Pediatrics Archer Review Crash Course Welcome! ● ● ● ● If you have a question please enter it in the chat! I will do my best to answer questions as we go, but if I miss one will always circle back to you! We will take 1-2 breaks throughout the class Handouts & powerpoint slides are located in the ‘Handouts’ section of your GoToWebinar control panel. You can download and print them from here! If you have any technical issues or questions about streaming, handouts, etc. please email support@archerreview.com Congenital Heart Defects Overview Definition ● ● ● Abnormalities in the structure of the heart Occur during the very beginning of gestation - the heart is formed by the 8th week of gestation! Commonly occur with chromosomal abnormalities and syndromes such as: ○ ○ ○ ○ Trisomy 21 Trisomy 18 Turners syndrome DiGeorge syndrome Congenital Heart Defects 1. 2. 3. 4. 5. 6. 7. 8. 9. 10. 11. 12. Atrial Septal Defect (ASD) Ventricular Septal Defect (VSD) Atrioventricular canal Patent Ductus Arteriosus (PDA) Tetralogy of Fallot Tricuspid atresia Coarctation of the aorta Aortic stenosis Pulmonic stenosis Transposition of the great arteries (TGA) Truncus arteriosus Hypoplastic Left Heart Syndrome (HLHS) Foramen ovale An opening between the right and left atrium present in fetal circulation Ductus arteriosus An opening between the pulmonary artery and aorta present in fetal circulation. Assessment ● ● ● ● ● ● ● ● ● ● Murmurs Left sided heart failure Tachycardia ● Tachypnea Diaphoresis ● Dyspnea Decreased UOP ● Grunting Fatigue ● Retrations Pallor ● Nasal flaring Cyanosis ● Cough Clubbing ● Wheezing Hypotension Prolonged capillary refill Right sided heart failure ● ● ● ● ● Weight gain Enlarged liver Edema Ascites JVD Interventions ● ● ● ● Surgical interventions Repair vs. palliation Cardiac assist devices Pharmacologic interventions ○ ○ ○ ○ Digoxin ■ Cardiac glycoside Ace-inhibitors ■ Anti-hypertensive Diuretics ■ Help will fluid volume overload Beta-blockers ■ Decrease HR NCLEX Question Which of the following heart sounds would the nurse expect to auscultate in her patient diagnosed with heart failure? Select all that apply. a. b. c. d. S1 S2 S3 S4 Answer: A, B, and C A is correct. The nurse would expect to hear an S1 heart sound in her patient with heart failure. S1 is a normal heart sound caused by the closing of the mitral and tricuspid valves. This heart sound should still be auscultated in a patient with heart failure. B is correct. The nurse would expect to hear an S2 heart sound in her patient with heart failure. S2 is a normal heart sound produced by the closure of the aortic and pulmonic valves. This heart sound should still be auscultated in a patient with heart failure. C is correct. The nurse would expect to hear an S3 heart sound in her patient with heart failure. This is an abnormal heart sound also known as a ventricular gallop. It occurs after S2 with the opening of the mitral valve, and is caused by a large amount of blood hitting a compliant left ventricle. Because this abnormal heart sound is associated with a large amount of blood, it is related to fluid volume overload. We see fluid volume overload in heart failure patients whose hearts are not effectively moving blood forward. That is why S3 is heart in patients with heart failure. D is incorrect. The nurse would not expect to hear an S4 heart sound in her patient with heart failure. S4 is also known as an “atrial gallop” it occurs before S1 when the atria contract to force blood into the left ventricle. It is caused by a stiff, noncompliant left ventricle. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Physiological adaptation Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatrics Lesson: Cardiac Atrial Septal Defect ASD Ventricular Septal Defect VSD Patent Ductus Arteriosus PDA PDA ● ● Machine-like murmur Can be closed surgically ● Alprostadil ○ ○ Medication that can be administered to keep the PDA open in certain heart defects. This can allow blood to get out to the body when it otherwise couldn’t. Tetralogy of Fallot Definition Congenital malformation involving four distinct heart defects: Pulmonary stenosis, right ventricular hypertrophy, VSD, and overriding aorta. Tet Spells ● ● ● ● Hypoxic spells that occur in TOF. Begins with irritability and hyperpnea and followed by a prolonged period of intense cyanosis leading to syncope. Thought to be secondary to a spasm of the infundibulum of the outflow tract, or a drop in systemic vascular resistance (SVR). A drop in SVR increases the right to left shunt and decreases pulmonary blood flow. Tet Spell Interventions Comfort and calm Knee-to-chest position Supplemental oxygen Sedation - morphine Volume Sodium bicarbonate Propranolol Phenylephrine Increases the SVR, which decreases R-->L shunting to increase pulmonary blood flow. Treatment ● ● ● ● If mild - can go home and grow until ready for surgery If critically ill with severe hypoxia - surgery is required in the neonatal period. Ideally, complete repair around 6 months of age. Can be earlier depending on signs and symptoms. Repair 1. 