Workshop Biostatistics in relationship testing ESWG-meeting 2014 Daniel Kling Norwegian Institute of Public Health and Norwegian University of Life Sciences, Norway Andreas Tillmar National Board of Forensic Medicine, Sweden http://www.famlink.se/BiostatWorkshopESWG2014.html Outline of this first session • Likelihood ratio principle • Theoretical: paternity issues – Calculation of LR “by hand”. – Accounting for: • • • • Mutations Null/silent alleles Linkage and linkage disequilibrium (allelic association) Co-ancestry DNA-testing to solve relationship issues Is Mike the father of Brian? DNA-data vWA D12S391 D21S11 …. 12,13 22,22 31,32.2 …. Mother of Brian: 12,14 23,23.2 30,30 …. Brian: 22,23 30,31 …. Mike: 13,14 Can we use the information from the DNA-data to answer the question? YES! We estimate the “weight of evidence” by biostatistical calculations. We How will follow recommendations given much the more (or less) probable is it by thatGjertson M is theet al., 2007 father of B, compared to being the in father of B? testing.” “ISFG: Recommendations onnot biostatistics paternity Calculating the “Weight of evidence” in a case with DNA-data H1: The alleged father is the father of the child H2: The alleged father is unrelated to the child We wish to find the probability for H1 to be true, given the evidence = Pr(H1|E) Via Baye’s theorem: Pr( H 1 | E ) Pr( H 2 | E ) Posterior odds Today we focus on the likelihood ratio (LR) Pr( E | H 1 ) Pr( H 1 ) Pr( E | H 2 ) Pr( H 2 ) LR (or PI) Pr( DNA | H 1 ) Pr( DNA | H 2 ) Prior odds LR= Pr( DNA | H 1 ) Pr( DNA | H 2 ) Pr( DNA | H 1 ) Pr( DNA | H 2 ) M AF GM GAF C Founders Genotype probabilities Child Transmission probabilities Assuming HWE 2*pi*pj*(1-Fst) Fst*pi+ (1-Fst)*pi*pi 2*pi*pj pi*pi Mendelian factor (1, 0.5, µ, etc) GC Pr( DNA | H 1 ) Pr( G C , G AF , G M | H 1 ) Pr( G C | G AF , G M , H 1 ) Pr( G AF , G M | H 1 ) Paternity trio – An example |, H )1 )G ,Pr( GGCAFDNA ,G , |GG |, H G | ,HG ) )|H )1 )G GCPr( , G|GG , |G ,GGMM| ,H )G Pr( |G ,G GAFAF , ,G |G HMM1 )|, H 1 ) Gr(CDNA ,Pr( G AFDNA G M1 )| H |H1Pr( Pr( Pr( ,Pr( H1Pr( ,G |,G H1M)1 ),HPr( C AF MAF M 1 1M C AFC AF MAF 1 C AF M C AF 1 M AF GM=a,b GAF=c,d 2,|G p|McAF pGG )Pr( Pr( DNA Pr( G C|DNA ,H G1AF ) |, H GPr( )G |H Pr( Pr( ,G )G DNA Pr( ,,G GG | H|, H |G)G) |Pr( ,HG Pr( G) G ,,HG Pr( | )GG,Pr( G G G H,, ,H ) ) |,Pr( Pr( H 1GG ) CAF Pr( |G ,G GAFMAF, G |, H G ,)H| 0.5 M 1 C 1 AFC MAFC 1 1MAF2 p 1Ma C Cp 1b AF AF C M AF 1 d1MM 0.5 M 1M C GC=a,c M AF GM=a,b 1 GAF=c,d Pr( DNA | H 1 ) p,cG MpAFd |, H 2,|G pAF pGGd1MM) |, Pr( )Pr( Pr( DNA Pr( G C|DNA ,H G1AF ) |, H GPr( )G |H Pr( ,G )G AFCPr( ,,G G|G |, H |GG ) |,HG Pr( )G ,HPr( | )GGPr( G G H 1G )2AF Pr( G G 1M) | Pr( 0.5 cAF,, ,H M 1 C 1 DNA MH AFC 2 ) 1MAF2 p 1Ma Cp 1b AF C M C GC=a,c Paternity trio – An example Gr(C|DNA ,H G AF GPr( |HPr( Pr( )G DNA Pr( |H | )G |Pr( ,H ,,HpG G2,M|G H, 1pGG )dM) |,Pr( H )) C Pr( |G , H ) Pr( G A G p1G p|AF A ) |, H )G ,1 G ,,G GG |, H Pr( )a CG Pr( | )GG,Pr( G G Pr( H 11GG ,G GAFMAF, G |, H G M 1G)1M)AF2 M M 1M) | 1H 1 ) cAF, ,H 0.5 1 1 C Pr( AF C MAF C 1b AF AF C M 1 M 0.5 AF DNA | CH LR= = 1 p,cG MpAFd |, H 2,|G pAF pGGd1MM) |, Pr( NA Pr( G C|DNA ,H G1AF ) |, H GPr( )G |H Pr( ,G )G AFCPr( ,,G G|G |, H |GG=) |,HG Pr( )G ,HPr( | )GGPr( G G H 1G )2AF Pr( G G 1M) | H 1 ) Pr( 0.5 cAF,, ,H M 1 C 1 DNA MH AFC 2 ) 1MAF2 p 1Ma Cp 1b AF C M 0.5 =2 p c p d Probability to observe a certain allele in the population (e.g. population frequency) pC xc 1 N 1 Paternity trio – real data M AF GM=10,11 1 GAF=13,14.2 )Pr( Pr( DNA Pr( G C|DNA ,H G1AF ) |, H GPr( )G |H Pr( ,G )G AFCPr( ,,G G| G |, H |GG1M)AF )G ,G HPr( | )GGPr( G ,, ,H GG14 ).Pr( HG1 G ) |Pr( G GM,AFG|,MH G, 1MH) 1| 2CM,|G pG Pr( H Pr( G | 13 H G, AF 2|,HGPr( p110 0.5 0.5 M 1 C 1 DNA M AFC1 ) M 111 ,G AF AF MAF1 )p 1MM 2|, Pr( C CpAF C AF C GC=10,14.2 M AF GM=10,11 Pr( DNA | H 1 ) GAF=13,14.2 H 1 )Pr( Pr( DNA G C| ,H G1AF ) , GPr( G |H ,G ) AF Pr( , G| G | G1 )AF | )G Pr( G ,, H G 1M2 H ) AF 2 ,G p13AF p131 G p14, .G2 M | H 1 ) Pr( HC|2 )H 2, GPr( p10M G, HCp11 0.5 M C 1 DNA M 1 AF M p14 .)2 | Pr( C GC=10,14.2 0.5 LR= 2 p13 p14.2 Paternity trio - Mutation M AF GM=10,11 GAF=13,15.2 Mutation? G Ar(C |DNA ,H G 1AF) | ,CG HPr( ) |G HPr( Pr( , )G GAFCPr( ,,G G|G |,|H GG )2Pr( |,H G Pr( )G ,G Hp Pr( |)G GPr( G ,G ,HG15 )2|, Pr( H HG11)G ) | Pr( G, G|, H G, H) | )H Pr( ) G AF 2CM,|G pG pG H | AF H G, G 0.5 M 1 C 1 DNA M AF C 1 ) 1MAF 1 M C AF 1 ,G AF MAF1 )p M 1 M.Pr( 1 13 10 11 C C AF AF MAF M 1M 1 GC=10,14.2 Mutations “The possibility of mutation shall be taken into account whenever a genetic inconsistency is observed” Brinkmann et al (1998) found 23 mutations in 10,844 parent/child offsprings. Out of these 22 were single step and 1 were two-step mutations. AABB summary report covering ~4000 mutations showed approx 90-95% single step, 5-10% two-step and 1% or less more than two steps. Note that these are the observed mutation rate, not the actual mutation rate (hidden mutations, assumption of mutation with the smallest step. Mutation rate depend on marker, sex (female/male), age of individual, allele size Mutations cont Allele: 9 10 11 -3 -2 -1 µ-3 µ-2 µ-1 12 0 1- µtot 13 14 15 +1 +2 +3 µ+1 µ+2 µ+3 µtot=µ+1+µ-1+µ+2+µ-2+….. Approaches to calculate LR accounting for mutations: LR~(µtot*adj_steps)/p(paternal allele) e.g “stepwise mutation model” LR~µ/A (A=average PE) LR~µ LR~µ/p(paternal allele) Paternity trio - Mutation M AF GM=10,11 ( mut 13 14 .2 mut 15 .2 14 .2 ) GAF=13,15.2 C Mutation model decreasing with range ( mut 13 14 .2 mut 15 .2 14 .2 ) GC=10,14.2 Total mutation rate mut 15 .2 14 .2 “Stepwise decreasing with range” 0 .5 µ Tot 50% for 15.2 to be transmitted 50% are loss of fragment size 0 .9 0 .5 90% of mutations are 1 step Paternity trio - Mutation M AF GM=10,11 GAF=13,15.2 (Gmut )mut ) G Ar(C |DNA ,H G 1AF) | ,CG HPr( ) |G H Pr( , )G GAFCPr( ,,G G |,|H GG )2 |,H G ) ,G |)G GPr( G ,H |, Pr( H HG11C)G ) |AF Pr( ,AF G G13,MAF |M, H | H 1.2) 14G.2AF pPr( GHpCPr( 2CM,|G p|G13 , )G pG Pr( |G H Pr( G H 15M1 M).Pr( G 14 .G 2 , 1H M 1 C 1 DNA M AF C1 ) 1MAF 1 M 1 ,G AF AF MAF M 1 ) 15Pr( 10 11 2 0.5 C AF 1 mut 15 .2 14 .2 GC=10,14.2 M 0 .5 µ Tot 0 .9 0 .5 AF Pr( DNA | H 1 ) GAF=13,15.2 GM=10,11 H 1 )Pr( Pr( DNA G C| ,H G1AF ) , GPr( G |H ,G ) AF Pr( , G| G | G1 )AF | )G Pr( ,G G AF ,, H G )2 | Pr( H ) AF p131 G p14, .G2 M | H 1 ) 2, GPr( p10M G, HCp11 Pr( HC|2 )H 0.5 M C 1 DNA M 1 2 AF p 13 M p 151M.2 C t 15 .2 14 .2 GC=10,14.2 0 .5 µ Tot