Medical Center 3 Department of Pathology, VU University Medical Center 1 2 Introduction Although hemodilution is suspected as the main cause of microvascular flow disturbances during cardiopulmonary bypass (CPB), this has never been investigated. We therefore investigated the effects of hemodilution with or without extracorporeal circulation on microvascular perfusion in a rat model for cardiopulmonary bypass. Methods Male Wistar rats were prepared for cremaster muscle intravital microscopy and subjected to hemodilution alone (n=9) or hemodilution with 75 minutes of CPB (n=9). Microcirculatory recordings, made at baseline and five consecutive time points during the experimental protocol, were analyzed for the number of perfused and non-perfused microvessels. Renal leukocyte counts were performed in renal cross-sections. Results Hematocrit levels similarly dropped to 0.24 ± 0.03 and 0.22 ± 0.02 after onset of hemodilution with or without CPB, respectively. Following onset of CPB, the number of perfused vessels dropped by 43% (from 9.4 (8.8-9.8) to 5.0 (3.8-7.0); P=0.008), whereas the initial reduction in perfused capillaries in the hemodilution group was only 8% (from 8.7 (8.5-9.2) to 8.0 (7.2-8.2); P=0.038). The reduced number of perfused vessels persisted after weaning from extracorporeal circulation in the CPB group. An increase in non-perfused microvessels was observed only after initiation of extracorporeal circulation. Renal leukocyte counts were higher following CPB than after hemodilution alone. Conclusions Cardiopulmonary bypass-induced hemodilution is associated with a large reduction in perfused capillaries and augmentation of stagnant microvessels, in contrast to hemodilution alone, which yields only minor microcirculatory disturbances. Moreover, increased renal leukocyte infiltration is observed in the CPB group. 18 Animal models 9. Lipid membranes, oxidative stress and amyloid-beta: Alzheimer’s disease triggering and imaging with multimodal laser-scanning microscopy N.V. Kuzmin1,2, J.C. Baayen2,3, H.D. Mansvelder2, M.L. Groot1,2 Institute for Lasers, Life, and Biophotonics, Amsterdam Neuroscience Campus Amsterdam, Amsterdam 3 VU University Medical Center, Amsterdam 1 2 Introduction Multimodal laser-scanning microscopy (MLSM) using second and third harmonic generation (SHG, THG) combined with two- and three-photon excited fluorescence provides non-invasive, label-free contrast of living brain tissue with sub-cellular resolution, intrinsic depth sectioning, reduced phototoxicity and fast acquisition times. In brain tissues MLSM reveals neurons, lipid myelin sheaths surrounding axons, erythrocytes, polarized microtubule arrays inside axons and dendrites blood vessels etc. We aim to use the MLSM to unveil the sequence of events leading to development of Alzheimer’s disease (AD). Methods MLSM imaging of living brain tissues was performed with a multiple-photon laser-scanning microscope. During real-time imaging we expose live brain cells to oxidants, amyloid-beta oligomers and mitochondrial toxins via local micro-injections. We calibrate the label-free harmonic signals with fluorescent dyes tracking membrane integrity, oxidants and amyloid-beta oligomers. Results We image interactions between live neurons in ex-vivo mouse brain slices and locally applied oxidants, amyloid-beta oligomers, mitochondrial toxins and excitotoxic agents – the key factors in AD onset hypotheses. We show that MLSM is a sensitive indicator of a mouse neuron health – ethanol-induced membrane lipid oxidation and increased permeability along with glutamateinduced cell components damage both result in increase of the THG signal intensity emitted by cell membranes and organelles respectively, accompanied by their morphological degeneration. Conclusions MLSM imaging proves to be a versatile technique both for morphological label-free imaging of mouse and human (healthy and AD) brain tissues brain tissue imaging and for sensitive visualization of dynamic changes in membrane integrity of mouse neurons. Our next step will be to apply MLSM to study the response of living human brain cells to Aβ oligomers and oxidation, study internalization, degradation and Aβ clearance by glial cells, as well as visualize the mode of action of treatment strategies. VU University Medical Center Science Exchange Day 2014 19 Animal models 10. Numbers of intrinsic cardiac adrenergic cells in rat heart: effect of hypertrophy V.W.W. van Eif1, S.J.P. Bogaards1, I. Schalij2, W.J. van der Laarse1 VU University Medical Center, Institute for Cardiovascular Research 1 Department of Physiology, 2 Department of Pulmonology, Amsterdam Introduction The efficiency of hypertrophied myocardium is reduced. Upregulation of oxygen consuming enzymes, like monoamine oxidase A (MAO-A), reduces efficiency and contributes to ROS production. Inhibition of MAO-A in isolated papillary muscle reduced oxygen consumption, suggesting endogenous catecholamine release. We hypothesize that intrinsic cardiac adrenergic (ICA) cells, which predominantly produce noradrenalin, are involved. Methods We counted ICA cells in sections of monocrotaline (MCT, 60mg/kg) administered male Wistar rats by tyrosine hydroxylase immunohistochemistry. Two-way ANOVA and post-hoc tests with Bonferroni correction were performed. Results The number (mean±SEM) of ICA cells in controls (n=3) was 207±29 cells/ml in the right free wall, 264±19 cells/l in the right side of the septum, 162±51 cells/ml in the left side of the septum, and 204±16 cells/ml in the left free wall. ICA cell density in the left and right side of the septum differed (P<0.05). MCT rats developed pulmonary hypertension and right ventricular hypertrophy. The number of ICA cells in these hearts (n=5 to 7) was 130±11 cells/ml in the right free wall, 238±13 cells/ml in the right side of the septum, 209±20 cells/ml in the left side of the septum, and 231±23 cells/ml in the left free wall. ICA cell density in the right free wall was smaller than in other areas of the hearts (P<0.05). The interaction of treatment and location was not significant (P=0.075). The decrease in ICA cell density in the right free wall can be explained by hypertrophy of cardiomyocytes. Conclusions We conclude that ICA cell density is high (about 200000 per rat heart) and that the number of ICA cells does not change in hypertrophied rat myocardium. 20 Animal models 11. 3D imaging of brain tumors Tonny Lagerweij1, Sophie A. Dusoswa1 , Adrian Negrean2 Esther Hendrikx3, Tom Wurdinger1 Department of Neurosurgery, Neuro-oncology Research Group, VU University Medical Center Department of Integrative Neurophysiology, Center for Neurogenomics and Cognitive Research, Neuroscience Campus Amsterdam, VU University 3 Molecular Cell Biology and Immunology, VU University Medical Center 1 2 Introduction Imaging of a brain tumor in its 3D microenvironment will gain insight in structure-to-function relationships and benefit new treatment options for patients with brain tumors. Our aim is to develop techniques to visualize 3-dimensional the brain tumor and its surrounding tissue at single cell resolution. Methods Tumor cells, expressing mCherry, are transplanted in the brain of nude mice. A cranial window covers the tumor to enable in vivo imaging. At different time points, mice are fixed under a 2-photon microscope and 3D stacks are imaged. Ex vivo; brains were perfused with a hydrogel solution and clarified by electrophoresis and index-matching. Tumor vasculature was stained with lectin-DyLight488 and visualized by 2-photon microscopy. Results During a 100 minutes intravital imaging session, we visualized migrating E98FM glioma cells. Furthermore, after carification of mice, we were able to clarify the brains, stain blood vessels and create a 3D reconstructions of the brain vasculature. Conclusions Intracranial injection of E98FM glioma cells results in a diffuse growing, infiltrative tumor. With intravital imaging, it was visualized that some of the E98FM cells. Clarification of brain results in highly transparent tissue in which the blood vessels are easily stained by lectin coupled fluorochromes. Combination of imaging techniques will reveal insight in the migration of brain tumor cells and might bring clues towards new therapies. VU University Medical Center Science Exchange Day 2014 21 Animal models 12. Neuropeptide secretion in the brain: Insights into dynamics of dense-core vesicles Claudia M. Persoon1, Ruud F.G. Toonen1, Matthijs Verhage1 Department of Functional Genomics, Center for Neurogenomics and Cognitive Research (CNCR), VU University/VU University Medical Center 1 Introduction Large dense-core vesicles (DCVs) transport and secrete a diverse range of neuropeptides important for neuronal development, communication and synaptic plasticity in the brain. Disruption of DCV exocytosis has been associated with many disease states ranging from cognitive disorders, stress and addiction problems, obesity to anorexia. In the neuron, DCVs are synthesized and filled with cargo at the Golgi network and actively transported along the cytoskeleton. Upon a calcium trigger, DCVs fuse with the plasma membrane of the soma, neurite or synapse to release their cargo. Although the secretory pathway of synaptic vesicles has been extensively studied in mammalian neurons, little is known about DCV trafficking and fusion mechanisms, dynamics and localization. Methods Hippocampal neurons were derived from mouse brain and cultured on glial islands to study single neurons in vitro. DCVs are visualized by expression of lenti viral particles containing a fusion protein of Neuropeptide Y, which localized to DCVs, and a fluorescent protein. This tool allows us to study transport and secretion of DCVs in living neurons. Results Quantitative analysis of endogenous cargo (ChgB) staining in hippocampal neurons showed a predominant localization of DCVs in axons. Total number of DCVs per neuron was highly variable and correlated with neurite length. Measurements of single release events upon different stimulation protocols showed a releasable pool of approximately 3‐4 % of the total DCV pool size. Conclusions Neuropeptide containing DCVs are mainly transported to axonal regions in hippocampal neurons, indicating a possible preference for presynaptic release of neuropeptides. Only a small part of the DCV pool is released in hippocampal neurons upon stimulation, suggesting the presence of a large reservoir of DCVs available for fast and plastic release. 22 Animal models 13. Deep brain stimulation of the nucleus accumbens core affects heroin seeking and impulsivity in rats Schippers M.C.1 Gaastra M.1, Mesman T.1, Van Mourik Y.1, Schetters D.1, Schoffelmeer A.N.M.1, Pattij T.1, De Vries T.J.1,2 1 2 Department of Anatomy and Neuroscience, VU University Medical Center Department of Molecular and Cellular Neurobiology, VU University Introduction Deep brain stimulation (DBS) is explored as a possible intervention for treatment refractory substance dependent patients. The nucleus accumbens (NA) is involved in reward mechanisms and therefore a promising target for DBS. Additionally, NA modulates impulsive behaviour, a key symptom in drug addiction. We therefore studied the effect of DBS of the NAcore in rat models of heroin seeking and impulsivity. Methods Male Wistar rats were bilaterally implanted with electrodes aimed at the NAcore. DBS was applied during heroin self-administration, progressive ratio of reinforcement schedule, extinction, cueinduced and drug-induced relapse. A separate group of rats was trained and tested with DBS in the five-choice serial reaction time task, to assess effects of DBS on inhibitory response control. Results NAcore DBS specifically reduced motivation for heroin taking and cue-induced relapse to heroin seeking. A negative correlation between baseline impulsive action and change in inhibitory response control as a result of DBS indicated a baseline dependent effect of DBS. Conclusions The present data show a beneficial effect of NAcore DBS on the motivation for heroin consumption and cue-induced relapse to heroin seeking. This confirms that the NAcore is a promising brain target for DBS in the treatment of refractory drug addicts. Additionally, DBS modulated impulsive action in a baseline dependent manner. This observation seems in line with accumulating evidence showing that there are intrinsic neurobiological differences between high and low impulsive animals. Further research should explore the mechanisms by which DBS of the NA is modulating addictive and impulsive behaviour. VU University Medical Center Science Exchange Day 2014 23 Biomarkers: Clinical 14. Atrial fibrillation coincides with increased intravascular depositions of the advanced glycation end-product Nε(carboxymethyl) lysine in the atria of the heart Mark P.V. Begieneman1,2,3, Liza Rijvers1, Bela Kubat2, Walter J. Paulus4, Wim Stooker5, Alexander B.A. Vonk6, Casper G. Schalkwijk7, Bert C. van Rossum8, Hans W.M. Niessen1,3,6, Paul A.J. Krijnen1,3. Pathology, VU University Medical Center Dutch Forensic Institute 3 Institute for cardiovascular research, VU University Medical Center 4 Physiology, VU University Medical Center 5 Onze Lieve Vrouwe Gasthuis 6 Cardiac Surgery, VU University Medical Center 7 Internal Medicine, Maastricht University Medical Center 8 Cardiology, VU University Medical Center 1 2 Introduction In patients with atrium fibrillation (AF), inflammation of the atrium is induced. In the blood of AF patients, increased plasma levels of the advanced glycation end product (AGE) Nε-(carboxymethyl) lysine (CML) have been described. It is known that AGEs induce inflammation in bloodvessels in heart failure. Albeit, the effect of AF on expression level of AGE’s within atrial tissue is unknown. This we have now analysed in atrial tissue in patients with idiopathic AF. Methods 35 patients with idiopathic AF (living patients) and 7 controls (autopsy material) were studied. Tissue slides of the left atria (LA) were stained with antibodies identifying neutrophilic granulocytes, lymphocytes, macrophages, VCAM-1 and CML. Staining was subsequently quantified in the epicardium and myocardium of the atria separately. Results In AF patients, significant increased expression of CML, independent of DM, was found in blood vessels of the LA in patients with AF compared to controls. Furthermore, significantly increased expression of VCAM-1 in blood vessels and a significant increase in the number of neutrophilic granulocytes, lymphocytes and macrophages was found in the LA of AF patients also compared to controls, especially in the epicardium. Finally, CML expression as found in the LA of patients with AF correlated positively with the increased numbers of macrophages. Conclusions Our findings indicate that in idiopathic AF the intramyocardial arteries of the LA have a proinflammatory status coinciding with a local increase in the number of neutrophilic granulocytes, lymphocytes and macrophages. 24 Biomarkers: Clinical 15. Fear conditioning, persistence of disruptive behavior and psychopathic traits: an fMRI study MD Cohn1*, A Popma1*, W van den Brink2, LE Pape1, M Kindt3, L van Domburgh1, TAH Doreleijers1†, and DJ Veltman4† Department of Child and Adolescent Psychiatry, VU University Medical Center Amsterdam Institute for Addiction Research, Academic Medical Center 3 Department of Clinical Psychology, University of Amsterdam 4 Department of Psychiatry, VU University Medical Center 1 2 Introduction Children diagnosed with Disruptive Behavior Disorders (DBD), especially those with psychopathic traits, are at risk of developing persistent and severe antisocial behavior. Deficient fear conditioning may be a key mechanism underlying persistence, and has been associated with altered regional brain function in adult antisocial populations. In this study, we investigated the associations between the neural correlates of fear conditioning, persistence of childhood-onset DBD during adolescence and psychopathic traits. Methods From a cohort of children arrested before the age of 12 years, participants who were diagnosed with Oppositional Defiant Disorder or Conduct Disorder in previous waves (mean age of onset 6.5 years, SD 3.2) were reassessed at mean age 17.6 years (SD 1.4) and categorized as persistent (n=25) or desistent (n=25) DBD. Using the Youth Psychopathic Traits Inventory and functional magnetic resonance imaging during a fear conditioning task, these subgroups were compared with 26 matched healthy controls from the same cohort. Results Both persistent and desistent DBD subgroups were found to show higher activation in fear processing-related brain areas during fear conditioning compared with healthy controls. In addition, regression analyses revealed that impulsive-irresponsible and grandiose-manipulative psychopathic traits were associated with higher activation, whereas callous-unemotional psychopathic traits were related to lower activation in fear-related areas. Finally, the association between neural activation and DBD subgroup membership was mediated by impulsiveirresponsible psychopathic traits. Conclusions These results provide evidence for heterogeneity in the neurobiological mechanisms underlying psychopathic traits and antisocial behaviour and, as such, underscore the need to develop personalized interventions. VU University Medical Center Science Exchange Day 2014 25 Biomarkers: Clinical 16. Elevated inflammatory levels in chronic widespread pain: basal inflammation and innate immune response Ellen Generaal, MSc1; Nicole Vogelzangs, PhD1, Gary J. Macfarlane, MD PhD2, Rinie Geenen, PhD3, Johannes H. Smit, PhD1, Joost Dekker, PhD1,4 , Brenda W.J.H. Penninx, PhD1 Department of Psychiatry and EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam 2 Aberdeen Pain Research Collaboration (Epidemiology Group), University of Aberdeen, Aberdeen, UK 3 Department of Clinical and Health Psychology, Utrecht University, Utrecht 4 Department of Rehabilitation Medicine, VU University Medical Center, Amsterdam 1 Introduction Dysregulation of the immune system may play a role in chronic widespread pain (CWP) although study findings so far are inconsistent. This cross-sectional study examined whether basal inflammatory markers and the innate immune response are associated with the presence and severity of CWP. Methods Data are from the Netherlands Study of Depression and Anxiety including 1632 subjects. The Chronic Pain Grade questionnaire was used to determine the presence and severity of CWP. Subjects were categorized in a CWP group (n=754) and a control group (n=878). Blood levels of the basal inflammatory markers C-reactive protein (CRP), interleukin (IL)-6 and tumor necrosis factor (TNF-) alpha were determined. In addition, 13 inflammatory markers were assessed after lipopolysaccharide (LPS) stimulation in a random subsample (n=707) to obtain a measure of the innate immune response. Results Compared to controls, subjects with CWP showed elevated levels of basal inflammatory markers. However, this association was no longer significant after adjustment for lifestyle and disease factors. For the LPS-stimulated inflammatory markers, we did find elevated levels in CWP subjects both before and after adjustment. Within subjects with CWP, pain intensity and pain disability were not associated with inflammation. Conclusions This study demonstrates elevated basal inflammatory levels and an exaggerated innate immune response in CWP. Since basal inflammatory markers show higher inter-individual variability, we suggest future studies to additionally assess stimulated inflammatory markers. Longitudinal research should investigate whether an exaggerated innate immune response is associated with the onset or perpetuation of CWP. 26 Biomarkers: Clinical 17. Gene-dosage Dependent Overexpression at the 13q Amplicon Identifies DIS3 as Candidate Oncogene in Colorectal Cancer Progression Florence L.M. de Groen, Oscar Krijgsman, Marianne Tijssen, Lianne E.M. Vriend, Bauke Ylstra, Erik Hooijberg, Gerrit A. Meijer, Renske D.M. Steenbergen and Beatriz Carvalho Department of Pathology, VU University Medical Center, Amsterdam Introduction Colorectal cancer (CRC) development is in most cases marked by the accumulation of genomic alterations including gain of the entire q-arm of chromosome 13. This aberration occurs in 40 - 60% of all CRC and is associated with progression from adenoma to carcinoma. To date, little is known about the effect of the 13q amplicon on the expression of the therein located genes and their functional relevance. We therefore aimed to identify candidate genes at the 13q amplicon that contribute to colorectal adenoma to carcinoma progression in a gene dosage-dependent manner. Methods Integrative analysis of whole genome expression and DNA copy number signatures resulted in the identification of 36 genes on 13q of which significant overexpression in carcinomas compared to adenomas was linked to a copy number gain. Five genes showing high levels of overexpression in carcinomas versus adenomas were further tested by qRT-PCR in two independent sample sets of colorectal tumours (n = 40 and n = 47). One candidate gene was functionally analysed by RNAi in CRC cell lines. Results DIS3 and LRCH1 revealed significant overexpression in carcinomas compared to adenomas in a 13q gain dependent manner. Silencing of DIS3 affected important tumorigenic characteristics such as viability, migration and invasion. Conclusions Significant overexpression of DIS3 and LRCH1 associated with adenoma to carcinoma progression is linked to the CRC specific gain of 13q. The functional relevance of this copy number aberration was corroborated for DIS3, thereby identifying this gene as novel candidate oncogene contributing to the 13q-driven adenoma to carcinoma progression. VU University Medical Center Science Exchange Day 2014 27 Biomarkers: Clinical 18. Human papillomavirus in sperm of healthy young men Roosmarijn Luttmer1, Maaike G. Dijkstra1, Divera Pronk1, Katja S. Jordanova2, Danielle A.M. Heideman1, Maaike C. Bleeker1, Hans Berkhof3, Peter G.A. Hompes2, Peter J.F. Snijders1, Chris J.L.M. Meijer1 Department of Pathology, VU University Medical Center, Amsterdam Department of Gynaecology and Obstetrics, VU University Medical Center, Amsterdam 3 Department of Epidemiology and Biostatistics, VU University Medical Center, Amsterdam 1 2 Introduction The human papillomavirus (HPV) is one of the most common sexually transmitted infections worldwide. Persistent infection with high-risk types of the virus (hrHPV) plays a key role in anogenital and oropharyngeal carcinogenesis. In men, penile HPV infections are associated with the presence of flat penile lesions. Recent studies have demonstrated the presence of HPV in sperm. Very few studies have however addressed the question of the source of HPV present in sperm. This study tested whether the detection of HPV in sperm is associated with HPV infections of the penile epithelium and/or the presence of flat penile lesions. Methods A cohort of 213 healthy male students provided 3 sperm samples (with intervals of >1 week) and 1 penile scraping per person. These samples were tested for HPV using the highly sensitive SPF10-PCR-EIA assay and the less sensitive GP5+/6+ PCR-EIA with subsequent genotyping. Combination of both assays enables a semi-quantitative estimation of HPV viral load. Penoscopy was performed to identify flat penile lesions. The concordance of semi-quantitative HPV viral load in sperm and penile scrapings was assessed. Differences in HPV prevalence and viral load in men with and without flat penile lesions were calculated. Results HPV was detected in sperm of 52% and 27% of participants (using SPF10-PCR and GP5+/6+-PCR respectively). The prevalence of HPV infections of penile epithelium was 45% (SPF10-PCR) and 34% (GP5+/6+ PCR). Flat penile lesions were detected in 15% of the population and associated with the presence of hrHPV in penile scrapes and sperm. Substantial to good concordances were detected between HPV detection in penile scrapings and in sperm (kappa 0,83; 0,77; 0,62 for >1, >2 and>3 semen samples HPV positive respectively). On a genotype-specific level, concordances between penile scrape and semen were moderate to substantial (HPV16: kappa 0.68; HPV51: 0,40; HPV42: 0.63; HPV variant jc9710: 0.59). Men with a high semi-quantitative viral HPV load in penile epithelium were more likely to have HPV positive sperm than men with a low viral load and with HPV negative penile scrapings (Fisher’s exact test p<0.001). Conclusion The presence of HPV in the sperm of healthy young men is a very common phenomenon and associated with a high HPV viral load of the infected penile epithelium and with the presence of flat penile lesions. These data indicate that HPV positivity in sperm might result from shedding of HPV particles and exfoliated HPV-infected cells from penile epithelium. Further research should clarify whether HPV positivity of sperm affects male fertility and clinical reproductive outcomes. This could warrant routine HPV screening of sperm samples used in programs of assisted reproduction, especially intracytoplasmatic sperm injection (ICSI). 28 Biomarkers: Clinical 19. Basal nuclei are more severely atrophic in behavioral variant Frontotemporal Dementia compared to Alzheimer’s Disease Christiane Möller MSc1*, Nikki Dieleman, MSc5, Wiesje M van der Flier, PhD1,2, Adriaan Versteeg3, Yolande Pijnenburg, MD PhD1, Philip Scheltens, MD PhD1, Frederik Barkhof, MD PhD3, Hugo Vrenken, PhD3,4 Alzheimer center & Department of Neurology, VU University Medical Center Department of Epidemiology & Biostatistics, VU University Medical Center 3 Department of Radiology & Nuclear Medicine, VU University Medical Center 4 Department of Physics & Medical Technology, VU University Medical Center 5 Department of Radiology, University Medical Center Utrecht 1 2 Introduction Patterns of cortical atrophy in Alzheimer’s disease (AD) and behavioral variant frontotemporal dementia (bvFTD) are often overlapping. The involvement of fronto-striatal circuits in bvFTD suggests that the basal nuclei may add in the diagnosis of these patients Therefore the aim of this study was to investigate whether volumes of the basal nuclei differ between bvFTD and AD. Methods We included 24 patients with probable bvFTD (63years±8, 41.7% females, MMSE 24±4.5), and matched them based on age, gender and educational level at a ratio of 1:3 to 72 probable AD patients (63years±8.2, 41.7% females, MMSE 21±4.9) and 72 patients with subjective memory complaints who served as controls (63years ±8.1, 41.7% females, MMSE 28±2.2). Participants were scanned at 3T MRI. From 3D T1-weighted fast spoiled gradient echo sequence, FIRST software estimated volumes of hippocampus, amygdala, thalamus, caudate nucleus, putamen, globus pallidus, and nucleus accumbens. MANOVA was used to compare volumes of all structures between groups. Results Volumes of hippocampus and amygdala only discriminated dementia from controls. Volumes of thalamus and putamen did not differ between groups. Post hoc comparisons revealed that bvFTD had more severe atrophy than AD in caudate nucleus, globus pallidus and nucleus accumbens. Conclusions Whereas hippocampus and amygdala only discriminated between controls and dementia, caudate nucleus, globus pallidus and nucleus accumbens were more severly affected in bvFTD than in AD and controls. These volume differences between bvFTD and AD provides evidence for the idea that volumes of basal nuclei could facilitate the discrimination between AD and bvFTD. VU University Medical Center Science Exchange Day 2014 29 Biomarkers: Clinical 20. Altered β-Adrenergic Receptor Signaling Contributes to the Development of Right Ventricular Diastolic Dysfunction in Pulmonary Arterial Hypertension Silvia Rain, MD1,2, Denielli da Silva Goncalves Bos, MSc1, M. Louis Handoko, MD PhD2,3, Nico Westerhof, PhD1,2, Ger Stienen, PhD2, Coen Ottenheijm, PhD2, Max Goebel2, Peter Dorfmüller, MD PhD5,6, Christophe Guignabert, PhD5,6, Marc Humbert, MD PhD5,6,7,8, Harm-Jan Bogaard, MD PhD1, Cris dos Remedios, DSc PhD9, Chandra Saripalli, MSc10, Carlos G. Hidalgo, PhD10, Henk L. Granzier, PhD10, Anton Vonk-Noordegraaf, MD PhD1, Jolanda van der Velden, PhD2,11*, Frances S. de Man, PhD1,2* Both authors contributed equally. Departments of 1 Pulmonology, 2 Physiology, 3 Cardiology and 4 Physics and Astronomy, VU University Medical Center/Institute for Cardiovascular Research, Amsterdam, The Netherlands 5 Université Paris-Sud, Faculté de Médecine, Le Kremlin-Bicêtre, France 6 Inserm U999, LabEx LERMIT 7 Service d’Anatomie Pathologique, Centre Chirurgical Marie Lannelongue, Le Plessis Robinson, France Assistance Publique-Hôspitaux de Paris, Service de Pneumologie, Département Hôspital Universitaire, Thorax innovation, (DHU-TORINO), Hôpital Bicêtre, France 9 Muscle Research Unit, Discipline of Anatomy & Histology, Bosch Institute, The University of Sydney, Sydney, Australia 10 Sarver Molecular Cardiovascular Research Program, Department of Physiology, University of Arizona, Tucson, USA 11 CIN – The Netherlands Heart Institute 8 Introduction: Patients with pulmonary arterial hypertension (PAH) develop right ventricular (RV) failure with impaired diastolic function. β-Adrenergic receptor (β-AR) density is decreased in the right RV myocardium of PAH patients. Inadequate downstream β-AR signaling may alter protein kinase A (PKA) phosphorylation and therefore change the function of important proteins regulating cardiomyocyte diastolic function. Methods: RV heart-lung transplantation tissue from PAH patients and non-failing donors was used. Titin, the major determinant of cardiomyocyte stiffness is regulated by PKA phosphorylation. Western blot (WB) analysis determined titin N2B serine 469 (PKA site) phosphorylation level. Functional assessments were performed to quantify the effect of PKA treatment on RV cardiomyocyte stiffness. Troponin I (cTnI) regulates cardiomyocyte Ca2+-sensitivity upon PKA-dependent serine 22/23 phosphorylation. WB analysis determined the level of cTnI serine 22/23 phosphorylation. Ca2+-handling proteins ensure rapid diastolic Ca2+-clearance. SERCA2a expression, total phospholamban (PLN) and PLN phosphorylation at serine 16 (PKA site) were determined by WB analysis. Results: Cardiomyocyte stiffness – titin serine 469 was significantly lower phosphorylated (p<0.0001). PKA incubation strongly decreased cardiomyocyte stiffness (Pinteraction<0.0001). Myofilament Ca2+-sensitivity – PKA mediated cTnI phosphorylation (serine 22/23) was reduced in PAH compared to donors ( p=0.0004). Cardiomyocyte Ca2+-clearance – SERCA2a expression and PLN serine 16 phosphorylation were reduced in PAH patients. Conclusions: Decreased PKA-dependent phosphorylation of titin, cTnI and PLN contribute to the development of RV cardiomyocyte diastolic dysfunction in PAH patients. Impaired β-AR signaling pathway may represent the determining mechanism involved in RV cardiomyocyte diastolic dysfunction in PAH patients. 30 Biomarkers: Clinical 21. Triage of high-risk HPV-positive women by combined cytology and methylation marker analysis: complementary clinical performance L.M.A. De Strooper1, A.T. Hesselink1, J.Berkhof 2, C.J.L.M. Meijer1, P.J.F. Snijders1, R.D.M. Steenbergen1, D.A.M. Heideman1 1 2 Department of pathology, VU University Medical Center Department of epidemiology and biostatistics, VU University Medical Center Introduction Testing for high-risk human papillomavirus (hrHPV) DNA will replace cytology as the primary cervical screening method due to its higher sensitivity for cervical pre-cancer (i.e., cervical intraepithelial neoplasia grade 2-3, CIN2-3) and cancer. The main drawback of hrHPV screening, however, is a 4-6% lower specificity for (pre-)cancer than cytology. To compensate for this limitation, triage of hrHPV-positive women has been proposed to keep the proportion of women referred for colposcopy and/or treatment within acceptable limits. Currently, cytology is the preferred triage tool, yet requires repeat cytology to reach a good sensitivity. DNA methylation analysis of promoter regions of CADM1 and MAL genes is a good, alternative triage assay1. Here, we evaluated the value of triage of hrHPV-positive women at baseline by combined analysis of cytology and the methylation marker panel CADM1/MAL. Methods A cohort of 250 consecutive hrHPV-positive cervical scrapes from women participating in populationbased screening (29-61 years) was evaluated for cytology and CADM1/MAL methylation. Clinical endpoints were CIN3 or worse (CIN3+) and CIN2 or worse (CIN2+). Results At a defined methylation marker threshold, combined baseline triage reached a sensitivity for CIN3+ of 86.8% at 64.8% specificity, and for CIN2+ of 84.5% at 69.9% specificity. The odds ratio for CIN3+ and CIN2+ of combined triage were 12.1 (95%CI:4.6-32.5) and 12.6 (95%CI:2.8-27.6) respectively, versus that of cytology alone (7.1 (95%CI:3.3-15.0), and 9.6 (95%CI:4.9-18.8), respectively), and methylation analysis alone (6.7 (95%CI:3.1-14.3) and 5.9 (95%CI:3.1-11.3)), respectively. Conclusions This study provides a promising baseline triage strategy for hrHPV-positive women in cervical cancer screening. 1 Hesslink et al. CCR 2011 VU University Medical Center Science Exchange Day 2014 31 Biomarkers: Clinical 22. Triaging borderline/mild dyskaryotic Pap cytology with p16/Ki-67 dual-stained cytology testing: cross-sectional and longitudinal outcome study Uijterwaal MH1, Witte B.I.1, Van Kemenade F.J.2, Rijkaart D.1, Ridder R.3, Berkhof J.4, Balfoort-Van der Meij A.5, Bleeker M.C.G.1, Snijders P.J.F1, Meijer C.J.L.M.1 Department of pathology, VU University Medical Center Department of pathology, Erasmus University Medical Center 3 Ventana Medical Systems, Inc. 4 Department of epidemiology and biostatistics, VU University Medical Center 5 Saltro Diagnostic Centre 1 2 Introduction Women with borderline/mildly dyskaryotic cytology smears (BMD) are currently followed-up with repeat-testing at 6 and 18 months. Objective To analyze the cross-sectional and longitudinal performance of p16/Ki-67dual-stainedcytology for detection of cervical intraepithelial neoplasia (CIN) grade 3 or worse (CIN3+) and CIN2+in women with BMD and to compare the results with baseline human papillomavirus (HPV) testing. Methods Conventional Pap cytology specimens of 256 women with BMD were dual-stained for p16/Ki-67 retrospectively and compared to baseline HPV results and long-term follow-up results. Results p16/Ki-67 dual-stained cytology showed a sensitivity of 100.0%, a specificity of 64.4% and a negative predictive value (NPV) of 100.0% for CIN3+. HPV testing demonstrated similar sensitivity (96.3%), and NPV (99.1%), but a significantly lower specificity (57.6%; p=0.024) for CIN3+. Sensitivity, specificity and NPV for CIN2+ of dual-stained cytology were 89.7%, 73.1%, and 95.1%, respectively, similar compared to HPV testing. Dual-stained cytology showed a significant lower referral rate than HPV testing (43.6% versus 49.1%; p=0.043). During long-term follow-up, no CIN3+ lesions developed in HPV positive, dual-stain negative women. Conclusions Comparable sensitivity and NPV of dual-stained-cytology for CIN3+, combined with a significantly higher specificity, makes p16/Ki-67 dual-stained cytology a viable alternative to HPV testing for triaging BMD. 32 Biomarkers: Clinical 23. Brain-derived neurotrophic factor and regional brain volume Laura S. van Velzen1, MSc, Lianne Schmaal1, PhD, Dick J. Veltman2, PhD, Brenda W. Penninx1, PhD 1 Department of Psychiatry and EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam, 2 Department of Psychiatry, VU University Medical Center, Amsterdam Introduction Brain-derived neurotrophic factor (BDNF) is a protein that is involved in neuronal survival and plasticity. Studies have examined a relationship between BDNF levels and hippocampal volume in region-of-interest analyses, due to involvement of BDNF in neurogenesis. BDNF also protects against neurodegeneration and this effect may not be limited to the hippocampus. We will use a whole-brain approach to examine the relationship between BDNF and regional brain volume in healthy subjects and patients with major depressive disorder. Methods Data was collected in the Netherlands Study of Depression and Anxiety (NESDA). Patients with a current MDD diagnosis or a current diagnosis of MDD and comorbid anxiety disorder (n = 155) and healthy subjects (n = 65) were included. Levels of BDNF were determined from blood samples and T1 magnetic resonance images were acquired using a 3T scanner. As BDNF levels did not differ between patients and controls, we combined these groups. We performed voxel based morphometry (VBM) regression analyses to examine the association between grey matter volume and BDNF values across all subjects. Age, gender, education level and scansite were included as covariates. Results We observed a positive relationship between BDNF levels and volume of the right inferior frontal gyrus, uncus, left thalamus, bilateral precuneus and cerebellum. A negative relationship was seen between BDNF levels and volume of the left precuneus (p = .001, uncorrected). Conclusions We suggest that BDNF protects against neurodegeneration in several cortical and subcortical areas and that the effect of BDNF is not limited to the hippocampus. VU University Medical Center Science Exchange Day 2014 33 Biomarkers: Clinical 24. Genome-wide DNA methylation profiling reveals novel biomarkers for early detection of cervical cancer Wina Verlaat1, Peter J.F. Snijders1, Chris J.L.M. Meijer1, Wim Van Criekinge2, Renske D.M .Steenbergen1 Department of Pathology, VU University Medical Center, Amsterdam Department of Mathematical Modelling, Statistics and Bioinformatics, Faculty of Bioscience Engineering, Ghent University, Ghent, Belgium 1 2 Introduction Cervical cancer is caused by a human papillomavirus (HPV) infection, but only a minority of HPVinfected women will develop cancer. Hence, with the introduction of primary HPV testing in cervical screening in The Netherlands in 2016, there is an urgent need for molecular markers enabling risk stratification of hrHPV-positive women. Markers based on DNA methylation of tumour suppressor genes are most promising. In this study we set out to define novel candidate methylation markers by genome-wide DNA methylation profiling. Methods Genome-wide DNA methylation profiles were determined by Methyl Binding Domain (MBD) based DNA enrichment followed by next generation sequencing analysis of 24 HPV-transformed cell lines and cervical tissue specimens. The most differentially methylated gene candidates were subsequently subjected to verification analysis on the same samples by a different method (i.e. multiplex targeted bisulfite next generation sequencing). Ultimately, methylation of verified candidates was assessed in an independent set of cervical tissue specimens (n=73) by methylationspecific PCRs (MSP). Results Of the most differentially methylated gene candidates scored by the MBD screen, hypermethylation of 7 genes in HPV-transformed cell lines and high grade lesions was confirmed by targeted sequence analysis. Of these 7 candidates 5 genes also revealed hypermethylation by MSP analysis in the independent series of precancerous lesions and cervical squamous cell carcinomas compared to normal tissue. Conclusions By genome-wide methylation profiling we identified 5 novel candidate methylation markers for cervical cancer and its precursor lesions. Further validation studies on cervical scrapes will reveal their value in HPV-based cervical screening programs. 34 Biomarkers: Clinical 25. Diagnostic Value of Amyloid Imaging in Early Onset Dementia Marissa D. Zwan1,2, Femke H. Bouwman1, Wiesje M. van der Flier1,3, Adriaan A. Lammertsma2, Bart N.M. van Berckel2, Philip Scheltens1. Alzheimer Center & Department of Neurology Department of Radiology & Nuclear Medicine 3 Department of Epidemiology & Biostatistics, Neuroscience Campus Amsterdam, VU University Medical Center, Amsterdam 1 2 Introduction In early onset dementia approximately one out of three patients has an atypical clinical presentation, which substantially complicates correct etiological diagnosis. [18F]Flutemetamol PET, an investigational imaging agent, is being studied for detection of amyloid deposition, a pathological hallmark of Alzheimer’s Disease (AD). Methods We included 80 patients with early onset dementia and physician diagnostic confidence <90% after a full routine diagnostic work-up for dementia. All patients underwent a [18F]Flutemetamol PET scan which were visually assessed as amyloid positive or negative. Before and after disclosing PET results, confidence in clinical diagnosis was determined. Also, impact on patient healthcare management was assessed after disclosing PET results. Results [18F]Flutemetamol PET scans were positive in 48 out of 63 (76%) patients diagnosed (pre-PET imaging) with AD and 4 out of 17 (24%) patients diagnosed with other dementias. Overall, after disclosing PET results confidence in etiological diagnosis increased from 76±12% to 90±16% (p<0.001). PET results led to a change in diagnosis in 16 (20%) patients; predominantly a negative PET result caused a change of the initial AD diagnosis to another dementia. In 27 (34%) patients, PET results led to a change in healthcare management. For 13 patients additional ancillary investigations were planned after access to the PET results. Conclusions [18F]Flutemetamol PET resulted in changes in the diagnostic process work-up of early onset dementia patients and the diagnostic confidence of the managing physicians. Especially in patients diagnosed with AD pre-PET imaging, a negative PET scan resulted in more changes in clinical diagnosis and patient management. VU University Medical Center Science Exchange Day 2014 35 Biomarkers: Experimental and Methods 26. Structural variant breakpoint detection in advanced colorectal cancer E van den Broek1, O. Krijgsman1, D. Sie1, J.C. Haan1, M. Komor1, J. Traets1, D.A.M.Heideman1, M.A. van de Wiel2, B. Carvalho1, I.D. Nagtegaal3, C.J.A. Punt4, B. Ylstra1, G.A. Meijer1, R.J.A. Fijneman1 Department of Pathology, VU University Medical Center, Amsterdam Department of Epidemiology & Biostatistics, VU University Medical Center, Amsterdam 3 Department of Pathology, Radboud University Nijmegen Medical Center, Nijmegen 4 Department of Medical Oncology, Academic Medical Center, Amsterdam 1 2 Introduction Colorectal cancer (CRC) development is accompanied by genomic alterations driving tumor initiation and progression. DNA copy number alterations could affect mRNA and subsequently protein expression levels. Interestingly, accompanying chromosome breakpoints represent structural variants (SV) that may affect gene architecture and thereby gene function. The aim of this study was to identify recurrent SV breakpoints in advanced CRC. Methods Tumor versus normal DNA from 352 advanced CRC samples from CAIRO and CAIRO2 clinical studies [Koopman et al. Lancet 2007; Tol et al. N Engl J Med 2009] were subjected to arrayComparative Genomic Hybridization (Agilent 180K arrays) to detect copy number alterations. Using these data, we determined the prevalence of recurrent breakpoints in genes. In addition, multiplexed amplicon analysis involving 48 cancer-related genes (Illumina TruSeq Amplicon Cancer Panel) was applied. Multi-Dendrix was used to identify modules of cancer driver genes. Results We identified 748 recurrent breakpoints in genes (FDR<0.1), occurring in less than 5% up to 40% (MACROD2) of all tumors. Mutation frequencies in APC, TP53 and KRAS were conform expectations. Multi-Dendrix analysis revealed modules of cancer driver genes that included commonly mutated CRC cancer genes as well as genes with recurrent breakpoints. Conclusions We were able to pinpoint the prevalence of 748 recurrent SV breakpoint genes using array-CGH from 352 CRC samples. Moreover, our studies revealed several breakpoints in genes that are mutually exclusive with the commonly mutated genes, and therefore represent novel candidate cancer driver genes. Further studies are required to investigate their functional and clinical relevance. 36 Biomarkers: Experimental and Methods 27. Measurement of serum testosterone, androstenedione and dehydroepiandrosterone (DHEA) levels using Isotope-Dilution Liquid-Chromatography Tandem Mass Spectrometry (ID-LC-MS/MS) Rahel M. Büttler1, Frans Martens1, Mariette T. Ackermans2, Marinus A. Blankenstein1, Annemieke C. Heijboer1. Department of Clinical Chemistry, Endocrine laboratory, VU University Medical Center, Amsterdam, the Netherlands. 2Department of Clinical Chemistry, Laboratory of Endocrinology, Academic Medical Center, Amsterdam, the Netherlands. 