PAEDS 1. These liver cysts are seen on ultrasound in a 10 year old child . He is apyrexial ad well apart from non tender distended abdomen , and presented because of his upper abdominal distention. But is otherwise asymptomatic. The most likely in this age group in South Africa is Select one :: A. B. C. D. E. Amoebiaisis Beta haemolytic streptococcus Hepatoblastoma Staphylococcus aureus Echinococcus cyst 2. Which of the following is important in the neonate for body temperature regulation? a. Adequate hydration b. Centrally-situated brown fat c. Subcutaneous fat and body hair d. Exposure of head to ambient temperature to allow auto-regulation e. Shivering thermogenesis 3. Choose the correct statement regarding the condition of this premature neonate shown Select one: a. Provided bowel is covered in plastic, there is no risk of bowel ischaemia b. Nasogastric tube drainage provides no benefit c. Usually achieve full oral feeds within one week after birth d. Associated with Intestinal malrotation e.Associated intestinal atresia precludes survival 3.2 ( use picture above ) Appropriate care of a baby born with exposed intestines proplasting through an abdominal wall defect includes Select one: A. high-flow oxygen, broad spectrum antibiotics, cover bowel with plastic clingwrap, kangaroo care B.nasogastric drainage, preservation of normothermia, protection of bowel with plastic, enlargement of defect if mesenteric constriction likely cause strangulation of blood supply C. Transfer to tertiary care after 24 hour stabilization period D. protection of baby in incubator or plastic bag to keep warm, prevent bowel from kinking and obstructing mesentery, monitor serum glucose, transfer to definitive care once mother fit for discharge with infant to tertiary care E. breastmilk feeds. protect bowel with warm saline-soaked swabs. maintain normothermia. analaesia 4. A 5 year old patient presented with several episodes of painless bright red rectal bleeding after stooling. The lesion shown is seen at colonoscopy (histology also shown). The following statements are all true of this lesion EXCEPT: (i.e. Choose the FALSE statement Select one: A. often premalignant B. autoamputation common C. mostly rectosigmold location D.. usuallv solitary E. mav prolapse out or anus 5.This girl has right hemihvpertrophv. She needs follow-up screening for the following solid-organ tumours: Select one: a. Neuroblastoma, leukemia b. lymphoma, cystic hygroma c. rhabdomyosarcoma, Ewing's sarcoma e. lymphangioma, renal cell carcinoma 6.A 3 year old polvtrauma patient who was knocked over by a car presents to the trauma unit with multiple injuries, Including a closed head injury. He is drowsy and uncooperative and has multiple abrasions and some long bone fractures. You are called to assess the abdomen which is tender and very distended, especially in the upper half of the abdomen, shouting at you when you press there and throwing off his oxygen mask. What procedure will aid your clinical assessment of the abdomen? Select one: a. Insertion of oro-gastric tube b. Cranial burr-hole placement C Nasal prong oxygen d. Intubation and gentle ventilation e. Chest drain insertion/ 7. This neonate presented with a picture of severe sepsis . Appropriate management includes Select one: a. Topical emollients and saline dressings b. Urgent surgical umbilical debridement and broad-spektrum antibiotics c. Urgent umbilical exploration with herniorrhaphy d. Anti-streptococcal antibiotics and analgesia e. Conservative care to avoid injury to umbilical vessels 8. This child has proven gastro-oesophageal reflux disease and has had 2 months or proton pump inhibitor therapy and been managed with small frequent feeds and head-up positioning. Possible indications for a gastric fundoplication in this child include Select one: a. single episode lower respiratory tract infection b. parental preference for surgery over longterm medication c. persistent vomiting despite growing well d.failure to thrive due to vomiting e, sibling who had haemorrhagic oesophagitis 9. Sudden onset of sever pain with vomiting, abdominal distension and no passage of stools in this neonates is most likely Select one: a. Scrotal abscess b. Testicular torsion c. Acute idiopathic scrotal edema d. Incarcerated inguinal hernia e. Epididiymo-orchitis. 