2023-10-22T20:47:13+03:00[Europe/Moscow] en true <p>bronchodilator, hypertonic saline, Pulmozyme, anti-pseudomonal ABs (if indicated) </p>, <p>heel prick at birth, genetic testing, sweat test </p>, <p>&gt;50% for age</p>, <p>&gt;=23; &gt;=22</p>, <p>test dose in clinic; can cause airway hyper-reactivity </p>, <p>Creon, zenpep, pertzye</p>, <p>lipase units per kg</p>, <p>constipation; colonic stricture (rare)</p>, <p>Pertzye; acid suppression therapy </p>, <p>twice daily with fat-containing meal + enzymes</p>, <p>lung function; weight </p>, <p>chest tightness, increased intra-ocular pressure, liver dysfunction</p>, <p>annual eye exam (patients &lt;18), LFTs </p>, <p>Tobramycin, aztreonam </p>, <p>tobramycin </p>, <p>cayston</p>, <p>bethkis, kitabis</p>, <p>Tobi Podhaler</p>, <p>tobramycin nebulizer</p>, <p>can't be taken with other CF therapies, fastest neb</p>, <p>&gt;=60</p>, <p>30-59</p>, <p>A,D,E,K</p> flashcards
CF (Therapeutics)

CF (Therapeutics)

  • bronchodilator, hypertonic saline, Pulmozyme, anti-pseudomonal ABs (if indicated)

    What is the order of therapy for CF? (4)

  • heel prick at birth, genetic testing, sweat test

    How do we diagnose CF? (3)

  • >50% for age

    What is the pediatric weight goal?

  • >=23; >=22

    Goal BMI for Men?

    Goal BMI for women?

  • test dose in clinic; can cause airway hyper-reactivity

    When prescribing Hypertonic saline, what must be done prior?

  • Creon, zenpep, pertzye

    What are the PERTs? (3)

  • lipase units per kg

    How do we dose PERTs?

  • constipation; colonic stricture (rare)

    What can occur when PERTs are dosed too high? (2)

  • Pertzye; acid suppression therapy

    If a patient is still having malabsorption, what else can we consider adding?

  • twice daily with fat-containing meal + enzymes

    How do we dose CFTR modulators?

  • lung function; weight

    CFTR modulators can improve ________ & increase ________.

  • chest tightness, increased intra-ocular pressure, liver dysfunction

    What are AE's of CFTR modulators? (3)

  • annual eye exam (patients <18), LFTs

    What monitoring is done for CFTR modulators? (2)

  • Tobramycin, aztreonam

    What are the treatment options for Pseudomonas? (2)

  • tobramycin

    ______ is the only AB approved for pseudomonas in CF.

  • cayston

    aztreonam

  • bethkis, kitabis

    Tobramycin Nebulizer (2)

  • Tobi Podhaler

    Tobramycin DPI =

  • tobramycin nebulizer

    _________ provides a more rapid inhalation.

  • can't be taken with other CF therapies, fastest neb

    What is unique about Aztreonam? (2)

  • >=60

    What chloride levels indicate a CF diagnosis?

  • 30-59

    What chloride levels indicate further testing required?

  • A,D,E,K

    What are the fat-soluble vitamins? (4)