Pediatric Nursing PEDIATRIC NURSING Extreme hypothermia shiver/chills increase o2 consumption decresed O2, increased CO2 ACIDOSIS o Extreme hypothermia burns brown fat for heat ketones/fatty acids ACIDOSIS Management o Dry baby immediately after birth (heat loss by evaporation) o Unang Yakap o Use heating devices (Radiation) Gooseneck lamp Floor lampv uneven distribution, more contact; prone to burns Radiant warmer- 18-24 inches away (safe), even distribution of heat Drop light o Avoid cold draft (convection) o Postpone the bath until temperature is stable (6 hours) o Use warm water during bathing o O-18 years old THE NEONATES The Immediate Delivery Room Care Administrative Order 2009 New Policies and Protocol on Essential Newborn Care A- airway B- body temperature C- certify the birth D- determine adaptation to extrauterine life- Apgar Score To reduce childhood mortality in support of the Millennium Developmental goal #4 2 strategies by the DOH Unang Yakap IMCI Airway 2 possible cause of death when there is no medical professional to attend the delivery o Asphyxiation o Aspiration Asphyxiation o Causes Umbilical cord is clamped no more O2 from the placenta hypoxia hypercapnia acidosis (more dangerous) CNS depression can potentiate death If cord is not cut- reverse circulation will Rh Incompatibility. o Prevention Babies must breathe after birth, neonates breath after birty by crying so stimulate to cry effectively after bityh A crying baby is a breathing baby o When he is delivered disorientation to space Suction with the bulb syringe PRN if (with nasal obstruction/meconium stained amniotic fluid) TO PREVENT ASPIRATION o deep suctioning might hit carin/hypoxia vagal stimulation arrhythmias (dec.HR) o Meconium stained (Meconium Aspiration Syndrome) Alveoli collapse because meconium is sticky and cannot be absorbed by the sinuses Sepsis since feces goes to the stomach Use wall suction but use whiffs of oxygen to allow rest If the HR drops more than 10bpm, stop the suctioning Oxygen can cause blindness (Retrolental Fibroplasia) use pulse oxymeter on the sole of the foot Encourage to cry to effectively to maximize lung expansion assess color (should be pinkish) Breathes but becomes bluer Transposition of the greater vessels give prostaglandin and prepare for surgical intervention Body Temperature Physiologic heat loss after birth (37.2 C down to 35.5-36.5 C) Extreme hypothermia (lower than 35.5) can cause COLD STRESS causing ACIDOSIS Prone to cold tress due to extreme hypothermia University of Santo Tomas College of Nursing / JSV Certify Identification and registration Identification- can be done by SN o Plastic bracelet on foot and crib card not reliable since it is detached o Footprints- more reliable (no longer recommended because of wrong technique of doing it) o Most ideal: DNA/HLA (Human Leukocyte Antigen Compatibility) less done Registration- MD, RN o Local Civil Registrar (municipio) then NSO for Birth Certificate Determine adaptation to Extra-uterine life APGAR Score APGAR SCORE- Done at 1 minute then at 5 minutes Criteria Pulse Respiration Activity Grimace Assess Cardiac rate Cry 0 Absent 1 <100 Absent Strong, regular Muscle tone Limp, floppy tone No response Weak, slow, irregular Some flexion Some grimace Gagging, crying, sneezing, pulls away from the stimulus Pink/Red all over CNS, response to stimulus, reflex irritability Color Appearance Pale/blue all over Acrocyanosis (hands and feet) 2 >100 Well flexedfetal position Activity Assessment Limp, floppy tone- frog like position WARNING o Most likely not also breathing 2-3 hours of not breathing - brain damage o Possibly dead o Premature o Narcotic effect Pediatric Nursing Mommy requested for pain killers twilight delivery Narcotics (Demerol, morphine sulfate) Give NALOXONE- give via endotracheal tube (narcotic antagonist) o Intubation Some Flexion o Drug user mother watch out for withdrawal symptoms in baby: seizure (do not breath well) Well flexed o Pull the arms of the baby baby will go back to fetal position Color Assessment Not so much reliable Pink- Caucasian Red- Afro-American 0-3 o Poor condition o Resuscitation needed, goes to ICU 4-6 o Fair condition but guarded o Closer monitoring, baby goes to NICU 7-10 o Good condition o Regular nursery care *Congenital deffect will not affect APGAR Phocomelia can have 10/10 score Abnormality Implication Birth weight 3,000 gms (6.5 lbs.) 2,500-3,500 IUGR Maternal DM Birth length 50 cm 19-20 inches Microcephaly Macrocephaly Mental retardation Hydrocephal us Spina bifida Chest Circumferenc e Abdominal Circumferenc e 31-33cm 31-33 AGA- appropriate for gestational Age At term i. 38-40 t0 41 weeks o 1 year old- same size of chest and abdomen 1.2 Color: o Normal: Pinkish or Reddish o Gray- septicemia due to intrauterine infection o Green- meconium stained due to fetal distress o Blue- congenital cyanotic cardiac disease o Yellow- pathologic jaundice due to blood incompatibility (ABO/Rh) o o 2. University of Santo Tomas College of Nursing / JSV o o o SGA- decreased size LGA- increased in size 33-35 cm o Pathologic Jaundice If noticed at birth or baby is less than 24 hours old Blood incompatibility Hgb hemolysis bilirubing unconjugated, indirect not excretable fat soluble Liver converts bilirubin through glucoronyltransferase conjugated, direct excretable water soluble urine and stool yellow Why neonates have hemolysis Neonates have to excrete excess blood because they are polycythemic (6-8 M RBC, 55-65% Hct, 16-18 Hgb) because baby is surviving in low oxygen in intrauterine Normal Head Preterm- 2nd day until 10th day Caused by normal accumulation of bilirubin due to expected hemolysis after birth o Regular Nursery Care (1) Initial Assessment 1. Take note of life-threatening abnormalities that require immediate referral Measurement Physiologic Jaundice Term Babies- 3rd day until 7th day decreased o2 kidneys stimulate erythropoietin increased RBC Sluggish blood flow- clot and thrombus formation Identify when you saw the jaundice (take not also (2) Eye Care ( ) o Prevents Opthalmia Neonatorum due to maternal gonorrhea or chlamydia o Done to all babies delivered either CS or NSD after initial bonding/breastfeeding o Broad spectrum antibiotic/povidone iodine eye drops on the lower conjuctival sac o Use half a grain of rice o Silver nitrate irritating and conjunctivitis, prevent by rinsing with isotonic solution o Antibiotic: betadine eyedrops (no rinsing, replaced silver nitrate) (3) Initial Cord Care Clamp when no longer pulsating (1-3 minutes) DO NOT MILK causes hemolysis of blood, hyperbilirubinemia A-V-A 1 artery 1 vein- organs may have defects (kidney and heart) o 1 kidney = kidney agenesis Choice of food affected (avoid sodium, preservatives) No contact sports Earliest attack of tonsillitis, tooth abcess go to MD attacks heart and kidneys Child can live as long as possible Prevent Infection o Clean with soap and water if soiled Promote drying o Do