LR= 0 .9 0 .5 2 p13 p14.2 Paternity trio – Silent allele M AF GM=10,11 GAF=17.2 C GC=10 ,s ,s GAF=17.2,17.2 GC=10,10 GAF=17.2, s GC=10,s Null/silent allele “STR null alleles mainly occur when a primer in the PCR reaction fails to hybridize to the template DNA...” “Laboratories should try to resolve this situation with different pairs of STR primers” “…no data from which to estimate the null allele frequency exists, consider a generous bracket of plausible values for the frequency and compute a corresponding range of values for the PI. If the resulting range of case-specific PI values are all large (as large as a laboratory’s threshold value for issuing non-exclusion paternity reports), then report that the PI is ‘‘at least greater than the smallest value’’ in the range” Impact of null/silent allele may vary on the pedigree and the genotype constellations Paternity trio – Silent allele M AF GM=10,11 GAF=17.2 GAF=17.2,17.2 GC=10,10 GAF=17.2, s GC=10,s Pr( DNA | H 1 ) 2Pr( , G | H ) Pr( G C | 0G. 5AF , G M , H 1 ) Pr( G AF pG10C ,GpAF 11 2M p 17 1.2 p s 0 . 5 C GC=10 M AF GM=10,11 C G =17.2 Pr( DNA AF | H1) Pr( DNA | H 2 ) GC=10 LR= 2 p10 p11 ( 2 p 17 .2 p s p 17 .2 p 17 .2 ) 0 . 5 ( p 10 p s ) 2 p 17 .2 p s 0 . 5 0 . 5 ( 2 ( p217 .2p 17 .p2 s p s p17 .2p 17 .p2 17 .2p)17.20). 5 0 .(5p10( p10 ps )p s ) Linkage and Linkage disequilibrium • Linkage – Can be described as the co-segregation of closely located loci within a family or pedigree. – Effects the transmission probabilities! • Linkage disequilibrium (LD) – Allelic association. – Two alleles (at two different markers) which is observed more often/less often than can be expected. – Effects the founder genotype probabilities, not the transmission probabilities! Marker 1 Marker 2 Mother: 16,18 21,24 If LD, different probabilities for each phase Chr3:1 Chr3:2 16 Chr3:1 Chr3:2 18 18 16 21 24 Distance R, Theta 21 24 If linkage, different probability of transmission 18 16 18 16 21 21 24 24 Mother: 16,18 21,24 Child1: 16,25 21,29 Child2: 16,22 24,30 Chr3:1 Chr3:2 Chr3:1 Chr3:2 16 25 paternal 25 16 21 29 paternal 21 29 Chr3:1 Chr3:2 Chr3:1 Chr3:2 16 22 paternal 22 16 24 30 paternal 24 30 Linkage and LD when it comes to forensic DNA-markers? • 14 pair of autosomal STRs < 50cM – Phillips et al 2012 – vWA-D12S391 (around 10cM, i.e. 10% recomb rate) • Linkage will have an effect on LR for some pedigrees – – – – Gill et al 2012, O’Connor & Tillmar 2012, Kling et al, 2012. Incest. Sibling, uncle-nephew. Impact of linkage will depend on • Pedigree • Markers typed • Individuals’ DNA data • LE for vWA-D12S391! – Gill et al 2012, and O’Connor et al 2011. Linkage cont. • Assuming LE (no allelic association) – Gill et al 2012: "...linkage has no effect at all in a pedigree unless: • at least one individual in the pedigree (the central individual) is involved in at least two transmissions of genetic material…, and • that individual is a double heterozygote at the loci in question." • Thus… – For standard paternity cases (father vs unrelated), linkage has no impact on LR – BUT for paternity vs uncle (or other close related alternative), linkage has impact on LR Presenting the evidence • Likelihood ratio (LR) or Paternity index (PI) • Posterior probability (must set priors) Li=Likelihood under hypothesis i πi=Prior probability for hypothesis i Simplifies to LR/LR+1, assuming two hypotheses with equal priors Subpopulation correction What is subpopulation effects? First developed by Wright in (1965) Balding (1994) Hardy Weinberg equilibrium How to estimate it? Reasonable values (0.01-0.05) Sampling formula (Fst = θ) p '( a i ) F st * n a i (1 F st ) * p ( a i ) 1 ( N O bs 1) * F st 24 Example 1. Genotype probabilities HWE Homozygouts: p(A)p(A) Heterozygots: 2p(A)p(B) HWD Homozygouts: Fst*p(A) + (1-Fst)*p(A)p(A) Heterozygouts: (1-Fst)*p(A)p(B) P ( A , A ) P (Sam pling tw o A:s)= * 0 (1 ) p ( A ) *1 (1 ) p ( A ) * 1 (0 1) P ( A , B ) P (Sam pling one A and one B)= 1 (1 1) p ( A ) (1 ) p ( A ) * 0 (1 ) p ( A ) * 0 (1 ) p ( B ) 1 (0 1) 25 * 1 (1 1) 2 (1 ) p ( A ) p ( B ) Example 2. Random Match Prob. H1: The profiles G1 and G2 are from the same individual H2: The profiles G1 and G2 are from different individuals Let G1=A,A and G2=A,A HWE: P ( D ata | H 1 ) 1 / RM P P ( D ata | H 2 ) P ( G 1) P ( G 1) * P ( G 2) 1 p ( A) 2 HWD: 1 / RM P P ( D ata | H 1 ) P ( D ata | H 2 ) P ( G 1) Sam pling P ( G 1, G 2) (1 )(1 2 ) 2 (1 ) p ( A ) 3 (1 ) p ( A ) 26 P (S am pling tw o A :s) P (S am pling four A :s) Example 3. Paternity H1: The alleged father (AF) is the real father H2: AF and the child are unrelated. p(A) = 0.05 Standard paternity case. First marker AF A/A mother B/B child A/B 27 Standard paternity case. First marker AF A/A mother B/B child A/B LR probability of data given A F father probability of data given A F unrelated P ( child | m other , A F ) 0 P ( child | m other ) LR 1 pA P ( m other ) P ( A F ) P ( child | m other , A F ) 1 0 P ( A F ) P ( m other ) P ( child | m other ) 1 P (S am pling the third A ) 1 2 (1 ) p A 20. 0.05 P (S am pling tw o A :s and tw o B :s) P (S am pling three A :s and tw o B :s) 1 (4 1) 28 1 3 2 (1 ) p A LR P ( m other ) P ( A F ) P ( child | m other , A F ) 0 P ( A F ) P ( m other ) P ( child | m other ) 1 P (S am pling the third A ) 1 2 (1 ) p A 1 (4 1) P (S am pling tw o A :s and tw o B :s) P (S am pling three A :s and tw o B :s) 1 3 2 (1 ) p A LR as a function of Theta 25 20 LR 15 10 5 0 0 0.05 0.1 0.15 Theta 0.2 0.25 29 0.3 Example 4. Siblings H0: Two persons are full siblings H1: The same two persons are unrelated The two persons are homozygous A,A (p(A)=0.05) We use the “IBD method” LR P ( D ata | H 0) 0 P ( D ata | H 1) P (S am pling tw o A :s)*P (IB D = 2|H 0)+ P (S am pling three A :s)*P (IB D = 1|H 0)+ P (S am pling four A :s)*P (IB D = 0|H 0) P (S am pling four A :s) 0.25 0.5 P (S am pling the third A ) 0.25 P (S am pling the last tw o A :s) P (S am pling the last tw o A :s) 0.25 0.5 2 (1 ) p A 0.25 1 (2 1) 2 (1 ) p A 1 (2 1) * 2 (1 ) p A 1 (2 1) 3 (1 ) p A * 3 (1 ) p A 1 (3 1) 1 (3 1) 30 Example 4. Siblings LR as a function of Theta 120 100 LR 80 60 40 20 0 0 0.05 0.1 0.15 Theta 31 0.2 0.25 0.3 Example 5. General relationships We have N number of founder genotypes If Fst!=0 these are not independent We use the sampling formula to calculate updated allele frequencies It is more complex to do by hand In simple pairwise relationships use the IBD method (See Example 4) Otherwise, use validated software! 32