Chapter 31- Care of Child with a Physical Disorder Jessica Gonzales RN, MSN Cardiovascular assessment Monitor apical and peripheral Pulses for rate, rhythm, and quality Auscultate for extra heart sounds Assess height And weight, Growth failure Can occur with Sever cardiac disease Periorbital edema Engorged Neck veins Monitor respirations for rate and effort Ausculate for adventitious sounds Abdominal distension Palpate for Hepatomegaly And splenogmegaly Monitor BP for hypo or hypertension cyanosis clubbing Peripheral edema •Palpate •inspect Congenital Heart Disease Etiology and pathophysiology: ♥ Family history of CHD ♥ Mom comes in contact with certain substances during first few weeks of pregnancy ♥ Mom with seizure disorder and on meds ♥ Depression and lithium ♥ Uncontrolled diabetes or lupus ♥ Rubella ♥ Chromosomal abnormalities (downs syndrome, turners) ♥ infection Left atrium Superior vena cava Right atrium mitral aortic pulmonic tricuspid Right ventricle Inferior vena cava Left ventricle 1. Inferior and superior vena cava from body into right atrium 2. Right atrium to right ventricle via tricuspid valve 3. Through pulmonary valve to pulmonary artery 4. Pulmonary artery to lungs 5. To pulmonary veins from lungs 6.Pulmonary veins to left atrium 7.Through mitral valve into left ventricle 8.Through aortic valve to aorta 9. To body Tissue Paper My Assests R I C U S P I D u l m o n i c i t r a l o r t i c • Types of defects: ♥ Pulmonary Blood flow ♥ Pulmonary Blood Flow ♥ Obstruction to systemic blood flow ♥ Mixed blood flow ♥ Cyanotic ♥ Acyonotic Cyanotic Pulmonary Blood flow ♥TGA Pulmonary Blood flow ♥TOF Acyanotic Pulmonary Blood flow ♥VSD ♥PDA ♥ASD Normal Blood Flow ♥COA Cyanotic •PDA •ASD •VSD R L R L Acyanotic 4 T’s •Tetralogy of fallot •Truncus Ateriosus •Transportation of the great vessels •Tricuspid Atresia Clinical manifestations • • • • • • • • • Cyanosis pallor Cardiomegaly, additional heart sounds (pericardial rubs, murmurs,) Discrepancies between apical and radial pulses Tachypnea Dyspnea, grunting, crackles, and wheezes Digital clubbing Hepatomegaly, splenomegaly Acyanotic Increased Pulmonary Blood flow Patent ductus arteriosus (PDA) is a condition in which a blood vessel called the ductus arteriosus fails to close normally in an infant soon after birth. (The word "patent" means open.) https://health.google.com/health/ref/Pate nt+ductus+arteriosus Acyanotic Increased pulmonary blood flow Atrial septal defect (ASD) is a congenital heart defect in which the wall that separates the upper heart chambers (atria) does not close completely. Congenital means the defect is present at birth. acyanotic Increased pulmonary blood flow Ventricular septal defect (VSD)describes one or more holes in the wall that separates the right and left ventricles of the heart. Ventricular septal defect is one of the most common congenital (present from birth) heart defects. It may occur by itself or with other congenital diseases. A large ventricular septal defect (VSD): a hole in the part of the septum that separates the ventricles, the lower chambers of the heart. The hole allows oxygen-rich blood from the left ventricle to mix with oxygen-poor blood from the right ventricle. An overriding aorta: the aorta is between the left and right ventricles, directly over the VSD. As a result, oxygen-poor blood from the right ventricle flows directly cyanotic Decreased Overriding aorta Pulmonary stenosis Pulmonary Blood flow Right ventricular hypertrophy Opening between ventricles Pulmonary stenosis : This defect is a narrowing of the pulmonary valve and the passage through which blood flows from the right ventricle to the pulmonary artery. In pulmonary stenosis, the heart has to work harder than normal to pump blood, and not enough blood reaches the lungs. Right ventricular hypertrophy : This defect occurs if the right ventricle thickens because the heart has to pump harder than it should to move blood through the narrowed pulmonary valve. Children with TOF may develop "tet spells“ (acute hypoxia) • The precise mechanism of these episodes is in doubt • presumably results from a transient In resistance to blood flow to the lungs with flow of desaturated blood to the body • characterized by a sudden, marked, increase in cyanosis