not use abdominal binders o Should fall-off between 7-10 days o Teach the mother to fold down the waist band for air drying o Ethyl alcohol (rubbing) - not used o Use Betadine when meconium stained When cord falls off o Assess the site o When bleeding Get cotton balls apply pressure to the site If does not stop, check for hemophilia (4) Vitamin K Pediatric Nursing To promote synthesis of prothrombin Neonates cannot synthesize Vitamin K because of absent intestinal bacterial flora Given IM 1 mg IM in thigh muscle- 0.1 cc (Vastus Lateralis)- biggest muscle mass and most highly developed for AGA (5.5-7.5lbs or 2500-3500gms/ Intrauterine growth chart 10-90%) Half a dose for SGA for day of discharge, half when birth Vitamin K can also be given ORALLY Avoid using the gluteal muscle (buttocks) because of the danger of sciatic nerve trauma causing paralysis o Use when the child has been walking for at least 1 year Offer oral Vit K if patients refuses IM o o o o (5) Inject Hepatitis B and BCG BCG intradermal; site may vary (6) Initial Bath Done best when vital signs especially temperature is stable/6 hours after birth Do not remove vernix caseosa Vernix o Waterproof o Slippery- prevent friction from ruggae of the vaginal canal o Insulation for the baby- contains heat and moisture for the baby o Keeps baby moist days after birth o Desquamation if with little vernix Oil bath o For meconium stained babies to remove vernix Home Bath o Depends on the schedule of the mother be flexible o Can get a bath anytime o Baby is sick Immediately after feeding o NO TUB BATH until cord if off (7) Rooming In (RA 7600) Provide Optimum Nutrition: RA 7600 on RoomingIn/Breastfeeding Act of 1992 EO #51: Milk Code of the Philippines Breastfeeding o The best feeding must be done at least 8x/day ON DEMAND AND EXCLUSIVE o Exclusive- ONLY breastmilk o On Demand- every time baby wants to o Passive natural immunity Until 1 year IgA- breastmilk IgG- placenta o If inverted nipple- NOT a contraindication o Breast pump Ideal: put milk in milk bag (with zipper and calibration) Practical: ice bag Label: date and time First in first out Put in freezer Good for 1 year (frozen) Kept continuously frozen Do not abruptly heat it destroys the immunoglobulins Use warm water bath soak it o Temporary Contraindication University of Santo Tomas College of Nursing / JSV o o If baby is critical Promote lactation still with mother breast pump Mastitis - discard pumped milk Absolute Contraindication Hepatitis, HIV, Active TB, Maternal substance abuse, surgical Reasons, injectable breast implant Parlodel (deladomone)- supress breastmilk production Give mother advice on the use of breast milk substitute: Type (infant formula only) Below 12 months , evaporated milk, condensed milk, am - can cause kwashiorkor Preparation: Sterilization/boiling 10-15 minutes from boiling point Feeding Method Do not prop the feeding bottle Aspiration Position Carry baby while feeding Burping Schedule Give water in between (8) RA #9288 Newborn Screening Act of 2004 Done to diagnose inborn errors in metabolism that may cause DEATH or MENTAL RETARDATION o Congenital adrenal hyperplasia Decreased cortisol, severe salt loss dehydration. If not treated, death in 9-13 Mx: NaCl supplement (tablet) Galactosemia Inability to metabolize galactose in milk Sx: vomiting, diarrhea, liver damage, cataract, growth failure and brain damage Mx: No animal source/milk/ NO BREASTFEEDING Soy Formula Isomil, Nursoy, Prosobee o Phenylketonuria Inability to utilize an essential amino acid causing mental retardation Phenylalanine converted to tyrosine converted to melanin (hyopigmentation) May go to the brain and cause MR Mx: special formula lofenalac/phenalac o G6PD (Glucose-6-Phosphate Dehydrogenase) Breakdown of RBC causing anemia Mx avoid triggers like beans, naphthalene, sulfas o Congenital Hypothyroidism (Cretinism) Deficiency in thyroid hormones causing physical, developmental and mental delay Mx: Thyroid supplement for life (Synthroid) Done by heel prick when baby is at least 24 hours old o GROWTH AND DEVELOPMENT Growth Increase in the number and size of cells Pediatric Nursing Measured in terms of quantity Development Capacity of functioning or skill Measured in terms of quality Milestones Principles of Growth and Development 1. Unique o individualized o No 2 person is exactly the same o Care plan should be individualized o Do not compare children with one another 2. Unified o All areas are important Physical, social, emotional 3. Continuous Process o Begins at conception and ends at death 4. Influenced by factors in the environment o Pre-natal factors: genetics and pregnancy care o Post-natal factors: home, school, city, country 5. Rate of growth varies o Rapid stages (growth spurts) Infancy Adolescence o Slow Periods (growth gaps) Toddler Preschool Schooler 6. Directional o Growth Horizontal and vertical o Development Cephalo-caudal (gross motor) Proximo-distal (fine motor) Assessment of Growth Physiologic weight loss o A couple of weeks after birth o 5-10% of birth weight o 1st baby check-up- 1 week after birth For follow-up Umbilical cord- dried; about to fall-off Jaundice status 1. Breastfeeding jaundicespresence of pregnanendiole decreased gucoronyltransferase jaundice o Baby has no longer a supply of growth hormone from mother stunting of growth o Expel meconium and urine, low amount of milk ingestion dec.weight o Days after birth, skin begins to desquamate o Newborns tends to sleep and sometimes eat Regain weight rapidly during infancy and adolescent stages Most rapid during infancy and adolescent stage o General trends in physical growth during childhood (hand-outs) *Computing for expected weight (birth weight is unknown) Below 1 year: Age in months/2 + 3 or 4 = weight (kg) Above 1 year: Age in years x 2 +8 = weight (kg) - weight for height o Height in cm 100 = weight in kg Less 10% for Orientals Filipinos *Computing for number of teeth Age in months 6 Assessment of Development University of Santo Tomas College of Nursing / JSV DDST- Denver Developmental Screen Test MMDST- Metro Manila Developmental Screen Test o Phoebe Williams 4 areas assessed (read handouts) o Fine motor- skills done by the small muscles (hands) 0,3,6,9 o Gross Motor- skills done by the large hands (body, torso) 2,4,6,8 o Language o Interpersonal Social 0 2 4 6 8 10 12 14 15 0 3 6 9 12 Cephalo caudal Cry Head lag no head control Cradle hold Support head Begins to have head control Lifts head on prone Full head control Lifts head and chest Sits with support Sits without support Sits alone Stands with support Stands without support Walks with support Walks alone Proximo distal Strong grasp reflex Grasp reflex gone Hand-regard hands are held open Plays with hand Beginning communication between brain & hand Palmar grasp Can hold bottle with 2 hands Pincer grasp Thumb and finger to hold objects Put things in and out of container *Games Children Play Criteria for picking toys