Neurological Disorders in the Pediatric Patient Why is the CNS function so important? What does it do? What happens with impairment? What affects the degree of disability? Changes to be noted in pediatric neurological disorders Reflexes: may be hypo/hyper LOC: may have altered mental status Cranial nerves: I, III II, IV, VI III, VIII V,VII IX, X Neuro assessment, cont. Vital signs:changes in BP, HR Eyes: changes in pupils,focus,gaze Behavior: subtle Respiratory status: assess 1st Motor function: movement? Spontaneous? Skin: dry vs. diaphoretic Neurological System of Children Top Heavy Cranial bones- thin, not well developed Brain highly vascular with small subarachnoid space Excessive spinal mobility Wedge-shaped cartilaginous vertebral bodies Assessment findings in children with neurological dysfunction Increased Intracranial Pressure (ICP) Reflects the pressure exerted by the blood, brain, CSF and any other spaceoccupying fluid or mass (tumors) Pressure sustained at 20mm Hg or higher Changes in pressure present with altered assessments other than normal Altered Mental Status Mnemonic = Mitten Metabolic Infections Toxins Trauma Endocrine Neurological/Neoplasm Assessment: Infant Irritability and restlessness Full to bulging fontanelles Increase in FOC Poor feeding, poor sucking, projectile vomiting Distension of superficial scalp veins Nuchal rigidity and seizures (late signs) Assessment: Child early signsIrritability, lethargy Sudden change in mood Headache, poor feeding Vomiting Ataxia Nuchal rigidity Deterioration of cognitive ability Assessment Child: Late signs Changes in Vital signs Seizures Photophobia Positive Kernig’s sign Positive Brudzinski’s sign Opisthostonos Therapeutic Intervention: Nursing care Medications Corticosteroid Decadron Osmotic diuretic Mannitol Nursing Care Minimize activity Monitor IV rate Place in semi-fowlers Monitor VS, Neuro VS, and behavior Treat for pain Organize care Educate parents Critical Thinking What would you expect as a first sign of IICP in an infant? What would you expect as an initial sign of IICP in a 10 year old child? Hyperfunction/Hypofunction Pediatric Seizures Epilepsy vs. “seizure episode” • Status epilepticus Febrile seizures- occur as a result of rapidly increasing core temperature (101.8 F– 38.8C) General seizures- occur as a result of insult of the nervous system Clinical Manifestations Generalized: Tonic-clonic- loss of consciousness(formerly called grand mal) Absence seizures-may have minor motoratonic (formerly called petit mal) Partial seizures- partial simple or partial complex (may be focal or r/t tumors) Diagnostic Tests: EEG CT, MRI Lumbar puncture CBC Metabolic screen for glucose, phosphorus and lead levels Jitteriness –vs- Seizure Jittery Seizure Responsive Not responsive to stimuli Gaze Okay Abnormal gaze Goals: What is the primary nursing goal when caring for the individual experiencing a seizure? What preventive measures does the nurse provide? How does the nurse maintain the airway of an individual experiencing a seizure? What is the priority nursing intervention following a seizure? Long term goal for children with seizure disorders Identify the cause and eliminate the seizure with minimum side effects using the least amount of medication while maintaining a normal lifestyle for the child Meningitis Bacterial Potentially fatal; abx given prophylactically if bacterial suspected. May kill within 24 hrs C/S take 72 hrs to process Infants at greatest risk Nuchal rigidity Severe headaches Contagious Viral Same s/s but milder and shorter duration May follow a viral infection May be accompanied by rash Nuchal rigidity Ataxia Not contagious Assessment and diagnostics: Bacterial Meningitis Streptococcus pneumoniae most common pathogen Diagnostics: LP, CSF eval (↑ WBCs, gram stain +) Treatment: ABCDs, cerebral edema, seizure control, abx, steroids Prevention: Vaccination (HiB, Pneumococcal vaccine) Assessment and diagnostics: Viral Meningitis May be preceded by viral infection, rash Diagnostics: LP, CSF eval (mildly ↑WBCs, negative gram stain) Treatment: self limiting; resolves in 714 days, monitored in hospital until ABCs are stable Medications: antivirals (Acyclovir) Diagnostic Tests: Lumbar Puncture Serum Glucose Level Blood Cultures Nursing Care for diagnostics of possible meningitis Lumbar puncture ASO titer CBC/electrolytes/serum glucose Hydrocephalus Hydro= Water Cephaly= of the head/brain Etiology and Pathophysiology: Congenital anomalies Trauma Unknown causes Types of Hydrocephalus Non-communicating or Obstructive Communicating Clinical Manifestations Infants- prior to fusion of cranial sutures 1. 2. 3. 4. 5. FOC increased at birth Changes in assessment of skull Forehead Eyes Behavior changes After closure of cranial sutures: 1. 