1. True or False: Cystic Fibrosis is the second most common fatal inherited disorder in childhood.
2. True or False: CF is an autosomal recessive gene disorder caused by mutations in a pair of genes
located on chromosome 17.
3. If both parents have a CF, what is the likelihood that their children will have the disease?
a. 0%
b. 25%
c. 50%
d. 75%
e. 100%
4. True or False: Genetic screening can be done to test the father if the mother has a mutant CF
gene.
5. True or False: The gold standard test for CF is genetic screening.
6. True or False: The age of the patient does not factor into a sweat chloride test.
7. All of the following are common conditions in patients with CF, except?
a. Pancreatic insufficiency
b. Parasinusitis
c. Gastrointestinal disorders
d. Male infertility
e. All of the above are common with CF
8. Describe 8 common findings of a patient with CF during a physical assessment.
9. Which of the following types of bronchiectasis are best described as bronchi that progressively
increase in diameter until they end in large, cyst like sacs in the lung parenchyma?
a. Varicose bronchiectasis (Fusiform)
b. Cylindrical bronchiectasis (Tubular)
c. Cystic bronchiectasis (Saccular)
10. Which of the following types of bronchiectasis are best described as bronchi that are dilated and
constricted in an irregular fashion similar to varicose veins with distorted, bulbous shapes?
a. Varicose bronchiectasis (Fusiform)
b. Cylindrical bronchiectasis (Tubular)
c. Cystic bronchiectasis (Saccular)
11. Which of the following types of bronchiectasis are best described as bronchi that are dilated and
rigid and have regular outlines similar to a tube?
a. Varicose bronchiectasis (Fusiform)
b. Cylindrical bronchiectasis (Tubular)
c. Cystic bronchiectasis (Saccular)
12. What are 4 clinical manifestations of bronchiectasis? (Worth 4 points)
13. True or False: A PFT of a patient with bronchiectasis may show obstructive, restrictive or a
combination of both lung disorders.
14. Describe 4 common findings of a patient with bronchiectasis during a physical assessment.