o Safety o Based on their developmental age o Must have a function or a purpose Infants o Can play o o Play with their BODY SENSES (sight, hearing, touch) o Solitary play/games o Toys Mobiles Rattles Teething rings Music boxes Squeeze toys o 3-4 monthsToddlers o share - possessive; cannot Pediatric Nursing o o o o o What is mine is mine, what is yours is mine Parallel Games; Loves to play BESIDE another child but must have each a toy Must promote walking or talking Toys: Promote skills of walking-push and pull toys, talking- toy telephone, coordination- blocks o Pre-schoolers o Loves to share and imitate adults in their play o Role Play; stage of make believe o Cooperative/Associative Games o Do not typecast toys o Toys: Role playing games, play school, play house, doctor-nurse kit School-Age o Must have a winner at the end of the game o Competitive Games o Toys: Card games, scrabble, hopscotch, skipping rope Theories in Development *Milestones are not affected by gender/sex Relationships Formation of developmental tasks (positive and negative) foundation of our personalities There is a body that is most important in each stage of our lives That is what the person will use in their relationship which lays down the foundation for the developmental tasks which then develops their personality Trust vs. Mistrust and Oral Stage (Infants) Mom and Baby Love trust know see Lust is the foundation of all relationship Baby used the mouth to get attention of mother through crying mommy will be known as the one who tends to the baby baby will trust mommy LOVE baby will develop trust If unanswered mistrust o Oral frustrations o Oral fixation o Oral residuals: Excessive thumb sucking, nail biting, over talkativeness, overeating, chain smoking, alcoholism, drug addiction o Why unanswered busy, unwanted, ignoran9 The infant receives stimulation and pleasure through his mouth. Answering their cry (needs) helps develop trust Nurses must watch out for fixation in patients which rests the GI system due to medical condition o Use non-nutritive sucking (pacifier) to replace oral need o Remove if it already pacified o Pacifier would not cause buckteeth as long as the teeth is still milkteeth o Do not improvise Autonomy vs. Shame and Doubt and Anal Stage (Toddlers) Finds pleasure in controlling his eliminatory function Toilet training begins: Right place Important facts about toilet training University of Santo Tomas College of Nursing / JSV o o Recommended to be started at 18 months with bowel first Spinal cord fully coated myelin sheath Most important factor is READINESS Physical- neurologic system readiness; Can feel the urge Psychological- please the mother Completed by 4 years Feeling of INDEPENDENCE develops through bowel training You can never feel dependent if you are insecure Narcissistic Child feels he can do whatever he wants, can feel the urge Behaviors to observe: o - set limits/ offer acceptable choices o Ritualistic or stereotype behavior To feel secure o Temper tantrums Ignore the behavior Frustrations because of the needs and the wants Time-out- 1 minute for each year of life Initiative vs. Guilt and Phallic Stage (Preschool) Oedipal/Electra Phase o Child turns toward the parent of opposite sex, usually resolved toward the end of this period How to resolve Oedipal/Electra o Negate Unresolved Electra complex: Querida Initiative develops if the child is allowed the freedom to initiate small activities and is appreciated for it Behaviors to observe: o Very curio ? o Asks many questions (300-400/day) o Exhibits interest in sex (gender) difference o Touches/Explores their body o Exhibits fear of bodily injury o Very imaginative- engages in fantasy play To solve the conflict (anxiety) o Fondle their genital o Exhibitionists o To seek revenge for the penis: Hit a person with it (Rapists) What to do o divert (alam na napansin) o You IGNORE In social situations, tell him to go to his room = provide privacy o When you give injection, cover it o Magical thinking kissing of wounds, non living things are alive Industry vs. Inferiority and Latency Stage (Schooler) Calmest stage in sexual development -latency The sexual drive (libido) is controlled and repressed interest on same sex only (normal homosexuals) Heroism crush of opposite sex, usually older Industry develops if the child is permitted to do things by himself and praised for the results ACHIEVEMENT ORIENTED YEARS Wants to prove their BEST in school Identity vs. Role Confusion and Genital Stage (Adolescent) Resurgence of sexual drives Develops relationships with members of the opposite sex Identity develops when there is feeling of belongingness and acceptance by others Pediatric Nursing Behaviors to observe: o Undergoes bodily changes corresponding to puberty o Moody and unpredictable o Attempts to make decision for himself o Makes long-range plans for the future (career plans) Puberty o First change in BOTH sexes: Increased height and weight (2nd period of growth spurts) Female: widening of the pelvis (ovoid) Male: broadening of the chest and shoulders o Physical changes in the female in order of appearance: Development of the breast buds (thelarche) Growth of pubic and axillary hair (pubarche, adrenarche) Menstruation (menarche)- usually unovulatory Average 10 ½ to 15 y/o Regular menstruation and ovulation- 6-14 months after menarche o Physical changes in the male in order of appearance: Increase in the size of the genitalia (scrotum) Growth of pubic, axillary, facial and leg hair Voice changes Production of spermatozoa (nocturnal emission) o No Menstrual Cycle Ovarian agenesis Polycystic ovary Hypothyroidism o No wet dreams Cryptorchidism Sx: Orchidopexy ABNORMAL PEDIA THE RISK NEONATES Pre-ecclampsia might lead to abruption placenta baby must be delivered Preterm- most common risk newborn PRETERM Born before the 38th week or before completing 37 weeks of gestation regardless of he birth weight 38 weeks = 37 weeks and 7 days Physiologic Handicaps Expected handicaps for preterm because of immature organs 1. Respiratory Distress Immature alveoli with less amount of surfactant Problems: atelectasis, prolong apnea (more than 20 secs), cyanosis, asphyxia Symptoms o Nasal flaring- because they are o o Fast breathing more than 60 Chest indrawing University of Santo Tomas College of Nursing / JSV Grunting- most accurate sign umuungol like a near collapsed lungs upon expiration) Suction first the mouth newborns are obligate nasal breathers If the nose is suctioned first stimulation of pharyngeal reflex aspiration of secretions Symptoms or respiratory distress not visible immediately after birth Body temperature- a more immediate problem (within 1 minute might have hypothermia) Management: o Assist MD in inserting ET Neonatologist Serve as an accessible route for administration of surfactants o Artificial surfactant given via ET (Survanta/Liquivent) o Give O2 by CPAP (Continuous Positive Airway Pressure)/ventilator