followed by syncope, and may result in hypoxic brain injury and death, prolonged crying, irritability treatment: • Calm infant- hold over shoulder or in knee chest position or have child squat (increases pressure on the left side of the heart, decreaseing the R to L shunt thus decreasing the amount of deoxygenated blood entering systemic circulation) • Morphine (to decrease spasm and supress resp center) • Oxygen (it is a potent pulmonary vasodilator and systemic vasoconstrictor. This allows more blood flow to the lungs) • Consider sedation and parlaysis with intubation if these measures fail cyanotic Increased Pulmonary blood flow Transposition of the great vessels is a congenital heart defect in which the two major vessels that carry blood away from the heart -- the aorta and the pulmonary artery -- are switched (transposed). Acyanotic Normal pulmonary blood flow Aortic coarctation is a narrowing of part of the aorta (the major artery leading out of the heart). It is a type of birth defect. Coarctation means narrowing Hematological assessment Gingival pallor or bleeding Jaundice, sclera, retinal hemorrhage Impaired thought Process or lethargy Tachycardia Auscultate for murmurs Tachypnea, orthopnea, dyspnea Lymphadenopathy or tenderness Abdominal tenderness, Hepatomegaly, splenomegaly Joint swelling, Bone and joint tenderness Blood in urine and abnormal Mentsraul bleeding Pallor,flushing Jaundice, Purpura, Petichiae, Scratch marks cyanosis Decreased muscle mass Palpate decreased cap fill time Disorders of Hematological Function • Anemia: The condition of having less than the normal number of red blood cells or less than the normal quantity of hemoglobin in the blood. The oxygencarrying capacity of the blood is, therefore, decreased Failure to produce (hem)oglobin due to lack of iron In anemia selective vasoconstriction of blood vessels allows nonvital areas to be bypassed to allow more blood to flow into critical areas. The skin is one of the areas to be considered “nonvital” and the result is pallor. Iron needed to bind O2 Tissue hypoxia= ↑cardiac input= ↓PVR & ↓blood viscosity (thinner blood) = tachycardia and heart murmur Iron containing O2 transport protein that carries O2 from the lungs to the body Reduces O2 carrying capacity of the blood O2 state to the tissues: dyspnea on exertion, fatique, fainting, lightheadedness, tinnitus, headache A genetic disorder characterized by an abnormal form of hemoglobin within the erythrocyte Damaged sickle RBC’s clump together and stick to the walls of blood vessels, blocking blood flow causing sever pain and permanent damage to brain, heart, lungs, kidneys, liver, bones, and spleen Ischemia in the small blood vessels and infarction in the small bones ↓ O2 = sickle shaped red blood cells break apart not acting effectively ↑Risk of infection due to damaged spleen from sickled cells getting trapped Ischemia in the small blood vessels and infarction in the small bones Aplastic Anemia is a rare but potentially life threatening syndrome of bone marrow failure characterized by pancytopenia ↓RBC’s fatigue due to ↓O2 infections Bruising and bleeding Failure to produce hemoglobin due to lack of iron •Iron replacement therapy •Nutritional or dietary counseling •Treatment of underlying cause broad spectrum antibiotics •Infection •Pain •Fatigue •Shortness if breath •Transfusions as needed •Isolation precautions per institute (reverse isolation) •Pallor •Dyspnea •Petechiae •bleeding •Fever •Infection Pain medications, local heat application ** hydration to prevent sickling Administer O2, semifowlers postion Good oral hygiene, patient safety Prophylactic antibiotics platelets bleeding •Prevent bruising •Control bleeding •Counsel family to not use salicylate drugs •Transfusion of RBC’s •IV gamma globulin and anti-D antibody therapy •splenectomy Idiopathic thrombocytopenic purpura (bleeding in the tissue) A bleeding disorder in which the immune system destroys platelets, which are necessary for normal blood clotting. Persons with the disease have too few platelets in the blood *antiplatelet antibody in the spleen Hemophillia • Hereditary (x-linked recessive transmitted by females found predominately in males) bleeding disorder characterized by deficincy in a blood clotting