2. 3. Pulmonary stenosis repaired by resecting the infundibular muscle Patch closure of VSD Pulmonary artery is opened and a patch placed to open up the outflow tract obstruction. NCLEX Question Which of the following statements about the heart defect tetralogy of fallot are true? Select all that apply. a. There is no permanent repair for tetralogy of fallot. b. In tetralogy of fallot, the right ventricle is enlarged due to pulmonary stenosis. c. Tetralogy of fallot is an acyanotic heart defect d. Morphine may be given to the child experiencing a tet spell. Answer: B and D A is incorrect. There is a total repair for tetralogy of fallot. It is usually completed around 6 months of age, unless the child's status requires intervention sooner. In this surgery, the pulmonary stenosis is repaired by resecting the infundibular muscle. There is a patch closure of VSD, and the pulmonary artery is opened and a patch placed to open up the outflow tract obstruction. This stops right to left shunting, and allows blood to easily flow to the lungs. B is correct. In tetralogy of fallot, the right ventricle is enlarged due to pulmonary stenosis. The pulmonary stenosis makes it very hard for the right ventricle to pump blood out to the lungs. This puts an extra workload on the right side of the heart, and therefore causes the muscle of the right ventricle to hypertrophy. C is incorrect. Tetralogy of fallot is a cyanotic heart defect, not acyanotic. In TOF, deoxygenated blood from the right side of the heart shunts through the VSD and to the overriding aorta, where it is distributed to the body. This distribution of deoxygenated blood causes cyanosis. D is correct. Morphine may be given to the child experiencing a tet spell. This intervention calms the child, decreases pulmonary vascular resistance, therefore increasing blood flow to the lungs to increase oxygenation and relieve the tet spell. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Risk potential reduction Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatrics Lesson: Cardiac Coarctation of the Aorta Definition Congenital cardiac condition characterized by a constriction of the descending aorta. Repair Specific findings ● Upper extremities ○ ○ ○ ○ ● Bounding pulses Hypertensive Warm Pink Lower extremities ○ ○ ○ ○ Weak or absent pulses Hypotensive Pale Cool NCLEX Question Which of the following assessment findings would lead the nurse to believe her patient could have a coarctation of the aorta? Select all that apply. a. b. c. d. +1 radial pulses and +3 femoral pulses Pale, cool feet and legs with warm pink hands and arms Hypertensive brachial blood pressure Hypotensive popliteal blood pressure Answer: B, C, and D A is incorrect. In coarctation of the aorta, there is a stricture in the aorta preventing blood flow out of the left ventricle. It usually occurs beyond the blood vessels that branch off to your upper body and before the blood vessels that lead to your lower body. So blood flow to the upper body is abundant, but hardly any can make it to the lower part of the body. Therefore, there are decreased lower extremity pulses, and increased upper extremity pulses. So the nurse would expect to palpate bounding +3 or +4 pulses in the radial pulse, but weak +1 or even absent femoral pulses. This is all due to the stricture in the aorta preventing blood flow from getting to the lower extremities. B is correct. Pale, cool feet and legs with warm pink hands and arms would be expected in a patient with coarctation of the aorta due to the stricture in the aorta preventing blood flow from getting to the lower extremities. C is correct. A hypertensive brachial blood pressure would be expected in a patient with coarctation of the aorta due to the stricture in the aorta preventing blood flow from getting to the lower extremities. D is correct. A hypotensive popliteal blood pressure would be expected in a patient with coarctation of the aorta due to the stricture in the aorta preventing blood flow from getting to the lower extremities. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Physiological adaptation Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatrics Lesson: Cardiac Transposition of the Great Arteries Definition A switch of the the aorta and pulmonary artery. The aorta is coming off of the RV and the pulmonary artery is coming off of the LV. Creates two parallel and separate tracks. Repair Balloon atrial septostomy - Creation of ASD to allow shunting in the unprepared TGA patient. Arterial switch NCLEX Question The LPN is discussing transposition of the great arteries with a family whose 2 day old son just received this diagnosis. Which of the following statements by the father indicates to the nurse that he understands his son’s condition? Select all that apply. a. b. c. d. “Instead of the pulmonary artery attaching to the right ventricle like it should, it is attached to the left ventricle. And the aorta is attached to the right ventricle instead of the left ventricle.” “Oxygenated blood from the lungs is recirculating on the right side of my son’s heart, and deoxygenated blood is re-circulating on the left side.” “Instead of the pulmonary artery attaching to the left ventricle like it should, it is attached to the right ventricle. And the aorta is attached to the left ventricle instead of the right ventricle.” “Oxygenated blood from the lungs is recirculating on the left side of my son’s heart, and deoxygenated blood is re-circulating on the right side.” Answer: A and D A is correct. This correctly explains transposition of the great arteries. In a healthy heart, the pulmonary artery attaches to the right ventricle and the aorta to the left ventricle. In transposition of the great arteries they are switched. B is incorrect. This statement would not indicate that the father understands transposition of the great arteries. This incorrectly explains the pattern of blood flow present in transposition of the great arteries. This LPN should reinforce that the right side of the heart is recirculating deoxygenated blood and the left side of the heart is recirculating oxygenated blood. C is incorrect. This statement would not indicate that the father understands transposition of the great arteries. In a healthy heart, the pulmonary artery attaches to the right ventricle and the aorta to the left ventricle. In transposition of the great arteries they are switched. The father has this reversed, and the LPN should reinforce education on transposition of the great arteries with him. D is correct. This correctly explains the pattern of blood flow present in transposition of the great arteries. This father understands that the right side of the heart is recirculating deoxygenated blood and the left side of the heart is recirculating oxygenated blood. NCSBN Client Need: Topic: Health promotion and maintenance Subtopic: Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatrics Lesson: Cardiac Hypoplastic Left Heart Syndrome Definition Disorder including 4 components: mitral stenosis or atresia, aortic stenosis or atresia, coarctation, and a hypoplastic left ventricle. Repair NCLEX Question Which of the following defects are part of the diagnosis Hypoplastic Left Heart Syndrome (HLHS)? Select all that apply. a. b. c. d. Atretic mitral valve Hypoplastic right ventricle Atretic tricuspid valve Hypoplastic left ventricle Answer: A and D A is correct. HLHS is a disorder including 4 components: mitral stenosis or atresia, aortic stenosis or atresia, coarctation, and a hypoplastic left ventricle. An atretic mitral valve is part of the diagnosis. B is incorrect. There is not a hypoplastic right ventricle in HLHS. Instead there is a hypoplastic left ventricle. C is incorrect. There is not an atretic tricuspid valve in HLHS. There is mitral stenosis or atresia, and aortic stenosis or atresia, but the tricuspid valve is intact and functioning. D is correct. HLHS is a disorder including 4 components: mitral stenosis or atresia, aortic stenosis or atresia, coarctation, and a hypoplastic left ventricle. A hypoplastic left ventricle is part of the diagnosis. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Risk potential reduction Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatrics Lesson: Cardiac Break Back at... Cleft lip and Cleft Palate Cleft Lip A congenital abnormality where there is a slip, or gap, in the upper lip on one or both sides. Cleft Palate A congenital abnormality where there is a split, or gap, in the hard palate (the roof of the mouth) Assessment ● ● ● ● ● ● Visible defect Monitor respiratory status Airway patency Nutritional status Weight gain Hydration Complications ● ● ● ● ● ● ● Feeding difficulties Weight loss Failure to thrive Speech and language delays Hearing issues Ear infections Aspiration Management ● Surgically corrected ○ ○ ● Pre-operative care ○ ○ ● Cleft lip first at 3-6 months of age Cleft palate second at 6-24 months of age Monitor for aspiration Assess airway patency frequently Post-operative care ○ ○ ○ ○ ○ Positioning: ■ Position upright for feedings ■ Cleft palate - can be prone post op to help drain secretions ■ Cleft lip should NOT be prone as this could disturb the suture line Protect suture line Elbow restraints to avoid toddler putting things in the mouth that would compromise the sutures No hard foods, straws, pacifiers, etc. No oral or nasal suctioning Feedings ● ● ● ● ● ● Specialized bottle to facilitate a good suction/latch Small, frequent feedings Upright position Burp frequently - will swallow a lot of air May take longer to feed than other children Monitor for aspiration ○ At risk for feeding to go out of their nose. NCLEX Question While assisting the intra-disciplinary team with interventions for a toddler who has just had a cleft palate repair, the nurse knows which of the following are appropriate? Select all that apply. a. b. c. d. Pacifier with oral sucrose to reduce postoperative pain Elbow restraints Specialized bottle for feedings Prone positioning Answer: B, C, and D A is incorrect. It is not appropriate to offer a toddler who is postoperative from a cleft palate repair a pacifier. This is because there is an incision with sutures in the palate of the mouth, and placing an object there could compromise the site. If the sutures break, the surgical site could open back up. B is correct. Applying elbow restraints is an appropriate intervention for a toddler who has just had a cleft palate repair. Toddlers are often putting things in their mouths, and pulling on things. It is a priority to protect their sutures, and we do not want the toddler to be able to pull out the sutures or put anything in their mouth that would compromise the suture line. Therefore, elbow restraints are often needed and an appropriate intervention. C is correct. Providing specialized bottles to the toddler who has completed their cleft palate repair will be very important for helping them establish feedings. It will be difficult for them to get good suction on a normal bottle, so specialized ones are needed. D is correct. Prone positioning is appropriate for the infant with cleft palate repair post-operatively to aid in drainage of secretions and maintenance of a patent airway. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Physiological adaptation Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Endocrine Omphalocele What is omphalocele? ● ● ● Congenital abnormality where the abdominal contents protrude through the umbilicus while remaining in the peritoneal sac. Occurs during weeks 9-10 of gestation. Usually diagnosed on a prenatal ultrasound. Assessment ● ● ● ● Visible defect Some infants have only the omphalocele Some also have cardiac defects Lung size can be affected Complications ● Hypothermia ● Dehydration ● Sepsis Surgical repair Management Pre-op ● ● ● ● ● Keep exposed intestines moist Cover with sterile gauze soaked in saline IV fluids IV antibiotics Thermoregulation Post-op ● ● ● ● Parenteral feeds Trophic feeds started enterally very gradually Monitor weight Very long hospital stay Gastroschisis vs. Omphalocele NCLEX Question The nurse observes a parent swaddling their infant with an unrepaired omphalocele. Which of the following statements would be appropriate? a. b. c. d. “Stop, you’ll kill your baby!!” “That is a nice, tight swaddle. It will really help sooth your new baby” “May I help you? We will need to be careful with their intestines, we do not want the swaddle to push them back inside.” “Swaddling is not allowed for these babies, please stop.” Answer: C A is incorrect. This is inappropriate to say to a parent as it would cause panic and upset them. The nurse wants to promote the parent bonding with their infant, and phrases like this will scare the parent and make them afraid to touch the baby, which is not therapeutic. B is incorrect. It is not appropriate to tightly swaddle an infant with an omphalocele. This would place pressure on their exposed intestines and could push them back inside of the baby, which we do not want. C is correct. This is a therapeutic statement. It educates the parent about the need to swaddle the baby only very loosely, and avoid any pressure on the exposed intestines so that they do not get pushed back inside of the baby. It also promotes bonding with the infant, as it encourages the parent to touch and care for their baby. D is incorrect. This is not appropriate. Swaddling is not ideal for an infant with an omphalocele due to the exposed intestines, but if it is done loosely and avoids placing pressure on the defect it can certainly be done. Telling the parent to stop will not promote bonding and decrease their interaction with the baby. The nurse should educate the parent on the necessary precautions when traveling and help them develop a positive relationship with their new baby. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Physiological adaptation Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Gastrointestinal Intussusception What is Intussusception? ● ● ● Occurs when one part of the intestine slips inside the other intestine “Telescoping” Often occurs where the small intestine and large intestine meet. Assessment ● ● ● ● ● ● Red currant jelly stools Cyclical abdominal pain Nausea Vomiting Green, bilious emesis Sausage-shaped mass in abdomen Treatment ● Enema to attempt to push the intestine back out ○ ○ ○ ● Air enema Hydrostatic enema Barium enema If successful a surgical repair is needed. Management Pre-op ● ● ● ● Monitor stool NPO IV fluids IV antibiotics Post-op ● ● ● Monitor bowel function Infection is common complication ○ Monitor temps, WBCs, CRP Slowly advance diet NCLEX Question Which of the following symptoms should the nurse monitor for in her patient suspected of intussusception? Select all that apply. a. b. c. d. Red currant jelly stool Hematemesis Palpable, sausage-shaped mass in RUQ Steatorrhea Answer: A and C A is correct. Red currant jelly stool is a classic finding of intussusception. When the bowel telescopes into another portion of the intestine, it causes intestinal obstruction and subsequently red currant jelly stools. B is incorrect. Hematemesis, or bloody vomiting, is not an expected finding in intussusception. We would expect vomiting of gastric contents, and possibly green bile if there is an obstruction. C is correct. Palpable, sausage-shaped mass in RUQ is a classic finding of intussusception. This is due to the physical telescoping of the intestine and the mass can sometimes be felt on palpation. D is incorrect. Steatorrhea is the passage of oily, pale, foul-smelling stool. It indicates fat malabsorption and can be a sign of Celiac disease, but would not be present in a patient with intussusception. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Physiological adaptation Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Endocrine Epiglottitis What is epiglottitis? ● ● Inflammation of the epiglottis Epiglottis ○ A leaf-shaped flap in the throat that prevents food from entering the windpipe and the lungs. It stands open during breathing, allowing air into the larynx ● ● Inflammation restricts the airway Caused by an infection ● ● Haemophilus influenzae type b Medical emergency ○ Bacterial Assessment ● ● ● ● ● ● ● ● Fever Difficulty swallowing Drooling Stridor Tripoding No cough Change in LOC Cherry red epiglottis The 4 D’s of epiglottitis ● ● ● ● Dysphagia Dysphonia Drooling Distress Treatment ● ● ● ● ● ● IV antibiotics Humidified oxygen Intubation and mechanical ventilation Keep the child calm No interventions until airway is secure Do not irritate the throat ○ ○ ○ ● ● ● Tripod position Avoid supine NO tongue depressor NO oral thermometer NO assessing the throat NPO Education ● ● ● Hib vaccine has reduced incidence Encourage parents to vaccinate to prevent When to call 911 ○ ○ ○ ○ ○ ○ ○ Trouble swallowing, breathing, and talking Straining the neck forward (trying to open the airway) Drooling (when it becomes too painful to swallow) A harsh raspy sound when inhaling (stridor), a sign that the airways are blocked Blue, purple, or gray skin or lips Trouble waking up to awake or arouse or unresponsive Trouble breathing NCLEX Question The nurse is assessing a 4 year old who was sent to the ED from urgent care. Assessment reveals tripod positioning, blue lips, mottled skin, inspiratory stridor, and excessive drooling. Vital signs are: Temp: 39 C HR: 188 RR: 46 O2: 82 % Which of the following is the priority nursing action at this time? a. b. c. d. Keep the child calm and call for emergency airway equipment Obtain IV access Assess the throat for a cherry red epiglottis Place the child on a high flow nasal cannula at 100% FiO2 Answer: A A is correct. Based on the presenting symptoms, the nurse suspects that this child has epiglottitis. Any child presenting with excessive drooling, distress, and stridor is highly suspicious for this medical emergency. In addition, this patient is already showing signs of circulatory compromise including circumoral cyanosis and mottling. The