Cleft Palate &/or Velopharyngeal Inadequacy Assessment or How to Determine Nose vs. Mouth Sounds KSHA Conference Presentation 10/01/2010 Sally Helton, MS, CCC-SLP Speech/Language Pathologist Children’s Mercy Hospitals & Clinics Kansas City, Missouri Hearing & Speech Department 913-696-5756 Introduction • • • • • • • Educational Background # Years at CMHC # Years CMHC Cleft Palate/Craniofacial Team # Years CMHC FFVN Team # Years Member ACPA Primary Job Function Other Job Functions Intent of Presentation • To provide information regarding diagnostic assessment for communication disorders due to cleft lip &/or palate &/or velopharyngeal inadequacy • To provide information regarding other issues that impact cleft lip &/or palate &/or velopharyngeal inadequacy • To provide information regarding importance of team approach to treatment • To provide referral criteria for more advanced assessment, perceptual &/or instrumental Basic Terminology Cleft Lip • A cleft of the lip which may be: -complete or incomplete -unilateral or bilateral -extend to the nostril -extend to the alveolus Cleft Palate • A cleft of the palate which may be: -complete or incomplete -unilateral or bilateral Cleft Palate cont’d. -submucous -overt: observe one or more of: -bifid uvula -zona pellucida -muscular diastasis -notch in posterior border of hard palate Cleft Palate cont’d. • Submucous cont’d. -occult (hidden) Cleft Palate cont’d. • Variations • Incidence • Other Clefts • Classification Systems ACPA • American Cleft Palate-Craniofacial Association 22q deletion • Deletion of genetic material from chromosome 22 • Other names: 22q11.2 deletion Shprintzen’s Syndrome Velo-Cardio-Facial Syndrome 22q deletion cont’d. • Other manifestations • Organ systems affects • Variable expression • Incidence • Significance in regard to education Flexible Fiberoptic Video Nasopharyngoscopy (FFVN) • Invasive procedure used to evaluate the structure & function of the velopharyngeal mechanism during speech. Velopharyngeal Mechanism • Velo: velum/soft palate • Pharyngeal: lateral & posterior pharyngeal walls • Pharynx: part of throat between esophagus & nasal cavity Velopharyngeal Port • Port or gateway formed by action of the pharynx & velum to control the flow of air and sound through the mouth & nasal passages Velopharyngeal Valve • Valve which closes & opens velopharyngeal port between nasopharynx & oropharynx • Formed by velum & aided by posterior & lateral pharyngeal walls • Nasopharynx: part of pharynx above soft palate & just behind nasal cavity • Oropharynx: part of pharynx below soft palate at the level of the oral cavity Velopharyngeal Valve Velopharyngeal Closure • Closing of nasal cavity from the oral cavity • Accomplished by using velum & pharynx & possibly adenoid tissue • Directs airflow through mouth instead of the nose Velopharyngeal Valve Velopharyngeal Inadequacy (VPI/A) • Generic term • Refers to any abnormal velopharyngeal function • Diagnosed perceptually (by listening) Velopharyngeal Inadequacy cont’d. • 3 basic subtypes: -velopharyngeal insufficiency (VPI/S) -velopharyngeal incompetency (VPI/C) -velopharyngeal mislearning Subtypes CANNOT be distinguished perceptually. Subtypes are not mutually exclusive. Velopharyngeal Insufficiency (VPI/S) • Structural defect of the palate &/or pharyngeal area Velopharyngeal Incompetency (VPI/C) • Neurogenic impairment • Movement disorder/motor planning • Not structural Velopharyngeal Mislearning • Functional disorder • Faulty learning of articulation patterns • Sound (phone) specific nasal air emission (s) Relationship of VPI/A Types Learning (articulation disorder) VP Mislearning Anatomy (structure) VP Insufficiency (VPI/S) Physiology (movement) VP Incompetency VPI/C Relationship of VPI/A Types cont’d. • Significance of relationship: if types are not mutually exclusive, treatment will need to target all types presented by the patient Relationship of VPI/A Types cont’d. • Significance of relationship: diagnostic assessment needs to determine types of VPI/A the patient presents diagnostic assessment should include perceptual evaluation & possible instrumental/more invasive evaluation such as FFVN Relationship of VPI/A Types cont’d. • Instrumental diagnostic assessment with FFVN needs to be a VALID study • Use or attempted use of high pressure consonants is REQUIRED for a VALID FFVN study • If high pressure consonants are not being used/attempted, speech therapy should occur first. Areas of Assessment • History • Language • Articulation • Voice • Resonance • Fluency • Nasal Air Emissions (NAE) • Oral Mechanism/Oral Peripheral Examination • Velopharyngeal Adequacy Tools Needed for Assessment • Tissues • Articulation test & score form • Gloves • Flashlight • Mirror • Reinforcers/Toys • Language test & score form • Resonance/NAE protocol form (stimuli) • Tape recorder (optional) Tools Needed for Assessment cont’d. • CMHC Protocol • ACPA Universal Parameters for Assessment (The Cleft Palate-Craniofacial Journal, January 2008, Volume 45, Number 1, Henningsson et.al., pg. 1-17) Assessment-History Areas to Consider • Cleft: type & surgical &/or prosthetic management of • School History (including learning issues) • Medical • Psychological Issues • Speech Therapy • Feeding/swallowing • Parents’ Concerns/Perspective • Peer Interactions Assessment-History Type of Cleft/Surgeries/Prosthesis • Type