factor (*factor VIII{A} or IX {B}) Prednisone: decreases antiplatelet antibodies platelets Bleeding into the tissue Bruising and petichiae Minimize bleeding IVIG Anti D antibody Disorders of Hematological Function Leukemia -ALL (acute lymphoblastic leukemia) uncontrolled proliferation of blast cells,which accumulate in the marrow causing crowding and depression of other cells • Hodgkins diseaseThis is a malignant lymphoma distinguished by painless, progressive enlargement of lymphoid tissue. Assessment of the Immune System Conjunctival redness Temperature for hyperthermia Palpate for adenopathy Auscultate for abnormal Breath sounds Inspect skin for hives, edema, lesions Auscultate for tachycardia Palpate for spleneomegaly Assess the joints for Swelling, redness, Tenderness, decreased mobility Disorders of the Immune System Infection with HIV produces Lymphopenia resulting in immunosupression and AIDS Symptoms may not Appear for 1 to 2 yrs •Nonspecific clinical manifestations •Prevent opportunistic infections •Administer prophylactic therapy for P. carnii (co-trimoxazole) beginning at 6 mos of age •Immunizations •Pulmonary hygiene •Promote adequate nutrition •Foster healthy growth and development Disorders of the Immune System Clinical manifestations: •Daily afternoon temperature spikes •macular rash on trunk and extremities •joint involvementswelling, pain, redness Medical management •Nonsteroidal antiinflammatory drugs •antirheumatic drugs •cytotoxic drugs •corticosteroids Assessment of the Respiratory System Observe for Alertness, change In mental status Temperature for hyperthermia Auscultate for abnormal Breath sounds Monitor respirations for rate, depth, and quality, Note any dyspnea, use of accessory muscles Percuss for dullness which indicates fluid Inspect skin color changes, especially cyanosis Intercostsal, suprasternal, Sternal and substernal retractions Chest diameter Disorders of the respiratory system Bronchopulmonary Dysplasia Premature lungs needing mechanical ventilation (high 02 and PIP) can injure the aveolar Saccules and lead to fibrosis of these structures •Long term O2 therapy •Cyanosis when breathing RA •Manifestations of right sided failure •Administer medications: bronchodilators, diuretic •Planned rest periods to decrease respiratory effort and conserve energy •Small frequent meals to prevent over distension of stomach •Counsel parents in ways to prevent respiratory infection •Teach parents CPR Disorders of the respiratory system • pneumonia Acute inflammation of the lung parenchyma (bronchioles, alveolar ducts, and sacs, and alveoli) Impairs gas exchange •Antibiotics if bacterial •Assess for respiratory distress •Provide family teaching Respiratory Distress •Wheezing, crackles •Use of accessory •muscles Disorders of Respiratory FunctionBronchitis/Bronchiolitis •Wheezing •Crackles •Tachypnea •Retractions Viral infection of the lower respiratory tract characterized by inflammation of the Bronchioles and production of mucous (usually caused by RSV) •Assess for respiratory Distress •Contact isolation •Prescribed Medications (RT) •O2 if needed •Fluids Asthma is a chronic, reversible, obstructive airway disease, triggered by various stimuli Inflammation and edema of muscle (spasms) •Wheezing •Use of accessory muscles Production of thick mucosa resulting in increased airway resistance, premature closure Of airways, hyperinflation, increased work of breathing, impaired gas exchange •Assess respiratory status •Administer prescribed meds •Promote adequate O2 •Fowler’s position •Increased RR •Cough •Fatigue •Anxiety •dyspnea Disorders of the respiratory system • Respiratory distress syndrome- mainly caused by a lack of a slippery, protective substance called surfactant, which helps the lungs inflate with air and keeps the air sacs from collapsing. Common in premature babies whose lungs are not fully developed. • • • • • • Sudden infant death syndrome Acute pharyngitis (sore throat)-inflammation of the pharynx Tonsillitis Croup – inflamation of the larynx (voice box)** Acute epiglotitis –bacterial infection of t he epiglottis Pulmonary tuberculosis-chronic bacterial infection caused by bacillius mycobacterium tuberculosis • Cystic fibrosis- an inherited disorder of the exocrine glands