1 Introduction The adrenal and gonadal androgens testosterone, androstenedione and dehydroepiandro-sterone (DHEA) play an important role in sexual development and fertility as well as in several other processes. We developed a method to assess serum testosterone, androstenedione and DHEA levels in one run using Isotope-Dilution Liquid-Chromatography Tandem Mass Spectrometry (ID-LC-MS/MS). Methods Sample preparation consisted of addition of internal standards (13C3-testosterone, 13C3-androstenedione and 2H6-DHEA) and a liquid-liquid extraction using hexane-ether. The samples were analyzed on an Acquity 2D UPLC system (Waters), equipped with a C4-column (Waters) and a Kinetex Fluorophenyl column (Phenomenex), and a Xevo TQ-S tandem mass spectrometer (Waters). Results The intra-assay CVs were <4%, <4.6% and <6.2% for testosterone, androstenedione and DHEA, respectively. The inter-assay CVs were <7% for testosterone and androstenedione and <9.3% for DHEA. At the lower concentrations inter-assay CVs were 9%, 7% and 9.3%, for testosterone (0.08 nM), androstenedione (0.48 nM) and DHEA (1.18 nM), respectively. Recoveries of spiked analytes were 101-107% and 97-106% for testosterone and androstenedione, respectively. Linearity was shown in dilution series. This method tested negative for interference from several steroid hormones. The method is suitable for EDTA and heparin plasma as well. The present testosterone method compared well (y = 1.000 x + 0.035 nmol/L; r = 0,9982) to another ID-LC-MS/MS method for testosterone in our lab. The latter method being concordant with a published reference method (Bui et al. 2013). Conclusion In conclusion, we developed a sensitive and accurate method to measure serum testosterone, androstenedione and DHEA serum levels in one run. VU University Medical Center Science Exchange Day 2014 37 Biomarkers: Experimental and Methods 28. A standard benchmark for assessing the reproducibility of brain atrophy measures in Alzheimer’s using the ADNI1 data set Cover KS1, van Schijndel R.A.2, Versteeg A.2, Vrenken H.1,2, van Dijk B.W.1, Barkhof F.1 1 2 Physics and Medical Technology, VU University Medical Center Radiology and Nuclear Medicine, VU University Medical Center Introduction To propose a standard benchmark for assessing the reproducibility of atrophy measures in Alzheimer’s disease and to demonstrate its use with hippocampal volume measurements. While many publications have compared the performance of algorithms for measuring brain atrophy in Alzheimer’s disease (AD), few have assessed their reproducibility, because of the additional burden of repeating a MRI acquistion at each patient’s visit. Although rarely mentioned in the literature, the widely available ADNI1 data set had two identical MRI image volumes acquired at each patient visit, making it an excellent and very large data set for reproducibility studies (Cover et al. 2011 Psychiatry Research: Neuroimaging 2011;193:182). Methods A total of 562 subjects in the ADNI1 study were found to have back-to-back (BTB) MRI acquisitions at both baseline and 12 month visits. Both FreeSurfer 5.3.0 and FSL/First 5.0.4 were run on all 4 MRI image volumes for each subject to calculate the percentage hippocampal volume change (PHVC) over the 12 month interval for both of the BTB acquisitions for the left hippocampus. Then the difference of the two PHVC for each subject was calculated yielding a BTB difference. The reproducibility of each algorithm was calculated from its BTB differences as the 50 percentile of the absolute value of the BTB differences. Results The list of ADNI1 MRI included in the benchmark and the computation resources used were provided by the neuGRID Consortium (www.neugrid4you.eu). For FSL/First (N=557), which only has cross-sectional mode, the reproducibility was 2.5% (2.3%-2.8% [95% confidence interval]). For FreeSurfer (N=75) in cross-sectional and longitudinal modes the reproducibilites were 3.3% (2.5%-3.7%) and 2.4% (1.5%-2.9%). Conclusions The three reproducibilities were similar, especially when considering the confidence intervals, but FreeSurfer was slightly smaller. To use the proposed standard benchmark, a researcher need only calculate the BTB reproducibility for new algorithms using the specified MRIs from ADNI1 and compare the reproducibilities to those presented here. Thus the proposed standard benchmark should be a valuable gauge by which to assess and compare the performance of brain atrophy algorithms. 38 Biomarkers: Experimental and Methods 29. Preclinical evaluation of [11C]JNJ7777120 as a PET tracer of histamine H4 receptors in the brain Funke U1,2, Smits R.A.3, Schuit R.C.1, Metaxas A.1, Vugts D.J.1, Janssen B.1, Spaans A.1,2, Kruijer P.S.2, Lammertsma A.A.1, Windhorst, A.D.1 Department of Radiology & Nuclear Medicine, VU University Medical Center BV Cyclotron VU 3 Griffin Discoveries BV 1 2 Introduction Neuroinflammatory factors can induce microglia motility via H4R activation. Further, H4R are functionally expressed on neuronal cells. The purpose of this study was to evaluate whether 11 C-labelled JNJ7777120, a highly potent and selective H4R antagonist, could serve as a potential PET tracer to image H4R in vivo. Methods Whole body PET images of male Wistar rats (~450 g, n=4) where acquired for 60 min following intravenous injection of 11 MBq [11C]JNJ7777120. Displacement studies were performed by administering 35 mg/kg thioperamide s.c., 15 min after [11C]JNJ7777120 injection. Results [11C]JNJ7777120 entered the brain rapidly with a maximal uptake of 0.6 %ID/mL at 3 min. At 25 min, uptake reached a SUV of 1.1, which was not displaced by thioperamide, but rather elevated to a SUV of 1.4. Conclusions Brain uptake of [11C]JNJ7777120 could not be displaced by another H4R targeting substance. Further studies are needed to investigate the reasons for this lack of displacement. These will include metabolic studies, the use of other H4R inhibitors, and in vitro studies to determine expression levels of H4R in healthy rat brains and such possessing neuroinflammatory foci. Research support: FP7/2007-2013, HEALTH-F2-2011-278850 (INMiND) VU University Medical Center Science Exchange Day 2014 39 Biomarkers: Experimental and Methods 30. The blood-derived transglutaminase Factor XIII colocalises with Aβ deposition in cerebral amyloid angiopathy and forms complexes with Aβ in vitro Mieke A.M. de Jager, Max V. Boot, John G.J.M. Bol, John J. Brevé, Benjamin Drukarch, Micha M.M. Wilhelmus Department of Anatomy and Neurosciences, Cellular Neuropharmacology section, Neuroscience Campus Amsterdam, VU University Medical Center 1 Introduction Cerebral amyloid angiopathy (CAA) is an important hallmark of Alzheimer’s disease and characterized by the formation of aggregated amyloid-β peptide (Aβ) deposits in brain vessel walls. CAA is associated with blood brain barrier leakage. Unfortunately, the mechanisms underlying the Ab deposition in CAA remain largely unclear. The transglutaminase enzyme Factor XIIIa (FXIIIa) is present in the blood and is important in the coagulation cascade by inducing fibrin clots via its crosslinking activity. Fibrin is associated with deposited Aβ in CAA, and Ab is a wellknown substrate for transglutaminase crosslinking by other transglutaminases. The aim of this study is to investigate whether blood-derived Factor XIIIa is present and active in CAA and might be involved in Aβ aggregation and deposition in the vessel wall. Methods We studied the distribution of FXIIIa, its in situ activity, and its activator thrombin in human post mortem brain sections of both AD and control cases using immunohistochemistry. Furthermore, we analysed the binding of FXIIIa to Aβ with surface plasmon resonance (SPR) and we tested the ability of FXIIIa to induce the aggregation and cross-linking of Aβ using Western blot analysis. Results We showed that the enzyme FXIII, its in situ activity and FXIII’s activator thrombin colocalise with the Aβ deposition in CAA. Furthermore, we showed that active FXIII (FXIIIa) has a higher binding affinity for Aβ1-42 compared to Aβ1-40. Interestingly, FXIIIa induced the formation of stable FXIIIa-Aβ complexes and oligomers in a calcium-dependent manner in which the glutamine at position 16 of the Aβ protein was of importance for complex formation. Conclusions We showed that FXIII and FXIIIa activity colocalise with the deposited Ab in CAA. In addition, we found that FXIIIa forms strong calcium-dependent protein-protein complexes with Ab, as well as oligomers. Together, our data suggests that FXIII is present and active in CAA, and that FXIIIa forms unique protein complexes with Ab that might play an important role in Aβ deposition in the vessel wall. 40 Biomarkers: Experimental and Methods 31. Recommendations on study design and data analysis for differential gene expression using RNA-seq E.I. Kooi, N. Ameziane, K. Roohollahi, M.P.G. Massink, J.C.D. Dorsman Clinical genetics, VU University Medical Center Introduction In the past few years, next-generation sequencing has become the preferred approach for the characterization and quantification of entire genomes. With respect to expression profiling, RNA-seq introduces fewer technical variance compared to conventional micro-arrays while providing additional information such as coding variants, alternative splicing, and novel transcripts. However, RNA-sequencing pioneers often find themselves confronted with practical considerations withholding them to embark on RNA-seq experiments. Based on our experience, with this poster we provide various practical considerations for differential gene expression analyses. Methods Total RNA from 12 head and neck squamous cell carcinoma cell lines and 6 matched fibroblasts cell lines were extracted. Extracts were prepared with TruSeq Stranded mRNA protocol and sequenced on a Hiseq2500 using the 100bps paired-end protocol. Subsequently, the impact of sequencing yield, strand information, alignment and read quantification was systematically analysed to come up with recommendations for RNA-seq study design and data analysis. Results Comparisons of single-end and paired-end analyses of all 18 samples shows very high similarity with regard to read counts (Pearson correlation ranging between 0.95 and 0.99). Furthermore, including strand-specific information only slightly increases the percentage of the transcriptome (3% of genes) that can be used for quantification. Alignment comparisons between TopHat and STAR show relatively good concordance in read counts (Pearson correlation ranging between 0.95 and 0.98). However, STAR has a higher mapping yield and accuracy compared to TopHat. More importantly, STAR's mapping speed is immensely higher than TopHat's, spending less than 30 minutes for whole transcriptome alignment compared to 24 hours for TopHat. Conclusions Our results show that sequencing costs can be drastically reduced when using RNA-seq for differential gene expression. Taken together with STAR's accurate and efficient mapping algorithm, cost-comparative RNA sequencing of large cohorts of samples is feasible in a short period of time VU University Medical Center Science Exchange Day 2014 41 Biomarkers: Experimental and Methods 32. Less is enough: scaling down protein input for phosphoproteomics based treatment selection in patients with advanced solid tumors Mariette Labots1, Koen van der Mijn1, Sander Piersma2, Richard de Haas1, Inge de Reus2, Jaco Knol2, Thang Pham2, Nicole van Grieken3, Gerrit Meijer3, Henk Verheul1, Connie Jiménez2 Department of Medical Oncology, VU University Medical Center OncoProteomics Laboratory, Department of Medical Oncology, VU University Medical Center 3 Department of Pathology, VU University Medical Center 1 2 Introduction Mass spectrometry-based phosphoproteomics of cancer cell- and tissue lysates provides a unique approach to evaluate the cell signaling network, revealing information on aberrantly activated signaling pathways and potential drug targets. To enable phosphoproteomics-based treatment selection for improved efficacy of targeted therapies in patients with advanced solid tumors, needle biopsies should provide reproducible profiles, representative of the individual tumor phospho-proteome. We have assessed reproducibility and tumor heterogeneity using limited input material. Methods Phosphopeptide immunoprecipitation (IP) using P-Tyr-1000 anti-phosphotyrosine-coated beads (PTMScan®, CST) was performed using 1, 5 and 10 mg protein from lysates of the colorectal cancer (CRC) cell line HCT116 and 3 patient-derived tumors. After measurement by LC-MS/MS, MaxQuant database searching and analysis were applied for phosphopeptide identification (ID), ion-intensitybased quantification and phosphosite localization. Results Cell line triplicates of 1, 5 and 10 mg protein input yielded a total of 454, 559 and 664 unique phosphosites, and a median number of 345 (range:266-376), 435 (236-448) and 501 (476-618) per replicate, respectively. The ID-reproducibility was 45% for 1 mg and 58% for 10 mg protein replicates. In tissue, a median total of 622 (427-754) unique phosphosites were identified per tumor, with a median number of 190 (91-353), 404 (199-512) and 546 (252-638) per sample using 1, 5 and 10 mg protein, respectively. Conclusions This scale-down study demonstrates that hundreds of phosphopeptides can be profiled at low ‘biopsy-level’ of protein input, enabling future phosphoproteomics-based therapy selection using patient tumor biopsies. CRC heterogeneity analyses are ongoing and will be presented at the meeting. 42 Biomarkers: Experimental and Methods 33. Discovery of biomarkers reflecting progression pathophysiology for relapse remitting and primary progressive MS subtypes by applying novel multiplex aptamer approach Arjan Malekzadeh1, Joep Killestein2 and Charlotte Teunissen1 1 2 Department of Clinical Chemistry, VU University Medical Center, Amsterdam Department of Neurology, VU University Medical Center, Amsterdam Introduction The patho-physiology of multiple sclerosis disease onset and progression remains undetermined. Understanding this is beneficial for prognosis, treatment strategies and for the development of new neuro-protective therapies. To unravel the patho-physiology of MS disease progression and possible identification of progression biomarkers, we performed proteomics on plasma proteins of patients with relapse-remitting MS (RRMS) with a benign disease course (n=10), very aggressive from onset RRMS (n=10) and primary progressive MS patients (PPMS) (n=10). Methods The proteomics was performed with aptamers by Somalogic, this assay detects 1129 blood biomarkers in a low volume of 65 µl of plasma. This method has been proven in other studies for other diseases however it has not yet been applied for MS. Results We observed 50 proteins differentially expressed between benign RRMS and aggressive RRMS. A comparison between aggressive RRMS and PPMS showed the expression of 112 proteins altered significantly. Generally, these proteins can be divided into; immune receptors, inflammatory response, growth factors, cell signaling, blood coagulation, cell adhesion, matrix metalloproteinases and neuronal/hormone homeostasis Conclusions This exploratory phase has led to the identification different pathways and markers. Subsequent validations with the best discriminating biomarkers with customized aptamer assays on larger sample size is required and ongoing VU University Medical Center Science Exchange Day 2014 43 Biomarkers: Experimental and Methods 34. De novo elucidation of metabolite clusters and their genetically influenced protein‑protein interaction sub‑networks based on a metabolome- and genome‑wide association study René Pool1,2,3,4,*, Harmen H.M. Draisma1,2,3,*, Mohammed El‑Kebir5,6,*, Jan Bert van Klinken3,7, Ko Willems van Dijk3,7, Cornelia M. van Duijn3,4,8, Christian Gieger3,9, Peter A.C. ’t Hoen3,7, Gunnar W. Klau5,6, Nicholas G. Martin3,10, Mark I. McCarthy3,11, Michael Kobl3,9, Andres Metspalu3,12, P. Eline Slagboom3,4,13, Tim D. Spector3,14, Konstantin Strauch3,9,15, Dorret I. Boomsma1,2,3,4 and Aaron Isaacs3,8 * These authors contributed equally 1 VU University Amsterdam, Faculty of Psychology and Education, dept. Biological Psychology, Amsterdam, The Netherlands 2 The EMGO+ Institute for Health and Care Research, Amsterdam, The Netherlands 3 ENGAGE: European Network of Genomic And Genetic Epidemiology 4 BBMRI-NL: Infrastructure for the Application of Metabolomics Technology in Epidemiology (RP4), The Netherlands 5 Centrum Wiskunde & Informatica (CWI), Life Sciences Amsterdam, The Netherlands 6 VU University Amsterdam, The Centre for Integrative Bioinformatics VU (IBIVU), Amsterdam, The Netherlands 7 Leiden University Medical Center, Department of Human Genetics, Leiden, The Netherlands Erasmus Medical Center, Department of Epidemiology, Rotterdam, The Netherlands 9 Institute of Genetic Epidemiology, Helmholtz Zentrum München - German Research Center for Environmental Health, Neuherberg, Germany 10 Queensland Institute of Medical Research, Genetic Epidemiology, Brisbane, Australia 11 Wellcome Trust Centre for Human Genetics, University of Oxford, Oxford, UK 12 University of Tartu, Estonian Genome Center, Tartu, Estonia 13 Leiden University Medical Center, Department of Molecular Epidemiology, Leiden, The Netherlands 14 King’s College London, Department of Twin Research & Genetic Epidemiology, London, United Kingdom 15 Institute of Medical Informatics, Biometry and Epidemiology, Chair of Genetic Epidemiology, LudwigMaximilians-Universität, Munich, Germany 8 Introduction: A genome‑wide association study (GWAS) is a hypothesis‑generating method to identify the associations between single‑nucleotide polymorphisms and an outcome, e.g. the serum level of a metabolite in humans. Serum levels of biochemically closely connected metabolites are influenced by proteins encoded by shared genes. It is difficult to identify such groups of biochemically closely connected metabolites from the results of single‑metabolite GWASs. We developed a method that finds connected proteins which are shared across different metabolites. Methods: The results of GWASs for the serum levels of 129 metabolites measured in seven cohorts (N = 7,478 subjects) by mass spectrometry‑based metabolomics techniques were pooled in meta‑analysis. For each metabolite, gene‑wise p‑value sets were calculated as input for the integrative network analysis approach “Heinz” to find 129 optimal sub‑networks of connected proteins in the protein‑protein interaction network “PINA”. The 129 metabolites were then clustered based on their sub‑network similarity. Subsequent “Heinz” analyses of the proteins of these clusters will yield ‘consensus’ PINA sub‑networks. Results: We found several metabolite similarity clusters containing two metabolites or more. A number of these were part of one single chemical class. The generated consensus PINA sub-networks designated to the metabolite similarity clusters will be analyzed using enrichment strategies. Conclusions: We developed a method to elucidate the genetically influenced biochemical basis of (co) variation for different metabolites. Our method finds sets of interacting genetically influenced proteins that are shared across distinct metabolites. Thereby it highlights connections among GWAS findings for individual metabolites as measured using metabolomics techniques. 44 Biomarkers: Experimental and Methods 35. Protein kinase activity profiling of patients with Alzheimer’s Disease and non-demented controls reveals pathway changes Andrea F.N. Rosenberger1,2, Riet Hilhorst3, Rik de Wijn3, Wiesje M. van der Flier1, Annemieke J.M. Rozemuller2, Philip Scheltens1 , Jeroen J.M. Hoozemans2 and Saskia M. van der Vies2 Alzheimer center & Department of Neurology and Department of Pathology, Neuroscience Campus Amsterdam, VU University Medical Center, Amsterdam 3 PamGene BV International, Wolvenhoek 10, 5211 HH ‘s-Hertogenbosch 1 2 Introduction Alzheimer’s disease (AD) is a progressive neurodegenerative disorder affecting a constantly growing proportion of our ageing population. There is currently no treatment or cure available. For the discovery of new biological markers and drugable targets it is essential to identify signaling pathways that are involved in AD pathology. This study is aimed at identifying protein kinases in human brain tissue at different stages of the disease. Signaling pathways that are activated in AD are identified and investigated. Methods For the detection of protein kinase activity brain tissue lysates from AD cases and non-demented controls are prepared (n=20). Kinase activity profiles of the samples are determined using a peptide-based microarray, which contains 140 peptides derived from known kinase substrate sequences covalently attached to a porous matrix. Fluorescently labelled anti-phosphoserine, anti-phosphothreonine and/or anti-phosphotyrosine antibodies are used to detect phosphorylated peptides on the chip. Results The phosphorylation of a subset of peptides (71) decreases with progression of the disease and can be linked to kinases using GeneGo software. FAK1 is known to be associated with senile plaques in AD and Lck, has previously been reported to be downregulated. Pathways which are changed in AD, f.e. the receptor mediated axon growth repulsion pathway, are identified. Conclusions Protein kinase activity profiling is a new approach to reveal new signaling pathways involved in AD pathology and can potentially lead to diagnostic biomarkers and drug targets for treatment of the disease. Those findings need to be validated in a larger cohort (n = 100). VU University Medical Center Science Exchange Day 2014 45 Biomarkers: Experimental and Methods 36. Substrate surface alter mechano-responses of vaginal fibroblasts from prolapsed tissues in premenopausal women with pelvic organ prolapse Alejandra M. Ruiz-Zapata1, Manon H. Kerkhof 2, Behrouz Zandieh-Doulabi1,3, Hans A.M. Brölmann2, Theo H. Smit1, Marco N. Helder1 1 Department of Orthopaedics, VU University Medical Center, Research Institute MOVE, Netherlands Institute for Regenerative Medicine 2 Department of Obstetrics & Gynaecology, VU University Medical Center 3 Department of Oral Cell Biology, ACTA-University of Amsterdam and VU University, Research Institute MOVE Introduction Pelvic organ prolapse (POP) is a disease characterised by the weakening of the pelvic floor and subsequent prolapse of the vagina, bladder or rectum outside the body affecting almost 50% of elderly women. Fibroblasts are responsible for tissue remodelling and maintenance, but little is known about their role in POP. Therefore, this study aimed to identify the effects of cyclic mechanical loading (CML) on two different substrate surfaces on extracellular matrix (ECM) remodelling factors by fibroblasts from women with prolapse. Methods Fibroblasts were isolated from the anterior vaginal wall of premenopausal women in two places: non-prolapsed (8 controls and 10 POP cases) and prolapsed site (10 POP cases). Cells from passage 3 were seeded on collagen-coated or uncoated bioflex®plates ± CML (Flexercell; 0,2Hz; 48h). Morphological changes were observed and matrix metalloproteinase (MMP)-2 and its inhibitor (TIMP-2) were evaluated at protein and gene expression levels. Results No differences were seen between healthy controls and the non-POP site from POP cases. Cell attachment and alignment was facilitated by collagen-coated surfaces. Mechanoresponses of vaginal fibroblasts to matrix components and mechanical loading were different in cells from prolapsed and non-prolapsed tissues with regard to secretion and activation of MMP-2, and gene expression of MMP-2 and TIMP-2. Conclusions Fibroblasts from the prolapsed vaginal wall have altered mechanoresponses depending on matrix substrate and compared to non-prolapsed sites. This indicates an acquired rather than an intrinsic defect which favours the development of autologous cell-based tissue engineering constructs to treat POP. 46 Biomarkers: Experimental and Methods 37. Quantitating neutrophil oxidative stress by Flow Cytometry Bob Smit1,2, Monique C. de Waard1,2 , Yvo M. Smulders2,3, Christa Boer2,4, Alexander B.A. Vonk2,5, Dennis Veerhoek2,5, Juan J. García Vallejo2,6, René. J.P. Musters2,7, Suzanne Kamminga2,4, Angélique M.E Spoelstra - de Man1,2 Department of Intensive Care, VU University Medical Center, Institute for cardiovascular research, VU University Medical Center 3 Department of Internal Medicine, VU University Medical Center 4 Department of Anaesthesiology, VU University Medical Center 5 Department of Cardiothoracic Surgery, VU University Medical Center 6 Department of Molecular Cell Biology & Immunology, VU University Medical Center 7 Department of Physiology, VU University Medical Center 1 2 Introduction Relative to pure in-vitro research, clinical research is subject to uncontrollable timetables, which further complicates the difficult measurement of highly reactive oxygen species (ROS). We therefore sought to establish an easy to perform assay to detect ROS in whole blood that is less subject to delay between sample preparation and analysis Methods Citrated whole blood samples were collected from healthy volunteers and from patients before (baseline) and during (1 hour of Cardiopulmonary Bypass, CPB) Coronary Artery Bypass Graft (CABG) surgery. 30 ml citrated whole blood was incubated for 1 hour with CellROX® Green, immediately after sampling. Erythrocytes were lysed via hypotonic shock. The remaining cells were washed three times with PBS and stored at room temperature, in the dark, until analysis. Mean Fluorescence Intensity of the neutrophil population, which is directly proportional to the ROS produced, was determined by flow cytometry as soon as possible after incubation of the second CABG sample. Conclusions Our current method is easy to perform, implementable into clinical research and is able to detect different ROS responses. 100 Mean Fluorescence Intensity (a.u.) Results As expected, little to no ROS production was demonstrated in healthy volunteers and baseline samples from CABG surgery patients, while an increase was found after one hour of CPB (figure). Interestingly, this method also showed separate ROS producing neutrophil populations, which warrants further investigation. 80 60 40 20 0 Healthy Baseline 1HR CPB VU University Medical Center Science Exchange Day 2014 47 Biomarkers: Experimental and Methods 38. (Z)-2-(4-[18F]fluoro-2-oxoindolin-3-ylidene)-N(4-methoxyphenyl)hydrazine carbothioamide is an aberrant P-gp tracer Verbeek, J.1; Eriksson, J.1; Syvänen, S.2; Voskuyl, R.A.2,3; de Lange, E.C.2; Huisman M.C.1; Lammertsma, A.A.1 and Windhorst, A.D.1 Department of Radiology & Nuclear Medicine, VU University Medical Center, Amsterdam Division of Pharmacology LACDR Leiden University, Leiden 3 Epilepsy institute of the Netherlands foundation (SEIN), Heemstede 1 2 Introduction Recently compound 1 has been characterized as a P-gp inhibitor that is not transported1. This characteristic is of particular interest for diseases which are implicated with increased P-gp expression levels, such as epilepsy and Alzheimer’s disease. The P-gp binding properties of two fluorine-18 labelled analogues were assessed in vivo. Methods [18F]fluoro ([18F]2a) and 6-[18F]fluoro ([18F]2b) analogues of 1 were synthesized, purified and formulated. Ex vivo biodistribution and metabolism of [18F]2a,b were investigated in rodents and cerebral uptake of [18F]2a was investigated using PET, both at baseline and after tariquidar pretreatment (15 mg.kg-1, iv), as well as in P-gp and BCRP knockout mice. Results Both [18F]2a,b were obtained in low overall yield (2.3 ± 0.9%). At 45 minutes after injection, fractions of intact [18F]2a in plasma and brain were 12% and 69%, respectively, and for [18F]2b 7% and 16%. Logan analysis showed a brain VT of 12.6 for [18F]2a at baseline, which did not change significantly to 13.2 after tariquidar treatment. Ten minutes after injection, brain SUV’s of 1.4 ± 0.1, 2.3 ± 0.3 and 1.8 ± 0.1 were observed in BCRP-, P-gp knockout and wild-type mice respectively. Conclusions [18F]2a,b were successfully synthesized and due to fast metabolism [18F]2b was not further studied. Tariquidar pre-treatment did not significantly alter [18F]2a brain VT indicating lack of pronounced P-gp substrate character. 48 Biomarkers: Experimental and Methods 39. Large lactate clearance shifts in the first 8 hours after traumatic brain injury are associated with increased mortality S.E. Dekker1, H.M. de Vries1, W.D. Lubbers1, C. Boer1 1 Anesthesiology, Institute for Cardiovascular Research, VU University Medical Center Introduction Impaired lactate clearance is predictive for mortality in general trauma patients, however the association of this biomarker with outcome in patients with traumatic brain injury (TBI) is unknown. This study examined the association between lactate clearance and mortality in these patients. Methods Lactate values were retrieved retrospectively from the medical records of 531 patients admitted to the emergency department (ED) between 2011-2012 with a head abbreviated injury score (AIS) ≥3. Patients without initial lactate drawn <30 minutes after admission, or without a second lactate measurement within 8 hours after admission were excluded. Lactate clearance was calculated as follows: Lactate clearance (%/hour)=((Lactateinitial–Lactatedelayed)/Lactateinitial)×100/Delay, and stratified as <-20, -19 to -10, -9 to 9, 10 to 19, and >20%/h. The dataset further included the Glasgow Coma Scale (GCS), Injury Severity Score (ISS), hospital and ICU days. Results Overall, 126 patients were included. Mortality rates in the <-20%/h group, -19 to -10%/h group, and -9 to 9%/h group were 57%, 10%, and 20% respectively. In the 10 to 19 group 4 of 23 patients died (17%), while in the highest lactate clearance group 16 of 38 patients died (42%; Χ2 p=0.01). AIS head, GCS, ISS, hospital and ICU days were not associated with lactate clearance. Lactate clearance was correlated with initial pH (r=-0.21, p=0.02) and initial base excess (r=-0.24, p=0.009). Conclusions Large shifts in lactate levels (lactate clearance <-20 or >20%/h) in the first 8 hours after ED admission are associated with higher mortality rates compared to moderate or stable lactate clearance. VU University Medical Center Science Exchange Day 2014 49 Biomarkers: Experimental and Methods 40. Synthesis of a 11C-labeled tissue transglutaminase inhibitor using a [11C]CO carbonylation reaction Van der Wildt, B.1, Bijkerk, J.1, Drukarch, B.2, Lammertsma, A.A.1, Windhorst, A.D.1 1 2 Department of Radiology and Nuclear Medicine, VU University Medical Center, Amsterdam Department of Anatomy and Neuroscience, VU University Medical Center, Amsterdam Introduction Tissue transglutaminase (tTG) is a calcium dependent enzyme that is responsible for the formation of isopeptide bonds between glutamine and lysine residues resulting in mechanically and metabolically stable protein oligomers. In neurodegenerative diseases characterized by specific protein aggregates such as Alzheimer’s, Parkinson’s and Huntington’s disease, tTG has been shown to be overexpressed, to be active in and to colocalize with the amyloid plaques. The aim of this research is to develop a PET tracer for imaging of active tTG in vivo to further explore its role in neurodegenerative diseases. Methods Compound 1 is a potent irreversible tTG inhibitor with a good selectivity towards other transglutaminase family members that structurally allows for labeling with carbon-11 at the carbonyl function of the acrylamide. Shortly, cyclotron produced [11C]CO2 is reduced to [11C]CO using molybdenum and subsequently transferred to the reaction vial using xenon as carrier gas. O O S N N O O N * H 1 Results The reference compound and precursor molecules for radiolabeling were synthesized in good yields. For radiolabeling, activation of the amine precursor by the addition of Li-HMDS to the reaction mixture was essential to obtain high radiochemical yields. After HPLC purification and formulation, the product was obtained on average in 40% yield, starting from [11C]CO, with a purity > 99 % and a specific activity > 100 GBq.µmol-1. Conclusions Compound [11C]1 could be obtained in high yield by activation of amine precursor prior to the reaction using Li-HMDS. Metabolism and biodistribution of [11C]1 will be evaluated in vivo. 50 Biomarkers: Experimental and Methods 41. Colorectal cancer candidate biomarkers identified by tissue secretome proteome profiling Meike de Wit1,2, Huub Kant2, Sander R. Piersma2, Thang Pham2, Sandra Mongera1, Maaike P.A. van Berkel3, Epie Boven3, Fredrik Pontén4, Gerrit A. Meijer1, Connie R. Jimenez2* and Remond J.A. Fijneman1*. Department of Pathology (Tumor Profiling Unit) Department of Medical Oncology (OncoProteomics Laboratory) 3 Department of Medical Oncology, VU University Medical Center, Amsterdam 4 Department of Genetics and Pathology, The Rudbeck Laboratory, Uppsala University, Uppsala, Sweden 1 2 *Shared corresponding authorship Introduction Colorectal cancer (CRC) is a major health problem. Biomarkers associated with molecular changes in cancer cells can aid early detection, diagnosis, prognosis, therapy selection, and disease monitoring. Tumor tissue secretomes are a rich source of candidate biomarkers. The aim of this study was to identify CRC protein biomarkers in tissue secretomes. Methods Secretomes of four pairs of fresh human CRC tissue and patient-matched normal colon tissue samples, and secretomes of five CRC cell lines were analyzed by GeLC-MS/MS. Data analysis was based on label-free spectral counting, Ingenuity Pathway Analysis, Secretome/SignalP, STRING and Cytoscape. Results 2703 proteins were identified in tissue secretomes, of which 409 proteins were significantly more present in CRC samples than in controls. Biomarker selection of 76 candidates was based on consistent and abundant over-representation in cancer- compared to control-secretomes, and presumed neoplastic origin. Overlap analysis with previously obtained datasets revealed 21 biomarkers suited for early detection of CRC. Immunohistochemistry confirmed overexpression in CRC of one candidate marker (MCM5). Conclusions We identified 76 promising biomarker proteins that have potential to be used for development of blood- or stool-based assays to support clinical management of CRC. Further studies are required to validate clinical applicability of these candidate biomarkers. VU University Medical Center Science Exchange Day 2014 51 Biomedical Engineering 42. Measuring mechanical changes of brain tissue in an Alzheimer’s mouse model in vivo Beekmans S.V. 1, Broersen R.2, Antonovaite N.1, Hoogland T.M.2, De Zeeuw C.I.24, Hol E.M.3 and Iannuzzi D.1 Biophotonics and Medical Imaging, VU Laserlab, VU University Amsterdam Netherlands Institute for Neuroscience, Royal Academy of Arts and Sciences (KNAW) 3 Brain Center Rudolf Magnus, UMC Utrecht, Utrecht 4 Department of Neuroscience, ErasmusMC, Rotterdam 1 2 Introduction Brain injuries and neurodegenerative diseases, such as Alzheimer’disease, lead to reactive gliosis in the brain parenchyma. Together with amyloid plaque deposition this gliosis might lead to a change in the stiffness of the brain. Currently, there is no instrument that can effectively acquire quantitative in vivo measurements of mechanical stiffness in the brain. In this study we apply ferrule-top technology to measure stiffness changes in the cortex of the brain of an Alzheimer mouse model, the APPswPS1dE9 mouse. Methods Mechanical stiffness will be measured for both the healthy mouse brain tissue and the tissue of the Alzheimer model by means of nano-indenation using ferrule-top technology. First, extracted and perfused C57/BL6 mouse brains will be tested in vitro to validate nano-indentation of soft tissue. Afterwards the experiment will be extended to fresh in vitro brain tissue and finally in vivo indentation-measurements will be done. Results Initial measurements on perfused mouse brains obtained by in vitro nano-indentation show that ferrule-top technology can be applied successfully to measure the Young’s modulus (YM) of brain tissue. We measured a YM of 1.7 ± 0.6 MPa in the cortex, whereas the YM of cerebellar tissue was measured at 0.6 ± 0.2 MPa. Conclusions A pilot study was performed to assess mechanical properties of mouse brain tissue using ferruletop technology. We were able to demonstrate that brain stiffness varies between cerebellum and cortex. This result is promising for future optomechanical experiments on brain tissue, which will set the basis for the field of optomechanical genetics. 52 Biomedical Engineering 43. Endoscopic polarization sensitive optical coherence tomography and in vivo animal lung imaging Jianan Li1, Fabio Feroldi1, Mattjis de Groot1, Jianhua Mo1, Frank Helderman1, Joop de Langen2, Johannes M.A. Daniels2, Katrien Grunberg3, Tom G. Sutedja2 and Johannes F. de Boer1 Institute for Lasers, Life and Biophotonics Amsterdam, Department of Physics and Astronomy, VU University Amsterdam 2 Department of Pulmonary Diseases, VU University Medical Center 3 Department of Pathology, VU University Medical Center 1 Introduction Optical Coherence Tomography is a low coherence interferometric technique that allows for high resolution in vivo imaging of biological tissue. Polarization Sensitive OCT is one of its extensions, as it can determine the birefringence of tissue. This can help distinguishing different types of tissue. Methods We developed a catheter that allows for minimally invasive diagnosis of the bronchi. The high scanning speed (52 frames per second) permits video rate imaging. The overall diameter of the endoscope is 1.65 mm. The resolution of the OCT system is about 15 µm. To consistently determine the birefringence of the tissue, a device that generates two orthogonal polarization states was used. Results 1) In vivo OCT image of a live goat lung 2) Ex vivo tissue birefringence image of chicken muscle and tendon Conclusions High resolution in vivo OCT images of lungs of live animals were acquired. The fast scanning speed allows for quick diagnosis of large volumes of tissue. The obtained OCT images are in agreement with the histological images of the same measured sample. The ex vivo birefringence image validates the polarization sensitive function of the system and demonstrates the potential of tissue specific imaging. This device can help the physician in guiding and limiting the excision of tissue for biopsy for cancer diagnosis. VU University Medical Center Science Exchange Day 2014 53 Biomedical Engineering 44. Dual-channel multi-photon microendoscope for label free optical diagnosis of diseases G. D. Galgano1, N.V. Kuzmin1, M.L. Groot1 Biophotonics & Medical Imaging, LaserLaB Amsterdam, Neuroscience Campus Amsterdam, VU University Amsterdam 1 Introduction High-resolution images of label-free biological tissue can be generated with multi-modal laser scanning microscopy (MLSM) , featuring high penetration depth and low photo-damage via recording of second and third harmonic signals and multi-photon excited (auto-)fluorescence (S. Witte et al., PNAS 108, 5970, 2011). By combination of the appropriate pair of channels it is possible to have morphological and target-specific image contrast from natural occurring structures of the human body (Hoover and Squier, Nat. Photonics 7, 23, 2013), making MLSM useful for optical diagnosis of a wide variety of diseases. Medical and clinical application demands image acquisition from difficult access areas in a minimally invasive way, what motivates the integration of MLSM technology into a microendoscopic setup. Methods The microendoscopic system features a simplified video-rate multi-photon microscope, equipped with an optical fiber flexible probe. Pump radiation of 1300 nm and 300 fs is used to produce higher order signals in the visible range, while keeping low levels of dispersion and non-linear effects in the silica fibers. Results The constructed probe features a coherent fiber bundle and a custom made micro-objective, which are assembled and characterized on resolution, field of view, imaging depth and image quality. Conclusions The results show that MLSM can be brought to an endoscopic system creating a versatile clinical diagnostic tool. 54 Biomedical Engineering 45. Towards novel antibiotics: targeting the essential bacterial cell division protein FtsQ M. Glas1, H.B. van den Berg van Saparoea1, G.M. Koningstein1, R. Nachane2, F. Figaroa2, E. Ab2, J. Hollander2, G. Siegal2, I.J.P. de Esch1, S. Luirink1 1 2 Amsterdam Institute for Molecules, Medicines and Systems (AIMMS), VU University Department of Protein Chemistry, Leiden University Introduction Bacterial resistance is an emerging problem. To counter the growing threat of drug resistance, the development of novel classes of antibiotics is of utmost importance. In this project the essential bacterial cell division protein FtsQ is investigated as a potential antibiotic drug target. During cell division FtsQ interacts with FtsB and FtsL forming a heterotrimeric complex. Interference with these critical interactions inhibits bacterial cell division and thus proliferation [1]. Methods The protein-protein interactions of FtsQ with FtsB and FtsL were biochemically confirmed in a pull down assay. Interactions were mapped at the amino acid level using different site-directed protein cross-linking techniques. Furthermore, using Target Immobilized NMR Screening (TINS) [2], a fragment library was screened for molecules that bind to FtsQ, and the resulting hits were validated by Surface Plasmon Resonance (SPR). Results The protein cross-linking experiments resulted in the identification of two interaction sites [3]. From the TINS fragment screen 72 hits were identified to bind to FtsQ. Validation of these hits using SPR resulted in the confirmation of a number of small molecules (fragments) that showed significant affinity for FtsQ. Conclusions We identified interaction hotspots in FtsQ that constitute potential targets for novel synthetic antimicrobial drugs. Furthermore, using two orthogonal screening methods several fragments were identified that interact with FtsQ. The binding sites of these molecules will be mapped and they will be optimized towards potent inhibitors of the essential protein-protein interactions of FtsQ. 1 F. van den Ent et al., Mol Microbiol, 2008. 68(1): p. 110-23. 2 S. Vanwetswinkel et al., Chem Biol, 2005. 12(2): p. 207-16. 3 H.B. van den Berg van Saparoea et al., J Biol Chem, 2013. 288(34): p. 24340-50. VU University Medical Center Science Exchange Day 2014 Cell division protein FtsQ. The interaction sites are indicated by dotted circles. 55 Biomedical Engineering 46. The effect of medication on fMRI resting state connectivity in focal epilepsy Kees Hermans1,2, Pauly Ossenblok3, Albert Colon4, Kees Visser5, Ruud Verdaasdonk2, Paul Boon1, Jan de Munck2 Department of Research and Development, Kempenhaeghe, Heeze Department of Physics and Medical Technology, VU University Medical Center, Amsterdam 3 Department of Clinical Physics, Kempenhaeghe, Heeze 4 Department of Neurology, Kempenhaeghe, Heeze 5 Philips Healthcare, Best 1 2 Introduction Previous studies have shown that spatial independent component analysis (ICA) of resting state fMRI enables the identification of resting state networks (e.g. default mode network, visual network, etc.) and, applied to patients with epilepsy, an epilepsy related network. The goal of this study was to investigate the effect of medication withdrawal on resting state networks in patients with refractory focal epilepsy. Methods Simultaneous EEG/fMRI data have been acquired for ten patients with focal epilepsy who were candidates for epilepsy surgery. Patients were scanned before the start of standard pre-surgical video-EEG when still on medication (condition A), and after medication withdrawal (condition B). EEG/fMRI data were analyzed using both the general linear model (GLM) approach and ICA. Spatial correlation of this map with all the ICs enabled identification of the epileptic IC (ICE). A similar procedure was used to identify the other resting state fMRI networks. The difference in functional connectivity between conditions A and B was quantified using a GLM approach applied to the concatenated time series of the resting state components. Results ICEs were identified in the resting state fMRI data of ten patients with measurements in conditions A and B. Significant differences in functional connectivity between resting states were found in each patient. A preliminary finding is that functional connectivity is higher after medication withdrawal. Conclusion In this study it was shown that differences in resting state functional connectivity caused by drugs withdrawal can be quantified for individual patients. 56 Biomedical Engineering 47. A yeast genome-wide screen uncovers roles for chromatin modifications and ubiquitin homeostasis in acetaminophen toxicity Angelina Huseinovic1, Chris Vos1, Jan Kooter2 Division of Molecular Toxicology, Amsterdam Institute of Molecules, Medicines and Systems, VU University Amsterdam 2 Department of Genetics, Amsterdam Institute of Molecules, Medicines and Systems, VU University Amsterdam 1 Introduction A yeast collection containing deletion strains for each non-essential gene is available. This provides the tools to link genotypes to drug sensitivity. We screened ~1500 single gene deletion strains towards acetaminophen (APAP) stress. Although APAP is a widely used analgesic and antipyretic drug, the exact causes of its side effects are still unknown. One risk factor, the bioactivation of APAP into NAPQI, is absent in yeast due to lack of a drug-metabolizing cytochrome P450. Yeast genomics may suggest novel pathways relevant to human APAP-sensitivity. Methods We used a Saccharomyces cerevisiae deletion library to perform a genome-wide loss-of-function screen. The growth of the deletion strains was quantified at various concentrations of APAP. The identified genes were grouped by function using the String protein interaction search tool. Results We identified 107 deletion strains that exhibited higher resistance to APAP compared to the wild type. Upon clustering these genes, two important central functions emerged: ubiquitin modification and RNA polymerase II transcription. Furthermore, 70 APAP sensitive deletion strains were identified. Here, two other clusters appeared: genes involved in histone modifications and chromatin remodeling and genes involved in vacuolar trafficking. Conclusions Our study shows that APAP has pleiotropic effects in the cell, which are unrelated to bioactivation by cytochrome P450. The transcriptional and epigenetic profile of the cell seems to be an important determinant in APAP-sensitivity. Furthermore, it remains to be seen which of the many roles of ubiquitin in the cell is crucial in APAP-toxicity and what is the relevance in humans. VU University Medical Center Science Exchange Day 2014 57 Biomedical Engineering 48. Single-molecule Acoustic Pushing (smAP!): Manipulating single-molecules with ultrasound Gerrit Sitters1,2, Douwe Kamsma1,2, Gijs Wuite1,2 and Erwin Peterman1,2 1 2 Department of Physics and Astronomy, VU University Amsterdam, Amsterdam LaserLaB Amsterdam, VU University Amsterdam, Amsterdam Introduction The ability to study individual biomolecules in vitro has greatly expanded our knowledge of biological systems. Existing single molecule techniques such as optical and magnetic tweezers or atomic force microscopy (AFM) allow manipulation of individual biomolecules such as DNA. They suffer from either being technically challenging or offering low experimental throughput. Methods We constructed a lab-on-chip device, by combining a microfluidic system and a piezo electric element, creating a layered resonator. The device is easy to assemble and cheap. It allows application of controllable forces up to hundreds of pN on tethered microspheres. Forces can be applied homogenously over an area of 0.5 cm2, allowing simultaneous measurement of multiple microspheres. Results We demonstrated the value of this approach by measuring the mechanic properties of multiple DNA molecules at the same time. This can be seen in figure 1, where two force-extension curvesA, a DNA protein interactionsB and two force clampingC measurement are shown. Figure 1 Conclusions In this study we have developed a novel technique to study single biomolecules. Since it is cheap and low tech it can be widely used by biophysicists and furthermore have application in lab on chip devices. 