of Cleft: - note type of cleft (i.e., left cleft lip & palate) • Surgeries Related to Cleft/VPI/A: - note surgeries regarding primary repair of cleft - note secondary surgeries in regard to VPI/A - note surgeries that may negatively impact VPA (i.e., tonsillectomy &/or adenoidectomy/T&A) • Prosthetic Management of Cleft/VPI: - note any prosthesis used in regard to cleft/VPI (i.e., palatal obturator, palatal lift) Assessment-History • Medical: Pregnancy Birth Newborn period Other conditions: heart congenital anomalies Significant illnesses/diseases Audiological Assessment-History • Speech Therapy: Enrollment: previous/ current length of enrollment # of sessions per week length per session group/ individual/combination Goals/Progress Treating SLPs name Results of Previous Evaluations Assessment-History • Parents’ Concerns/Perspective: Start with a general question: “How do you feel (name) is doing with communication/speech?” Follow-up with specific questions regarding: understandability, articulation skills, hypernasality/NAE, voice, language skills Assessment-History • School History: Name of School Grade Enrolled Regular Education/Special Education (or combination) Therapies Enrolled in Special Classes/Educational Help Receive Any teacher concerns regarding learning Results of recent reports/grades Assessment-History • Psychological Issues: -Obtain results of any psychological, educational &/or IQ testing, if available. Assessment-History • Feeding/Swallowing: -Inquire as to any history of difficulty with: sucking, chewing, swallowing -This includes both liquids & solids. - Any history of nasal regurgitation of liquids -Any issues with textures, temperatures, spiciness/blandness - Swallow studies/Oral Pharyngeal Motility (OPM) studies - History should be from birth to current age Assessment-History • Peer Interactions: - First find out if the child has opportunities for peer interactions -Then find out if they have age-appropriate interactions with their peers or if they have difficulties Determining Nasal Patency • Need to determine patency (airflow) of each nostril • Need to determine patency for both breathing & production of nasal sounds • If airflow is restricted or obstructed, it may mask SEVERITY &/OR INCIDENCE of resonance/NAEs Determining Nasal Patency cont’d. • Procedure: 1. Tell the patient to blow their nose. 2. Place the mirror under both nostrils (or one at a time). 3. Tell the patient to close their mouth & breath out of their nose. 4. Keep the mirror under the nostrils. 5. Tell the patient to say /m/. Determining Nasal Patency cont’d. • Place the mirror under both nostrils (or 1 at a time) Determining Nasal Patency cont’d. • Tell the patient to close their mouth and breathe out of their nose. Determining Nasal Patency cont’d. • Keep the mirror under the nostrils & tell the patient to say /m/. Determining Nasal Patency cont’d. • Variability in Responses Determining Nasal Patency cont’d. • Recording responses/information Recording Nasal Patency Information Nasal Obstruction: Right Nostril Occluded a. Inhalation/exhalation b. Sustained /m/ (3 secs.) none partial complete (Circle response) none partial complete Left Nostril Occluded none partial complete none partial complete Assessment-Articulation • Intent of Articulation Assessment: 1. To obtain as much information as possible regarding articulation abilities. Assessment-Articulation cont’d. • Intent of Articulation Assessment cont’d.: 2. Use information not only to diagnose articulation/phonological deficit/disorder BUT: a. Determine possible causes for deficit/ disorder b. Determine if attempt to use &/or use enough high pressure consonants to determine VP adequacy c. Determine if compensatory articulations are being used d. Help determine prognosis for improvement with/without speech therapy Assessment-Articulation cont’d. • General Guidelines: It is very important to watch the face/nose/mouth! Allows you to observe: nasal grimace, incorrect placement, facial/neck tension etc. True for both assessment & therapy. Assessment-Articulation cont’d. • General Guidelines cont’d.: Watch for lip & tongue mobility &/or restrictions. Watch for dental abnormalities which might impact correct sound production. This includes dental appliances. Watch for respiratory abnormalities. Assessment-Articulation cont’d. • Guidelines: 1. Transcribe the entire production phonetically including correct productions. 2. Note if response was spontaneous or imitative. Assessment-Articulation cont’d. • Guidelines cont’d.: 3. Use “narrow phonetic transcriptions” for errors not transcribable with normal phonetic symbols. Other Narrow Transcriptions • • • • • • • Nasal Air Emission / / Denasal / / Nasalized Resonance[ ] Unaspirated [ ] Unreleased [ ] Interdental [ ] Lateralized [ ] Other Narrow Transcriptions • Transcription Symbols for Compensatory Articulation Errors Assessment-Articulation cont’d. • Guidelines cont’d.: 4. Note any vowel errors. 5. If more than just a few nasal air emissions (NAE) occur, count as errors when scoring. Assessment-Articulation cont’d. • Guidelines cont’d.: 6. Do stimulability testing. 7. Note any differences during conversational speech. 