o Prolonged ventilator Might develop bronchopulmonary dysplasia P. aeroginosa o Monitor pulse oximeter (danger of retinopathy of prematurity/ retrolental fibroplasia) O2 not greater than40% o On NPO during respiratory distress o Good urine output = good cardiac output 1-1.5 cc/kgbw/hour o 2. Regulation of Body Temperature Immature hypothalamus Less amount of subcutaneous tissue Poikilothermia- can go very high low (dependent on the environment) due to immature hypothalamus Management: o o Put in incubator- provides neutral temperature o KMC- Kangaroo Mother Care 3. Nutritional Difficulties Prone to aspiration/ gastric distention Hypoglycemia Causes o Poor suck and gag must not be removed o Uncoordinated swallowing must not be removed o Small gastric capacity Management o Gavage (OGT) feeding inserted at the mouth Orogastric feeding Breastmilk or formula Special preemie formula (25 cal/oz) O-lac, Pre-Nan Similac Special Care o Small frequent feeding o If observed to be sucking refer preemie nipple (shorter, smaller, opening is cross-cut) o Upright position during feeding o Right Lateral position after feeding Promote gastric emptying 4. Hematologic Difficulties Immature liver function (no glucoronyl transferase) Jaundice due to indirect bilirubin due to hemolysis, liver cannot convert Problem: o Early and prolong jaundice o Prone to kernicterus o Bleeding Pediatric Nursing Photoisomerization more skin exposed Management o Phototherapy as ordered Phototherapy o Maximum exposure except the eyes and genitals Increase in temperature vascular engorgement priapism (continuous erection of the penis) Cover eyes to prevent loss of moisture o Regular turning to all sides: front back, side to side every 30 mins o Check temperature regularly o Promote feeding and hydration Prevent dehydration Promote faster elimination of bilirubin o Promote bonding/breastfeeding if allowed o Breast feeding jaundice - mas matagal mawala pag breastfed (prenanendiole decreases glucoronyl transferase) o Physiologic jaundice is normal after 1 day; if not maternal antibody destroys o Bilirubin can go to the brain causing kernicterus (pre-term only) 5. Low Resistance to Infection Most common cause of death Immature immune system Problem: Sepsis neonatorum (nosocomial infection) Management o Note for signs of infection Fever- not a sign for preterm (immature hypothalamus) Hypothermia- sign for preterm Poor feeding o Strict compliance with Nursery aseptic protocol o Antibiotics as ordered A risk because of immature liver (post antibiotic hepatitis) POST MATURE INFANT Born more than 42 weeks in gestation Problem: placental degeneration causing decreased uteroplacental perfusion Manifestations o Long but thin o Dry cracking skin o No vernix and lanugo o Long hair and nails o Alert look o Possible IUFD o Associated Problems o Hypoxia due to placental insufficiency o Hypoglycemia due to decrease glycogen o Fetal distress Restlessness of the baby- earliest sign o Seizure disorders might develop cerebral palsy o Cold stress due to less subcutaneous fats o Meconium aspiration Due to respiratory distress Infection o Polycythemia causing hyperbilirubinemia Not critical for kernicterus Phototherapy but not as long as that of a preterm DRUG A Unborn child is passively addicted to the drug University of Santo Tomas College of Nursing / JSV Neonates are born SGA and may show signs of withdrawal 12-24 hours after birth Manifestations of Withdrawals o GIT Irritability Earliest Diarrhea hypokalemia, dehydration Regurgitation Vomiting Anorexia o CNS Irritability: Tremors, Irritability, High-pitched cry, Restlessness, Seizures Management o Environmental modulation to decrease external stimuli (NICU) Placed in incubator for sound incubation o Providing adequate nutrition and hydration (IV line) o Drug Therapy Phenobarbital- anticonvulsant Chlorpromazine (Thorazine)- CNS depressant/ antipsychotic Diazepam- muscle relaxant o Seizure Precaution Airway is maintained give whiffs of O2 Do not suction while having a seizure Refer mother to social service of the hospital can go to rehab FETAL ALCOHOL SYNDROME (FAS) Facial Features o Hypoplastic maxilla o Hypoplasticphiltrum o Short palpebral fissures o Thin upper lips Neurologic Symptoms o Microcephaly o Mental retardation Growth o Prenatal growth retardation (SGA) o Persistent postnatal growth lag Irritability and Hyperactivity, restlessness No withdrawal BABY OF DIABETIC MOTHER Mommy with diabetes decreased insulin increased glucose in blood blood goes to baby 1 glucose supply for baby increased production of insulin intrauterine hyperinsulinism more glucose absorption macrosomia (above 4000gm) uterine stretch reach maximum point contractions preterm delivery, fractured clavicle (greenstick fracture) after birth hypoglycemia Baby may be diabetic in the future Macrosomic Baby o Large shoulders (broad) bigger than head Management o While fracture is healing hold figure 8 to facilitate fracture healing o Monitor signs and symptoms of hypoglycemia Restlessness Tremors Irritability o Monitor blood glucose level (CBG) Can be done on great toe 40-60 mg/dl; 2-3 mmol (normal) 1 mmol = 20 mg/dl o If CBG lower than 40 mg/dl give glucose (D50W in a vial) as ordered; bolus BLOOD INCOMPATIBILITY Pediatric Nursing ABO/RH (erythroblastosis fetalis) Orientals- 99% have Rh (+) (D antigen) Rh (-) = no Rh factor (D antigen); can only receive (-) Rh (+) = can receive blood from Rh (+) and (-) Mother Rh negative Rh positive Type A Type B Type O Type AB Baby Rh positive No problem Type B Type A Type A or B No problem any blood type Uteroplacental barrier prevents blood of baby and mother to mix Through pinocytosis, antibodies cross membrane (Mother (-) and Baby (+)First baby not affected birth of placenta production of antibody (anti-Rh (+)) second pregnancy uteroplacental barrier allows antibodies to cross membrane hemolysis Manifestations: o Jaundiced/ Alive but with pathologic jaundice Management: o Exchange transfusion remove blood o o o replacement with fresh whole blood (Rh Negative) Di napwede Rh (+) because of the presence of antibodies Mother cannot donate because antibodies came from her PREVENTION is the best intervention If mommy and baby are not compatible: After 1st baby, (baby) determines presence of maternal If mother is not compatible with baby and RhIg (RHOGAM) is given to mother within 72 hours after delivery or abortion of an incompatible fetus o EXCHANGE TRANSFUSION o Can be given during pregnancy ___________________________________________________ o NEONATES WITH CONGENITAL DEFECTS CONGENITAL HEART DISEASE All congenital conditions are risky 1st trimester- most critical period for the mother Overall cause of the problem: mixing/shunting of oxygenated and unoxygenated blood Acyanotic o Left Side shunt going to the right o Aorta does not get unoxygenated blood Cyanotic o Right shunt going to the left o Aorta gets unoxygenated blood systemic circulation Decreased