priority nursing action in this emergency is keeping the child calm and calling for emergency airway equipment. The child is at risk of losing their airway, and airway is always the priority! B is incorrect. It is inappropriate to attempt to obtain IV access on a child suspected of epiglottitis before emergency airway equipment is available. The priority action at this time is keeping the child calm and calling for emergency airway equipment. C is incorrect. It is inappropriate to assess the throat for a cherry red epiglottis at this time. Although presence of a cherry red epiglottis would confirm the diagnosis of epiglottitis, this child is at risk of losing their airway. The priority action will be to protect that airway before assessing the throat. . D is incorrect. Placing the child on a high flow nasal cannula at 100% FiO2 is not the priority at this time. This answer probably sounded right, because you see the O2 is 82% and they have circumoral cyanosis. Oxygen sounds like the right answer! But this intervention addresses the ‘C’ in your ABC’s - circulation. And the priority is always ‘A’, airway! This child is at risk of losing their airway, so all interventions need to wait until there is emergency airway equipment close by. If anything upsets the child their airway could spams and obstruct completely making it impossible to intubate them. That is why keeping the child calm and calling for emergency airway equipment is the priority in epiglottitis patients. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Risk potential reduction Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Respiratory RSV/Bronchiolitis What is bronchiolitis? ● ● Inflammation of the bronchioles Bronchioles ○ ○ ● Alveoli ○ ○ ● ● Smallest branches of the airway Lead to alveoli Air sacs Location of gas exchange in the lungs Thick mucus clogs up the bronchioles Leads to decreased gas exchange in alveoli ○ ○ Air trapping Collapsed alveoli Overview ● ● Most common in children under 2 years old Seasonal illness ○ ● Causative agent usually viral ○ ● ● Most common in winter Respiratory Syncytial Virus (RSV) Very contagious Worst on days 4-6 Assessment ● ● ● Cough Fever Increased work of breathing ○ ○ ○ ○ ● Retractions ■ Subcostal ■ Intracostal ■ Tracheal tug Nasal flaring Head bobbing Tachypnea Lung sounds ○ ○ Crackles Wheezing ● Hypoxia ○ ○ ○ ○ ● Circumoral cyanosis Mottling Delayed capillary refill Decreased SpO2 Changes in behavior ○ ○ ○ Irritability Lethargy Poor feeding Treatment Supportive treatment ● Oxygenation ○ ○ ● Fluid & Nutrition ○ ○ ○ ● ● Nasal cannula - high flow nasal cannula Always humidified NGT Enteral feedings IVF Antipyretics Analgesics Nursing Considerations ● Continue to monitor respiratory status for changes ○ ○ ● Work of breathing - improving? Worsening? Continuous pulse oximetry Maintain airway at all times ○ ○ ○ Semi fowlers preferred positioning Keep neck extended to open airway ■ Shoulder roll Suction available Education ● Infection prevention ○ ○ ● Droplet precautions Isolate from others as able at home Prevention ○ Palivizumab for at risk patients ■ Synagis ■ Premature infants ■ CF ■ Trisomy 21 NCLEX Question The nurse is assigned to care for a 18 month old diagnosed with bronchiolitis. She was born at 32 weeks gestation, but has no other past medical history. Which of the following does the nurse anticipate including in the plan of care? a. b. c. d. Ceftriaxone administration Humidified oxygen administration Contact precautions IV fluids Answer: B and D A is incorrect. Bronchiolitis is usually caused by a viral infection, most commonly respiratory syncytial virus (RSV). Ceftriaxone is an antibiotic, and antibiotics will not be effective against viral infections for they are not supported in the treatment of bronchiolitis. B is correct. Treatment of bronchiolitis will be primarily symptom management. Many children will require oxygen administration as the mucous in their bronchioles lessens gas exchange in the alveoli. Oxygen administration should be humidified to prevent drying out the mucous membranes. C is incorrect. Contact precautions are not sufficient for bronchiolitis. This infection is likely caused by a respiratory virus such as RSV and spread through droplets in the air, so droplet precautions will be necessary. This will include a gown, gloves, and mask when the nurse enters the room. Frequent handwashing is also key to preventing the spread of this infection. D is correct. Due to the increased work of breaking that bronchiolitis causes, IV fluid administration may be necessary in the treatment of bronchiolitis if the patient is unable