Hyperthyroidism Defintion THYROTOXICOSIS Increased thyroid hormone levels with biological effects on tissues and systems HYPERTIROIDISM Hyperfunction of thyroid gland History Have described different forms of hyperthyroidism Parry (1786), Flajani (1808), Graves (1835), Basedow (1840), Moebius (1886), Plummer (1913 – adenomul toxic), Adams, Purves, Mc Kenzie (1956 – long-acting thyroid stimulator immunoglobulins – LATS) Thyrotropic axe TRH piytuitary II- I2 TSH MIT T T44 fT fT44 T4 DIT T T33 fT fT33 T3 thyroglobulin II-- TBG HYPERTIROIDISM Etiolology : incidence Autonomic - >40 ani - b=f other (< 1%) Graves disease - < 40 ani - f / b = 10 / 1 HYPERTIROIDISM Most frequent forms Basedow-Graves disease Toxic adenoma Plummer Toxic multinodular goiter TSH TSH TSH T4 T4 T4 Hypertiroidism – etiology A. tirotoxicosis with hyperthyroidism 1. Thyroid stimulation TSI Graves disease TSH thyrotropinoma Resistance to thryoid hormone action Refetoff syndromes Human Chorionc Gonadotropin Trophoblastic tumors hiperemesis gravidarum 3. Iodine induced 2. Autonomous thyroid function Toxic adenoma Toxic multinodular goiter Non-autoimmune difuse hyperthyroidism(familiala, sporadic?) Thyroid carcinoma follicular struma ovarii Jod-Basedow Iodine contrast media, amiodarone (thyroid excess and autonomous thyroid function) Hypertiroidism - etiology B. Thyrotoxicosis without hyperfunction of the thyroid gland 4. Distruction thyroiditis subacute de Quervain thyroiditis Silent thyroiditis Drug induced (amiodarone, interferon-alfa) Irradiation, 5. External intake Iatrogenic Factitia foods (« hamburger thyrotoxicosis ») HYPERTIROIDISM / THYROTOXICOSIS signs and symptoms Simptoms due to increased number of cathecolamine receptors Simptoms due to metabolic actons of thyroid hormones palpitation (tachicardia, atrial fibrilation) Increasd perspiration tremor , hiperreflexia, eyelids retraction Weight loss with increased appetite , decreased fat and muscle mass termofobia Warm skin, fine, moist; onicholisis Muscle weakness, osteoporosis Menstrual problems in women and gynecomastia in men Simptoms induced by thyrpid hormone effects on central nervous system Nervousness , irritability, psychological labillity, Clinical signs 33 35 54 65 70 75 82 85 88 89 89 91 99 0 25 50 75 100 frequent stool pretibial oedema ophtalmopathy increased appetite weakness Dyspnea tachicardia82 weight loss astenia Palpitatii termofobia Hipersudatie nervousness Clinical symptoms 10 gynecomastia 10 10 splenomegaly 71 77 eye symptoms 97 Tremor 97 skin manifestations fibrilation thyroid trill 100 goiter 100 tachicardia 0 20 40 60 80 100 Hypertiroidism - simptoms SIGNS CAUSE Thyroid Diffuse goiter Uninodular goiter Multinodular goiter Non-palpable thyroid Painfull thyroid Graves’ disease, autoimmune thyroiditis with thyrotoxicosis Thyroid autonomy Thyroid autonomy Exogenous thyroid hormones Subacute thyroiditis Associated signs Ophtalmopaty Pretibial mixoedema Acropachy Graves’ disease Graves’ disease Graves disease Cardio-vascular signs and symptoms signs Tachicardis, continous, nocturnal + effort associated dyspnea Systolic Hypertension Increased cardiac output FC peripheral resistance miocardial contractility Cardiotireosis Atrial fibrilation : 10% Congestive hearth failure Rarely < 40 ani Corrected by euthyroid state Anticoagulant treatment Embolic risk (8%) Fibrilation, Aged patients Worsening coronary hearth disease Neuro muscular signs Nervosness, irritability, Emotional disturbance Disturbance of attention and mood. Pseudo psychotic forms Tremor Muscle weakness Rapid reflexes, Amiotrophy (pseudo miopathic forms) Hypokaliemic periodic paralysis Digestive signs Tranzit accelerat (motor) pseudodiaree = poli exoneratie Anomalii hepatice Icter, citoliza, hipocolesterolemie