O2 saturation ACYANOTIC Left to right side shunt CYANOTIC Right to left side shunt Aorta does not get unoxygenated blood Aorta gets unoxygenated blood 1. Ventricular Septal Defect 2. Atrial Septal Defect 3. Patent DuctusArteriosus 4. Coarcation of Aorta 5. Pulmonary Stenosis 6. Aortic Stenosis 1. Tetrallogy of Fallot 2. Transposition of the Great Vessels 3. Tricuspid Atresia T= cyanotic! ACYANOTIC HEART DEFECTS Congestion of cardiac chamber heart compensates by increasing heart rate CHF Left Sided Failure and Right Sided Failure A-anim B- breathing (CC) C- CHF (complication) D- interventions Left Sided Failure (lung related symptoms): o Earlier to recognize o Respiratory Symptoms: Dyspnea, Productive cough (pink frothy sputum), Rales/crackles Right Sided Failure: Systemic Symptoms, Distended neck veins, Pedal edema, Ascites, Hepatomegaly CC: Early: Pulmonary Symptoms - Dyspnea (refuses to suck), Fast breathing, Moist cough, Rales/crackles DX: o Chest x-ray Pulmonary edema and cardiomegaly o Echocardiography Identifies type and size of defect o Cardiac Catheterization Identifies pressure inside the heart (beginning CHF) Identifies need for surgery Best rest, apply pressure dressing, assess for pedal pulsation (the used leg will have a weaker pulsation on the first 4 hours, if no pulsation, possible thrombus embolectomy, heparin) Corrective Surgery: o If in failure and defect is large (no possible spontaneous closure) o There is possibility of spontaneous closure Open Heart Surgery o Defect is inside the heart/risky since it involves stopping the heart o Procedure: Induction of asystole (cardioplegia) Induction of hypothermia Use of bypass machine (ECMO) Extracorporeal Membrane Oxygenator Induction of hyperkalemia bradycardia Closed Heart Surgery o Defect is outside the heard Induction of hypothermia Medical/Nursing Management: o Drugs: Digoxin Diuretics o Diet - Low sodium, low cholesterol o Decrease cardiac demand o Decrease occurrence of infection Objective #1: Prevent CHF o Improve Cardiac Output University of Santo Tomas College of Nursing / JSV Pediatric Nursing Cardiac Glycoside (Digoxin) Increase strength of contraction Given before meals- so you can assess for toxicity (first sign of toxicity is GI symptoms) Hold if slow CR o 1y/o lower than 100 o 1-5 y/o lower than 80 o 6-10 y/o lower than 70 o 11 and up lower than 60 12 hours interval o Prevent Sodium Retention and Promote Elimination of Excess Fluids Diuretics- Furosemide (Lasix) Given during acute stage of CHF Not a maintenance drug ACE Inhibitors- Captopril/Enalapril Prevent sodium and water retention 1-1.5 ml/kg BW/hour o Low sodium intake Low Sodium Formula- Lonalac Clarification on solids allowed Not all salty foods are rich in sodium! Enough salt to taste but no more added during eating Tocino, soda, Objective #2: Decrease Oxygen Demand o Cluster nursing care o Quiet play activity - toys that can be played in bed o Decrease stress and anxiety level Limit crying Course your interventions through the mother o Small frequent feeding Objective #3: Prevent Respiratory Infections o Because of pulmonary edema o Vitamin C - for non-asthmatics- vitamin C is an allergen o Promote Immunization 1. ATRIAL SEPTAL DEFECT Increased amount of blood in the right atria overstretching effect of the myocardium (compensation) heart pumps faster (increased HR) will eventually decrease contraction (exhaustion) decreased cardiac output systemic effects (CHF) May close by itself Congestive heart failuredecreased o Same manifestions Kidney symptoms most dangerous Congenital heart failure digoxin, diuretics o No aspirin in children since the cause it not an infarct o No NTG o No statins 2. VENTRICULAR SEPTAL DEFECT Blood from left ventricle goes to right congestion of right ventricle hypertrophy overstretch compensation exhaustion decreased CO CHF 3. PATENT DUCTUS ARTERIOSUS Fetal structure Should have closed at birth ligamentum arteriosum More pressure in the aorta blood goes to pulmonary artery right ventricle hypertrophy University of Santo Tomas College of Nursing / JSV Can be managed by meds (may not need surgery) Management: o Indomethacin- prostaglandin inhibitor 4. COARCATION OF THE AORTA Constriction of the descending part aorta blood goes back left ventricle hypertrophy Greater BP on the upper part of the body Hypotension in the lower part of the body 5. AORTIC STENOSIS Constriction of the aorta increased blood in the left ventricle 6. PULMONIC STENOSIS Constriction of the pulmonary artery increased blood in right ventricle CYANOTIC HEART DEFECTS o o C- central cyanosis C- clubbing of fingers o o C- clots (thrombus) C- cerebral thrombosis (CVA) o P- propanolol o P- penicillin o P- phlebotomy o P- promote fluids o P- promote rest o P- polycythemia (monitor) 1. TRANSPOSITION OF THE GREAT VESSELS Right ventricle aorta Left ventricle pulmonary artery Pure unoxygenated blood is delivered into the systemic circulation; symptoms may be seen on delivery room table More favorable if with septal defect (ductus arteriosus) less symptomatic Sx: o Persistent cyanosis in spite of vigorous crying (central oxygen) o Hypoxia in spite of O2 therapy Management o Palliative - Emergency Balloon Septostomy Followed by corrective Open Heart Surgery (Miller-Rashkind Procedure) o Prostaglandin- open ductus arteriosus temporarily 2. TETRALLOGY OF FALLOT D- displaced aorta R- right ventricular hypertrophy O- opening in the septum (VSD) P- pulmonary artery stenosis More pressure in the right side of the heart because of pulmonary stenosis right to left shunting blood goes to the displaced aorta (center) delivery of mixed unoxygenated blood to the systemic circulation Symptoms usually seen when child is more active because of increased oxygen demand o Exertional dyspnea with central cyanosis o (hypercyanotic state) relieved Squatting Delaying of venous return decreased pressure in the right ventricle relieve of symptoms Knee chest position in babies o Clubbing of fingers due to peripheral hypoxia Shamrock test Due to peripheral hypoxia, additional capillaries are formed (collateral circulation is made) o Polycythemia due to chronic hypoxia Pediatric Nursing Can cause sluggish circulation formation o clots and thrombus lodge in cerebral circulation cerebral infarct Prevented by phlebotomy o Stunted physical growth and delayed development Management: o Palliative: Close Heart Goal: increase amount of blod going to the lungs Blalock Taussig (goal: increase amound going to lungs, anastomoses subclavian), Potts, Glenn Shunt, Waterson side to side anastomosis; not preferred since it may causes a weak wall which is prone to aneurysm o Corrective Open Heart o Nsg Mgt. Decrease demand for oxygen Cluster nursing care Allay anxiety Quiet play activity Small frequent feeding Propanolol (Inderal) Dilation of blood vessels Propanolol Penicillin Prophylactic antibiotic for bacterial endocarditis; lung filters Monitor Hgb and Hct count- detects