58 Biomedical Engineering 49. Development of a baby friendly non-contact method for measuring vital signs, first results of clinical measurements in an open incubator on a Neonatal Intensive Care Unit John H.G.M. Klaessens1, Marlies van den Born1, Albert van der Veen1, Janine Sikkens-vd Kraats1, Frank A.M. van den Dungen2, Rudolf M. Verdaasdonk1 1 2 Department Physics and Medical Technology, VU University Medical Center Department of Pediatrics, VU University Medical Center Introduction For infants and neonates in an incubator vital signs, such as heart rate, breathing, skin temperature and blood oxygen saturation are measured by sensors and electrodes sticking to the skin. This can damage the vulnerable skin of neonates and cause infections. In addition, the wires interfere with the care and hinder the parents in holding and touching the baby. These problems initiated the search for baby friendly ‘non-contact’ measurement of vital signs. Methods Using a sensitive color video camera and specially developed software, the heart rate was derived from subtle repetitive color changes. Potentially also respiration and oxygen saturation could be obtained. A thermal camera was used to monitor the temperature distribution of the whole body and detect small temperature variations around the nose revealing the respiration rate. Results After testing in the laboratory with volunteers, two babies were monitored (with parental consent) in the neonatal intensive care unit (NICU) simultaneously with the regular equipment. From the color video recordings accurate heart rates could be derived and the thermal images provided accurate respiration rates. To correct for the movements of the baby, tracking software could be applied. At present, the imaging processing was performed off-line. Using narrow band light sources also non-contact blood oxygen saturation could be measured. Conclusions Baby friendly non-contact monitoring of vital signs has proven to be feasible and can be developed into a real time system. VU University Medical Center Science Exchange Day 2014 59 Biomedical Engineering 50. LC-MS based metabolomics as a tool for studying the Warburg effect Petra Krumpochova1, Martin Giera2,3, Bas Teusink3, Manfred Wuhrer1, Martine Smit4, Azra Mujic-Delic4, Filipe Branco dos Santos3 and Wilfried Niessen1 Division of BioAnalytical Chemistry, Amsterdam Institute of Molecules, Medicines and Systems, VU University Amsterdam 2 Center for Proteomics and Metabolomics, Leiden University Medical Center 3 Center for Integrative Bioinformatics, VU University Amsterdam 4 Division of Medicinal Chemistry, Amsterdam Institute of Molecules, Medicines and Systems, VU University Amsterdam 1 Introduction The metabolic phenomenon where cancer cells rely on aerobic glycolysis instead of oxidative phosphorylation, was described for the first time by Otto Warburg over 80 years ago and it was named after him. Aerobic glycolysis is an inefficient way to generate ATP producing only 2 molecules of ATP per molecule glucose, whereas oxidative phosphorylation generates 32 ATP molecules per molecule glucose. The question immediately arises as to why cancer cells would switch to a less productive form of energy production. One hypothesis describes increased aerobic glycolysis as an adaptation to hypoxic environment. Although the exact mechanisms underlying the Warburg effect are unclear, the importance of increased glycolysis in cancer cells has been experimentally demonstrated. Methods In the here presented project, we aim for the development of an integrated systems biology approach to investigate the underlying mechanisms of the Warburg effect. At the core of our project, we established simple, fast and reproducible liquid chromatography mass spectrometry (LC-MS/MS) based analytical platforms for detection and quantification of glycolytic intermediates as well as purine and pyrimidine metabolites. In addition a gas chromatography mass spectrometry (GC-MS) platform for detection and quantification of amino acids was established. Results Glycolytic intermediates were separated on a C18 column by ion-pairing LC, whilst purine and pyrimidine metabolites were separated on a Luna NH2 column operated in the HILIC mode. Selective reaction monitoring on a triplequadrupole instrument was applied for detection. Amino acids were separated using GC after derivatization using a Zebron ZB-AAA column and detected by MS in selective ion monitoring mode. Conclusions The applicability of the new platform was demonstrated by analyzing intracellular metabolite levels in yeast samples and extracellular metabolites of NIH 3T3 mammalian cell lines. All platforms will be further applied to various biological matrices in the context of the Warburg effect. 60 Biomedical Engineering 51. Chronic hypoxia-enforced inhibition of vascularization; Involvement of HIF1α and HIF2α Tessa Nauta1,4, Ester Weijers1, Cees Oudejans2, Sue Gibbs3, Rik Scheper4, Victor van Hinsbergh1, Pieter Koolwijk1 Department of Physiology, Institute of Cardiovascular Research, VU University Medical Center, Amsterdam 2 Department of Clinical Chemistry, VU University Medical Center, Amsterdam 3 Department of Dermatology, VU University Medical Center, Amsterdam 4 ASkin BV, Amsterdam 1 Introduction Successful transplantation and tissue engineering requires adequate vascularization. Even though short term hypoxia stimulates angiogenesis, in chronically hypoxic tissues, endothelial cells have reduced angiogenic capacities. The Hypoxia Inducible Factors (HIF1α and HIF2α) regulate the expression of many genes under hypoxic conditions. Therefore, this study aims to investigate the role of HIF1α and HIF2α in chronic hypoxia-enforced inhibition of vascularization. Methods Human microvascular endothelial cells (hMVECs) were (pre)cultured at 20% or 1% oxygen for 14 days and transfected with short interfering RNAs (si-control, si-HIF1α or si-HIF2α) and either (i) seeded on top of 3D fibrin matrices and stimulated with VEGF and TNFα to induce sprouting or (ii) stimulated with VEGF and TNFα to isolate total RNA after 24 hours that was analyzed by genome-wide RNAsequencing. Results hMVECs (pre)cultured at 20% oxygen formed sprouts in vitro, whereas - surprisingly - the cells preconditioned at 1% oxygen did not. Cells transfected with si-HIF2α were able to overcome this inhibition and formed sprouts at 1% oxygen, while the cells transfected with si-HIF1α or si-control could not. The RNA-seq data showed in three different hMVECs between 530 and 630 differentially regulated genes under chronic hypoxia, between 695 and 705 differentially regulated genes in si-HIF1α transfected hMVECs and between 705 and 745 differentially regulated genes in si-HIF2α transfected hMVECs. Conclusions Clearly, no tube-like structures were formed under chronic hypoxia. However, transfection of chronic hypoxic cells with si-HIF2α restored the sprouting. This indicates that counter-intuitively HIF2α impairs endothelial tube formation in vitro. The genome-wide RNA-sequence analyses will provide us with information about the involved genes and pathways downstream of HIF2α. VU University Medical Center Science Exchange Day 2014 61 Biomedical Engineering 52. The Forces that Shape our Spine: Mechanics in Somitogenesis Ben Nelemans1, Manuel Schmitz1, Marjolein Blaauboer1, Theo Smit1 1 Department of Orthopedic Surgery, VU Medical Center Introduction The middle layer in vertebrate embryos rhythmically organizes its mesenchymal cells from head to tail into epithelialized segments, called somites (Fig. 1). These cell blocks are the precursors for our segmented skeleton. This robust clockwise epithelialization is accompanied by an oscillating gene network, called the segmentation clock. We hypothesize that besides the genetic mechanism, mechanics play an important role in this process and might even induce the periodic gene expression. However, little is known about the forces that shape embryos. Methods Chick embryos are mechanically manipulated in vitro with micromanipulators. The embryos are axially stretched during development to identify the role of embryo elongation during segmentation. With immunohistology we analyze the interactions between the different embryonic layers, the cells in them and the matrix components that surround them. Results Our preliminary results show that additional longitudinal tension can double the already formed segments and potentially change the number of segments. The doubled segments have similar morphology to normal somites. Conclusions The axis patterning in the vertebrate embryo seems sensitive to forces. Understanding the role of forces in the spatiotemporal segmentation could hopefully provide us with valuable information on processes where mesenchymal to epithelial transitions play a role, not only in body plan development, but also wound healing and cancer metastasis. Figure 1: Two day old chick embryo, starting segmentation, in vitro 62 Biomedical Engineering 53. Quantification of air flows produced by medical equipment disturbing the clean air in the field of surgery using large field background subtraction imaging Rudolf Verdaasdonk1, Niek van Asperen1, Albert vd Veen1, Keith Cover1, John Klaessens1, Peter Vandertop2 1 2 Department of Physics and Medical Technology, VU University Medical Center Department of Neurosurgery, VU University Medical Center Introduction Medical equipment is usually cooled by an internal air fans exiting the chassis on the side or the rear. These air exhausts can induce a major disturbance of the laminar flow of clean air in the operating room (OR) specially created above the field of surgery to prevent contaminations. Methods A special large field air flow visualization technique has been developed to study and quantify the air flow around equipment used in the OR that might potentially disturb the laminar flow in the operating field. By digital subtraction of the fine line pattern in the background of the field of interest, optical distortions induced by small density gradients in flowing air can be visualized with high contrast and sensitivity. Short bursts of air contrast were induced at the exhaust frame of medical equipment and followed in time. Specially developed analysis software calculated speed and direction of the air flow. Results Measurements revealed that the exhaust of cooling air of critical equipment like an operating microscope and surgical navigation system were blowing air at high speed into the clean laminar field. Also devices warming the patient with hot air can blow into the ‘clean’ field of surgery. Conclusions Large field background Schlieren digital subtraction imaging shows to be a sensitive and quantitative technique to study air flows. The awareness of the disturbance of the clean laminar air flow should lead to guidelines to improve the design and positioning of medical equipment in the OR to reduce infections. VU University Medical Center Science Exchange Day 2014 63 Biomedical Engineering 54. Parallel scanning laser ophthalmoscope (PSLO) for retinal imaging Kari V. Vienola1,2, Mathivanan Damodaran1,2, Boy Braaf1,2, Mattijs de Groot1,2, Koenraad Vermeer2, Johannes F. de Boer1,2 1 2 LaserLaB, Department of Physics and Astronomy, VU University Rotterdams Oogheelkundig Instituut Introduction High-speed imaging of the retina is crucial for obtaining high quality images in the presence of eye motion. To improve the speed of traditional scanners, a high-speed ophthalmic device is presented using a digital micro-mirror device (DMD) for confocal imaging with multiple simultaneous spots. Methods An experimental ophthalmic imaging system was constructed based on an 850 nm LED and a DMD containing 1024x768 micro-mirrors. Single mirror elements are sparsely turned ON to create multiple spots over the whole field of view. The DMD is programmed to project series of shifted point pattern configurations, effectively scanning the spots over the sample surface. The backscattered light from the retina is tapped off via a beam-splitter and imaged onto a CMOS camera. A confocal image is constructed by applying an image mask of virtual pinholes to each recorded frame. A wide-field confocal image is then created by combining all frames in a single image. Results In the figure a dollar note was imaged with all mirrors ON (widefield) and with multiple spots configuration (every 100th mirror ON). In widefield mode light is detected from different planes above and below the focal plane. When using multiple spots and virtual pinholes, only light from the focal plane is detected. The image on the right shows clearly the microstructure of the bank note. Conclusions It is possible to create confocal images with the PSLO system. In theory the DMD can achieve higher frame rates than traditional scanner-based systems (> 2 kHz) by illuminating the sample with multiple spots. 64 Biomedical Engineering 55. AFM nanoindentation reveals mechanical properties of extracellular vesicles from Red Blood Cells Daan Vorselen1,2, Jack J.W.A. van Loon2,3, Wouter H. Roos1, Gijs J.L. Wuite1 Department of Physics and Astronomy and LaserLab Amsterdam, VU University, Amsterdam 2 Department of Oral Cell Biology, Academic Centre for Dentistry Amsterdam (ACTA), University of Amsterdam and VU University, Amsterdam 3 Department of Oral and Maxillofacial Surgery/Oral Pathology, VU University Medical Center, Amsterdam 1 Introduction Extracellular vesicles (EVs) are endogenous particles involved in cell to cell communication. EVs transport proteins and RNA, appear to play a role in disease and are interesting as a potential drug delivery system. From proteomic studies it is known that many extracellular vesicles (EVs) contain cytoskeletal proteins. These proteins could give rise to unique structural and mechanical properties of EVs, and thereby affect interaction with target cells. Methods RBC EVs were isolated from RBCs from donors by stimulating with Ca2+ ionophore and subsequent differential centrifugation. We studied the mechanics of RBC EVs by performing nanoindentations using AFM (atomic force microscopy). Results Liposomes with a similar lipid composition as RBC EVs show behavior which corresponds to an elastic shell with an empty core. RBC EVs however behave more like an elastic shell with a filled core, characterized by a Hertzian force response (~ 1 MPa). Furthermore, indentation of these vesicles can show multiple types of breaks. They show large break events corresponding to ripping of the membrane or a collapse of the interior and small reversible break events that correspond to different structural states of the vesicle. We show that the interior of RBC EVs is dense (using CryoEM) and contains spectrin, which may explain how the interior influences the mechanics. Conclusions These observations suggest a contribution of a structured interior of the vesicle to the mechanical properties. Our results show that extracellular vesicles differ mechanically from liposomes and inspire further experiments with artificial vesicles to investigate the role of the vesicle mechanics in the interaction with the target cell. VU University Medical Center Science Exchange Day 2014 65 Clinical and Epidemiological surveys 56. A way out of depression in the visually impaired: results from a path-analysis RMA van Nispen1, H.P.A. van der Aa1, H.L .Vreeken1, D.L. Knol², C. Roeygens³, H.C. Comijs4, GHMB van Rens1 Department of Ophthalmology, VU University Medical Center ² Department of Epidemiology and Biostatistics, VU University Medical Center ³ Rehabilitation centre ‘Blindenzorg Licht en Liefde’ 4 Department of Psychiatry VUmc/GGZinGeest 1 Introduction Depression is negatively associated with low vision rehabilitation (LVR) outcomes; insight into associated factors is essential to treat depression. The objective was to investigate the prevalence, severity and associated factors of depression in visually impaired older adults. Method In a cross-sectional study, LVR outpatients (50+) from Belgium and the Netherlands were invited to participate in structured face-to-face interviews at home (N=384). Independent variables (sociodemographics, health indicators), mediating variables (coping, adaptation to vision loss (AVL), activities of daily living (ADL), mobility, reading), and the outcome (CES-D depression screener and CIDI diagnostic interview) were assessed. A path-analyses was performed (Mplus) to investigate the associated factors of depression. Results Prevalence of depression was 28% (CES-D>=16); the half-year incidence of major depression was 6.1%. Gender, youth trauma and life-time depression were independently associated with depressive symptoms as were the mediators coping, AVL and ADL. The association genderdepression was also mediated by coping, AVL and ADL. Conclusions The prevalence of depression among visually impaired elderly is high, comparable with international studies, but remains unrecognised. Outpatient occupational therapy and social work targeted at ADL, adaptation and coping problems may positively influence depression outcomes. A promising outpatient stepped-care program under study may directly impact on depression. 66 Clinical and Epidemiological surveys 57. Preoperative anemia alters the probability of packed red blood cell transfusion in patients undergoing vascular surgery David Burtman1,2, Christine F. Vermeulen1, Jan D. Blankensteijn1, Christa Boer2 1 Vascular Surgery, Institute for Cardiovascular Research, VU University Medical Center Anesthesiology, Institute for Cardiovascular Research, VU University Medical Center 2 Introduction Perioperative packed red blood cell (PRBC) transfusion is independently associated with postoperative morbidity and mortality. In this study, we investigated whether preoperative anemia increases the probability of perioperative PRBC transfusion in patients undergoing elective vascular surgery. Methods This retrospective study included 1630 patients who underwent elective vascular surgery between 2004 and 2013. Study parameters included perioperative hemoglobin levels, gender, duration of surgery, and PRBC transfusions. Severe anemia was defined as a hemoglobin <6.2 mmol/L, and mild anemia was defined as a hemoglobin ≥6.2 and <8 mmol/l (males) or ≥6.2 and <7.4 mmol/l (females). Results The lowest preoperative hemoglobin levels for males and females were 7.9 ± 1.5 and 7.4 ± 1.4 mmol/L, respectively. The prevalence of mild and severe preoperative anemia was 29.8% and 6.3% in the total study population. Multinomial regression to reveal predictors for PRBC transfusion included the level of preoperative anemia, duration of surgery and gender. Multinomial regression analysis for PRBC transfusion showed that a short duration of surgery (< 3 hours) reduced the probability of transfusion with an odds ratio of 0.06 (95% CI 0.04-0.09; P<0.001), while severe and mild anemia increased the probability of PRBC administration by 10.1 (6.2-16.5; P<0.001) and 2.6 (1.9-3.5; P<0.001). Gender was not of influence on PRBC transfusion. Conclusions Preoperative anemia is a common problem in patients undergoing vascular surgery and increases the probability for perioperative blood transfusion. Therefore, it may be useful to normalize hemoglobin levels preoperatively in order to reduce postoperative morbidity and mortality. VU University Medical Center Science Exchange Day 2014 67 Clinical and Epidemiological surveys 58. The role of perceived barriers in explaining socioeconomic differences in adherence to the fruit, vegetables and fish guidelines in older Dutch adults S.C. Dijkstra1, J.E. Neter1, M.M. van Stralen1, I.A. Brouwer1, M. Huisman2,3,4, M. Visser1, 2 ¹ Department of Health Sciences and the EMGO Institute for Health and Care Research, Faculty of Earth and Life Sciences, VU University Amsterdam 2 Department of Epidemiology and Biostatistics and the EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam 3 Department of Sociology, VU University Amsterdam 4 Department of Psychiatry, VU University Medical Center, Amsterdam Introduction People with low socioeconomic status (SES) have less healthy diets. In order to reduce differences in diet between SES groups information is needed about why low SES groups eat less healthy. In this study we identified barriers for meeting the fruit, vegetable and fish guidelines and investigated SES differences in older adults. Additionally, we examined to what extent these barriers explained why lower SES groups adhere to the dietary guidelines less often. Methods Analyses were performed in 1,057 older adults, aged 55-85 years, participating in the Longitudinal Aging Study Amsterdam. Indicators of SES were level of income and education. Respondents were asked to indicate the two most important barriers they experienced for meeting the fruit, vegetable and the fish guideline. We used a short food frequency questionnaire to assess fruit, vegetable and fish intake. Results Lower SES groups were more likely to perceive barriers to meet the guidelines, in particular that fruit, vegetables and fish were expensive. The association between income and adherence to the fruit guideline was mediated by “perceiving any barrier to meet the fruit guideline”. The association between income and adherence to the fish guideline was mediated by “perceiving any barrier to meet the fish guideline” and the barrier “fish is expensive”. Conclusions Perceived barriers for meeting the dietary guidelines are common in older adults, especially in lower SES groups. These barriers and particularly cost concerns partly explained the lower adherence to the guidelines for fruit and fish in lower income groups in older adults. 68 Clinical and Epidemiological surveys 59. Longitudinal data analysis with auxiliary item information to handle missing questionnaire data Iris Eekhout1, Craig Enders2, Jos W.R. Twisk3, Michiel R. de Boer4, Henrica C.W. de Vet5, Martijn W. Heymans6 Department Epidemiology and Biostatistics, VU University Medical Center, Amsterdam Department of Psychology, Arizona State University, United States 3 Department Epidemiology and Biostatistics, VU University Medical Center, Amsterdam 4 Department Methodology and Applied Biostatistics, Faculty of Earth and Life Sciences, Institute for Health and care Research, Amsterdam 5 Department Epidemiology and Biostatistics, VU University Medical Center, Amsterdam 6 Department Epidemiology and Biostatistics, VU University Medical Center, Amsterdam 1 2 Introduction Previous studies show that missing values in multi-item questionnaires can best be handled at the item score level. The aim of this study is to investigate a novel method for dealing with incomplete item scores in longitudinal questionnaire data. This novel method incorporates item information at the background when simultaneously the study results are estimated. Methods The investigated method includes the item scores or some summary of a parcel of item scores as helping variables, while using the total score of the multi-item questionnaire as the main focus of the analysis. That way the item scores help estimating the incomplete information of the total scores. The performance of these methods was examined in several simulated longitudinal data conditions and analyzed through bias in regression coefficient estimates and related standard errors. Furthermore, the methods are demonstrated in a clinical patient dataset. Results Results show that including the item information results in more precise estimates of study results in terms of regression coefficient estimates and standard errors, compared to not including the item information in the analysis. Conclusions The inclusion of a parcel summary is an efficient method that does not over-complicate model estimations and is therefore recommended in situations when questionnaire scale scores are incomplete due to missing item scores in clinical studies. VU University Medical Center Science Exchange Day 2014 69 Clinical and Epidemiological surveys 60. Body-image in gender dysphoria; concepts of selfperception & physical appearance revisited for different subtypes T.C. van de Grift, MD, MSc1,2, P.T. Cohen-Kettenis, PhD1,3, T.D. Steensma, PhD1, R.E. Dikmans, MD2, G. De Cuypere, MD, PhD3, H. Richter-Appelt, PhD3, I.R. Haraldsen, MD, PhD3 & B.P.C. Kreukels, PhD1,3 Department of Medical Psychology, VU University Medical Center, Amsterdam Department of Plastic, Reconstructive & Hand Surgery, VU University Medical Center, Amsterdam; 3 European Network for the Investigation of Gender Incongruence (ENIGI; Amsterdam, Ghent, Hamburg & Oslo) 1 2 Introduction Body-image (BI) and physical appearance (PhA) are key influencers of gender dysphoria (GD). This study aims to use the two concepts to provide a framework in understanding GD and its specifiers (biological sex, sexual preference and onset age (OA)). Methods Data collection was part of the European Initiative for the Investigation of Gender Incongruence. Between 2007 and 2012, 660 individuals with GD (1.31:1 male-female ratio) were included in the study. Sexual preference and OA were obtained during psychological diagnostics. Body satisfaction was measured through the Body Image Scale, and physical compatibility with the desired gender was measured using the clinician-reported PhA scale. Results The majority of male-to-females (MtFs) reported ‘non-homosexual’ sexual orientation. Most female-to-males (FtMs) reported ‘homosexual’ sexual orientation and had early onset (EO) GD. FtMs have an appearance which is more compatible with the experienced gender and a more positive BI than MtFs. Besides genital dissatisfaction, problem areas for MtFs include body movement, head & neck, and hair, whereas FtMs are mainly dissatisfied with hip and chest regions. Within the MtFs, those with EO GD and a homosexual sexual orientation have more compatible appearances with regard to their gender identity. Conclusions FtMs, and EO & homosexual MtFs have more favorable PhA and BI, although both groups have their areas of concern. Body-image problems in GD go further than solely genital dysphoria and therefore deserve attention in psychological support. 70 Clinical and Epidemiological surveys 61. New insights into the spectrum of genotypes and phenotypes in Hypomyelination with Atrophy of the Basal Ganglia and Cerebellum (H-ABC) Eline M.C. Hamilton, Emiel Polder, Carola G.M. van Berkel, Truus E.M. Abbink, Nicole I. Wolf, Marjo S. van der Knaap Department of Child Neurology, VU University Medical Center and Neuroscience Campus Amsterdam, Amsterdam Introduction Hypomyelination with Atrophy of the Basal Ganglia and Cerebellum (H-ABC) is a rare leukodystrophy that was identified by MRI pattern analysis. Exome sequencing in 11 H-ABC patients recently revealed the same de novo mutation in the TUBB4A gene, which encodes β-tubulin. A mutation in this gene is also associated with adult onset dystonia type 4, in which the brain MRI is normal. We here describe the mutation spectrum, phenotype and MRI characteristics in a cohort of 42 H-ABC patients. Methods We initiated a cross-sectional observational study in our database of H-ABC patients, which involved DNA analysis, evaluation of sequential MRIs and clinical inventory. Results The TUBB4A mutation observed in the first 11 H-ABC patients was by far the most common. Additionally, 13 other mutations were identified, located at different structural domains within β-tubulin. The clinical features were rather homogeneous, but the severity ranged from patients with a normal early development followed by slow neurological deterioration, to patients who acquired no intentional movements. MRI showed lack of myelin, disappearance of the putamen, variable cerebellar atrophy and highly variable cerebral atrophy. We also found pathogenic TUBB4A mutations in some patients with less typical MRI abnormalities. Patients with the common mutation had the mildest disease. Conclusions The work here demonstrates that the distinctive H-ABC MRI pattern defines a largely homogeneous clinical phenotype of variable severity. The results are strongly suggestive of a genotypephenotype correlation. It is likely that there is a disease continuum associated with TUBB4A mutations, in which extrapyramidal movement abnormalities constitute the core feature. VU University Medical Center Science Exchange Day 2014 71 Clinical and Epidemiological surveys 62. Functional Gene-Set Analysis of Attention Deficit/ Hyperactivity Disorder (ADHD) Anke R. Hammerschlag1,2, Christiaan de Leeuw1,3, Andrea Goudriaan4, Tinca J.C. Polderman1, Matthijs Verhage5,6, August B. Smit4, Henning W. Tiemeier7,8, Mark H.G. Verheijen4, Danielle Posthuma1,6,7 Complex Trait Genetics, Department of Functional Genomics, Neuroscience Campus Amsterdam, VU University Amsterdam 2 The Generation R Study Group, Erasmus MC Rotterdam 3 Institute for Computing and Information Sciences, Radboud University 4 Department of Molecular and Cellular Neurobiology, Neuroscience Campus Amsterdam, VU University Amsterdam 5 Department of Functional Genomics, Neuroscience Campus Amsterdam, VU University Amsterdam 6 Department of Clinical Genetics, VU University Medical Center 7 Department of Child and Adolescent Psychiatry, Erasmus MC Rotterdam 8 Department of Epidemiology, Erasmus MC Rotterdam 1 Introduction Attention Deficit/Hyperactivity Disorder (ADHD) is a neurobehavioral developmental disorder affecting about 3-7% of children worldwide. Despite the high heritability of ADHD (~75%), genome-wide association studies (GWAS) failed to find significant genetic associations. The aim of our study is to detect functional gene sets that might be important to the risk of ADHD. Using gene-set analysis, the combined effect of genetic variants is tested, resulting in more statistical power. Moreover, testing genes with similar cellular function provides immediate functional meaning which may lead to more biological insight into the etiology of ADHD. Methods 2,787 ADHD cases and 2,635 controls were included in the analysis. Synaptic, glial and lipid gene sets have been manually curated by experts of the Center for Neurogenomics and Cognitive Research (CNCR), and were based on cellular function. Gene-set analysis was conducted with JAG software (http://ctglab.nl/software/jag), including self-contained tests and competitive tests. Results Four lipid gene sets showed significant associations with ADHD. However, the four groups included the UGT1A gene family, consisting of nine genes physically overlapping in the genome. After correction for this gene family, the associations of the lipid groups were no longer significant. Conclusions No statistically significant associations between gene sets and ADHD were revealed. Future plan is to increase statistical power by conducting functional gene-set analysis in a larger sample of 12,600 ADHD cases and 83,600 controls. 72 Clinical and Epidemiological surveys 63. Mental rotation in women with Complete Androgen Insensitivity Syndrome: an fMRI study J. van Hemmen1,2, D.J. Veltman3, A. Dessens4, P.T. Cohen-Kettenis2, J. Bakker1,5 Neuroendocrinology Group, The Netherlands Institute for Neuroscience, Amsterdam Department of Medical Psychology, VU University Medical Center, Amsterdam 3 Department of Psychiatry, VU University Medical Center, Amsterdam 4 ErasmusMC-Sophia, Dept. of Pediatrics, Div. of Pediatric Endocrinology, Rotterdam 5 Interdisciplinary Applied Genoproteomic Group - Neurosciences, University of Luik, Luik, Belgium 1 2 Introduction The exact mechanisms involved in the sexual differentiation of the human brain are still being debated. The mental rotation (MR) task is a visuospatial task, eliciting sex differences in performance as well as in neural activation patterns. We compared individuals with Complete Androgen Insensitivity Syndrome (CAIS), who have XY chromosomes, but a female phenotype due to non-functional androgen receptors, to control men and women in order to investigate the role of sex hormones and sex chromosomes on the sexually differentiated neural activation patterns during MR. Methods In this study, 20 women with CAIS, 29 control men and 30 control women performed a 3D MR task during fMRI acquisitions. Between-group comparisons were performed regarding the neural activation patterns during MR in four MR related regions of interest. Results Between-group comparisons showed that men had higher levels of neural activation than women with CAIS and control women in the left inferior parietal cortex, and than women with CAIS in the left superior parietal cortex. Conclusions Women with CAIS showed a female-typical neural activation pattern during MR. These results indicate that the sexual differentiation of visuospatial neural activation patterns is not influenced by sex chromosomal composition, but is more likely to be prone to androgenic factors. Future studies using this unique model are likely to provide further understanding of the influence of sex hormones and sex chromosomes on other sexually-differentiated cognitive functions and neural properties. VU University Medical Center Science Exchange Day 2014 73 Clinical and Epidemiological surveys 64. Latent class growth (mixture) models: How do we handle predictors of class membership? Trynke Hoekstra1,2, Jos Twisk1,2 1 VU University Medical Center, Department of Epidemiology and Biostatistics VU University, Department of Health Sciences and the EMGO Institute for Health and Care Research 2 Introduction Common longitudinal models such as multilevel models or Generalised Estimating Equations can only to some extent handle individual variability in development; they do not allow for the revelation of subgroups of individuals with distinct developmental trajectories. To identify such trajectories, a range of techniques are available, of which latent class growth (mixture) models (LCGM) are probably the most flexible. The aim of LCGM is to (statistically) identify the number and characteristics of distinct subgroups (classes). This poster will focus on methodological challenges concerning particularly the incorporation of predictors of these classes. Methods We will explain a commonly used one-step approach, a relatively conservative two-step approach and a novel three-step approach currently available using data of the Amsterdam Growth and Health Study (www.aggo.nl). In the conservative two-step approach, individuals are first assigned to their most-likely class, providing a categorical variable denoting class membership. This variable can then be analyzed in a subsequent step using common regression techniques or ANOVA. This approach ignores possible uncertainty in class assignment, which is overcome by the one-step approach, where predictors are already included while forming the classes. However, these variables then influence the class formation process, hereby clouding the interpretation of them. This issue is overcome by the new three-step approach. Results Detailed results will be provided; the three approaches provided fairly similar results. Conclusions Slight differences between the three approaches were observed. Because of the lack of methodological studies available on this topic, researchers are advised to carefully choose which approach to take. 74 Clinical and Epidemiological surveys 65. Psychological posttraumatic growth in head and neck cancer survivors C. J. M. Holtmaat1, C. F. van Uden-Kraan1,2, N. van der Spek1, C. R. Leemans2, I. M. Verdonck-de Leeuw1,2 1 2 Department of Clinical Psychology, VU University Department of Otolaryngology/Head and Neck Surgery, VU University Medical Center Introduction While the adverse effects of head and neck cancer (HNC) on quality of life are well demonstrated, information on psychological posttraumatic growth (PTG) of HNC survivors is scarce. The aim of this study is to investigate PTG among HNC survivors and the association with demographic factors, psychological distress and quality of life. Methods A cohort of 113 HNC survivors who received treatment with curative intent at the VU University Medical Center were asked to complete the Posttraumatic Growth Inventory (PTGI), the Hospital Anxiety and Depression Scale (HADS), the EORTC Quality of Life Questionnaire (EORTC QLQ-C30) and questions on demographics. To assess gender and educational level differences in PTG an independent samples t-test and an ANOVA were used. Pearson correlations were used to investigate the association of age, depression, anxiety and quality of life with PTG. Results In total 87 HNC survivors (35.6% female, mean age 57.7) returned the questionnaires (response rate 77.0%). Fifty-five percent (55.1%) reported no or small and 44.9% reported moderate to high levels of PTG. The level of PTG did not differ between males and females or between people with different educational levels. There were no significant correlations between PTG and age, depression, anxiety and quality of life. Conclusion Almost half of the HNC survivors reported PTG, which was not associated with demographics, distress or quality of life. Further research on other factors that may influence PTG in HNC survivors, such as personality and coping style, is warranted. VU University Medical Center Science Exchange Day 2014 75 Clinical and Epidemiological surveys 66. Efficacy and safety of intrauterine insemination in patients with moderate to severe endometrisis Lisette van der Houwen1, Anneke Schreurs1, Roel Schats1, Cornelis Lambalk1, Peter Hompes1, Velja Mijatovic1 1 Endometriosis Center, Division of Reproductive Medicine, Department of Obstetrics and Gynaecology, VU University Medical Center Introduction This study was performed to evaluate the efficacy and safety of two different IUI treatment strategies and the additional effect of long term pituitary down-regulation in moderate to severe endometriosis. Methods A retrospective analysis was established including all patients with moderate to severe endometriosis, who started IUI between January 2007 and July 2012. A maximum of six cycles were included. Two treatment strategies were compared; IUI with controlled ovarian hyperstimulation (COH) (n=20, 61 cycles, IUI+COH) versus IUI without COH in the first three cycles followed by IUI with COH (n=45, 184 cycles, IUI+natural/COH). The additional effect of preceding long term pituitary downregulation was investigated. Results Eight (40.0%) and 7 (15.6%) ongoing pregnancies were accomplished in patients undergoing IUI+COH and IUI+natural/COH, respectively (p=0.05). Cox regression showed a HR of 3.2 (95%CI1.1-8.5, p=0.02), reflecting a significantly higher chance on ongoing pregnancy in patients receiving IUI+COH. Preceding long term pituitary down-regulation tended to result in a higher ongoing pregnancy rate (adjusted HR 1.8, 95%CI0.6-5.1, p=0.26). Eight (40.0%) versus 16 (35.6%) recurrences of endometriosis were reported in patients undergoing IUI+COH versus IUI+natural/ COH, respectively (p=0.73). Preceding long term pituitary down-regulation tended to result in a higher chance on endometriosis recurrence (adjusted HR 2.3, 95%CI0.98-5.3, p=0.06). Conclusions IUI with COH could be a valuable treatment in moderate to severe endometriosis. Preceding long term pituitary down-regulation might positively influence the ongoing pregnancy rate and can be considered. Whether this treatment strategy can be structurally offered prior to IVF must be investigated in a randomized controlled trial. 76 Clinical and Epidemiological surveys 67. The dopaminergic reward system and leisure time exercise behavior: A candidate allele study Charlotte Huppertz1,2, Meike Bartels1,2,3, Maria M. Groen-Blokhuis1, Conor V. Dolan1, Marleen H.M. de Moor1, Abdel Abdellaoui1,3, Catharina E.M. van Beijsterveldt 1, Erik A. Ehli4, Jouke-Jan Hottenga1, Gonneke Willemsen1,2, Xiangjun Xiao5, Paul Scheet6, Gareth E. Davies4, Dorret I. Boomsma1,2,3, James J. Hudziak7, Eco J.C. de Geus1,2,3 Department of Biological Psychology, VU University Amsterdam, The Netherlands EMGO+ Institute for Health and Care Research, VU University Medical Center 3 Neuroscience Campus Amsterdam, VU University Medical Center 4 Avera Institute for Human Genetics, Avera McKennan Hospital and University Health Center, South Dakota, USA 5 Department of Community and Family Medicine, Geisel School of Medicine, Dartmouth College, New Hampshire, USA 6 Department of Epidemiology, University of Texas M.D., Anderson Cancer Center, Department of Epidemiology, Texas, USA 7 Department of Psychiatry, Medicine, and Pediatrics, Vermont Center for Children, Youth and Families, College of Medicine, University of Vermont, Vermont, USA 1 2 Introduction Twin studies provide evidence that genetic influences contribute strongly to individual differences in exercise behavior. We hypothesize that part of this heritability is explained by genetic variation in the dopaminergic reward system. Eight single nucleotide polymorphisms (SNPs: rs265981, rs6275, rs1800497, rs6280, rs1800955, rs1611115, rs2519152, rs4680) and three variable number of tandem repeats (VNTRs in DRD4, upstream of DRD5, and in DAT1) were investigated for a potential association with regular leisure time exercise behavior. Methods Data on exercise activities and at least one SNP/VNTR were available for 8,768 individuals aged 7 to 50 years old that were part of the Nederlands Twin Register. Exercise behavior was quantified as weekly metabolic equivalents of task (MET) spent on exercise activities. Mixed models were fitted in SPSS with latent genetic factors as random effects. Results None of the SNPs/VNTRs were associated with exercise behavior (p> .02), despite sufficient power to detect even small effects. Conclusions We did not confirm that allelic variants involved in dopaminergic function play a role in creating individual differences in exercise behavior. Possible reasons for this will be discussed, including the fact that exercise behavior is a complex phenotype that is difficult to define and measure, and that it is probably influenced by many genetic variants with very small effects. A plea is made for large genome-wide association studies to unravel the genetic pathways that affect exercise behavior in order to help personalize the strategies to increase this health-enhancing activity. VU University Medical Center Science Exchange Day 2014 77 Clinical and Epidemiological surveys 68. Prevalence and comorbidity of pain symptoms in the general population L. Ligthart1,2, C.M. Visscher3, C.M.H.H. van Houtem4, A. de Jongh4,5 & D.I. Boomsma1,2 Department of Biological Psychology, VU University Amsterdam EMGO+ Institute for Health and Care Research 3 Department of Oral Kinesiology, Academic Centre for Dentistry Amsterdam, University of Amsterdam and VU University Amsterdam, MOVE Research Institute Amsterdam 4 Department of Social Dentistry and Behavioural Sciences, Academic Centre for Dentistry Amsterdam, University of Amsterdam and VU University, Amsterdam, The Netherlands 5 School of Health Sciences, Salford University, Manchester, United Kingdom 1 2 Introduction The prevalence of individual pain disorders has often been studied, but few studies investigate many different pain types at once. We aimed to investigate how different pain types relate to each other and to comorbid traits, especially anxiety and depression, in the general population. Methods We analyzed data from a large population-based cohort of Dutch twin families (11.530 subjects). Pain was assessed in eight body sites: back, neck, head, abdomen, joints, chest, teeth and face. The Graded Chronic Pain Scale (von Korff, 1993) was used to assess the pain intensity and disability. Anxious depression was measured with a subscale of the Adult Self Report (Achenbach, 1997). Results All pain types except chest pain and toothache were more common in women than in men. Women were also more likely to report chronic pain. The prevalence of most pain types was relatively similar across age, except for headache and abdominal pain, which decreased, and joint pain, which strongly increased with age (with 4% and 17% chronic joint pain in the youngest and oldest age groups, respectively). Strong and consistent comorbidity was observed: having any type of pain was associated with an increased risk of any other type of pain (correlations between 0.1 and 0.7), as well as anxious depression. Conclusions Chronic pain is very common in the adult Dutch population (21%). We observed strong comorbidity of different pain symptoms and anxious depression. Given the severe disability caused by these conditions, research into the causes of this comorbidity is warranted. 