8. Rate the overall intelligibility/understandability of speech. Assessment-Articulation cont’d. • Guidelines cont’d.: 9. Note any weak pressure consonants &/or reduced intra-oral air pressure. Assessment-Articulation cont’d. • Test Selection: Consider age of patient, language abilities etc. Want a test that will keep the patient’s interest. Want to assess sounds in as many positions as possible. Want to assess as many consonant blends as possible. Compensatory Misarticulations • • • • Learned articulation errors Are mostly errors of PLACEMENT Are typical to those with “cleft palate speech” Develop as a means or strategy to overcome structural difficulties due to the cleft • Are used to attempt to obtain valving for high pressure consonants • Become part of child’s phonology • Can be very persistent Types of Compensatory Misarticulations • • • • • • • • • • • • • Glottal Stops Laryngeal Stops Pharyngeal Stops Mid-dorsum Palatal Stops Laryngeal Fricatives Pharyngeal Fricatives Velar Fricatives Mid-dorsum Palatal Fricatives Posterior Nasal Fricatives Laryngeal Affricates Pharyngeal Affricates Mid-dorsum Palatal Affricates Posterior Nasal Affricates Types of Compensatory Misarticulations cont’d. • • • • Atypical Backing of /l/ Atypical Backing of /n/ Atypical Backing of /r/ Novel or idiosyncratic misarticulations Glottal Stop / / • Most common error • Normal sound in many languages – English: vowel initiation • Voiced Stop consonant with glottal placement • Laryngeal / Vocal cord valving – Adduct – Pressure build-up below glottis GLOTTAL STOP / / • Greater pressure builds up – Consonant substitution > vowel initiation • Excessive tension – Lower vocal tract – > intense opening / closing vocal cords – Ventricular vocal cords adduct / contact Glottal Stop / / • Substituted: whole class of stops • Frequently co-articulated – One manner of production – Two places of production • Deviant / nonphonemic place effects manner • Perceptually distinct – Pharyngeal stop / omission Glottal Stop / / Laryngeal Stop • Substitution for stop sounds • Base of tongue – Moves posteriorly toward PPW (posterior pharyngeal wall) – Epiglottis contacts PPW • Momentarily blocking airstream • Larynx thought to move – Superiorly – Assist stopping airflow Pharyngeal Stop • Lingua-pharyngeal consonant articulation – Contact: tongue base to PPW – Pressure build-up / Sudden release • • • • • Manner of production: Stop/Plosive Contact: high or low Substitution for /k/ , /g/ Not used as co-articulation Voiced / / or unvoiced / / Pharyngeal Stop Mid-Dorsum Palatal Stop • Stop consonant made in approximate place of “y” • Mid-section of tongue (dorsum) contacts mid-section of palate • Typically substituted for /t/ or /k/ (voiceless) & /d/ or /g/ (voiced) • Perceptually is a cross between /t-k/ or /d-g/ • May represent a place compromise between anterior & posterior • May have been learned to use tongue to occlude palatal fistula • Only mid-dorsum compensatory articulations are not behind the uvula for place of articulation • Voiced / / or unvoiced / / Laryngeal Fricative • • Substitution for fricative sounds • Tongue base • Larynx moves up – Posterior • Variant – Pushes epiglottis toward PPW – Narrows airstream Constriction – Epiglottis & PPW – Pharyngeal fricative Pharyngeal Fricative • • • • • • • Lingua-pharyngeal fricative articulation Tongue moves posteriorly toward PPW Dorsum of tongue flattened Constriction of airstream = frication Substituted: fricatives & affricates Co-articulation Voiced / / or unvoiced / / Pharyngeal Fricative Velar Fricative • Fricative production made at back velar for place of articulation • Similar to /k/ or /g/ but tongue isn’t touching the palate • Common substitution for sibilant fricatives or as distortion of /k/ or /g/ which then lack stop quality due to VP port leak • Seen with dysarthria due to reduced range of movement in back of tongue • Voiced / / or unvoiced / / Mid-Dorsum Palatal Fricative • Substitution for fricative sounds • Same positioning as mid-dorsum palatal stop but positioning creates frication • May be place compromise to attempt to achieve valving for airflow • Voiced / / or unvoiced / / Posterior Nasal Fricative • May be called velopharyngeal fricative • Turbulent VP fricative articulation occurring with small VP opening • Tongue moves back to help occlude the port (lingual assist), velum approximates PPW but does not touch. Result is constricted airflow through the VP port; velum “flutters” against PPW or adenoid pad • Perceived as frication/”snorting” • May occur as selective substitution for sibilant fricatives & affricates • Can be co-produced with any high pressure consonants • May be obligatory due to VPI/S or learned • Notable occurrence in individuals without clefts as phone specific nasal emission • Symbol: / / Laryngeal Affricate • Substitution: affricate sounds • Tongue base posterior – Epiglottis Brief contact PPW • Then constrict airstream • – Stopping – Then frication • Larynx moves superiorly Pharyngeal Affricate • Combines pharyngeal fricative & glottal stop • Less frequent in occurrence than glottal & pharyngeal stops as well as pharyngeal fricatives • Mostly substituted for oral affricates “ch” & “j” • Dorsum of tongue moves posteriorly to contact PPW • Tongue contact constricts airstream to create stopping followed by frication • Does not occur as co-articulation • Voiced / / or unvoiced / / Mid-Dorsum Palatal Affricate • Substitution for affricate sounds • Same positioning for mid-dorsum palatal stop but positioning creates affrication • May