CONTENTS LIST Cardio lo gy - Self-Assessment 117 SELF -A S S E S S ME N T CO M MU NIC AT I ON/ETH ICS Topic: Discussion with patient with heart failure around lifestyle modifications following a presentation of acute decompensated heart failure. KEY POINTS: • Initiate the session Greet patient, obtain patient’s name, introduce self Demonstrates respect and interest, and attends to patient’s physical needs • Providing the correct amount and type of information Chunks & checks ‘Mr Jones can you tell me about your condition and the problems that you have been having?’ ‘Did you know a large part of preventing future episodes of heart failure are down to lifestyle modifications?’ ‘These changes can be small but can make a big difference to your health’ They can be difficult to follow all of the time but they are important your future well being.’ Address any concerns or knowledge gaps the patient has Give explanation at appropriate times • Aiding Accurate Recall and Understanding Organises Explanation (discrete sections with logical sequence) ‘The changes we would like you to make revolve around reducing the amount of fluids you have in a day, reducing salt intake reducing alcohol intake and keeping track of your weight’. 'Most of the symptoms that made you feel unwell are to do with the amount of fluid in your body'. 'If you reduce your Fluid intake to 1 to 1.5 L a day it will significantly help your heart to keep working efficiently'. 'Salt is important in regulating how much fluid is in your body it. The more salt we take in the more likely we are to retain fluid'. CARDIOLOGY CONTENTS LIST RCSI 11 8 Ca rd i o l o g y - S e l f - A s s e ssme n t CONTENTS LIST '1 teaspoon of salt equals 2.2 g of sodium'. 'We recommend you should not to exceed 1 teaspoon of salt a day'. 'You should limit your alcohol intake limited to 2 drinks a day or as low as you can get it down'. 'Monitoring your weight is a really proactive way that you can stay on top of your heart failure if you notice more than 0.9 kg (>2 pounds) weight gain in 24 hours, 2 days in a row, or develop symptoms of shortness of breath, chest pain, palpitations, increased tiredness, dizziness. or lightheadedness, or increasing swelling of the legs or abdomen, then you should come back to us here in the hospital'. Check patient’s understanding periodically ‘Do you have any questions so far, Mr Jones ?’ • Achieving a Shared Understanding: Incorporating the patient’s perspective How do you feel about making these changes? ‘Do you need any further clarification?’ Elicit patient’s beliefs, understanding and reactions Pick up and respond to patient’s verbal and non-verbal cues • Planning: Shared Decision Making Relate explanations to patient’s perspective Provide opportunity to encourage patient to contribute ‘These changes will help to contribute to you staying well and keeping your heart healthy.’ Involve patient & explore management options Negotiate a mutually acceptable plan ‘I can provide you with some literature and link you in with our specialist nurse who has some more information about how to proactically apply these strategies.’ Checks with patient if they accept the plan and concerns have been addressed • Closing the session Summarise session Safety net ‘Should you have any other questions or queries then please come back to me and ask me and I can get you the information. Final check - patient agrees and is comfortable with the plan R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 CARDIOLOGY CONTENTS LIST CONTENTS LIST Cardio lo gy - Self-Assessment 119 Other topics to consider : • Explaining limitations in terms of physical exercise to someone who has had a STEMI • Explaining a valvular replacement procedure to someone with critical AS • Explaining the need for prophylactic antibiotics following IE • Discussing lifelong anticoagulation medication in refractory A fib. CARDIOLOGY CONTENTS LIST PRACTICE YOURSELF Practice yourself using the Calgary Cambridge method RCSI CONTENTS LIST Re spirato ry - Self-Assessment 223 SELF -A S S E S S ME N T CO M MU NIC AT I ONS / ETH ICS SCENA R I O S Communication should be a collaborative process with the patient. The Calgary-Cambridge model acts as a framework for developing your communication skills. One worked example (smoking cessation) is seen below and an additional of topics to practice and discuss with colleagues. Topic: Obtaining Consent for a Bronchoscopy KEY POINTS: • A bronchoscopy is a day procedure usually performed in an endoscopy unit or in the ICU. The bronchoscope is a flexible tube used to visualise the vocal chords and airways, and to obtain tissue samples. The patient receives sedation but not general anaesthesia so can be aware or alert during the procedure • Indications: Bronchoscopy is used for the investigation of symptoms such as haemoptysis, and persistent cough, or it may be used to investigate and evaluate the airways in infection. • Potential Complications: Desaturation (>5%), Pneumothorax (<0.5%), Infection (<5%), Cardiac arrythmias (1-5%), bleeding from biopsy (1-5%), Asthma like reaction (1-5%), Laryngospasm (<1%), fever (<1%), death (rare), as well as complications from the sedation. • Types of tissue samples: Endo-bronchial biopsy, bronchial brushings, bronchial washings, transbronchial biopsy, trans-bronchial needle aspiration (EBUS), broncho-alveolar lavage. RESPIRATORY CONTENTS LIST COMMON PITFALL Bronchoscopy is not the same as EBUS. EBUS is an endobronchial technique using an US to visualise +/guide a biopsy of surrounding structures e.g. mediastinal lymph nodes. RCSI 22 4 Re s p i r a t o r y - S e l f - A s se ssme n t CONTENTS LIST Topic: A Brief Health Intervention for Smoking Cessation KEY POINTS: • Unassisted quit rate is 2-3%. A brief health intervention increased that rate by 1-3% (which only takes 5-10minutes) • Smoking/ tobacco use is one of the largest causes of preventable death • Brief advise on the dangers of smoking should be given at every opportunity • A brief intervention is a range of effective health behaviour change interventions that are patient-centred, short and can be provided in a variety of healthcare settings • The 5 A’s Model can be used as a framework when raising the issue of smoking and support them in their attempt to quit. 1. A – Ask Identify and document tobacco use for every patient at every visit “Do you smoke? How much do you smoke per day? How many years have you been smoking for?” 2. A – Advise In a clear, strong and personalised manner urge every tobacco user to quit “Smoking is detrimental for your health. Your breathing difficulties from COPD, have been caused by your smoking habit. It is extremely important for you to stop smoking, to prevent your COPD getting worse, reduce your lung cancer risk and improve your overall quality of life” 3. A – Assess Is the tobacco user currently willing to quit? “Have you considered quitting yourself? Are you ready to give up smoking?” 4. A – Assist For the patients willing to quit, support them with counselling and pharmacotherapy to assist them in their attempt to quit “I can help you in your efforts to quit smoking. There is a hospital Tobaccos Cessation Support programme that I can refer you to. I can also prescribe nicotine replacement patches to help with cravings when you stop smoking” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 RESPIRATORY CONTENTS LIST CONTENTS LIST 5. Re spirato ry - Self-Assessment 225 A – Arrange Schedule a follow-up contact in person or by telephone, preferably within the first week of the quit date “What date do you want to set for yourself to quit?” “I will call you on the following Thursday to see how you’re getting on, and if there is anything more I can do support you” Topic: Breaking Bad News: New Diagnosis of Lung Cancer KEY POINTS: • Prepare adequately for the consultation, ensuring you’ve read all of the patient’s background medical history and have all of their test results and anticipated some of the questions they may have after hearing the news. • SPIKES Framework is a helpful model for structuring the consultation. Also use the Calgary-Cambridge Model for giving Information in conjunction. S - Setting Choose a comfortable, private and quiet room This may not always be possible, but avoid standing in a corridor Have tissues available and ensure you are uninterrupted Check with patient if they would like a family member or friend in with them P - Perception Establish the patient’s starting point and what they already know or what they might be expecting Discuss the events leading up to the diagnosis: symptoms, investigations, scans, biopsies I - Invitation Check if the patient is ready to receive their results today. Some patients may recognise it is not the news they hoped for and may want to put off the results K - Knowledge Deliver the information in sizeable chunks (warning shots), avoiding medical jargon Leave pauses to allow the patient to digest what you’re telling them Provide the diagnosis in clear and unambiguous language RESPIRATORY CONTENTS LIST RCSI 22 6 Re s p i r a t o r y - S e l f - A s se ssme n t CONTENTS LIST E - Emotions and Empathy Ensure you tone is respectful, slow and clear Recognise and respond to emotions If you do not know information or answer to their question, tell them that you do not know and make an effort to find accurate information as soon as is possible or after discussion with their specialist S - Strategy and Summary Make a plan together and inform the patient what the next steps are Written material can be helpful Ensure the patient’s questions and concerns have been addressed Highlight where the patient can go for more questions or concerns Offer to inform family members or NOK for them if they wish R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 RESPIRATORY CONTENTS LIST Ga st roente ro lo gy - Acute Ga stroenteritis 243 CONTENTS LIST • GI acute complications (less likely in viral gastroenteritis) Bowel perforation Fulminant colitis Toxic megacolon Intestinal obstruction • GI chronic complications Post-infectious Irritable Bowel Syndrome: may improve with trial of oral probiotics or Rifaximin. Recurrent or refractory Clostridium difficile infection • Other: Haemolytic Uraemic Syndrome (Associated with EHEC O157:H7). HUS is a triad of microangiopathic anaemia, renal failure, and thrombocytopenia P R O GNOS IS • Most acute gastroenteritis episodes are self-limiting CO M MU NIC AT I ON AND ETH ICS Topic: Open Disclosure in the case of healthcare-associated diarrhoea (C. diff). Explain to a patient about their diagnosis and cause of same. KEY POINTS: • Initiate the session Greet patient, obtain patient’s name, introduce self Demonstrates respect and interest, and attends to patient’s physical needs • Providing the correct amount and type of information Chunks & checks “Mr. Smith, can you tell me about your feelings/ knowledge about what has happened so far?” Address any concerns or knowledge gaps the patient has Give explanation at appropriate times • Aiding Accurate Recall and Understanding Organises Explanation (discrete sections with logical sequence) “When you first came in Mr. Smith, you were suffering from symptoms of pneumonia” GASTROE