Scoliosis Evaluation and Decision Making for the Pediatrician John F. Sarwark, MD Children’s Memorial Hospital Head, Orthopedic Surgery Northwestern University’s Feinberg School of Medicine, Professor of Orthopedic Surgery Cynthia R. LaBella, MD Children’s Memorial Hospital Medical director, Institute for Sports Medicine Northwestern University's Feinberg School of Medicine Instructor of Clinical Pediatrics Copyright © 2005 Children's Memorial Hospital. All rights reserved. 1/37 Scoliosis: Overview • • • • • • Definition Etiologies Making the diagnosis When to refer Natural history/prognosis Treatment Copyright © 2005 Children's Memorial Hospital. All rights reserved. 2/37 Scoliosis is strictly defined • Cobb angle measurement on Xray: • Lateral curvature > 10° Copyright © 2005 Children's Memorial Hospital. All rights reserved. 3/37 Scoliosis: Etiologies • Two categories • Structural • Non-structural Copyright © 2005 Children's Memorial Hospital. All rights reserved. 4/37 Non-structural etiologies • • • • Leg length discrepancy Inflammation Neurogenic / disc pathology Hysterical Copyright © 2005 Children's Memorial Hospital. All rights reserved. 5/37 Structural etiologies • • • • Idiopathic (most common) Congenital Neuromuscular (e.g. cerebral palsy) Miscellaneous (lengthy list) Copyright © 2005 Children's Memorial Hospital. All rights reserved. 6/37 Miscellaneous scoliosis: examples • Associated with other conditions • Osteoid osteoma • Metabolic • Rickets • Osteogenesis Imperfecta • Infection (late sequela) • Limb deficiency syndromes • Burn scar (truncal) • Congenital heart disease • Chest wall asymmetries Copyright © 2005 Children's Memorial Hospital. All rights reserved. 7/37 Morquio-Brailsford Syndrome • Mucopolysaccharidosis • Spine normal at birth • Kyphoscoliosis develops with growth • Usually also present: • Odontoid hypoplasia • Short stature • Aortic valve abnormalities • Hearing loss • Corneal opacities Copyright © 2005 Children's Memorial Hospital. All rights reserved. 8/37 Neurofibromatosis • Spine involvement is common • Often exhibit bony dyplasia • Curves tend to be sharp and progressive Copyright © 2005 Children's Memorial Hospital. All rights reserved. 9/37 Osteoid Osteoma Night pain Limited spinal mobility Tenderness Xray may reveal classic features • Bone scan often diagnostic • • • • Copyright © 2005 Children's Memorial Hospital. All rights reserved. 10/37 Marfan Syndrome Scoliosis develops in most cases Often have double and triple curves Curves start earlier Curves are more progressive, resistant, and rigid • Brace management less effective • • • • Copyright © 2005 Children's Memorial Hospital. All rights reserved. 11/37 Normal Spinal Alignment • Anteroposterior view……0° curvature • Sagittal (lateral) view • Thoracic kyphosis……….20-40° (varies) • Lumbar lordosis…………40-60° (varies) Copyright © 2005 Children's Memorial Hospital. All rights reserved. 12/37 Idiopathic Scoliosis • Idiopathic scoliosis with onset after age 10 is most common and classic form Copyright © 2005 Children's Memorial Hospital. All rights reserved. 13/37 Idiopathic Scoliosis: Incidence • 2% referred after screen • 0.3% require treatment • Female:male – 7:1 (at >30°) Copyright © 2005 Children's Memorial Hospital. All rights reserved. 14/37 Idiopathic Scoliosis: Incidence • Incidence of scoliosis in relation to curve magnitude • Most scoliosis is low magnitude Copyright © 2005 Children's Memorial Hospital. All rights reserved. 15/37 Scoliosis: Diagnosis The physical examination is the first line of detection Copyright © 2005 Children's Memorial Hospital. All rights reserved. 