2. Eyes S & S of ICP Diagnostic Tests LP MRI/ CT scan Skull X-ray FOC Transillumination Interventions: Surgical Shunting to bypass the point of obstruction by shunting the fluid to another point of absorption Complications of Shunts Infections Blocked shunts Seizures Nursing Interventions Monitor VS and neurological status Assess functioning of the shunt Assess operative site Assess for infection Positioning of the patient Activity of patient Promote nutrition Education Critical Thinking What is the most important assessment data on a child who has just had a shunt placement for hydrocephalus? What is the most important teaching for the parents or caregivers? Spina Bifida Most common defect of the CNS Occurs when there is a failure of the osseous spine to close around the spinal column. Types of spina bifida Meningocele: sac filled with spinal fluid and meninges Myelomeningocele: more severe, sac filled with spinal fluid, meminges, nerve roots and spinal cord. Clinical Manifestations: Visualization of the defect Motor sensory, reflex and sphincter abnormalities Flaccid paralysis of legs- absent sensation and reflexes, or spasticity Malformation Abnormalities in bladder and bowel function Diagnostic Tests: Prenatal detection Ultrasound Alpha-fetoprotein Following Birth: NB assessment X-ray of spine X-ray of skull Surgical Intervention Immediate surgical closure Prior to closure keep sac moist & sterile Maintain NB in prone position with legs in abduction preoperatively Nursing Interventions: Pre-OP: Meticulous skin care Protect from feces or urine Keep in isolette Post-Op Nursing Interventions Assess surgical site Monitor VS and neuro VS Institute latex precautions Encourage contact with parents/care givers Positioning Skin Care Nursing Interventions cont... Antibiotic therapy Prevent UTI Education Emphasize the normal, positive abilities of the child Critical Thinking Would you expect a 5-year-old with meningomyelocele to have bladder/bowel sphincter control? Which type of neural tube defect is most likely to have no outward signs or symptoms? Cerebral Palsy (CP) Static Encephalopathy- spastic CP most common type (80%) Nonspecific term give to disorders characterized by impaired movement and posture Non-progressive Abnormal muscle tone and coordination Assessment Jittery (easily startled) Weak cry (difficult to comfort) Experience difficulty with eating (muscle control of tongue and swallow reflex) Uncoordinated or involuntary movements (twitching and spasticity) Assessment cont... Alterations in muscle tone Abnormal resistance Keeps legs extended or crossed Rigid and unbending Abnormal posture Scissoring and extension (legs feet in plantar flexion) Persistent fetal position (>5 months) Diagnostic Tests: EEG, CT, or MRI Electrolyte levels and metabolic workup Neurologic examination Developmental assessment Complications Increased incidence of respiratory infection Muscle contractures Skin breakdown Injury Goals & Interventions: Early detection Head Injuries Concussions: Assessment and Nursing Care Grades 1-3: higher the number, more severe the injury Involves transient impairment “Second impact syndrome: Assess and manage according to grade Treatment is supportive Usually observed in the ED If unconscious > 5 minutes, may be admitted Removal from sports ranges from 1 wk-entire season Nurse as Provider: Care Plan Brian, 10 years old, sustained a head injury when he collided with a tree while riding his bicycle.He did not have on a helmet. He is now unconscious in the PICU and is receiving an intravenous drip of Mannitol, central venous pressure monitoring, EEG and ECG monitoring, is being mechanically ventilated, and has a urinary catheter. Brian's parents have just arrived on the unit. How can the nurse prepare the parents for Brian's appearance? What are Brian's immediate needs? Fill in the appropriate steps of the Care Plan below for Brian for the next 24 hours. Assessment and Diagnosis Planning and Implementation Evaluation CASE STUDY: The nurse is assigned to an 14-year-old female who is being observed after a head injury sustained while playing soccer. She lost consciousness for a few minutes when it happened. What should the client and her parents be told about the recovery time after a concussion? What should the client and her parents be told about playing soccer again? What should the nurse tell the parents and the client about second impact syndrome? What can the family do to assess her symptoms at home and determine if she is ready to play competitive sports again? Mental Retardation “Significant sub average, general intellectual functioning existing concurrently with deficits in adaptive behavior and manifested during the developmental period”. American Association of Mental Deficiency Autism Not clearly understood Characterized by impaired social, communicative, and behavioral development Usually noted in the first year of life Nursing interventions/education Home setting -reduce environmental stimuli -communicate age appropriately; use of touch and verbalization -safety with toys and articles that could be harmful -routines: ritualism with ADLs -long term care to include therapists and support groups Acute care setting -keep one constant caregiver; room quiet as possible -may become aggressive when touched by a stranger; refer to parents for communication techniques -monitor for safety at all times: removing tubes, etc. -encourage to include therapists and support groups in care Down syndrome Trisomy 21- the most common chromosomal abnormality resulting in mild to profound mental retardation Assessment Primary concern with cardiac and GI anomalies What are the most obvious indications of Down’s Syndrome in a newborn? Goals and Interventions Primary focus on the parents and care givers to provide support and achieve a realistic view of the child’s capabilities Support siblings Refer to family counseling services Support parents in feelings of guilt and chronic sorrow