78 Clinical and Epidemiological surveys 69. Cortical Thickness and Inattention/Hyperactivity Symptoms in Young Children- The Generation R Study Sabine E. Mous1,2, Ryan L. Muetzel1,2, Hanan El Marroun1,2, Tinca J.C. Polderman3, Aad van der Lugt4, Vincent W. Jaddoe1,5, Albert Hofman5, Frank C. Verhulst2, Henning Tiemeier2,5, Danielle Posthuma2,6,7, Tonya White2,4 The Generation R Study Group, Erasmus MC Dep of Child and Adolescent Psychiatry/Psychology, Erasmus MC–Sophia 3 Center for Neurogenomics and Cognitive Research (CNCR), Neuroscience Campus Amsterdam (NCA), VU University 4 Department of Radiology, Erasmus MC 5 Department of Epidemiology, Erasmus MC 6 Center for Neurogenomics and Cognitive Research, VU University 7 Department of Clinical Genetics, section Medical Genomics, VU MC 1 2 Introduction While many neuroimaging studies have investigated the neurobiological basis of Attention-Deficit/ Hyperactivity Disorder (ADHD), few have studied the neurobiology of attention problems in the general population. However, the ability to pay attention falls along a continuum within the population, with children with ADHD at one extreme of the spectrum. Therefore, a dimensional perspective of evaluating attention problems has an added value to the existing literature. Methods This study is embedded within the Generation R Study and includes 444 six-to-eight year-old children with parent-reported attention and hyperactivity measures and high-resolution structural brain imaging data. We investigated the relationship between cortical thickness across the entire brain and Child Behavior Checklist (CBCL) attention scores. Results We found that greater attention problems were associated with a thinner right and left postcentral gyrus. When correcting for potential confounding factors and multiple testing, these associations remained significant. Conclusions In a large, population-based sample we showed that young children who show more attention problems and hyperactivity have a thinner cortex in the region of the right and left postcentral gyrus. The postcentral gyrus, being the primary somatosensory cortex, reaches its peak growth early in development. Therefore, the thinner cortex in this region may reflect either a deviation in cortical maturation or a failure to reach the same peak cortical thickness compared to children without attention or hyperactivity problems. VU University Medical Center Science Exchange Day 2014 79 Clinical and Epidemiological surveys 70. Dietary intake of Dutch food bank recipients Judith E. Neter1, S. Coosje Dijkstra1, Marjolein Visser1,2, Ingeborg A. Brouwer1 Department of Health Sciences and the EMGO Institute for Health and Care Research, Faculty of Earth and Life Sciences, VU University Amsterdam 2 Department of Epidemiology and Biostatistics, VU University Medical Center 1 Introduction Recipients of the food bank are a very specific group of people with low socioeconomic status, who are limited in their food choices due to their dependency on food parcels. A healthy diet can contribute to the prevention of nutrition-related chronic diseases. Therefore, this study aims to determine the dietary intake of Dutch food bank recipients. Methods In this cross-sectional study (Food Bank study) we obtained information on socio-demographic characteristics by means of a general questionnaire and food intake by means of three 24-hour recalls per participant. Data were collected of 177 food bank recipients from 13 different food banks throughout the Netherlands. Habitual nutrient, fruit and vegetable intake were analyzed with SPADE. Results Preliminary analyses of 167 participants showed that the habitual energy intake (1947.1 kcal) is lower compared with the dietary recommendations. The habitual intakes of carbohydrate (47.3 en%), total fat (36.1 en%) polyunsaturated fatty acids (6.7 en%) and trans fatty acids (0.6 en%) were according the dietary recommendations, while the habitual protein (15.2 en%) and saturated fat (13.3 en%) were higher than recommended. Furthermore, the habitual fiber (16 g), fruit (78.5 g) and vegetable (128.9 g) intakes were lower than recommended. Conclusions Many food bank recipients do not meet the dietary guidelines for a healthy diet. Only 5% and 15% of the participants met the dietary recommendation for fruit and vegetables, respectively. Interventions are needed to decrease protein and saturated fat intake and increase the fiber, fruit and vegetable intake of Dutch food bank recipients. 80 Clinical and Epidemiological surveys 71. Palliative care case management in primary care: A descriptive study about the flexibility, duration and content of care Annicka van der Plas1,2, Anneke Francke1,2,3, Wim Jansen2,4, Kris Vissers5, Luc Deliens1,2,6, Bregje Onwuteaka-Philipsen1,2 VU University Medical Center, Department of Public and Occupational Health, EMGO+ Institute for Health and Care Research, Amsterdam 2 Center of Expertise in Palliative Care VU University medical center 3 Nivel Netherlands Institute for Health Services Research, Utrecht 4 VU University Medical Center, Department of Anaesthesiology, Amsterdam. 5 Radboud University Nijmegen Medical Center, Department of Anaesthesiology, Pain, and Palliative Medicine, Nijmegen, the Netherlands. 6 Ghent University and Vrije Universiteit Brussel, End-of-Life Care Research Group, Brussels, Belgium 1 Introduction In case management an individual or small team is responsible for navigating the patient through complex care. In palliative care case management flexibility of care, duration of care for as long as needed, and attention to physical, psychological, social, and spiritual wellbeing are considered central points. The objective of this study is to describe the number, duration and content of contacts the case manager has with patients and/or informal carers, and the time span between first and last contact. Methods Case managers of 12 palliative care case management initiatives completed a questionnaire for every contact they had with a patient and/or informal carer. Results For 738 included patients, there were 4278 recorded contacts between the case manager and the patient and/or informal carer. The median number of contacts was 4, with a range from 1 to 36 contacts per patient. Home visits were done between zero to 22 times per patient, and lasted 48 minutes (median). Contacts by telephone occurred zero to 19 times per patient and lasted 30 minutes (median). The time between the first and last contact ranged from zero days up to two years. Topics most discussed during contacts were physical complaints, psychological issues, life expectancy and incurability of illness. Information on care services and illness was mostly given. Conclusions Case management in primary care is delivered flexible with regard to the number and duration of contacts. Time between the first and last contact was also variable. Content of care covered all domains of palliative care. VU University Medical Center Science Exchange Day 2014 81 Clinical and Epidemiological surveys 72. Determinants of Undernutrition in Older Adults receiving Home Care Rachel van der Pols-Vijlbrief1, Hanneke Wijnhoven1, Marjolein Visser1,2 Department of Health Sciences, EMGO+ Institute for Health and Care Research, VU University, Amsterdam 2 Department of Epidemiology and Biostatistics, EMGO+ Institute for Health and Care Research, VU University Medical Center, Amsterdam 1 Introduction Undernutrition is highly prevalent among older persons receiving home care, difficult to treat, and associated with negative health outcomes. The purpose of this study was to identify the most important, determinants of undernutrition in this vulnerable group. Methods In total, 308 older men and women living at home were screened by home care nurses for undernutrition with the SNAQ65+ screening tool and completed the developed questionnaire. Information on demographics, physical activity, nutritional intake, appetite, functional, cognitive and health status, depression, social network, oral health, sight and hearing difficulties and pain was asked. Multivariate backwards logistic regression analyses were used to identify the determinants of undernutrition. Results Of the participants, 39.3% was undernourished or ‘at risk’ and 60.7% was well nourished. Mean age was 81.6 years (SD: 7.7). The results suggest that being married (OR:0.393), a good appetite (OR:0.652), not needing help with grocery shopping (OR:0.463), and eating more snacks (OR:0.676) significantly lowers the risk for undernutrition. Furthermore, ADL independency (OR:1.130), not physically active (OR:1.860), higher number of falls (OR:2.874), intestinal problems (OR:2.397), and hospitalization (OR:1.288) significantly increased this risk. Conclusions Under nutrition is a multi-factorial problem with various determinants in different domains. A multidimensional prevention strategy should target the modifiable determinants; poor physical activity and appetite, support needed with groceries, low intake snacks, ADL and intestinal problems. 82 Clinical and Epidemiological surveys 73. Measurement properties of questionnaires assessing participation in children and adolescents with a disability: a systematic review JFM Rainey1, R.M.A .van Nispen1, C.H. van der Zee2, G.H.M.B. van Rens1 1 2 Department of Ophthalmology, VU University Medical Center Department of Epidemiology and Biostatistics, VU University Medical Center Introduction The aim of the present study is to critically appraise the measurement properties of questionnaires measuring participation in minors with a disability. Method Bibliographic databases were searched for studies evaluating the measurement properties of self-report or parent-report questionnaires measuring participation in children and adolescents (0-18 years) with a disability. The methodological quality of the included studies and the results of the measurement properties were evaluated using a checklist developed on consensus-based standards. Results The search strategy identified 3977 unique publications, of which 22 were selected; these articles evaluated the development and measurement properties of 8 different questionnaires. The Child and Adolescent Scale of Participation was evaluated most extensively, generally showing moderate positive results on content validity, internal consistency, reliability and construct validity. The remaining questionnaires also demonstrated positive results. However, at least 50% of the measurement properties per questionnaire were not (or only poorly) assessed. Conclusions Studies of high methodological quality, using modern statistical methods are needed to accurately assess the measurement properties of currently available questionnaires. Moreover, consensus is required on the definition of the construct ‘participation’ to determine content validity and to enable meaningful interpretation of outcomes. VU University Medical Center Science Exchange Day 2014 83 Clinical and Epidemiological surveys 74. Anxiety in Parkinson’s disease: mind = body? S. Rutten1-3, I. Ghielen1, C. Vriend1,2,4, H.W. Berendse4,5, J.H. Smit1,3, Y.D. van der Werf2,4,6, O.A. van den Heuvel1,2,4 Department of Psychiatry, VU University Medical Center (VUmc), Amsterdam Department of Anatomy & Neurosciences, VUmc, Amsterdam 3 EMGO Institute for Health and Care Research, VUmc, Amsterdam 4 Neuroscience Campus Amsterdam, VUmc, Amsterdam 5 Department of Neurology, VUmc, Amsterdam 6 Netherlands Institute for Neuroscience, Amsterdam 1 2 Introduction Although Parkinson’s disease (PD) is best known for its characteristic motor symptoms, the nonmotor symptoms, that occur in almost all PD patients, are believed to have an even greater impact on daily functioning and quality of life. This is especially true for anxiety, which is prevalent in almost half of PD patients. Anxiety is, however, often not recognised in clinical practice, and scientific literature on this subject is limited. The goal of this study was to reach a better understanding of anxiety in PD. Methods For this cross-sectional study, 294 patients with idiopathic PD were included. Symptoms of anxiety were measured with the Beck Anxiety Inventory (BAI). We dissected the BAI with principal component analysis. The interconnection of symptoms of anxiety with depression, autonomic and motor dysfunction was assessed through factor analysis and multiple regression analyses. Results Clinically relevant anxiety was present in 45% of patients. Factor analysis of the BAI resulted in one affective and four somatic subscales. Multiple regression analyses demonstrated that depressive symptoms contributed significantly to the outcome of all subscales of the BAI. The somatic subscales were partially explained by symptoms of motor dysfunction and autonomic failure. The score on the affective subscale was not influenced by these motor and autonomic symptoms. Conclusions Anxiety affects a large proportion of PD patients and comprises one affective and four somatic dimensions. There is overlap between symptoms of anxiety, autonomic failure and depression in patients with PD. The strong interplay between motor and non-motor symptoms in PD militate a holistic approach of PD in clinical practice. The affective subscale of the BAI is not influenced by the severity of motor or autonomic symptoms. This subscale might therefore be a more pure measure of anxiety in PD patients and prove useful for future research. 84 Clinical and Epidemiological surveys 75. The association between psychosocial stress and mortality is mediated by lifestyle and chronic diseases: the Hoorn Study Femke Rutters, PhD1,2, Stefan Pilz, PhD1,2,3, Anitra Koopman, Msc1,2, Simone P. Rauh, sc1,2, Saskia J. Te Velde, PhD1,2, Coen D. Stehouwer, MD, PhD4, Petra Elders, MD, PhD2,5, Giel Nijpels, MD, PhD2,5, Jacqueline M. Dekker, MD, PhD1,2 Department of Epidemiology and Biostatistics, VU University Medical Center, Amsterdam EMGO+ Institute for health and care research, VU University Medical Center, Amsterdam 3 Department of Internal Medicine, Division of Endocrinology and Metabolism, Medical University of Graz, Graz, Austria 4 Department of Internal Medicine and Cardiovascular Research Institute (CARIM), Maastricht University Medical Centre, Maastricht 5 Department of General Practice, VU University Medical Center, Amsterdam 1 2 Introduction Psychosocial stress is associated with chronic disease. Experiencing stressful life events may lead to premature mortality, by inducing behavioural, endocrine and metabolic changes. We evaluated whether in the general population the number of stressful life events is associated with mortality, and whether this relationship is mediated by behavioural changes and morbidities. Methods Design, setting, patients: The Hoorn study; a population-based cohort study among older men and women. Main outcome measure: Stressful life events experienced during the previous 5 years were assessed by questionnaire. We calculated Cox proportional hazard ratios (HRs) for all-cause and causespecific mortality during follow-up for those who experienced stressful life events compared to those who did not. Results We included 2385 participants (46% male; 62±7 years). During 20 years of follow-up 834 (35%) participants died, of whom 239 (28.6%) died of cardiovascular disease and 235 (28.2%) of cancer. Compared to the group with no stressful life events, the age, sex and socioeconomic status adjusted HRs (95% confidence intervals) for all-cause mortality compared to those who had 1 event, 2 events, 3 events and ≥ 4 events were 0.89 (0.72-1.09), 1.01 (0.81-1.24), 1.29 (1.00-1.66) and 1.44 (1.08-1.92), respectively. Similar results were observed for cardiovascular mortality and cancer mortality. Mediation analysis showed that smoking, physical inactivity, prevalent type 2 diabetes and cardiovascular disease were statistically significant mediators of the association between stressful life events and mortality. Conclusions Having 3 or more stressful life events is associated with a significantly increased risk for mortality in an elderly population-based cohort. This association is mediated by smoking, physical inactivity, type 2 diabetes and cardiovascular disease. VU University Medical Center Science Exchange Day 2014 85 Clinical and Epidemiological surveys 76. The quantity and quality of daily activities in relation with fall history and future falls in older adults Kimberley S. van Schooten1, Sietse M. Rispens1, Petra J.M. Elders2, Paul Lips3, Jaap H. van Dieën1 en Mirjam Pijnappels1 MOVE Research Institute Amsterdam, Faculty of Human Movement Sciences, VU University Amsterdam 2 EMGO+ Institute, VU University Medical Center 3 MOVE Research Institute Amsterdam, Department of Internal Medicine and Endocrinology, VU University Medical Center 1 Introduction Sedentary behavior and balance and gait impairments are important risk factors for falls in older adults. However, most studies investigated the relation with falls retrospectively, while this might be biased by fear of falling or recall. Moreover, subjective reports of physical activity are often used, while these are known to have limited validity and precision. In this study, we compared the associations between falls determined retrospectively and prospectively with potential risk factors as measured by accelerometry. Methods We measured 121 older adults with an average age of 75.5 (SD 7.1) years. Six-months fall incidence was retrospectively obtained by recall and prospectively by monthly telephone contact. In addition, all participants answered validated questionnaires assessing risk factors for falls and wore a 3D trunk accelerometer during one week. Based on the accelerometer data, five activities were classified: locomotion, sitting, standing, lying and an unclassified category. The total duration of these activities was calculated and for the locomotion bouts, variables describing gait quality were estimated. The associations of the questionnaires, duration of the activities and gait quality variables with retrospective and prospective falls were investigated using logistic regression. Results Participants were classified as fallers if they experienced one or more falls in 6 months; 34% of the participants had a history of falls and 38% experienced falls during follow-up. Depression, cognition, fear of falling, grip force, processing speed and executive function were significantly associated with retrospective falls, as well as the accelerometry-derived index of harmonicity (gait smoothness), strength of the signal’s dominant frequency (measure of gait variability), movement intensity and locomotion duration. Prospectively, none of the questionnaire results was significantly associated with falls. Accelerometry-derived walking speed, standard deviation and range of the signal (measures of intensity), harmonic ratio (gait symmetry), local dynamic stability, and the duration of unclassified activities were significantly associated with prospective falls. The best prediction model for future falls comprised local dynamic stability, the duration of the unclassified activities and fall history. Using these variables, 84.1% of the non-fallers and 55.8% of the fallers were correctly classified. Conclusions Our results show that variables associated with falls differ between retrospective or prospective analyses. Moreover, the employed questionnaires were not able to discriminate between future fallers and non-fallers, while the accelerometry-derived variables could. 86 Clinical and Epidemiological surveys 77. A twin-sibling study of components of adolescent physical fitness N.M. Schutte1,2, M. Bartels1,2, I. Nederend1,2, E.J.C. de Geus1,2 1 2 Department of Biological Psychology, VU University Amsterdam EMGO+ Institute for Health and Care Research, VU University Medical Center, Amsterdam Introduction Physical fitness can be defined as a set of components that determine exercise ability and performance in sports. Because exercise ability may be a major driver of voluntary exercise behavior it is important to understand the source of the substantial variation in the components of physical fitness seen already among adolescents. Most studies have focused on aerobic fitness but other components like strength, flexibility and balance also play an important role in exercise ability. The purpose of this study was to determine the causes of individual differences in isometric strength, explosive strength, upper body flexibility and motor balance in an adolescent sample. Methods Hand grip strength, explosive leg strength (vertical jump), flexibility (sit and reach) and balance were examined in 227 healthy monozygotic and dizygotic twin pairs and 38 of their singleton siblings (mean age 17.2 ± 1.2). Results Monozygotic twin correlations were consistently greater than dizygotic twin/twin-sibling/siblingsibling correlations for all components (hand grip 0.78 and 0.37 respectively, explosive leg strength 0.72 and 0.27, flexibility 0.83 and 0.33, balance 0.31 and 0.24), suggesting a moderate to high genetic contribution to the variation in these physical fitness components in this adolescent sample. Analysis of the cross-trait/cross-twin correlations indicated that there is a common set of genes influencing hand grip strength and explosive leg strength. Conclusions Individual differences in physical fitness components hand grip strength, explosive leg strength, flexibility and balance are for a substantial part due to genetic factors and there is genetic covariation between hand grip strength and explosive leg strength. VU University Medical Center Science Exchange Day 2014 87 Clinical and Epidemiological surveys 78. Two-part joint regression modeling to analyze longitudinal left censored patient reported outcomes Alette S. Spriensma1,2, Marieke ter Wee3, , Michiel R. de Boer4, Martijn W. Heymans1,2,4, Jolanda J. Luime5, Pascal H. de Jong5 , Maarten Boers1,3, Jos W.R. Twisk1,2,4 Department of Epidemiology and Biostatistics, VU University Medical Center, Amsterdam EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam 3 Department of Rheumatology, VU University Medical Center, Amsterdam 4 Department of Methodology and Applied Biostatistics, Faculty of Earth and Life Sciences, Institute of Health Sciences, VU University, Amsterdam 5 Department of Rheumatology, University Medical Center, Rotterdam 1 2 Introduction Patient reported outcomes often result into scores that have a lower limit. The true score of a patient, however, can lie outside of this limit, which results into left censoring/an excess of zeroes in the outcome variable. Several so-called two-part statistical models have been developed to deal with an excess of zeroes. These models contain two distributions: A binomial distribution to distinguish between left censored observations and uncensored observations, and a normal distribution (or other distribution) that deals with the uncensored part; resulting into two separate regression coefficients. However, the scores of patient reported outcomes should be seen as one process. Therefore, the purpose of this study is to use the two-part joint mixed modeling approach to analyze longitudinal HAQ trial data and to compare the performance of these newer methods with the traditional methods. Methods A linear mixed model and a logarithmic transformation of the linear mixed model (ln(x+1)) approach are to be compared with a two-part joint binomial/normal (Tobit) mixed model and a binomial/gamma two-part joint mixed model. In order to compare the models, differences between observed and predicted values will be used. Results The predicted values of the linear mixed model and the log-transformed linear mixed model showed similar results and did not predict the zeroes accurately. Of the two two-part joint models, the Tobit model showed the best prediction; the binomial/Gamma did not perform very well. Conclusions The Tobit model showed the best performance in estimating the distribution of the HAQ-score (0-3). 88 Clinical and Epidemiological surveys 79. Predictors of dizziness in older persons: a 10-year prospective cohort study in the community Otto R. Maarsingh1,2, Hanneke Stam1,2, Peter M. van de Ven1,3, Natasja M. van Schoor2, Matthew J. Ridd4, Johannes C. van der Wouden1,3 Department of General Practice & Elderly Care Medicine, VU University Medical Center, Amsterdam, The Netherlands 2 EMGO+ Institute, VU University Medical Center, Amsterdam, The Netherlands 3 Department of Epidemiology and Biostatistics, VU University Medical Center, Amsterdam, The Netherlands 4 NIHR School for Primary Care Research, University of Bristol, Bristol, United Kingdom 1 Introduction The current diagnosis-oriented approach of dizziness does not suit older patients. Often, it is not possible to identify a single underlying cause, and when a disease is revealed, therapeutic options are limited. Identification of long-term predictors of dizziness in older people may provide new leads for the approach of dizziness in older patients. Methods Population-based cohort study of 1,379 community-dwelling participants, aged 60 years or older, from the Longitudinal Aging Study Amsterdam (LASA), during 7- and 10-year follow-up. Regular dizziness was ascertained during face-to-face medical interviews. We investigated 26 predictors from six domains (socio-demographic, medical, medication, psychological, sensory, and balance/ gait). We performed multiple regression analysis with presence of regular dizziness at 7-year follow-up and 10-year follow-up as dependent variables. Results Predictors of regular dizziness at 7-year follow-up were living alone, history of regular dizziness, history of osteo/rheumatoid arthritis, history of cancer (not significant [n.s.]), use of nitrates, presence of anxiety or depression, impaired vision, and impaired function of lower extremities. Predictors of regular dizziness at 10-year follow-up were living alone (n.s.), history of regular dizziness, history of cancer (n.s.), use of anxiolytics (n.s.), and impaired function of lower extremities. Both models showed good calibration (Hosmer-Lemeshow P value of respectively 0.36 and 0.31) and fair discrimination (adjusted AUC after bootstrapping of respectively 0.77 and 0.71). Conclusions Dizziness in older age was caused by multifactorial conditions. A multifactorial approach, targeting identified predictors amenable for treatment (e.g. physiotherapy for impaired function of lower extremities), may be superior to the current diagnosis-oriented approach. VU University Medical Center Science Exchange Day 2014 89 Clinical and Epidemiological surveys 80. The sex, age, and cognitive domain dependent associations between regular voluntary exercise behavior and cognitive functioning Suzanne Swagerman1, Eco de Geus1,2, Dorret Boomsma1, Kees-Jan Kan1 1 2 Department of Biological psychology, VU Amsterdam Emgo+ Institute for Health and Care Research, VU University Medical Center Introduction Does cognitive functioning benefit from regular exercise? The answer is unclear, because empirical results are mixed. This is partly due to (1) differences in study design (observational or experimental), (2) the definition and reliability of measures of exercise behavior, (3) the composition of the sample, and (4) the cognitive domain tested. Methods We examined the associations between average energy expenditure per week (in weekly METhours) and cognitive performance in various cognitive domains, while controlling for sex and age effects. Using the widely used Computerized Neurocognitive Battery, accuracy and speed measures were obtained in the neurocognitive domains of Abstraction and Mental Flexibility, Attention, Working memory, Episodic Memory, Verbal Ability, Spatial Ability, Sensorimotor speed, Motor Speed, and Emotion. The population based sample comprised 327 males and 449 females between 13 and 86 years old (mean age 43.9). Results Univariate analyses showed that subjects who reported more leisure time exercise tended to perform faster and more accurate on the majority of tasks than those who were less active. Multivariate analyses showed that sex and age confounded these relationships. Accuracy on attention and memory related directly to weekly METhours, and only weakly so. Conclusions Our results suggest that in the base population the effects of voluntary regular leisure exercise behavior on cognitive function are limited, but do not preclude beneficial effects of exercise in clinical samples. 90 Clinical intervention 81. Microcirculatory changes during goal-directed or mean arterial pressure-guided fluid therapy in abdominal surgery N.A.M. Dekker1, J. Stens1, S. de Wolf1, R. van der Zwan1, N. Koning1, C. Boer1 Department of Anesthesiology, Institute for Cardiovascular Research, VU University Medical Center 1 Introduction This study compared the effect of pulse pressure variation (PPV) and cardiac index (CI) guided fluid therapy versus mean arterial pressure (MAP) guided fluid therapy on microcirculatory perfusion in patients undergoing elective abdominal surgery. Methods Patients were randomized into a PPV/CI- guided group (n=11) or a MAP-guided (n=12) group. PPV, CI and MAP were measured using the non-invasive finger arterial blood pressure measurement device ccNexfin. A MAP of 70 mmHg was maintained. In the PPV/CI group, an intraoperative algorithm was used keeping the PPV under 12% and CI above 2.5 L/min/m2 using fluid therapy and dobutamine and noradrenaline infusion, respectively. Sublingual perfused vessel density (PVD) was measured reflecting microvascular perfusion after anesthesia induction, and every subsequent hour using sidestream dark field imaging. Results The first hour during surgery, a higher fluid volume was administrated in the PPV/CI-guided group than the MAP-guided group (1014 ± 501ml versus 629 ± 463ml; P=0.07). This was associated with a slightly reduced microcirculatory perfusion 16.7 ± 3.1 mm/mm2) compared to MAP-guided group (17.9 ± 3.9 mm/mm2; P=0.41). The administered fluid volume correlated inversely with PVD (r=-0.59, P=0.011). Two hours after the start of surgery, the PVD in the PPV/CI group restored and tended to be higher than in the MAP-guided group (21.1 ± 1.9 vs. 18.1 ± 3.4 mm/mm2; P=0.09). Conclusion Microcirculatory perfusion improved as surgery progressed in the PPV/CI-guided group. Our findings suggest that goal-directed and MAP-guided fluid management are associated with distinct patterns in fluid resuscitation, possibly affecting microvascular perfusion. VU University Medical Center Science Exchange Day 2014 91 Clinical intervention 82. Unilateral versus bilateral upper limb training after stroke A.E.Q. van Delden1, C.E. Peper1, P.J. Beek1, G. Kwakkel1,2 1 MOVE Research Institute Amsterdam, Faculty of Human Movement Sciences, VU UniversityAmsterdam, Amsterdam 2 Department of Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center, Amsterdam Introduction Within the plethora of treatment methods for the paretic upper limb, unilateral and bilateral training protocols represent conceptually contrasting approaches with the same ultimate goal. In the Upper Limb TRaining After stroke (ULTRA-stroke) project, unilateral and bilateral upper limb training were compared with each other to assess the effectiveness of these interventions and to examine how the observed changes in sensori-motor functioning relate to changes in interlimb interactions. Methods and Results A systematic review and meta-analysis revealed no clinically relevant significant differences in effectiveness between unilateral and bilateral training in patients with acute and chronic stroke. A randomized clinical trial comparing unilateral, bilateral, and dose-matched conventional upper limb training with patients starting the intervention between 1-6 months after stroke showed similar results: no significant differences in change scores regarding clinical effects and bilateral coupling were found between groups. However, the bilateral training group showed more control over the paretic hand (i.e., greater movement harmonicity and larger wrist amplitudes) after training than both other groups. Conclusions Unilateral and bilateral training are not superior to dose-matched conventional treatment or each other in improving upper limb sensori-motor functioning after stroke. Although more control over the paretic hand after bilateral training may indicate a beneficial influence of bilateral coupling during training, this improvement did not translate into better outcomes on clinical measures in favor of bilateral training. 92 Clinical intervention 83. The first Dutch experience with the use of Strattice™ for single-stage implant based breast reconstruction R.E.G. Dikmans, MD¹, F. El Morabit¹, D.J. Hofstede, MD², S.M.H. Tuinder, MD³, A.A.W.M. van Turnhout, MD, PhD4, O.T. Zöphel, MD, PhD5, Y.C.M.M. Smulders, MD5, M.G. Mullender, PhD¹ Department of Plastic, Reconstructive & Hand Surgery, VU University Medical Center, Amsterdam ² Department of Plastic, Reconstructive & Hand Surgery, BovenIJ Hospital, Amsterdam ³ Department of Plastic, Reconstructive & Hand Surgery, Maastricht University Medical Center, Maastricht 4 Department of Plastic, Reconstructive & Hand Surgery, Tergooi Hospitals, Hilversum 5 Department of Plastic, Reconstructive & Hand Surgery, Medisch Spectrum Twente, Enschede 1 Introduction Recently, Strattice™, a porcine acellular dermal matrix has emerged as a method to assist in singlestage implant based breast reconstruction. It forms an envelope to hold the prosthesis and gives potentially an improvement of esthetic outcome. In the Netherlands, Strattice™ is used in several centers. The objective of this study is to evaluate the complications after the first experience with this technique. Methods A retrospective chart review was conducted of patients who underwent Strattice™ assisted singlestage implant based breast reconstruction in four different centers in the Netherlands between 2010 and 2013. Collected data are comorbidities, BMI, smoking, post-operative radiation and complications. Results 78 patients underwent single-stage breast reconstruction with the use of Strattice™ unilateral (54 patients) or bilateral (24 patients). A total of 99 breasts were included and evaluated. The following complications occurred; seroma 23,23%, necrosis 17,17%, wound dehiscence 14,14%, hematoma 13,13%, erythema 13,13%, infection 11,11%, pain 10,10% and hemorrhage 3,03%. Due to one of these complications 19,19% of the breasts underwent re-operation with an explantation rate of 3,03%. Conclusions Strattice™ assisted single-stage implant based breast reconstruction appears to be followed by several complications, mainly seroma production. These results are comparable with complication rates reported in literature on implant based breast reconstruction. The use of Strattice™ seems to be a promising technique, but more experience needs to be gained. Given the potential role of Strattice™ in breast reconstruction and the lack of solid evidence, level I studies are necessary. VU University Medical Center Science Exchange Day 2014 93 Clinical intervention 84. Implementation of quality of life in routine peadiatric care for adolescents with type 1 Diabetes in The Netherlands: an evaluation study Minke Eilander1, Maartje de Wit1, Frank Snoek1 1 Medical psychology, VU University Medical Center Introduction The Quality of Life (QoL) method aims to improve paediatric care for youngsters with type 1 diabetes. Adolescents complete the MIND Youth Questionnaire (MY-Q) regarding their QoL and the outcomes are discussed. Additionally parental well-being can be examined. In the Netherlands, 11 hospitals started the usage of the method in 2010. Experiences of the users were studied. Methods The diabetes team members, the adolescents and the parents completed an online survey regarding their overall experience with the QoL method and the implementation. With the teams also a semi structured interview was conducted. Results 36 team members, 29 adolescents and 66 parents completed the online survey and 10 diabetes teams were interviewed. The method is often used as a screening tool (by 94.1%); teams appreciate the possibility to concrete their feelings about adolescents (85.3%). Even though 91.2% reported the method as a high valued addition to the routine care, interviews reveal that 2 out of 10 interviewed teams successfully implemented the QoL method. However, all teams want the QoL method to be a part of the routine care in the nearby future. 78.8% of parents and 41.4% of adolescents appreciate the usage of the MY-Q. An additional 41.4% of adolescents provided a neutral opinion. 62.1% of adolescents and 78.8% of parents consider it a good idea if the method is more frequently used. According to 80% of the parents whose well-being was examined by the diabetes teams, it contributed to the paediatric diabetes care. Conclusions Implementation of the QoL method in routine care seems difficult, although the method is highly appreciated by the teams. Adolescents themselves are neutral to positive about the usage; parents are overall positive. It seems worthwhile to continue the usage and further implementation of the QoL method. More effort should be made to solve logistic problems. 94 Clinical intervention 85. Beneficial effects of aortic valve replacement on myocardial energetics in aortic valve stenosis patients A Güçlü1,6, P. Knaapen1, H.J. Harms3, A.B.A. Vonk4, W. Stooker5, A.A. Lammertsma3, A.C. van Rossum1, J. van der Velden2,6, T. Germans1 Department of Cardiology Department of Physiology 3 Departments of Radiology & Nuclear Medicine 4 Department of Cardiothoracic Surgery, Institute for Cardiovascular Research (ICaR-VU), VU University Medical Center, Amsterdam 5 Department of Cardiothoracic Surgery, Onze Lieve Vrouwe Gasthuis Amsterdam 6 ICIN-The Netherlands Heart Institute, Utrecht 1 2 Introduction Aortic valve replacement (AVR) in symptomatic aortic valve stenosis (AVS) patients is associated with a favorable prognosis. It is already known that reduction in left ventricular (LV) loading conditions leads to regression of LV hypertrophy. However, data regarding the effects of AVR on myocardial energetics are currently lacking. Therefore, this pilot study was conducted to study the effects of AVR on myocardial energetics. Methods Ten AVS patients were included (normal coronary arteries, mean age 62±10 years, 7 male). Echocardiography was performed prior to AVR and repeated after 4 months to assess peak aortic valve gradients. Changes in LV mass (LVM) and volumes were assessed by CMR. Additionally, [11C]acetate PET was performed to obtain myocardial oxygen consumption (MVO2). Next, myocardial external efficiency (MEE), i.e. the ratio between external work and MVO2, was calculated. Fourteen healthy controls (mean age 48±11 years, 9 male) underwent similar scanning protocols. Results After AVR, peak aortic valve gradient decreased from 88±20 to 24±12 mmHg, (p<0.001), as well as LVM index from 104±21 to 75±16 g∙m-2 (p<0.001). MVO2 significantly decreased from 0.11±0.03 to 0.09±0.02 mL∙min-1∙g-1, (p=0.02), which was comparable to the MVO2 observed in controls (0.10±0.02 mL∙min-1∙g-1). In addition, cardiac work significantly decreased from 15439±2631 to 10774±2446 mmHg·mL, (p<0.001), reaching similar values as in controls (10117±2268 mmHg·mL). Consequently, AVR resulted in a significant improvement in MEE from 32±7 to 37±5 %, (p=0.02). Conclusions At 4 months follow-up, the detrimental effects of AVS are partially reversed by AVR in patients with normal coronary arteries and preserved ejection fraction, evident from regression of LV hypertrophy and improvement of myocardial efficiency. VU University Medical Center Science Exchange Day 2014 95 Clinical intervention 86. Beware: Body awareness training in the treatment of wearing-off related anxiety in patients with parkinson’s disease I. Ghielen1, C.J.T. de Goede2, M. Houniet-de Gier3, E. Colette3, I.A.L. Burgers-Bots2, H.W. Berendse4,6, S. Rutten1, G Kwakkel2, OA van den Heuvel1,5,6, EEH van Wegen2 Department of Psychiatry, VU University Medical Center Department of Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center 3 Department of Medical Psychology, VU University Medical Center 4 Department of Neurology, VU University Medical Center 5 Department of Anatomy & Neurosciences, VU University Medical Center 6 Neuroscience Campus Amsterdam 1 2 Introduction Approximately 60% of patients with Parkinson’s Disease (PD) that receive dopamine replacement therapy eventually develop the wearing-off phenomenon due to on-off fluctuations. Wearing-off is not only accompanied by motor symptoms but also by non-motor symptoms, such as anxiety, which have a major impact on the patient’s quality of life. We developed and pilot-tested the effectiveness of a comprehensive Body Awareness Intervention to reduce the negative impact of wearing-off and increase self-efficacy. Methods Four PD patients participated in the experimental body-awareness pilot group therapy for 6 weeks, 2 sessions per week. The Body Awareness Intervention combines elements and techniques from physical and psychological therapies. The randomized controlled trial (36 PD patients) will be performed with a control group that receives treatment as usual. Patients will be randomly assessed to one of the conditions. Self-efficacy, mobility, mood, and quality of life will be assessed prior to and after both interventions. Results The patients participating in the pilot group rated the intervention as very positive. Patients reported being more able to relax and being less afraid of losing control. A 14,6% average reduction on the Beck Anxiety Inventory (BAI) score was found. Pilot results were used to optimize the treatment protocol for implementation in the randomized controlled trial. Conclusions The Body Awareness Intervention is appreciated by the patients and brings body and mind together in the treatment of wearing-off. The added value of this new approach, compared with treatment as usual, will now be tested in a randomized controlled study. 96 Clinical intervention 87. Effectiveness of an intercultural module: drop-out and no-show rates in non-Western migrants with affective disorders Annelies van Loon1, Anneke van Schaik1,3, Jack Dekker2, Aartjan Beekman1,3. GGZ inGeest, Amsterdam, the Netherlands, Arkin Academy, Arkin Mental Health Institute, Amsterdam, the Netherlands. 3 Department of Psychiatry, VU university Medical Center, Amsterdam, the Netherlands. EMGO+ , Institute for Health and Care Research, VU University Medical Center, Amsterdam Funding: Netherlands Organization for Health Research and Development (ZonMw) 1 2 Introduction Non-Western outpatients in specialized mental health care seem to benefit less from treatment because of early drop-out. In this study we explored the effects of a cultural competence training for therapists on the drop-out and no-show rates among Turkish and Moroccan migrants with depressive and anxiety disorders. Methods A randomized clinical trial was performed between January 2009 and January 2012. A total of 220 Moroccan and Turkish adult patients were randomly assigned to mental health workers who were trained in a cultural module and to those who were not. Drop-out and no-show rates were registered over a 6- month period after the intake session. Several possible determinants of outcome were explored by analyzing medical files. Results There were no significant differences in drop-out rates (21% versus 12%) and mean no-show between the intervention and control group. Compared to other studies the rates were relatively moderate. Language problems predicted a significantly lower drop-out rate in both conditions. Conclusions Training in cultural competence did not reduce the drop-out and no-show rates. Possibly there was no difference between the conditions because the therapists in the usual care condition were also competent in motivating and treating migrant patients. Implications for future research and practice are to collaborate more intensively with general practitioners to obtain more insight in the reasons of drop-out among outpatients in specialized mental health care. VU University Medical Center Science Exchange Day 2014 97 Clinical intervention 88. Implementation index: an indicator measuring level of implementation of school-based interventions Femke van Nassau1, Trynke Hoekstra2,3, Grace Skrzypiec4, Phillip Slee4, Amika Singh1, Willem van Mechelen1, Johannes Brug3, Mai Chin A Paw2 Department of Public and Occupational Health, VU University Medical Center, The Netherlands Faculty of Earth and Life Sciences, Department of Health Sciences, VU University, The Netherlands 3 Department of Epidemiology and Biostatistics, VU University Medical Center, The Netherlands 4 School of Education, Flinders University, Adelaide, Australia 1 2 Introduction Insight into the process of implementation is crucial to explain intervention effectiveness during implementation. We developed an implementation index score for the school-based Dutch Obesity Intervention in Teenagers (DOiT) program. The aim of the implementation index was to define a school-level implementation score. Methods Development of the index was based on recommendations of Domitrovich et al. and the implementation index of Dix et al. We included 44 items divided over six factors; fidelity, dosage and quality of delivery at both intervention and support level. Items were derived from the selfreported questionnaire of teachers completed after implementation of DOiT. Using Mplus, we conducted factor coefficient analyses to identify the best combination of items within one factor, and removing poor indicators. We used standardized coefficient scores to calculate a score for each of the six factors. We combined the six factor scores into one final index score for each teacher. Data were then aggregated to school level. Results School-level implementation scores were calculated, providing a variation in implementation between schools. We identified ‘low’ and ‘high’ implementing schools and explored the difference in index item scores between these two groups, indicating which of the 44 items contributed to high implementation. Conclusions The DOiT implementation index can provide insight into the dynamic nature of implementation processes and key factors that are expected to be critical for achieving effectiveness during large scale implementation, allowing translation of research into daily practice. 