NTEROLOGY CONTENTS LIST RCSI 24 4 G as t ro e n t e ro l o g y - Ac u t e Gast ro e n t e r it is CONTENTS LIST “You were treated with an antibiotic called co-amoxiclav, to help treat your pneumonia” “This helped clear up the lung infection but unfortunately has resulted in a second infection of the bowel” “This is why you are having frequent diarrhoea” “This infection is called C.diff and it relates directly to the antibiotics that we prescribed you” “I am sincerely sorry this has happened to you” Check patient’s understanding periodically “Do you have any questions so far, Mr. Smith?” • Achieving a Shared Understanding: Incorporating the patient’s perspective Relate explanations to patient’s concerns, expectations and ideas Provide opportunity and encourage patient to contribute “Do you need any further clarification?” Elicit patient’s beliefs, understanding and reactions • Pick up and respond to patient’s verbal and non-verbal cues Planning: Shared Decision Making Relate explanations to patient’s perspective Provide opportunity to encourage patient to contribute “In order to treat this infection, we need to give you another antibiotic. This is a different antibiotic that you have NOT had before” Involve patient & explore management options • Negotiate a mutually acceptable plan “We can start the antibiotic today, if you are agreeable?” Checks with patient if they accept the plan and concerns have been addressed Closing the session Summarise session Safety net Final check patient agrees and is comfortable with the plan R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 GASTROENTEROLOGY CONTENTS LIST 26 8 G as t ro e n t e ro l o g y - I n flammat o r y Bo we l Dise ase TOP TIP Other topics may include: 1. Providing dietary advice and management of flares. 2. Counselling around conception and pre-natal health as well as drugs such as methotrexate, and biologics during conception and pregnancy. (IBD patients have increased risk of voluntary childlessness) CONTENTS LIST C OMM UNICATION/ETH ICS Topic: Education regarding need for colonoscopy surveillance Purpose of Consultation: To explain and provide information on the need for colonoscopy surveillance to a patient with IBD. A patient with IBD has an increased risk of colorectal cancer especially after about 8-10 years after initial flare. KEY POINTS: • Initiating the session Greet patient & introduce yourself and your role Demonstrate respect and interest • Providing the correct amount and type of information Chunks & Checks Assess the patient’s starting point “Mr. Reid, what is your understanding of why you have been getting regular colonoscopies?” “Do you know what your last colonoscopy showed?” “How do you tolerate the colonoscopy procedure?” Use patient responses to guide how to proceed • Aiding Accurate Recall and Understanding Organise your explanation (can use categorisation to help) “Colonoscopy surveillance is done regularly in order for us to be able to detect any abnormalities early and treat it” “People with your condition have an increased risk of developing abnormal cells, called dysplasia, and if left untreated they could result in bowel cancer” Use repetition and summary to reinforce Avoid medical jargon Use visual methods if needed to convey information Check patient’s understanding: “Could you tell me what you have understood from our conversation so far?” • Achieving a shared understanding- incorporation the patient’s perspective Discover the patient’s thoughts and feelings about the information and encourage interaction rather than a one-way transmission R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 GASTROENTEROLOGY CONTENTS LIST CONTENTS LIST Ga st roent erol ogy - Infla mma tory Bowel Disea se 269 Provide opportunity and encourage the patient to contribute Respond to verbal and non-verbal cues “Do you have any questions or concerns about anything?” • Planning: Shared Decision Making Allow patient to understand decision-making process “The timing of your next surveillance colonoscopy depends on the duration of your disease, and the findings on the last colonoscopy” “Depending on these factors, according to official guidelines, a colonoscopy may be booked for you every 1, 3 or 5 years” Involve patient in decision making and explore management options, and negotiate a mutually acceptable plan Check with patient if they accept plan and if concerns have been addressed “Are you happy for me to proceed and book your next surveillance colonoscopy?” “Have I addressed all your questions and concerns” • Closing the Session Forward plan and safety net, and ensure appropriate point of closure FU RTHE R RE A DING • ECCO guidelines for management of IBD Management of UC available here Management of CD available here GASTROE NTEROLOGY CONTENTS LIST ONLINE RESOURCE RCSI 28 8 G as t ro e n t e ro l o g y - Malab so r p t io n CONTENTS LIST C OMMUNICATIO N/ETH I CS Topic: Medical Ethics and Nutrition KEY POINTS: • Malabsorption is a spectrum of disorders leading to a specific adverse outcome for patients. Management requires an MDT approach and development of specific communication skillset by the clinician to identify condition, investigate cause and support treatment plan and therapeutic trials, facilitated by allied health professionals. This requires a lot of patient communication and often psychological supports • Irish Medical Council Guide to Professional Conduct 2016 also comments on Nutrition and Hydration: ONLINE RESOURCE “45.2 If a patient is unable to take sufficient food or drink orally, you should consider giving nutrition and/or hydration by subcutaneous, intravenous or enteral feeding routes. You should assess whether doing this will be of overall benefit to the patient, taking into account the patient’s views, if known, and balancing the benefits, burdens and risks of each form of treatment. You should be sensitive to the emotional impact on the patient and their family of not providing nutrition and/or hydration. If you decide that providing artificial nutrition or hydration through medical intervention will not be of overall benefit to the patient, you must make sure the patient is kept as comfortable as possible and their symptoms addressed. Where possible, you should tell the patient and/or those close to them of your decision and the reasons for it” F U RTH ER READ ING ESPEN is a good source for information on nutrition assessment, malabsorption and intestinal failure available here R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 GASTROENTEROLOGY CONTENTS LIST CONTENTS LIST G a s t roent erol ogy - Eme rg e n c y: No n -Va ricea l Upper GI H a emorrha ge 301 CO M P L IC ATION S • Shock • Acute kidney injury • Perforated peptic ulcer disease • Rebleeding (40% mortality in patients with a rebleed) • Death P R O GNOS IS • In patients aged > 80, with multiple comorbidities, disseminated cancer and renal or liver failure, mortality is up to 75%. • Use of prognostic scoring identifies patients with poor prognosis for early endoscopic intervention (Rockall score= risk stratification to identify patients with likely adverse outcomes after OGD) CO M MU NIC AT I ON/ETH ICS Topic: Obtaining consent for an OGD KEY POINTS: • For full Calgary-Cambridge Model example see PSC Chapter Communication/Ethics section • Consent for OGD in upper GI haemorrhage is important, especially since the aetiology is unknown until the investigation performed. Therefore, consent should cover the diagnostic test, risk of bleeding and risk of sedation, along with the risks associated with endoscopic injection, clipping, gold probe and APC interventions. FU RTHE R RE A DING Expert Review: Management of acute upper gastrointestinal bleeding. BMJ 2019; 364:l536 GASTROE NTEROLOGY CONTENTS LIST FURTHER READING RCSI CONTENTS LIST Hepatology - Liver Failure (Acute & Chronic) 329 P R O GNOS IS • Child-Pugh and Maddrey Grading Scales can guide prognosis • Median Survival: • Compensated Cirrhosis = 12 years • Decompensated Cirrhosis = 1.6 years CO M MU NIC AT I ON/ ETH ICS Topic: Obtaining consent to perform a Large Volume Paracentesis KEY POINTS: • Initiating the Session & Establishing rapport Greets patient, confirms their name and introduces self Demonstrates respect and interest • Identifies the reason for consultation “What is your understanding about what is happening so far?” Answer any questions/ concerns the patient may have. “I’m here today to discuss a procedure, we would recommend, to help with the swelling/ fluid in your abdomen.” • Providing the correct amount and type of information Chunks and Checks Give information about procedure in manageable chunks and check patient’s understanding. “The procedure involves the insertion of a needle, using local anaesthetic, to drain the fluid from your abdomen” • Aiding accurate recall and Understanding Organises explanation and plans related to the patient’s perspective Uses clear & concise language “The procedure is performed at the bed side.” “Local anaesthetic is used to numb the area, in order that you don’t feel any pain.” “The needle is used to insert a tube into the abdomen, and then the needle is removed while the tube stays in place.” “The tube will then remain in place for 6-8 hours to drain the fluid from the abdomen, before being removed. The removal is not painful.” “Do you have any questions so far?” HEPATOLOGY CONTENTS LIST RCSI 33 0 Hepatology - Liver Failure (Acute & Chronic) CONTENTS LIST • Achieving a shared understanding Relates explanation to patient’s perspective Ask the patient what information is helpful. Benefits of procedure “When the ascites/fluid is drained, your abdomen will be a lot softer and less uncomfortable. You’ll also be able to breathe more easily. During the procedure a sample can be taken to help diagnose the problem” Risks of the procedure “The risks of the procedure include but are not limited to; pain & discomfort around the insertion site, bleeding at the site, internal bleeding, injury to a blood vessel, organ puncture, infection, adverse reaction to the local anaesthetic (lidocaine)” These are the risks but not always appropriate to give long list like this. Risk of not doing the procedure “The fluid accumulation could become worse, impairing your diaphragm from working properly, and making it difficult to breathe for yourself.” Provides opportunity and encourages patient to contribute Elicits patient’s beliefs and reactions “Do you have any questions or concerns on anything we have discussed so far?” • Planning: Shared decision making Involves the patient and encourages them to contribute their own ideas and explores management options with patient Negotiates a mutually acceptable plan & checks with patient if they accept the plan and if all of their concerns have been addressed “Do you have any further questions before we proceed, or has anything been unclear that you would like further information on? Is it acceptable to you to proceed with the large volume paracentesis procedure?” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST 34 0 Hepatology - Non-Alcoholic Fatty Liver Disease KEY POINT TIPS procedures can precipitate hepatic encephalopathy CONTENTS LIST Statins Important to use in NAFLD due to increased cardiovascular risks particularly in NASH Careful to monitor rise in transaminases Use with caution in Cirrhosis as increased risk of Rhabdomyolysis • Procedural management TIPSS: treatment of Portal hypertension in interventional radiology in end stage decompensated liver disease • Surgical Management Bariatric Surgery: the most effective therapy for NAFLD; not only does it cure diabetes, but it leads to the resolution of NASH in >90% cases at one year. Liver transplant for advanced decompensated liver disease or HCC C OMPLICATIONS • End-stage liver disease and its sequelae P RO GNOSIS • 1/3 of patients will die from CLD or progress to liver transplantation • NAFLD: MELD scoring system may be used; the higher the score the higher the mortality. • NASH: approx. 1/3 remain stable (fibrosis stage), 1/3 progress and 1/3 regress • Increased overall mortality risk with NASH, and higher rates of CVD related deaths C OMMUNICATIO N/ETH I CS Topic: Counselling the patient on weight loss and importance of same KEY POINTS: • Initiate the session Greet patient, confirm name and introduce self and your role. Demonstrate respect and interest R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST CONTENTS LIST Hepatology - Non-Alcoholic Fatty Liver Disease 341 • Providing the correct amount and type of information Chunk & check Give information in chunks and check patient’s understanding 5As framework Ask Elicit if patient is open to discussing their weight Assess patient’s starting point “What is your understanding about your condition?” “Is this a good time to discuss your weight?” KEY POINT The 5As framework is integrated through the Calgary-Cambridge model. 5As Framework for behaviour change - Ask - Advise - Assess - Assist - Arrange If the patient is not ready to undertake behaviour change, the consultation won’t progress. Advise Benefits of losing weight “I think if we could make lifestyle changes, we could prevent your liver disease from progressing” “10% weight loss can result in >90% of the fat being shifted from the liver.” Assesses Elicit the patient’s health status, psychosocial factors and barriers to weight loss. What have they tried in the past? Assist Help the patient to develop a weight loss goal and a plan of action. Arrange Identify a way to execute the plan successfully • Aid accurate recall and understanding Use clear and concise language Use signposting and categorisation “First thing is to look at your diet…” “Second thing is to look at your level of physical activity” • Achieving a shared understanding Provides opportunity and encourages patient to contribute Elicits patient’s beliefs, reactions and feelings HEPATOLOGY CONTENTS LIST RCSI 34 2 Hepatology - Non-Alcoholic Fatty Liver Disease CONTENTS LIST • Planning: Shared decision-making Aim to involve the patient in the decision-making process and aim to increase patient’s commitment to plans made Negotiate a mutually acceptable plan Check with patient if plan is acceptable F U RTH ER R EAD ING ONLINE RESOURCE • EASL Guideline on the Management of Non-Alcoholic Fatty Liver Disease: available here R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST CONTENTS LIST Hepatology - Viral Hepatitis 353 CO M MU NIC AT I ON/ETH ICS Topic: HBV: Counselling the need for family screening and for compliance with long-term antiviral therapy KEY POINTS: • Rationale of consultation is to: Educate the patient around transmission with a view to halting further infections. Counsel them regarding long term antiviral drug compliance Counsel them regarding need for family screening • KEY POINT This guide follows the Calgary-Cambridge Communication Framework Initiate the session Greet patient, obtain name and introduce self Assess patient’s starting point “What do you know about hepatitis B and how it affects you?” “How do they feel about testing and screening?” “Do they have concerns about long-term therapy/ screening?” Chunk and Checks Gives information in manageable chunks, checks for understanding, uses patient’s response as a guide to how to proceed “Are you aware of how you might have contracted the virus?” “Do you know how to stop further transmission of the infection?” “HBV is a blood born virus, which can be transmitted through bodily fluids or ‘vertically’ if the person is pregnant” • Aiding accurate recall and understanding Organises explanation and plans related to the patient’s perspective Uses repetition and summarisation to reinforce information Uses concise and easy to understand language “HBV is a blood born that may spread through the use of contaminated needles, contaminated blood products, or through sexual contact.” “HBV can survive outside the body at least 7 days and be capable of causing infection.” HEPATOLOGY CONTENTS LIST RCSI 35 4 Hepatology - Viral Hepatitis CONTENTS LIST “HBV is highly contagious, and transmission occurs between sexual partners and household contacts with infected blood or other fluids as well as contact with skin lesions.” “Highest rates of infection occur between sexual partners.” “Screening and vaccination are recommended for household contacts, including children of those newly diagnosed with HBV.” “People should not share toothbrushes or razors. All open wounds cuts and scratches should be covered, and any blood spillages should be cleaned with bleach solution.” “To avoid transmission of the virus to other people, compliance with lifestyle factors and anti-viral medications is important” Check patient’s understanding periodically. • Achieve a shared understanding: Incorporating the patient’s perspective Provides opportunity and encourages patient to contribute Picks up and responds to verbal and non-verbal cues Elicits patient’s beliefs, reactions and feelings. “Do you have any questions and concerns on what we have discussed so far?” • Planning and shared decision making. Explores management options Negotiates a mutually acceptable management plan “We will arrange for your family to be screened and vaccinated against Hepatitis B.” “You will continue to take your anti-viral medications regularly” • Closing the session: Forward plan and summarise session Final check patient comfortable with plan “Are you happy with the plan?” “Do you have any further questions or concerns that I have not yet addressed?” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST CONTENTS LIST Hepatology - Haemochromatosis 365 • Chronic heart failure Cardiomyopathy, conduction defects, arrhythmia • Hypogonadism • Bone mineral density loss • More prone to infection P R O GNOS IS • If Diagnosed before onset of cirrhosis and diabetes patients will have a normal life expectancy • If diabetes is present, there is a 4.3 increased relative risk of death • If cirrhosis is present, there is a 2.4 increased relative risk of death • 11% increased risk of dying of cancer (especially hepatocellular carcinoma) CO M MU NIC AT I ON/ETH ICS Topic: Genetic counselling regarding diagnosis and screening of family members, or consent prior to ordering the HFE test. KEY POINTS: • Initiate the session Greet patient, introduce oneself and your role Establish Rapport Identify reason for consultation To discuss the implications of a positive diagnosis of haemochromatosis in terms of genetic screening for the patient’s family. KEY POINT Use the CalgaryCambridge Framework for Communication • Providing the correct amount and type of information Assess patient’s starting point “What is your understanding of your diagnosis?” “Are you aware as that there is a genetic component to HH?” “Are you aware that there is a screening programme in order to identify those with the genetic component in order to help prevent the development of complications?” HEPATOLOGY CONTENTS LIST RCSI 36 6 Hepatology - Haemochromatosis CONTENTS LIST Chunks and Checks “How do you feel about genetic testing and screening?” “Do you have any concerns about screening?” “What is your understanding of the treatment and the long-term management for haemochromatosis?” • Aiding Accurate Recall and Understanding Organises explanation and plans related to the patient’s perspective KEY POINT Genetic screening has a wider impact than just the patient being tested. For example, think about the impact testing for the Hunting Gene, or BRACA gene would have on a family. The initial consultation to discuss testing may need to be followed up with a further consultation, where you meet a wider family group. FURTHER READING Uses clear & concise language “A blood test will be able to tell us what gene mutation is causing your haemochromatosis” “The gene may be passed on to offspring. Your partner and children should be screened for the gene” “If anyone tests positive, through screening, we can arrange follow up for them to avoid them developing complications.” • Achieving a shared understanding incorporating the patient’s perspective Relates explanations to patient’s perspective Provides opportunities and encourages patient to contribute “Do you have any questions or concerns at this point?” “Is there anything that has been unclear up until this point?” • Closing the session: Planning and shared decision-making Explores management options Forward plan and summarise session Final check patient comfortable with plan and all concerns have been addressed. F U RTH ER R EAD ING • 2010 EASL guidelines available here R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST 37 4 Hepatology - Wilson’s Disease KEY POINT Guide to Professional Conduct and Ethics for Registered Medical Practitioners 8th Edition 2019: o 17.1 Genetic testing can help to diagnose an illness or help to predict the development of an illness in the future. Patients must have counselling about the possible consequences of genetic testing before you seek their consent KEY POINT Use the CalgaryCambridge Model of Communication CONTENTS LIST C OMMUNICATIO N/ETH I CS Topic: Consent and genetic counselling of a patient with suspected Wilson’s Disease KEY POINTS: • Initiate the session Greet patient, introduce yourself and explain your role Establish Rapport Identify reason for consultation Genetic counselling and consent for genetic testing for Wilson’s Disease • Providing the correct amount and type of information Assess patient’s starting point "What is your understanding of your diagnosis?” “Are you aware that there is genetic component to your condition and that it can be tested for?” “How do you feel about genetic testing?” “Do you have any concerns?” Chunks and Checks “Wilson’s Disease is an autosomal recessive disorder. What is your understanding of this?” • Aiding Accurate Recall and Understanding Organises explanation and plans related to the patient’s perspective KEY POINT Genetic screening has a wider impact than just the patient being tested. For example, think about the impact testing for the Hunting Gene, or BRACA gene would have on a family. The initial consultation to discuss testing may need to be followed up with a further consultation, where you meet a wider family group. Uses clear & concise language “Autosomal recessive conditions, means that there is a 25% chance of a child being affected, a 50% chance of a child being an asymptomatic carrier and 25% chance of a child being unaffected nor a carrier.” “Genetic testing is recommended for siblings and children of affected persons with Wilson’s Disease, in order to manage people early and prevent the development of complications” “A blood test will be able to tell us if you and your family have the genetic mutation” “If anyone tests positive, through screening, we can arrange follow up for them to avoid them developing complications.” Elicit patient’s beliefs, reactions and feelings “How do you feel about this so far?” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST Hepatology - Wilson’s Disease 375 CONTENTS LIST • Achieving a shared understanding incorporating the patient’s perspective Relates explanations to patient’s perspective Provides opportunities and encourages patient to contribute “Do you have any questions or concerns at this point?” “Is there anything that has been unclear up until this point?” • Closing the session: Planning & Shared decision-making Check that patient accepts plan and all concerns are addressed FU RTHE R RE A DING • 2012 EASL guidelines on Wilsons Disease HEPATOLOGY CONTENTS LIST available here ONLINE RESOURCE RCSI 38 4 Hepatology - Primary Sclerosing Cholangitis CONTENTS LIST C OMMUNICATIO N/ETH I CS KEY POINT Use the CalgaryCambridge model for communication Topic: Consent for OGD for variceal surveillance in established cirrhosis KEY POINTS: • Initiate the session: Greet patient, confirm their name and introduce yourself Establish rapport Identifies the reason for the consultation: Consent for an OGD for surveillance of varices secondary to liver cirrhosis due to PSC • Providing the correct amount and type of information Assess the patient’s starting point “What do you understand about the procedure?” “Do you know why this is recommended?” • Aiding accurate recall and understanding Chunks and Checks Organises and explains procedure to the patient in language they can understand Check’s patient’s understanding periodically. “The procedure is called an oeosophagogastroduodenoscopy or OGD. It involves a doctor who uses an instrument called an endoscope to look at the inside lining of your oesophagus (food pipe), stomach and duodenum (first part of the small intestine).” “This is done so that we can get a good view of the blood vessels along your oesophagus to check to see if they have become swollen and dilated because of the problem that you have with your liver.” “This is important because if these blood vessels get too swollen there is a chance they could cause bleeding, and even become life-threatening.” “You may receive sedation for the procedure, where you may be slightly aware but not completely asleep.” “Do you have any questions so far?” Benefits of Procedure “If the swollen blood vessels are identified during the procedure, we can immediately treat them by a procedure called ‘banding’. This will prevent them from enlarging.” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 HEPATOLOGY CONTENTS LIST Hepatology - Primary Sclerosing Cholangitis 385 CONTENTS LIST Risks of the procedure: “As with every procedure there are some risks. Commonly, bloating, abdominal discomfort, and bruising at the injection side can occur. You may also feel drowsy and disorientated for some time after receiving sedation.” “1 in 1,000 will experience bleeding from the oesophagus (food pipe), stomach or duodenum. This is often minor and can generally be stopped through the endoscope. Rarely, it can be more significant bleeding where surgery or interventional radiology is needed to stop the bleeding.” “1 in 5,000 will accidentally get a hole (perforation) in the oesophagus, stomach or duodenum. This can cause a leak of stomach contents into the abdomen. If a hole is made, you will be admitted to hospital for further treatment which may include surgery” • Achieving shared understanding: Incorporating the patient perspective Provide opportunity and encourage the patient to contribute. Elicit patient’s beliefs reactions and feelings • Closing the session: Planning and shared decision-making Negotiate a mutually acceptable plan Forward plan and summarise session Check patient is comfortable with plan and has no further questions FU RTHE R RE A DING • UK PSC Guideline (BSG) HEPATOLOGY CONTENTS LIST available here ONLINE RESOURCE RCSI 39 6 Hepatology - Primary Biliary Cholangitis CONTENTS LIST C OMPLICATIONS • Osteoporosis (↓Vitamin D) • Hypercholesterolaemia and xanthomas • Cirrhosis and associated complications • PBC recurrence post liver transplant (30% after 10 years) P RO GNOSIS • Once jaundice develops survival < 2 years • Early stage with treatment may have normal life-expectancy C OMMUNICATIO N/ETH I CS Topic: Consent for OGD for variceal surveillance secondary to cirrhosis in PBC (See chapter on ‘PSC’ for full Calgary-Cambridge communication model example) F U RTH ER READ ING ONLINE RESOURCE • 2017 EASL guidelines for PBC • Bezafibrate for PBC- 2018 NEJM BEZURSO trial R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 available here available here HEPATOLOGY CONTENTS LIST CONTENTS LIST Nephrology - Self-Assessment 457 SELF -A S S E S S ME N T CO M MU NIC AT I ON/ETH ICS TO PICS Topic: Obtaining consent to commence haemodialysis KEY POINTS: • The procedure: Haemodialysis is a procedure that will be needed to carry out several times per week. It takes approximately 3-4 hours per session. It functions to replace the work of the kidneys. It cleans the blood by removing waste products normally functioning kidneys would remove. During haemodialysis the patient will need to be attached to the machine via tubes connected to your permcath/fistula/ central line, are therefore largely confined to the bed during that time. During the procedure, the patient may need blood tests, or receive blood products. • Benefits Haemodialysis is a life-sustaining process. It is not however a cure for the kidney damage It will improve some of the symptoms you have been having • Risks Bacterial or viral contamination of blood (including Hep B and Hep C), which may cause sepsis or long-term infection and disease including liver disease Bleeding due to blood clotting problems or disconnection of the rubes Clotting of access site Infection or bleeding at access sites (permcath, central line, fistula) Allergic reaction and shock Cardiac arrest or shock • Common Side effects during procedure Light-headedness or fainting (typically due to fluid removal during dialysis) Nausea Palpitations NEPHROLOGY CONTENTS LIST RCSI 45 8 Nephrology - Self-Assessment CONTENTS LIST • Alternative options Peritoneal dialysis Kidney transplant No haemodialysis: this will result in death without spontaneous kidney damage recovery Topic: Obtaining consent for a renal biopsy in glomerulonephritis with acute kidney failure KEY POINTS: • Introduction “Hello my name is_____, I am one of the doctors on the kidney team currently looking after you” “I’d like to discuss a procedure with you, and get your consent for this.” • Providing the Correct Amount and Type of Information Assess patient’s starting point “Would you prefer me to call you Malik or Mr. Abbas?” “Have you ever needed this procedure done before?” Gives explanation at appropriate times Chunks and checks “You initially came to us with signs and symptoms of kidney damage.” “This was confirmed on the blood and urine tests that we conducted” “Currently, we do not have a diagnosis for the cause of the kidney damage. This makes treating the underlying problem more difficult” Give explanations at appropriate times avoiding jargon • Aiding Accurate recall and understanding Organise your explanation and divide it into sections Use explicit sign-posting “In order to get a clearer diagnosis for the cause of your kidney damage, a biopsy of the kidney would be helpful to guide the right treatments for you” “I’d like to go through the procedure itself, benefits of doing the procedure, risks of the procedure and alternative options for this procedure” Use repetition and summarising to reinforce the information Use concise language that’s easily understood R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 NEPHROLOGY CONTENTS LIST CONTENTS LIST Nephrology - Self-Assessment 459 “The procedure is performed at your bedside. You will be asked to lie on your back. An Ultrasound is used to guide the biopsy needle. Local anaesthetic is used to numb the area for the biopsy. Once the area is numb, a kidney biopsy needle is used to take a sample of the tissue. You may feel the movement or pressure of the needle but you should not feel pain.” “After the procedure you will need to lie on your back for 6 hours, this will help compress the biopsy site to help prevent complications.” “The benefits of doing the kidney biopsy would be to help diagnose the problem that has led to your kidney injury. It will also help guide the correct treatments that are likely to be effective for your condition” “Early correct treatment, helps avoid long-term kidney damage” “There are several risks with the procedure” “Infection, bleeding (uncommonly this can be severe), pain at the biopsy site., passing blood in the urine or heavy clots in the urine ( risk of 1 in 100), the ned for a blood transfusion due to blood loss, rarely a nephrectomy (removal of the kidney) may be needed to stop the bleeding ( 1 in 1000 to 1 in 1500), death is possible from the procedure” The risks should be given in chunks and check with the patient how much information they wish to receive. Use visual methods of conveying information Check patient’s understanding “Do you have any questions so far, Mr Abbas, or is there anything that is not clear to you?” • Achieve a shared understanding: incorporating the patient’s perspective Relate explanations to previously elicited concerns or beliefs Provide opportunity and encourage patient to contribute Picks up and responds to verbal and non-verbal cues Elicit patient’s belief, reactions and feelings and addresses where necessary NEPHROLOGY CONTENTS LIST RCSI 46 0 Nephrology - Self-Assessment CONTENTS LIST • Planning: Shared Decision Making Shares own thinking as appropriate: thoughts, and dilemmas “I believe a biopsy can be helpful here to ensure you get onto the right therapy as soon as possible, and hopefully avoid long-term kidney damage” Involve the patient and offer choices “There is the option of starting a treatment and monitoring your kidney’s response without a biopsy” Ascertain the level of involvement the patient wishes in making the decision and negotiate a mutually acceptable plan Checks with patient if accepts plan and concerns have been addressed “Do you consent to proceeding with the kidney biopsy?” “Do you have any further concerns or queries that we have not yet discussed?” • Closing the Session Contracts with patient regarding the next steps for patient and physician “If you consent to proceeding, Mr. Abbas, please read and sign this consent form. I will then arrange for you to have the procedure tomorrow morning” Ensure an appropriate point of closure, summarise the session briefly and final check the patient is comfortable with the plan R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 NEPHROLOGY CONTENTS LIST CONTENTS LIST Endocrinology - Self-Assessment 549 SELF -A S S E S S ME N T CO M MU NIC AT I ONS AND ETH ICS Topic: Discussion with patient with type 2 Diabetes around lifestyle modifications secondary to presentation HHS. KEY POINTS: • Initiate the session Greet patient, obtain patient’s name, introduce self Demonstrates respect and interest, and attends to patient’s physical needs • Providing the correct amount and type of information Chunks & checks ‘Mr Sullivan can you tell me about your condition and the problems that you have been having?’ ‘you have a very important role to play in managing your diabetes not only with your medication but also with diet and exercise.’ ‘These changes can be small but can make a big difference to your health’ They can be difficult to follow all of the time but they are important your future well being.’ Address any concerns or knowledge gaps the patient has Give explanation at appropriate times • Aiding Accurate Recall and Understanding Organises Explanation (discrete sections with logical sequence) ‘The changes we would like you to make revolve around getting enough exercise and being aware of your sugar intake.’ Exercise Even a small amount of exercise 30mins per day of light exercise including walking can help to reduce your weight and therefore help you to get control of your diabetes. Weight reduction is key to help you to manage your blood sugars and reduces other risk factors including high blood pressure. ENDOCRINOLOGY CONTENTS LIST RCSI 55 0 Endocrinology - Self-Assessment CONTENTS LIST You should try and build up exercise slowly and gradually and be aware that this may mean that you will need less medication. Diet Being aware of your sugar intake is very imporntant in managing your sugars. The ideal is to cut out all processed sugars entirely such as sweets and chocolates and to be aware of the sugar content of other foods and drinks such as orange juice which can have a very high sugars. It can be helpful to keep a diary of your food to see what you are eating. Check patient’s understanding periodically ‘Do you have any questions so far, Mr Sullivan ?’ • Achieving a Shared Understanding: Incorporating the patient’s perspective How do you feel about making these changes? ‘Do you need any further clarification?’ Elicit patient’s beliefs, understanding and reactions Pick up and respond to patient’s verbal and non-verbal cues • Planning: Shared Decision Making Relate explanations to patient’s perspective Provide opportunity to encourage patient to contribute ‘These changes will help to contribute to you staying well and staying on track with your diabetes.’ Involve patient & explore management options Negotiate a mutually acceptable plan ‘I can provide you with some literature and link you in with our specialist nurse who has some more information about how to practically apply these strategies.’ Checks with patient if they accept the plan and concerns have been addressed • Closing the session Summarise session Safety net ‘Should you have any other questions or queries then please come back to me and ask me and I can get you the information. Final check patient agrees and is comfortable with the plan R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 1 ENDOCRINOLOGY CONTENTS LIST CONTENTS LIST Endocrinology - Self-Assessment 551 Other topics to consider Diabetes Mellitus • Patients should also be educated on the symptoms of hyperglycaemia, including blurred vision, thirst, frequent urination, or tiredness, and should see their physician immediately if these occur • If patients smoke, they should be strongly advised to quit, and offered appropriate treatments as needed • Patients should be up to date with their vaccination schedule • The physician should help the patient plan how often to check blood glucose. The most likely times would be before each meal and at bedtime. Patients may also check 2 hours after meals and when exercising. • Patients should usually have an HbA1c performed every 3 months Addison’s Disease • Patients with Addison's disease should be instructed to carry a medical alert (bracelet or card) warning about their condition and what should be done in case there is loss of consciousness or major trauma, stress, or infection • Patients should be empowered by careful education, so that they know when to increase replacement doses appropriately (e.g., when febrile, or vomiting, or in preparation for elective surgical procedures) • Patients should have syringes with hydrocortisone (100 mg). These should be administered in an emergency, and NOK should be trained in case of unconsciousness or major trauma. If available, prefilled syringes should be provided. • Lifestyle modification (including maintenance of a healthy weight, regular exercise, avoidance of alcohol excess, dietary salt restriction, and smoking cessation). Dietary salt restriction may reduce the dose of aldosterone blocking drug required ENDOCRINOLOGY CONTENTS LIST RCSI CONTENTS LIST Ge ro n to lo gy - Self-Assessment 69 SELF -A S S E S S ME N T CO M MU NIC AT I ON AND ETH ICS 1. Use the Calgary Cambridge method of giving information to explain the diagnosis of dementia to a patient and their carer. Set up the consultation with few physical barriers adopting open posture and using positive communication skills including active listening. Chunk information for the patient and check for understanding. Assess for capacity KEY POINTS: • Establish baseline understanding of condition and impact to date. • Counsel the patient around long-term sequelae of the disease. • Discuss progressive and ongoing nature of the disease sensitively • Discuss the pathophysiology of the dementia • Discuss the pharmacological management and their progression. • Discuss adaptations to the home and the ongoing role of the MDT in managing the disease. • Counsel around supports outside of the hospital. • Provide literature and valid online information for further selfdirected research. • Allow the patient and their carer to ask questions. ETHICS: CAPACITY ASSESSMENT; CONSENT V ASSENT 2. Communicating diagnosis of delirium and its implications to a family member/caregiver. Using the Calgary Cambridge model of communication as a guide. Set up the consultation with few physical barriers within the room. Adopt an open posture and body language. Use positive communication skills including active listening using nodding and appropriate eye contact. Chunk information for the family member and check for understanding. KEY POINTS: • Establish the diagnosis and the key points of the diagnosis and the areas of deficit. GERONTOLOGY CONTENTS LIST SCAN HERE Calgary Cambridge method or click here TOP TIP CURVES for assessment of capacity Choose/Communicate - Can the patient communicate their decision to you and can they make a choice between the options Understand - Can they understand what you are saying. A good way of deciding on this is to get them to repeat back in their own words what they are being asked. Reason - Can they provide logical explanations of what is being asked and their own logic for their conclusion Value - Is the patient's decision in line with their values as previously or otherwise known. Emergency - In times when there is a threat to life capacity assessment may be done afterward. Surrogate in the absence of capacity is there a surrogate to advocate for the patient in their best interest. RCSI 70 G ero n t o l o g y - S e l f - A sse ssme n t CONTENTS LIST • Discuss/outline the aetiology and key percipients. • Outline strategies for lessening delirium. • Discuss some of the possible risks. • Outline the long-term complications. • Counsel on possible supports within the hospital and the community upon discharge. • Counsel on the impact of the physical environment with regard to lessening symptoms. 3. Discussing strategies for maintaining well-being and reducing frailty with a patient. Using the Calgary Cambridge model of communication as a guide. Set up the consultation with few physical barriers within the room. Adopt an open posture and body language. Use positive communication skills including active listening using nodding and appropriate eye contact. Chunk information for the family member and check for understanding. KEY POINTS: • Establish that frailty is a health state rather than diagnosis. • Establish the key features that are assessed when assessing frailty. • Discuss/outline contributing factors and ways of combatting/ reversing these. • Counsel on possible supports within the hospital and the community upon discharge. • Outline the long-term complications. • Counsel on the impact of the physical environment with regard to lessening symptoms. 4. Counselling regarding Anticoagulation for atrial fibrillation post stroke 5. Discussing with a patient the importance of engaging in moderate to heavy exercise following a stroke. 6. Discussion regarding functional deficits that may be present post stroke and the role of each of the MDT members in rehabilitating these deficits. R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 GERONTOLOGY CONTENTS LIST CONTENTS LIST Ne u ro lo gy - Self-Assessment 163 SELF -A S S E S S ME N T CO M MU NIC AT I ON AND ETH ICS Topic: Discussion with a patient with newly diagnosed epilepsy about the need to start on an anti-epileptic medication KEY POINTS: • Driving The patient must cease driving immediately In Ireland, a person with epilepsy can drive provided they have been free of seizures for one year and are certified fit to drive by a doctor • Triggers Discuss the importance to avoid alcohol and maintain good sleep hygiene • Family members Educated around recognising a seizure and when to administer medications • Fertility Some anti-epileptic medications are teratogenic, and patients need to be advised of this and about appropriate contraception Topic: Discussion of genetic testing in Huntington’s disease and its implications KEY POINTS: • Huntington’s disease has an AD inheritance pattern, is invariably fatal and currently has no cure • Testing is fraught with bioethical dilemmas • Testing one family member has implications for other family members and their offspring If one member does not wish to know, and the other tests positive or negative, it can affect them Having a positive test for the gene unfortunately does not change the outcome and can add to anxiety Testing can alleviate anxiety by remove uncertainty NEUROLOGY CONTENTS LIST RCSI CONTENTS LIST Rhe u m ato lo gy - Self-Assessment 265 SELF -A S S E S S ME N T CO M MU NIC AT I ON/ETH ICS Topic: Explaining the risks and benefits to starting methotrexate medication for rheumatoid arthritis. KEY POINTS: • Initiate the session: Greet patient, obtain patient’s name, introduce self Demonstrates respect and interest, and attends to patient’s physical needs • Providing the correct amount and type of information Chunks and Checks ‘Mrs Byrne can you tell me about your condition and the problems that you have been having?’ ‘What medications have you been taking so far?’ ‘Have you heard of a medication called methotrexate?’ ‘What do you know about it?’ Address any concerns or knowledge gaps the patient has Give explanation at appropriate times • Aiding Accurate Recall and Understanding Organises Explanation (discrete sections with logical sequence) ‘Methotrexate is a very useful medication that we use in the treatment of RA and other conditions.’ ‘It is an immune modulator, which means that it works to decrease your own body’s immune response.’ ‘It is known as a disease altering medication or DMARD’ ‘It is once a week medication so you would only have to remember to take it once a week.’ ‘As with any medication or procedure there are a certain things that you need to be aware of before you take this medication.’ ‘Generally most people have very little if any side effect however it is important that you are aware that it can have serious side effects that we will monitor at your clinic visits but that if you feel are happening you should contact us immediately.’ RHEUMATOLOGY CONTENTS LIST RCSI 26 6 Rh e u m a t o l o g y - S e lf - Asse ssme n t CONTENTS LIST These include Liver damage. (Explain hepatotoxicity including jaundice nausea and vomiting.) We will monitor your liver function with blood tests closely at the start and then less as we are sure that it is causing no damage. Pulmonary fibrosis. Methotrexate can cause lung damage and make you become short of breath however this is a rare side effect and again we would be monitoring you for signs of this. As this medication works to decrease your immune response there is an increased risk of you picking up infection. There is a chance that this medication could disrupt how your bone marrow works. We would be monitoring for all of these side effects closely and if they are likely to happen then they are more likely to happen when you first start taking the medication. However we would monitor you at every visit. Check patient’s understanding periodically ‘Do you have any questions so far, Mrs Byrne?’ • Achieving a Shared Understanding: Incorporating the patient’s perspective How do you feel about taking this medication? ‘Do you need any further clarification?’ Elicit patient’s beliefs, understanding and reactions Pick up and respond to patient’s verbal and non-verbal cues • Planning: Shared Decision Making Relate explanations to patient’s perspective Provide opportunity to encourage patient to contribute ‘This medication has been shown to help stop the progression of RA and to reduce the likelihood of disability and disease activity.’ Involve patient & explore management options Negotiate a mutually acceptable plan ‘We can do the screening blood test for you today and then look to start the medication next week if you would like?’ Checks with patient if they accept the plan and concerns have been addressed R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 RHEUMATOLOGY CONTENTS LIST CONTENTS LIST Rhe u m ato lo gy - Self-Assessment 267 • Closing the session Summarise session Safety net ‘‘Should you have any other questions or queries then please come back to me and ask me and I can get you the information. Final check patient agrees and is comfortable with the plan Topic in communication that could be covered in clinic review: • Joint assessment: DAS28-CRP score • Assess for extra-articular involvement shine • Medication compliance and complications • Screen for comorbidities: Infections, Osteoporosis, CVD risks, depression • Vaccination: yearly flu vaccination, & vaccinate against pneumococcal pneumonia • Assess for impairment of physical function: HAQ, grip strength • Return to work (occupational health): may need adjustments • Lifestyle advice: healthy eating, regular exercise, smoking cessation • Family planning annals E.g. Methotrexate/Leflunomide CI in pregnancy Systemic Lupus Erythematous • Patients with SLE should be advised to avoid excessive sun exposure and to use a sunblock with a sun protection factor (SPF) of ≥15. • In women of reproductive age, conception and pregnancy- related issues should be discussed early in the disease course so that specialist advice can be given and patients counselled regarding outcomes in relation to disease-related activity. • Although >50% of all lupus pregnancies are completely normal, all pregnant lupus patients would be considered high risk and be managed by a specialist obstetric team. Scleroderma Raynaud's prevention. Patients should: • Maintain central body temperature • Protect their hands • Minimise scratching, to avoid secondary infection • Use frequent emollients for pruritus • Avoid smoking. RHEUMATOLOGY CONTENTS LIST RCSI Haematology - Self-Assessment 383 CONTENTS LIST SELF -A S S E S S ME N T Practice communication scenarios or discussing medical ethics with others. Below are worked examples and further topics with some key points for exploration that might arise within the haematology specialty. CO M MU NIC AT I ON/ETH ICS Topic: Obtaining consent to give a blood transfusion (if patient unable to consent this should be discussed with the next of kin at an appropriate time). KEY POINTS: • Initiating the Session & Establishing rapport Greats patient, confirms their name and introduces self Demonstrates respect and interest “Good afternoon, I am one of the doctors on the Haematology team looking after you. Could I check your name and date of birth you please?” “Nice to meet you, how would you like me to address you? Julie or Mrs. Fleming?” KEY POINT No persons outside the courts can consent to treatment on behalf of an incapacitated adult. Treatment should be provided, in consultation with the NOK, acting in the patient’s best interests. • Identifies the reason for consultation “We, your team, would recommend for you to receive a blood transfusion. I’m here to discuss this with you, and to provide you with information around the benefits and risks of this, in order for you to make an informed decision about this treatment.” • Providing the correct amount and type of information • Chunks & checks Give information about procedure in manageable chunks and check patient’s understanding. “Your blood count, also called haemoglobin, is very low.” “This is due to the bleed from your bowel that you had when you came into hospital.” “Because the blood count is very low, it has been making you feel the symptoms you mentioned to us this morning such as feeling very tired, lethargic, and having chest pain when walking with, Mary, the physiotherapist. HAEMATOLOGY CONTENTS LIST RCSI 38 4 Haematology - Self-Assessment • CONTENTS LIST “These symptoms have impacted your rehabilitation” “Is there anything I haven’t been clear on, or you’d like to ask me about at this point?” Aiding accurate recall and Understanding Organises explanation using concise and easy to understand language. Uses repetition and summarisation if needed “A blood transfusion, would help bring the blood count back towards normal levels” “A blood transfusion is given as an infusion via the cannula you have, here at your bedside” “Before giving a transfusion, I would need to take a blood sample that tells us your blood type” • Achieving a shared understanding Relates explanation to patient’s perspective Ask the patient what information is helpful “Would you find it helpful if I talked through the benefits and risks of giving/receiving a unit of blood?” Benefits of the blood products: “It would improve your symptoms of fatigue, tiredness and chest pain.” “It may help you progress in rehab” “Rehabilitation is a step closer to getting back home” Risks of the procedure “Common side effects include a fever, rash or itching” “Uncommonly, giving you too much blood may result in you developing shortness of breath” “Giving the blood, also includes unavoidable antibodies in the product, which may complicate future pregnancy or complicate giving you a transplant in the future if you needed it” “Rarely the wrong blood type may be given to you that can result in a very serious immune reaction” “Very rarely, blood borne disease may be transmitted through the transfusion” Risk of not doing the procedure “Your blood count may take a very long time to recover by itself” R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 HAEMATOLOGY CONTENTS LIST Haematology - Self-Assessment 385 CONTENTS LIST “The haemoglobin could drop further to dangerous levels” “Very low blood counts or haemoglobin can result in heart attacks and calf pain, because of the low oxygen levels moving around your body” “Would you like me to explain anything further?” Provides opportunity and encourages patient to contribute Elicits patient’s beliefs and reactions • “What are your thoughts?” Planning: Shared decision making Involves the patient and encourages them to contribute their own ideas and explores management options with patient Negotiates a mutually acceptable plan & checks with patient if they accept the plan and if all of their concerns have been addressed “Do you consent to receive a blood transfusion?” • Closing the Session Contracts with the patient the next steps “If you’re agreeable, I will ask you to sign the consent form. Just because you’ve signed the form, does not mean you cannot change your mind at any point.” “In order for us to proceed with the blood transfusion, I will need to come back to you in a few moments to take a blood test for your blood type.” Final checks “Is there anything else you’d like to ask or discuss with me?” “Are you happy for me to go ahead and prescribe the blood?” HAEMATOLOGY CONTENTS LIST RCSI 38 6 Haematology - Self-Assessment KEY POINT A derivative of blood products such as IV albumin (as used in liver failure) may or may not be accepted by a Jehovah’s witnessthis is an individual decision and should be discussed with the patient before prescribing CONTENTS LIST Topic: Life-threatening bleed in a patient who is a Jehovah’s Witness KEY POINTS: • Jehovah witness is a Christian denomination religion in which members believe that it is against their God to receive blood products. This may lead to medical challenges for the patient’s care if blood products or surgery is required. Many regard the non-consensual transfusion of blood products as a physical violation. • Jehovah’s Witnesses can have differing beliefs around receiving blood products. This is why it is important to discuss this with the patient. Moreover, if the patient is incapacitated, and this is being discussed with the NOK, bear in mind the family may not share or agree with your patient’s religious beliefs, and the wishes of the patient are paramount. No other persons can consent on behalf of another adult. The majority of Jehovah Witness patients will refuse all blood products A minority do not believe their God prohibits blood products and will therefore accept blood transfusion if required Some will accept blood plasma fractions or a reinfusion of their own blood • An adult patient who has capacity has the right to refuse or consent to treatment. Therefore, an adult patient has the right to refuse a life-saving blood transfusion (differs and becomes more challenging in the cases of children) • In Ireland, there are hospital liaison committees to support and offer guidance to a Witness patient going through a medical procedure. Topic: Breaking Bad News: New cancer diagnosis (AML) KEY POINTS: • Prepare adequately for the consultation, ensuring you’ve read all of the