be place compromise to achieve valving for airflow • Voiced / / or unvoiced / / Posterior Nasal Affricate • Substitution for affricate sounds • Posterior dorsum of tongue & velum – Create at VP valve • Stopping • Frication • Audible NAE / Posterior Nasal Fricative • Amenable to speech treatment – Tongue placement / Oral airflow Atypical Backing of /l/ • • • • Backed oral production of /l/ Move place of production back to velar area Characteristic of cleft palate speech Less impact on intelligibility than other compensatory misarticulations • Symbol: / / Atypical Backing of /n/ • Backed production of /n/ • Placement may be anywhere on palate including velum • Characteristic of cleft palate speech • Less impact on intelligibility than other compensatory misarticulations • Symbol: / / Atypical Backing of /r/ • • • • Backed oral production of /r/ Placement is farther back, may be on velum Characteristic of cleft palate speech Less impact on intelligibility than other compensatory misarticulations • Symbol: / / Novel or Idiosyncratic Misarticulations • Individuals will make their own unique misarticulations • Idiosyncratic misarticulations tend to occur more in patients with cleft palate • Novel/idiosyncratic misarticulations may include compensatory error co-articulated with normal placement production with manner error or placement may be also in error Observations Regarding Compensatory Misarticulations • Are active errors • Can be changed in therapy • Need to eliminate/reduce as many as possible prior to FFVN for valid study • Are “stubborn”; therefore, really need to apply the “new pathways” techniques/principles Assessment-Resonance • Resonance -hypernasality -assimilative hypernasality -hyponasality -cul-de-sac -denasality -mixed resonance Assessment-Resonance cont’d. Definitions • Resonance: -vibratory response of a body or air-filled cavity to frequency of sound -quality of voice resulting from sound vibrations in pharyngeal, oral &/or nasal areas -refers to both perceptual & physical aspects Assessment-Resonance cont’d. Definitions • Hypernasality: -excess nasal resonance on vowels & vocalic consonants (i.e., “ir” as in “bird”), glides (“w, y”) or liquids (“l, r”) -transcribed as: ~ Assessment-Resonance cont’d. Definitions • Assimilative Hypernasality: -excess nasal resonance on vowels in presence of nasal consonants (“m, n, ng”) -transcribed as: ~ Assessment-Resonance cont’d. Definitions • Hyponasality: -reduction in nasal resonance -affects nasal consonants -is NOT opposite of hypernasality/can co-occur Assessment-Resonance cont’d. Definitions • Cul-de-sac Resonance: -blind pouch/passage with only one outlet -resonance sounds as if in a cave -created by trapping resonance (or sound) in back of mouth -tongue placed back in mouth toward pharyngeal wall Assessment-Resonance cont’d. Definitions • Denasality: -nasal air flow is completely blocked -prevents nasal air flow for nasal consonants -/m/ sounds like /b/ -/n/ sounds like /d/ -”ng” (as in “ring”) sounds like /g/ Assessment-Resonance cont’d. Definitions • Mixed Resonance: -combination of hypernasality, assimilative hypernasality, hyponasality, &/or cul-de-sac resonance -can have any combination -severity may vary between resonance types Assessment-Resonance cont’d. Procedure • Rating Scale: Numerous rating scales exist Ratings are usually descriptive & numerical Rating is SUBJECTIVE CMHC currently uses a 7-point scale CPCF Journal (January 2008) article shows how to convert various scales to a 4-point scale Assessment-Resonance cont’d. Procedure • Rating Scale cont’d.: CMHC 7-point rating scale: 7 None 6 5 Slight Mild 4 3 Mild-Mod Mod 2 1 Mod-Sev Severe Assessment-Resonance cont’d. Procedure • Hypernasality: Areas to Assess: Spontaneous Speech Sample Sustained Vowel Sentence Imitation task Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: Areas to Assess: Spontaneous Speech Sample Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: Areas to Assess: Sustained Vowel /i/ Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: 1. Place glove on your hand. 2. Tell child you’re putting the glove on because “in a little while I’m going to gently touch your nose”. 3. Tell child “we’re going to practice how long we can say a sound”. 4. Tell child “right now my hand with the glove is going to stay over here by me”. Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: 4. Tell child “I want you to say /i/ for as long as you can”. 5. Tell child “Let’s do it together”. 6. Tell child “Good! Now this time I want you to say /i/ until my finger is on your side of the table”. Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: 7. Tell child “Now I want you to say /i/ again for as long as you can (until my finger is on your side of the table). While you say /i/, I’m going to gently open & close your nose”. Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: Areas to assess: Sentence Imitation Task Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: 1. Tell child: “I want you to say what I say”. 2. Say “I see a big black dog”. 3. “Say it again”. “Good” 4. Do the same with the other 2 sentences: “Put your feet by the seat.” “He has a beet to eat.” Assessment-Resonance cont’d. Procedure • Hypernasality cont’d.: Sentence Imitation Task cont’d. Assessment-Resonance cont’d. Procedure • Assimilative Hypernasality: Area to assess: Sentence Imitation Task Assessment-Resonance cont’d. Procedure • Assimilative Hypernasality cont’d.: Area to Assess: Sentence Imitation Task cont’d. Assessment-Resonance cont’d. Procedure • Assimilative Hypernasality cont’d.: 1. Tell child: “I want you to say what I say”. 