to meet their fluid requirements through PO intake. An isotonic crystalloid solution will be used to ensure the patient remains hydrated until they can safely take PO fluids again. NCSBN Client Need: Topic: Physiological Integrity Subtopic: Basic care, comfort Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Respiratory Cystic Fibrosis What is Cystic Fibrosis? ● ● ● Autosomal recessive disorder Mutation leads to a buildup of excessive mucus in the airways Mucus leads to airway obstruction Pathophysiology ● ● Mucus is both excessive and very thick Causes mechanical obstructions throughout the body ○ ○ ○ ○ Bronchi Small intestines Pancreatic ducts Bile ducts Testing ● Newborn screening ○ ○ ● Sweat chloride test ○ ○ ● Meconium ileus ■ Meconium is thicker and stickier than normal, creates a blockage and first stool doesn’t pass. Test for elevated levels of immunoreactive trypsinogen ■ Substance normally produced by the pancreas and released into the small intestine Sweat is collected and analyzed for increased levels of chloride Sweat tastes salty Genetic testing ○ ○ DNA analyzed Mutation present Assessment ● Respiratory ○ ○ ○ ● Excessive mucus Frequent respiratory infections Hypoxemia ■ Clubbing ■ Cyanosis ■ Barrel chest Gastrointestinal ○ ○ ○ ○ Intestinal obstruction Meconium ileus Large, bulky, frothy, foul smelling stool Fat soluble vitamin deficiency ■ ADEK ■ Malnutrition ■ Failure to thrive ● Endocrine ○ ● Integumentary ○ ○ ● Diabetes Salty tasting sweat Elevated chloride in sweat Reproductive ○ Males are infertile Treatment ● Airway clearance ○ ○ ● Respiratory infections ○ ○ ○ ● Monitor for Treat with IV antibiotics Prevent! Respiratory support ○ ○ ● Chest physiotherapy Vest therapy Monitor work of breathing Oxygen as needed ● Promote nutrition and growth ○ ○ ○ ○ High calorie, high protein diet Increased fluid intake Monitor serial weights Pancreatic enzymes ■ Give within 30 min of eating every meal and snack ■ Sprinkle capsules on food ■ Fat soluble vitamin replacement Bronchodilators NCLEX Question The nurse is working in the normal newborn nursery. When she observes which of the following signs, she would suspect cystic fibrosis and notify the healthcare provider for further testing? a. b. c. d. Steatorrhea Hyperhidrosis Meconium Ileus Barrel chest Answer: C A is incorrect. Steatorrhea are stools that are bulk, frothy, and foul smelling. They are caused by the excretion of abnormal quantities of fat in the stool. This does occur in cystic fibrosis, but would not be present yet in a newborn just being diagnosed. B is incorrect. Hyperhidrosis is a medical condition in which a person sweats excessively and unpredictably. This is not a sign of cystic fibrosis in the newborn. The newborn with cystic fibrosis will have elevated levels of chloride in their sweat, causing it to taste salty, but they will not sweat excessively. C is correct. Meconium Ileus is very frequently the first sign of cystic fibrosis in a newborn. It is a bowel obstruction that occurs when the infant’s first stool is thicker and stickier than usual, causing a blockage in the ileum. D is incorrect. Barrel chest is a long term complication of cystic fibrosis, but not a sign that would be present at birth in the newborn. Barrel chest refers to a broad, deep chest that is large and cylindrical. It occurs when the patient has been suffering from hypoxemia due to cystic fibrosis for a prolonged period of time. NCSBN Client Need: Topic: Effective, safe care environment Subtopic: Coordinated care Reference: Hockenberry, M., Wilson, D. & Rodgers, C. (2017). Wong’s essentials of Pediatric Nursing (10th ed.) St. Louis, MO: Elsevier Limited. Subject: Pediatric Lesson: Respiratory Cerebral Palsy What is Cerebral Palsy? ● ● ● A motor disability that appears in early childhood Affects the child’s ability to move, and maintain balance and posture It is the most common permanent physical disability in kids Pathophysiology ● Damage to areas of the brain that control movement ○ ○ ○ ● Cerebellum Motor cortex Basal ganglia Causes: ○ ○ ○ ○ Anoxia Meningitis TBI Intracranial hemorrhage Assessment ● ● ● Abnormal movements Poor muscle tone Abnormal postures ○ ● Contractures Chronic respiratory infections But….How do I study?!?! Answer: The Sure Pass Program If you follow the Sure Pass Program and fail the NCLEX, Archer will give you a 100% money back refund for ALL PRODUCTS! Sure Pass Program Details What you get: 1. Immediate on-demand access to most recent live Rapid Prep AND multiple topic-wise webinars, a total of 40 hours, 2-months access. 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