Congenital Urogenital Malformations

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Prefinal

 Renal agenesis

Topics

 Renal hypoplasia

 Supernumerary kidneys

 Renal fusion

 Ectopic kidney

 Ureteral atresia

 Duplication of the ureter

Renal agenesis

 Virtually always unilateral.

 Kidney is either absent or undeveloped.

 Usually causes no symptoms and found incidentally.

Renal Agenesis

Renal hypoplasia

 May appear as one small kidney with the other one larger than normal.

 Small kidneys also have small arteries and are associated with hypertension requiring nephrectomy.

Renal hypoplasia

Renal fusion (horseshoe

 Prevalence 1 in 1,000 people.

 Most frequent abnormality seen is a horseshoe kidney containing 2 excretory systems and 2 ureters.

 Usually asymptomatic but are prone to obstruction.

Renal fusion (horseshoe

Ectopic (Pelvis Kidney)

 In simple ectopy, the kidney does not ascend properly and is found in the pelvis or over the brim.

 Prone to obstruction and infection.

 Less commonly crossed ectopy without fusion. The kidney then lies on the opposite side and is not attached to the normally placed kidney.

Ectopic Kidney (Pelvis

Ureteral atresia

 The ureter may be absent or fails to extend to the bladder and therefore with a blind ending.

 It is associated with ipsilateral absent or multicystic kidney.

 Bilateral atresia is incompatible with life.

Unilateral atresia is usually asymptomatic but may cause hypertension.

Ureteral atresia

Duplication of the ureter

 One of the most common congenital malformations of the urinary tract with duplication found in 0.9% of a series of autopsies.

 More common in females and is often bilateral.

 Often asymptomatic but commonly presents with persistent or recurrent urinary tract infections.

Duplication of the ureter

Supernumerary kidneys

 Third kidney is very rare and not to be confused with the relatively common unilateral duplication of the renal pelvis.

Supernumerary kidneys

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