Genital abnormalities men gynecomastia (40%) Erectile dysfunction infertility women Menstrual abnormalities disovulation Bone abnormalities Skin problems Decreased BMD : distruction>formation Spontaneous fractures Hypercalcemia, hypercalciuria alkaline phosphatase and osteocalcin pruritus Localized edema Alopecia Metabolic abnormalities Hypocholesterolemia Hyperglicemie, worsening of diabetes mellitus Positive diagnosis Clincal signs and symptoms TSH: suppressed (excepton TSH-secreting pituitary adenoma) FT4 and/or FT3 Etiologic diagnosis history pregnancy Painfull thyroid drugs Clinical signs goiter Extrathyroidal signs TSH receptor stimulating immunoglobulins (TRAb) Scintigraphy Urinary iodine HYPERTIROIDISM Peripheral metabolism Parameter Hypertiroidism Hypotiroidism Basal metabolic rate Cholesterole SHBG Osteocalcin OH-proline Pyridinoline < 240 ms > 360 ms Deep tendon reflex Qkd interval HYPERTIROIDISM / TIROTOXICOSIS Paraclinical diagnosis TSH, fT4 TSH↓, fT4↑ Hyipertiroidism T3 tirotoxicosis fT3↑ Exoftalmie + Exophtalmos - TS-Ab + Ultrasound Scintigram I123 TS-Ab hypoechoic TS-Ab + Graves’s disease Multiplee hot nodules TS-Ab - TSH↓, fT4= TSH ↑, fT4↑ fT3 TSH adenoma Syndrome Refetoff fT3↓ Euthyroid sick syndrome Critical diseases Dopamine, Hypoechoic thyroid TS-Ab - Subacute thyroiditis Toxic adenoma Hashimoto’s thyroiditis Toxic multinodular goiter Jod-Basedow Tirotoxicosis factitia Struma ovarii (rarely) HYPERTIROIDIS / THIROTOXICOSIS Imagery: Graves’disease Thyroid ultrasound HYPERTIROIDISM / THYROTOXICOSIS Imagery : toxic adenoma Thyroid ultrasound Scintigram HYPERTIROIDISM / THYROTOXICOSIS tests: toxic adenoma TSH Studer Wyss T4 PTU HYPERTIROIDISM / THYROTOXICOSIS tests: toxic adenoma TSH Studer Wyss PTU Querido TSH TSH T4 HYPERTIROIDISM / THYROTOXICOSIS tests: toxic adenoma fT4 TSH Studer Wyss PTU Querido TSH Werner fT4 T4 HYPERTIROIDISM / THYROTOXICOSIS Complications Hearth atrial fibrilation resistant to treatment hyperkinetic hearth failure Infertility / amenorrhea Osteoporosis (postmenopausal) Thyrotoxic periodic paralysis flaccid paralysis and hypokalemia asian men reversible on treatment Apathetic hyperthyroidism Aging patients Thyrotoxic crisis (thyrotoxic storm) Etiology determinant factors Undertreated thyrotoxicosis Recently developed untreated hyperthyroidism Precipitating factors medical infecţions Diabetic ketoacidosis Lung embolism Labor or pregnancy Premature stopping treatment I131 treatment surgery Thyrotoxic crisis severe signs and symptoms of thyrotoxicosis severe hipermetabolism fever over >38oC (til 41-42oC) Neuro-psychological symptoms “thyrotoxic encephalopathy" - cardio-vascular symptoms tachicardia - >140/min, arhitmias (atrial fibrillation ) Hearth failure (left, global) Variations of arterial blood pressure gastro-intestinal symptoms Mimikin acute abdomena Jaundice (index of severity) Graves disease Most frequent cause of hyperthyroidism Prevalence 1% 19/1000 ♀ 1,6/1000 ♂ (Sex ratio 7 / 10) Incidence 2 - 3 cases / year /1000 ♀ Young female patient, psychological trauma Autoimmune, familial Asociated with other autoimune diseases: tip 1DM, adrenal insufficiency, vitiligo, miastenia gravis Stimulating immunoglobulins perspiration flushes < 40 years Lymp node enlargement amiotrophie dispnea Gynecomastia in ♂ Weigh loss nervosness, emotional instability exophtalmos goiter (± thrill) Hot, mois skin palpitations, tachicardia, low response apetit to digytalis diarheea tremor acropachia oligo/amenorrea Local mixedoema Muscle weakness, fatigability Graves’ disease goiter Graves’ disease Graves’ disease GOITER Difuse Elastic Homogenous painless Vascular (thrill) Graves exophtalmos Graves ophtamopathy Eyelid edema, periorbital edema, proptosis Increase tears production