16/37 Scoliosis: Clinical Examination • Inspection • Shoulder height asymmetry • Scapular prominence • Waist line asymmetry • Flank crease • Pelvic asymmetry • Adams Forward Bend Test • Sine qua non for scoliosis evaluation Copyright © 2005 Children's Memorial Hospital. All rights reserved. 17/37 The Screening Exam • Adam’s Forward Bend Test • Prominence is accurately measured using scoliometer • Scoliometer measures the angle of trunk rotation (ATR) • Misleading traps • Pelvis level? (LLD?) • Back pain Copyright © 2005 Children's Memorial Hospital. All rights reserved. 18/37 Scoliometer measures ATR Copyright © 2005 Children's Memorial Hospital. All rights reserved. 19/37 Angle of trunk rotation (ATR) Copyright © 2005 Children's Memorial Hospital. All rights reserved. 20/37 ATR Correlates With Cobb Angle Copyright © 2005 Children's Memorial Hospital. All rights reserved. 21/37 Location of Curve Copyright © 2005 Children's Memorial Hospital. All rights reserved. 22/37 When to Refer • Refer when: • ATR >5-7 degrees or • Cobb angle >20 degrees • False negative (“missed”) – 0.1% • False positive (over-referred) – 5% Copyright © 2005 Children's Memorial Hospital. All rights reserved. 23/37 Scoliosis: Natural history • Effects of growth and puberty Copyright © 2005 Children's Memorial Hospital. All rights reserved. 24/37 Natural History of Curve Progression in Idiopathic Scoliosis • Curves < 30° are stable • Curves > 50° tend to progress • Avg. rate = 1°/year • Factors in curve progression • Vertebral rotation • Translatory shifts Weinstein • Curve severity JBJS 65A:447, 1983 Copyright © 2005 Children's Memorial Hospital. All rights reserved. 25/37 Natural History Curve progression is defined as increase of 5 or more degrees Copyright © 2005 Children's Memorial Hospital. All rights reserved. 26/37 Risk Factors for Progression • • • • Magnitude of curve at presentation Curve location Level of maturation Risser grade • Extent of iliac crest ossification on AP Xray Copyright © 2005 Children's Memorial Hospital. All rights reserved. 27/37 Long Term Sequelae • Cosmetic deformity • Psychosocial effects • No increased back pain in general – except for T-L curves as adults • If curve is >80° • Cor Pulmonale • If curve is >100° • Cardiopulmonary death (rare) Copyright © 2005 Children's Memorial Hospital. All rights reserved. 28/37 Physical Deformity • Coronal plane curve – “Cobb angle” • Sagittal plane – Hypokyphosis ! • Rotational deformity rib effect Copyright © 2005 Children's Memorial Hospital. All rights reserved. 29/37 Psychosocial effects • Scoliosis has been shown to increase risk of • Suicidal thought • Worry • Concern over body image • Support groups and counseling may be appropriate Copyright © 2005 Children's Memorial Hospital. All rights reserved. 30/37 Non-Prognostic Factors • Factors that do not predict curve progression • Family history • Thoracic kyphosis • Lumbar lordosis • Lumbosacral anomalies • Trunk balance Copyright © 2005 Children's Memorial Hospital. All rights reserved. 31/37 Impact of Early Presentation and Diagnosis • • • • • Earlier detection Smaller curves are easier to treat Conservative treatment more likely Surgery needed less often If surgery is needed: • Less complex • Earlier intervention may have greater impact on prognosis Copyright © 2005 Children's Memorial Hospital. All rights reserved. 32/37 Scoliosis treatment • Treatment options are based on natural history and curve severity Copyright © 2005 Children's Memorial Hospital. All rights reserved. 33/37 Copyright © 2005 Children's Memorial Hospital. All rights reserved. 34/37 Copyright © 2005 Children's Memorial Hospital. All rights reserved. 35/37 Scoliosis Treatment Summary Copyright © 2005 Children's Memorial Hospital. All rights reserved. 36/37 Thank you Copyright © 2005 Children's Memorial Hospital. All rights reserved. 37/37