10. The abdominalities on this x rays all features of the following group of conditions Select one; a. Peutz-Jehger's syndrome b. VACTERL association c. Beckwith-Wiedemann syndrome d. Poland sequence 11. This 1 month old male infant presented with persistent vomiting for 2 weeks and abnormal ultrasound findings as shown. His biochemical picture is most likely A. B. C. D. E. Hyperchloraemic Normal Alkalinuric Hyponatraemic Acidotic 12. Orchidopexy in the child with a unilateral, palpable testis in the inguinal canal should ideally be performed at the following Age Select one: a. at 5-6 years of age b. at 6-12 months of age c. after puberty d. after 2 years of age e. as soon as diagnosed, regardless of age 13. Early operative cholangiogram is indicated in babies with conjugated jaundice and pale stools to confirm or exclude biliary atresia because (choose the TRUE statement) Select one: a. surgery is easier in smaller babies b. time in hospital is saved as other test results take a long time to come out c. if a Kasai portoenterostomy is unsuccesful, the patient can be put onto the liver transplant list sooner d. it is the most likely cause of jaundice in a baby e. a successful Kasai portoenterostomy may prevent progression to liver cirrhosis 14. This one month old male infant presented with persistent vomiting of gastric contents . Ultrasound findings are shown ,, the appropriate further management is th following Select one: a. Nasogastric drainage and nil per mouth for urgent surgery within next few hours b. Controlled intravenous correction of chloride and hydration status with surgery only if no improvement on conservative c. Urgent Heller's myotomy d. Biochemical normalization then Ramstedt pyloromyotomy/ e. Potassium replacement if hypokalaemic once passing adequate volumes of urine and repeat ultrasound in one week if still vomiting F.Correct dehydration with 10% dextrose water and give protein pump inhibitors 15.. A one day old premature infant has esophageal atresia. Pick the most CORRECT statement below regarding essential practice to safely transport this patient to a tertiary hospital for further care. Select one: A.regular suctioning of upper esophageal pouch through nasal tube/ b. skin to skin contact with mother c. monitoring of haemoglobin d. oral dextrose water if no intravenous access e. cardiac echogram prior to transport 16. Choose the correct statement regarding the use of propranolol in the treatment of the lesion shown Select one: a. not indicated in this location b. Side effects like hypoglycaemia and bronchospasm never occur in children C. more effective and better side-effect profile than steroids d. second-line treatment for cases where surgery is not feasible e. not indicated in this 3 month old patient as lesion will spontaneously involute 16.2 ( use Above picture ) All of the following statement are correct with respect to the lesion shown except for the following Select one: a. propranolol is a non-selective beta-blocker that can shrink hemangiomas b. rapid growth of this lesion means it is a malignant tumour c. spontaneous involution >70%/ spontane involusie >70% d. amblyopia, scarring and associated brain abnormalities can occur e. Hypothyroidism and low platelets can result from multiple large lesions like this 17. 2 week old 1,3kg girl suddenly develops abdominal distension and bloody stools after blood transfusion . She was previously doing well . The most likely diagnosis is Select one: A.Spontaneous intestinal perforation B.. Normal premature infant x-ray C.Grade 2 necrotizing enterocolitis D.Hirschsprung's enterocolitis 18. In an 8 year old girl with episodes of abdominal pain lasting for 2-3 hours at a time about once a week over the past 3 months (not related to meals) and mild generalized abdominal tenderness but no localizing or peritonitic signs or palpable masses, differential diagnosis includes Select one: a. subacute appendicitis, Wilms tumour, gastric outlet obstruction b. gastritis, abdominal tuberculosis, colonic diverticulosis c. abdominal wall muscle spasm, acute apendicitis, ascariasis d. constipation, urinary tract infections, mesenteric adenitis e. urinary tract infections, recurrent abdominal pain syndrome, acute cholecystitis 19. Correct management of this septic 3 day old boy with a grossly distended , tender abdomen include : Select one: a. Endotracheal intubation, gastric decompression, broad spectrum antibiotics b. Perineal examination, intravenous fluids, broad spectrum antibiotics C.Fluid resuscitation, broad spectrum antibiotics, urgent laparotomy D.High dose ampicillin, give gentamicin only if good urine output, needle decompression of abdomen E. Nil by mouth, nasogastric drainage, restrict intravenous fluid intake 20. A three-day old term infant passed a small amount of meconium for the first time today, but his abdomen remains distended and he has been vomiting milk feeds since yesterday. He has a normal anus and an empty processus vaginalis bilaterally. After a contrast enema his abdomen is less distended and a lot of meconium plugs are passed out of the anus. The most likely cause of his distal bowel obstruction is: Select one : A. Ascariasis B. Aganglionis C. Atresia D. Atelectasis E. Abdominal wall defect 21. A 6 week old boy was born at 34 weeks gestation and now presents with a one day history of