2. Say “Hand the mean dog some meat”. 3. Say “The swing is neat and clean”. Assessment-Resonance cont’d. Procedure • Hyponasality: Areas to Assess: Sustained nasal /m/ Sentence Imitation Task Assessment-Resonance cont’d. Procedure • Hyponasality cont’d.: 1. Tell child: “I want you to say what I say”. 2. Say “My mama makes lemon jam”. 3. Say “Nancy is a nurse”. Assessment-Resonance cont’d. Procedure • Other Resonance Types: Cul-de-sac, denasality, mixed resonance Specific stimuli not used Rate/make observations regarding while assessing other resonance areas & articulation as well as during conversational speech Assessment-Resonance cont’d. Procedure • Infant-Toddler Assessment: 1. SLP rates severity of overall hypernasality in spontaneous speech. 2. SLP rates severity of overall hyponasality in spontaneous speech. 3. SLP asks parents to rate severity of hypernasality. 4. SLP asks parents to rate severity of hyponasality. 5. SLP asks if parents perceive any CHANGES in resonance. If so, when & how? Assessment-Nasal Air Emissions (NAE) • Nasal air emissions (NAE): -audible -inaudible -nasal grimace -nasal turbulence/rustle Assessment-NAE cont’d. • Audible Nasal Air Emissions: -oral consonants produced (emitted) through the nose -airstream is heard from the nose -transcribed as: ~ Assessment-NAE cont’d. • Inaudible Nasal Air Emissions: -oral consonants produced through the nose -not heard perceptually -detected by mirror exam Assessment-NAE cont’d. • Nasal Grimace: (NG) -noticeable movement of nose during speech -movement may occur at nares, mid-nose, nasal bridge -movement may be unilateral or bilateral -movement occurs in attempt to achieve velopharyngeal closure -movement is subconsciously used to move oral sound back to oral cavity from nasal cavity Assessment-NAE cont’d. • Nasal Turbulence/Rustle: (NT) -oral consonant sound occurs during partially opened velopharyngeal valve -air flow is turbulent with noted noise/rustle Assessment-NAE cont’d. Procedure • Nasal Air Emissions-Audible & Inaudible: Areas to Assess: Isolation CV Syllables Phoneme-Loaded Sentences Stop/Plosive Fricative/Affricate Mixed Nasal/Oral Loaded Words & Sentence(s) Conversational Speech Single High Pressure Consonant Words (IPAT) Stimulability for Correction Assessment-NAE cont’d. Procedure • Area to Assess: Isolation Assessment-NAE cont’d. Procedure • Isolation: 1. Tell child “we’re going to say some sounds”. 2. “First we will do them without my mirror.” 3. “Then we will do them with my mirror.” 4. “Say /s/”. Assessment-NAE cont’d. Procedure • Isolation cont’d.: 5. “Say /p/”. 6. “Say /t/”. 7. “Say /k/”. 8. “Say “sh”. Assessment-NAE cont’d. Procedure • Isolation cont’d.: 9. “Now let’s do them again with my mirror”. 10. Repeat each sound while holding the mirror under the nostril(s). Assessment-NAE cont’d. Procedure • Area to Assess: CV Syllables Assessment-NAE cont’d. Procedure • CV Syllables: 1. Tell child “we’re going to say some more sounds”. 2. “First we will do them without my mirror.” 3. “Then we will do them with my mirror.” 4. “Say /sa/”. Assessment-NAE cont’d. Procedure • CV Syllables cont’d.: 5. “Say /pa/”. 6. “Say /ta/”. 7. “Say /ka/”. 8. “Say “sha”. Assessment-NAE cont’d. Procedure • CV Syllables cont’d.: 9. “Now let’s do them again with my mirror”. 10. Repeat each sound while holding the mirror under the nostril(s). Assessment-NAE cont’d. Procedure • Areas to Assess: Phoneme-Loaded Sentences Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences: 1. Tell child “now we’re going to say some sentences”. 2. “First we will do them without my mirror.” 3. “Then we will do them with my mirror.” 4. “Say ‘Peter has a paper puppy”. Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences cont’d.: 5. “Say ‘Buy a baby bib’.” 6. “Say ‘Tell teddy to try’.” 7. “Say ‘Daddy did the dishes’.” 8. “Say ‘Katie likes cookies’.” 9. “Say ‘Go get a bigger egg’.” Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences cont’d.: 10. “Now let’s do them again with my mirror”. 11. Repeat each of the plosive-loaded sentences while holding the mirror under the nostril(s). Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences cont’d.: 12. “Now we have some more sentences to do”. 13. “Say ‘Silly Sue eats icicles’.” 14. “Say ‘Zippers are easy to close’.” 15. “Say ‘Should I wash the dishes?’.” 16. “Say ‘The garage hid the treasure’.” Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences cont’d.: 17. “Say ‘Chad’s teacher was at church’.” 18. “Say ‘Jack wore a soldier’s badge’.” 19. “Say ‘Feed five frogs fish food’.” 20. “Say ‘Vic veered everywhere’.” 21. “Say ‘Thank you for the birthday present’.” Assessment-NAE cont’d. Procedure • Phoneme-Loaded Sentences cont’d.: 22. “Now let’s do them again with my mirror”. 23. Repeat each fricative & affricate-loaded sentence while holding the mirror under the nostril(s). Assessment-NAE cont’d. Procedure • Area to Assess: Mixed Nasal/Oral Loaded Words & Sentence(s) Assessment-NAE cont’d. Procedure • Mixed Nasal/Oral Loaded Words & Sentence(s): 1. Tell child “say ‘hamper hamper hamper’.” 2. “Good! Now do it again as fast & as many times as you can.” 3. “Now say ‘donna donna donna’.” 