98 Clinical intervention 89. Ablation of colorectal liver metastases by irreversible electroporation: results of the COLDFIRE-I ablate-andresect study K. Nielsen1*, H.J. Scheffer2*, A.A.J.M. van Tilborg2, G. Kazemier1, J.M. Vieveen3, J.W.M. Niessen4, S. Meijer1, M.R. Meijerink2, M.P. van den Tol1. * contributed equally Department of Surgery, VU University Medical Center, Amsterdam Radiology and Nuclear Medicine, VU University Medical Center, Amsterdam 3 Anesthesiology, VU University Medical Center, Amsterdam 4 Pathology, VU University Medical Center, Amsterdam 1 2 Introduction Irreversible electroporation (IRE) is a new, non-thermal, image guided technique for tumor ablation. The application of an electric field across cells creates nanopores in the cell membrane, inducing cell death. Surrounding -acellular- connective tissue is relatively preserved, so the framework of vulnerable structures such as blood vessels and bile ducts should remain intact. We present results of the COLDFIRE study: a prospective single centre pilot study of patients with colorectal liver metastases treated with IRE before surgical resection. The aim was to evaluate safety, feasibility and (histological) changes of the ablated tissue after IRE. Methods Ten patients with resectable CRLM were included. Main exclusion criteria were cardiac arrhythmias and epilepsy. During laparotomy, the metastases were treated with IRE and resected 60 minutes later. Safety and feasibility were assessed based on adverse events, laboratory values, technical success and ultrasound confirmation of the ablation zone. Tissue response was assessed using triphenyl tetrazolium chloride (TTC) vitality staining and (immuno)histochemical stainings (HE, complement-3d and caspase-3). Results Ten lesions with a mean diameter of 2.4cm were successfully treated with IRE and resected, on average, 84 minutes later (range 51-153 minutes). One minor adverse event, a mild transient arrhythmia without hemodynamic consequences, occurred during IRE. Ultrasonography showed a sharply demarcated hypoechoic ablation zone around the tumor. TTC showed avitality of all lesions, covering the complete tumor in 8/10 lesions. Immunohistochemistry confirmed irreversible cell damage in and around the tumor. Conclusions This ablate-and-resect study demonstrated physiological and immunohistochemical cell death caused by IRE of liver metastases of colorectal origin in humans. VU University Medical Center Science Exchange Day 2014 99 Clinical intervention 90. The structure of the geriatric depressed brain and response to electroconvulsive therapy Mardien L Oudega1,2,3, Eric van Exel1,2,3, Max L. Stek1, Mike P. Wattjes4, Wiesje M. van der Flier5,6, Hannie C. Comijs1,3, Annemieke Dols1, Philip Scheltens2,5, Frederik Barkhof2,4, Piet Eikelenboom1,7, Odile A. van den Heuvel1,2,8 Department of Psychiatry, VU University Medical Center, Amsterdam Neuroscience Campus Amsterdam, VU University Medical Center, Amsterdam 3 EMGO Institute for Health and Care Research and VU University Medical Center/GGZ inGeest, Amsterdam 4 Department of Radiology, VU University Medical Center, Amsterdam 5 Department of Neurology and Alzheimer Center, VU University Medical Center, Amsterdam 6 Department of Epidemiology & Biostatistics, VU University Medical Center, Amsterdam 7 Department of Neurology, Academic Medical Center, Amsterdam 8 Department of Anatomy and Neurosciences, VU University Medical Center, Amsterdam 1 2 Objective Electroconvulsive therapy (ECT) is the treatment of choice in severe geriatric depression. High remission rates may be influenced by specific brain morphology, accompanying geriatric depression. Our objective was to identify the relationship between brain structure, symptom profile, and ECT response. Methods In a naturalistic cohort of 55 patients with a major depressive disorder, structural magnetic resonance imaging scans were made prior to ECT. Voxel-based morphometry was applied to determine regional differences in gray matter (GM) volume between patients and 23 matched healthy controls. Results Depressed patients with psychotic symptoms showed significantly higher remission rates and smaller regional GM volume of the left inferior frontal gyrus (IFG). Patients with late onset depression showed smaller regional GM volume of the bilateral lateral temporal cortex. Larger size of response in the whole patient group was related to smaller pretreatment regional GM volume of the right lateral temporal cortex, whereas faster speed of response was related to smaller pretreatment regional GM volume of the right IFG. Conclusions ECT is most effective in depressed patients with psychotic symptoms showing smaller GM volume of the left IFG and bilateral temporal cortex. Smaller volume of the IFG pretreatment was related to faster treatment response and smaller volume of the right lateral temporal cortex pretreatment was related to larger response to ECT. These results are possibly explained by the connectivity between these brain regions and interconnected network which is particularly activated by the ECT-induced seizures. 100 Clinical intervention 91. Hematopoietic stem cell transplantation for Metachromatic Leukodystrophy D.F. van Rappard1, J.J. Boelens2, M.S. van der Knaap1, N.I. Wolf1 1 2 Child Neurology, Center for White Matter Disorders, VU University Medical Center Blood and Marrow Transplantation Program, University Medical Center Utrecht Introduction Metachromatic leukodystrophy (MLD) is a severe white matter disease, caused by a deficiency of the ARSA enzyme. This study aims to evaluate the effectiveness of hematopoietic stem cell transplantation (HSCT) as a treatment for MLD Methods 13 MLD patients were followed pre and post HSCT to evaluate clinical outcome and white matter abnormalities on MRI. MRI’s were evaluated using the modified Loes scoring system for MLD. Results Survival: at this moment, 10 out of 13 patients are surviving (median follow up 29 months) with a 5 year survival probability of 83.5%. A significant difference in survival probability between symptomatic (69%) (N=7) versus presymptomatic (100%) (N= 6) patients at time of transplantation was found. In 2 of the 10 surviving patients, MRI scans showed, after an initial worsening in scores, a final improvement. Patients with the late infantile type of MLD exhibited a greater decline in gross motor function (expressed by higher scores on the GMFC) post HSCT compared to the adult and juvenile onset type. Conclusions A higher overall survival, stabilization or improvement of MRI abnormalities and less decline in motor function post HSCT are observed for presymptomatic juvenile or adult patients. In symptomatic late infantile or early juvenile patients, primarily a delay of disease progression, as opposed to complete halt of the disease, following HSCT was observed. VU University Medical Center Science Exchange Day 2014 101 Clinical intervention 92. The therapeutic potential of IGFBP7 in specific eradication of leukemic stem cells in acute myeloid leukemia Han Verhagen1, Dave de Leeuw1, Meyram Çil1, Walter Pouwels1, Arjo Rutten1, Monique Terwijn1, Patrick Celie2, Gert Ossenkoppele1, Gerrit Jan Schuurhuis1 and Linda Smit1. 1 2 Department of Hematology, VU University Medical Center, Amsterdam Protein facility, The Netherlands Cancer Institute, Amsterdam Introduction Acute myeloid leukemia (AML) is a heterogeneous disease characterized by the accumulation of abnormal immature myeloid cells in the bone marrow (BM). Despite high remission rates after chemotherapy treatment, many AML patients experience a relapse which is hard to treat and leads to a poor overall survival. The main cause of this present treatment failure is the insufficient eradication of a subpopulation of chemotherapy resistant leukemic cells with stem cell-like features called leukemic stem cells (LSC). We aim to develop novel anti-LSC therapies eradicating LSC while sparing hematopoietic stem cells (HSC) and the extent to which LSC differ from HSC is therefore of critical importance. LSC and HSC share a similar immune phenotype, CD34+CD38-, and can be further discriminated by using leukemia-associated phenotypic markers. Methods We have compared gene expression profiles of LSC compared to HSC and of LSC with that of the bulk of the AML and identified insulin growth factor binding protein-7 (IGFBP7) as differentially expressed. To elucidate the therapeutic potential of IGFBP7, we have generated rhIGFBP7 to test whether it can efficiently eradicate LSC in vitro and in vivo. Results We show that IGFBP7 induces apoptosis of AML cells, cooperates with chemotherapy and suppresses the outgrow of chemotherapy resistant cells in vitro. Conclusions Altogether, our result suggest that AML patients might benefit from combination therapy consisting of chemotherapy and IGFBP7 and that this combination might potentially overcome conventional drug resistance in LSC and the bulk of the AML and thus improve AML patient survival. 102 Clinical intervention 93. Hyperemic and hyperemia free pressure indices have an equivalent diagnostic accuracy when compared to myocardial blood flow quantified by H215O PET perfusion imaging Guus de Waard MD1, Ibrahim Danad MD1, Ricardo Petraco MD2; Paul Teunissen MD1, Pieter Raijmakers MD, PhD3, Tim van de Hoef MD4, Adriaan Lammertsma PhD3, Justin Davies MBBS, PhD2, Paul Knaapen MD, PhD1, Niels van Royen MD, PhD1 Department of Cardiology; iCaR-VU, VU University Medical Center, Amsterdam, The Netherlands Department of Cardiology; ICCH, Imperial College London, London, United Kingdom 3 Department of Nuclear Medicine; VU University Medical Center Amsterdam, The Netherlands 4 Department of Cardiology; AMC, The Netherlands 1 2 Introduction Revascularization of intermediate coronary artery stenosis guided by the fractional flow reserve (FFR) improves clinical outcomes and therefore recommended by clinical guidelines. Recently, it has been proposed that physiological lesion assessment during resting conditions might render an equivalent diagnostic performance. This study evaluated the performance of the established FFR as well as the hyperemia free instantaneous wave-free ratio (iFR), Pd/Pa ratio and finally the iFR during hyperemia (iFRa) compared them to the non-invasive gold standard, H215O PET perfusion imaging. Methods This study included 49 intermediate coronary stenoses (≥40% diameter) in patients with suspected coronary artery disease who were scheduled for coronary angiography. H215O PET perfusion imaging and intracoronary pressure measurements were obtained under both basal conditions and pharmacologically induced hyperemia. FFR, iFR, iFRa and Pd/Pa were computed and the diagnostic performance of these pressure indices was then compared to PET perfusion using predefined cutoff values. Results Mean stenosis diameter was 62±15%. Diagnostic accuracy was 78% for FFR, iFR and Pd/Pa, and 71% for iFRa. Diagnostic agreement as expressed by area under the receiver operator curve was similar across all physiological indices: 0.85 for FFR, 0.88 for Pd/Pa, 0.86 for iFR and 0.85 for iFRa (P>0.05 for all indices). Conclusions Hyperemic and hyperemia free pressure derived intracoronary indices for the assessment of moderate coronary artery stenosis, have an equivalent diagnostic accuracy when compared to H215O PET perfusion imaging. VU University Medical Center Science Exchange Day 2014 103 Clinical intervention 94. Intensive combination treatment regimens, including prednisolone, are effective in treating early rheumatoid arthritis patients regardless of additional etanercept: 1 year results of the COBRA-light trial Marieke ter Wee1, Debby den Uyl1, Maarten Boers1,2, Pit Kerstens2,3, Mike Nurmohamed1,2, Dirkjan van Schaardenburg1,2, Alexandre E. Voskuyl1, Willem F. Lems1,2 VU University Medical Center, Amsterdam Jan van Breemen Research Institute | Reade, Amsterdam 3 Westfriesgasthuis, Hoorn 1 2 Introduction Recently, we demonstrated the noninferiority of COBRA-light therapy compared to original COBRA therapy after 26 weeks in patients with early active RA. Objective: to assess the one-year results of these two protocolized strategies, aiming minimal disease activity, in terms of disease activity (DAS44), functional outcome (HAQ), and radiographic progression (SHS), and to assess the effect of addition of etanercept. Methods An open, randomized controlled, noninferiority trial in 164 patients with active early RA, following a treat-to-target protocol incorporating the addition of etanercept if DAS44 ≥ 1.6 at weeks 26 or 39. Results Both groups showed major mean improvements in DAS44 after 52 weeks: –2.40 (± 1.2) in COBRA, and –2.05 (± 1.0) in the COBRA-light group (ns). Most improvement in DAS44 was reached after 26 weeks treatment: mean decrease in DAS44 between weeks 26 and 52 was 0,2 in COBRA and 0.4 in COBRA-light therapy. In both groups, functional ability improved, and minimal radiological progression of joints was found. Treatment actually instituted was often less intensive than required by protocol: of the total population (n=164), 110 patients (67%) required etanercept (more in COBRA-light), and of those only 57 patients (52%) actually received etanercept. Conclusion Intensive treatment with COBRA or COBRA-light therapy both have major, comparable favorable effects on disease activity, functional ability and radiological outcome after one year in early RA patients. Protocolized addition of etanercept was often not implemented by treating rheumatologists, and patients receiving it appeared to have limited added benefit, probably due to low disease activity levels at initiation of etanercept. 104 Clinical intervention 95. The evaluation of a worksite intervention to promote a healthy lifestyle among employees in two different organizations Debbie Wierenga1,2,3, Luuk Engbers1,3 , Pepijn van Empelen3, Willem van Mechelen1,2 Body@Work, Research Centre on Physical Activity, Work and Health, TNO-VUmc, Amsterdam Department of Public and Occupational Health, EMGO+ Institute for Health and Care Research, VU University Medical Center, Amsterdam 3 Netherlands Organization for Applied Scientific Research, TNO Expertise Centre Life Style, Leiden 1 2 Introduction The aim of this study is to systematically evaluate the natural course of implementation of multiple lifestyle interventions at two worksites (hospital and university). Additionally, the effectiveness of the programme was assessed in a quasi-experimental controlled trial. Methods Quantitative and qualitative data on nine process components were obtained 6 and 12 months after start of implementation. The impact of the intervention on employee lifestyle behaviour (physical activity, nutrition, smoking, alcohol use and vitality) was measured at baseline and 12-month follow-up using questionnaires Results The programme was implemented partly as planned as 84.9% of all planned interventions were delivered, which were mainly easily-implemented environmental and educational interventions. High programme reach (96.6%) and participation (75.1%) was achieved. Satisfaction with the programme was moderate (6.8 ± 1.1). It appears facilitating if ‘the programme matches employee needs’, ‘employees have a positive attitude towards implementation’ and ‘employees believe it is good that their employer thinks about their health’. Effects were found for days of fruit consumption in the intervention group (β: 0.44 days/week, 95%CI 0.02 to 0.85), and for days of vegetable intake in the low participation group (β: -0.358, 95%CI -0.691 to -0.026). Conclusions This study seems to indicate that the primary precondition for a WHPP in a non-research context is not that an intervention has to be evidence-based, but it should be easily implemented, at minimal costs and effort. Implementing lifestyle interventions that target different aspects resulted in high awareness and participation but only one intervention was actually embedded in the hospitals’ general health policy. VU University Medical Center Science Exchange Day 2014 105 Clinical intervention 96. Stress reduction through mindfulness meditation, heart rate variability biofeedback or physical activity: a randomized trial J.E. van der Zwan1, W. de Vente2, A.C. Huizink1, S.M. Bögels2, E.I. de Bruin2 1 2 Department of Developmental Psychology, VU University Research Institute of Child Development and Education, University of Amsterdam Introduction World-wide there is a high prevalence of stress; therefore, the need for stress-reducing methods is high. The purpose of this study was to compare the efficacy of three stress-reducing interventions — heart rate variability (HRV) biofeedback, mindfulness meditation, and physical activity — on stress and its related symptoms. Methods 76 participants (20 males; mean age 25.8, range 18-40) were randomly allocated to HRVbiofeedback, mindfulness meditation, or physical activity. The three interventions consisted of 2 hours psycho-education and introduction to the intervention techniques followed by five weeks of daily exercises at home. For the HRV-biofeedback condition, exercises consisted of slow breathing (~6 breaths per minute) while using a HRV-biofeedback device; the mindfulness meditation exercises consisted of several guided mindful meditations recorded on a CD; for the physical activity exercises participants were free to choose a vigorous intensity activity of their liking. Psychological wellbeing, stress, anxiety, depression, and sleep quality were assessed prior to and after the training (pre-test and post-test), and 6 weeks later (follow up), using questionnaires. Results Results indicate an overall beneficial effect consisting of reduced stress, anxiety and depressive symptoms and improved psychological wellbeing and sleep quality. No significant betweenintervention effect was found on any of the outcome variables. Conclusions Results suggest that HRV-biofeedback, mindfulness meditation, and physical activity are equally effective in reducing stress, anxiety and depressive symptoms and promoting psychological wellbeing and sleep quality. 106 Clinical – Surveys on Volunteers 97. Cognitive functioning and blood pressure as a function of age Kees-Jan Kan1, Suzanne Swagerman1, Annemarie Kraaijeveld1, Eco de Geus12, Dorret Boomsma12 1 2 Department of Biological Psychology, VU University Amsterdam EMGO+ Institute for Health and Care Research, VU University Medical Center Introduction High blood pressure in the elderly is commonly treated with anti-hypertensives, which - as been suggested recently - enhance cognitive decline and thus threaten mental health. As cognitive functioning and blood pressure are both age dependent and the relationships are inconclusive, we aimed to investigate, , using multivariate modelling, the age-dependencies of cognitive functioning and blood pressure across various well-defined (neuro)cognitive domains in a population based sample. Methods In a population representative sample consisting of 250 males and 347 females between 10 and 86 years old, we measured diastolic and systolic blood pressure and accuracy performance on 17 neurocognitive tests from the Dutch computerized neurocognitive battery. Results Subjects with relatively high levels of diastolic and/or systolic blood pressure and elderly tended to perform relatively poor on the majority of tasks. Once sex and (linear and nonlinear) age effects were taken into account, correlations between blood pressure and cognitive performance dropped to near 0. Evidence for an intrinsic relationship between blood pressure and cognitive functioning was thus absent. Conclusions Our results suggest that in the base population high blood pressure does not have negative consequences for cognitive functioning. Results from recent studies, showing that antihypertensives enhance cognitive decline, need to be taken seriously. Negative effects of antihypertensives on cognitive health should be weighted against their (limited) positive effects on physical health. VU University Medical Center Science Exchange Day 2014 107 Diagnostic studies – Patients 98. Two new adult cases with AUTS2 mutations, including a two basepair deletion, further delineate the AUTS2 syndrome G. Beunders1, S.A. de Munnik2, N. van der A.3, B. Ceulemans4, E. Voorhoeve1, A.J. Groffen1, W.M. Nillesen2, E.J.Meijers-Heijboer1, R.F. Kooy3, H.G. Yntema2, E.A. Sistermans1 Department of Clinical Genetics, VU University Medical Center, Amsterdam, The Netherlands Department of Human Genetics, Radboud university medical centre, Nijmegen, The Netherlands 3 Department of Medical Genetics, University and University Hospital Antwerp, Antwerp, Belgium 4 Department of Neurology- Paediatric Neurology, University Hospital Antwerp and University of, Antwerp, Belgium 1 2 Introduction We recently described a new ID syndrome, AUTS2 syndrome that is characterised by low birth weight, feeding difficulties, intellectual disability, microcephaly and mild dysmorphic features. All cases thus far were caused by chromosomal rearrangements, mutations at the base pair level disrupting AUTS2 have not yet been described. Methods Here we present the full clinical description of two new adult cases with AUTS2 syndrome found by diagnostic exome sequencing and array CGH. Results The phenotypic features of both male cases include: intellectual disability, microcephaly, feeding difficulties, dysmorphic features and joint contractures. Both cases have intragenic AUTS2 mutations (one two-basepair deletion in exon 7 and one deletion of exon 6) that are predicted to cause a frame shift of the full length transcript but are unlikely to affect the shorter 3’ transcript starting in exon 9 that is expressed in human brain. Conclusions The similarities between the phenotypes of both cases are striking and further confirm that AUTS2 syndrome is a single gene disorder with a recognisable phenotype. 108 Diagnostic studies – Patients 99. Comparison of quantitative cardiac perfusion measurements using PET and CMR Joost J. Binnerts1†, René A. Kroes2,3†, Lourens F.H.J. Robbers1, Paul F.A. Teunissen1, Maurits R. Hollander1, Mark B.M. Hofman3, Albert van Rossum1, Paul Knaapen1, Aernout M. Beek1, Niels van Royen1 Department of Cardiology, VU University Medical Center, Amsterdam Department of Physics and Medical Technology, Tergooi, Hilversum 3 Department of Physics and Medical Technology, VU University Medical Center, Amsterdam 1 2 Introduction Positron emission tomography (PET) is currently the non-invasive reference method in quantifying myocardial blood flow (MBF), a measure commonly used for the detection of coronary artery disease (CAD). Quantitative cardiac magnetic resonance perfusion (CMR) may add a safer alternative to provide objective estimates of cardiac perfusion. This study aims to validate its accuracy against PET in patients after acute myocardial infarction (AMI). Methods First pass perfusion CMR and [15O]H2O-PET imaging was performed and compared on forty-eight patients who had suffered an AMI and undergone successful primary percutaneous coronary intervention (PCI). Results Preliminary results show poor overall correlation between PET and CMR in 17 patients when comparing segments. In certain patients, however, PET and CMR perfusion data match reasonably well. General PET and CMR perfusion data of larger myocardial areas correlate more favourably. Conclusion Comparing two separate physical principles like PET and CMR is not a straightforward process. Differences in slice thickness, segmentation protocol and reproducibility have to be overcome first. Our initial results suggest that careful slice matching could improve the correlation between PET and CMR perfusion data. VU University Medical Center Science Exchange Day 2014 109 Diagnostic studies – Patients 100. Anti-Mullerian hormone serum levels decrease in female to male transsexual women using testosterone as cross-sex therapy M.Caanen1, R.Soleman2, E. Kuijper1, B. Kreukels2, P. Hompes1, M. van Trotsenburg1, F. Broekmans3, C. Lambalk1 ¹Department of Obstetrics and Gynaecology, VU University Medical Center ²Department of Medical Psychology and Medical Social Work, VU University Medical Center ³Department of Obstetrics and Gynaecology, University Medical Center Utrecht Introduction Since Polycystic ovary syndrome (PCOS) is associated with elevated AMH levels, it is still unclear whether this is a consequence of the amount of excessive small follicles or due to hyperandrogenism, although it is assumed that androgens promote multiple early follicle growth, of which high AMH levels could be a reflection. The aim of this study therefore is to investigate the influence of androgenic treatment on AMH levels in women, the female-to-male transsexual served as a study model. Methods 22 De novo female-to-male transsexuals treated with cross-sex hormone therapy: 8 weeks of GnRH-agonist to block endogenous ovarian activity. Subsequently 16 weeks androgenic stimulation by combination of testosterone (5g/day, transdermally) and an aromatase-inhibitor (letrozole: 2,5mg/day, orally) plus continuation of the GnRH-agonist. Hormone measurements were done prior to and and after the androgenic treatment. Results After 8 weeks of agonist the serum AMH (µg/L) levels before androgen treatment were normal: mean 4.4+4.4 and 16 weeks of testosterone/letrozole therapy serum AMH levels were significantly lowered in all women to a mean of 1.4+2.1, (p=0.000). As expected, androgens were elevated after treatment. Conclusions Prolonged testosterone administration in female-to-male transsexuals, results in a very strong decline of AMH serum levels rather than an increase as expected. This challenges the earlier idea that hyperandrogenism in PCOS is a cause of elevated serum AMH levels. 110 Diagnostic studies – Patients 101. Hysterosalpingo-foam sonography (HyFoSy), a new technique to confirm proximal tubal occlusion after treatment of a hydrosalpinx by an Essure® device prior to in vitro fertilization IVF (IVF) Dreyer K.¹, Mijatovic V.¹, Emanuel M.H.², Hompes P.G.A.¹ ¹Department of Reproductive Medicine, VU University Medical Center, Amsterdam ²Department of Gynecology and Obstetrics, Spaarne Hospital, Hoofddorp Introduction Proximal occlusion of a hydrosalpinx by hysteroscopic insertion of an Essure® device may offer a safe and effective alternative to laparoscopic tubectomy prior to IVF. In this pilot study we investigate the accuracy of HyFoSy compared to hysterosalpingography (HSG) to confirm proximal tubal occlusion after Essure® treatment for hydrosalpingen. Methods In 23 patients, who were treated by Essure® devices for hydrosalpingen prior to IVF, we performed a HyFoSy as well as a HSG 12 weeks post-procedure. Results In 22 out of 23 (96%) patients, the HyFoSy procedure was successful in terms of an adequate filling of the uterine cavity. One patient refused HSG examination. In the 21 patients who underwent a successful HyFoSy as well as a HSG, the HyFoSy showed proximal occlusion in 27 of the 29 treated hydrosalpingen, compared to proximal tubal occlusion in 28 of the 29 treated hydrosalpingen at HSG. The mean procedure time of HyFoSy was significantly shorter (6 minutes ± 2) compared to HSG (11 minutes ± 5) (p = 0,01). Also the mean VAS pain score during HyFoSy (1,7 cm ± 1,9) was significantly lower compared to HSG (4,3 cm ± 2,3) (p < 0,001) Conclusions HyFoSy is a promising new sonographic technique to confirm proximal tubal occlusion, in patients treated with hysteroscopic placement of Essure® devices for hydrosalpinges, prior to IVF. HyFoSy can easily be performed at the outpatient clinic by a gynecologist himself. It is less time consuming, without radiation and HyFoSy is a less painful investigation compared to HSG. VU University Medical Center Science Exchange Day 2014 111 Diagnostic studies – Patients 102. Altered Proteobacteria Composition in Patients with Acute Uncomplicated Diverticulitis A. Eck1, L. Daniels2, M.A. Boermeester2, J.A. Bogaards3, P.H.M. Savelkoul1, A.E. Budding1 Department of Medical Microbiology and Infection Control, VU University Medical Center Gastrointestinal Surgery, Academic Medical Center, University of Amsterdam 3 Department of Clinical Epidemiology and Biostatistics, VU University Medical Center 1 2 Introduction There is increasing evidence of the role gut microbiota play in health and disease. Disease specific variations have been found for a number of intestinal disorders. Yet, little is known about microbiota variations in acute diverticulitis. Our aim was to characterize the baseline fecal microbiota composition in patients with a first episode of acute uncomplicated diverticulitis and to identify differences between diverticulitis patients and controls. Methods Patients were diagnosed with diverticulitis and sampled by rectal swabs. To obtain gut microbial profiles, we used the IS-Pro technique: a high throughput PCR based profiling technique which combines bacterial species differentiation by the length of the 16S-23S rDNA interspace region with instant taxonomic classification by phylum specific fluorescent labeling of PCR primers. Results We compared 31 patients and 25 controls. Shannon diversity of the phylum Proteobacteria was significantly higher in patients (p < 0.002). Differences in overall bacterial community composition were assessed and principal coordinates analysis (PCoA) revealed that in the Proteobacteria phylum patients were grouped separately from controls. Clinical status was predicted by the Proteobacteria profile using a partial least squares discriminant analysis (PLS-DA). With crossvalidation specificity was 76% and sensitivity 81%. Considering all phyla, specificity was 84% and sensitivity 88%. Conclusions Diverticulitis patients demonstrate a dysbiosis signature in their intestinal microbiota, evident in the Proteobacteria phylum. We consider that specific members of this phylum play a role in the pathophysiology of diverticulitis. Clinical implications may be for treatment, as microbial stratification may guide antibiotic regimen and for diagnostics, as these species are potential biomarkers. 112 Diagnostic studies – Patients 103. Assessing Muscle Endurance in Adolescents with Cerebral Palsy using a Submaximal Repetitions to Fatigue Test M.M. Eken, MSc1,2, H. Houdijk, PhD2,3, C.A.M. Doorenbosch1,4, H. Dekkers, MD2, Prof. J.G. Becher, MD, PhD1, A.J. Dallmeijer, PhD1 Department of Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center, Amsterdam 2 Heliomare Rehabilitation, Research and Development, Wijk aan Zee 3 MOVE Research Institute Amsterdam, Faculty of Human Movement Science, VU University, Amsterdam 4 Academy of Human Kinetic Technology, University of Applied Sciences, The Hague 1 Introduction The aim of the present study is to compare muscle endurance in adolescents with cerebral palsy (CP) with typically developing (TD) adolescents using a new protocol based on a submaximal repetitions-to-fatigue (RTF) test. Methods Thirteen adolescents with CP (spastic CP, GMFCS I-II) and fourteen TD adolescents (mean age (yr:mo): respectively 15:9 and 15:8) performed series of isotonic knee extensions at three different submaximal torques (~60-90% of maximal voluntary contraction (MVC)) until exhaustion. Load endurance curves were assessed as the linear relationship between imposed (relative and absolute) torque and number of repetitions. Results No significant difference was observed between relative (%MVC) load endurance curves of CP and TD adolescents. Load endurance curves of absolute torque (Nm/kg) showed significant higher torques in the TD adolescents as a function of repetition compared to the CP adolescents. Conclusions The load endurance curves of relative torque (%MVC) seems to demonstrate that muscle endurance is similar in CP and TD adolescents, which is in contrast to earlier reported lower muscle fatigability in individuals with CP. The load endurance curves of absolute torque (Nm/kg) indicate a reduced capacity in adolescents with CP to endure loads at similar absolute loading conditions when comparing to TD adolescents, which is in agreement with clinical observations. VU University Medical Center Science Exchange Day 2014 113 Diagnostic studies – Patients 104. The hippocampus in multiple sclerosis: Function, structure and its relation with memory performance Hanneke E. Hulst1, Menno M. Schoonheim1, Quinten van Geest1, Bernard M.J. Uitdehaag2, Frederik Barkhof3, Jeroen J.G. Geurts VU University Medical Center, Neuroscience Campus Amsterdam, Department of Anatomy and Neurosciences 2 VU University Medical Center, Department of Neurology 3 VU University Medical Center, Department of Radiology 1 Introduction Multiple sclerosis (MS) is a neuroinflammatory and degenerative disease of the central nervous system, resulting in physical symptoms and memory impairment. The hippocampus plays an essential role in memory function and is therefore interesting to study in the context of memory impairment in MS. Our aim was to investigate structural and functional hippocampal changes in MS and to identify the most important hippocampal parameter(s) for memory performance. Methods Structural MRI, resting-state and task-based functional MRI data were acquired from 57 MS patients (39 females) and 28 healthy controls (HC, 19 females). Hippocampal volume, hippocampal lesions, hippocampal activity during a memory task and hippocampal functional connectivity were determined. A memory composite score was calculated based on a subset of memory tests from a larger neuropsychological test battery. A linear regression analysis was used to define important hippocampal parameters for memory function in MS. Results Hippocampal volume was significantly smaller in patients with MS compared to HCs, and patients had one hippocampal lesion on average. Increased hippocampal connectivity was detected between the left hippocampus and the right posterior cingulum. In this patient group, hippocampal activation during a memory task was previously shown to be increased in cognitively preserved and decreased in cognitively impaired patients, but did not differ from controls in the patient group as a whole. Multivariate regression showed that memory dysfunction in MS was related to male sex (beta = .41), lower hippocampal activity (task fMRI; beta = .32), and higher hippocampal functional connectivity with the posterior cingulum (beta = .35; adjusted R2 = 0.32, p < .001). Conclusions The unique combination of advanced hippocampal neuroimaging measures showed that increased hippocampal functional connectivity, decreased hippocampal activity and male sex were associated with worse memory performance in MS. This underlines the predictive power of functional measures in MS, and indicates that functional activation and functional connectivity are two distinct entities to measure memory functioning. 114 Diagnostic studies – Patients 105. Compensatory fronto-parietal hyperactivation during setshifting in unmedicated patients with Parkinson’s disease Niels J.H.M. Gerrits1,5, Ysbrand D. van der Werf1,2,5, Kim M.W. Verhoef1, Dick J. Veltman4,5, Henk J. Groenewegen1,5, Henk W. Berendse3,5, Odile A. van den Heuvel1,4,5 Department of Anatomy & Neurosciences, VUmc, Amsterdam Netherlands Institute for Neuroscience, an Institute of the Royal Netherlands Academy of Arts and Sciences, Amsterdam 3 Department of Neurology, VUmc, Amsterdam 4 Department of Psychiatry, VUmc, Amsterdam 5 Neuroscience Campus Amsterdam (NCA), Amsterdam 1 2 Introduction Patients with Parkinson’s disease (PD) often suffer from impairments in executive functions, such as mental rigidity, which can be measured as impaired set-shifting. Previous studies have shown that set-shifting deficits in PD patients result from a hypo-excitation of the caudate nucleus and lateral prefrontal cortices. These studies, however, included patients who used dopaminergic medication and employed set-shifting paradigms in which task performance also depended on other cognitive mechanisms. To circumvent these potential confounding factors, we tested PD patients that were not yet using dopaminergic medication and developed a new set-shifting paradigm. Methods Eighteen patients and thirty-five matched healthy controls performed the set shifting task, while measuring their task-related neural activation with functional MRI. Results Behaviourally, PD patients, compared with healthy controls, made more errors on repeat, but not set-shift trials. There were no group differences in switch costs or normalized switch costs. PD patients, compared with healthy controls, showed increased task-related activation of the inferior parietal cortex (IPC) and pre-supplementary motor area (preSMA), and a decreased activation of the right ventrolateral prefrontal cortex (VLPFC) at set-shift trials. Normalized switch costs, in addition, correlated in patients, but not in controls, with activation of the right prefrontal cortex. Conclusions The data suggest that, despite decreased task-related activation of the right VLPFC, these earlystage unmedicated PD patients do not yet suffer from set-shifting deficits due to compensatory hyperactivation in the IPC and preSMA. VU University Medical Center Science Exchange Day 2014 115 Diagnostic studies – Patients 106. Birt-Hogg-Dubé syndrome patients with and without pneumothorax: findings on chest CT Johannesma P.C.1, van Waesberghe J.H.T.M.2, Reinhard R.2, Gille J.J.P.3, van Moorselaar R.J.A.4, Houweling A.C.3, Starink Th.M.5, Menko F.H.3, Postmus P.E.1 Department of Pulmonary Diseases, VU University Medical Center Department of Radiology, VU University Medical Center 3 Department of Clinical Genetics, VU University Medical Center 4 Department of Urology, VU University Medical Center 5 Department of Dermatology, VU University Medical Center 1 2 Introduction Birt-Hogg-Dubé (BHD) syndrome is an autosomal dominant disorder characterized by fibrofolliculomas, pulmonary cysts, (recurrent) spontaneous pneumothorax (SP) and renal cancer. The relationship between pulmonary cysts and pneumothorax in BHD has not been clarified yet. We compared chest CT findings in BHD patients (N=45) with and without pneumothorax. Methods Chest CT findings of 18 BHD patients with a history of (recurrent) SP and 27 BHD patients without SP were evaluated. The cysts on chest CTs were scored for presence, number, size, shape, craniocaudal distribution, relation to pleura and abutting to or enclosed lower pulmonary arteries and veins. Results Conclusions The number of lung cysts in BHD patients with a history of (recurrent) pneumothorax is significantly higher (p<0.008) compared to that in BHD patients without a history of pneumothorax. The size of lung cysts is not a benchmark for occurrence or recurrence rate of SP in BHD patients. 116 Diagnostic studies – Patients 107. Clinical cases; Spontaneous pneumothorax at the age of 14. Radiological evidence of Birt-Hogg-Dubé syndrome Johannesma P.C.1, van den Borne B.E.E.M.2, Nagelkerke A.F.3, van Waesberghe J.H.T.M.4, Paul M.A. 5, Menko F.H.6, Postmus P.E.1 Department of Pulmonary Diseases , VU University Medical Center Department of Pulmonary Diseases, Catharina Hospital Eindhoven 3 Department of Pediatrics, VU University Medical Center 4 Department of Radiology, VU University Medical Center 5 Department of Thoracic Surgery, VU University Medical Center 6 Department of Clinical Genetics, VU University Medical Center 1 2 Introduction In children spontaneous pneumothorax (SP) is far less frequent than in adults with an incidence of 4/100,000 annually. We present two identical cases of SP at age 14. Case reports – Results Patient 1 suffered from 4 episodes of SP treated with respectively thoracoscopic pleurodesis, pleurarubbing and tube thoracostomy performed twice. CT-chest revealed multiple cysts mainly in basal parts of the lung (R>L). This combination of recurrent SP and lung cysts indicated Birt Hogg-Dubé (BHD) syndrome, which was confirmed by FLCN mutation analysis. Patient 2 suffered from 2 episodes of SP of the right lung treated with respectively pleural rubbing and pleurectomy during VATS. Chest-CT showed multiple cysts in the basal parts of both lungs (R>L). Two years later he was referred to VUmc because relatives were diagnosed having BHD syndrome. Genetic Testing confirmed BHD. Conclusions BHD is an autosomal dominant inherited disorder, which clinically manifests as fibrofolliculomas, renal tumours, lung cysts and (recurrent) pneumothorax (SP). Clinical manifestations of BHD usually present in adults from the age of 20 onward. SP in pediatric population is relatively rare, we report here two cases of BHD –genetically confirmed- in two pediatrics with recurrent SP. We illustrate that BHD should be considered as underlying cause of SP during childhood. VU University Medical Center Science Exchange Day 2014 117 Diagnostic studies – Patients 108. Primary Spontaneous Pneumothorax: a pilot study on the frequency of FLCN mutation (Birt-Hogg-Dubé syndrome) Johannesma P.C.1, Menko F.H.2, Reinhard R.3, van Waesberghe J.H.T.M.3, van Moorselaar R.J.A.4, Starink Th.M.5, Postmus P.E.1 Department of Pulmonary Diseases , VU University Medical Center Department of Clinical Genetics, VU University Medical Center 3 Department of Radiology, VU University Medical Center 4 Department of Urology, VU University Medical Center 5 Department of Dermatology, VU University Medical Center 1 2 Introduction Spontaneous pneumothorax (PSP) is often diagnosed without a known underlying cause. Air filled cavities (blebs, bullae, cysts, ELC) are found in 90%, predominantly subpleural in apex of the upper lobes. A disease with (recurrent) pneumothorax, lung cysts in lower lobes and renal cancer is an autosomal dominant condition due to germline mutations in FLCN gene; the Birt-Hogg-Dubé syndrome (BHDS). Frequency of BHD in PSP patients is unknown. Methods PSP patients (n=509) diagnosed between 1990 and 2012 were invited by letter to the last known address - to participate in study for evaluation of the presence of BHD. The responders (n=42) underwent skin examination by a dermatologist, FLCN mutation analysis and chest-CT. Results Mean age first PSP was 33.6 years (SD ± 15.2), 75.0% was (former) smoker, 27.5% smoked soft drugs. Recurrence PSP was 52.5%, mean 2 episodes (range: 1-13).Three patients had pathogenic FLCN germline mutation (7.1%; 95% CI: 0.0150 ; 0.1948), two had multiple bilateral episodes of PSP, all three had multiple basal lung cysts. Fibrofolliculomas confirmed in two, none had renal abnormalities on renal MRI. No basal lung cysts were found on chest CT in patients without pathogenic FLCN mutation. Conclusions BHD might be more common among PSP patients than currently assumed. 118 Diagnostic studies – Patients 109. Chest CT for primary spontaneous pneumothorax (PSP): findings: Birt-Hogg-Dubé versus non-Birt-Hogg-Dubé patients Johannesma P.C.1, van Waesberghe J.H.T.M.2, Reinhard R.2, Gille J.J.P.3, van Moorselaar R.J.A.4, Houweling A.C.3, Starink Th.M.5, Menko F.H.3, Postmus P.E.1 Department of Pulmonary Diseases, VU University Medical Center Department of Radiology, VU University Medical Center 3 Department of Clinical Genetics, VU University Medical Center 4 Department of Urology, VU University Medical Center 5 Department of Dermatology, VU University Medical Center 1 2 Introduction Current guidelines advise chest X-ray in cases of primary spontaneous pneumothorax (PSP). A disease with high incidence of pneumothorax is Birt-Hogg-Dubé (BHD) syndrome, caused by germline mutations in the FLCN (folliculine) gene which causes fibrofolliculomas, recurrent SP, lung cysts and renal cancer. Methods We evaluated Chest CT findings of SP patients with or without pathogenic FLCN mutation. Chest CT’s were scored for presence, number, size, shape, craniocaudal distribution, relation to pleura and abutting to or enclosed lower pulmonary arteries and veins. Results Conclusions It is possible to differentiate between BHD and non-BHD patients with PSP based on CT findings. Including chest CT in guidelines for PSP improves detection BHD. VU University Medical Center Science Exchange Day 2014 119 Diagnostic studies – Patients 110. Novel (ovario)leukodystrophy related to AARS2 mutations Sietske H. Kevelam1, Cristina Dallabona2, Daria Diodato3,Tobias B. Haack4, Lee-Jun Wong5, Gajja S. Salomons6, Eline M.Hamilton1, Truus E.M. Abbink1, Nicole I. Wolf1, Massimo Zeviani7, Adeline Vanderver8,Daniele Ghezzi3, Marjo S. van der Knaap1,9 Department of Child Neurology, VU University Medical Center, The Netherlands Department of Life Sciences, University of Parma, Italy 3 Unit of Molecular Neurogenetics, IRCCS, Italy 4 Institute of Human Genetics and Helmholtz Zentrum, Germany 5 Department of Molecular & Human Genetics, Baylor College of Medicine, USA 6 Department of Clinical Chemistry, VU University Medical Center, The Netherlands 7 Mitochondrial Biology Unit - MRC,UK 8 Center for Genetic Medicine Research, Department of Neurology,USA 9 Department of Functional Genomics, CNCR, VU University, The Netherlands 1 2 Introduction The study was focused on leukoencephalopathies of unknown cause with the aim to define a novel similar phenotype suggestive of a common genetic defect, based on clinical and MRI findings, and to identify the causal genetic defect. Methods Next generation exome sequencing was performed in two unrelated patients with a leukoencephalopathy. Their MRI findings were compared to available MRIs in a database of unclassified leukoencephalopathies; 11 patients with similar MRI abnormalities were selected. Clinical and MRI findings were investigated. Results Next generation sequencing revealed compound heterozygous mutations in AARS2 encoding mitochondrial alanine-tRNA synthetase in both patients. Functional studies in yeast confirmed the pathogenicity of the mutations in one patient. Sanger sequencing revealed AARS2 mutations in 4 of the 11 additional patients. The 6 patients with mutations had childhood to adulthood onset signs of neurological deterioration consisting of ataxia, spasticity and cognitive decline with features of frontal lobe dysfunction. MRIs showed a leukoencephalopathy with involvement of left-right connections and ascending and descending tracts, and cerebellar atrophy. Females had ovarian failure. Conclusions Mutations in AARS2 have been found in a severe form of infantile cardiomyopathy in two families. We present 6 patients with a new phenotype caused by AARS2 mutations, characterized by leukoencephalopathy and, in female patients, ovarian failure, indicating that the phenotypic spectrum associated with AARS2 variants is much wider than previously reported. 120 Diagnostic studies – Patients 111. Brain activation patterns reflect quality of motor control of the paretic upper limb after stroke Floor E. Buma1,2, Joost van Kordelaar3, Matthijs Raemaeckers2, Erwin E.H. van Wegen3, Dietsje Jolles4, Nick F. Ramsey2, Gert Kwakkel3,5 Centre of Knowledge, Rehabilitation Centre ’De Hoogstraat’, Utrecht Dept. Neurology & Neurosurgery, Rudolf Magnus Institute of Neuroscience, UMC Utrecht, Utrecht 3 Dept. Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center, Amsterdam 4 Dept. Leiden Institute for Brain and Cognition, Leiden University, Leiden 5 Amsterdam Rehabilitation Research Center, Reade Centre for Rehabilitation and Rheumatology, Amsterdam 1 2 Introduction Patients with stroke often show increased brain activation in ipsilesional and contralesional secondary sensorimotor areas and cerebellum. However, it is unclear whether these areas can ‘take-over’ lost neurological function to restore quality of motor control after stroke. The present study investigated how cortical activation patterns are associated with quality of motor control in terms of smoothness of upper limb movements at week 5 and 26 after stroke. Methods In 17 patients, cortical activation levels in 12 regions of interest were determined with fMRI while a finger flexion-extension task was performed. In the same patients, smoothness of the grasp aperture was assessed during a reach-to-grasp task by determining the normalized jerk of finger movements with 3D kinematic analyses. Analyses of variance with post-hoc Pearson correlation coefficients were conducted to investigate how activation in each region of interest was associated to smoothness of grasp aperture. Results Higher activation in the ipsilesional premotor cortex, insula and cerebellum as well as contralesional supplementary motor area, insula and cerebellum correlated significantly with more normalized jerk of grasp aperture at week 5 after stroke. Conclusions This study suggests that involvement of secondary sensorimotor areas early after stroke results in less efficient motor strategies culminating in unsmooth, jerky movements. Additionally recruited sensorimotor areas may therefore not be able to restore quality of motor control after stroke. This finding suggests that neurorehabilitation should aim to enhance true neurological recovery of the primary motor system by optimizing quality of motor control within the first 5 weeks after stroke. VU University Medical Center Science Exchange Day 2014 121 Diagnostic studies – Patients 112. Diaphragm dysfunction in pulmonary arterial hypertension patient E. Manders1,2, P.I. Bonta3, J.J. Kloek4, P. Symersky4, N. Westerhof1, G.J.M. Stienen2, A. Vonk Noordegraaf1, F.S. de Man1 and C.A.C. Ottenheijm2 Department of Pulmonology, Institute for cardiovascular research, VU University Medical Center, Amsterdam 2 Department of Physiology, Institute for cardiovascular research, VU University Medical Center, Amsterdam 3 Department of Pulmonology, Amsterdam Medical Center, Amsterdam 4 Department of Cardiothoracic surgery, Amsterdam Medical Center, Amsterdam 1 Introduction Recently, it was suggested that patients with pulmonary arterial hypertension (PAH) suffer from diaphragm dysfunction due to increased loading. To test this, we studied the contractile strength of diaphragm muscle fibers of PAH-patients. Furthermore, we determined whether diaphragm fiber contractile strength correlates with in vivo measures of diaphragm function, disease severity and exercise capacity. Methods Mean inspiratory and expiratory pressures (MIP/MEP) were assessed in patients with chronicthromboembolitic pulmonary hypertension (CTEPH, N=8). Diaphragm and non-diaphragm muscle biopsies were obtained during pulmonary endarterectomie (N=12). For muscle fiber contractile measurements, triton-permeabilized single fibers were mounted between a force transducer and a length motor. Maximal active tension (Fmax, normalized to cross sectional area), the rate constant of force redevelopment (ktr), and active stiffness was measured at saturating Ca2+-concentration (pCa4.5), while Ca2+-sensitivity was determined at non-saturating Ca2+-concentrations. Results Diaphragm fiber F­max was significantly lower compared to non-diaphragm fibers in CTEPH-patients (141 ± 25 [mN/mm­2] vs. 162 ± 16 [mN/mm­2]). Active stiffness, reflecting the number of cycling cross-bridges, was not different between groups, while the tension/stiffness ratio, an estimate of the force per cross-bridge, was significantly lower in diaphragm muscle (2.6 ± 0.2 vs. 3.0 ± 0.5 [a.u.]). The ktr, a measure of cross-bridge cycling kinetics, was significantly lower in diaphragm fibers (9.0 ± 2.4 vs. 11.2 ± 2.7 [s-1]) and Ca2+-sensitivity, expressed as pCa50, was also significantly lower in diaphragm muscle fibers (6.10 ± 0.06 vs. 6.14 ± 0.07). Diaphragm F­max was significantly correlated with MEP ([% of predicted], p = 0.03, r2 = 0.57), 6MWT ([m], p = 0.03, r2 = 0.42) and VO2max ([L/min], p = 0.03, r2 = 0.47). No correlation was found between diaphragm Fmax and mean pulmonary artery pressure, cardiac output or pulmonary vascular resistance. Non-diaphragm F­max did not correlate with any of the parameters tested. Conclusions Although caution is in order when comparing diaphragm fibers with fibers of other skeletal muscles, our results suggest that the contractile function of diaphragm muscle fibers is hampered. The correlations between diaphragm fiber contractile function and exercise parameters such as 6MWT and VO2max, suggests that diaphragm weakness might contribute to the limited exercise capacity of CTEPH-patients. 122 Diagnostic studies – Patients 113. Contrast-Enhanced MRI as method to monitor response to anti-angiogenic therapy Marcus J.T.1, Pieters - van den Bos I.C.2, de Langen A.J.3,Verdaasdonk R.1 Physics & Medical Technology, Institute for Cardiovascular Research, VU University Medical Center Radiology, VU University Medical Center 3 Pulmonology, VU University Medical Center 1 2 Introduction Early monitoring of tumor respons to anti-angiogenic therapy is relevant. Thus the vascular permeability is to be measured. The aim is to set up a procedure for quantification of this permeability. Methods Dynamic contrast enhanced (DCE) MRI was used with a bolus of extracellular Gd contrast agent (MagnevistR). This was applied on a patient with colo-rectal liver metastases, and a patient with non small cell lung cancer. For analysis, a dual compartment tissue model was used: plasma (Vp) and the extracellular extravascular space (Ve). Contrast concentration in Ve was calculated from the convolution of the impulse response function and the arterial input function. The transfer constants between the 2 compartments were calculated: Ktrans and Kep. Results Functional maps of permeability parameters Ktrans and Kep were obtained. In the liver metastases, Ktrans ranged between 0.175 and 0.550 [min-1], displaying heterogeneity within the tumor and a central region with lowest values (probably central necrosis). Kep ranged between 0.353 and 1.97 [min-1]. In the lung tumor, Ktrans ranged between 0.2 and 0.32 [min-1]. Conclusions A workflow for quantification of tumor permeability is presented. The spatial heterogeneity within the tumor needs further exploration. Also, the validity and accuracy of the permeability parameters are still to be assessed. VU University Medical Center Science Exchange Day 2014 123 Diagnostic studies – Patients 114. Non-invasive assessment of the speed of cardiac contraction MJ van Rijssel 1, M.A.J.M. van Eijnatten1, R.M. Verdaasdonk1,2, J.H. Meijer1,2 1 2 Department of Physics and Medical Technology, VU University Medical Center Institute for Cardiovascular Research, VU University Amsterdam Introduction When the electrical conductivity of a human thorax is measured, a signal synchronous with the heart activity can be obtained. The time derivative of this electrical signal shows a characteristic pulse around the moment of ejection of the ventricles. The time difference between the peak of this C-wave (C-point) and the R-point in the ECG, is called the Initial Systolic Time Interval (ISTI). ISTI shows a substantial variation in practise of about 15-25% of the cardiac cycle. Explorative research after cardiac surgery and during haemodialysis has shown that ISTI depends on the circulating blood volume. ISTI is also affected by diseases of the autonomous nervous system (Parkinson’s disease) and is influenced by training in sports. Methods The timing of the C-point was compared with other markers of the cardiac cycle obtained by echocardiography, in a group of 16 healthy volunteers. Heart rate was varied by the application of an exercise stimulus on a stationary bicycle. The cycle markers from echocardiography were: opening and closure of the aortic valves, maximum diameter of the aortic arch and of the descending aorta. Results The C-point coincides with the maximum diameter of the aortic arch over a wide range of heart frequencies. However, while the other markers show a trend with the RR-interval, the C-point occurs at a constant time interval after opening of the valves. Conclusion The present study links the simply measurable ISTI to the time interval between the maximum electric activity of the heart and the moment of maximum diameter of the aortic arch during systole. It shows that the non-invasive ISTI can be used as a diagnostic tool to evaluate the speed of cardiac contraction in a large variety of clinical and non-clinical situations. 124 Diagnostic studies – Patients 115. Predictive value of diffusion-weighted imaging without and with contrast-enhanced magnetic resonance imaging in head and neck squamous cell carcinoma Daniel P Noij 1, Pim de Graaf , MD PhD1, Petra J.W. Pouwels, PhD2, Redina Ljumanovic, MD PhD1, Dirk L. Knol, PhD3, Patricia Doornaert, MD4, Remco De Bree, MD PhD5, Jonas A. Castelijns, MD PhD1 Department of Radiology and Nuclear Medicine, VU University Medical Center Department of Physics and Medical Technology, VU University Medical Center 3 Department of Epidemiology and Biostatistics 4 Department of Radiation Oncology, VU University Medical Center 5 Department of Otolaryngology / Head and Neck Surgery, VU University Medical Center 1 2 Introduction Several studies have reported on the predictive value of diffusion-weighted imaging (DWI), but none of these studies compared the predictive value of DWI to contrast-enhanced T1-weighted imaging (CE-T1WI). We compared the predictive value and interobserver agreement of pretreatment DWI without and with CE-T1WI in patients with head and neck squamous cell carcinoma (HNSCC) treated with (chemo)radiotherapy ((C)RT). Methods We retrospectively studied 78 patients who underwent pretreatment MRI for HNSCC staging. ADC-values were calculated with two sets of b-values: 0-750 s/mm2 (ADC750) and 0-1000 s/mm2 (ADC1000). Volume of the tumor and largest lymph node was assessed on T1 by one observer. Two observers assessed the ADC in two sessions: without and with the use of CE-MRI. Bland-Altman plots were used to compare both methods. We assessed interobserver agreement and intersession agreement with ICC. ADC-values were related to progression free survival (PFS) using Cox regression analysis. Results Mean follow-up was 18 ± 9 months. ICC range was 0.81-0.92 in the primary tumor and 0.61-0.83 in lymph nodes. Without using CE-T1WI, ADC-values were lower compared than with CE-T1WI (P <0.001). Intersession ICC range was 0.84-0.89. Pretreatment primary tumor volume and lymph node ADC1000 were independent significant predictors of PFS in both sessions (P <0.05). Conclusions Pretreatment primary tumor volume and lymph node ADC1000 are significant independent predictors of PFS in HNSCC treated with (C)RT. PFS can be predicted equally well with ADC-values acquired without and with using CE-T1WI. VU University Medical Center Science Exchange Day 2014 125 Diagnostic studies – Patients 116. Cognitive Subtypes in Alzheimer Disease defined by Latent Class Analysis N.M.E. Scheltens1, MD, F. Galindo Garre2, PhD, Y.A.L. Pijnenburg1, MD, PhD, A.E. van der Vlies1, PhD, L.L. Smits1, MSc, T. Koene3, MSc, C.E. Teunissen4, PhD, F. Barkhof5, MD, PhD, Ph. Scheltens, MD, PhD, W.M. van der Flier1,2, PhD 1 Alzheimer Center and Department of Neurology. Neuroscience Campus Amsterdam, VU University Medical Center (VUmc) Amsterdam 2 Department of Epidemiology and Biostatistics, VUmc Amsterdam 3 Alzheimer Center and Department of Medical Psychology, VUmc 4 Department of Clinical Chemistry, VUmc Amsterdam 5 Department of Radiology, VUmc Amsterdam Introduction We aimed to identify cognitive subtypes in Alzheimer Disease (AD) by performing latent class analysis (LCA) of neuropsychological test results. Methods For LCA we used neuropsychological test results of 938 patients with probable AD. Cluster membership was analyzed for associations with demographics, APOE genotype, CSF biomarkers and MRI characteristics. Results LCA revealed eight clusters, which were characterized by disease severity and impairment of specific cognitive domains: mild-memory (MILD-MEM), mild-executive (MILD-EXE), mild-diffuse (MILD-DIFF), mild-visuoperception-language (MILD-VILA), moderate-memory (MOD-MEM), moderate-visuospatial (MOD-VISP), moderate-language (MOD-LAN) and severe-diffuse (SEV-DIFF). MILD-VISP was the youngest, MOD-MEM and SEV-DIFF were least educated. MOD-LAN and SEV-DIFF had most severe medial temporal lobe atrophy, while global cortical atrophy was most severe in MOD-VISP. Multinomial logistic regression analysis with MILD-MEM as reference cluster and cluster membership as dependent variable also revealed an association between APOE e4 negative genotype and MOD-VISP, higher tau and MOD-LAN, lower ptau and MILD-EXE and MILD-DIFF, more posterior cortical atrophy and MOD-VISP and SEV-DIFF. Conclusions LCA identified eight clusters with distinct cognitive profiles, demonstrating clinical heterogeneity in AD. Associations with demographics, APOE genotype, tau, ptau and MRI characteristics suggest biological underpinning. 126 Diagnostic studies – Patients 117. Perturbations during treadmill walking offer opportunities for functional assessment of ankle stiffness L.H. Sloot MSc1, K.L. de Gooijer-van de Groep MSc2, H. Kristinsdóttir3, S. van Eesbeek MSc3, J.H. de Groot PhD2, C.G.M. Meskers MD PhD2, E. de Vlugt PhD3, J. Harlaar PhD1 Department of Rehabilitation, VU Medical Center Department of Rehabilitation Medicine, Leiden University Medical Center 3 Biomechanical Engineering, Delft University of Technology 1 2 Introduction Clinical assessment of joint stiffness is performed under passive conditions. Yet, therapy like botulinum toxin may be targeted at functional improvement. We therefore aimed to develop a method to quantify joint stiffness during active conditions, i.e. walking. Methods The method is to be developed for regular treadmill walking and based on techniques for center of pressure analysis and leg segment tracking (Optotrak, Northern Digital, Canada) and joint moment calculation. To estimate ankle stiffness, small ankle rotations need to be applied at any instant of stance without disturbing the gait pattern and inducing instability. Results Initially, a custom dual belt treadmill (Forcelink, the Netherlands) with 3-dimensional force and moment registration was constructed to apply the perturbations. Timing of the perturbation was based on the moment of heel strike (recorded from the forces) and a fixed delay based on previous steps. The perturbations induced an additional 50 Nm (relative to 100 Nm ankle torque during walking in the unperturbed case). Gait was slightly disturbed but restored within 5 steps. Conclusion This unique measurement set-up allows us to measure ankle position and ankle torque by fast perturbations while walking. This permits us to determine the functional ankle stiffness and the underlying contributors i.e. connective tissue and (activated) muscle. Assessment of ankle joint stiffness during active functional conditions will be a valuable expansion of current gait analysis to direct and evaluate therapy like botulinum toxin. VU University Medical Center Science Exchange Day 2014 127 Diagnostic studies – Patients 118. The coupling of the right ventricle to its load during exercise in pulmonary hypertension Spruijt O.A.1, Bogaard H.J.1, de Man F.S.1,, Oosterveer F.1, Groepenhoff H.1, Westerhof N.1,2, Vonk-Noordegraaf A.1 Department of Pulmonology1 and Physiology2, VU University Medical Center, Amsterdam Introduction The aim of this study was to investigate whether coupling of the right ventricle (RV) to its load deteriorates during exercise in patients with pulmonary hypertension (PH). Methods We prospectively included 10 patients with idiopathic pulmonary arterial hypertension and 2 patients with chronic thromboembolic pulmonary hypertension. All subjects underwent a 3 minute’ submaximal (40% of maximal workload) supine exercise protocol with a pulmonary artery catheter in situ. Resting and exercise hemodynamics were continuously recorded and the coupling of the RV to its load was assessed using pressure-volume loop analysis at rest and after 3 minutes of sub maximal exercise. Results Patients characteristics and resting hemodynamics (median and interquartile range): age 55 (44-62); New York Heart Association (NYHA) functional class: 7 patients NYHA II / 5 patients NYHA III; mean pulmonary artery pressure 48 (41-50) mmHg; pulmonary arterial wedge pressure 11 (712) mmHg; pulmonary vascular resistance 529 (369-691) dyn∙s/cm5; cardiac index 3,2 (2,8-3,3) L/min/m2; right atrial pressure 9 (4-11) mmHg. During exercise, RV contractility (Ees) did not change despite a significant increase in RV afterload (Ea), resulting in a decrease in RV coupling (Ees/Ea) (figure 1). Figure 1: Conclusion PH patients show a variable but substantial deterioration in coupling of the RV to its load during exercise. It remains to be determined whether the change in coupling during exercise is related to disease severity. 128 Diagnostic studies – Patients 119. Altered neural connectivity during an n-back task in unmedicated Parkinson´s disease patients James P. Trujillo*1,4, Niels J.H.M. Gerrits*1,5, Dick J. Veltman4,5, Henk W. Berendse3,5, Ysbrand D. van der Werf1,2,5#, Odile A. van den Heuvel1,4,5# *,# Both authors contributed equally to this work Department of Anatomy & Neurosciences, VU University Medical Center (VUmc), Amsterdam Netherlands Institute for Neuroscience, an Institute of the Royal Netherlands Academy of Arts and Sciences, Amsterdam 3 Department of Neurology, VUmc, Amsterdam 4 Department of Psychiatry, VUmc, Amsterdam 5 Neuroscience Campus Amsterdam (NCA), Amsterdam 1 2 Introduction Patients with Parkinson’s disease (PD) often suffer from impairments in executive functions. We investigated these impairments by studying activity and connectivity patterns during a working memory task in unmedicated PD patients compared with matched healthy controls. Methods Sixteen unmedicated patients with PD and 35 matched healthy-controls performed a visuospatial n-back task while we measured their behavioural performance and neural activity using functional MRI. Using a region-of-interest (ROI) approach, we assessed group differences in activity in the bilateral inferior parietal, bilateral dorsolateral prefrontal cortex, and bilateral caudate nucleus. We furthermore assessed the functional connectivity of the dorsolateral prefrontal cortices, and the effective connectivity within the fronto-parietal and the fronto-striatal networks. Results PD patients, compared with controls, only had marginally lower overall accuracy scores yet showed increased task-related neural activity in the bilateral dorsolateral prefrontal cortex, bilateral caudate nucleus and left inferior parietal cortex. We found reduced functional connectivity of the dorsolateral prefrontal cortices in the PD group, and a more disconnected fronto-parietal network within in the PD patients compared with controls when assessing effective connectivity. Conclusions The findings seem to indicate that the task-related network in patients with PD shows compensatory hyperactivation in order to maintain behavioural performance in the presence of network deficits due to altered effective and functional connectivity. VU University Medical Center Science Exchange Day 2014 129 Diagnostic studies – Patients 120. Innovative Molecular Drug Imaging: Pioneering Work in Children S.E.M. Veldhuijzen van Zanten1,2, i, M.H.A. Jansen1,2, i, D.G. van Vuurden1,2, M.C. Huisman3, D.J. Vugts4, O.S. Hoekstra3, G.A.M.S van Dongen3,5, G.J.L. Kaspers1,2 Department of Pediatrics, VU University Medical Center Neuro-Oncology Research Group, VU University Medical Center 3 Department of Radiology & Nuclear Medicine, VU University Medical Center 4 Department of Nuclear Medicine & PET research, VU University Medical Center 5 Department of Otolaryngology/Head and Neck Surgery, VU University Medical Center i Shared first authorship 1 2 Introduction We are the first to report the use of molecular drug imaging in children. We aim to determine the feasibility of the procedure and aim to analyzing the therapeutic- and toxic potential of bevacizumab in these children. Methods Three patients, aged 6, 7 and 17 years, diagnosed with diffuse intrinsic pontine glioma (DIPG) were included after standard treatment with radiotherapy. Each patient received 0.1mg/kg bevacizumab, labeled with 0.9MBq/kg zirconium-89(89Zr). Whole body PET-CT scans were performed at 1, 72 and 144 hours post-injection. Researchers closely monitored the feasibility of the procedure. To determine the tumor uptake and biodistribution of 89Zr-bevacizumab, Standardized Uptake Values (SUVs) were calculated. Results No adverse events occurred during any of the study procedures and scans were of good quality. Tumor uptake was shown in two out of three patients and was limited to the T1-MRI contrastenhanced part of the tumor, with SUVs of 1.8/15.0 versus 0.4/0.6 in the non-enhancing versus enhancing part, respectively. The highest 89Zr-bevacizumab uptake in organs was observed in the liver, followed by the kidneys, lungs, and bone marrow. Conclusions Administration of 89Zr-bevacizumab followed by a repeated PET-scan procedure is feasible in children. Bevacizumab uptake in organs was high in all three DIPG patients. However, only two patients showed significant bevacizumab uptake in their tumor. Moreover, uptake was limited to the contrast-enhancing part, suggesting that blood-brain barrier disruption is required for bevacizumab accessibility. With this first successful introduction of molecular drug imaging in children with cancer, we emphasize it’s importance in treatment decision-making. 130 Diagnostic studies – Patients 121. Clinical Staging of Major Depressive Disorder: an empirical exploration Judith Verduijn, MD1, Yuri Milaneschi, PhD1, Albert M. van Hemert, MD, PhD2, Robert A. Schoevers, MD, PhD3, Ian B. Hickie, MD, FRANZCP4, Brenda W.J.H. Penninx, PhD1, Aartjan T.F. Beekman, MD, PhD1 Department of Psychiatry and EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam, The Netherlands 2 Department of Psychiatry, Leiden University Medical Center, Leiden, The Netherlands 3 University of Groningen, University Medical Center Groningen, Department of Psychiatry, Groningen, The Netherlands 4 Brain and Mind Institute, University of Sydney, Sydney, Australia 1 Introduction Clinical staging has been proposed to supplement psychiatric diagnoses. We examined the construct and predictive validity of a clinical staging model for MDD that distinguishes eight consecutive stages (0,1A,1B,2,3A,3B,3C,4) based on severity and duration of symptoms, and number of episodes. Methods At baseline 2393 Netherlands Study of Depression and Anxiety participants were assigned to the eight stages of the model, of them 2069 were followed-up after two years. For construct validity, differences between stages in clinical characteristics (e.g.: severity, age of onset, co -morbid anxiety) were studied. Predictive validity was measured by the extent to which baseline stages predicted 2-year follow-up outcomes (e.g. MDD presence). Results Most clinical characteristics and follow-up outcomes showed a significant linear trend across stages with later stages having worse outcomes than early stages, confirming validity of the model. Both construct and predictive validity analyses suggest that the model performs best in the early (mostly pre-clinical) stages (0,1A,1B,2). However, in the later (clinical) stages (2,3A,3B,3C,4), validity analyses showed no differences between each consecutive stage, but only between stages with long-lasting symptoms (3A,4) compared to stages differing in number of episodes (2,3B,3C). The long-lasting stages had generally the worst outcomes. Conclusions This study showed reasonable validity for an MDD staging model that based it stages purely on clinical characteristics. Results suggest that, contrary to the number of episodes, duration of exposure to the depressed state best characterizes later stages of MDD. Future studies should test whether modifications to these later stages improve the validity of the model. VU University Medical Center Science Exchange Day 2014 131 Diagnostic studies – Patients 122. Functional deficits in response inhibition in de novo Parkinson’s disease Chris Vriend, MSc1-3, Niels J.H.M. Gerrits, Msc2,3, Henk W. Berendse, MD PhD3,4, Dick J. Veltman, MD PhD1,3, Odile A. van den Heuvel, MD PhD1-3, Ysbrand D. van der Werf, PhD2,3,5 Department of Psychiatry, VU University Medical Center Department of Anatomy & Neurosciences, VU University Medical Center 3 Neuroscience Campus Amsterdam, VU/VUmc 4 Department of Neurology, VU University Medical Center 5 Netherlands Institute for Neuroscience, Royal Netherlands Academy of Arts and Sciences 1 2 Introduction Behavioral impairments in motor response inhibition and initiation are common in Parkinson’s disease and are associated with reduced impulse control. However, no published study has yet investigated the behavioral and functional correlates of motor response inhibition in de novo Parkinson’s disease. Furthermore, the role of dopamine denervation in impulse control remains under debate. Methods Twenty-one de novo Parkinson’s disease patients and 37 matched healthy controls performed a stop-signal task during fMRI. In addition, 15 patients with Parkinson’s disease underwent [123I]FPCIT dopamine transporter (DaT) SPECT imaging to measure DaT availability in the caudate head, posterior putamen and nucleus accumbens, as an indicators of striatal dopaminergic denervation. Results Patients with Parkinson’s disease were slower on response initiation and inhibition and these types of slowing were unrelated to each other. Task-related activation of the response inhibition network, including the inferior frontal gyrus, was reduced. The activity in the inferior frontal gyrus correlated negatively with motor symptom severity in Parkinson’s disease and positively with DaT availability in the caudate head. Conclusions These findings reveal for the first time that de novo Parkinson patients exhibit functional deficits in brain areas of the response inhibition network and we tentatively suggest that these deficits are related to dopaminergic denervation of the caudate head. This study provides insights into the neural underpinning of impulse control deficits and the possible development of impulse control disorders in Parkinson’s disease. 132 Diagnostic studies – Patients 123. Force-sarcomere length relations in patients with thin filament myopathy caused by mutations in NEB, ACTA1 and TPM3 Josine M. de Winter1,3, B. Joureau1, C.T. Pappas2, G.J.M. Stienen4, A. Beggs5, N. Clarke6, H. Granzier3, C.C. Gregorio2, C.A.C. Ottenheijm1,3 Dept. of Physiology, VU University Medical Center, Amsterdam, The Netherlands Dept. of Cell Biology, University of Arizona, Tucson AZ, USA 3 Dept. of Physiology, University of Arizona, Tucson AZ, USA 4 Dept. of Physics and Astronomy, VU University, Amsterdam, The Netherlands 5 Division of Genetics and Program in Genomics, The Manton Center for Orphan Disease Research, Boston Children’s Hospital, Harvard Medical School, Boston, MA, USA 6 Institute for Neuroscience and Muscle Research, The Children’s Hospital at Westmead, NSW, 2145, Australia 1 2 Introduction: Mutations in the nebulin gene (NEB), skeletal muscle alpha-actin1 gene (ACTA1), and alpha-tropomyosin 3 gene (TPM3) lead to thin filament myopathies, such as nemaline myopathy (NM), congenital fiber type disproportion (CFTD) and cap disease (CAP). A hallmark feature of these myopathies is muscle weakness. Here, we aimed to elucidate the effect of NEB, ACTA1 and TPM3 mutations on thin filament length by determining the sarcomere lengthdependence of force. Methods: Quadriceps biopsies from NM, CFTD, and CAP patients (n=16) with mutations in either the NEB, ACTA1, or TPM3 were compared to biopsies from controls (n=3). Using permeabilized muscle fibers, maximal active tension was determined at incremental sarcomere lengths (range 2.0–3.5 µm) to obtain the force-sarcomere length relationship. Results: The maximal active tension and the force-sarcomere length relationship data are summarized in the table below (a leftward shift of the force-sarcomere length relation indicates shorter thin filaments). The classification of severity is based on the age of onset. Data are presented as mean±SD. Maximal active tension (mN/mm2) CTRL 164±17 Shape of forcesarcomere length ACTA1 mild form ACTA1 severe form NEB mild form NEB severe form TPM3 mild form TPM3 severe form 139±27 54±13# 76±5# 18±5# 156±13 95±14# Un-affected Modest leftward shift Modest leftward shift Marked leftward shift Un-affected Un-affected relation # Significantly lower compared to CTRL Note that, in contrast to patients with ACTA1 and TPM3 mutations, fiber preparations from both mildly and severely affected NEB patients have a disturbed force-sarcomere length relation. Conclusions: Our data suggest that mutations in NEB result in the most pronounced changes in thin filament length. Insights in the mechanisms underlying weakness in patients with thin filament mutations are necessary to improve specific treatment strategies. This work was supported by the ERA-NET E-Rare (7th Framework Programme) grant NEMMYOP and a VIDI grant from the Dutch Organization for Scientific Research. VU University Medical Center Science Exchange Day 2014 133 Diagnostic studies – Patients 124. Is capacity for upper extremity motor recovery fixed after a first-ever ischemic stroke? C. Winters, MSc¹, E.E.H. van Wegen, PhD¹, A. Daffertshofer, PhD² and G. Kwakkel, PhD¹,³ Department of Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center, Amsterdam, The Netherlands. 2 Faculty of Human Movement Sciences, MOVE Research Institute Amsterdam, VU University, Amsterdam, The Netherlands. 3 Department of Neurorehabilitation, Reade Centre for Rehabilitation and Rheumatology, Amsterdam, The Netherlands. 1 Introduction Spontaneous neurological recovery after stroke is a poorly understood process. The aim of the present paper was to investigate the proposed proportional recovery of upper extremity capacity, and to identify clinical characteristics of patients who do not fit this model. Methods A change in the Fugl-Meyer Assessment (FMA) arm score measured within 72 hours and at six months poststroke served to define motor recovery. Capacity for FMA recovery was predicted using the proposed model of maximal potential recovery. Hierarchical cluster analysis was used to separate non-fitters (i.e., outliers) from fitters. Group comparisons between non-fitters and fitters were made using clinical determinants measured <72 hours poststroke. Subsequent logistic regression analysis served to predict patients who may not fit the proposed maximal potential recovery model. Results The majority of patients (~70%; N=146) showed a fixed proportional upper extremity motor recovery of about 78%. Sixty-five patients had substantially less upper extremity motor improvement than predicted. These non-fitters had significantly more severe neurological impairments within 72 hours poststroke (p-values<0.01). Logistic regression analysis revealed that absence of finger extension, facial palsy, more severe lower extremity paresis, and more severe type of stroke as defined by the Bamford classification were significant predictors of not fitting the proportional recovery model of upper extremity motor recovery. Conclusions Stroke patients show an almost fixed proportional upper extremity motor recovery. Patients with more extended infarcts affecting multiple modalities show significantly less spontaneous recovery than predicted. The neurobiological mechanisms responsible for insufficient spontaneous recovery require further investigation. 134 Literature Surveys 125. Helminth infections and mrconutrients in schoolchildren: a systematic review and meta-analysis Brechje de Gier1,2, Maiza Campos Ponce1, Margot van de Bor2, Colleen M. Doak1, K.Polman1 1 Department of Health Sciences, section Infectious Diseases; VU University Amsterdam Department of Health Sciences, section Health and Life Sciences; VU University Amsterdam 2 Introduction Helminth infections and micronutrient deficiencies are both highly prevalent in developing countries. Neither condition typically causes overt disease but they do lead to indirect morbidity and impaired physical and cognitive development. We aimed to systematically review current evidence on the relationship of helminth infections with micronutrient status in schoolchildren worldwide. Methods We included both observational studies and RCTs. We used random effects meta-analysis 1) to estimate cross-sectional associations between helminths and micronutrient status; 2) to estimate anthelminthic treatment effects on micronutrient status, and 3) to estimate effects of micronutrient supplementation on helminth (re)infection. Results Meta-analyses of observational studies showed a significant association between helminth infections and serum retinol (SMD (standardized mean difference) -0.30 [-0.48;-0.13]) but not serum ferritin (SMD 0.00 [-0.7;0.7]). Conversely, meta-analyses of anthelminthic RCT studies did show a positive effect on ferritin (SMD 0.14 [0.08;0.20]) but not on retinol (SMD 0.04 [-0.06;0.14]). We did not find enough studies to pool data on other micronutrients besides ferritin and retinol. When evaluating helminth (re)infection rates in micronutrient supplementation studies, only multi-micronutrient interventions showed a modest protective effect (OR 0.77 [0.61; 0.97]). Conclusions We found significant associations between helminth infections and micronutrient status in schoolchildren. Our results showed distinct associations with either serum retinol or serum ferritin. More evidence is needed to further unravel the interrelationship between helminth infections and micronutrient status. VU University Medical Center Science Exchange Day 2014 135 Literature Surveys 126. Efficacy of intrauterine insemination in moderate to severe endometriosis. A systematic review and meta-analysis of observational data Lisette van der Houwen1, Anneke Schreurs1, Pam Kaspers2, Roel Schats1, Cornelis Lambalk1, Peter Hompes1, Velja Mijatovic1 Endometriosis Center, Division of Reproductive Medicine, Department of Obstetrics and Gynaecology, VU University Medical Center 2 Medical Library, VU Amsterdam University Library 1 Introduction A systematic review and meta-analysis is conducted to evaluate the efficacy of intrauterine insemination (IUI), since the role of this treatment in moderate to severe endometriosis patients is discussed. Methods To identify all relevant publications systematic searches were performed in the bibliographic databases PubMed, EMBASE, Cinhal and The Cochrane Library from inception to September 12th, 2013. Search terms expressing ‘endometriosis’ were used in combination with terms comprising ‘IUI’. Studies including moderate to severe endometriosis patients reporting pregnancy rates after IUI were independently selected by two reviewers. Studies were excluded if pregnancy was not specified for moderate to severe endometriosis patients receiving IUI treatment. A weighed mean pregnancy rate per patient and cycle was calculated by using Microsoft Excel (Neyeloff et al. 2012). Results Our search revealed 510 unique citations. Seventeen articles fulfilled our criteria; after exclusion of one article due to overlapping data and inclusion of our own data, seventeen articles (12 retrospective; 5 prospective) were included for the analysis. Fourteen studies reported pregnancy per patient; 165 pregnancies in 474 patients. Thirteen studies reported pregnancy per cycle; 140 pregnancies in 1088 cycles. The calculated weighed mean pregnancy rate per patient was 32.3% (95%CI 22.7%-41.9%) and per cycle 12.4% (95%CI 8.1%-16.7%). Conclusions This meta-analysis of observational data showed that IUI could be a valuable treatment in moderate to severe endometriosis. Whether this treatment can be structurally offered prior to IVF must be investigated in a randomized controlled trial including efficacy, safety and cost-effectiveness. 136 Literature Surveys 127. What is the evidence for physical therapy poststroke? A systematic review and meta-analysis J.M. Veerbeek (MSc)1, E.E.H. van Wegen (PhD)1, R.P.S. van Peppen (PhD)2, P.J. van der Wees (PhD)3, H.J.M. Hendriks (PhD)4, M.B. Rietberg (MSc)1, G. Kwakkel (PhD)1,5 Department of Rehabilitation Medicine, MOVE Research Institute Amsterdam, VU University Medical Center, Amsterdam 2 Department of Physiotherapy, University of Applied Sciences Utrecht 3 Scientific Institute for Quality of Healthcare (IQ healthcare), Radboud University Nijmegen Medical Centre 4 Department of Epidemiology, Maastricht University 5 Centre of Neurorehabilitation, Rehabilitation Centre READE, Amsterdam 1 Introduction Physical therapy (PT) is one of the key disciplines in interdisciplinary stroke rehabilitation. The aim of this systematic review was to summarize the latest evidence for stroke rehabilitation interventions in the domain of PT. Methods Randomized controlled trials (RCTs) regarding PT in stroke rehabilitation were retrieved through a systematic search. Low risk of bias RCTs were quantitatively analyzed. Differences between poststroke phases were explored in subgroup analyses. A best evidence synthesis was performed for neurological treatment approaches. Results The search yielded 467 RCTs (N=25 373), identifying 53 interventions. Strong evidence was found for positive effects of 13 interventions related to gait, 11 interventions related to arm-hand activities, 1 intervention for ADL and 3 interventions for physical fitness. Summary Effect Sizes (SESs) ranged from 0.17 (95%CI 0.03-0.70; I2=0%) for therapeutic positioning of the paretic arm to 2.47 (95%CI 0.84-4.11; I2=77%) for training sitting balance. There is strong evidence that a higher dose of practice is better, with SESs ranging from 0.21 (95%CI 0.02-0.39; I2=6%) for motor function of the paretic arm to 0.61 (95%CI 0.41-0.82; I2=41%) for muscle strength of the paretic leg. Subgroup analyses yielded significant differences with respect to timing poststroke for 10 interventions. Neurological treatment approaches showed equal or unfavorable effects when compared to other training regimes. Conclusions There is strong evidence for PT interventions favoring intensive high repetitive task-oriented and task-specific training in all phases poststroke. Effects are mostly restricted to the actually trained functions and activities. Suggestions for prioritizing PT stroke research are made. VU University Medical Center Science Exchange Day 2014 137 Preclinical disease models 128. Suppression of the Local Renin-Angiotensin System to reduce Fibrosis J.J. Akershoek1,2, M. Vlig1, C.D. Richters3,4, R.H.J. Beelen4 and M.M.W. Ulrich1,2 Association of Dutch Burn Centres, Beverwijk VU University Medical Center, Department of Plastic, Reconstructive and Hand Surgery, Amsterdam 3 Euro Tissue Bank, Beverwijk 4 VU University Medical Center, Department of Molecular Cell Biology and Immunology, Amsterdam 1 2 Introduction The healing of burn wounds often results in a hypertrophic scar. This type of scar formation is probably the result of an exaggerated and prolonged inflammation response. Suppression of the inflammatory response might result in less fibrosis to the skin. There is an increasing interest in the role of Renin-Angiotensin System (RAS) in fibrosis. The RAS not only regulates blood pressure, but is also locally active and plays a role in inflammation and remodelling. The biological active component of the RAS, Angiotensin II (AngII), can bind to either AngII receptor 1 (AT1) or 2 (AT2) which respectively has pro- or antifibrotic effects. Methods In an animal study, we investigated the role of Captopril, an inhibitor of the RAS, on the healing of contact burn wounds. The burn wounds (partial thickness) were created on the back of male rats. Subsequently the animals were treated systemically or locally with Captopril for 14 days. Results The wound size increased slightly during the first week in all treatment groups. No difference in wound closure was observed two weeks after wounding. Furthermore, immunohistological analysis showed a decreased influx of inflammatory cells at day 7 in the group receiving topical treatment. Especially the number of neutrophils was reduced, where the number of monocytes showed no difference between the treatment groups. Both treatment groups showed reduced αSMA expression compared to the control. Conclusions These results indicate that topical treatment with Captopril has potential in suppressing the inflammatory response in burn wounds, and therefore may contribute to the reduction of fibrosis. 138 Preclinical disease models 129. Toward stem cell based therapy for diseases affecting the retinal pigment epithelium Anna Bennis1,2, Theo G.M.F. Gorgels 1, Vivi M. Heine2, Arthur AB Bergen1,3,4 Dept. Molecular Ophthalmogenetics, Netherlands Institute for Neuroscience, Amsterdam Stem Cell Laboratory, VU University Medical Center, Amsterdam 3 Dept Ophthalmology, Academic Medical Center, Amsterdam 4 Dept Clinical Genetics, Academic Medical Centre, Amsterdam 1 2 Introduction The retinal pigment epithelium (RPE) is a monolayer of pigmented cells forming a part of the blood/retina barrier that interacts with the photoreceptors in the maintenance of visual function. Degeneration of the RPE is involved in multiple retinal diseases, such as age related macular degeneration (AMD). Future therapies for AMD likely involve tissue engineering, using transplantation of RPE-like cells which are derived from in vitro differentiating stem cells. The current protocols are inefficient in the generation of functional RPE cells. We aim to optimize the protocol for differentiation of stem cells into RPE cells, by gathering and applying data of in vivo gene expression in the retina. Methods Using an optimized 3D-culture system and growth factor protocol, human embryonic stem cells a re differentiated into RPE. Several techniques are used to assess RPE differentiation states, including morphology, pigmentation, RT-PCR and immunocytochemistry. We developed a new strategy to define and characterize the transcriptome of the RPE: we determined the transcriptomes of the RPE, photoreceptors and choroid. By subtracting possible contaminating RNA of the adjacent layers, we obtained a purified list of genes specifically expressed in the RPE. We did this for mouse and human RPE. Results We optimized RPE differentiation protocols and determined a set of RPE signature genes that are found in mouse and human. Conclusions The gene expression profiles of the mouse and human RPE are quite similar. We can use these expression profiles to optimize the characterization of the in vitro RPE differentiation. VU University Medical Center Science Exchange Day 2014 139 Preclinical disease models 130. SPPL2b is dramatically increased in early stages of Alzheimer’s disease and associates with amyloid plaques and neurofibrillary tangles Del Campo M1,2, Wouters D.1, Fluhrer R.3, Schröder B.4, Hoozemans J.5, Teunissen C.E.1 Clinical Chemistry, VU University Medical Center, The Netherlands Alzheimer center, VU University Medical Center, The Netherlands 3 Deutsches Zentrum für Neurodegenerative Erkrankungen (DZNE), Ludwig-Maximilians Universität, Germany 4 Institute of biochemistry, CAU Kiel University, Germany 5 Pathology, VU University Medical Center, The Netherlands 1 2 Introduction Alzheimer’s disease (AD) is the most common form of dementia with unknown aetiology characterized by the presence of amyloid beta (Aβ) plaques and neurofibrillary tangles (NFT). SPPL2b is an enzyme that can process TNFα and BRI2, substrates involved in Aβ plaque and NFT formation. Since changes in BRI2 and TNFα were previously identified in early stages of AD, we aim to investigate whether SPPL2b expression is also changed in AD hippocampus. Methods SPPL2b expression levels were quantified in post-mortem human homogenates from AD patients (n=14) and controls (n=13) by western blot. SPPL2b immunostaining was evaluated on paraffin sections from AD patients (n = 12) and age-matched controls (n=15). Results SPPL2b levels were 10-fold increased (p<0.0001) in AD hippocampus compared to non-demented controls. SPPL2b was strongly correlated (r=0.785,P<0.000) to Braak stages showing a significant increased from Braak III to IV, stages in which cognitive impairment starts. Strong SPPL2b immunoreactivity in the hippocampus was observed in early AD stages (p<0.0001), which was localised in NFT and Aβ plaques. Preincubation and comparison of staining patterns of SPPL2b family members proved that the observations were SPPL2b-specific. Conclusions We found a dramatically increase of SPPL2b in early stages of AD. SPPL2b processes BRI2 and TNFα, proteins involved not only in Aβ homeostasis but also in chronic inflammation and NFT formation. These data reveal a novel potential AD etiological factor that links Aβ plaques and NFT and thus forms a new and promising target for disease modifying therapies. 