irritability and right groin mass as shown . The most likely diagnosis Select one: A. incarcerated inguinal hernia B. inguinal lymphadenitis C. non-communicating hydrocoele D. testicular torsion e, communicating hydrocoele 22.This neonate was born by caesarian section due to a large antenatally detected mass protruding from the buttocks behind the anus. The correct diagnosis is: a. rhabdomyosarcoma b. haemangioma c. lymphatic malformation D.sacrococcygeal teratoma E.neuroblastoma 23. A one year old child presents with a one day history of a red, painful, fluctuant swelling in the submandibular area. The most likely responsible organism is:/ Select one: A.staphylococcus aureus b. mycobacterium bovis c. bartonella henselae (cat scratch disease) d. ascaris lumbricoides e. respiratory syncytial virus 24. The photo shows laparotomy findings of the small bowel in a term neonate . This condition would most likely have presented with the following symptoms Select one: a. gasless abdomen on AXR b, oligohydramnios C. scaphoid abdomen d. delayed passage of meconium e. bile-stained vomiting/ 25. The differential diagnosis of a midline neck swelling in a child includes all of the following Select one: a. Branchial cyst, thryoglossal duct cyst, thymic cyst, parotidomegaly, lymph nodes b. Thyroglossal cyst, cystic hygroma, plunging ranula, ectopic thyroid/ C.Dermoid cyst, submental lymphnode, pyramidal thryoid lobe, thryoglossal duct cyst d.Branchial cyst, dermoid cyst, cystic hygroma, submandibular lymphnode 26. Choose the correct statement regarding timing of surgery for this premature infant with reducible ingunial hernia Select one; a. Perform elective bilateral inguinal heriotomies after weight of 5kg OR age of 3 months achieved b. Only operate if hemias become irreducible or strangulate c. Low risk of incarceration in premature infant and usually spontaneously resolve <18 months d. Perform elective bilateral inguinal hemiotomies prior to discharge home e. Urgent repair if intercurrent pneumonia ( high risk of incarceration and bowel strangulation from coughing) 27. Choose the TRUE statement regarding antenatally diagnosed gastroschisis from the following Select one: a. Poorly diagnosed with antenatal ultrasound b. Amniocentesis must be performed as chromosomal abnormalities are common c. Preferred antenatal investigation is MRI d.Must be delivered in a hospital with a paediatric surgeon available e. Delivery should be by Caesarean section 28. A 1 month old child who was previously well presents with bile stained vomiting. The most appropriate further investigation is Select one : A. MRI B. Contrast enema C. Contrast meal and follow up D. Contrast swallow E. Ultrasound scan 29. This neonate has respiratory distress with 'bubbling saliva' and CXR as shown. During transport to a tertiary centre, the following is essential Select one: A. Controlled hypothermia B.Naso-oesophageal tube suction C.Normal saline as maintenance fluid D. Early intubation and mechanical ventilation E. Keep baby exposed for monitoring 30.Which one of the following statements is true in ALL neonates with congenital causes of bowel obstruction Select one: a. maternal polyhydramnios present b. nasogastric tube drainage required c. meconium is not passed d. abdominal distension present e. bilious vomiting present 31. A 2 month old female s perineum is. Shown . There is no normal anus . Correct diagnosis is Select one: a. vestibular fistula b. perineal fistula c. cloaca malformation d. normal perineum e. epispadias 32. This 5 year old boy presents with a large central abdominal mass which has been growing slowly over the past 2 months. He is anemic, hypertensive and has lost weight. An abdominal x-ray shows central calcifications. The most likely diagnosis is a Select one: A.neuroblastoma B.lymphangioma C. hepatoblastoma D . lymphoma E . abdominal TB F. faecaloma 33. Choose the correct statement regarding this upper GIT contrast meal and followthrough done for a 1-year old patient with failure to thrive, recurrent aspiration pneumonia and severe gastro-oesophageal reflux disease. Select one: A.malrotation without midgut volvulus B.Indicates need for urgent pneumatic reduction C. Further investigation with ultrasound indicated D. Surgery only indicated if associated bilious vomiting 34. Regarding testicular torsion, the following is TRUE Select one: A. Testicular salvage for surgery performed after 12 hours remains excellent/ B. It rarely occurs during the neonatal period or puberty C. Orchidopexy of the unaffected testis is not routinely done at surgery D.It may present with abdominal pain and vomiting/ Dit mag met buikpyn en braking presenteer E.An ultrasound with Doppler is essential before surgery 35. This 6 month old girl was referred because of an "absent vagina". On examination she has a normal anus and