patient’s background medical history and have all of their test results and anticipated some of the questions they may have after hearing the news. • SPIKES Framework is a helpful model for structuring the consultation. Also use the Calgary-Cambridge Model for giving information in conjunction. S- Setting Choose a comfortable, private and quiet room R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 HAEMATOLOGY CONTENTS LIST CONTENTS LIST Haematology - Self-Assessment 387 This may not always be possible, but avoid standing in a corridor Have tissues available and ensure you are uninterrupted Check with patient if they would like a family member or friend in with them P- Perception Establish the patient’s starting point and what they already know or what they might be expecting Discuss the events leading up to the diagnosis: symptoms, investigations, scans, biopsies I- Invitation Check if the patient is ready to receive their results today. Some patients may recognise it is not the news they hoped for and may want to put off the results K - Knowledge Deliver the information in sizeable chunks (warning shots), avoiding medical jargon Leave pauses to allow the patient to digest what you’re telling them Provide the diagnosis in clear and unambiguous language E- Emotions and Empathy Ensure you tone is respectful, slow and clear Recognise and respond to emotions If you do not know information or answer to their question, tell them that you do not know and make an effort to find accurate information as soon as is possible or after discussion with their specialist S- Strategy and Summary Make a plan together and inform the patient what the next steps are Written material can be helpful Ensure the patient’s questions and concerns have been addressed Highlight where the patient can go for more questions or concerns Offer to inform family members or NOK for them if they wish HAEMATOLOGY CONTENTS LIST RCSI 38 8 Haematology - Self-Assessment CONTENTS LIST Topic: Consultation around fertility and the effects of chemotherapy on future fertility KEY POINTS: • Chemotherapy can affect male or female fertility- the effects of which may be temporary or permanent. • For younger females, it may also result in early menopause • During chemotherapy, a person may still be able to become pregnant, but the chemotherapy is harmful to the growing foetus. It is therefore important to discuss reliable contraceptive methods during chemotherapy and sometime afterwards (duration should be advised based on regime and specialty but majority would advise waiting >2 years after chemotherapy) • There are several ways to try to preserve fertility and the options should be discussed with your patient, such as freezing embryos, freezing eggs or freezing ovarian tissue (rarer) • Other fertility options include: using donor eggs, using donor sperm, using donated embryos, surrogacy or adoption. R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 HAEMATOLOGY CONTENTS LIST CONTENTS LIST Infectious Disease - Self-Assessment 443 SELF -A S S E S S ME N T CO M MU NIC AT I ON & ETH ICS Topic: HIV diagnosis KEY POINTS: • HIV remains a disease with significant stigma attached. This stems largely from the route of transmission. There is really only one risk factor for HIV acquisition; being human. • Though verbal consent is still sought in most settings for testing, universal testing is now the norm in many settings. All pregnant woman in Ireland are offered testing. Only by expanding testing and treating those infected will incidence fall. • Patient-doctor confidentiality is important in HIV diagnosis • In a High Court Decision delivered on the 21st February 2018 Judge Michael Twomey ruled that a teenager’s HIV status was not to be disclosed to his suspected sexual partner. The Child and Family agency sought clarification from the courts whether a breach in confidentiality was permitted to inform his suspected sexual partner about his HIV diagnosis, to prevent harm occurring to them. The court ruling issue. Legal Test Patient confidentiality breach may occur “on the balance of probabilities that the failure to breach confidentiality creates a significant risk of death or very serious harm to an innocent third party” HIV Infection The court determined that HIV, although a serious condition, is no longer a terminal one but rather a chronic infection that can be managed. And therefore the court had ruled that HIV is not “very serious harm” to justify breaching a patient’s confidentiality, and transmission risk can be reduced through the use of condoms. Societal Issues If permission had been granted to breach confidentiality, this may impact the medical profession in the future. It may mean that medical professions could decide to disclose the diagnosis to the partner, or even be responsible if they failed to breach confidentiality and INFECTIOUS DISEASE CONTENTS LIST RCSI 44 4 Infectious Disease - Self-Assessment CONTENTS LIST harm came to a third party. Furthermore, it may prevent those with STD seeking help or treatment from medical professions out of fear of the doctor disclosing information to their partner. Topic: Majority of global burden of Dengue Fever is in areas of poverty PRACTICE YOURSELF KEY POINTS • Discuss global health inequalities, in the context of Dengue fever and other infectious diseases • ONLINE RESOURCE For further reading on health inequalities in Dengue Fever available here R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 INFECTIOUS DISEASE CONTENTS LIST CONTENTS LIST Dermatology - Atopic Dermatitis/ Eczema 461 CO M P L IC ATION S • Staphylococcus (superimposed infection) • Recurrent conjunctivitis • Eczema herpeticum This is a rapid development of numerous monomorphic, punched-out erosions with haemorrhagic crusting, vesicles may or may not be present P R O GNOS IS • AD impacts all aspects of patient’s quality of life and emotional well-being • Patients with AD have an increased risk of cardiovascular disease CO M MU NIC AT I ON/ETH ICS Topic: Encourage compliance with daily luke-warm baths emollient FU RTHE R RE A DING • Eichenfield LF et. al, Guidelines of care for the management of atopic dermatitis: Journal of the American Academy of Dermatology. 2014 Jul • Silverberg JI. Comorbidities and the impact of atopic dermatitis. Annals of Allergy, Asthma & Immunology. 2019 Apr 26. DERMATOLOGY CONTENTS LIST PRACTICE YOURSELF FURTHER READING RCSI CONTENTS LIST Dermatology - Psoriasis 471 CO M MU NIC AT I ON/ETH ICS Topic: Explaining the risks versus benefits of biologic treatment with the view of commencing therapy • Providing the Correct Amount and Type of Information Assess patient’s starting point “Would you prefer me to call you John or Mr. Reilly?” “Mr. Reilly, have you heard of the drug Infliximab before?” “What do you know about this medication?” Gives explanation at appropriate times Chunks and checks “Infliximab is an immunosuppressant therapy” “It is a type of medication called a ‘biologic.’” “It is given as an infusion over 3 hours every 8 weeks” “Do you understand all of this information so far, or is there anything you’d like me to explain further?” “The benefit to you in starting Infliximab is that it could improve your psoriasis and help with the uncomfortable constant itch you have mentioned, where the other medications we have tried have failed to do” “Although considered relatively safe, like all drugs it does have some side effects, although not everyone will experience these. Would you like me to go through these with you now?” “The side effects include sinusitis, increased risk of infection both new and recurrence of latent infections, increased risk of non-melanoma skin cancers, allergic reaction, worsening of heart failure, and very rarely lymphoma or nervous system disorders (demyelination)” “Do you have questions on any of this information, or need me to clarify anything further?” “In order to reduce the risk of developing some of these side effects, we check the bloods for any latent infections and treat these before you start on Infliximab, and we monitor your bloods regularly while on treatment” Give explanations at appropriate times avoiding jargon DERMATOLOGY CONTENTS LIST RCSI 47 2 Dermatology - Psoriasis CONTENTS LIST • Aiding Accurate recall and understanding Organise your explanation and divide it into sections Use explicit sign-posting “There are 3 things we need to do before starting the medication. The first thing we will need to do is take blood samples. The second thing we need to do is to organise for you to get a CXR for screen for TB. And the third thing we need to do is a Mantoux test” Use repetition and summarising to reinforce the information Use concise language that’s easily understood Use visual methods of conveying information “This is an information leaflet about the things we discussed that you can take the opportunity to read now or take home with you to read later” Check patient’s understanding • Achieve a shared understanding: incorporating the patient’s perspective Relate explanations to previously elicited concerns or beliefs Provide opportunity and encourage patient to contribute Picks up and responds to verbal and non-verbal cues Elicit patient’s belief, reactions and feelings and addresses where necessary • Planning: Shared Decision Making Shares own thinking as appropriate: thoughts, and dilemmas “I believe Infliximab could be the right option for you to control your psoriasis. It is immunosuppressing which carries risks, but your quality of life as you have described it is being significantly impacted by your psoriasis” Involve the patient and offer choices “How to you feel about starting Infliximab?” “Other options are to try an alternate biologic such as Adalimumab, or continue with topical therapies” Ascertain the level of involvement the patient wishes in making the decision Negotiates a mutually acceptable plan R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST CONTENTS LIST Dermatology - Psoriasis 473 Checks with patient if accepts plana and concerns have been addressed “Are you happy to start the process of starting on Infliximab?” “Do you have any further concerns or queries that we have not yet discussed?” • Closing the Session Contracts with patient regarding the next steps for patient and physician “I’m going to order the blood tests, and necessary investigations, and you are to book the next appointment to see me again in 3 weeks time to review the results” Ensure an appropriate point of closure, summarise the session briefly and final check the patient is comfortable with the plan FU RTHE R RE A DING • DermNetz for further images of Psoriasis available here DERMATOLOGY CONTENTS LIST ONLINE RESOURCE RCSI 48 0 Dermatology - Herpes Zoster CONTENTS LIST C OMMUNICATIO N/ ETHI CS Topic: Obtaining consent for a lumbar puncture from a patient suspected of having VZV intracranial infection. KEY POINTS ON CAPACITY: • The issue of capacity is a very important ethical issue here Capacity is time and decision specific 5 principles of Capacity Presume capacity in all Make every effort to support the individual to make a decision for themselves A patient has the right to make an unwise decision Decisions acted