140 Preclinical disease models 131. BRI2 protein ectodomain activates critical pathological pathways involved in early stages of Alzheimer’s disease Del Campo M.1,2, Oliveira C.R.3, Pereira C.F.3 , Teunissen C.E.1 Clinical Chemistry, VU University Medical Center, The Netherlands Alzheimer center, VU University Medical Center, The Netherlands 3 Center for Neuroscience and cell biology, University of Coimbra, Portugal 1 2 Introduction Alzheimer’s disease (AD) is the most common form of dementia pathologically characterized by the presence of amyloid beta (Aβ) plaques and neurofibrillary tangles (NFT). The BRI2 ectodomain accumulates in Aβ plaques in early stages of AD hippocampus and regulates critical proteins involved in the initial steps of the amyloid cascade, the prevailing hypothesis about AD pathogenesis. Here we investigated whether the BRI2 ectodomain activates important pathways involved in early stages of AD in vitro, including apoptosis, the unfolded protein response (UPR) and the phosphorylation of glycogen synthase kinase 3 β (GSK3β), which is involved in NFT formation. Methods Non differentiated SH-SY5Y cells were exposed to recombinant BRI276-266. Cell viability was assed by MTT assay. Apoptosis was examined by analysis of the activity of Caspases 3 and 9. The proand anti-apoptotic proteins Bcl-2 and Bax, the UPR related proteins (GRP78 and Xbp-1) and the phosphorylation of GSK3β (P- GSK3β) were analysed by western blot. Results BRI2 ectodomain led to a 10% cell death, increased Bax/Bcl-2 ratio and increased activity of caspases 3 and 9, indicating an activation of the apoptosis pathway. Strikingly, BRI2 incubation led to an increase of the UPR protein Xbp-1 but not of GRP78 suggesting that BRI2 accumulation can partially activate the UPR. Incubation with BRI2 increased P-GSK3β levels. Conclusions Here we show that BRI2 ectodomain, which accumulates in AD tissue, can activate important molecular pathways involved in early stages of AD including NFT formation and neurodegeneration. Thus, these data reveal not only a new player in AD pathogenesis but also a novel potential target for the development of new disease modifying therapies. VU University Medical Center Science Exchange Day 2014 141 Preclinical disease models 132. Identification of proteins directly interacting with the HELLP-syndrome associated lincRNA using ChIRP Allerdien Visser1, Roel van der Schors2, Cees Oudejans1, Marie van Dijk1 Department of Clinical Chemistry, Institute for Cardiovascular Research, VU University Medical Center 2 Center for Neurogenomics and Cognitive Research, Neuroscience Campus Amsterdam, VU University 1 Introduction Recently, a long non-coding RNA has been identified to be associated with the HELLP-syndrome, a pregnancy-specific disease. Strong indications exist for the LINC-HELLP RNA to function in the cell cycle of placental cells. LincRNAs predominantly function through interactions with proteins. To investigate how the LINC-HELLP RNA exerts its effects on the cell cycle we used Chromatin Isolation by RNA Purification (ChIRP) to identify the directly interacting proteins. For method optimization we used a known lincRNA-protein interaction present in placental cells, i.e. KCNQ1OT1 binding to DNMT1. Methods Biotin-labeled morpholinos targeting KCNQ1OT1 (n=2), LINC-HELLP (n=4) or a non-targeting control morpholino were hybridized to crosslinked and DNAse-treated lysates of a placental cell line. Subsequently, the hybridized morpholinos were extracted from the lysates using streptavidincoated magnetic beads. Results KCNQ1OT1 qRT-PCR and DNMT1 dot blot on the extracted RNA and proteins, respectively, gave a significantly higher expression in the KCNQ1OT1 morpholino-targeted samples compared to control, confirming the suitability of the ChIRP method. Comparing the LINC-HELLP samples to control upregulation of the LINC-HELLP RNA was detected by qRT-PCR. More interestingly, extracted proteins analyzed by mass spectrometry identified a protein complex involved in the regulation of RNA stability only present in the LINC-HELLP morpholino-targeted samples. Conclusions By using ChIRP we were able to confirm a known lincRNA-protein interaction (KCNQ1OT1-DNMT1) as well as identifying a protein complex specifically bound to LINC-HELLP. When the mass spectrometry results have been validated more insight has been gained upon the specific actions of the LINC-HELLP RNA in the cell cycle. 142 Preclinical disease models 133. Vanishing White Matter diseased astrocytes inhibit oligodendrocyte progenitor cell maturation S. Dooves1,2, N. Land1,2, J.A. van der Kreeke1,2, M.S. van der Knaap1 and V.M. Heine1,2 Center for Children with White Matter Disorder, VU University Medical Center Stem Cell lab, Neuroscience Campus Amsterdam, VU University/VU University Medical Center 1 2 Introduction Vanishing White Matter (VWM) is a severe leukoencephalopathy mainly affecting children. VWM is caused by mutations in eIF2B, a gene involved in translation initiation. Previous research has shown that mainly the astrocytes and oligodendrocytes of the brain white matter are affected in these patients. However, it is still unknown what cell type primarily is involved. In this study, we looked at the effect of VWM mutations in astrocytes on oligodendrocyte progenitor cell (OPC) maturation. Methods Astrocytes from WT and VWM mice are cultured together with WT OPCs for 7 days. OPC maturation is analyzed by immunostainings and PCR. To investigate whether VWM astrocytes inhibit OPC maturation through direct contacts or through secreted factors, co-cultures received conditioned medium from WT and VWM astrocytes. Furthermore, astrocytes from WT mice are cultured together with VWM OPCs to look at how the VWM mutation specifically effects OPCs. Results VWM astrocytes inhibit OPC maturation as is apparent from decreased MBP and MOG expression. Conditioned medium from VWM astrocytes significantly decreases the number of mature oligodendrocytes in WT astrocyte-WT OPC cultures. In cultures of WT astrocytes with VWM OPCs the maturation is normal. Conclusions VWM astrocytes inhibit OPC maturation, probably through soluble factors that are secreted into the medium. In co-cultures of WT astrocytes and VWM OPCs the OPCs maturate normally into mature oligodendrocyte, suggesting that the maturation defect seen in VWM mice is mainly caused by defective astrocytes. VU University Medical Center Science Exchange Day 2014 143 Preclinical disease models 134. C1-esterase inhibitor co-localizes with C3d and C4d and is produced locally in the myocardium after acute myocardial infarction Reindert Emmens1,3,4, Umit Baylan1,3, Benno Naaijkens1,3,5, Rashmi Karia1, Diana Wouters4, Sacha Zeerleder4,6, Suat Simsek7, Marieke van Ham4, Hans Niessen1,2,3, Paul Krijnen1,3 Department of Pathology, VU University Medical Center, Amsterdam Department of Cardiac Surgery, VU University Medical Center, Amsterdam 3 ICaR-VU, Institute of Cardiovascular Research, VU University Medical Center, Amsterdam 4 Department of Immunopathology, Sanquin Research, Amsterdam 5 Interuniversity Cardiology Institute of the Netherlands, Utrecht 6 Department of Hematology, Academic Medical Center, Amsterdam 7 Department of Internal Medicine, Alkmaar Medical Center, Alkmaar 1 2 Introduction Complement is an important contributor to the inflammatory response which damages the cardiac muscle following acute myocardial infarction (AMI). However, it is not precisely known how this complement activation is regulated. For instance, the role of endogenous C1-esterase inhibitor (C1-inh), a compound which inhibits complement activation, has never been described for AMI. In this study we analyzed the presence of endogenous C1-inh in the heart during AMI. Methods C1-inh was visualized immunohistochemically in cardiac tissue of patients who died during various phases of AMI (combined n=28) and control patients (n=9). Complement activation markers C3d and C4d were visualized in the same tissue. Serping1 (C1-inh gene) transcription levels were measured in a rat model of AMI. Ischemia-reperfusion-induced C1-inh production in vitro was analyzed in endothelial cells and cardiomyoblasts with immunofluorescence microscopy. Results Especially during phase 2 AMI (infarct age of twelve hours to five days), a large deposit of endogenous C1-inh was visible in the infarct core, and correlated strongly with the presence of C3d and C4d. In the rat AMI model, serping1 transcription levels in the heart were increased from 2 hours till at least 7 days after AMI. Both endothelial cells and cardiomyoblasts were observed to have an increased quantity of intracellular C1-inh as result of ischemia and reperfusion in vitro. Conclusions Endogenous C1-inh is present in the infarct core of AMI patients and coincides with complement activation. Also, AMI stimulates production of C1-inh locally in the heart, an effect which can be simulated in vitro. 144 Preclinical disease models 135. Impulse Control Disorders in Parkinson’s disease: from preclinical model to prevention and treatment O.A. van den Heuvel1,2,3, C. Vriend1,2,3, Y.D. van der Werf2,3, P. Voorn2,3, J. Booij4, P. Raijmakers5, H.W. Berendse3,6, T. Pattij2,3 Department of Psychiatry, VU University Medical Center Department of Anatomy & Neurosciences, VU University Medical Center 3 Neuroscience Campus Amsterdam 4 Department of Nuclear Medicine, Academic Medical Center Amsterdam 5 Department of Radiology & Nuclear Medicine, VU University Medical Center 6 Department of Neurology, VU University Medical Center 1 2 Introduction Impulse control disorders (ICD) occur in 15-35% of Parkinson’s disease (PD) patients in response to dopamine replacement therapy (DRT, dopamine agonists > L-Dopa) and have a tremendous impact on patients and caregivers. The overall aim is to understand, alleviate, and prevent ICD in PD. As part of a new translational research line, we studied the relationship between dopamine depletion and impaired response inhibition, both in a rat PD model and in de novo PD patients, and now aim to bring this line of research to the level of drug development, molecular imaging and clinical trials. Methods Study 1 (preclinical): rat PD model (n=24 rats) using striatal lesions (neurotoxin 6-hydroxydopamine) and the translational response inhibition (Stop-Signal) task Study 2 (clinical): a) r etrospective longitudinal study (n=31 de novo PD) on the relationship between baseline pretreatment striatal dopamine transporter (DaT) binding (SPECT) and risk to develop ICD after DRT, b) cross-sectional fMRI study using Stop-Signal task (n=21 de novo PD + 37 controls) Preliminary results Study 1: L -Dopa administration after dorsomedial striatal dopamine depletion has limited effects on measures of response inhibition. Study 2: a) reduced striatal DaT availability predates the development of ICD after DRT, and b) task-related activation of the response inhibition network was reduced in PD patients and correlated positively with striatal DaT availability. Conclusions We have a good preclinical experimental set-up to test the effect of DRT on response inhibition. Also, human data indicate that nigrostriatal dopaminergic degeneration (DaT SPECT) and inhibitory control (fMRI) might be useful as biomarkers to predict the risk of ICDs in response to DRT in PD. VU University Medical Center Science Exchange Day 2014 145 Preclinical disease models 136. Generation of iPSCs from patients with 4H syndrome Dwayne Holmes1,2,3, Nicole Wolf1, Marjo S. van der Knaap1,Gerard Pals2 and Vivi Heine1,3 Pediatrics - Child Neurology, VU University Medical Center Clinical Genetics, VU University Medical Center 3 Stem Cell Lab, VU University 1 2 Introduction 4H syndrome is a childhood neural disorder involving hypomyelination of the central nervous system, reduced cerebellar volume, and impaired gonadal development. While the exact pathophysiology of 4H syndrome remains unknown, a mutation in the POLR3 gene was found responsible for hypo-myelination in leukodystrophies fitting 4H criteria. This raises the possibility of treating the disorder through a gene correction – cell replacement therapy, as well as creating in vitro disease models to study 4H pathophysiology. Methods Patient and control fibroblasts were converted to induced pluripotent stem cells (iPSCs) using a lentivirus containing all four reprogramming factors and a reporter gene to signal successful integration. Around 6 days after transfection, cells were transferred to a new plate and maintained in a serum/feeder free culture. Within 30 days, colonies with embryonic stem cell-like (ESC) morphology appeared in culture. Several colonies per fibroblast line were picked and expanded. Each colony was characterized for pluripotency by checking for ESC associated markers, and an ability to generate cells from all three germ layers. Results iPSCs were successfully generated and characterized for two 4H patients (3 lines each), one unaffected parent of a patient (2 lines), and two controls (2 and 3 lines, respectively). Cells with neural rosette morphology were observed on an iPSC line from the healthy parent. When induced toward neural lineage, these cells expressed early neural markers, as well as producing cells with more defined neuronal morphology. Conclusions iPSCs suitable for further testing and disease modelling have been derived from 4H patient tissue. 146 Preclinical disease models 137. Homocysteine induces apoptosis of arterial smooth muscle cells via NOX4-produced reactive oxygen Nynke E. Hahn1,9, Ellis N. ter Horst1,2,3,9,Jessica A. Sipkens1,9, Victor W.M. van Hinsbergh4,9, Rene J.P. Musters4,9, Coen D.A. Stehouwer10, Jan A. Rauwerda5,9, Jacqueline M. Hornstra4,9, Yvo M. Smulders7,9, Etto C. Eringa4,9, Kathy K. Griendling10, Hans W.M. Niessen1,6,9, Paul A.J. Krijnen2,9, Department of Pathology, VU University Medical Center, Amsterdam Department of Cardiology, Academic Medical Center, Amsterdam 3 Interuniversitary Cardiology Institute of the Netherlands, Utrecht 4 Department of Physiology, VU University Medical Center, Amsterdam 5 Department of Vascular Surgery, VU University Medical Center, Amsterdam 6 Department of Cardiac Surgery, VU University Medical Center, Amsterdam 7 Department of Internal Medicine, VU University Medical Center, Amsterdam 8 Department of Internal Medicine and Cardiovascular Research Institute Maastricht, University Medical Center, Maastricht 9 Institute of Cardiovascular Research, VU University Medical Center, Amsterdam 10 Division of Cardiology, Emory University, Atlanta GA, United States of America 1 2 Introduction Elevated levels of homocysteine (Hcy) form a vascular risk factor and can induce apoptosis of endothelial cells and vascular smooth muscle cells. Recent studies have shown that NADPH oxidase (NOX)-mediated reactive oxygen species (ROS) play a role in Hcy-induced apoptosis of endothelial cells. In this study we have analyzed the effect of Hcy on the different NOX isoforms and their role in human arterial smooth muscle cells (SMCs). Methods Human arterial SMCs isolated from the human umbilical cord were incubated with 100 µM Hcy for 24 hours and were analyzed for cell viability by determining phosphatidylserine exposure via Flow cytometry and caspase 3 activity measurements. With use of digital imaging microscopy, expression of NOX1, 2 and 4 and production of ROS were studied. NOX4 small interference RNA (siRNA) were used to specify the role of NOX4 in Hcy-induced apoptosis. Results Hcy induced a significant increase in phosphatidylserine exposure and caspase 3 activity in arterial SMC. This was accompanied by a significant translocation of NOX4 from the cytoplasm to (peri) nuclear regions, coinciding with a significant increase in local ROS production. Hcy did not affect expression levels, nor subcellular localization of NOX1 and NOX2. Knock-down of NOX4 using siRNA significantly reduced Hcy-induced (peri)nuclear NOX4 expression, concomitant ROS production and apoptosis in isolated arterial SMCs. Conclusion Pathophysiological concentrations of Hcy induce apoptosis of human arterial SMCs via NOX4 mediated ROS production. VU University Medical Center Science Exchange Day 2014 147 Preclinical disease models 138. MicroRNA-214 controls thyroid hormone levels by targeting Dio3 in the post-MI heart Rob Janssen1, Marian Zuidwijk1, Alice Muller1, Alain van Mil2, Ellen Dirkx3, Leon de Windt3, Cees Oudejans4, Warner Simonides1 Department of Physiology, ICaR-VU, VUmc University Medical Center Department of Cardiology, University Medical Center Utrecht 3 Department of Cardiology, CARIM School for Cardiovascular Diseases 4 Department of Clinical Chemistry, ICaR-VU, VUmc University Medical Center 1 2 Introduction Changes in expression of microRNAs (miR), as well as changes in thyroid hormone (TH) metabolism are associated with remodeling following myocardial infarction (MI). Several studies suggest that MI-induced upregulation of the TH-inactivating enzyme Dio3 in the left ventricle (LV) and the associated reduction of tissue TH levels contribute to the development of heart failure. In this study we addressed the hypothesis that miR-214 plays a role in regulating TH metabolism following MI by repressing Dio3 mRNA. Methods MI was induced in mice by occlusion of the left descending coronary artery. MiRs were isolated from the remodeling LVand analyzed using qPCR. MiR/target-interaction was analyzed using luciferase-reporter constructs. Results MiR-214 is upregulated in the remodeling LV at 1 week post-MI (A). We confirmed the predicted repression of Dio3 by miR-214 using a luciferasereporter construct containing the 3’UTR of Dio3 (B). Additional analysis showed that miR-214 levels increased from day 5 until 8 weeks post-MI (C), whereas a previous study showed that Dio3 mRNAlevel was maximal at 3-5 days post-MI, and subsequently decreased towards a steady elevated level 8 weeks post-MI. In an additional model ofcardiac-overloadwe showed that suppression of miR-214 expression using anti-miR-214 resulted in increased Dio3 mRNAlevels. A. B. C. Conclusions We found that Dio3 mRNA is a target of miR-214.Reciprocal changes in cardiac miR-214 and Dio3 expression were observed in several mouse models. Based on these observations, we hypothesize that increased expression of miR-214 is aimed at reducing Dio3 activity, thereby preventing an excessive and potentially lethal reduction of cardiac TH levels. 148 Preclinical disease models 139. Diaphragm muscle weakness in a novel mouse model for nebulin-based nemaline myopathy B. Joureau1, J.M. de Winter1, Kelly Stam1, A.H.Beggs2, D. Buck3, GJM Stienen1, H. Granzier3, C.A.C Ottenheijm1,3. Department of Physiology, VU University Medical Center Amsterdam, The Netherlands 2 Division of Genetics and Program in Genomics, The Manton Center for Orphan Disease Research, Harvard Medical School, Boston, MA, USA 3 Department of Physiology, University of Arizona, Tucson, AZ, USA 1 Introduction Nemaline myopathy (NM) is the most common non-dystrophic congenital myopathy, and is characterized by muscle weakness. Seven genes – all coding thin filament proteins - are implicated in NM. The main form of NM results from nebulin gene (NEB) mutations. Recently, we have generated a mouse model with a deletion of NEB exon 55, a mutation known to frequently occur in NM patients. Importantly, this model allows studying the diaphragm, a muscle whose function is very difficult to investigate in human NM. It has been postulated that the diaphragm is particularly affected in NM, and that this explains why many children with NM develop respiratory failure. Here we used NebΔExon55 mice to test the hypothesis that diaphragm strength is more affected than peripheral muscle strength. Methods Small (diameter: ~70 μm) fiber bundles of m. diaphragm and soleus were dissected from homozygous NebΔExon55 mice and from wt littermates. Bundles were permeabilized and mounted between a force transducer and length motor. Sarcomere length was set at 2.3 µm. Fiber bundles were activated by exposure to solutions with saturating [Ca2+] (pCa 4.5) and non-saturating [Ca2+] (pCa 5.8). Maximal tension, crossbridge cycling kinetics (ktr), active stiffness and calciumsensitivity of force were determined. Results Data are summarized in the table below. Diaphragm Soleus NebΔExon55 NebΔExon55 (fraction of wt) (fraction of wt) Maximal Tension (pCa 4.5; mN/mm2) 0.27±0.03*,# 0.44±0.02* Ktr (pCa 4.5; s-1) 0.53±0.03*,# 0.79±0.02* Active Stiffness (pCa 4.5; mN/mm2) Calcium Sensitivity (Force at pCa 5.8/4.5) 0.25±0.03* 0.33±0.01* 0.74±0.02*,# 0.85±0.04* Mean±SEM; * p<0.05 WT vs. NebΔExon55; # p<0.05 Diaphragm NebΔExon55 vs. Soleus NebΔExon55 Conclusions In line with our hypothesis we observed that the diaphragm muscle is more affected than peripheral skeletal muscle in this mouse model of nebulin-based NM. We speculate that preferential diaphragm weakness contributes to respiratory failure in NM. VU University Medical Center Science Exchange Day 2014 149 Preclinical disease models 140. Copy number profiling of human and murine retinoblastoma E.I. Kooi1, B.M. Mol1, T. van Harn2, A.C. Moll3, J. Cloos4,5, G.J.L. Kaspers5, H. te Riele1,2, J.C. Dorsman1 Clinical genetics, VU University Medical Center Division of molecular biology, Dutch cancer institute 3 Ophthalomology, VU University Medical Center 4 Hematology, VU University Medical Center 5 Pediatric oncology, VU University Medical Center 1 2 Introduction Retinoblastoma (Rb) is a rare but aggressive pediatric cancer that developes in the retina. Tumor development is initiated by bi-allelic inactivation of RB1, while malignant tumor proliferation is driven by additional genomic instability. Characterizing the copy number profiles of Rb tumors is a key step in identifying carcinogenesis networks that drive Rb development. Methods Following a comparative oncogenomics approach, in which variants detected in mouse oncogenomes are used as a biological filter on human oncogenomes, this study aims to identify copy number alterations driving Rb. Using high-density SNP-array platforms developed for men and mouse, copy number profiles of an unselected cohort of 74 human Rb samples were determined and of seven double knockout murine pRb-/-p130-/- tumors. Results Strikingly, our data showed that mouse Rb tumors arising from germline bi-allelic inactivated cells have a copy number stable genome. Only two acquired copy number alterations were detected in just one single tumor including a focal deletion of the CDH11 locus mapping to 16q loss in humans. On the contrary, all mouse Rb tumors with somatically acquired bi-allelic mutations (published data) did show genomic instability. A similar contrast in variability in Rb genomes was observed in the human Rb cohort, in which genome stability in young hereditary Rbs is more stable compared to tumors from old non-hereditary Rbs. Conclusions In summary, copy number data on both human and murine Rbs show that Rb tumors have variability in genome stability similar between the two species. Using the murine copy number profiles, the minimal region of 16q-loss was narrowed down to a single gene level. Furthermore, our data shows that the different murine mouse models recapitulate human Rb genetics well, advocating for their exploitation as translational models in Rb-research. 150 Preclinical disease models 141. Towards a stem cell transplantation therapy for VWM Prisca Leferink1,2, Marjo S. Van der Knaap1 and Vivi M. Heine1,2 Center for Children with White Matter Disorders, Pediatrics, VU University Medical Center, Amsterdam 2 Stem cell laboratory, VU University/VU University Medical Center, Amsterdam 1 Introduction Vanishing White Matter disease (VWM) is one of the most prevalent genetic childhood leukoencephalopathies, clinically characterized by neurological deterioration and ataxia. VWM is linked to mutations in any of the genes encoding for the 5 subunits of the eukaryotic translation initiation factor 2B (eIF2B), important for protein synthesis. In the VWM brain large regions are hypomyelinated, the glial cells seem to be predominantly affected, and remyelination is defective. Therefore, the aim of this project is to develop a patient-specific glial precursor cell (GPC) transplantation therapy, to possibly repair the pathology and achieve functional recovery of the remained intact neurons. Methods Patient specific induced pluripotent stem cells (iPSCs) are obtained via lentiviral infection of fibroblasts with transcription factors Oct3/4, Sox2, Klf4 and c-Myc. This leads to nuclear incorporation of those four genes and the reprogramming back to pluripotent stem cell stage. These iPSCs still harbor the genetic defect, therefore gene therapy in which the mutation is corrected is required. The corrected iPSCs will be differentiated into GPCs, after which their functionality will be evaluated both in vitro in co-cultures with neurons, and in vivo with transplantation in VWM mouse models. Results The human fibroblasts are successfully reprogrammed into iPSCs. Additionally, healthy human embryonic stem cells (hESCs) have successfully been differentiated into GPCs. Conclusions Progress is made towards a stem cell transplantation therapy for VWM, further research is required to investigate the functionality of both VWM and healthy GPCs. VU University Medical Center Science Exchange Day 2014 151 Preclinical disease models 142. Quantification of IFT-dynein dynamics in C. elegans J. Mijalkovic1, B. Prevo1, P. Mangeol1, F. Oswald1, E.J.G Peterman1 1 Department of Physics and Astronomy and LaserLab, VU Amsterdam, The Netherlands Introduction Cilia are organelles that extend from the surface of most eukaryotic cells, with important roles in chemo- and mechanosensation. These structures are built and maintained by bidirectional trafficking of microtubule motors in a specific transport process called Intraflagellar Transport (IFT). Dysfunctional IFT is associated with several human diseases, including Bardet-Biedl syndrome and polycystic kidney disease. In C. elegans chemosensory cilia, two types of kinesin-2 motors drive anterograde transport, whereas cytoplasmic dynein 2 (IFT-dynein) is responsible for retrograde transport. The mechanism and properties of IFT-dynein are relatively poorly understood. Here we set out to quantify its dynamics in order to gain a better understanding of the complete IFT mechanism. Methods We use MosSCI (Mos1-mediated single copy insertion) to generate mutant nematodes with eGFP or PA-GFP tagged IFT-dynein at endogenous expression levels. These motor proteins are visualized and tracked in living C. elegans using fluorescence microscopy, allowing for quantification of velocities, motor distributions and other parameters. To obtain insight into the behavior of individual IFT-dynein motors we employed photoactivation of PA-GFP. Subsequent movies were analyzed using in-house kymograph and single particle tracking software. Results Analysis reveals that IFT motor proteins move in groups (trains). IFT-dynein velocity is not constant along the cilium: motor trains speed up as they depart from the tip and decelerate as they reach the base. On a single-molecule level, tracking IFT-dynein provides information on behavior such as run lengths, pausing and turn-arounds. Conclusions Our results reveal new quantitative information on IFT-dynein dynamics at endogenous expression levels in a living organism. Understanding of IFT and dynein activity in vivo at both bulk and single-molecule level is expected to bring us a step closer to understanding ciliary disorders. 152 Preclinical disease models 143. Neuronal differentiation of iPS cells for disease modeling Aishwarya. G. Nadadhur1,2, Matthijs Verhage2, Vivi. M. Heine1,2 1 Stem cell lab, VU University/ VU University Medical Center, Amsterdam Center for Neurogenomics and Cognitive Research (CNCR), VU, Amsterdam 2 Introduction Induced pluripotent stem cells (iPSCs) are human embryonic stem cell (hESC) like, derived by reprogramming adult somatic cells (e.g. fibroblasts) with forced expression of specific genes. The iPSCs are used as in-vitro model to study phenotype of many disorders, as they can be derived from patient cells and further differentiated into any desired cell type. Our goal is to study the brain cell (neurons and glia) phenotypes and possible therapy methods of Fragile X syndrome (FXS) using patient derived iPSCs. Neuroepithelial stem cells (NES) are embryonic neural precursors, which further differentiate into neurons and glia during development. Methods 5 iPS cell lines were generated from 2 FXS patient fibroblasts by forced expression of “Yamanaka factors”. We derived NES cells from hESC and iPSCs based on previously published methods and also our novel methods. Shortly hESC or iPSCs were neural induced in N2:B27 based medium and re-plated on PLO/Laminin in same medium with FGF2. These were further differentiated to GABAergic neurons by induction with Sonic hedgehog, followed by induction with Valporic acid, after which they were maintained in neurobasal medium with neuronal survival factors. Results Characterization of iPSC lines by RNA analysis confirms pluripotency. Comparison of different populations of NES cells by morphology and expression of neural stem cell markers suggests presence of different types of NES cells. GABAergic neuronal differentiations show good expression of dendritic and neuronal markers and also calcium influxes, which suggest culturing for longer might induce synaptic activity. Conclusion It will be interesting to study the phenotype of human iPSC-derived neurons in comparison to hESC derived control neurons. And, further analysis is required to report different NES cell population and their individual roles in development. VU University Medical Center Science Exchange Day 2014 153 Preclinical disease models 144. Microglia phenotyping in pre-active MS lesions Laura A.N. Peferoen1*, Daphne Y.S. Vogel1,2*, Kimberley Ummenthum1, Marjolein Breur2, Wouter Gerritsen1, Christien D Dijkstra2, Sandra Amor1,3 Department of Pathology, VU University Medical Center, the Netherlands Department of Molecular Cell Biology and Immunology, VU University Medical Center, the Netherlands 3 Department of Neuroimmunology Unit, Blizard Institute, Queen Mary University of London, UK 1 2 Introduction Multiple Sclerosis (MS) is a complex disease of the central nervous system, characterized by areas of demyelination and inflammation. Well before any myelin and blood-brain barrier damage, clusters of activated microglia are noticeable. These clusters are considered to be the first stage of lesion formation and therefore called ‘pre-active lesions. However, they do not always progress into full-blown active destructive lesion. This strongly suggest that some regulation exists. Microglia are the innate macrophages of the brain. Macrophages can fulfil a dual role: proinflammatory (M1) and anti- inflammatory (M2). Here we postulate that a switch from an antiinflammatory to a pro-inflammatory phenotype of microglia in pre-active lesions, may be crucial in lesion development. Methods Human primary isolated microglia are cultured and stimulated to either a M1 or M2 phenotype and characterized by marker expression and cytokine profile. By immunohistochemical staining the activation status of microglia in pre-active lesions will be determined. Results In vitro data reveal that human microglia are able to be activated towards pro- and antiinflammatory phenotypes. Typical M2 markers are scarcely observed in pre-active lesions, whereas M1 markers are abundantly present. Conclusions Based on histopathological microglia phenotyping, it is not possible to predict whether a preactive lesion will turn into a demyelinating lesion. This suggests that another intrinsic factor might control this switch. A possible candidate is the myelin producing oligodendrocyte, not the victim but maybe the key player in MS lesion formation. 154 Preclinical disease models 145. Endothelial AMPKa2 regulates whole body glucose uptake Erik van Poelgeest1, Michiel P. de Boer2, Rick I. Meijer2, Erik H. Serné2, Geerten P. van Nieuw Amerongen1, Erik A. Richter, Benoit Viollet, Victor W.M. van Hinsbergh1, Yvo M. Smulders2, Etto C. Eringa1 VU University Medical Center, Amsterdam 1 Laboratory for Physiology 2 Department of Internal Medicine Institute for Cardiovascular Research (ICaR-VU) Introduction An increase in muscle tissue delivery of glucose and insulin due to insulin-induced vasodilatation of arterioles and the subsequent increase in muscle microvascular perfusion is known to be a requisite response to food intake. An impairment of this physiological response could play a role in the development of both hyperglycemia and hypertension. The energy regulator AMP-activated Kinase (AMPK) has intriguingly been shown to play a role in the regulation of arteriolar diameter by the endothelium. We hypothesized that activation of endothelial AMPK for insulin to induce vasodilatation. Methods Using our CreER/Loxp AMPK endothelium-specific inducible knockout mice we investigated insulin-induced capillary recruitment (contrast enhanced ultrasonography) and whole-body insulin sensitivity (hyperinsulinemic euglycemic clamp) and oral glucose tolerance tests. Using pressure myography we explored the mechanism of insulin-induced dilatation in skeletal muscle arterioles. Results Strikingly, AMPKEKOα2 mice are glucose intolerant. Systolic blood pressure possibly trends to be increased. Puzzling, both peripheral insulin sensitivity and capillary recruitment on insulin appear normal. Tissue-wide AMPKa2-/- mice do show decreased insulin-induced arteriolar dilatation in vivo and ex vivo as well as peripheral insulin resistance. Conclusions Endothelial AMPK could play a role in the development of both glucose intolerance and hypertension. Further experiments will be done to clarify the mechanism, i.e. in an endothelial knockout model of both AMPK’s subunits (AMPKEKO α1α2). VU University Medical Center Science Exchange Day 2014 155 Preclinical disease models 146. Predicting Glycated Haemoglobin in the Non-Diabetic General Population: a DIRECT Study Simone P. Rauh1, Martijn W. Heymans1, Marjan Alssema1, Giel Nijpels2, Coen D. Stehouwer3, Barbara Thorand4, Wolfgang Rathmann5, Christa Meisinger4, Annette Peters4, Tonia Ludwig4, Charlotte Glümer6, Oluf Pedersen7, Henna Cederberg8, Johanna Kuusisto8, Ewan R. Pearson9, Paul W. Franks10,11, Femke Rutters1, Jacqueline M. Dekker1 Department of Epidemiology and Biostatistics and the EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam, The Netherlands 2 Department of General Practice, VU Medical Center, Amsterdam, The Netherlands 3 Department of Internal Medicine and Cardiovascular Research Institute Maastricht, Maastricht University Medical Centre, Maastricht, The Netherlands 4 Institute of Epidemiology II, Helmholtz Zentrum München - German Research Center for Environmental Health, Neuherberg, Germany 5 Institute of Biometrics and Epidemiology, German Diabetes Center, Leibniz Center for Diabetes Research at Heinrich Heine University Düsseldorf, Düsseldorf, Germany 6 Research Centre for Prevention and Health, Glostrup Hospital, Capital Region of Denmark 7 The Novo Nordisk Foundation Center for Basic Metabolic Research, Faculty of Health and Medical Sciences, University of Copenhagen, Denmark 8 Department of Medicine, University of Kuopio and Kuopio University Hospital, Kuopio, Finland 9 Medical Research Institute, Ninewells Hospital and Medical School, University of Dundee, Dundee, Scotland, United Kingdom 10 Department of Clinical Sciences, Genetic and Molecular Epidemiology Unit, Lund University, Skane University Hospital Malmö, Malmö, Sweden 11 Department of Public Health and Clinical Medicine, Umea University, Umea, Sweden 1 Introduction: Recently, glycated haemoglobin (HbA1c) levels have been introduced as diagnostic criterion for type 2 diabetes. Our study evaluates whether predictors from the previously developed DETECT-2 screening tool could be used to predict HbA1c levels 6 years later. Methods: Data from 5,762 initially non-diabetic subjects from three population-based cohorts (Hoorn Study, Inter99, KORA S4) were used to predict HbA1c levels at follow-up. Using backward selection, age, BMI, waist circumference, use of anti-hypertensive medication, current smoking and parental history of diabetes remained in sex-specific linear regression models. To minimize overfitting of coefficients, we performed internal validation using bootstrapping techniques. Discrimination and calibration were assessed using classification tables (comparing highest/ lowest 50% HbA1c levels) and calibration graphs. The model was externally validated in 2,765 nondiabetic subjects of the population-based cohort METSIM. Results: At baseline, mean HbA1c level was 5.6%. During a mean follow-up of six years, 2.3% of the subjects developed HbA1c levels ≥6.5%. With respect to discrimination, our model classified 60% of the subjects correctly as having high/low HbA1c levels. Calibration plots showed that predicted HbA1c levels were underestimated in the Inter99 cohort and overestimated in the Hoorn and KORA cohorts, indicating that the model’s intercept should be adjusted for each cohort to improve predictions. External validation showed similar model performance in the METSIM cohort. Conclusions: In the non-diabetic population, simple predictors can be used to discriminate between future highest and lowest HbA1c levels. Actual HbA1c values are cohort-dependent. As a next step, for identifying high-risk individuals, current HbA1c levels can be added to the model. 156 Preclinical disease models 147. In Vitro Sonothrombolysis in Whole Blood for Myocardial No-reflow S.T. Roos1,2; F.T. Yu3; X. Chen3; O. Kamp1,2; J.J. Pacella3; F.S. Villanueva3 Cardiology department, VUmc, Amsterdam, The Netherlands ICIN – Netherlands Heart Institute, Utrecht, The Netherlands 3 Center for Ultrasound Molecular Imaging and Therapeutics, Pittsburgh, USA 1 2 Introduction Acute myocardial infarction can be treated with percutaneous coronary intervention. Adequate microvascular perfusion is often not restored due to microvascular obstruction (MVO), partly caused by microvascular microthrombi. This negatively influences clinical outcomes. We tested the hypothesis that ultrasound (US) mediated microbubble (MB) destruction can achieve microvascular clot lysis in our in vitro MVO model. Methods The model comprised of a phantom vessel containing an intraluminal mesh with 40 µm pores to simulate a cross section of the microcirculation. Bovine blood microthrombi were injected into the blood filled system, increasing upstream pressure, measured with an upstream fluid filled transducer. Partially degassed bovine whole blood and lipid MBs (2x106 MB/ml) were infused at 0.75ml/min. US was delivered at 1 MHz with a variable pulse length and peak-to-peak pressure of 1.5MPa. US was applied for 20 minutes during continuous pressure monitoring, in pulses every 3 seconds to allow MB replenishment between pulses. Control experiments utilized no MB, no US or saline as the perfusate. Experimental manipulations included the addition of tPA to the blood perfusate during US and MB delivery. Experiments were repeated 3-7 times. Results Upstream pressure decreased progressively during US delivery. US parameters affected the efficacy; thrombolysis increased with increasing acoustic pressure and duty cycle. Upstream pressure did not drop completely to zero using whole blood perfusate, when tPA was added pressure fell close to zero. Conclusions High acoustic pressure sonothrombolysis with MB can achieve reperfusion in whole blood, but with less efficacy than in PBS, suggesting differences in fluid dynamics affect bubble dynamics. VU University Medical Center Science Exchange Day 2014 157 Preclinical disease models 148. The micro- but not macro-vascular lung endothelium of pulmonary arterial hypertension patients shows a defective adaptation to high fluid shear stress Robert Szulcek1, 3, R.D. Fontijn2, S. Joemai3, A.J. Horrevoets2, K. Hartemink4, C. Dickhoff4, A. Vonk-Noordegraaf1, H.J. Bogaard1 and G.P. van Nieuw Amerongen3 Department of Pulmonary Diseases, Department of Molecular Cell Biology and Immunology, 3 Department of Physiology, 4 Department of Lung- and Endocrine Surgery, Institute for Cardiovascular Research (ICaR-VU), VU University Medical Center, Amsterdam 1 2 Introduction We hypothesize that endothelial cell activation, injury and death, caused by un-physiological high levels of fluid shear stress (HSS), is required for the pulmonary vascular remodeling found in pulmonary arterial hypertension (PAH). Therefore we tested whether pulmonary microvascular (MVEC) and pulmonary arterial endothelial cells (PAEC) from PAH patients are capable to adjust their morphology and function to HSS. Methods Static cell cultures were compared to cells under HSS (up to 25dyn/cm2). Different flow profiles (laminar, bifurcation-like) were applied and electrical impedance of the cell layers was recorded to assess barrier function. Results Striking differences were found in structural adaptation to HSS, as control MVEC re-aligned in flow direction, whereas MVEC from PAH patients failed to align after 72hrs application of HSS. Specifically, 65.3%±1.4 of the control MVEC elongated and 72.4%±4.4 of them re-aligned within an angle less than 20˚ relative to the flow direction, whereas only 47.2%±8.5 of PAH MVEC showed a stretched morphology and oriented randomly to the flow. In contrast, PAH PAEC responded similarly as control MVEC to HSS challenge. Application of bifurcation-like HSS to PAH MVEC caused severe cell loss at branch points, while control MVEC and PAH PAEC were able to withstand those flow patterns. Interestingly, upon HSS stimulation, expression of genes known to play a role in shear sensing and adaptation, was similarly up-regulated in all PAH and control samples. Under static culture conditions a two times lower protein expression of the known shear sensor CD31 as well as an significant increase in Tiam1 and phosphoERK1/2 was found in PAH MVEC and PAEC. Whereas endothelial barrier function remained unaffected, as PAH and control cells formed similar barriers with a resistance of 800-1100ohms. Conclusions PAH MVEC but not PAEC have a hampered ability to adapt to HSS, which can result in severe endothelial damage at branch points of the lung microvasculature. These findings imply that treatment strategies normalizing pulmonary blood flow and/or protect endothelial cells from injury, could prevent or reverse the vascular remodeling in PAH. 158 Preclinical disease models 149. Expression of CORIN and STOX2 and their effect on NODAL in the first trimester fetal placenta Hari Krishna Thulluru1,2, Gunilla Kleiverda3, Cees Oudejans1,2, Marie van Dijk1,2 Department of Clinical Chemistry, VU University Medical Center, Amsterdam Institute for Cardiovascular Research, VU University Medical Center, Amsterdam 3 Department of Gynecology, Flevoziekenhuis, Almere 1 2 Introduction Our group has previously shown the effect of maternal (decidual) Nodal on feto-placental NODAL and STOX1 expression indicating their potential maternal-fetal interaction.CORIN, a cardiac protease, and STOX2, a paralog of preeclampsia (PE) susceptibility gene STOX1, have lately been described as pre-eclamptic susceptibility genes. Recently, corin deficient mice showed PE like symptoms while PE patients had low corin levels. STOX2 was found to be downregulated in term PE deciduas. We therefore sought to investigate if CORIN and STOX2 factors might function in the same pathway as STOX1 and Nodal. Methods CORIN and STOX2 mRNA expression in human first trimester tissues (6-12 gestational weeks) were measured by qPCR, while STOX2 cellular localization was studied by immunohistochemistry (IHC). Conditioned media (CM) from decidual cells with CORIN and STOX2 siRNA-mediated knockdown was placed on placental cells and NODAL expression was measured. Results In tissues, CORIN was expressed at higher levels in decidua than in placenta while STOX2 was expressed almost equally in both. IHC analyses of STOX2 showed predominantly cytoplasmic signal in placenta and nuclear in decidua tissues. Placental cells that can invade the decidua also showed nuclear expression. CM of CORIN and STOX2 knockdown in decidua and a decidual stromal cell line gave downregulated NODAL expression in placental cells. Conclusions These preliminary findings demonstrate a potential shared pathway between CORIN, STOX2 and NODAL in the development of PE. VU University Medical Center Science Exchange Day 2014 159 Preclinical disease models 150. Traction force microscopy: a study of the endothelium during thrombin-mediated contractility Erik T. Valent1, Lona J. Kroese1,Ramaswamy Krishnan2, Victor W.M. van Hinsbergh1, Geerten P. van Nieuw Amerongen1 VU University Medical Center, Institute for Cardiovascular Research, Department of Physiology, Amsterdam, The Netherlands 2 Beth Israel Deaconess Medical Center, Center for Vascular Biology Research, Boston, Massachusetts, USA 1 Introduction Different studies indicate that endogenously generated endothelial contractility plays a key role in barrier dysfunction. Interestingly, the nature and distribution of these forces remains largely unknown. With the use of traction force microscopy (TFM), we aim to study the contractions of endothelial monolayers in thrombin mediated hyperpermeability. Methods Previously described TFM methods are used to generate force maps of HUVECs monolayer under basal and after stimulation with the vaso-active agent thrombin. Results Novel overlays of traction force maps with images of the endothelium revealed a heterogenic force landscape with characteristic punctuated hot spots. These highly dynamic and fluctuating forces were very time and location dependant and assumed to be the consequence of mechanical feedback from within the monolayer. Upon thrombin stimulation traction forces were increased significantly (baseline 47± 2.4 Pa vs thrombin 131± 4.8 Pa) as well as the size of the hotspots. Intercellular gap formation is typically observed at locations where two force hotspots pull in opposite direction and when the cell-cell interaction is thorn apart, an area of low traction forces is formed. Conclusion This study shows highly dynamic balancing of forces within resting endothelial monolayers. During thrombin-mediated contractility, hotspot location and force vector angle are of key importance in relation to the formation of inter-endothelial gaps. Funding: Dutch Heart Foundation 160 Preclinical disease models 151. GM-CSF stimulation of monocytes enhances migration over endothelial cells Daphne Y.S. Vogel1,2, Priscilla D.A.M. Heijnen1, Marjolein Breur1, Helga E. de Vries 1, Sandra Amor2,3, Christine D. Dijkstra1 Department of Molecular Cell Biology and Immunology, Neuroscience Campus Amsterdam VU University Medical Center, Amsterdam, the Netherlands 2 Department of Pathology VU University Medical Center, Amsterdam, the Netherlands 3 Department of Neuroimmunology Unit, Blizard Institute, Barts and the London School of Medicine and Dentistry, Queen Mary University of London, United Kingdom 1 Introduction Multiple sclerosis (MS) is a chronic inflammatory demyelinating disease of the central nervous system. Infiltration of macrophages into the central nervous system is crucial for disease onset and progression. Granulocyte-macrophage colony-stimulating factor (GM-CSF) has been shown to be essential for the migration of monocytes acrossthe blood brain barrier, since blocking GM-CSF inhibits clinical signs of experimental autoimmune encephalomyelitis(EAE), an experimental model for MS. Although the role of GM-CSF in MS is less apparent, GM-CSF can activate monocytes and macrophages. Higher levels of GM-CSF in cerebrospinal fluid during MS relapses indicate that GMCSF may play an important role in leukocyte recruitment. Methods To elucidate which cells produce GM-CSF and express the GM-CSF receptor we performed immunohistochemistry on MS lesions. GM-CSF receptor is expressed by neurons in the rim of the lesion, whereas GM-CSF is expressed by inflammatory cells in the perivascular space. To investigate the effect of GM-CSF on macrophages, the levels of expression of CD40 and mannose receptor (MR) were determined using flow cytometry to investigate the activation status. GM-CSF induces the expression of both CD40 and MR on macrophages as shown in active MS lesions. Next we assessed the migratory capacity of monocytes towards CCL2 in the presence of GM-CSF in a transwell culture system using a monolayer of human endothelial cells. Conclusion Altogether our data indicate that GM-CSF is a potent stimulator of monocyte migration in human in vitro models, which is supporting the relevance of previous findings in EAE models for neuroinflammation in human disease. VU University Medical Center Science Exchange Day 2014 161 Preclinical disease models 152. Faster cross-bridge relaxation rates correlate with increased tension cost in HCM with the R403Q MYH7 mutation E. Rosalie Witjas-Paalberends1, Claudia Ferrara2, Beatrice Scellini2, Judith Montag3, Ger J.M. Stienen1,4, Michelle Michels5, Carolyn Ho6, Theresia Kraft3, Corrado Pogessi2, Jolanda van der Velden1,7. Department of Physiology, VU University Medical Center, Amsterdam, The Netherlands Department of Physiology, University of Florence, Florence, Italy 3 Inst. of Molecular and Cell Physiology, Hannover Medical School, Hannover, Germany 4 Department of Physics and Astronomy, VU University, Amsterdam, The Netherlands 5 Thorax Center, Cardiology, Erasmus Medical Center, Rotterdam, The Netherlands 6 Brigham and Women’s Hospital, Cardiology, Boston, USA 7 ICIN- Netherlands Heart Institute, Utrecht, The Netherlands 1 2 Introduction The first mutation found to be associated with hypertrophic cardiomyopathy (HCM) is the R403Q mutation in the gene encoding β-myosin heavy chain. R403Q locates in the globular head of myosin (S1), responsible for the actin interaction, hence motor function of myosin. According to the 2-state model of action-myosin interaction total cross-bridge turnover rate can be described by the sum of the cross-bridge association (fapp)and detachment (gapp) rates. Gapp is equivalent to the slow rate of cross-bridge relaxation (slow krel­), which equals the energetic cost of tension generation, i.e. tension cost (expressed by ATP utilization/tension). In the present study we studied to what extent cross-bridge kinetics in HCM with the R403Q mutation correlated with cross-bridge energetics. -1 -1 -2 Tension cost (mmol×L s / kN×m ) Methods & Results 5 Left ventricular multicellular muscle strips and myofibrillar preparations were isolated from 3 HCM patients with the 4 R403Q(1) R403Q mutation. 