early polycythemia Assist in phlebotomy as needed to be done Viscous blood is remove and replaced by plasma Increase fluids/Maintain IVF line as necessary Juicy fruits, Sherbets, Soup, Iced candy Positioning during attacks squat, kneechest- infants, give O2 Monitor activity tolerance/LOC ___________________________________________________ NEURAL TUBE DEFECTS Cause: inadequate intake of FOLIC ACID during pregnancy Not enough folic acid Posterior lamina is missing or absent contents went out 85% of children with neural tube defects develop HYDROCEPHALUS Drugs, radiation Sources of Folic acid o Green leafy vegetables o Nuts o Legumes o Brown rice o Strawberries Spina Bifida Oculta- hidden; no sac o Usually not visible externally o Dimple at sacral area o With hair o No intervention necessary Cystica- with sac o Intervention is necessary o Meningocele- consist of sac-like cyst of meninges filled with spinal fluid University of Santo Tomas College of Nursing / JSV Meningomyelocele- protrusion of a sac-like cyst containing meninges, spinal fluid and spinal cord with its nerves. Paralysis of lower extremities. Clubbed foot-talipes equinovarum. o Encephalocele- herniation of the brain and meninges through a defect in the skull - most dangerous o How to assess: Observe for movement of the lower extremities, apply pain With movement- meningocele (+) talipesequinovarus (clubfoot)meningomyelocele Overall objectives of nursing care: o Protect the sac against pressure, injury and infection Intervention: o Surgical closure preferred within 24-48 hours after birth to prevent local infection and trauma to the exposed tissues o Prone position o During feeding pressure on the sac o o No problem with breastfeeding o Cover the sac with sterile gause with plain NSS keep moisture to prevent cracks HYDROCEPHALUS o Hydrocephalus enlarged ventricles brain pushed against the cranium increased pressure baby still has fontanels, can expand able to accommodate the swelling o May be caused by a tumor o Complication of encephalitis o Bulb-shaped head, Sunset eyes, Distended scalp veins o High pitched cry, Increased ICP o Give morphine to decrease pain Interventions: o Position side-lying (especially if opisthotonic) o Assessment of signs of increased ICP: measure HCOD (head circumference of the day) o Measures to prevent increased ICP Surgical Management: o Ventriculostomy - to relieve pressure o Insertion of shunt to bypass the point of obstruction (ventriculoperitoneal shunt) So CSF can be recycled Drainage of CSF in the peritoneum CSF reabsorbed by the blood vessels o Shunt Revision- based on the length of the tube inserted in the body (scheduled) o Obstruction of catheter (unscheduled shunt revision) Increased ICP o Medications are not effective o In adults, permanent shunting is done with: Removal of brain lesions Clipping of aneurysms Post-op Nursing Care of Shunt Insertion: o Routine post-op VS monitoring o Position: FLAT on the unoperative side to prevent pressure on the shunt valve and too rapid drainage and reduction of CSF that may cause subdural hematoma o Do not carry the infant o Monitor for increased ICP o Observe for abdominal distention (peritonitis or abdominal ileus) o Pediatric Nursing ___________________________________________________ GIT PROBLEMS A lot of GIT problems are HEREDITARY 1. CLEFT LIP AND CLEFT PALATE Can cause problems with airway More common in males Cleft palate- speech, defects in ear, hearing problem SURGERY is a PRIORITY Will have coping problems as they grow up Surgery o Cheiloplasty/Z-plasty Cleft Lip Repair Usually done 3 times Not un urgent procedure, not life threatening Delayed until they are no longer surgically at risk o Rule of 10 (way of determining surgical risk) 10 lbs. 10 gms of Hgb (at least) Less than 10,000 WBC At least 10 weeks old (2 ½ months) Rarely used because if other perimeters are ok, surgery can proceed Pre-op: o Feeding technique: dropper used with SAP; drop at side o pressure Post-op: o Position: NEVER ON PRONE (No head control) o Prevent tension on the suture lines: LOGANS to hold suture in splace Anticipate needs to lessen crying Use of arm restraint Restraint removed every 2 hours; need consent Clean suture lines after feeding 2. CLEFT PALATE Surgery o Uranoplasty/Palatoplasty Done before speech development begins Cannot be done in the same time with cheiloplasty (kontra yung care plan) Post-op o SHOULD BE DONE ON PRONE To promote natural drainage of secretions o Observe for bleeding Frequent swallowing o Use ELBOW RESTRAINT To protect suture lines Prevents flexion of the arms o Feeding device post-op Drink from cups NEVER USE STRAW, nipple Big spoon for solids No breastfeeding ESSR enlarge nipple, suck (give time), swallow (give time), rest o Speech Rehabilitation/Hearing Test nasal twang 3. ATRESIA OF THE ESOPHAGUS No connection between the upper and lower segment of the esophagus University of Santo Tomas College of Nursing / JSV Manifestations o Drooling of mucus after birth o Mother with polyhydramnios 4. TRACHEOESOPHAGEAL FISTULA Fistula between esophagus and trachea Problems: o Aspiration Possible cause of death o Nutrition Manifestations o Observe reaction of baby to feeding o COUGHING CHOKING CYANOSIS Dx: o NGT- coiling o X-ray o Ultrasound Management: o Surgery ASAP Pre-op: o Prevent aspiration Suctioning Strict NPO o Promote nutrition Gastrostomy feeding TPN as ordered (check blood sugar) Check for patency of the tube Flush with small amount of h2o If hyperglycemic refer to MD give insulin as ordered 5. CHALASIA / GASTROESOPHAGEAL REFLUX (GER) Caused by immaturity of the cardiac sphincter Symptoms o Frequent reflux of stomach content right after feeding o No precipitating factors Mgt. Self-limiting (resolves as the child gets older) Proper feeding technique o Small frequent feedings o Thickened formula / breast milk o Upright position during feeding o Burp frequently during feeding o Right lateral semi-upright position after feeding Medical management: o Metoclopramide (Reglan) to increase Lower esophageal sphincter tone and to stimulate upper GI tract motility. o Ranitidine (Zantac) to inhibit gastric secretions o Surgery: Nissen Fundoplication 6. PYLORIC STENOSIS Caused by hypertrophy of the muscles of the pyloric sphincter NOT HEREDITARY Gradual hypertrophy of muscles of pyloric sphincter accumulation of food in stomach increased pressure vomiting f & e imbalance hypokalemia alkalosis Manifestations o Hours after they eat abdomen is distended o Positive peristaltic wave (waterbed) o Projectile vomiting (yellow, acidic, sour smell) Milk (curdles) o Dehydration o Metabolic alkalosis o Hypokalemia Pediatric Nursing o o Weight loss Palpable olive-shaped mass in RUQ Palpatory technique is least reliable o Barium Swallow X-ray String Sign Dx Dx: Congenital Aganglionic Megacolon Ganglion cells- nerve supply, nerve cells Absence of parasympathetic nerve supply (ganglion cells) on the large intestines