on for or on behalf of a person who lacks capacity must be made in their best interests Choose the least restrictive option (if there is a chance the patient may recover capacity, consider if the decision can be delayed until the person regains capacity) ONLINE RESOURCE In order for a patient to have capacity they must: Understand the information given to them Retain that information in making the decision Use and apply that information to themselves Communicate their decision F U RTH ER READ ING • Irish Medical Council Guide to Professional Conduct and Ethics for registered Medical Practitioners 8th Edition 2019, Chapter 3, Part 10 available here • DermNetz for further clinical images of Herpes Zoster available here R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST 48 6 Dermatology - Erythema Nodosum CONTENTS LIST C OMMUNICATIO N/ETH I CS Topic: History taking on a patient with Erythema Nodosum to ascertain likely aetiology of the EN • Initiating the session Establish initial rapport Greet patient and name Introduce yourself, your role and nature of interview Demonstrate respect and interest to the patient’s physical comfort Identify the reason for the consultation Identify the patient’s problems “What problems brought you to the hospital?” Listen attentively to the patient’s opening statement without interrupting or directing patient’s response Confirms list and screens “So the painful rash on your shins started last week, do you have any trouble with your bowels such as diarrhoea?” Negotiates agenda taking both patient’s and physician’s needs into account “I’d like to ask you some more questions that may help identify the cause for this rash, this will help start the right treatments for your rash. It may take some time for the rash to heal” TOP TIP Explore symptoms of IBD, Sarcoid, Haematological malignancies and infections • Gathering Information Exploration of patient’s problems Encourage patient to tell the story Use open and closed questioning technique appropriately Listen attentively and facilitate patient’s responses verbally and non-verbally Clarify patient’s statements that are unclear Use concise easily understood questions and avoid jargon Additional skills for understanding the patient’s perspective Actively determine and appropriately explore patient concerns, beliefs. Expectations and how each problem affects the patient’s life R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST CONTENTS LIST Dermatology - Erythema Nodosum 487 • Providing Structure Make organisation overt Progress from one section to another using sign posting “You’ve had intermittent abdominal pains, diarrhoea, with blood and mucous for the last 6 months before the painful rash started on your shins. I’d like to ask you now more about any previous medical diagnoses you have.” Attend to flow; the interview follows a logical sequence Attend to timing of interview and stay on task • Building Relationship Develop rapport, demonstrate appropriate non-verbal behaviour, use empathy, provide support and willingness to help Involve the patient: share thinking with the patient and encourage the patient’s involvement “What I’m thinking is now, is that the bowel symptoms you’ve been having are linked to this rash” • Closing the session Give preliminary information and checks patient understanding Summarise session Contract with patient next steps for patient and physician F URTHER REA D ING DermNetz: Erythema Nodsoum for further clinical images of EN available here DERMATOLOGY CONTENTS LIST ONLINE RESOURCE RCSI 49 4 Dermatology - Erythema Multiforme CONTENTS LIST MA NAGEM ENT 1. Preventative Vaccination of common associated infections: VZV, Hep A, Hep B vaccinations 2. Non-Pharmacological Majority of cases need no treatment Discontinue drug if causative 3. Pharmacological General Principle Treat underlying infection and supportive care Symptomatic relief Oral antihistamines Topical corticosteroids Oral involvement Mouthwashes with local anaesthetic and antiseptic If severe mucosal involvement (EM major) patient may need hospitalisation, and restrict oral intake Ocular involvement Ophthalmology referral & review Recurrent Disease Antiviral Prophylaxis for HSV infections e.g. Acyclovir 10mg/kg/day for at least 6 months If EM fails to respond consider immunosuppressive therapy e.g. Dapsone, Hydroxychloroquine C OMPLICATIO NS • Significant eye involvement may rarely result in loss of vision • Residual mottled skin discolouration P ROGNO SIS • PRACTICE YOURSELF Virtually all patients with EM recover with no sequelae C OMM UNICATION/ ETH I CS Topic: Discuss vaccination recommendations for prevention for a patient with vaccine hesitancy R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST Dermatology - Pyoderma Gangrenosum 503 CONTENTS LIST CO M MU NIC AT I ON/ETH ICS Topic: Obtaining consent for a punch skin biopsy • Providing the Correct Amount and Type of Information Assess patient’s starting point “Would you prefer me to call you Una or Mrs Fox?” “Have you had a skin punch biopsy before?” Gives explanation at appropriate times Chunks and checks “The rash you have looks like a condition called Pyoderma gangrenosum.” “Have you heard of this condition before? What do understand about pyoderma gangrenosum?” “This condition can look like several other conditions that result in ulcer formation like this. A skin biopsy can help make the right diagnosis and therefore inform the correct treatment options for you” Give explanations at appropriate times avoiding jargon • Aiding Accurate recall and understanding Organise your explanation and divide it into sections Use explicit sign-posting “The biopsy is a day procedure that involves removing a small piece of skin with local anaesthesia” Use repetition and summarising to reinforce the information Use concise language that’s easily understood Use visual methods of conveying information “This is an information leaflet about the things we discussed that you can take the opportunity to read now or take home with you to read later” Check patient’s understanding • Achieve a shared understanding: incorporating the patient’s perspective Relate explanations to previously elicited concerns or beliefs Provide opportunity and encourage patient to contribute Picks up and responds to verbal and non-verbal cues Elicit patient’s belief, reactions and feelings and addresses where necessary DERMATOLOGY CONTENTS LIST RCSI 50 4 Dermatology - Pyoderma Gangrenosum • CONTENTS LIST Planning: Shared Decision Making Shares own thinking as appropriate: thoughts, and dilemmas “I believe a biopsy can be helpful here to ensure you get onto the right therapy as soon as possible” Involve the patient and offer choices “There is the option of starting a treatment and monitoring response without a biopsy” Ascertain the level of involvement the patient wishes in making the decision and negotiate a mutually acceptable plan Checks with patient if accepts plan and concerns have been addressed “Do you consent to proceeding with the skin biopsy?” “Do you have any further concerns or queries that we have not yet discussed?” • Closing the Session Contracts with patient regarding the next steps for patient and physician “If you consent to proceeding, please read and sign this consent form. I will then book an appointment for you for the procedure as soon as is available” Ensure an appropriate point of closure, summarise the session briefly and final check the patient is comfortable with the plan FURTHER READING F U RTH ER READ ING • Su WP, et al. Pyoderma Gangrenosum: Clinicopathologic correlation and proposed diagnostic criteria. Int. J. Dermatol. 2004; 43:790-800 R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST Dermatology - Bullous Diseases 513 CONTENTS LIST • Dermatitis Herpetiformis Gluten free diet for life is strongly recommended Topical Treatments Dapsone: screen for G6PD deficiency and titrate dose If intolerant to Dapsone: Ultra-potent topical corticosteroids e.g. Betnovate or systemic steroids or rituximab CO M P L IC ATION S • Anxiety and depression • Secondary bacterial, fungal and viral infections • Complications of systemic and immunosuppressive treatments • Nutritional deficiencies and dehydration when mucosal involvement present CO M MU NIC AT I ON/ETH ICS Topic: Discussion with patient on the importance of adherence of a gluten-free diet, who has dermatitis herpetiformis and who is non-compliant with a gluten free diet for their Coeliac disease KEY POINTS: • Gluten free diet (GFD) will improve the skin condition • It will improve gut function and associated symptoms Both of these will improve overall quality of life • Long-term inflammation from coeliac disease can result in lymphoma (MALToma) • See Gastroenterology Chapter: Coeliac Disease for full list of complications FU RTHE R RE A DING The BLISTER trial ‘Bullous Pemphigoid Steroids and Tetracyclines Trial available here DERMATOLOGY CONTENTS LIST ONLINE RESOURCE RCSI 52 0 Dermatology - Dermatomyositis CONTENTS LIST MA NAGEMENT 1. • Prevention Manage the underlying condition • Screen for malignancy for a minimum of 3 years after presentation with dermatomyositis to reduce morbidity and mortality 2. • Non-pharmacological Treatments Photoprotection including fully covering clothing and SPF 50 daily • MDT input: physiotherapy for muscle weakness, Occupational therapy for home adaptions, SALT for swallow assessment, and Dietetics for optimal nutrition 3. • Pharmacological Treatments Topical Cutaneous Treatments Corticosteroids Tacrolimus • Oral Treatments Cutaneous treatments Hydroxychloroquine Azathioprine Methotrexate (or sub-cut) Muscle inflammation treatments Oral steroids e.g. Prednisolone 1mg/kg with slow taper Methotrexate (or sub-cut) P RO GNOSIS PRACTICE YOURSELF • Most patients require treatment throughout their lifetime, but DM completely resolves in about 1 in 5 patients • Patients who have a disease affecting their heart of lungs, or who also have underlying cancer, do less well and may ultimately die from their disease C OMMUNICATIO N/ETH I CS Topic: Counsel a patient with dermatomyositis regarding the risk of malignancy and the screening investigations required and follow-up needed R CS I Hand b o o k o f C lin i ca l Me d ic in e 1 st Ed it io n Vo l 2 DERMATOLOGY CONTENTS LIST Misce llan e o u s - Self-Assessment 547 CONTENTS LIST SELF -A S S E S S ME N T CO M MU NIC AT I ON AND ETH ICS Topic: Patient refuses treatment for drug toxicity and you are asked to make a capacity assessment KEY POINTS: • Every adult is presumed to have capacity • Capacity can fluctuate by time or day and is decision specific • Low MMSE score is NOT a substitute for capacity • llness can affect capacity temporarily • There are 4 decision-making abilities that constitute capacity Understanding Everything should be done to help the person understand Expression of choice Appreciation The person should be able to express a choice. Frequent reversal of choice may be considered lack of capacity The person needs to be able to weigh up the facts of the decision and apply the facts to themselves Reasoning The person needs to be able to infer consequences of their choice MISCELLANEOUS CONTENTS LIST RCSI