Systemic connective tissue disorders

2017-07-29T18:10:38+03:00[Europe/Moscow] en true Sjögren's syndrome, Systemic scleroderma, Behçet's disease, Kawasaki disease, Marfan syndrome, Dermatomyositis, Goodpasture syndrome, Microscopic polyangiitis, Polyarteritis nodosa, CREST syndrome, Granulomatosis with polyangiitis, Takayasu's arteritis, Connective tissue disease, Mixed connective tissue disease, Primrose syndrome, Arteritis, Thrombotic microangiopathy, Eosinophilic fasciitis, Inflammatory myopathy, Polymyositis, Cutaneous small-vessel vasculitis, Drug-induced lupus erythematosus, Polymyalgia rheumatica, Eosinophilia–myalgia syndrome, Congenital contractural arachnodactyly, Undifferentiated connective tissue disease, Inclusion body myositis, Lethal midline granuloma, Juvenile dermatomyositis, Dermatopolymyositis flashcards Systemic connective tissue disorders
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  • Sjögren's syndrome
    Sjögren's syndrome (SjS, SS) is a long-term autoimmune disease in which the moisture-producing glands of the body are affected.
  • Systemic scleroderma
    Systemic sclerosis, or systemic scleroderma, is an autoimmune disease of the connective tissue.
  • Behçet's disease
    Behçet's disease is a rare immune-mediated small-vessel systemic vasculitis that often presents with mucous membrane ulceration and ocular problems.
  • Kawasaki disease
    Kawasaki disease is a disease in which blood vessels throughout the body become inflamed.
  • Marfan syndrome
    Marfan syndrome (MFS) is a genetic disorder of connective tissue.
  • Dermatomyositis
    Dermatomyositis (DM) is a connective-tissue disease related to polymyositis (PM) that is characterized by inflammation of the muscles and the skin.
  • Goodpasture syndrome
    Goodpasture syndrome (GPS; also known as Goodpasture’s disease, antiglomerular basement antibody disease, or anti-GBM disease) is a rare autoimmune disease in which antibodies attack the basement membrane in lungs and kidneys, leading to bleeding from the lungs and kidney failure.
  • Microscopic polyangiitis
    Microscopic polyangiitis is an ill-defined autoimmune disease characterized by a systemic, pauci-immune, necrotizing, small-vessel vasculitis without clinical or pathological evidence of necrotizing granulomatous inflammation.
  • Polyarteritis nodosa
    Polyarteritis nodosa, also known as panarteritis nodosa, periarteritis nodosa, Kussmaul disease, Kussmaul-Maier disease or PAN, is a systemic vasculitis of small- or medium-sized muscular arteries, typically involving renal and visceral vessels but sparing the pulmonary circulation.
  • CREST syndrome
    CREST syndrome, also known as the limited cutaneous form of systemic sclerosis (lcSSc) is a multisystem connective tissue disorder.
  • Granulomatosis with polyangiitis
    Granulomatosis with polyangiitis (GPA), previously known as Wegener's granulomatosis (WG), is a systemic disorder that involves both granulomatosis and polyangiitis.
  • Takayasu's arteritis
    Takayasu's disease (also known as "aortic arch syndrome," "nonspecific aortoarteritis," and "pulseless disease") is a form of large vessel granulomatous vasculitis with massive intimal fibrosis and vascular narrowing, most commonly affecting often young or middle-age women of Asian descent, though anyone can be affected.
  • Connective tissue disease
    A connective tissue disease is any disease that has the connective tissues of the body as a target of pathology.
  • Mixed connective tissue disease
    In medicine, mixed connective tissue disease (also known as Sharp's syndrome), commonly abbreviated as MCTD, is an autoimmune disease in which the body's defense system attacks itself.
  • Primrose syndrome
    Primrose syndrome is a rare, slowly progressive genetic disorder that can vary symptomatically between individual cases, but is generally characterised by ossification of the external ears, learning difficulties, and facial abnormalities.
  • Arteritis
    Arteritis is the inflammation of the walls of arteries, usually as a result of infection or autoimmune response.
  • Thrombotic microangiopathy
    Thrombotic microangiopathy, abbreviated TMA, is a pathology that results in thrombosis in capillaries and arterioles, due to an endothelial injury.
  • Eosinophilic fasciitis
    Eosinophilic fasciitis (/ˌiːəˌsɪnəˈfɪlɪk ˌfæʃiˈaɪtᵻs, ˌiːoʊ-, -ˌfæsi-/), also known as "Shulman's syndrome", is a form of fasciitis, the inflammatory diseases that affect the fascia, the connective tissues surrounding muscles, blood vessels and nerves.
  • Inflammatory myopathy
    Inflammatory myopathy (inflammatory muscle disease or myositis) is disease featuring weakness and inflammation of muscles and (in some types) muscle pain.
  • Polymyositis
    Polymyositis (PM) ("inflammation of many muscles") is a type of chronic inflammation of the muscles (inflammatory myopathy) related to dermatomyositis and inclusion body myositis.
  • Cutaneous small-vessel vasculitis
    Cutaneous small-vessel vasculitis (also known as "Cutaneous leukocytoclastic angiitis", "Cutaneous leukocytoclastic vasculitis", "Cutaneous necrotizing venulitis" and "Hypersensitivity angiitis") is inflammation of small blood vessels (usually post-capillary venules in the dermis), characterized by palpable purpura.
  • Drug-induced lupus erythematosus
    Drug-induced lupus erythematosus (DIL or DILE) is an autoimmune disorder (similar to systemic lupus erythematosus [SLE]) caused by chronic use of certain drugs.
  • Polymyalgia rheumatica
    Polymyalgia rheumatica (PMR) is a syndrome with pain or stiffness, usually in the neck, shoulders, upper arms, and hips, but which may occur all over the body.
  • Eosinophilia–myalgia syndrome
    Eosinophilia–myalgia syndrome (EMS) is an incurable and sometimes fatal flu-like neurological condition linked to the ingestion of the dietary supplement L-tryptophan.
  • Congenital contractural arachnodactyly
    Beals syndrome (congenital contractural arachnodactyly, Beals-Hecht syndrome) is a rare congenital connective tissue disorder.
  • Undifferentiated connective tissue disease
    Undifferentiated connective tissue disease (UCTD) is a disease in which the body mistakenly attacks its own tissues.
  • Inclusion body myositis
    Inclusion body myositis (IBM) is an inflammatory muscle disease characterized by slowly progressive weakness and wasting of both distal and proximal muscles, most apparent in the muscles of the arms and legs.
  • Lethal midline granuloma
    Lethal midline granuloma is a condition affecting the nose and palate.
  • Juvenile dermatomyositis
    Juvenile dermatomyositis (JDM) is an idiopathic inflammatory myopathy (IMM) of presumed autoimmune dysfunction resulting in muscle weakness among other complications.
  • Dermatopolymyositis
    Dermatopolymyositis (also called PM/DM) is a family of myositis disorders that includes polymyositis and dermatomyositis.