Part affected constricts 4 segments of large intestine o Ascending o Transverse o Descending o Recto-sigmoid If large intestines is full of contents reverse peristalsis small intestine absorb the toxins stomach breaks down fecal matter Manifestations: o Early (nursery) Delayed meconium o Late Constipation (stool is very hard, quality!) Ribbon-like/pellet-like stool early signs University of Santo Tomas College of Nursing / JSV Pre-op: o Promote elimination Regular colonic irrigation Palliative COLOSTOMY o Promote nutrition High calorie High protein Vitamins Low in residue no fiber! Small frequent feeding if with distention Corrective Surgery: o Endorectal Pull-Through Procedures more difficult 7. INTUSSUSCEPTION Hyperactive portion of the small intestine telescopes/invaginates into the lumen of another Most common in infants Manifestations o Bile stained vomiting (green, bitter) since it comes small intestines o Blood vessels caught between the layers decreased blood supply necrosis bleeds currant jelly stools (blood with mucus in the stool) o Appendix might burst perforation peritonitis o Sausage-shaped mass o Spasmodic abdominal pain Management: o Barium Hydrostatic Reduction Technique GI tract is a hollow organ difficult to visualize a hollow organ without contrast (enema can low) Used as TREATMENT reduce the telescoping with barium given under pressure (enema can high increase pressure) Surgery o When barium hydrostatic reduction technique is not successful push barium out, reduce the telescoping with barium given under pressure o Prevent perforation and peritonitis 8. Rectal Biopsy Barium enema to determine extent tail! o Surgery o Fredet-Ramstedt Procedure Pyloromyotomy with pyroplasty Pre-op o Correct existing fluid and electrolyte imbalance IVF for dehydration/KCL for hypokalemia and alkalosis o Correct nutritional imbalance Thickened formula/TPN PRN Rice cereal (cerelac) Denser, heavier to vomit Abdominal distention with possible fecaloid vomitus Weight loss 9. IMPERFORATE ANUS More common in girls Manifestations: o Absence of meconium o Unable to insert rectal thermometer o If female: meconium passes via vagina (rectovaginal fistula) o If male: meconium passes through urinary bladder greenish urine (recto-vesical fistula); violates sterility of urinary bladder Management: o Step 1: Colostomy in the nursery (Palliative) o Step 2: Before 1 year old (10 months) Corrective Surgery: Anoplasty/ Pullthrough procedure Must heal first before closing colostomy Must delayed to allow the child to feel the urge o After 6 months Closure of colostomy o May be prone to fecal spillage; problem with control since only internal sphincter is present o Avoid foods with easy transit; dairy products o Sharts=ipot ___________________________________________________ KIDNEY PROBLEMS 1. A CC: abdominal mass Pre-op: o Avoid pressure over the mass Do not put on prone position Do not wear tight waist band Do not vigorously scrubbing the body Do not palpate Manifestations: vague, weight loss Management: o Nephrectomy followed by chemotherapy NEPHRITIS Cause Sx Caused by GABHS - Hematuria - Hypertension - Periorbital edema (local) NEPHROSIS/NEPHROTIC SYNDROME Unknown cause (auto-immune) - Proteinuria - Hypoproteinemia - Decreased plasma osmotic pressure fluid shifting edema ascites, Pediatric Nursing anasarca hypovolemia hypotension - Hyperlipidemia secondary to Dx Mgt - Increased BUN - Increased creatinine - Increased ASO titer (NV: 0-200 IU) - RBC in the urine - Renal biopsy - CBR in acute stage - Anti-HTN - Diuretics - Antibiotics (does not respond to penicillin) - Decreased Na, decreased CHON (variable) if increased creatinine - Skin Care - Additional pillows for periorbital edema mechanism to increase protein - Protein in the urine - Decreased serum protein Ambulate as tolerated Bed sore precautions Diuretics Steroids (Prednisone) can lead to bloated effect - High CHON, Low Na, Low fat diet - Skin care - PEDIATRIC RESPIRATORY CONDITIONS 1. THROAT PROBLEMS: PHARYNGITIS/TONSILITIS Caused by GABHS Manifestations: o Kissing tonsils Airway obstruction Can t be removed if it is inflamed because tonsils are highly vascular NO emergency tonsillectomy Wait till infection is over and swelling is controlled Management: o If (+) GABHS Antibiotic (penicillin/ erythromycin if with allergy) o Health center: Cotrimoxazole/ Amoxycillin o Soft to liquid diet in small frequent feeding o Comfort measures: Safe throat remedies: Calamansi, ginger, tamarind, breastmilk Calamansi- not given if with tonsillitis Warm saline gargle Antipyretic PRN (NO ASA) (Acetaminophen) (Biogesic, Tempra, Tylenol, Calpol) Gastric upset (earliest) Tinnitus (few days after intake) Bleeding (prolonged use) o o Less than 12 years old Viral infection Surgery o 2 criteria: big tonsil which causes dyspnea, collection of pus, recurrent inflammation 3 times a year or more o Tonsillectomy when on preschool (not in infants/toddler); planned required surgery; no incision Pre-op: University of Santo Tomas College of Nursing / JSV o Check dental (loose teeth) and bleeding status (bleeding disorder) - prevent aspiration Post-op: o Prone or Lateral position while asleep Promote natural drainage of secretion o Observe for bleeding Frequent swallowing and restlessness o If bleeding provide kidney basin spit blood o Prevent bleeding Ice collar- vasoconstriction on the are and decreasing pain Avoid suctioning, throat clearing Avoid valsava maneuver- frozen osteorized papaya o Diet resumes once fully awake and can swallow COLD, CLEAR, NON-IRRITATING Cool water, ice cold apple juice, frozen gelatin, suck on frozen popsicle, sherbet Ice cream NOT ADVISABLE, if given, make sure child drinks lots of cold water after Iced cold ginger ale Then SOFT diet then DAT No red colored juices 2. SPASMODIC CROUP/LARYNGOTRACHEOBRONCHITIS (LTB) Etiology: Virus Manifestations o Hoarseness of voice o Cough-brassy spasmodic seal like sound, sucessively o Inspiratory stridor o Fever o Unconsciousness o Laryngospasm respiratory distress Management: o Supportive Care Prevent coughing causing laryngospasm and respiratory distress Avoid respiratory irritants and sudden temperature changes Feed and hydrate with aspiration precaution Decrease demand for oxygen Administer high humidity with MIST THERAPY during attacks Bring child inside steamy bathroom for 15 minutes pakulo, ilagay sa plangana, towel to inhale Cool mist vaporizer (steam inhalation) 3. BRONCHIAL ASTHMA Asthma in children is only acute Only bronchioles are affected Condition can be reversed If chronic may reach alveoli later on in life EMPHYSEMA 2 Kinds of Asthma: o Extrinsic Asthma- allergen from the outside (food, environment) Foods rich in protein, iodine Foods with artificial colors Foods with preservatives o Intrinsic Asthma- idiopathic/ innert on the patient Stress Anxiety Mechanisms responsible for symptoms: o Bronchospasm o Inflammation and edema of the airways Pediatric Nursing o