4. “Good! Now do it again as fast & as many times as you can.” Assessment-NAE cont’d. Procedure • Area to Assess: Conversational Speech Assessment-NAE cont’d. Procedure • Conversational Speech: Areas to Rate/Observe in regard to NAEs: Present vs. Absent Pervasive vs. Inconsistent vs. Occasional Nasal Turbulence Nasal Grimacing Assessment-NAE cont’d. Procedure • Area to Assess: Single High Pressure Consonant Words Assessment-NAE cont’d. Procedure • Area to Assess: Single High Pressure Consonant Words cont’d. Stimuli: Iowa Pressure Articulation Test (IPAT) Assessment-NAE cont’d. Procedure • Iowa Pressure Articulation Test (IPAT): Single Items /-k-/ /-g-/ /k-/ /g-/ /t-/ /-f-/ /-f/ /-z-/ /-s-/ /s-/ “sh-” /-s/ /-g/ “-sh” “j-” /-k/ “-sh-” MONKEY _____ WAGON _____ CAT _____ GIRL _____ TABLE _____ TELEPHONE _____ LEAF _____ SCISSORS _____ PENCIL _____ SOAP _____ SHOE _____ BUS _____ PIG _____ FISH _____ JEEP _____ BOOK _____ DISHES _____ Two-Item Blends /-sm/ /-ks/ “-per” /sk-/ /sm-/ /sn-/ /st-/ /kr-/ /sp-/ /tr-/ /kl-/ /gl-/ /bl-/ /br-/ /dr-/ /tw-/ /pl-/ POSSUM _____ BOOKS _____ PAPER _____ SKY _____ SMOKE _____ SNAKE _____ STOVE _____ CRAYON _____ SPOON _____ TREE _____ CLOWN _____ GLASS _____ BLOCKS _____ BROOM _____ DRUM _____ TWELVE _____ PLATE _____ “-ker” “-ork” “-sher” /gr-/ “-ger” /-lf/ CRACKER FORK WASHER GRASS TIGER WOLF _____ _____ _____ _____ _____ _____ 3-Item Blends /-mps/ /str-/ STAMPS STRING _____ _____ Assessment-NAE cont’d. Procedure • IPAT cont’d.: 1. Tell child “we’re going to same some words without pictures”. 2. “I want you to say what I say.” 3. “Say ‘monkey’ , say ‘wagon’ etc. Assessment-NAE cont’d. Procedure • Area to Assess: Stimulability for Correction Assessment-NAE cont’d. Procedure • Overall Rating of Nasal Air Emissions: Present vs. Absent Audible Inaudible Pervasive/Inconsistent/Occasional Nasal Turbulence Nasal Grimace (describe) Severity Rating: none/slight/mild/mild-moderate/moderate/moderate-severe/ severe Assessment-NAE cont’d. Procedure • Infant-Toddler Assessment: 1. SLP performs overall rating of nasal air emissions. 2. Note if stimulable for correction. 3. Note if could not test (CNT) or did not test (DNT). Assessment-Velopharyngeal Adequacy (VPA) Procedure • Intent: To PERCEPTUALLY determine VP adequacy Assessment-Velopharyngeal Adequacy (VPA) cont’d. Procedure • VP Ratings: Velopharyngeally Adequate (VP/A) or Velopharyngeally Inadequate (VPI/A) Assessment-Velopharyngeal Adequacy (VPA) cont’d. Procedure • VP Ratings cont’d: Other possibilities: Borderline VPI/A Questionable Assessment-Velopharyngeal Adequacy (VPA) cont’d. Procedure • VP Ratings cont’d.: Other Possibilities cont’d.: Unable to determine at this time Could not test Assessment-Language Procedure • Intent: to determine if language skills are age-appropriate Assessment-Language cont’d. Procedure • Guidelines for Test Selection: 1. Assess receptive & expressive skills 2. Choose an age/developmentally-appropriate test 3. With most patients, want in-depth testing (vs. screening) Assessment-Language cont’d. Procedure • Additional Information: If there are time or cooperation restraints: At CMHC we prioritize EXPRESSIVE over receptive due to the greater depth of information gained OR We DEFER language testing to the treating SLP Assessment-Voice Procedure • Intent: to assess voice for abnormalities in pitch, volume, &/or quality Assessment-Voice cont’d. Procedure • Assessment of Pitch: Make observations regarding pitch level-high, low, normal Note if vocal fry is present due to talking at bottom of pitch range. Note if vocal strain is heard due to talking at top of pitch range. Note if able to vary pitch or is the pitch range limited/monotonous. Observe if using diplophonia (talking with 2 simultaneous pitch levels). If time permits, attempt to modify level/range etc. BE CAREFUL NOT TO CONFUSE HIGH PITCH WITH HYPERNASALITY!!! They may CO-OCCUR, but are not synonymous. Assessment-Voice cont’d. Procedure • Assessment of Volume: Note if volume is too soft/quiet, excessively loud, cannot be maintained over time (varies). FREQUENTLY low pressure (due to VP valve issues) reduces the volume &/or ability to maintain a consistent volume. If time permits, attempt to modify volume. Assessment-Voice cont’d. Procedure • Assessment of Quality: Note if: hoarseness huskiness harshness aphonic breathiness raspiness Assessment-Fluency Procedure • Intent: to assess if speech is fluent or dysfluent Assessment-Oral Mechanism/Oral Peripheral Examination Procedure • Intent: to assess oral mechanism for structure & function deficits Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Selection of Protocol: formal or informal Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Positioning of Patient: eye level at level of oral cavity seated, erect Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Initial Observations: Note if cleft exists & type (none, overt, submucous) Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Initial Observations: Overt Cleft • Note if lip &/or palate • Note if unilateral (if so, note if right or left) or bilateral or midline or facial • Note if complete or incomplete • Note if repaired or unrepaired Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Initial Observations: Submucous Cleft Palate • Note if bifid uvula • Note if notch in hard palate • Note if