is otherwise well with no palpable abdominal mass. She had normal genitalia and no other problems at birth. The following statement is TRUE regarding this condition:/ Select one: a. She has vaginal atresia and will need vaginal reconstruction. b. She has labial adhesions which will soften with topical estrogen. C.She has a cloaca and needs an ultrasound to look for hydrometrocolpos. d. She has ambiguous genitalia and needs chromosome studies e. She has an involuted vagina and needs estrogen and progesterone level testing 36. The primary role of surgery in the premature infant whose abdominal x ray is shown is Select one: a. to correct metabolic acidosis/ b. to remove full-thickness bowel necrosis and debris c. to improve ventilation d. to perform colostomy e. to empty stool from intestines f. to resect all diseased bowel 37. This 5-month old previously well infant has a 2-day history of bloody stools and vomiting and abdominal x-ray as shown. The abdomen is very distended but not tender. Appropriate initial management includes the following: Select one: a. broad spectrum antibiotics, trial of oral rehydration solution, send stool for culture/ b. intravascular volume resuscitation, nasogastric drainage, abdominal ultrasound/ c. Immediate laparotomy d. Nasogastric tube drainage and intravenous maintenance fluid for trial of "drip and suck e, blood group type and crossmatch, urgent Meckel's technetium scan 38. Choose the CORRECT statement(s) regarding the injury shown on the chest x-ray of this 8 year old motor-vehicle accident victim. Select one: a. If the lung fields are normal on early chest x-ray and there are no other bony or solid viscera injuries, pulmonary contusion is ruled out/ B. Rib fractures in children commonly occur with low velocity impact accidents c. Head injury is less likely to cause death than thoracic injury d. Children with rib fractures are at higher risk for associated liver and spleen injuries e. Children cannot sustain severe pulmonary contusions without fracturing ribs as well 39. A 6 year old child presents with a history of 2 days of vomiting, loose stools, and increasing abdominal pain that initially started in the peri- umbilical region, and has now moved to the right iliac fossa. His oxygen saturation is 99% on room air, he has a pulse rate of 180 beats per minute, a capillary refill time of 3 seconds, and a temperature of 38 degrees Celsius. Choose the best initial course of management out of the following Select one: a. Nasal prong oxygen b. 10ml/kg half-Darrows-Dextrose solution/ c. Morphine infusion d. Tepid water sponging & rectal NSAID antipyretic e.20ml/kg isotonic crystalloid bolus iv 40. A 3 year old presents with a high grade temperature, right upper quadrant abdominal pain and tenderness for 2 days and tender hepatomegaly. His liver ultrasound is shown. The 2 most likely possible aetiological agent(s) in this case is/are:/ Select one or more: A.amoeba histolytica B.echinococcus granulosis C. streptococcus epidermidis D. mycobacterium tuberculosis E.. enterococcus spp. F. staphylococcus aureus 41. All of the following statements regarding passage of meconium in patients with anorectal malformations are true EXCEPT for (i.e. choose the FALSE statement): Select one: A . Passage of meconium excludes anorectal malformation B . Meconium passed per urethra with an imperforate anus indicates an anorectal malformation with recto-urethral fistula C . Delayed diagnosis with 'bucket-handle' malformation is common as meconium can still be passed through a perineal fistula D . Without surgical repair, build-up of meconium and gas in the proximal rectum in a child with an anorectal malformation may lead to bowel necrosis and perforation E .During the first 24 hours after birth the perineum of a male with an imperforate anus should be monitored for signs of meconium via the rethra or a perineal fistula 42. This 6 month old baby presented with rectal bleeding and something red prolapsing through the anus .it is the first time that this has happened, he is also recovering from gastroenteritis the correct management of the condition is shown is : Select one or more: a. Skin emollient and antifungal cream for napkin dermatitis only b. Resection of mass C.Push back mass into anus and strapping buttocks together to prevent it coming out again and treat precipitating diarrhoea d. Remove child from parents care immediately until perpetrator of sexual assault found e. Cover lesion with warm wet swabs and await spontaneous reduction 43. Which one of the following signs suggest acute appendicitis Select one: a. Right iliac fossa pain that comes and goes B.Right abdominal pain that gets progressively worse C. Abdominal pain for 3 hours d. Previous episodes of severe adominal pain over the past 3 months e. Bouts of vomiting followed by abdominal pain/