characterized by excessive thick mucous that obstructs the lungs and GI tract Measure height And weight for growth failure Assessment of the GI System Temperature for hyperthermia Inspect abdomen for distention, depression, umbilical herniation Auscultate to assess bowel sounds (do first) Palpate for tenderness, rigidity, masses and organomegaly Inspect skin for pallor, jaundice, carotenimia Inspect mouth For caries, periodontal Disease, lesions, And clefts Palpate hard and soft palates for defects Inspect the anus for rectal bleeding and nonpatency Disorders of Gastrointestinal Function Cleft lip and cleft palate are birth defects that affect the upper lip and roof of the mouth. They happen when the tissue that forms the roof of the mouth and upper lip don't join before birth. The problem can range from a small notch in the lip to a groove that runs into the roof of the mouth and nose. This can affect the way the child's face looks. It can also lead to problems with eating, talking and ear infections. •Ensure adequate intake of food and fluids without aspiration. •Special feeding devices may be used. •Frequent burping is necessary. •Assist parents in dealing with the diagnosis Treatment usually is surgery to close the lip and palate. Doctors often do this surgery in several stages. Usually the first surgery is during the baby's first year. With treatment, most children with cleft lip or palate do well. Disorders of Gastrointestinal Functionconstipation/dehydration The passage of hardened stools; may be associated with failure of complete evacuation of the colon with defecation •Add fluid or carbohydrate to the formula, add foods with bulk, and increase fluid intake. •Manually dilate the sphincter; administer mild laxatives/enemas. •Obtain history of bowel patterns educate on dietary changes and normal stool patterns. Disorders of Gastrointestinal Function- diarrhea/gastroenteritis • May be a result of a number of disease processes that cause abnormal losses through the skin, respiratory, renal, and GI systems – vomiting/diarrhea • Diarrhea- A disturbance in intestinal motility characterized by an increase in frequency, fluid content, and volume of stools •Assess for clinical manifestations of dehydration. •Observations should include I&O; vital signs; body weight; skin color, temperature, and turgor; capillary refill; presence or absence of the sensation of thirst; and in infants, assessment of the fontanels. •I&O, promotion of rehydration, correction of electrolyte imbalances, provision of age-appropriate nutrition, prevention of the spread of the diarrhea, prevention of complications, support of the child and family Disorders of Gastrointestinal Function• Gastroesophageal reflux The backflow of gastric contents into the esophagus resulting from relaxation or incompetence of the lower esophageal sphincter • Hypertrophic pyloric stenosis Pyloromytomy: Relieves obstruction Narrowing of pyloric sphincter at the outlet of the stomach • Intusseception Telescoping of one portion of the Intestine into an adjacent portion Causing an obstruction • Hirschprungs disease Congenital anomaly characterized by absence of nerves to a section of the intestine causing inadequate mobility Which leads to the absence of propulsive movements, causing accumulation of intestinal contents and distention of bowel Disorders of Gastrointestinal Function-hernias • • • • • Umbilical Femoral Inguinal Hiatal Diaphragmatic A protrusion of the bowel through an abnormal opening in the abdominal wall Most common in children Surgical repair Usually closes by the time the child is 3 years old Measure height And weight for growth failure Assessment of the GU System Uremic encephalopathyLethargy, poor concentration, confusion Temperature for hyperthermia Ear abnormalities Monitor RR for abnormal rate and depth of respiration Monitor blood Pressure for hypo Or hypertension Abdominal distension Bladder For distension Palpate kidneys for Tenderness, and enlargemnt Hypospadias, epispadias Inspect skin for peripheral cyanosis, slow cap refill time, pallor, peripheral edema Inspect the anus for rectal bleeding and nonpatency Disorders of Genitourinary Function• • UTI- characterized by inflammation, usually of bacterial origin, of the urethra, bladder, ureters, or