muscular diastasis • Note if repaired or unrepaired • Note if occult Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Lips Tongue Nose Teeth Mandible/Maxilla Alveolus Hard Palate Soft Palate Other Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Lip Movements Tongue Movements Soft Palate Movement Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Lips • Assess/Observe: Symmetry scarring thinness/thickness continuity of muscle notching limited mobility/tight frenulum protruding premaxilla open resting posture lip pits Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Lips • Assess/Observe: protrusion retraction approximation Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Tongue • Assess/Observe: size shape scarring lingual frenulum Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Tongue • Assess/Observe: protrusion depression lateralization elevation-outside oral cavity elevation-inside oral cavity circling lips clicking Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Nose • Assess/Observe: size/width shape nostrils (opening & nasal alae) tip nasal bridge columella septum scarring symmetry Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Nose • Assess/Observe: patency obstruction Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Teeth • Assess/Observe: occlusal relationship incisor relationship supernumerary teeth rotated teeth missing teeth crowding primary/permanent condition (cavities) appliances Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Teeth Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • How to Assess Teeth: Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Mandible/Maxilla • Assess/Observe: micrognathia macrognathia protrusion retrusion arch formation/collapse hypoplasticity mid-face retrusion Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Alveolus • Assess/Observe: residual cleft fistula Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structured Assessed: Hard Palate • Assess/Observe: repaired vs. unrepaired width shape/height of palatal vault scarring/fissures/protuberance surgical alterations fistula palpated notch coloring Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Soft Palate • Assess/Observe: repaired vs. unrepaired bifid uvula zona pellucida length/width/thickness shape during phonation symmetry at rest & during phonation scarring/surgical alterations fistula Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Functions Assessed: Soft Palate • Assess/Observe: degree of movement direction of movement fluidity of movement pharyngeal movement Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Other • Assess/Observe: tonsils pharynx epiglottis craniofacial/other anomalies (eyes, ears, hands, etc.) Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Structures Assessed: Other cont’d. Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Additional Assessment/Technique Information: • Compare normal vs. abnormal • Judgment improves with experience Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Additional Assessment Technique/Information: • Assessing infants & toddlers Assessment-Oral Mechanism/Oral Peripheral Examination cont’d. Procedure • Additional Assessment Technique/Information: • Assessing the less cooperative patient Assessment-Order of Rationale • Order of Assessment: 1. 2. 3. 4. 5. History Nasal Patency Articulation Iowa Pressure Articulation Test Nasal Air Emissions-isolation, syllable, sentences, mixed words/sentences 6. Hyponasality 7. Assimilative Hypernasality 8. Hypernasality-sustained vowel, sentence imitation (9. Language) 10. Oral mechanism examination Assessment-Order of Rationale cont’d. • John Wesley saying: Do all the good you can By all the means you can In all the ways you can In all the places you can To all the people you can As long as ever you can Assessment-Order of Rationale cont’d. • Order of Assessment cont’d.: 1. History: I have reviewed medical chart/reports etc. prior to seeing the patient, but I can ask caregivers questions while child plays with an age-appropriate toy (NOTE: gives me time to observe child). 2. Nasal Patency: need to establish as impacts articulation/resonance/NAE/VP adequacy test results 3. Articulation: If ALL I get done is this, I can at least make some observations regarding resonance,NAE, VP adequacy, voice, expressive vocabulary, ability to follow directions etc. Assessment-Order of Rationale cont’d. • Order of Assessment cont’d.: 4. Iowa Pressure Articulation Test: rather non-invasive test measure & can make additional observations similar to those on articulation test 5. Nasal Air Emissions: testing without the mirror is non-invasive/non-threatening -testing with the mirror MAY BE threatening to some patients 6/7/8. Hyponasality/Assimilative Hyponasality/Hypernasality: The first 2 are also noninvasive/non-threatening HOWEVER testing for HYPERNASALITY involves use of GLOVES. This can be stressful/threatening for many children. If I were to START with tests involving GLOVES, I may lose the child entirely and, therefore, accomplish little testing & get minimal diagnostic information. Assessment-Order of Rationale cont’d. • Order of Assessment cont’d.: 9. Language: As covered previously, this is a lower priority than the other areas. 