8 HCM sarcomere mutation-negative (HCMsmn) 3 R403Q(2) patients served as control. In the muscle strips force generating 2 R403Q(3) capacity and ATP utilization were measured to obtain tension HCM smn 1 cost and in the myofibrillar preparations cross-bridge kinetics 0 was analyzed. The fraction of mutated R403Q mRNA was 0.0 0.2 0.4 0.6 0.8 analyzed using specific specific restriction digests and realtimeSlow krel (s-1) PCR.restriction. Compared to HCMsmn tension cost was higher in the muscle strips of the 3 R403Q patients which showed a positive linear correlation with relaxation kinetics in the corresponding myofibrillar preparations (figure). Variation in cross-bridge function among the 3 R403Q patients could not be explained by differences in R403Q mRNA levels. Conclusions Cross-bridge cycling efficiency was decreased in HCM due to the R403Q mutation while crossbridge kinetics was increased. This suggests that the apparent gain in function regarding kinetics leads to a loss off function with respect to cross-bridge cycling efficiency in HCM due to the R403Q mutation. 162 Quality of Care – Safety 153. ‘Am I at risk?’: Understanding how health risk information is (mis)understood N.M.M. Bogaerts1, O.C. Damman1, M.J. van den Haak2 and D.R.M. Timmermans1 Department of Public and Occupational Health, EMGO Institute for Health and Care Research, VU University Medical Center 2 Department of Language and Communication, Faculty of Arts, VU University 1 Introduction Numerous studies have shown that people have difficulty in understanding risk information. To gain more insight into how people interpret risk information, we conducted a qualitative study based on the Dutch online cardiometabolic risk assessment www.testuwrisico.nl. Methods We conducted 16 semi-structured interviews with people between 45 and 65 years. They completed the risk assessment while an eye-tracker registered their visual attention. They were then interviewed for thirty minutes about the risk information they received at the end of the assessment. Data were analyzed by identifying problems in risk interpretation and by comparing eye-gaze patterns. Results We identified several problems related to risk interpretation. One important problem was that people perceived relatively high risks (e.g. 25%) as low. They felt that only extreme risks were reason for worry. People compared their risk to an impossible risk of 100%, and a bar chart visualization seemed to reinforce this. Another problem was that people had problems deriving meaning from the (numerical) risk information. They were interested to compare their risk to that of other people. The test does provide comparative information, but both eye-tracking patterns and people’s verbalizations showed that this information was not optimally used. Conclusions In order to help people derive meaning from health risk information, alternative formats should be developed and tested. One option could be to test different types of risk comparison information (e.g. average risk or lowest possible risk). VU University Medical Center Science Exchange Day 2014 163 Quality of Care – Safety 154. Manual therapy for neck pain? Barriers and facilitators explored Marije F. Dikkers1, Marjan J. Westerman1, Sidney M. Rubinstein1, Maurits W. van Tulder1, Johannes R. Anema2 Department of Health Sciences, VU University Department of Public and Occupational Health, VU University Medical Center 1 2 Introduction Treatment of neck pain with manual therapy (MT) appears more effective and cost-effective than general practitioner (GP) care and physiotherapy (PT). However, referral to MT for neck pain is relatively low. This study was designed to identify the barriers and facilitators for GPs and physiotherapists to refer patients with neck pain to MT. Methods Qualitative explorative study. Semi-structured interviews with GPs (n=13), physiotherapists (n=10), manual therapists (n=7) and their patients with neck pain (n=27). Three focus groups with additional stakeholders (e.g. policy makers) were conducted to validate the interview results. Thematic analysis was used. Results All stakeholders mentioned that it is not clear how MT differs from PT and that there are concerns about adverse effects of MT for neck pain among patients and practitioners. Practitioners emphasized patients’ preferences are prominent in their decision making. Another factor is whether GPs and physiotherapists perceive it is part of their professional role to refer to MT. Both physiotherapists and GPs mentioned that trust in the quality of care provided by manual therapists to patients with neck pain is a facilitator. Finally, GPs and physiotherapists mentioned availability of MT plays a role. Conclusions A number of factors were identified that can stimulate or hinder MT referral in GPs’ and physiotherapists’ neck pain management, such as understanding of the MT domain, professional role orientation, and inter-professional trust. These factors will be addressed in a subsequent project to test a strategy to improve the implementation of MT in neck pain management in primary care. 164 Quality of Care – Safety 155. Changes in error and risk management after CRM training. Results of a controlled study P.F. Kemper, Msc1*, M.C. de Bruijne, MD PhD1, C. van Dyck, PhD2, K.L. So, MD3, P. Tangkau, MD4, C. Wagner, PhD 1,5 Department of Public and Occupational Health, EMGO Institute for Health and Care Research, VU University Medical Center, Amsterdam 2 Faculty of Social Sciences, Department of Organizational Science, VU University, Amsterdam 3 Department of Intensive Care, Albert Schweitzer Ziekenhuis, Dordrecht 4 Department of Intensive Care, Reinier de Graaf Gasthuis, Delft 5 The Netherlands Institute of Health Services Research (NIVEL), Utrecht 1 Introduction Crew Resource Management (CRM) is an increasingly applied method in health care in order to improve patient safety by applying non-technical skills, leading to an optimal use of all resources in the team and their environment. The present study evaluated the effectiveness of CRM in the Intensive Care Unit (ICU). Methods Six ICUs participated in a paired controlled trial, with one pre-test and two post-test measurements (after 3 and 12 months). Three ICUs received CRM training and were compared to a matched control unit. The 2-day classroom-based training was delivered to multidisciplinary groups. All levels of Kirkpatrick’s evaluation framework were assessed using a mixed method design. Results Level I: Participants were very positive directly after the training. Level II: Attitudes towards behaviour to optimise situational awareness were relatively high at baseline and remained stable. Level III: Self-reported behaviour to optimise situational awareness improved in the intervention group. No changes were found in observed explicit professional oral communication. Level IV: Patient outcomes were unaffected. Error management culture and job satisfaction improved in the intervention group. Patient safety culture improved in both control and intervention units. Conclusions Based on the results we can conclude that CRM changes how participants manage errors and risks, as well as increases job satisfaction. Although self-reported behaviour improved, there was no change in explicit professional communication, neither did patient outcomes improve. This is an indication that although CRM provides the fundament for quality improvement, improvements in clinical outcomes require a further implementation of multiple CRM initiatives. VU University Medical Center Science Exchange Day 2014 165 Quality of Care – Safety 156. Regional change in DTI parameters due to upgrade of MRI scanner: effects on TBSS and ROI analysis Petra J.W. Pouwels1, Frederik Barkhof2, Rudolf M. Verdaasdonk1, Joost P.A. Kuijer1 Department of Physics and Medical Technology, Neuroscience Campus Amsterdam, VU University Medical Center 2 Department of Radiology and Nuclear Medicine, Neuroscience Campus Amsterdam, VU University Medical Center 1 Introduction Diffusion tensor imaging (DTI) is used in many neuroradiological protocols. Repeated DTI measurements were prospectively acquired on healthy volunteers before and after an upgrade of a 3T MRI scanner to check for possible systematic variation. Methods DTI acquisition was performed before and after a hardware upgrade of a GE 3T MRI scanner in 13 male healthy subjects (mean age 33.8 ± 8.6 years). Data were processed with FSL, resulting in FA (fractional anisotropy), MD (mean diffusivity), AD (axial diffusivity), and RD (radial diffusivity), followed by TBSS analysis of all parameters. Results Pairwise comparison of repeated measurements before the upgrade did not show significant differences. Pairwise comparison of repeated measurements before and after upgrade (representing a longitudinal study design) showed significant differences in FA, AD, RD, and MD. At tfcecorrected p<0.01, differences were present in >25% of the skeleton, especially located in the body of the corpus callosum. In an unpaired groupwise comparison (representing a cross-sectional study design) still 5% of the skeleton remained significantly different. Bland-Altman plots of values in selected ROIs show that the deviating values only partially scale with mean values of the DTI parameters, while no differences in SNR were observed as a result of the upgrade. Conclusions Quantitative MRI measures as obtained with DTI are sensitive to scanner modifications, even when using the same scanning protocol. This emphasizes the need to include healthy subjects as controls both before and after a scanner upgrade, and to take scanner upgrade into account in the study design. 166 Quality of Care – Safety 157. Actual and preferred place of death as quality indicators for palliative care? De Roo ML1, Miccinesi G.2, Onwuteaka-Philipsen B.D.1, Van Den Noortgate N.3, Van den Block L.4, Bonacchi A.2, Donker G.A.5, Lozano Alonso J.E.6 , Moreels S.7, Deliens L.1,4, Francke A.L.1,5, on behalf of EURO IMPACT Department of Public and Occupational Health, VU University Medical Center, EMGO Institute for Health and Care Research, Amsterdam, The Netherlands 2 Cancer Prevention and Research Institute (ISPO), Florence, Italy 3 Department of Geriatrics, Ghent University Hospital, Ghent, Belgium 4 End-of-life Care Research Group Vrije Universiteit Brussel and Ghent University, Vrije Universiteit Brussel, Brussels, Belgium 5 NIVEL, Netherlands Institute for Health Services Research, Utrecht, The Netherlands 6 Public Health Directorate General, Regional Ministry of Health, Government of Castilla y León, Valladolid, Spain 7 Scientific Institute of Public Health, Public Health and Surveillance, Health Services Research, Brussels, Belgium 1 Introduction Dying at home and at the preferred place of death have been suggested as indicators of highquality palliative care. More insight is needed in their usefulness as quality indicators (QIs). We aim to describe the scores of the existing QIs ‘the percentage of patients dying at home’ and ‘the percentage of patients who died in their place of preference’ and to assess if they are feasible and informative. Methods A mortality follow-back study was conducted, based on registrations from representative GP networks regarding home-dwelling patients (n=3752) who died non-suddenly in Belgium, the Netherlands, Italy and Spain. We assessed relationship between QIs and care characteristics using logistic regression. Results The percentage of home deaths ranged between 35.3% and 50.6% in these countries; whereas 67.8% to 86.0% of patients whose preference was known died at their preferred place. Both QIs were strongly associated with GP palliative care provision (OR 1.55-13.23 and 2.30-6.63). The QI on the preferred place of death offers a broader view than the QI concerning home deaths, considering all preferences met in all locations. GPs did not know the preferences in 39.6% to 70.3%. Conclusions GPs know their patients’ actual place of death, making the percentage of home deaths a feasible QI. However, patients’ preferred place of death was often unknown to the GP. We recommend using information from relatives if information from GPs on the preferred place of death is lacking. Timely communication about where patients want to be cared for remains a challenge for GPs. VU University Medical Center Science Exchange Day 2014 167 Quality of Care – Safety 158. Sport and exercise as markers of health for people with diabetes M.S. Stuij, MSc1, dr. A. Elling-Machartzki2, prof. dr. T.A. Abma1 1 2 Department of Medical Humanities, EMGO+ Institute, VU University Medical Center Mulier Institute Introduction An illness may influence people’s sporting behavior and meanings given to sport and exercise. Our study focuses on narratives around sport, exercise, health and illness of people with diabetes. Methods We developed an exploratory questionnaire for people with diabetes based on qualitative pilot studies. Main topics were (changed) meanings of sport and physical activity and experiences with medical support. Most of the respondents were recruited via the Dutch Diabetes Association. A total of 174 people completed the questionnaire (type 1: 82; type 2: 92). Data were analysed using SPSS. Results Most respondents are quite active in sports and physical activity. The (experienced) positive effects of physical activity on diabetes is an important motivation for both groups. While type 1 diabetics are more intrinsically motivated (pleasure), people with type 2 more often report that the meaning of sport and exercise has changed and that they need external advice and support. In general, most respondents are quite critical about their experienced medical guidance in sport and exercise. Conclusions These (preliminary) results point toward the need for more insight into differences in (changed) meanings and experiences between patients (type diabetes, socio-demographical, sport history) and critical issues in the experiences with medical guidance in continuing or taking up sports and physical activity after diagnosis. 168 Quality of Care – Safety 159. Toward optimal organ at risk sparing in complex radiotherapy treatments: an exponential trade-off with tumor volume dose homogeneity Jim P. Tol, Max Dahele, Patricia Doornaert, Ben J. Slotman, Wilko F.A.R. Verbakel Department of Radiotherapy, VU University Medical Center, Amsterdam Introduction Conventional radiotherapy typically aims for a homogenous dose to the tumor volume (PTV) while sparing nearby organs at risk (OAR). We quantified and characterized the trade-off between PTV dose inhomogeneity (IH) and OAR sparing in complex head and neck plans delivered using a rotational radiotherapy technique. Methods 13 simultaneous integrated boost plans were created per patient, for 10 patients. PTV boost(B)/elective(E) optimization priorities were systematically increased. IHB&IHE, defined as (100%-V95%)+V107% was evaluated against the average of the mean dose to the combined composite swallowing and combined salivary organs (D-OARcomp). To investigate the influence of OAR size and position with respect to PTVB/E, OAR dose was evaluated against a modified Euclidean distance (DMB/DME) between OAR and PTV. Results Excellent logarithmic fits described the D-OARcomp/IHB and IHE relationship in all patients (mean R2=0.98/0.97 respectively). Allowing an increase in average IHB and IHE over a clinically acceptable range, e.g. from 0.4±0.5 to 2.0±2.0% and 6.9±2.8 to 14.8±2.7%, respectively, corresponded to a decrease in average dose to the composite salivary and swallowing structures from 30.3±6.5 to 23.6±4.7Gy and 32.5±8.3 to 26.8±9.3Gy. The increased IHE was mainly accounted for by an increase in V107%, by on average 5.9%. A linear correlation was found between DME and dose to composite swallowing structures and contralateral parotid and submandibular glands (R2=0.83,0.89,0.95). Mean ipsilateral parotid dose correlated with DMB (R2=0.87). Conclusions OAR sparing is highly dependent on the permitted IHB/IHE. IHE substantially influences OAR doses. These results are relevant for clinical practice and for future automated treatment-planning strategies. VU University Medical Center Science Exchange Day 2014 169 Quality of Care – Safety 160. Exploring treatment delays in the care of patients diagnosed with ST-segment elevation myocardial infarction undergoing primary percutaneous coronary intervention: a cross-sectional study Joppe Tra1, Ineke van der Wulp1, Martine C. de Bruijne1, Cordula Wagner1 1 Department of Social Medicine, EMGO+ Institute / VU University Medical Center Introduction A short delay between symptom onset and treatment for patients diagnosed with ST-segment Elevation Myocardial Infarction (STEMI) is vital to prevent cardiac damage and mortality. Therefore, international cardiology guidelines recommend a maximum time span of 90 minutes between first (para)medical contact and percutaneous coronary intervention (PCI). It is unclear whether patients are treated within this recommended time span, and what factors are associated with treatment delays. Methods In a cross-sectional study, the time between first electrocardiogram and start of PCI procedure was measured by means of chart review in seven PCI centres. Patients discharged in 2012 with a diagnosis of STEMI were included in the study. Data were analysed by means of multivariable generalized linear models, accounting for clustering of patients in hospitals. Results In total, 1017 patient charts were included. The majority of the patients (78.6%) were treated within 90 minutes after conducting the first electrocardiogram (median: 64 minutes). Significantly longer delays were found among patients of whom their first electrocardiogram was conducted at the general practitioner (+24 minutes); who had acute heart failure on arrival (+18 minutes); or who were transported between hospitals for PCI (+15 minutes). Conclusions The guideline recommended target for timely treatment of STEMI patients is frequently missed. In optimising the process of care, direct referral to PCI centres is important. To establish this, the general public requires education on sign and symptom recognition of STEMI. Additionally, regional STEMI care networks require strengthening and should include all stakeholders, including emergency departments and general practitioners. 170 Quality of Care – Safety 161. Policy for the return of clinically relevant individual research results by Dutch biobanks Eric Vermeulen1, Martin Boeckhout 2, Rob P.B. Reuzel2, Gerhard A. Zielhuis2, A. Cecile J.W. Janssens3, Marjanka K. Schmidt4 Department of Clinical Genetics, Section Community Genetics, EMGO Institute for Health and Care Research, VU University Medical Center Amsterdam The Netherlands Cancer Institute, Amsterdam 2 Radboud University Medical Center, Nijmegen 3 Erasmus University Medical Center, Rotterdam 4 The Netherlands Cancer Institute, Amsterdam 1 Introduction Biobanks can return ‘actionable’ individual research results to donors. The Dutch Code of Good Conduct, self-regulation for biobanks, provides a guideline. Biobanks are advised to formulate policy for (not) returning individual research results. Methods We performed a literature research, two expert meetings and interviews with biobank representatives. Results The Dutch professional Code of Good Conduct is restrictive towards the feedback of individual research findings. The Code proposes that only clinically relevant, validated and actionable results are fed back and this only if the donor/patient has consented to a return of results. This leaves unanswered the question how to decide about the clinical relevance in individual cases. How results should and could be returned is another problem that biobanks have to decide on. As yet, a few Dutch biobanks have a policy formulated about feedback of research findings and the return of individual research results takes place on an incidental basis. Several biobanks experiment with ways to return results through a portal. Conclusions In order to facilitate the formulation of feasible ‘return of results policies’ biobanks need information concerning how to decide about clinical relevance and how to return results to individual donors. VU University Medical Center Science Exchange Day 2014 171 Grants Desk VU/VUmc Academic research is increasingly becoming dependent on extramural financial support. Many researchers do not make sufficient use of external sources of funding and grants. The Grants desk provides: •Up-to-date knowledge, expertise and capacity to attract appropriate funding; •Grants database; •Advice on national and international grant schemes and funds; •Support of the entire application process; •Assistance in the formation of research consortia. Our priorities and added value: EU grants (Horizon 2020): most money, most potential, and most bureaucracy Talent support (Veni-Vidi-Vici-ERC): coach individuals during preparation of personal grants Grant strategy: strategic advice for individuals and departments The Grants desk team: Dr. Leo Klomp Head grants desk international grants National, European and Guido Leerdam, MA EU-adviser European and international grants Linde van Ittersum, MA Grants adviser National, European and international grants Jeroen van Leur, LL.M Legal adviser Legal advice Drs. Marco Last Grants adviser Personal Grants Dr. Bart Jordi Grants adviser Personal Grants Contact information: Building: Faculty of Medicine, room G-526; Van der Boechorststraat 7-9 T: +31 (20) 444 9923 E: subsidiedesk@vu.nl W: www.intranet.vu.nl/subsidiedesk/ Index Subjectgroup Title of subject Abstract nr./Poster nr. A Animal Models 1-13 B Biomarkers: Clinical 14-25 C Biomarkers: Experimental and Methods 26-41 D Biomedical Engineering 42-55 E Clinical and Epidemiological Surveys 56-80 F Clinical Intervention 81-96 G Clinical – Surveys on Volunteers 97 H Diagnostic Studies – Patients 98-124 I Literature Surveys 125-127 J Preclinical Disease Models 128-152 K Quality of Care – Safety – Auditing 153-161 Nr. of Presenting Title of abstract poster author 56 Aa, H.P.A. van der A way out of depression in the visually impaired: results from a path-analysis E Emgo+ 1 Aarts, E. Extracting gene-behavior relations in mice using Markov modeling on longitudinal automated home cage data A NCA 2 Acar, S. Closer look at the machinery of cilia: Focusing on the steps of IFT kinesins A Laserlab Suppression of the Local Renin-Angiotensin System to reduce Fibrosis J MOVE 128 Akershoek, J.J. Subject Research group Institute 8 Akker, R.F.P. van den Microvascular flow disturbances in a rat model of cardiopulmonary bypass are not caused by hemodilution A ICaR-VU 42 Beekmans, S.V. Measuring the mechanical response of mouse brain tissue with Alzheimer Disease in-vivo D Laserlab 14 Begieneman, M.P.V. Atrial fibrillation coincides with increased intravascular depositions of the advanced glycation end-product Nε-(carboxymethyl)lysine in the atria of the heart B ICaR-VU 129 Bennis, A. Toward stem cell based therapy for diseases affecting the retinal pigment epithelium J NCA 98 Two new adult cases with AUTS2 mutations, including a two basepair deletion, further delineate the AUTS2 syndrome H NCA Beunders, G. 173 Nr. of Presenting Title of abstract poster author Subject Research group Institute 99 Binnerts, J.J. Comparison of quantitative cardiac perfusion measurements using PET and CMR H ICaR-VU 3 Boer, M.P. de AMPK Activation Regulates Microvascular Perfusion and Insulin-mediated Vasoreactivity Through Control Over Endothelin-1 Activity A ICaR-VU 4 Bogaards, S.J.P. MAO-A inhibition reduces basal oxygen consumption and restores isoprenaline sensitivity of hypertrophied rat papillary muscle in vitro A ICaR-VU 153 Bogaerts, N.M.M. ‘Am I at risk?’: Understanding how health risk information is (mis)understood K Emgo+ 26 Broek, E. van den Structural variant breakpoint detection in advanced colorectal cancer C VUmc CCA 57 Burtman, D Preoperative anemia alters the probability of packed red blood cell transfusion in patients undergoing vascular surgery E ICaR-VU 27 Büttler, R.M. Measurement of serum testosterone, androstenedione and dehydroepiandrosterone (DHEA) levels using Isotope-Dilution LiquidChromatography Tandem Mass Spectrometry (ID-LC-MS/MS) C NCA 100 Caanen, M. Anti-Mullerian hormone serum levels decrease in female to male transsexual women using testosterone as cross-sex therapy H NCA 130 Campo, M. del BRI2 protein ectodomain activates critical pathological pathways involved in early stages of Alzheimer’s disease J NCA 131 Campo, M. del SPPL2b is dramatically increased in early stages of Alzheimer’s disease and associates with amyloid plaques and neurofibrillary tangles J NCA 5 Chandrupatla, D.M.S.H. Improvement of an experimental rat model of rheumatoid arthritis for positron emission tomography A VUmc CCA 15 Cohn, M.D. Fear conditioning, persistence of disruptive behavior and psychopathic traits: an fMRI study B Emgo+ 28 Cover, K.S. A standard benchmark for assessing the reproducibility of brain atrophy measures in Alzheimer’s using the ADNI1 data set C NCA 81 Dekker, N.A.M. Microcirculatory changes during goal-directed or mean arterial pressure-guided fluid therapy in abdominal surgery F ICaR-VU 82 Delden, A.E.Q. van Unilateral versus bilateral upper limb training after stroke F MOVE 6 Detiger, S.E.L. Slow BMP-2 release from a fibrin-hyaluronate hydrogel for intervertebral disc regeneration in a large animal model A MOVE Identification of proteins directly interacting with the HELLP-syndrome associated lincRNA using ChIRP J ICaR-VU 132 Dijk, M. van 174 Nr. of Presenting Title of abstract poster author 58 Dijkstra, S.C. The role of perceived barriers in explaining socioeconomic differences in adherence to the fruit, vegetables and fish guidelines in older Dutch adults. E Emgo+ 154 Dikkers, M.F. Manual therapy for neck pain? Barriers and facilitators explored K Emgo+ 83 The first Dutch experience with the use of Strattice™ for single-stage implant based breast reconstruction F MOVE 133 Dooves, S. Vanishing White Matter diseased astrocytes inhibit oligodendrocyte progenitor cell maturation J NCA 34 De novo elucidation of metabolite clusters and their genetically influenced protein‑protein interaction sub‑networks based on a metabolomeand genome‑wide association study C Emgo+ 101 Dreyer, K. Hysterosalpingo-foam sonography (HyFoSy), a new technique to confirm proximal tubal occlusion after treatment of a hydrosalpinx by an Essure® device prior to in vitro fertilization IVF (IVF) H ICaR-VU 102 Eck, A. Altered Proteobacteria Composition in Patients with Acute Uncomplicated Diverticulitis H VUmc CCA 59 Eekhout, I. Longitudinal data analysis with auxiliary item information to handle missing questionnaire data E Emgo+ 84 Eilander, M. Implementation of quality of life in routine paediatric care for adolescents with type 1 diabetes in the Netherlands: An evaluation study F Emgo+ 103 Eken, M.M. Assessing Muscle Endurance in Adolescents with Cerebral Palsy using a Submaximal Repetitions to Fatigue Test H MOVE 134 Emmens, R. C1-esterase inhibitor co-localizes with C3d and C4d and is produced locally in the myocardium after acute myocardial infarction J ICaR-VU 43 Feroldi, F. Endoscopic polarization sensitive optical coherence tomography and in vivo animal lung imaging D Laserlab 29 Funke, U. Preclinical evaluation of [11C]JNJ7777120 as a PET tracer of histamine H4 receptors in the brain C NCA 44 Galgano, G. Dual-channel multi-photon microendoscope for labelfree optical diagnosis of diseases D Laserlab 104 Geest, Q. van The hippocampus in multiple sclerosis: Function, structure and its relation with memory performance H NCA 16 Elevated inflammatory levels in chronic widespread pain: basal inflammation and innate immune response B Emgo+ Compensatory fronto-parietal hyperactivation during set-shifting in unmedicated patients with Parkinson’s disease H NCA Dikmans, R.E.G. Draisma, H.H.M. Generaal, E. 105 Gerrits, N.J.H.M. Subject Research group Institute 175 Nr. of Presenting Title of abstract poster author Subject Research group Institute 125 Gier, B. de Helminth infections and mrconutrients in schoolchildren: a systematic review and metaanalysis I Emgo+ 45 Glas, M. Towards novel antibiotics: targeting the essential bacterial cell division protein FtsQ D AIMMS 60 Grift, T.C. van de Body-image in gender dysphoria; concepts of selfperception & physical appearance revisited for different subtypes E NCA 17 Groen, F.L.M. de Gene-dosage Dependent Overexpression at the 13q Amplicon Identifies DIS3 as Candidate Oncogene in Colorectal Cancer Progression B VUmc CCA 85 Güçlü, A. Beneficial effects of aortic valve replacement on myocardial energetics in aortic valve stenosis patients F ICaR-VU 61 Hamilton, E.M.C. New insights into the spectrum of genotypes and phenotypes in Hypomyelination with Atrophy of the Basal Ganglia and Cerebellum (H-ABC) E NCA 62 Hammerschlag, A.R. Functional Gene-Set Analysis of Attention Deficit/ Hyperactivity Disorder (ADHD) E NCA 63 Hemmen, J. van Mental rotation in women with Complete Androgen Insensitivity Syndrome: an fMRI study E NCA 46 Hermans, K. The effect of medication on fMRI resting state connectivity in focal epilepsy D ICaR-VU 135 Heuvel, O.A. van den Impulse Control Disorders in Parkinson's disease: from preclinical model to prevention and treatment J NCA 86 Heuvel, O.A. van den BEWARE: Body awareness training in the treatment of wearing-off related anxiety in patients with parkinson’s disease F NCA 64 Hoekstra, T. Latent class growth (mixture) models: How do we handle predictors of class membership? E Emgo+ 136 Holmes, D. Generation of iPSCs from patients with 4H syndrome J NCA 65 Psychological posttraumatic growth in head and neck cancer survivors E Emgo+ 137 Horst, E.N. ter Homocysteine induces apoptosis of arterial smooth muscle cells via NOX4-produced reactive oxygen J ICaR-VU 66 Efficacy and safety of intrauterine insemination in patients with moderate to severe endometrisis E ICaR-VU 126 Houwen, L. van der Efficacy of intrauterine insemination in moderate to severe endometriosis. A systematic review and meta-analysis of observational data I ICaR-VU 67 E Emgo+ 176 Holtmaat, C.J.M. Houwen, L. van der Huppertz, C. The dopaminergic reward system and leisure time exercise behavior: A candidate allele study Nr. of Presenting Title of abstract poster author 47 Huseinovic, A. A yeast genome-wide screen uncovers roles for chromatin modifications and ubiquitin homeostasis in acetaminophen toxicity. D AIMMS 30 Jager, A.M. de The blood-derived transglutaminase Factor XIII forms complexes with Aβ and is both present and catalytically active in Aβ deposition in cerebral amyloid angiopathy C NCA 138 Janssen, R. MicroRNA-214 controls thyroid hormone levels by targeting Dio3 in the post-MI heart J ICaR-VU 106 Johannesma, P. Birt-Hogg-Dubé syndrome patients with and without pneumothorax: findings on chest CT H VUmc CCA 108 Johannesma, P. Clinical cases; Spontaneous pneumothorax at the age of 14. Radiological evidence of Birt-HoggDubé syndrome H VUmc CCA 109 Johannesma, P. Primary Spontaneous Pneumothorax: a pilot study on the frequency of FLCN mutation (Birt-HoggDubé syndrome) H VUmc CCA 107 Johannesma, P. Chest CT for primary spontaneous pneumothorax (PSP): findings: Birt-Hogg-Dubé versus non-BirtHogg-Dubé patients H VUmc CCA 139 Joureau, B. Diaphragm muscle weakness in a novel mouse model for nebulin-based nemaline myopathy J ICaR-VU 48 Kamsma, D. Single-molecule Acoustic Pushing (smAP!): Manipulating single-molecules with ultrasound D Laserlab 97 Kan, K.J. Cognitive functioning and blood pressure as a function of age G NCA 7 Kedar, G.H. A post docking role of the Synaptotagmin1-C2B base domain A NCA 155 Kemper, P.F. Changes in error and risk management after CRM training. Results of a controlled study K Emgo+ 110 Kevelam, S.H. Novel (ovario)leukodystrophy related to AARS2 mutations H NCA 49 Klaessens, J.H.G.M. Development of a baby friendly non-contact method for measuring vital signs, first results of clinical measurements in an open incubator on a Neonatal Intensive Care Unit D ICaR-VU 8 Koning, N.J. Microvascular flow disturbances in a rat model of cardiopulmonary bypass are not caused by hemodilution A ICaR-VU 140 Kooi, E.I. Copy number profiling of human and murine retinoblastoma J VUmc CCA 31 Recommendations on study design and data analysis for differential gene expression using RNA-seq C VUmc CCA Brain activation patterns reflect quality of motor control of the paretic upper limb after stroke H MOVE Kooi, E.I. 111 Kordelaar, J. van Subject Research group Institute 177 Nr. of Presenting Title of abstract poster author Subject Research group Institute 50 Krumpochova, P. LC-MS based metabolomics as a tool for studying the Warburg effect. D AIMMS 9 Kuzmin, N.V. Lipid membranes, oxidative stress and amyloidbeta: Alzheimer’s disease triggering and imaging with multimodal laser-scanning microscopy A NCA 10 Laarse, W.J. van der Numbers of intrinsic cardiac adrenergic cells in rat heart: effect of hypertrophy A ICaR-VU 32 Labots, M. Less is enough: scaling down protein input for phosphoproteomics based treatment selection in patients with advanced solid tumors C VUmc CCA 11 Lagerweij, T. 3D imaging of brain tumors A VUmc CCA 141 Leferink, P. Towards a stem cell transplantation therapy for VWM J NCA 68 Ligthart, L. Prevalence and comorbidity of pain symptoms in the general population E Emgo+ 87 Loon, A. van Effectiveness of an intercultural module: drop-out and no-show rates in non-Western migrants with affective disorders. F Emgo+ 18 Luttmer, R. Human papillomavirus in sperm of healthy young men B VUmc CCA 33 Malekzadeh, A. Discovery of biomarkers reflecting progression pathophysiology for relapse remitting and primary progressive MS subtypes by applying novel multiplex aptamer approach C NCA 112 Manders, E. Diaphragm dysfunction in pulmonary arterial hypertension patients H ICaR-VU 113 Marcus, J.T. Contrast-Enhanced MRI as method to monitor response to anti-angiogenic therapy H ICaR-VU 114 Meijer, J.H. Non-invasive assessment of the speed of cardiac contraction H ICaR-VU 142 Mijalkovic, J. Quantification of IFT-dynein dynamics in C. elegans J Laserlab 19 Möller, C. Basal nuclei are more severely atrophic in behavioral variant Frontotemporal Dementia compared to Alzheimer’s Disease B NCA 69 Mous, S.E. Cortical Thickness and Inattention/Hyperactivity Symptoms in Young Children- The Generation R Study E NCA 143 Nadadhur, A.G. Neuronal differentiation of iPS cells for disease modeling J NCA 88 Nassau, F van Implementation index: an indicator measuring level of implementation of school-based interventions. F Emgo+ 51 Nauta, T. Chronic hypoxia-enforced inhibition of vascularization; Involvement of HIF1α and HIF2α D ICaR-VU 178 Nr. of Presenting Title of abstract poster author 52 Nelemans, B. The Forces that Shape our Spine: Mechanics in Somitogenesis D MOVE 70 Neter, J.E. Dietary intake of Dutch food bank recipients E Emgo+ 89 Nielsen, K. Ablation of colorectal liver metastases by irreversible electroporation: results of the COLDFIRE-I ablate-and-resect study F VUmc CCA 115 Noij, D.P. Predictive value of diffusion-weighted imaging without and with contrast-enhanced magnetic resonance imaging in head and neck squamous cell carcinoma H VUmc CCA 90 The structure of the geriatric depressed brain and response to electroconvulsive therapy F NCA 135 Pattij, T. Impulse Control Disorders in Parkinson's disease: from preclinical model to prevention and treatment J NCA 144 Peferoen, L.A.N. Microglia phenotyping in pre-active MS lesions J NCA 12 Persoon, C.M. Neuropeptide secretion in the brain: Insights into dynamics of dense-core vesicles A NCA 71 Plas, A. van der Palliative care case management in primary care: A descriptive study about the flexibility, duration and content of care. E Emgo+ Endothelial AMPK_2 regulates whole body glucose uptake J ICaR-VU Oudega, M.L. 145 Poelgeest, E. van Subject Research group Institute 72 Pols-Vijlbrief, R. van Determinants of Undernutrition in Older Adults der receiving Home Care E Emgo+ 34 Pool, R. De novo elucidation of metabolite clusters and their genetically influenced protein‑protein interaction sub‑networks based on a metabolomeand genome‑wide association study C Emgo+ 156 Pouwels, P.J.W. Regional change in DTI parameters due to upgrade of MRI scanner: effects on TBSS and ROI analysis K NCA 20 Rain, S. Altered β-Adrenergic Receptor Signaling Contributes to the Development of Right Ventricular Diastolic Dysfunction in Pulmonary Arterial Hypertension B ICaR-VU 73 Rainey, J.F.M. Measurement properties of questionnaires assessing participation in children and adolescents with a disability: a systematic review E Emgo+ 91 Rappard, D.F. van Hematopoietic stem cell transplantation for Metachromatic Leukodystrophy F NCA 146 Rauh, S.P. Predicting Glycated Haemoglobin in the NonDiabetic General Population: a DIRECT Study J Emgo+ 157 Roo, M.L. de Actual and preferred place of death as quality indicators for palliative care? K Emgo+ 147 Roos, S.T. In Vitro Sonothrombolysis in Whole Blood for Myocardial No-reflow J ICaR-VU 179 Nr. of Presenting Title of abstract poster author Subject Research group Institute 35 Rosenberger, A.F.N. Protein kinase activity profiling of patients with Alzheimer’s Disease and non-demented controls reveals pathway changes C NCA 36 Ruiz-Zapata, A.M. Substrate surface alter mechano-responses of vaginal fibroblasts from prolapsed tissues in premenopausal women with pelvic organ prolapse C MOVE 74 Rutten, S. Anxiety in Parkinson’s disease: mind = body? E NCA 75 Rutters, F. The association between psychosocial stress and mortality is mediated by lifestyle and chronic diseases: the Hoorn Study E Emgo+ 116 Scheltens, N.M.E. Cognitive Subtypes in Alzheimer Disease defined by Latent Class Analysis H NCA 13 Schippers, M.C. Deep brain stimulation of the nucleus accumbens core affects heroin seeking and impulsivity in rats A NCA 76 Schooten, K.S. van The quantity and quality of daily activities in relation with fall history and future falls in older adults E MOVE 77 Schutte, N.M. A twin-sibling study of components of adolescent physical fitness E Emgo+ 117 Sloot, L.H. Perturbations during treadmill walking offer oppor-tunities for functional assessment of ankle stiffness H MOVE 37 Smit, B. Quantitating neutrophil oxidative stress by Flow Cytometry C ICaR-VU 78 Spriensma, A.H. Two-part joint regression modeling to analyze longitudinal left censored patient reported outcomes E Emgo+ 118 Spruijt, Q.A. The coupling of the right ventricle to its load during exercise in pulmonary hypertension H ICaR-VU 79 Stam, H. Predictors of dizziness in older persons: a 10-year prospective cohort study in the community E Emgo+ 21 Strooper, L. de Triage of high-risk HPV-positive women by combined cytology and methylation marker analysis: complementary clinical performance B VUmc CCA 158 Stuij, M.S. Sport and exercise as markers of health for people with diabetes K Emgo+ 80 The sex, age, and cognitive domain dependent associations between regular voluntary exercise behavior and cognitive functioning E NCA 148 Szulcek, R. The micro- but not macro-vascular lung endothelium of pulmonary arterial hypertension patients shows a defective adaptation to high fluid shear stress J ICaR-VU 149 Thulluru, H.K. Expression of CORIN and STOX2 and their effect on NODAL in the first trimester fetal placenta J ICaR-VU 180 Swagerman, S. Nr. of Presenting Title of abstract poster author 159 Tol, J.P. Toward optimal organ at risk sparing in complex radiotherapy treatments: an exponential trade-off with tumor volume dose homogeneity K VUmc CCA 160 Tra, J. Exploring treatment delays in the care of patients diagnosed with ST-segment elevation myocardial infarction undergoing primary percutaneous coronary intervention: a cross-sectional study K Emgo+ 119 Trujillo, J.P. Altered neural connectivity during an n-back task in unmedicated Parkinson´s disease patients H NCA 22 Triaging borderline/mild dyskaryotic Pap cytology with p16/Ki-67 dual-stained cytology testing: cross-sectional and longitudinal outcome study B VUmc CCA 150 Valent, E.T. Traction force microscopy: a study of the endothelium during thrombin-mediated contractility J ICaR-VU 127 Veerbeek, J.M. What is the evidence for physical therapy poststroke? A systematic review and meta-analysis I MOVE 120 Veldhuijzen van Zanten, S.E.M. Innovative Molecular Drug Imaging: Pioneering Work in Children H VUmc CCA 23 Velzen, L.S. van Brain-derived neurotrophic factor and regional brain volume B NCA 38 Verbeek, J. (Z)-2-(4-[18F]fluoro-2-oxoindolin-3-ylidene)-N-(4methoxyphenyl)hydrazine carbothioamide is an aberrant P-gp tracer C NCA 53 Verdaasdonk, R. Quantification of air flows produced by medical equipment disturbing the clean air in the field of surgery using large field background subtraction imaging D NCA 121 Verduijn, J. Clinical Staging of Major Depressive Disorder: an empirical exploration H Emgo+ 92 Verhagen, H. The therapeutic potential of IGFBP7 in specific eradication of leukemic stem cells in acute myeloid leukemia F VUmc CCA 24 Verlaat, W. Genome-wide DNA methylation profiling reveals novel biomarkers for early detection of cervical cancer B VUmc CCA 161 Vermeulen, E. Policy for the return of clinically relevant individual research results by Dutch biobanks K Emgo+ 54 Parallel scanning laser ophthalmoscope (PSLO) for retinal imaging D Laserlab 151 Vogel, D.Y.S. GM-CSF stimulation of monocytes enhances migration over endothelial cells J NCA 55 AFM nanoindentation reveals mechanical properties of extracellular vesicles from Red Blood Cells D laserlab Functional deficits in response inhibition in de novo Parkinson’s disease H NCA Uijterwaal, M.H. Vienola, K. Vorselen, D. 122 Vriend, C. Subject Research group Institute 181 Nr. of Presenting Title of abstract poster author Subject Research group Institute 39 Vries, H.M. de Large lactate clearance shifts in the first 8 hours after traumatic brain injury are associated with increased mortality C ICaR-VU 93 Waard, G. de Hyperemic and Hyperemia Free Pressure Indices have an Equivalent Diagnostic Accuracy when Compared to Myocardial Blood Flow Quantified by H215O PET Perfusion Imaging F ICaR-VU 94 Wee, M. ter Intensive combination treatment regimens, including prednisolone, are effective in treating early rheumatoid arthritis patients regardless of additional etanercept: 1 year results of the COBRAlight trial F VUmc CCA 86 Wegen, E.E.H. van BEWARE: Body awareness training in the treatment of wearing-off related anxiety in patients with parkinson’s disease F NCA 95 Wierenga, D The evaluation of a worksite intervention to promote a healthy lifestyle among employees in two different organizations F Emgo+ 40 Wildt, B. van der Synthesis of a 11C-labeled tissue transglutaminase inhibitor using a [11C]CO carbonylation reaction C NCA 123 Winter, J.M. de Force-sarcomere length relations in patients with thin filament myopathy caused by mutations in NEB, ACTA1 and TPM3 H ICaR-VU 124 Winters, C. Is capacity for upper extremity motor recovery fixed after a first-ever ischemic stroke? H MOVE 41 Colorectal cancer candidate biomarkers identified by tissue secretome proteome profiling C VUmc CCA 152 Witjas-Paalberends, Faster cross-bridge relaxation rates correlate with E.R. increased tension cost in HCM with the R403Q MYH7 mutation J ICaR-VU 96 Zwan, J.E. van der Stress reduction through mindfulness meditation, heart rate variability biofeedback or physical activity: a randomized trial F Emgo+ 25 Zwan, M.D. Diagnostic Value of Amyloid Imaging in Early Onset Dementia B NCA 182 Wit, M. de Vormgeving: Gerda Lieftink, DPC VUmc 184