Accumulation of tenacious secretions Complications: ACIDOSIS Management o Allergen control Skin testing followed by Hyposensitization (for 3 years) Supportive Management during exacerbation o Administer bronchodilators/ aerosol o IVF for hydration and drugs (aminophylline, steroids for status asthmaticus o Position Upright Orthopneic o Allay anxiety o Promote oral fluids with aspiration precaution Limit milk Avoid vitamin C- allergen o Promote breathing exercises (purse-lip breathing) Swimming 4. EPIGLOTTITIS Air is obstructed Cause: hemoophilus influenza Sx: Drooling, dysphonia, dysphagia, child sits upright leaning forward with chin thrust out (Tripod/sniffing position) Management o Hospitalization ASAP o Do not insert anything into the mouth o Prepare tracheostomy set at bedside o IVF for hydration and antibiotic (Cephalosporin) for 7-10 days o Corticosteroid PRN to decrease inflammation o Prevention by immunization: H Influenza type B (Hib) vaccine Dx o Lateral Neck X-Ray 5. PEDIATRIC ASTHMA PEDIATRIC ASTHMA Acute Affects bronchial area only Good prognosis/Reversible Cure is possible ADULT ASTHMA Chronic (as seen in COPD) Irreversible No cure Remission and exacerbation Same causes: Extrinsic Asthma triggers that produced symptoms (easy to control) Intrinsic Asthma caused by the person itself ex. stress, anxiety Mechanisms responsible for symptoms: 1. Bronchospasm 2. Inflammation and edema of the airwats 3. Accumulation of tenacious secretions Death due to RESPIRATORY ACIDOSIS Allergologist Allergen control skin testing followed by hyposensitization (for 3 years) to increase tolerance Mx during Exacerbation *Administer bronchodilators/aerosol *IVF drugs (aminophylline, steroids) *Position: orthopneic position *Allay anxiety * Promote oral fluids with aspiration precaution limit milk, avoid vit C * Promote breathing exercise (purse lip breathing) Status asthmaticus do not respond to treatment; given steroids 6. RHEUMATIC FEVER Complication of -strepto infection Jones Criteria Assessment Manifestations: o Migratory polyarthritis joint pains o Chorea (St.Vitus Dance) involuntary jerks/ misconstrued as mannerisms o Erythema marginatum rashes on the trunk o Subcutaneous nodules on the extensor side o Carditis - endocarditis covers the chambers and forms the valves o Mitral valve stenosis Dx: o Jones Criteria plus ASO titer = rheumatic fever Normal value of ASO (Anti-streptolysin O) = 0-200 IU o Echocardiography if with valve damage (Mitral valve: stenosis/insufficiency) = rheumatic heart disease Management: o OBJ 1: Decrease demand from the weakened heart CBR/Modify lifestyle after discharge Cluster care o OBJ 2: Prevent further cardiac damage (RHD) Meds: Penicillin IM once a month for 3-5 days/ASA/Steroids EMLA patch: lidocaine; numbs the part to be injected o OBJ 3: Safety precaution for chorea 7. KAWASAKI DISEASE Mucocutaneous lymph node syndrome; fatal and rare Etiology: unknown Manifestations: o Fever unresponsive to antibiotic, conjunctival inflammation, strawberry tongue, erythema of palms and soles with peeling, cervical lymphadenopathy o Most dangerous when coronary artery is involved; aneurysm formation and risk for rupture Management: o High dose of IV GAMMA GLOBULIN o Aspirin o Monitor cardiac status. Assess for symptoms of CHF o Monitor I&O o Comfort measures: skin and mouth care o Promote adequate rest HEMATOLOGIC PROBLEMS *Aplastic anemia- occupation (rad tech) 1. IRON DEFICIENCY ANEMIA Above 6 months- at risk for anemia o Iron from mother has been used up and due to overfeeding of milk Adolescent- due to weight reduction diet and heavy menstrual loss University of Santo Tomas College of Nursing / JSV Pediatric Nursing Management o Introduction of supplementary/ complementary feedings at 6 months (one at a time only to rule-out allergy) o Iron rich foods: Cereals LUGAW Potato, Egg yolk DO NOT GIVE EGG WHITE UNTIL BABY IS ABOVE 1 YEAR OLD (ALLERGY) Dark green leafy vegetable; the darker the leaves, the higher the iron content Dark meat (organ meat), beef liver Iron fortified milk preparation Supplemental iron preparation (FeSO4) with Vitamin C Tell mother that stool turns black prevents absorption of iron Use straw, brush teeth and tongue 2. HEMOPHILIA Deficient in Factor VIII (Antihemophilic Factor) Pattern of transmission is X-linked Transmitted as X-linked from carrier MOM to AFFECTED SON (symptomatic) Daughter gets it as a trait from carrier mom (asymptomatic) Affected son gives it to daughters as a trait only Affected sons will have all normal sons Xa X X X aX XX y X ay Xy Xa X Xa Xa Xa Xa X y X ay Xy *Impossible to happen Early Symptom o Prolonged bleeding from the umbilical cord o Early petechiae Late Symptoms o Easy bruising o Easy epistaxis and gum bleeding o Hemarthrosis- bleeding in between the ball joints (pain and swelling) Given morphine, tramadol, demerol o Intracranial hemorrhage major cause of death Management o Medical: Transfusion of Factor VIII, cryoprecipitate, platelet concentrate o Vasopressin (ADH) activates clotting factors o Prevent bleeding (avoid trauma) contact sports Soft bristled tooth brush No aspirin o Can undergo circumcision, removal of teeth as long as Factor VII is ok o P- protect (protective devices) o R- rest (immobilize) o I- ice (vasoconstriction) o C- compress (apply pressure) o E- elevate (above the heart) o S- support (parents, MDs, RNs, dentist, PT, nutritionist, psychiatric, etc.) 3. LEUKEMIA Most common form of childhood cancer University of Santo Tomas College of Nursing / JSV Malignant disease of the bone marrow and the lymphatic system Imature WBC (lymphoblasts) increased formation of lymphoblasts cancer Immature WBC not capable of phagocytosis is formed Lymphocytic Lymphoblasts from lymphatic system Most common in pediatrics Good prognosis Myelocytic Lymphoblasts from myeloid stem cell (which becomes RBCs, WBCs, Platelets) Common in adults Poor prognosis (6 months- 2 yrs) 3 Primary consequences: o Infection, Anemia, Bleeding tendencies Manifestations: Bone pain Earliest sx: Intractable infection Dx: o Peripheral blood smear o Bone Marrow biopsy (more definitive) Lumbar puncture To determine CNS involvement o Position: Prone in children o Site: Iliac crest Management (4 phases) o Remission Induction IV (systemic chemotherapy) Protective isolation o CNS Prophylactic/ Sanctuary Therapy Intrathecal chemotherapy Sanctuary therapy o Intensification/ Consolidation Therapy Regular systemic and intrethecal chemo Hairfall o Maintenance Therapy combining drug regiment with periodic CBC, CXR, Lumbar tap o 2 years of remission is considered cure! Most ideal: BONE MARROW TRANSPLANT (Most Ideal) o Difficult to find a compatible match o Should be HLA compatible (Human leukocyte antigen) Below 5 years old o Death is a form of a sleep; Reversible o From fairy tales 6-9 years old o Death is a person;reversible o Grim Reaper, Bogeyman, Devil monster, Above 9 years old o End of life on earth; Irreversible