Incomplete close eyelids during night Fotofobia, Eye disconfort, pruritus, “alergy Painfull eyes, associated or not with eye mouvments Dyplopia Intermitent: when patinets is tired Inconstant Constant: when reading Graves ophtalmopathy NOSPECS Class Definition 0 No phisical signs and symptoms 1 Only signs, no symptoms (upper lid retraction, stare, proptosis to 22 cm) 2 Soft tissue involvement (symtpoms and signs) 3 Proptosis > 22 cm 4 Extraocular muscle involvement 5 Corneal involvement 6 Sight loss (optic nerve involvement) Severity of Graves ophtalmopathy Degree Signs and symptoms EUGOGO (European Group on Graves’ Orbitopathy) Mild 1. 2. 3. 4. Minimal or moderate edema Proptosis <25 mm Diplopia: absent or intermitent No optic nerve envolvement Moderate Important edeme 1. And/or proptosis >25 mm 2. And/or inconstant dyplopia 3. And/or corneal point lesions 4. No optic nerve involvement Severe Constant dyplopia 1. And/or optic nerve involvement Clinical Activity Score (CAS) 1. 2. 3. 4. 5. 6. 7. Spontaneous retroocular pain Pain at eye mouvments Eyelid erithema Corneal increased vascularity Chemosis Edema of caruncula Eyelid edema Every item has 1 point. Active ophtalmopathy: >3 poins Graves’ ophtalmopathy Eyelid retraction Graves’ ophtalmopathy Eyelid edema Graves’ ophtalmopathy Superioar eyelid edema Graves’ ophtalmopathy Eyelid edema Graves’ ophtalmopathy Enlarged eyelid opening Graves’ ophtalmopathy Corneal involvment Graves’ ophtalmopathy Corneal and conjunctival problems Graves’ ophtalmopathy Exophtalmos Graves’ ophtalmopathy Exophtalmos Graves’ ophtalmopathy Ophtalmoplegia Graves’ ophtalmopathy Graves’ ophtalmopathy CT of orbotal area Pretibial mixoedema Nodous eritema Acropachy Toxic adenoma (Plummer) Isolated thyroid nodule autonomous Extranodular parenchima is not functioning Evolutia adenomuui toxic 1 2 3 4 5 Autonomous functioning tissue TSH Normal secretion 1 2 3 4 Normal secretion Autonomous secretion 5 TSH level Toxic multinodular goiter Hearth signs and symptoms are dominant 10 - 15 % of atrial fibrillation in aged patients is associated with TMG Hearth failure Compressive goiter Subacute thyroiditis Neck pain Tirotoxicosis Post viral Trifase evolution Hipoechogenicity hyperthyroidism hypothyroidism euthyroidism inhomogenous Pseudo nodular Absence of iodine uptake and “white scintigram” hipertiroidism eutiroidism hipotiroidism HYPERTHIROIDISM / THYROTOXICOSIS Age-related characteristics Newborns • neonatal Graves disease (goiter exophtalmos, thyrotoxicosis) • temporarly • permanent • familial non-autoimmune thyrotoxicosis Children • Graves disease • increased growth rate Aging patients •Toxic adenoma / TMNG / Graves • clinical signs are less obvious • suspected when • it is an unexpected weight loss • atrial fibrilation and hearth failure unresponssive to digitalis Amiodarona si tiroida O I C Celular : I se opune intrarii tiroxinei si fixarii T3 de receptorii nucleari TSH us in prima saptamina fara hipotiroidie Tiroida: C 4 H9 C 2 H5 Hipofiza tireotropa : O O CH2 CH2 N C 2 H5 acumulare de iod - efect Wolf Chaikoff citotoxicitate foliculaira Periferic : conversie T4 in T3 (inhiba 5’ deiodaza) manifestari tirotoxice putin marcate amiodarona Amiodarone –induced hyperthyroidism Type I : hyperfunctional (previous thyroid autoimmunity) Type II : distructive (previous normal thyroid) women 1/2 men 2/3 N, Scintigram positive absente Scintigram absent IL6 Normal and Tg Ultrasound volume Normal volume Hypervascularity (grad 1-3) Hipoechoic, hipovascular (grad 0) Classic treatment ATS 6-9 month KCLO4 Potasium perclorate Glucocorticoids Prognosis Sponaneous regression (3-6 month) Prolonged hyperthyroidism Spontaneous regression (36 month) Transitory hypothyroidism Affected individuals 123I uptake Echodoppler