kidneys Nephrotic syndrome- characterized by proteinuria, hypoalbuminemia, hyperlipidemia, altered immunity and edema. Increased permeability to protein, protien leaks through the glomerular membrane resulting in albumin in the urine. Once albumin is lost colloidal osmatic pressure decreases permiting fluid to escape from the intravascular spaces to the intirstial spaces. The volume decrease stimulates antidiuertic hormone to reabsorb water = edema. • Acute glomerulonephritis- antibodies interact with antigens that remain in the glomeruli, leading to immune complex formation and tissue injury, filtration decreases and excretion of less Na and H2O. High Blood pressure, edema, and heart failure may result. • Wilm’s tumor- • Structural defects of gu tract Assessment of the EndocrineSystem Measure height And weight for growth Failure, plot size of head Assess vision Monitor pulse Increase= hyperthyroid Decrease=hypothyroid Auscultate to note for murmurs Palpate hair & nails Lethargy, poor concentration, confusion, irritability Facial abnormalities, mouth for abnormal odors and Dental delay’s Monitor blood Pressure for hypo Or hypertension Assess for sexual development Assess muscle Strength and tone Inspect skin for color changes, hirsutism, easy bruising Palpate to note dryness, coldness, changes in texture Disorders of Endocrine Function • Hypothyroidism • Hyperthyroidism A chronic condition Characterized by inadequate amount of thyroid hormone to meet metabolic needs. Congenital- T4 is not produced which is essential for growth and development especially brian development, left untreated = MR. Acquired- inadequate amount of T4 • Diabetes mellitus 3 p’s •Polydipsia •Polyuria •Polyphagia A chronic metabolic disorder that results from either a partial or complete deficiency in insulin. Type 1- characterized by beta cell destruction, leading to absolute insulin deficiency. Type II- insulin resistance, progressive deterioration of Insulin secretion Assessment of the Musculoskeletal System Measure height And weight for growth Inspect posture and gait Palpate spine to assess curvature Palpate boney Structures for tenderness, Masses, lesions Assess, muscle mass, tone Observe for structural abnormalities Asymmetrical limbs Disorders of Musculoskeletal Function Scoliosis Legg-Calvé-Perthes Disease •Developmental Dysplasia of the Hip Surgery to correct A spinal deformity that usually Involves lateral curvature of the Spine, spinal rotation, and thoracic Kyphosis (hunch back) A disorder caused by decreased blood supply to the femoral head; results in epiphyseal necrosis and degeneration A developmental abnormality of the femoral head, the acetabulum, or both; subluxation of the hip Disorders of Musculoskeletal Function Osteomyelitis Talipes (Clubfoot) •Infection within the bone •In children, the metaphysis of the femur, the tibia, and the humerus are the areas most affected. •It can occur at any age; the peak incidence in children is between ages 3 and 15 years, and boys are affected twice as often as girls. •Congenital deformity of the foot and ankle •Varies in severity; may involve one foot or both feet •Manipulation and application of a series of short leg casts; changed weekly to allow for further manipulation Disorders of Musculoskeletal Function Septic Arthritis •Duchenne’s Muscular Dystrophy A sex-linked inherited disorder characterized by gradually progressive skeletal muscle wasting and weakness Joint aspiration and surgical irrigation Broad-spectrum IV antibiotics Fractures An infection of a joint, which can occur from bacteria in the blood or as a direct extension of an existing infection Most common sites in children are long bones, clavicles, wrists, fingers, and skull. No effective treatment Assessment of the Neurological System Measure head size, Palpate fontanels Tachycardia Increased ICP Assess LOC, Cerebullar status- gait Balance and coordination Cranial nerve function Esp pupillary response, Taste, olfaction, and tactile sense Hypertension Increased ICP Assess reflexes Assess muscle tone and strength Disorders of Neurological Function Meningitis An infection of the meninges that is usually caused by bacterial invasion and less Common by viruses. The bacteria Enter the meniges through the