10. Oral Mechanism Examination: This is another area that may be stressful/threatening to the children. REMEMBER for most young children, people look in their mouths when they aren’t feeling well (i.e., strep test). ALSO, although each discipline on the team looks in the child’s mouth for a different purpose (i.e., dental vs. plastics vs. speech vs. ENT), usually at least one is able to accomplish this. In other words, if I CAN’T/DON’T get this information someone should have some of it. OF COURSE, if you are the only person doing the assessment (not part of a team), this may be of a little more importance. I always try to keep the GRAND SCHEME in mind. If I DON’T get this done, how negatively will it impact my diagnostics/ability to help the child? Am I better off DIFFERING till another time so as to not alienate the patient OR is it imperative that I accomplish this on this date? Other Issues Impacting Cleft Lip/Palate &/or Velopharyngeal Inadequacy • Possible Issues: feeding problems development/cognition educational issues psychosocial issues hearing problems multiple anomalies syndromes genetic issues Importance of the Team Approach to Treatment • Why team management? Benefit for the patient/family Benefit for the professionals Importance of Team Approach to Treatment cont’d. • The GREATEST IMPORTANCE is that team care helps to provide the BEST OUTCOME for the patient! Guidelines for Referrals for Perceptual &/or FFVN (Instrumental) Evaluations • Perceptual • FFVN Perceptual Guidelines including Articulation • Perceptual Evaluation performed within 6 months of FFVN • Uses some high pressure consonants • Validity of study • Can be prior to study or same day of • Scheduling variables: behavior, fatigue, time factor (distance traveled) • Actually attempting to use the palate Necessary Therapy Guidelines • A good solid course of therapy should be provided prior to consideration for either perceptual or FFVN evaluation. • At least one individual, 45-minute session per week for a minimum of 4 months, but preferably longer. • The more high pressure consonants the child has or is attempting, the more valid the study, the more likelihood we will be able to truly help them. Age Guidelines • Majority are at least 4 years of age or older • Cooperation • High pressure consonants • Age normally distinguish oral vs. nasal sounds (2 years old) FFVN Teams at CMHC • With Plastic Surgery • 3 speech/language pathologists (SLP) • Claudia Magers, MS, CCC-SLP • Sally Helton, MS, CCC-SLP • Sabrina Wallace, MS, CCC-SLP • With ENT • 1 SLP • Claudia Magers, MS, CCC-SLP Referral Guidelines for FFVN • Refer patients: • Suspect velopharyngeal inadequacy (VPI/A) • Suspect nasal obstruction • Who present with disorders of vocal production (pitch, quality, intensity) • Who present with possible or known disorder of structure &/or function of larynx Referral Guidelines for FFVN Suspect Velopharyngeal Inadequacy • Cleft Palate • Neurological impairments, especially with oralmotor involvement • Pre-tonsillectomy &/or adenoidectomy at high risk for VPI/A following surgery • Post-tonsillectomy &/or adenoidectomy Referral Guidelines for FFVN Suspect Velopharyngeal Inadequacy cont’d. • Hypernasal vocal resonance • Speech impairment including compensatory articulations, reduced intra-oral air pressure, &/or nasal air emissions • Pre-maxillary advancement at risk for VPI/A following advancement Referral Guidelines for FFVN Suspect Nasal Obstruction • Hyponasal or denasal vocal resonance • Post-pharyngeal flap surgery • Pre-tonsillectomy &/or adenoidectomy • Obstructive Sleep Apnea Referral Guidelines for FFVN Present with Vocal Disorders • Affecting: • Pitch • Quality • Intensity Referral Guidelines for FFVN Present with Laryngeal Disorder • Possible or known disorder of structure &/or function of larynx • i.e., vocal cord nodules, polyps • i.e., vocal cord dysfunction Guidelines Impact on Success of Studies • Allow to be highly successful in completion of valid studies • Don’t do unnecessary studies • “Don’t burn bridges” • Applies to both perceptual & age guidelines Guidelines for Referral for Perceptual &/or FFVN (Instrumental) Evaluation • If in doubt, give us a call! • At 816-234-3677 ask to speak to Claudia Magers, MS, CCC-SLP (Toll Free: 1-888-2398152) • At 913-696-5750 ask to speak to either Sally Helton, MS, CCC-SLP or Sabrina Wallace, MS, CCC-SLP (Toll Free: 1-888-460-6432) Guidelines for Referral to Children’s Mercy Hospitals & Clinics Cleft Palate/Craniofacial Teams • # of Teams/Plastics Surgeons: 3 Virender K Singhal, MD, MBA Shao Jiang, MD Alison Kaye, MD Location of Services: Children’s Mercy Hospital, 24th & Gillham Rd., Kansas City, Missouri Children’s Mercy South/College Blvd. Clinics 5808 W. 110th St./5520 College Blvd. Overland Park, Kansas Contact Person for Scheduling: Stephanie Taylor, Cleft Palate Coordinator 816-234-3677 (Hearing & Speech @ CMHC @ Gillham Rd.) Toll Free: 888-239-8152 Final Thoughts • Partnership: -CMHC SLPs are in partnership with you the treating SLP -we all ultimately want the best outcome possible for these children Contact Information • Sally Helton Hearing & Speech 913-696-5756 (direct line) shelton@cmh.edu Initial contact: by phone Authorization/Releases “The Bottom Line” • I view these children as jigsaw puzzles. They come with the all the pieces and it is my job to figure out how they fit together. Closing Good luck with your diagnostics & therapy for your patients/students with cleft lip & palate &/or VPI!