Thyrotoxicosis treatment AIM: to decrease thyroid hormones to normal levels Distruction of thyroid 1. surgery Radio iodine Inhibition of thyroid hormone synthesis (ATD) Antithyroid drugs Glucocorticoids adjuvant therapy Decreases conversion of T4 to T3 3. inhibition 2. ATD glucorticoids (high doses) propranolol iodine Reduction of receptor coupling -blokers plasmaferesis Antithyroid drugs Imidazole derivatives (methimasole) H H N N S NH S N Inhibit TPO COOC2H5 carbimasole Thyourheea derivatives (thiouracile) H H N CH3-CH2-CH2 S N NH NH O S O propilthiouracile Inhibits TPO Inhibits type 1deiodinase Treatment of hypothyroidism ATD 2 possibilities Continous high dosage and association ofthryoid drugs when hypothyroidism occurs Decreasing dosage to the minimal dosage that maintans an euthyroid state Graves disease Young women 1,5 years at least Monitoring the resullts TS-Ab < 50%cure in toxic adenoma /GMNT Only a temporary solution Antithyroid drugs Dosage Adults 10-20 mg x 2 po initially Dosage will be decreased to ½ doza when patient becomes euthyroid Children: initial;y 15-20 mg/m2 divided in 2 doses Later: minomal efficient dose Treatment of hyperthyroidism other possibilities Litium inhibits TPO high toxicity Stable Iodine solution 1 g iodne 2 g KI 20 ml distilated water Preoperative for surgery 3 × 20 picături pe zi, 1014 zile Nodule necrosis with alcohol toxic adenoma Potassium perclorate amiodarone induced thyrotoxicosis Lugol Antiimflamatory drugs subacute thyroiditis Type II amiodarone induced radioactive iodine: Graves disease 80-100 mCi/g 131I x thyroid wight (g) 100 x RIU 123I (24 h) Radioactive iodine: toxic adenoma TSH I* T 4 Surgery Graves disease tyroidectomy (near) total indications GMNT Increased thyroid nodule tyroidectomy (near)total adenomul toxic lobectomy Complications hypothyroidism hypoparathyroidisme (35%) laringeal nerve paralisis hemorrhage during surgery GRAVES OPHTALMOPATHY Total thyroidectomy or ATD + terapie prednisone ! 10 mg x 4 – 7d Form of ophtalmopathy? recente –immunosupressive prednisone 25 mg x 4, 7-14 d metilprednisolone 250 iv, repeated at 3 days (pulse) Polyclonal immunoglobulins old (GAG infiltration, fibrosis) Retroorbitar irradiation enlargement of the orbitis surgery on orbital muscles other plastic surgery procedures Tratamentul exoftalmiei basedowiene Decompresie orbitara Inainte Dupa tratament Graves ophtalmopathy Orbital decompression Before After treatment Thyreotoxic crisis Objectives I. Inhibition of thyroid hormone synthesis and liberation II.Decreased action of thyroid hormones on target tissues Reduction of thyroid hormone concentration Conversion inhibition of T4 into T3 Adrenergic blokade III.Treatament of systemic symptoms fever dehydration supportive IV.Treatament of precipitating factors Thyrotoxic crisis Inhibiton of hormone synthesis Antithyroid drugs (ATD) Large doses, per os Propiltiouracile (PTU) - 1200 - 1500 mg/d (200-250mg la 4h); Methimasole (MMI) - 120 mg/d (20 mg la 4h); Inhibition of TH liberation Iodine-containing compaunds Lugol sol; saturate solution of KI (SSKI) -p.o., 5 drops every 6h; Contrast media (inhibition of conversion of T 4 into T3): Criza tireotoxica Inhibition II. Reduction of TH action on target tissues of peripheral conversion T4 to T3 propilthyouracil; Adrenergic ipodate, iopanoate; propranolol; glucocorticoids blokade: betablokers - propranolol – most used: iv, large doses short-action blokers (labetalol, esmolol); reserpine, utile guanetidine: în contraindicaţiile -blocantelor; Removal of thryoid hormone excess plasmapheresis; dialysis Thyrotoxic crisis Treatment od systemic symptoms fever Coated with cold sheets drugs paracetamole Dihydration heath failure glucocorticods IV. Treatment of precipitating factors