blood stream and spread through the csf. Children under 2- poor feeding, irritability And lethargy, high pitched cry, bulging Fontanel, fever, resistance to being held, Opisthotonos (hyperextension of the Neck) •Check for neurolical signs and monitor LOC •Administer prescribed meds (antibiotic, steroid for cerebral Edema, anticonvulsant) •Keep room quite and decrease Environmental stimuli Older children- respiratory or GI problems, nuchal rigidity (stiff neck), HA, kernigs sign, bruzinski sign, petichial rash Disorders of Neurological Function Occurs with a number of anomalies A condition caused by an imbalance in the production and absorption of CSF In the ventricular system. When production exceeds absorption, CSF Accumulates, usually under pressure and Produces a dilation of the ventricles. Communicating hydrocephalus- an impaired Absorption of CSF in the arachnoid space Noncommunicationg hydrocephalus- obstruction to the flow of CSF through the ventricular system Increased ICP- HA, emesis, irritability, Lethargy, apathy, and confusion Disorders of Neurological Function Surgical treatment- removal of obstruction and insertion of shunts to provide primary drainage of the CSF to an extracranial compartment, usually the peritoneum (ventriculperitonel shunt or VP shunt) Disorders of Neurological Function Spina Bifida Defective closure of the vertebral Column that may occur anywhere But usually occurs in the lumbosacral area. •Occulta- does not affect spinal cord May be dimpling of the skin, nevi, hair tuft •Meningocele- sac consisting of meninges and CSF protruding outside the vertebrae. The spinal cord is not involved Myelomeningocele (most common)Similar to meningocele but spinal Cord and nerve roots are involved Resulting in sensorimotor deficits, Urinary and bowel problems No cure. Surgery to minimize infection. Preoperatively- apply a sterile dressing To the lesion and constantly moisten it With saline. Use protective devices And handle infant with care. Disorders of Neurological Function • Encephalitis- An inflammation of the CNS, mainly the brain and spinal cord • Cerebral palsy- group of disabilities caused by injury or insult to the brain either before or during birth • Seizure disorders- disturbances in normal brain function that result in abnormal electrical discharges in the brain, which can cause LOC, uncontrolled body movements, changes in behaviors and sensation, and changes in the autonomic system. Many underlying causes: •Prenatal or perinatal hypoxia •Infection •Congenital malformaiton •Metobolic disturbances •Lead poisoning •Head injury •Tumor •Medication •Toxin exposure •Administer prescribed meds •Prevent injury •Document all seizure activity Disorders of Integumentary Function Antihistamines Clip fingernails • Contact – inflammation of the skin resulting from contact with environmental antigens • Diaper- form of contact dermatitis, exposure to feces and urine Keep the diaper area clean and dry; change diapers as soon as possible; cleanse area with mild soap and water, pat dry. • Atopic (eczema)- a pruritic response Hydration of the skin; control pruritus; decrease inflammation; and prevent secondary infections. • Seborrheic – cradle cap Crusts should be soaked with warm water and compresses until loosened; shampoo and rinse. Disorders of Integumentary Function • Acne Vulgaris – inflammatory process of the skin commonly seem in adolescents meticulous skin care is emphasized • Psoriasis- a chronic proliferative skin disorder characterized by thick, scaly patches and inflammation • Herpes Simplex – a common infection, transmitted by direct contact of infected body fliuds with nonintact skin or mucous membranes • Candidiasis (thrush)-white patches of candida Nystatin suspension; frequently found on moist tissues, tongue, administer after buccal cavity, vagina feedings. Inform parents that the full 7-day course of nystatin is to be completed. Teach parents to sterilize bottles, nipples, pacifiers, and teethers Disorders of Integumentary Function • Parasitic infections –scabies, head lice • Bacterial Infections- impetigo, folliculitis, and cellulitis The assessment of systemic signs and symptoms, areas involved, and appearance of lesions are helpful in establishing the type of infection.